I toddler chu a limping tan nghal em? Nge a hip a na em? A châng chuan heng thil tenawm tak takte hi kan ngaihven vak lo mai thei. Mahse, heng symptoms te hi a la awm reng a nih chuan tlem tal ngaihtuah a pawimawh. A chhan chu hengte hi naupangte hip disorder hmuh tur awm lo tak Legg-Calve-Perthes disease tih chhinchhiahna a ni thei a ni. Chuvangin, vawiin hian he thu hi chipchiar zawkin sawi ila, kan sawi dawn em ni?
Legg-Calve-Perthes natna hi eng nge ni?
A awlsam zawngin sawi ila, hei hi naupang kum 2 leh 12 inkar hip joint tichhe thei dinhmun a ni a, kan hip joint hi thigh bone chunglam (`femoral head` kan tih) ball ang chi leh hip bone-a socket ang chi atanga siam a ni. Cup chhunga ball fit ang mai a ni. Chuvangin, Legg-Calve-Perthes natnaah hian thil thleng chu chu ball ang maia thigh bone hmuna thisen supply chu rei lo te chhung atan a tlahniam emaw, a tawp emaw a ni
Ngaihtuah teh, kan taksa peng tin hian dam khawchhuah nan thisen a mamawh a ni. Thisen atang hian oxygen leh nutrients kan hmu thin. Chuvangin, chutianga thisen kal chu a tawp chuan chu ruh tissue chu a thi tlem ta hle a ni. Hei hi damdawi lamah chuan `avascular necrosis` emaw `osteonecrosis` emaw an ti a. Mahse, hun eng emaw chen hnuah chuan thisen kal chu a intan leh ta a ni. Tichuan ruh peng chhia chu a insiamtha tan ta a ni. Mahse, a châng chuan ruh siam thar chu a hma ang bawkin a ṭhang lo thei a ni. Chu chu hetah hian buaina chu a ni.
He natna hi natna pawl pakhat `osteochondroses` an tih zinga mi a ni. Chung zingah chuan ruh pakhat tawp lo thang lian zel chu degeneration leh remodeling a awm a. A intan nghal a, a chhan hriat theih loh. He natna hi stage hrang hrangah a lo awm a, a kal zelna zawng zawng hi kum engemaw zat a daih thei. Hei hian i fa a nghawng dan chu ruh inthlak danglamna zau zawngah a innghat a ni. Amaherawhchu, uluk taka enkawl a nih chuan naupang tam zawk chuan damna tha tak an nei thei a ni.
He natna hi hming dang engemaw zatin an sawi bawk:
- Perthes natna a ni
- Perthes natna a ni
- Legg Calve a ni
- Legg-Perthes a ni
- Calve-Perthes-a chuan a rawn ti a
- Coxa plana (hip a zau) a ni.
Perthes natna hi engtiang chiahin nge a tlem? Tuin nge dawng tlangpui?
Khawvel pumah he natna hian naupang 12,000 zinga pakhat vel a vei a ni . Hmeichhia aiin mipa naupangin a let nga zetin an vei tam zawk.
Kum lamah chuan naupang kum 5 leh 7 inkar ah a tam ber a, amaherawhchu naupang kum 2 emaw kum 12 emaw velah a lo awm thei a ni.
Legg-Calve-Perthes natna hi a awm reng em?
Hei hi naupang femur lu degeneration leh rebuilding an ti a. Hetiang kalphung hi kum engemaw zat a awh a ni. Chuvangin, natna hi hun eng emaw chen atan a ni. Mahse, ruh pianzia chu a tidanglam reng thei a ni.
He natna hian nakin lawkah harsatna a thlen thei ang em?
Ni e, vanduaithlak takin a chang chuan a ti thei. Thigh bone ball chu a pianzia a dik lo lutuk a nih chuan hip joint socket-ah a in fit tha lo mai thei. Enkawlnain hei hi nasa takin a siam \ha thei a, mahse, he inmil lohna hi a awm reng chuan naupang a lo puitlin rualin hip joint-ah harsatna a thlen thei a, chu chu hun kal zelah arthritis ang chi a ni
Legg-Calve-Perthes natna lan chhuah dan chu engte nge ni?
