I naute thinlunga he natna hmuh tur awm lo tak hi i zir dawn teh ang? (Aortic Arch tihbuai) .

Nausen piang thar in lama hruai haw hi chhungkaw tan chuan hun hlimawm tak a ni. Mahse chutih rual chuan nu leh pate tan hlauhna tlem a thlen thei bawk. "Naute a tha em?", "Naute thaw a tha em?", "Engvangin nge a tap nasa em?" Hetiang zawhna hi i nei tawh mai thei. A tam zawkah chuan hengte hi thil pangngai a nih laiin, a chang chuan tlem a fimkhur deuh ngai dinhmun a awm fo thin. Vawiin hian nausen piang thara lo awm thei, mahse enkawl vat ngai thinlung natna hmuh tur awm lo tak chungchang kan sawi dawn a ni. Chu chu Interrupted Aortic Arch, a tawi zawngin IAA a ni.

A awlsam zawngin sawi ila, Interrupted Aortic Arch (IAA) hi eng nge ni?

Hei hi hrethiam tur chuan kan thinlung hnathawh dan hi han thlir hmasa ila. I thinlung hi chamber pali nei main water pump a ni ang tih han ngaihtuah teh.

• Upper chamber pahnih (Atria): Taksa atanga thisen "blue" deoxygenated "blue" chu chamber khatah a lut a, lung atanga oxygenated "red" blood chu chamber dangah a lut leh bawk.
• Chamber hnuai lam pahnih (ventricles): Hengte hi pumping chamber lian ber berte an ni. Khawthlang lamah chuan oxygen tlachham thisen chu lungah an thawn a, chu chu la chhuak turin. A lehlamah chuan taksa pum puia sem darh turin oxygen tamna thisen sen an pump chhuak a.

Taksa pum puia oxygenated thisen phurtu thisen kalna kawngpui ber chu Aorta an ti a . A tlangpuiin cane, emaw arch ang maia siam a ni.

Tunah chuan Interrupted Aortic Arch (IAA) -ah chuan aorta arch chu a kim lo. Tui tank atanga in chhung zawnga tui phurtu main pipe chu hmun hnih ah a inthen ang mai a ni . Chumi avang chuan thinlung hian engtiang pawhin nasa takin pump mah se, taksa hnuai lam ah oxygen tamna thisen a thawn thei lo. Hei hi natna khirh tak, nunna atana hlauhawm tak a ni. A chhan chu taksa peng thenkhatin thisen an dawn loh chuan chu taksa pengte chu a hlawhchham thei a, naute tan pawh hlauhawm tak a ni thei a ni.

Engtin nge i naute hian he natna hi a nei tih i hriat theih ang? Eng nge a lan chhuah dan?

IAA vei naute hian a pian hnu ni engemaw zat chhungin a natna lan chhuahna a nei tlangpui. Hei hi a chhan chu naute pian hma hian naute thinlung hian nu taksa atangin oxygen a dawng a, chu chu harsatna a ni lova, mahse a pian hnuah chuan naute thinlung hian a mah chauhin hna a thawh a ngai a ni. Chutah chuan he buaina hi a lo chhuak ta a ni.

A hnuaia symptoms te hi i fimkhur hle tur a ni.

Heng symptoms zinga pakhat tal i hriat chuan doctor pan nghal vat la, reilote lovah i hmu nghal ang. A tul chuan i naute chu damdawi in hnai ber Emergency Treatment Unit (ETU)-ah hruai la.

Hetiang dinhmun nena lo awm thei thinlung chhiatna dang

IAA vei naute hian a rualin thinlung lama harsatna dang engemaw zat an nei thei bawk.

• Ventricular Septal Defect (VSD): Hei hi thinlung pumpui hnuai lam pumping chamber (ventricles) pahnih inkar bang chhunga khur awm a ni. Mak tak maiin VSD neih hi IAA vei tan chuan hun eng emaw chen atan tanpuitu a ni thei a, a chhan chu oxygen nei thisen thenkhat chu khur kaltlangin taksaah a kal thei a ni.
• Atrial Septal Defect (ASD): Hei hi thinlung chunglam chamber pahnih inkar bang chhunga khur awm a ni.
• Truncus Arteriosus: Hei hi thinlung atanga thisen kalna kawng lian pahnih (aorta leh pulmonary artery) te inzawmkhawma pakhat siamna hmun a ni.

Engvangin nge naute chungah hetiang hi a thlen? Eng nge a chhan?

He thu i hriat hian nu leh pa kan nih angin i rilruah zawhna lo lang hmasa ber chu, "Hei hi kan sualna a ni em?" Dik tak chuan a ni lo.

