Mi thenkhat chuan mak tak maiin an kut zungtang an ben let thin tih i hmu tawh mai thei, a nih loh leh an khup chu hnunglam hla takah an ben a, chu chu hnunglam zawng zawngah an kal vek tih i hmu tawh mai thei. Mi thenkhat chuan hei hi ‘double-jointed’ an ti bawk. Dik tak chuan a tam zawkah chuan hei hi harsatna lian tak a ni lo. Mahse hetiang joint flexibility hi i neih ve bawk a, chubakah joint na leh hliam i neih fo chuan Joint Hypermobility Syndrome an tih condition i nei thei bawk. Hemi chungchang hi awlsam takin, i hriatthiam theih dan tur angin sawi ila.
A awlsam zawngin, Joint Hypermobility Syndrome hi eng nge ni?
Kan ruhte hi tissue layer thuk tak hmanga inzawmkhawm a ni. Heng ligament te hi kan ti a ni . Kan rubber band ang mai an ni a, chu chuan kan ruhkawrte chu a vawng tlat a, a hmunah a vawng tlat a ni. Joint Hypermobility Syndrome vei tan chuan heng ligament te hi a chak lo emaw, a lo chhuak emaw a ni. Rubber band hman atanga inzawm khawm ang mai an ni. Chuvangin an ruhte chu a tlangpui aia nasain a ben thei a ni. Hetiang flexibility lutuk hi natna nen a inzawm chuan he condition hi Joint Hypermobility Syndrome kan ti thin. Connective tissue disorder tiin a thliar hrang a ni .
‘Swelling’ leh ‘syndrome’ hi eng nge an danglamna?
Hei hi mi tam tak buaina hmun a ni. Joint hypermobility, a nih loh leh ruh ben lutuk theihna hi khawtlang nunah a hluar hle. I elbows, wrists, fingers, leh knees ang chi joint te chu an normal range aia tam i bend thei a nih chuan chu chu hypermobility an ti.
Mahse mi tam zawk tan chuan hei hian natna leh hriselna lama harsatna dang a thlen lo. Mahse mi ṭhenkhat tân chuan he insiamrem lutuk hian chhinchhiahna tam tak a thlen a, chu chu ruh natna, ruh leh ruh hliam fo, hahna, leh ril leh zun kawng lama harsatna te a ni Chu chu Joint Hypermobility Syndrome kan tih lai a ni. A awlsam zawngin, flexibility tam lutuk + symptoms = syndrome.
Hetiang dinhmun hi naupang leh puitling tleirawl zingah a tam ber. Hmeichhia leh Asian leh African-Caribbean hnam chhuak zingah pawh a tam deuh hlek bawk. Mahse thu lawmawm tak chu kum upat deuh deuh hian he natna hi a tlahniam duh hle.
Hei hi natna khirh tak dang chhinchhiahna a ni thei ang em?
Ni e, a châng chuan joint hypermobility hi a na zawk, genetic condition chhinchhiahna a ni thei bawk. Chungte chu Heritable Disorders of Connective Tissue (HDCT) an ti a. Joint Hypermobility Syndrome nena inzawm thei thil awm lo thenkhat chu hetiang hi a ni:
- Ehlers-Danlos Syndrome: Hei hi kan cartilage, ruh, thau leh thisen tichhe thei natna chi khat a ni. Kan connective tissue te, chakna leh inthlak danglamna pe thei te hian .Hetiang dinhmun hi protein collagen a chhiatna avanga lo awm a ni.
- Marfan Syndrome: Hei hi connective tissue tichhe thei natna a ni bawk. Kan connective tissue-a thil pawimawh tak, fibrillin leh elastic fiber siamtu gene a chhiatna avanga lo awm a ni.
- Down Syndrome: Hei hi genetic condition a ni a, kan thluak leh taksa thanlenna tichhe thei a ni. Down Syndrome vei te hi an piang a, extra chromosome an nei a.
Nang pawhin heng symptoms te hi i nei ve em? A lo en ve teh...
