I taksaah, a bik takin i ke emaw, i kut emaw-ah hian lump emaw tumor thar emaw i hmuh hian engtin nge i ngaih? A tam zawkah chuan thil pangngaiah kan ngai a, kan ngaihthah thin. Mahse, a châng chuan, chutiang thil tê tê pawh chu kan ngaihven tûr thil a ni thei. Vawiin hian cancer hmuh tur awm lo tak, lump anga lang thei chungchang kan sawi dawn a ni. Hei hi fibrosarcoma an ti a.
A awlsam zawngin fibrosarcoma chu eng nge ni?
Fibrosarcoma hi cancer chi khat a ni a, soft tissue-ah a awm thin. Damdawi lamah chuan hei hi sarcoma kan ti a. Tunah chuan soft tissue chu eng nge ni tih i ngaihtuah mai thei. A awlsam khawp mai. Kan taksa peng hrang hrang inzawmkhawm leh vawn tlat tu tissue a ni. A dik tak chuan kan taksaa ruh leh ruh ang chi thil inzawmkhawmtu tendon leh ligament ang chi thilte hi heng connective tissue-ah hian an awm a ni.
Fibrosarcoma cancer hi taksa chhung thuk tak soft tissue-ah a lo awm fo thin. Ke (hip emaw thigh bone vel), kut chunglam, khup emaw, trunk emaw-ah a tam ber. Lu emaw, kawr emaw-ah pawh a lo awm tam lo hle bawk. A châng chuan he cancer hi ruh chhungah emaw, ruh khuh tu fibrous connective tissue-ah emaw pawh a lo awm thei bawk.
Nangmah emaw, i fa emaw hian he diagnosis hi i dawng a nih chuan, a hnua thil thleng tur chu thil tam takah a innghat a ni. I kum, cancer lian leh te, a awmna hmun te hian hmun a chang vek ang. I doctor chuan i diagnosis a zirin engkim a hrilhfiah ang.
Hei hi chi hnih lian tak a ni.
Fibrosarcoma hi chi hnih ah then theih a ni. Heng chi hnih hi an danglam hle a ni.
| Cancer chi hrang hrang | Hrilhfiahna |
|---|---|
| Nausen/Pianpui Fibrosarcoma a awm | Hetiang chi hi pian tirh emaw, pian hnu lawkah emaw hmuh tur a awm tlangpui. He tumor hi a thang chak hle a, mahse taksa peng dangah a darh a rinawm loh hle. Chuvangin, a dam vek theih dinhmun a ni . |
| Puitling chi hrang hrang Fibrosarcoma | Hetiang chi hi kum 20 leh 60 inkar puitlingah hmuh tur a tam ber a, mahse a chang chuan naupang kum upa zawk leh puitling naupang zawkah a awm thei. Infantile type ang lo takin a tlangpuiin a aggressive zawk a, enkawl a harsa zawk thei bawk. |
Fibrosarcoma hi a awm lo hle a ni. Puitling leh naupangah pawh a tlem hle. Chuvangin taksaa lump lo awm apiang hi cancer a ni tih hlau suh. Mahse, lump thar lo awm apiang chu doctor hnenah entir hi a finthlak hle.
He natna lan chhuah dan engte nge ni?
Fibrosarcoma symptoms a lan theih nan hun rei tak a ngai tlangpui. Heng tumor te hi taksa chhung thuk takah soft tissue-ah an lo awm thin avangin, tumor chu a lian tawk a, a bul hnaia nerve emaw thisen kalna kawng emaw a press thei hma chuan engmah i hre lo mai thei.
Hengte hi a lan chhuah dan tlangpui chu a ni:
- Lump nem tak, natna nei lo emaw, na deuh emaw: Hei hi ke, kut leh ke ruh ah a awm thei.
- A tingling sensation emaw sharp, stabbing pain: A chang chuan "pins and needles" kan ti thin. Hei hi tumor bula nerve pakhat pressure vang pawh a ni thei.