He natna chhinchhiahna hi vawi khatah a lang vek lo. Zawi zawiin an lo thang lian a. A châng chuan, a tirah chuan eng thil nge thleng tih pawh i ngaihtuah thiam lo.
A tir lama hmuh theih symptoms: 1.1.
- Limping: Naupang chu a ke pakhat a hrual emaw, kal a harsat emaw angin a lang thei. Hei hi hip natna hmuna rit tihtlem nan tih a ni. Vawi tam tak chu limp hi natna chhinchhiahna hmasa ber a ni. Naupang chuan a ke ruh tliak chhan pawh a hre lo mai thei. Ngaihtuah teh, i fapa Sadeep-a chu a hma angin a tlan leh a inkhel tawh lo va, a kal laiin a ke pakhat a hrual ang maiin a lang. A tirah chuan a na tih pawh a sawi lo. Chutiang chuan a intan thei a ni.
- Hip pain: I fain natna a neih chuan a natna hi a tir lamah a nih a rinawm ber. Chutah chuan ruh a thisen supply a tlahniam a, ruh chu a chhe tan ta a ni. He natna hi exercise, tlan leh inkhelh hian a zual zel a ni.
- Referred pain: Naupang thenkhat chuan hip na ai chuan khup, kawr, pelvis, emaw pum chhungah na na an nei thei.
- Leg cramps: Hip joint nena inzawm ke ruh (leg muscles) ah hian tightening leh cramping pain a awm thei.
A hnua lo lang thei symptoms te:
- Trendelenburg gait: Hei hi hip joint-a harsatna a awm huna hmuh theih kal dan chiang tak a ni. Hip muscle chak lohna avang hian naupang a kal chuan a natna lam pelvis chu hnuai lam hawiin a inher a.
- Limited joint movement: Naupang hian hip a rotate a harsat thei. Pawn lam hawia khup leh khup chhung lam hawi theihna a tlahniam thei.
- Muscle atrophy: Naupang kawr leh a hnute ruh te hi a lian lo a, a hring angin a lang thei.
- Ke sei zawng inang lo: Ke pakhat chu a dang aiin a tawi zawkin a lang thei.
Eng thilin nge Legg-Calve-Perthes natna hi a thlen?
He natna hi femur lu (ischemia)-a thisen pek a tlahniam emaw, a tawp emaw avanga lo awm a ni tih kan sawi tawh a. Ruh pakhatin thisen a\angin oxygen leh nutrients a dawn avangin thisen a hloh chuan ruh tissue chu a thi tan a, a chhe ta a ni. Hei hi `avascular necrosis` emaw `osteonecrosis` emaw an ti a.
A tlangpuiin thisen kalna kawng a inkhar emaw, a tawi emaw chuan kawng hnih zinga pakhatah a thleng thei a ni. A chhung lam atangin a block thei a, artery natna vang emaw thisen zam vang emaw a ni thei a, pawn lam atanga block theih a ni bawk a, chu chu a hring vang a ni. Mahse, zirchiangtute chuan Legg-Calve-Perthes natnaah hian he thisen supply tlahniam chhan hi eng nge ni tih chiang takin an la hre lo. Naupang hrang hrangah chhan hrang hrang avangin a thleng thei.
Risk factors te pawh a awm thei
Research atanga a lan dan chuan naupang he natna vei zinga a chanve vel chuan thisen zam ( blood clotting disorder ) an nei tih a tarlang . Theory dang chu he natna hi traumatic injury emaw repetitive strain injury emaw avanga lo awm a ni thei a, chu chuan ruh lama thisen kal chu a tikhawlo thei a ni. Tin, case 10% vel chu inherited gene mutation nena inzawm niin an ngai bawk.