Interrupted Aortic Arch (IAA) hi genetic defect avanga lo awm a ni . A awlsam zawngin kan chromosomes te hi kan taksa siam dan tur instruction zawng zawng awmna ‘lehkhabu’ a ni. Hetiang dinhmunah hian chromosome tlemte tak, thinlung leh thisen kalna kawng siam dan tur hrilhfiahna awmna chu a awm lo. Hei hian aorta a siam tha lo thin.

Vawi tam tak chu IAA vei naute hian genetic condition dang DiGeorge syndrome an nei bawk. Hei hi chromosome khata hmun khat bo vang a ni bawk. DiGeorge syndrome vei naupangte hian natna kai an nei fo thei a, an hmaiah pawh danglamna engemaw zat (cleft lip ang chi) an nei thei bawk.

Engtin nge doctor-te hian hei hi an hriat chian tak?

I naute damdawi ina i hruai hian doctor-te’n naute chu an enfiah a, hetiang thinlung natna hi an rinhlelh chuan, a finfiahna atana test ber chu echocardiogram a ni.

A châng chuan, naute chu nausen pum chhunga a la awm laiin anomaly scan (ultrasound scan) tih a nih laiin hetiang heart defect hi hriat theih a ni.

Hei hi eng enkawlna nge ni? Naute hi a dam thei ang em?

Ni e, a dik tak zet. Hei hi natna khirh tak ni mah se, operation hmangin a dam vek thei a ni . Enkawl dan hi hmunpui pahnih ah then theih a ni.

1. Surgery hmaa tih nghal tur

Diagnosis a nih hnuah naute chu neonatal intensive care unit (NICU)-ah dah nghal a ni. A tum ber chu naute chu operation atana a inpeih hma loh chuan taksaa thisen kal zel hi a ni.

Hetiang ti tur hian Doctor ten fing tak an hmang thin. Naute tin an pian hma hian aorta leh lung lama thisen phurtu artery inkarah hian hun eng emaw chen inzawmna (ductus arteriosus) a awm a. Hei hi a pian hnu darkar engemaw zat emaw, ni engemaw zat emaw chhungin a mah chauhin a khar thin.

Mahse IAA dinhmunah chuan doctor-te chuan he hun eng emaw chen inzawmna hi khar an phal dawn lo. Kawngpui lian khar laia ‘bypass’ hman ang mai a ni. He bypass hi hawn reng rawh.Damdawi pakhat Prostaglandin E1 tih chu saline-ah naute hnenah pek a ni. Hei hian naute taksa hnuai lam chu surgery neih hma loh chuan thisen engemaw zat a dawng thei a ni.

2. Nunna chhanhim thei surgery

Naute dinhmun a nghet tawh chuan pediatric cardiac surgeon-te chuan an zai thin.

• Thil pawimawh ber: Aorta hmun pahnih, a inthen leh inthen tawhte chu an inzawm leh a, chu chuan arch kimchang tak a siam ta a ni.
• Thil dang: Chutih rual chuan naute hian VSD (thinlung khur) a neih chuan he surgery neih chhung hian a khar bawk ang. A hmaa damdawi hmanga hawn tawh bypass (PDA) pawh khar a ni dawn a, a chhan chu tunah chuan main path zawh fel a nih tawh avangin a ngai tawh lo.

Hei hi surgery buaithlak tak a ni a, mahse Sri Lanka rama doctor thiam tak takte chuan hetiang surgery hi hlawhtling takin an ti thin.

Surgery hnuah naute hmalam hun chu eng ang nge ni ang?

Hei hi a pawimawh ber a ni. Surgery hlawhtling tak an neih hnuah naupang tam zawk chuan nun pangngai leh hrisel tak an hmang thei a ni . Statistics atanga a lan dan chuan operation an neih atanga kum 10 hnuah pawh mi 81% aia tam an la dam.

Mahse hriat reng tur pawimawh ber chu operation hnuah pawh i dam chhung zawng cardiologist follow-up hnuaiah i awm a ngai a ni . Hun ruat saah clinic-ah kal a ngai a, i thinlung a thawk tha em tih hriat nan echocardiogram ang chi test i neih a ngai bawk. A châng chuan, i tar hunah chuan enkawlna engemaw chen i mamawh leh mai thei. Chuvangin doctor thupek zawm a pawimawh.

I naute hian he natna hi a nei tih i hriat chuan i khawvel pum pui a lo tla thla tawh ang maia inhriat chu thil pangngai tak a ni. Mahse, tunlai hian medical science hi a hmasawn hle tih hre reng ang che. Natna hi a hmaa hriatchhuah a nih a, uluk taka enkawl a nih chuan i naute chu naupang dang ang bawka hlim theihna chance tha tak a nei a ni.