- Abnormal swelling: Hetiang swelling hi tumor hian thisen kalna kawng a press hian a awm thei.
Heng symptoms te hi natna dang, na lo zawkte nen a inang thei a, chuvangin doctor chauhvin heng inthlak danglamna te hi fibrosarcoma vang nge, natna dang, cancer ni lo (benign) vang a ni tih chiang takin a hre thei ang.
Fibrosarcoma vei chhan leh hlauhawmna te chu engte nge ni?
Zirchiangtute chuan fibrosarcoma thlentu dik tak hi an la hre chiang lo. Mahse, cell-a genetic mutations hian hmun a chang niin an ngai. A awlsam zawngin kan cell-a DNA-ah hian inthlak danglamna a awm a. Heng inthlak danglamna te hian cell te chu rang tak leh thunun theih lohvin a inthen darh a, cancer tumor a siam thin.
A bik takin naupang fibrosarcoma-ah hian genetic mutation tlanglawn tak hmuhchhuah a ni. Chung zinga 90% vel chu NTRK gene family-a harsatna awmte nen a inzawm a ni. Heng genes te hian hna an thawh that loh chuan cancer tumor a lo awm thei a ni.
Risk tipung thei thil
Researcher te chuan hereditary condition thenkhat hian fibrosarcoma vei theihna a tipung thei tih an hmuchhuak.
- Chhungkaw adenomatous polyposis a awm thin
- Li-Fraumeni natna a ni
- Neurofibromatosis chi khat `(Neurofibromatosis chi 1)`
- Basal cell carcinoma syndrome tih loh tur
- Retinoblastoma natna a ni
- Tuberous sclerosis natna a ni
- Werner natna `(Werner natna)`
Chu bâkah, damdawi lam thil dang ṭhenkhat chu hei hi a inzawm thei bawk:
- Bone infarction (ruh lama thisen kal tlem avanga ruh cell thi) .
- Ruh natna rei tak (Chronic osteomyelitis) .
- Fibrous dysplasia a awm thin
- Paget-a natna chu ruh a ni
Environment leh i medical history kal tawh nena inzawm risk factors pawh a awm bawk:
- Tun hmaa cancer awmna hmuna radiation therapy dawng tawh.
- Cancer awmna hmunah kang nasa tak a awm.
- Chemical thenkhat, thorium dioxide, vinyl chloride, arsenic te nena inzawmna.
- Surgery hmanga taksa chhunga metal part (e.g. chromium, cobalt, nickel) dah luh.
Engtin nge doctor hian hei hi a hriat chian? (Diagnosis) tih a ni.
Doctor-te chuan fibrosarcoma hmuhchhuah nan test eng emaw zat an nei a. Heng test atanga thu hriatte hian cancer stage leh grade a hril a ni.
- MRI scan (Magnetic Resonance Imaging): Hei hi fibrosarcoma hriat theihna atana hman tlanglawn ber a ni. Tumor lian leh te, a awmna hmun te, thisen kalna kawng emaw, nerve emaw a nghawng em tih chiang takin a tarlang thei a ni.
- CT scan (Computed Tomography scan): Hei hian X-ray hrang hrang leh computer hmangin i soft tissue leh ruh te chu three-dimensional (3D) image a siam a.
- Biopsy: Hei hian tumor atanga tissue te tak te (core needle biopsy) emaw, tumor pumpui (excisional biopsy) emaw enfiah nan lakchhuah a ni. Pathologist chuan laboratory-ah tissue chu a enfiah a, cancer cell a awm em tih a enfiah thin.
- Immunohistochemistry (IHC): Hei hi laboratory test bik a ni a, antibodies an tih protein hmangin tumor chu fibrosarcoma emaw soft tissue cancer chi dang emaw a nih leh nih loh finfiah a ni.
Engtin nge cancer stage hrang hrangte hi an hriat theih?