I fain Legg-Calve-Perthes natna a vei theihna tipung thei thil thenkhat chu hetiang hi a ni:
- Ruh a lo thang sawn tlai.
- Nau piang rit lo.
- A san zawng a tlahniam (kum nena khaikhin chuan).
- Ha lam thil danglam tak tak.
- Economic level hniam takah awm.
- Secondhand smoke nena inzawmna nei.
- Thisen zam (blood clotting disorder) a awm.
- HIV hrik kai.
- Infiamna emaw gymnastics emaw ang chi thila inhmang (hei hi sawisel a hlawh a, mi zawng zawng tan a ni lo).
- Gene `COL2A1` ah hian inherited mutations a awm a.
Pawimawh: Naupang zawng zawng hian heng risk factors te hi nei mahse he natna hi an vei vek dawn lo. Heng thil engmah awm lo pawhin a lo thanglian theih bawk. Hengte hi hriat chian a pawimawh a, natna lanchhuahna a awm chuan damdawi lam thurawn lak nghal a pawimawh.
He natna hian engtin nge ka fa chu a nghawng ang?
Active Legg-Calve-Perthes disease lai hian i fa hip joint-a femur lu chu degeneration (breakdown) a tawk a, chutah chuan remodeling (rebuilding) a tawk leh thin. He degeneration phase hi kum khat vel a ni thei . Remodeling leh formation phase hi kum hnih atanga kum nga vel a ni thei .
Naupang thenkhat chuan ruh tissue tihchhiat an nei tam zawk. Hei hi an thisen tlakchhamna (ischemia) a nasat zawk vang emaw, hun rei zawk a awm vang emaw pawh a ni thei. A nih loh leh, ruh chu a chak lo tawh a, a chungah rit lutuk dah a nih chuan a chhe zual thei bawk. Naupang thenkhatah chuan femur lu zungbun chu a tlakbuak a, a flatten bawk. Tichuan hip joint socket-ah a in fit tha lo.
Ruh chu a lo thang leh tan chuan a pianphung pangngaiah a lo thang leh thei a ni. Mahse, naupang ruh zawng zawng hi a lo thang leh vek lo. Thigh ruh thenkhat chu an size leh shape hmasa angin an kir leh ngai lo. Ṭhenkhat chu hip joint socket aia lian pawh a ni thei. I doctor chuan heng result te hi nghawng a tum ang a, a pangngai hnaih thei ang bera siam a tum ang.
Naupang thenkhat chu an hip chu cast-ah hun rei lote chhung immobilized tir a ngai mai thei. Mi dangte chuan zai an ngai mai thei. Heng enkawlnate hian ruh chu a lo thang tha leh \ha leh \hin. Naupang hip joint a dam tha lo chuan symptoms an nei chhunzawm zel thei. Hip dysplasia hian nakin lawkah arthritis ang chi harsatna a thlen thei a ni.
Engtin nge Legg-Calve-Perthes natna hi hmuhchhuah a nih?
Doctor in a tih hmasak ber chu i fate chu uluk taka taksa enfiah tir hi a ni . Tichuan, i fa ruhte en turin X-ray an la a. X-ray hmangin Perthes natna hi a awm leh awm loh, eng stage-ah nge a awm tih leh a nasat zia a hriat theih. A châng chuan, doctor chuan MRI (Magnetic Resonance Imaging) scan hmanga chipchiar zâwka en theih nân a rawt bawk thei bawk.
Legg-Calve-Perthes natna hi eng enkawlna nge ni?
Enkawlna chu natna nasat dan, a dinhmun leh naupang kum a zirin a innghat a ni. Naupang naupang zawkte chu an ruh a thang chak zawk avangin intervention tlem zawkin an dam tlangpui. Naupang kum upa zawkte chuan enkawlna tam zawk an mamawh mai thei. Doctor team pakhat chuan i fate tana tha tur enkawlna ruahmanna siam turin an thawk ho ang.
