I fa taksaah rawng mak tak mai i hmu a, i lungngai em? Chu hmun i khawih chuan i hrehawm deuh mai thei. Naupangte vun lama harsatna awm tlangpui niin i ngai mai thei a, mahse hei hi tlem a danglam deuh niin i ngai mai thei. Hetiang hunah hian hei hi hriat chian a pawimawh hle. Vawiin hian kan sawi dawn a, naupangte zingah a awm thin, mahse mi tam takin an la hre lo a, mahse hriat hlawh tak a ni.
Juvenile Localized Scleroderma chu eng nge ni?
A awlsam zawngin, hei hi autoimmune condition a ni a, naupang vun chu a tlangpuiin a thim a, a tight bawk. Chumi hming dang chu `(Morphea)` a ni.
‘Scleroderma’ tih thumal ngei pawh hi Greek tawng pahnih atanga siam a ni. "sclera" tih awmzia chu 'hard' tihna a ni a, "derma" tih awmzia chu 'vun' tihna a ni. Chuvangin a awmzia chu "hard skin" tih a ni. "Localized" tih hian specific a ni tihna a ni a, taksa hmun tlemte chauh a nghawng tihna a ni.
Awle, tunah chuan hetiang thil hi engtin nge a lo awm tih kan en ang. Kan taksaah hian natna laka min vengtu defence system kan nei vek a. Immune system kan ti a. Mahse hetiang dinhmunah hian naupang ngei pawhin a taksa hriselna (immune system) chuan a vun ngei chu a bei sual tan ta a ni . He attack chhanna atan hian vun chu a lo hring (inflammation) tan a ni. He a hring hian vun chhunga cell te hian protein collagen an tih chu a siam tam lutuk thin.
Hliam tuar hnua hliam lo awm ang maiin han ngaihtuah teh. Mahse hetah hian thil thleng chu vun hi hliam awm lovin hliam ang maiin a khauh a ni. Hei hi `(fibrosis)` kan ti a. Hei hi i fa taksaah hian hmun rawng danglam tak angin i hmu thei a ni.
He natna chi hrang hrang hi engte nge ni?
Hetiang natna hi chi hrang hrang a awm a, Localized Scleroderma. Type tin hian symptoms a inang lo deuh vek a.
| Natna chi hrang hrang | Hrilhfiahna |
|---|---|
| Circumscribed emaw Plaque Morphea emaw a ni thei | Hei hi a tam ber chi a ni. Plaque round emaw oval emaw ang chi pakhat emaw a aia tam emaw angin a lang. Hengte hian vun a nghawng ber a ni. A châng chuan vun hnuaia tissue pawh a nghawng tlem thei bawk. |
| Linear Morphea tih a ni | Hetiang chi ah hian spot te chu line ang deuhin a lang thin. Mi pakhatin ruler hmanga line a siam ang mai a ni. Chungte chu naupang kut leh ke bulah a lo lang thei a ni. Hei hi a hlauhawmna chu he nghetna hian a hnuaia ruh leh ruhte pawh a nghawng thei a, chu chuan chu ruhte chu ben leh tihdik a harsat phah a ni. Hei hian naupang thanlenna a nghawng thei bawk. |
| Morphea tlangpui a ni | Hemiah hian taksa peng hnih aia tam ah hian hliam lian pali aia tam a lo lang thin. A tlangpuiin trunk leh ke-ah an lang tam ber. Heng spot te hi an inzawm khawm thei a, an lian thei bawk. |
| Morphea thuk tak a ni | Hei hi a na ber leh a tlem ber chi a ni. Vun hnuai lam thuk tak, taksa ruh leh ruh te a nghawng a ni. Naupang pawhin hetiang chi natna hi a nei thei bawk. |
He natna lan chhuah dan engte nge ni?
Hetiang a nih chuan a natna lan chhuah dan hi hun kal zelah a inthlak zauh zauh thin. A tir lama i hmuh ang kha a ni lova, rei vak lo hnua i hmuh ang kha a ni. Heng spot te hi engtin nge an inthlak danglam tih hi han en ila.
- A bul tanna: A hmasa berin naupang vunah hian a sen hring (reddish-purple spot) a lo lang thin. Hetih lai hian vun hi a la nghet lo hle.
- Middle stage: Ni engemaw zat hnuah heng hmunte hi a khauh a, a hring deuh bawk. A hmun lai takah chuan waxy shine dum emaw sen emaw a la a. A chhehvelah hian pink emaw purple emaw halo a lang thei.
- Nakinah: Hun a kal zel a, he vun hi a reh ang a, chutiang hmuna vun chu a sen emaw, a var emaw pawh a ni thei a, a rawng a hloh thei bawk.
Natna khirh takah hmuh tur symptom dang
A nasat deuhah chuan he natna hian vun hnuaia tissue te pawh a nghawng a, chuvangin symptom dang pawh a lang thei bawk.
- Natna leh hrehawmna.
- Ke leh ruh leh taksa peng hrang hrangte incheina tlem.
- Hmaiah heng hruihrual te hi a lo lang a nih chuan ha emaw, mit lamah emaw harsatna a thlen thei a ni.
Heng hmunte hi enkawl a nih chuan a bo thei a, mahse a chang chuan a lo chhuak leh thei bawk.
Hetiang dinhmun a lo awm chhan hi eng nge ni?
Dik tak chuan he natna (Scleroderma) hi a chhan dik tak hi hmuhchhuah a la ni lo . Amaherawhchu, doctor-te chuan genetic leh environmental factors inkawp avanga lo awm niin an ngai.