Doctor-te chuan cancer hi eng chen nge a darh tawh tih leh a nasat zia hriat nan stage hrang hrangah an thliar hrang a ni. Hei hian tumor lian leh te, a awmna hmun leh a darh tawh loh a ngaihtuah a ni. Cancer "grade" pawh an en bawk. Hei hi microscope hmanga en chuan cancer cell te hi a pangngai lo ang tih hi a ni. Cell pangngai lo anga langte chu "high-grade" cancer anga ngaih an ni a, chu chu a na zawk thei a ni.
| Dawhsan | Hrilhfiahna |
|---|---|
| Phase I ah hian a awm | Hengte hi fibrosarcoma grade hniam tak tak an ni. Tumor hi centimetre 5 aia lian a nih chuan advanced stage anga ngaih a ni. |
| Phase II-na a ni | Mid-grade emaw high-grade emaw fibrosarcoma a awm thei. Tumor hi centimetre 5 aia lian a nih chuan a hmasawn zawk. |
| Stage III-na a ni | Fibrosarcoma grade sang tak a awm. Tumor hi centimetre 5 aia lian a ni a, a bul hnaia lymph node-ah a darh thei bawk. |
| Stage IV-na a ni | Fibrosarcoma eng grade emaw size emaw pawh nise taksa peng emaw tissue hla tak takah a darh (metastasized) tawh a ni. |
I doctor chuan i cancer stage a zirin enkawl hnuah eng nge a chhuah dawn tih a hrilhfiah ang che.
Hei hi eng enkawlna nge ni?
Fibrosarcoma enkawl dan hi thil tam takah a innghat a, chung zingah chuan i hriselna zawng zawng, i duh zawng leh cancer chi hrang hrang te pawh a tel.
Puitling chi fibrosarcoma enkawlna
- Surgery: Hetiang tih danah hian doctor-te chuan cancer cell awm tawh lo turin cancer natna hrik leh a chhehvela tissue hrisel tlemte chu an paih chhuak thin.
- Radiation Therapy: Radiation therapy hi operation hmain tumor tihtlem nan emaw, operation hnua cancer cell la awm zawng zawng tihchhiat nan emaw pek theih a ni.
- Chemotherapy hmanga enkawlna:Doctor thenkhat chuan he damdawi hi pe mahse, puitling atanga fibrosarcoma tan chuan a hlawhtling vak lo. Hetiang cancer chi hi chemotherapy lakah hian a chhang tha lo fo thin.
Nausen fibrosarcoma enkawl dan
- Surgery: Naupangah chuan surgery hmanga tumor lakchhuah hian natna chu a tidam kim thei fo thin.
- Radiation leh/ emaw chemotherapy: Heng enkawlnate hi operation hmaa tumor tihtlem nan emaw, a hnua cell la awmte tihchhiat nan emaw hman a ni. Puitling form ang lo takin naupang fibrosarcoma tam zawk chuan chemotherapy an dawng tha hle.
- Targeted Therapy: He enkawlna hian `NTRK` gene lama harsatna a awm avangin cell te chu rang taka inthen darh thei lo turin a titawp thei a ni. Hei hian tumor a ti tlem thei a, operation pawh a ti awlsam thei bawk.
Enkawl hnuah engtin nge a dinhmun? (Prognosis) tih a ni.
Infantile fibrosarcoma tan chuan outcome a tha hle. Chûng zînga a tam zâwk chu operation, radiation, chemotherapy emaw, targeted therapy emaw hmanga tihdam vek theih a ni. Kum 10 chhunga damchhuah zat hi 90% vel a ni. Surgery hmanga cancer hnuhma zawng zawng hlawhtling taka paih chhuah theih chuan chu zat chu 100% a hnaih tawh a ni.