Joint Hypermobility Syndrome chhinchhiahna ber leh langsar ber chu ruh leh ruh natna a ni. Chu bâkah, heng thilte hi i nei ve em tih pawh en rawh:
- Joint leh ligament-a hliam tam tak: Entirnan, ke ruh tliak, khup hliam, leh ke ruh tliak te hi a awm fo thin.
- Joint leh muscle stiffness: Taksaah a nghet lo tih hriatna, zing thawh hmasak ber emaw, rei vak lo ding hnu emaw pawh nise.
- Chauhna: Chhan bik nei lovin chau reng reng.
- Taksaah balance tlakchhamna: I tlu reng ang maia inhriatna leh balance hloh reng reng ang maia inhriatna.
- Zun leh ek lama harsatna: Mi thenkhat chuan he natna nen hian pum na leh pum na an nei thei.
- Luak chhuak leh muhil: Luak chhuak leh lu hah lo, ding chhuak nghal ang maia luak chhuak leh luak chhuak ang maia inhriatna.
- Vun sei leh sei tak neih: Mi thenkhat vun hi a tlangpui aia inzawm lo zawk a ni thei.
Engvangin nge hetiang thil hi a lo thlen?
Hetiang dinhmun hi a chhan dik tak hi hriatchhuah a la ni lo. Mahse, thlah khat atanga thlah dangah a kal zel niin an ngai . Chumi awmzia chu i nu, i pa emaw, i chhungte hnai tak emaw chuan he natna hi a neih chuan nang pawhin i vei theihna a sang zawk tihna a ni.
Scientist-te chuan hei hi kan taksaa Collagen an tih protein siamtu genes inthlak danglam vang niin an ngai. Kan sawi tawh ang khan collagen hi kan ruh, kan ruh (ligament) leh kan ruh (tendon) te chakna leh inthlak danglam theihna petu a ni. Joint Hypermobility Syndrome vei te hian he collagen defect hi an nei a, chu chuan an ligament a tichak lo hle. Ligament a chak loh chuan ruhte chu a lo chhuak a, a ben tur aia nasain a ben tan thin.
Engtin nge hei hi i hmuh theih, Doctor?
Doctor i pan dawn chuan a tih hmasak ber tur chu i ruhkawr chhunga i range of motion enfiah nan taksa enfiahna a ni ang. Tin, a hmaa kan sawi tawh genetic condition dang enfiah nan thisen test pawh an ti thei bawk.
Chu bakah, i ruh (joint) te a inthlak danglam theih dan tehna atana hmanraw bik engemaw zat a awm bawk.
Beighton chuan goal a khung
Hei hi point 9 scale a ni. He test hian i flexibility a teh a ni. A hnuaia mite hi i tih theih chuan point khat theuh i dawng ang.
| Check tihna thiltih | Points hmuh a ni |
|---|---|
| I khup ben lovin hmalam pan a, i kutphah te leiah i dah thei em? | 1 point a hmu a ni |
| I elbow te chu i ben leh thei ang em? | Elbow pakhat tan point 1 (a vaiin 2) . |
| I khup hnunglam i ben thei em? | Khup khatah point 1 (2 total) . |
| I kutpui chu hnunglam hawiin i kut hmawr lamah i hnawih thei ang em? | Thumb pakhat tan point 1 (a vaiin 2) . |
| I kut zungtang te tak te chu degree 90 aia tam hnunglam i ben thei em? | Kut zungtang te tak te pakhat tan point 1 (a vaiin 2) . |
He test-ah hian score 4 emaw a aia tam emaw i score a , thla 3 tal ruh pali emaw a aia tam emaw i na a nih chuan , i doctor chuan Joint Hypermobility Syndrome i nei thei tih a ringhlel mai thei.
Zawhna panga awmna quiz
Tin, doctor chuan heng zawhna 5 te hi a zawt thei bawk ang che:
1. I khup ben lovin i kutphah te chu leiah i dah thei tawh em?
2. I kutpui chu i ben thei a, i kut hnuai lamah i hnawih thei tawh em?
3. Naupan lai khan i taksa chu mak tak maiin i ben a, i thiante i ti lawm em? A nih loh leh split i ti thei em?
4. Naupang emaw, puitling naupang emaw i nih lai khan i kekawrte emaw, i khup emaw vawi khat aia tam i dislocate em?
5. ‘Double-jointed’ ah i inngai em?