Hei hian naupang thenkhat chuan hetiang immune system reaction hi an nei thei tihna a ni. Tichuan, boruak chhunga thil engemaw, natna hrik emaw, vun hliam emaw chuan chu natna chu a tichhuak thei a ni. Mahse hei hi natna hrik kai theih a ni lo .
Doctor, engtin nge hei hi i diagnose?
Doctor hnena i fa i hruai dawnin a tih hmasak ber tur chu naupang chu uluk taka enfiah a, a symptoms te zawt che a ni. Vawi tam tak chu vunah a hring hring awm dan atang hian natna hi hriat theih a ni.
Mahse, a natna hriat chian nan leh natna thukzia hriat chian nan a chang chuan test eng emaw zat tih a ni thei.
- Skin biopsy: Hei hi mole atanga vun te tak te tak tak lak a, microscope hmanga enfiah a ni. Hei hian vun cell-a inthlak danglamna awmte chiang takin a hmu thei a ni.
- MRI scan: Hei hi a nghetna hian vun a nghawng thukzia leh a hnuaia taksa ruh leh ruhte a nghawng em tih hriat nan hman a ni.
Hei hi eng enkawlna nge ni?
Enkawlna tum ber chu inflammation control te, natna darh zel tur tihtawp te, vun tightness tihziaawm te hi a ni. Nausen chi hrang hrangah natna chi hrang hrang a awm avangin, chu naupang tan pawh enkawl dan tur bik a ni.
| Enkawl dan tur | Hrilhfiahna |
|---|---|
| Corticosteroid hmanga tihdam theih a ni | Hengte hi damdawi chak tak tak an ni a, swelling control thei an ni. Vunah cream hnawih angin pek theih a ni a, pill ei tur angin pek theih a ni a, thisen zam chhunga injection angin pek theih a ni bawk. |
| Topical cream dangte pawh a awm bawk | (Calcipotriene, Tacrolimus) ang chi hriak hian chu hmunah chuan immune system hnathawh chu a control a, a tihtlem bawk. |
| Immunomodulating agents te pawh a awm bawk | Natna hi a na zawk a nih chuan immune system titawp thei damdawi (Methotrexate, Mycophenolate mofetil ang chi) pek thin a ni. |
| Light therapy (Thlalak hmanga enkawlna) . | Ultraviolet (UV) rays hmanga vun chhunga hmun dum awmte ti nem thei enkawlna a ni. Mahse, doctor chuan fimkhur takin a rawt a, a chhan chu vunah side effect a thlen thei a ni. |
| Taksa lam enkawlna | Hei hian taksa ruh tichak turin nasa takin a pui a, ruhkawr a thawk tha thei a, vun elasticity a ti sang bawk. |
He natna hi hmuhchhuah hmasak a, enkawl hmasak a nih chuan a rah a tha zawk hle tih hre reng ang che . Chuvangin i fa vunah danglamna eng emaw i hmuh chuan rei lovah Doctor pan rawh.
Nu leh pa angin engtin nge i fate i ṭanpui theih?
Naute vun venhim nan thil awlsam tlemte i tih theih a awm.
- Sahbawn leh detergent rimtui tak tak hman loh tur.
- Vun sensitive tan pawha tha, gentle moisturizer hmang fo ang che.
- Inbual dawnin tui lum aiah tui lum hmang zawk tur a ni.
- In lama boruak lum vawn reng nan humidifier hman hian vun vawt lo turin a pui thei a ni.
- Pawn chhuah dawnin ni laka inven nan sunscreen vuah ngei ngei tur a ni.
He dinhmun hian engtin nge naupang nun a nghawng?
He thu hi i hriat chuan i hlau mai thei a, mahse hlimna tak tak chu he natna vei naupangte hian nun pangngai, hlim tak an hmang thei tih hi a ni .
- Dam chhung: He natna hian engti kawng mahin naupang dam chhung a nghawng lo. Ngaihtuah buai suh.
- Nitin nun: Naupang tan sikul kal te, infiam te, infiamna te, a tih dan pangngai anga thil danga tel te tan daltu a awm lo. Dik tak chuan exercise hian taksa ruh a tichak a ni.
- Chaw: Ei leh in bik a ngai lo. Ei leh in inthlau tak, nutritious diet hi a tawk.
- Rilru hriselna: 1.1.A châng chuan, naupang pakhatin an vun pianhmang a inthlâk danglam avângin khawtlângah a nuam lo deuh emaw, a mualpho deuh emaw pawh a ni thei. Chutih hunah chuan anmahni hrethiam a, mahni inrintawkna pe a, hei hi an sualna a ni lo tih hrilhfiah a pawimawh hle.
Take-Home Thuchah a ni
- Juvenile Localized Scleroderma hi a awm lo hle a, mahse a na lo hle a, naupang vun a ti thim thei a ni.
- Hei hi kan taksa hriselna (immune system) a tha lo vang a ni. Hei hi natna hrik kai theih a ni lo.
- I vunah hmun dum, rawng danglam tawh i hmuh chuan, reilote lova doctor pan nghal a pawimawh hle.
- Hetiang dinhmun hi enkawlna tha tak nen uluk taka thunun theih a ni a, naupang dam chhung pawh a nghawng lo.
- Nu leh pate hmangaihna, \anpuina leh fuihna hi naupang tan he dinhmun nena hlawhtling taka nung thei tura chakna ropui tak a ni.
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