Puitling atanga lo chhuak fibrosarcoma dinhmun hi a buaithlak zawk. Vawi tam tak chu heng tumor te hi nerve emaw thisen kal dan emaw tichhe thei khawpa lian an lo seilian hnuah hmuhchhuah a ni. Cancer dang ang bawkin, a hmaa hmuhchhuah hian result tha zawk a thlen thin. Cancer hi a lo zual tawh chuan enkawl a harsa lehzual thin. Damlo zinga a chanve vel chuan enkawl hnuah natna hi an nei leh thei a ni.
Hetiang dinhmun hi i neih chuan engtin nge i in enkawl ang?
Mi tam tak chuan cancer an vei tih an hriat hian tanpui theih lohvin an inhria. Heng rilru natnate hmachhawn dan tha ber pakhat chu enkawl lai leh enkawl zawhah mahni in enkawl hi a ni. I tih theih ṭhenkhat chu hetiang hi a ni:
- I follow-up plan hrethiam rawh: I doctor hnenah dam leh hunah leh follow-up appointment-ah eng nge i beisei tur tih zawt rawh.
- Manage Anxiety: Cancer lo lang leh tur hriat hmasak nan enkawlna hnua check-up neih fo hi a pawimawh hle. Mahse, lungkhamna a thlen thei bawk. Chumi chungchang chu counselor nen sawiho rawh.
- Ṭanpuina dil rawh: I enkawl chhung hian tanpuina i mamawh ngei ang. I hmangaihte’n ṭanpui che an nghak reng mai thei. I tanpui theih dan tur hrilh rawh.
- Hriselna \ha lam ngaihtuah rawh: Chaw \ha ei te, exercise \ha neih te, mut \ha te hi a pawimawh hle.
- Chawl:Cancer leh cancer enkawl dan hian i chau hle thei a ni. Enkawl lai hian a theih ang anga chawlh hahdam tum ang che.
- Stress do rawh: Meditation, relaxation exercise, leh deep breathing exercise ang chi thilte hian stress tihziaawmna kawngah a pui thei a ni.
Engtikah nge Doctor i hmuh a ngaih?
Enkawl zawhah kum hnih hmasa ber chu thla thum danah doctor i pan tlangpui ang a, chumi hnuah kum li atanga kum nga chhung chu a rei deuh deuhin i hmu ang. Fibrosarcoma hi a lo lang leh a nih chuan, chu chu kum nga hmasa berah a thleng tlangpui a, he schedule hian a lo lang leh thei a nih chuan a hmaa hriat theih nan a pui ang.
Lump thar emaw, natna thar emaw i neih apiangin i doctor i biak tur a ni.
Engtikah nge Emergency Treatment Unit (ETU)-ah i kal a ngaih?
Cancer enkawlna tam tak hian i taksa hriselna a nghawng a, chu chuan natna kai theihna a tipung a ni. Enkawl laiin Emergency Department (ETU) pan a ngai thei tur symptom thenkhat chu hetiang hi a ni:
- Khawsik chu 38.3 degree Celsius (100.4 Fahrenheit) aia sang a ni.
- Khua a vawt a, a khur bawk.
- Mucus nen khuh.
- Pum natna.
- Diarrhea awm reng.
- Nausea leh luak chhuak reng reng.
Take-Home Thuchah a ni
- Fibrosarcoma hi cancer chi khat, taksa inzawmkhawmna (connective tissue)-a lo awm thin a ni.
- Hei hi chi hnih a awm a, chungte chu nausen chi (dam theih fo) leh puitling chi (aggressive zawk) te an ni.
- I taksaa lump thar, numbness, emaw, a danglam bikna emaw a lo awm chu ngaihthah suh. Doctor hmu nghal rawh.
- Enkawl dan tur (surgery, radiation, chemotherapy) chu cancer chi hrang hrang, a stage leh i hriselna dinhmun a zirin a innghat a ni.
- Natna hi a hmaa hriatchhuah hi a hlawhtling thei tur chuan a pawimawh hle.











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