He enkawlna ruahmannaah hian:
- Hip natna chu chawlh hahdam leh rit phurh tihtlem: Naupang chuan rei vak lo kal chu a chawlhsan emaw, a tihtlem emaw a ngai thei a, a nih loh leh kekawrte ang chi support a hman a ngai thei bawk.
- Nonsteroidal anti-inflammatory drugs (NSAIDs): Hengte hi over-the-counter pain reliever leh anti-inflammatory damdawi (aspirin leh ibuprofen ang chi) te an ni. Hip joint-a natna leh hliam control-na atan an pui thei a ni.
- Physical therapy: Physical therapist chuan i fa chu a hip a normal leh theihna turin exercise bik a zirtir ang. I fa chu heng exercise te hi practice turin i puih a ngai mai thei bawk.
- Traction: Hei hian orthopedic traction device hmanga hip joint chu zawi zawiin a hmunah a hruai lut a ni. He enkawlna hi ni engemaw zat chhunga tih thin a ni.
- Plaster cast emaw brace emaw:Ruh chu a insiam thar lai hian i doctor chuan hip joint socket-a ruh chu a hmunah nghet taka dah theih nan cast emaw brace emaw hman a rawt thei ang. Hei hian ruh chu socket atanga a lo seilian chhuah rualin a pianzia dik takah a lo thang leh ang.
- Surgery: Naupang thenkhat chu ruh siam thar leh tur leh ruhkawr chhunga a hmuna siam that nan operation an mamawh mai thei. Hei hi osteotomy an ti a. Mi dangte chuan hip socket sei emaw, siam danglam emaw tûrin operation an mamawh thei a, chu chu arthroplasty an ti a ni.
Engtin nge Legg-Calve-Perthes natna hi tihdam theih?
I fa hian Legg-Calve-Perthes natna a vei a nih chuan kum engemaw zat chhunga awm thei tur damdawi lam zinkawng i hmachhawn ang a, a stage hrang hrang a awm ang. Hei hian naupang naupan lai hun chu eng emaw chen a nghawng dawn a ni – a then chu a tlem zawk ang a, a then chu a tam zawk ang. Mahse, heng zawng zawng hi a tawp hnu chuan naupang tam zawk chuan an thiltih pangngai chu engmah tihkhawtlai emaw, natna lan chhuahna kal zel emaw awm lovin an thawk chhunzawm thei ta a ni.
I fa kum 7 hnuai lam a nih chuan conservative treatment hmangin a dam kim theihna a sang zawk tih hre reng ang che. Kum 7 aia upa an nih chuan zai a ngai tam zawk. A hun taka enkawlna mumal an dawn loh chuan, hip ruh pawh a chhe reng a nih chuan an upat deuh deuh chuan hip osteoarthritis an nei thei a ni.
Perthes natna hi ven theih a ni em?
Vanduaithlak takin, ni lo. Tunah hian Perthes natna laka inven dan tur hriat a la awm lo.
Perthes natna chungchangah hian ka doctor hnenah eng nge ka zawh ang?
I fa hian Legg-Calve-Perthes natna a vei a nih chuan enkawlna chungchangah zawhna tam tak i nei ang a, a dam lehna atanga i beisei tur chu i nei ang. I doctor chuan theihtawp chhuahin i fa chungchang chipchiar takin a hrilhfiah ang.
Hetiang zawhna hi i zawt thei ang:
- "Doctor, tunah hian ka fa natna hi eng stage-ah nge a awm?"
- "He dinhmun hi engtiang chiahin nge a chhiat?"
- "Engtin nge naupang nunphung leh a game khelh dan hi kan thlak danglam ang?"
- "Eng thil nge he dinhmun hi nghawng thei nia i ngaih?"
- "Enkawl lai hian eng symptom emaw inthlak danglamna nge kan fimkhur tur?"
- "Hemi chungchang hi engtin nge ka fa chu ka zirtir ang, eng nge a beisei tur?"
