Cystic fibrosis damdawi ORKAMBI chungchang i zir dawn em ni? (Lumacaftor; Ivacaftor) te chuan an rawn ti a.

I doctor-in nangmah emaw, i hmangaih tak emaw chuan cystic fibrosis (CF) an vei tih a hrilh hian, damdawi an pek tur chungchangah zawhna tam tak i nei ngei ang. Thil buaithlak tak a nih avangin an damdawi pek tur chungchang hi hriat chian a pawimawh hle. Vawiin hian chutiang damdawi bik pakhat chungchang kan sawi dawn a ni. ORKAMBI an tih combination pill a ni a, damdawi pahnih Lumacaftor leh Ivacaftor tih te inzawmkhawm a ni.

Hei hi eng damdawi nge ni? Hei hian eng nge a tih tak tak?

A awlsam zawngin sawi ila, cystic fibrosis (CF) hi kan taksaa protein pakhat chhiatna avanga lo awm a ni. Hei hian kan lung leh taksa peng hrang hranga secretions, a bik takin mucus te chu a ti thim hle a, a sticky hle bawk. Ngaihtuah teh, normal takin kan lung chhunga mucus hi a luang deuh a, chuvang chuan awlsam takin a chhuak thin. Mahse CF vei mipa mucus hi a takah chuan a thim a, glue ang mai a ni. He mucus thick tak hi lungah a tang a, thawk harsatna a thlen a, khuh a thlen a, natna hrik a kai fo bawk.

Lumacaftor-a chuan; He damdawi Ivacaftor an tih hian chu protein dik lo ka sawi tawhah chuan kal a, eng emaw chen a siam that chuan hna a thawk a ni. Gate chhe tawh siam that ang mai a ni. He protein hian hna a thawk tha tan chuan taksa cell chhunga chi leh tui kal dan chu a inthlau hle. Tichuan chu mucus thick, sticky tak chu a lo hring deuh a, lung atang chuan lakchhuah a awlsam tan ta a ni. Hei hian CF symptom tam tak a control thei a ni.

Damdawi ei hmaa doctor hnena i hrilh tur thilte

He damdawi hi i ei tan hmain i hriselna chanchin kimchang i doctor hriattir hmasak phawt a pawimawh hle . A chhan chu he damdawi hman hian dinhmun thenkhatah hian fimkhur bik a ngai a ni. A hnuaia dinhmunte hi i neih chuan doctor hnenah hrilh ngei ang che.

He damdawi hi engtin nge i hman?

Hei hi a pawimawh ber a ni. He damdawi hi i hman dik loh chuan a result a tlahniam thei.

• Chaw thau tak nen ei rawh: Hei hi dan pawimawh ber a ni . He damdawi hi taksain a hip lut tha tur chuan chaw thau tak nen ei tur a ni. Entirnan, egg, butter, cheese, peanuts, avocado ang chi thil nen la rawh. Naupang te tak te hnena pek a nih chuan nu hnute tui, powdered milk emaw full-fat dairy products yogurt, cheese te nen i pe thei bawk.
• I doctor-in a tih ang chiah khan ei rawh: a dose dik tak, a hun takah ei rawh. I doctor-in chawlhsan tura a tih hma loh chuan hmang chhunzawm zel ang che.
• Grapefruit tui nen ei loh tur: He damdawi hi ei lai hian grapefruit emaw grapefruit tui emaw in loh tur.
• Naupang hnena pek a nih chuan: He damdawi hi naupang kum 6 chunglam tan pek theih a ni. Mahse, i doctor chuan hemi chungchangah hian thupek bik a pe ang che.

Damdawi ka ei tam lutuk chuan engtin nge ni ang?

Damdawi pek aia tam i ei nia i hriat chuan Colombo National Hospital-a National Poisons Information Center-ah call nghal la, a nih loh leh damdawi in hnai ber Emergency Department (ETU)-ah kal nghal rawh.

Dose pakhat ka theihnghilh a nih chuan engtin nge ni ang?

Dose i ei theihnghilh chuan i hriatreng veleh ei nghal rawh. Mahse, i dose leh tur thleng darkar 6 aia rei lo a nih chuan missed dose kha ei suh. Skip la, a hun ruatah dose dang ei leh rawh. Vawi khatah vawi hnih ei ngai suh.

He damdawi nena inzawm thei damdawi dang

Hei hi fimkhur hle tur a ni. ORKAMBI hian damdawi dang tam tak nen a inzawm thei a ni. Chumi awmzia chu damdawi dang nena ei hian ORKAMBI nghawng a tidanglam thei a, damdawi dang nghawng a tidanglam thei a, side effect na tak a thlen thei tihna a ni.

A hnuaia tarlan te hi he damdawi nena inzawm thei damdawi tlemte chauh a ni. He list hi a kim lo.

Damdawi ei huna ngaihtuah tur dang

• Damdawi lam enfiah fo: I doctor chuan clinic-a lo kal fo turin a hrilh ang che. A hun takah kal la, thisen test ang chi thil ti rawh. I symptoms te a reh loh chuan hrilh rawh.
• I mit en rawh: He damdawi hian mitdelna (cataract) a thlen theihna chance tlem a nei a, a bik takin naupangte tan chuan mitdelna (cataract) a thlen thei a ni. Chuvangin damdawi ei lai hian mit lam doctor hnenah a hun takah i mit enfiah tir tur a ni. I mit hmuh danah danglamna i hmuh chuan doctor hnenah hrilh nghal rawh.
• Birth control-ah fimkhur rawh: Hei hi hormonal birth control pill i hman chuan a pawimawh hle. ORKAMBI hian an thawh that loh phah mai thei. Chuvangin, naupai venna dang, condom emaw diaphragm emaw hman chungchangah i doctor nen inbiakna neihpui ngei ang che.

Damdawi avanga side effect lo awm thei te

Damdawi dang ang bawkin he damdawi hian mi thenkhatah side effect a nei thei a ni. Ṭhenkhat chu serious an ni a, ṭhenkhat chu mild an ni.

Engtin nge damdawi chu i dahkhawm leh i paih thin?

• Storage: Tablet te hi naupang leh ran vulh te hmuh theih lohna hmunah dah tur a ni . Room temperature (20-25 degree Celsius inkar) ah dah tur a ni. Damdawi expired hman loh tur.
• Hman dan: Damdawi hman hun tawp tawh emaw, mamawh tawh lo emaw paih dan tha ber chu pill te chu a bawm atanga lakchhuah a, coffee ground hman tawh, lei emaw, ui bawlhhlawh ang chi thil nen chawhpawlh a, bag khar nghet takah dah a, bawlhhlawh bawmah paih hi a ni. I doctor-in a tih loh chuan toilet-ah damdawi chu paih suh.