Heng zawhna pahnih emaw a aia tam emaw hi "yes" tih i chhan chuan Joint Hypermobility Syndrome i nei thei a ni.
Hei hi eng enkawlna nge ni?
Hetiang dinhmun hi damdawi a la awm lo. Mahse i natna lan chhuah dan chu i thunun thei a, nun pangngaiin i hmang thei bawk. Enkawlna tum ber chu i ruhte venhim leh i natna enkawl hi a ni.
I ruh chhehvela taksa ruhte tihchak hian an dawn thlawpna a tipung thei a, a humhim thei bawk. Ṭanpui tûra i tih theih ṭhenkhat chu hetiang hi a ni:
- Posture tha vawng reng rawh: Ding laiin i khup chu tlem han ben la. I khup chu an huam chin aia tam ben loh tur.
- Support tha tak nei pheikhawk bun rawh: Orthotics bik hmang la, a bik takin ke flat i neih chuan.
- Physical Therapist hmu rawh: Natna tihziaawmna tur, taksa ruh chakna tihpun nan leh dinhmun leh taksa inthlauhna tihchangtlun nan physical therapist tanpuina lak a pawimawh hle.
Natna atan chuan i doctor chuan over-the-counter pain reliever acetaminophen emaw ibuprofen emaw ang chi a rawn rawt thei ang. Mahse damdawi lam thurawn tel lo chuan mahni indam ngai suh. Natna a nasat chuan i doctor nen enkawl dan tur dik tak sawipui rawh.
Ei leh in hian hei hi a nghawng em?
Research atanga a lan dan chuan Joint Hypermobility Syndrome leh gastrointestinal disorders, a bik takin Irritable Bowel Syndrome (IBS) te hi inzawmna a awm thei a ni. Hetiang natna vei zingah hian IBS symptoms (abdominal na, bloating, constipation, or diarrhea) hi a awm fo thin.
Chuvangin i doctor chuan ei tur thenkhat chu rei lo te enchhin turin a ti mai thei che a ni. Hei hi exclusion diet an ti a . Hei hian ei leh in lama harsatna i neih leh neih loh a hriat theih nan a pui thei che a ni. Hetianga test thin food group hrang hrangte chu:
- Gluten-free diet: Buh leh barley ang chi thlai chi hrang hranga protein awm, gluten awmna ei tur ei loh tur.
- Lactose tel lo ei leh in: Lactose awmna ei tur ei loh tur, chu chu bawnghnute leh bawnghnute atanga siam sugar chi khat a ni.
- Low-FODMAP diet: Chaw thenkhata awm, awlsam taka hmin theih sugar (lactose, fructose, fructans, galactans, polyols) awmna ei tur khap.
A pawimawh ber chu hetianga ei leh in thlak danglam hma hian, .I doctor nen in inbia ngei tur a ni. A kaihhruaina hnuaia heng thilte hi tih hi a him ber.
Take-Home Thuchah a ni
- Hypermobility hi thil awm dan tlangpui a ni a, mahse natna leh hliam tam tak ang chi symptoms nen a awm chuan Joint Hypermobility Syndrome a ni thei.
- Damdawi awm lo mah se, a natna lan chhuah dan chu enkawl theih a ni. A pawimawh ber chu ruhkawr vel ruh (muscle) tihchak hi a ni.
- Heng symptoms te hi i neih chuan doctor pan ngei ngei tur a ni a, diagnosis leh treatment plan mumal tak i nei ang.
- Hetiang dinhmun hi genetic a nih avangin ven theih a ni lo a, mahse uluk taka enkawl a nih chuan ruhte hi venhim theih a ni.
- A tam zawkah chuan heng symptoms nasat dan hi kum upat dan azirin a tlahniam a, chuvangin lungngai suh.











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