Legg-Calve-Perthes hi natna hmuhchhuah nghal a nih avangin zawhna tam tak neih hi thil pangngai a ni. I doctor-in i fa dinhmun a hrilhfiah hnuah chuan i beisei tur chu i hre chiang hle ang. A dawt leh tur chu i fate chu an hriatthiam theih ang anga hrilhfiah hi a ni.
Hlimna chhan tam tak a awm. Naupang tam zawk chuan enkawlna an tan hnuah pawh harsatna an tawk tam lo. Anni hian tihkhawtlai engemaw zat an nei thei a, mahse a tlangpuiin hun rei lote chhung atan a ni. Orthopaedic therapy chi khat emaw an mamawh mai thei. Mahse a tawpah chuan an dam kim a rinawm hle.
Take-Home Thuchah a ni
Legg-Calve-Perthes natna chungchang i hriat chuan i hlau deuh mai thei. Amaherawhchu, a pawimawh ber chu a hmaa fimkhur hi a ni.
- A hmaa chhinchhiahnate chu hre rawh: I fa chu a ke a ke a chhe emaw, a hip a na tih a sawi emaw chuan ngaihthah mai mai suh la, damdawi lam thurawn zawng rawh.
- Enkawlna mumal tak a pawimawh: Doctor thupek dik tak zawm rawh. Enkawlna hian hun rei tak a daih thei a, a hrehawm pawh a ni thei a, mahse naupang hmalam hun atana a tul tak zet a ni.
- I fa chu \anpui rawh: Hemi hun chhung hian i fa hian i hmangaihna, i enkawlna leh i rilru chakna a mamawh a ni. An inkhelh theih loh te, an tlan theih loh te, an zuang thei lo te pawhin an lungngai hle mai thei. Hriatthiamna nei la, he hun chhung hian an tan awm reng rawh.
- Beiseina nei reng rawh: Naupang tam zawk chu he natna atang hian an dam chhuak vek a, nun pangngai an hmang thin. Chuvangin, positive taka awm reng a pawimawh.
Hemi chungchanga zawhna i neih belh chuan i doctor zawh zak suh. An lawm hle ang che.
👩🏽 ⚕️ Zawhna dang (FAQ)
💬 Legg-Calve-Perthes disease (LCPD) hi naupang tê tête ke ruh tliak thlentu natna a ni em?
Aih! Hei hi naupang kum 4 leh 10 inkar vela natna awm lo tak a ni a, ‘thighbone chunglam ball (Femoral head)’-a thisen kal chu a tawp nghal a ni. Thisen a bo chuan chu ball ruh (cartilage/bone) chu a ro/thi vek a, a round shape chu a flat ta a ni. (A chhan hi medical science pawhin a la hre lo).
💬 Ka fain Perthes natna a vei tih chhinchhiahna hmasa ber chu eng nge ni?
Nute hriat chhuah ber chu naupang chu hliam tuar lovin a ke pakhatah a ke pakhatah a tlu tan thin. Chu mai ni lovin, naupang chu a kekawr, a hip, groin, a nih loh leh a khup pawh a na mai thei (a bik takin tlan/inkhelh hnuah) tiin a tap thin.
💬 He hip ruh ro tak hi a lo thang leh ang (heal) ang tih hi a dik em?
Awle! Mak tak maiin a dik a ni! Thla/kum engemaw zat hnuah chuan ruh thi chu thisen a pe leh ang a, ‘ruh thar chu circle-ah a lo piang ang’ (Bone regeneration). Hemi chhung hian doctor-te chuan naupang chu kal/rit phurh an phal dawn lo va, naupang chungah wheelchair emaw brace (Braces, Cast) emaw dahin ball siam thar chu ‘grow in a circle’ turin an zirtir ang. (A na tak tak thenkhatah chauh operation neih a ngai).
` Legg-Calve-Perthes, Perthes natna, hip na, naupang natna, ruh natna, ke ruh, naupang hriselna











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