I ke veilam chu a hring deuh a, a dang aiin a rit zawk em? A chang chuan a na mai mai a, a tingling ang maiin a awm em? Mi tam takin heng symptoms te hi an ngaihven vak lo. Mahse a chang chuan hei hi a chhan chu i ngaihtuah aiin a pawi deuh thei bawk. Chutiang chhan pakhat chu he natna ‘May-Thurner Syndrome’ an tih hi a ni thei. Eng nge a nih hi awlsam takin han thlir ila.
A awlsam zawngin May-Thurner Syndrome hi eng nge ni?
A awlsam hle mai. Kan taksaah hian thisen kalna kawng chi hnih a awm a. Thinlung atanga taksa peng dang thlenga oxygenated thisen phurtu vein te hi ‘Arteries’ kan ti thin. Chutiang bawkin thisen hman tawh, oxygen nei tawh, thinlunga phur kir lehtu vein te chu ‘Veins’ kan ti thin.
Hetiang dinhmun Turner syndrome an tih ah hian i ke dinglam (right iliac artery)-a thisen phurtu main artery chu i ke veilam (left iliac vein) atanga i thinlunga thisen phur kir lehtu main vein chungah a kal a, a compress a ni. Tui pipe-a ke pen ang maiin han ngaihtuah teh. Tichuan tui luang chu a titawp ta a ni lawm ni? Chutiang bawkin, chu thisen kalna kawng chuan thisen kalna chu a compress chuan ke veilam atanga thisen kal chu a titawp a ni. Hetiang dinhmun hi `(Cockett syndrome)` an ti bawk.
He dinhmun hian engtin nge taksa a nghawng?
Ke veilam atanga a chung lam panna thisen kal a tihkhawtlai chuan ke veilam ah thisen thenkhat a inzawm khawm emaw, a ding reng emaw a ni. Hemi chungchanga hlauhawm ber chu hetiang hmun khatah thisen a inkhawm hian chu vein chhungah chuan thisen zam a lo awm theihna chance a sang hle a ni. Damdawi lam hawi chuan hei hi ‘deep vein thrombosis’ (DVT) kan ti a ni.
DVT hi natna khirh tak a ni a, a lo awm nghal thei a ni. He thisen zam hi a lo chhuak a, lung chhunga vein pakhatah a tlakbuak chuan nunna atana hlauhawm tak a ni thei.
A tlangpuiin heng ang symptoms hi DVT a lo awm hian a lo awm thei a ni.
| DVT natna lan chhuah dan | |
|---|---|
| A hring leh a rit | A hring leh a rit tih hriatna, a tam zawk chu ke pakhatah (he thu-ah hian ke veilam). |
| Na | Ke na na tak emaw, throbbing sensation emaw, a bik takin groin area-ah. |
| Vun rawng a danglam | Ke vun rawng sen emaw sen emaw a inthlak danglam. |
| Vein atanga chhuak | Ke ruh (veins) te chu a hring a, a chung lamah a rawn lang tan thin. |
Tin, hmeichhe thenkhat chuan May-Turner syndrome nen hian pelvic congestion syndrome an tih natna an nei thei a, hei hi pum hnuai lam vein-a harsatna awm chuan natna rei tak a thlen thin a ni.
He dinhmun hi tuin nge hmu tam ber?
May-Turner syndrome hi hmeichhiaah a tam deuh hlek a, puitling kum 20 leh 50 inkarah pawh a awm ve bawk .
Mahse mak tak mai chu mi panga zinga pakhat vel hian he natna hi ``iliac vein compression an tih hi an nei a ni.`` Mahse mi zawng zawng hian symptom an nei vek lo. Mi tam tak chuan May-Turner syndrome an nei tih hi DVT an neih hnuah chauh an hrechhuak thin. Chumi hma chuan symptom nei lo an ni mai thei.
Engtin nge May-Turner syndrome hi hriat theih?
I doctor hnenah i natna lan chhuah dan i hrilh hnuah a enfiah ang che a, i natna hriat chian nan i thisen kalna kawng enfiahna test bik thenkhat tih a rawt thei bawk ang.
| Test chi hrang hrang | A awlsam zawngin sawifiah a ni |
|---|---|
| Ultrasound hmanga scan `(Ultrasound)` hmanga tih a ni | Natna nei lo test, sound wave hmanga taksa chhunga thisen kalna kawngte enna. Hei hi DVT enfiahna hmasa ber a ni. |
| CT scan hmanga tih a ni | X-ray machine bik hmanga thisen kalna kawng chipchiar taka thlalak lak. |
| MRI Scan (MRI) hmanga tih a ni. | Magnet leh radio wave hmanga thisen kalna kawng thlalak chiang tak tak hmuh. |
| Venogram hmanga enfiah a ni | Vein pakhatah tui bik (contrast dye) inject a ni a, X-ray hmangin thisen kal dan enfiah a ni. Hei hian vein blockage awmna hmun dik tak chu a hriat theih nan a pui thei a ni. |
| Intravascular Ultrasound hmanga tih a ni | Camera te tak te tak nei tube (catheter) chu thisen kalna kawngkhar chhungah dahin a chhung lam atanga enfiahna hmanraw dik tak a ni. |
Hei hi eng enkawlna nge ni?
May-Turner syndrome enkawlna tum ber chu constricted vein chu a pangngaia siam leh a, thisen kal dan tihchangtlun a, DVT vei theihna tihziaawm a ni.
Symptoms chauh a awm chuan
A tlangpuiin DVT nei lo leh ke na leh natna ang chi symptoms chauh nei tan chuan doctor chuan a hnuaia enkawlna te hi a rawt thei ang:
- Angioplasty leh stenting: Hei hian balloon tipped tube te tak te tak te chu vein chhungah dahin, a zim laiah balloon chu inflating a ni. Hei hian vein a hawng a, thisen a luang chhuak thei bawk. Chumi hnuah chuan vein chhungah mesh ang chi cylindrical device stent an tih chu dah a ni a, chu chu a zim leh tawh loh nan a ni.
- Surgery: A then phei chuan thisen kalna kawng (artery) tawi tawh chu vein atanga hla zawka sawn chhuah nan surgery tih theih a ni. A nih loh leh, bypass surgery hmanga thisen kalna tur kawng thar siam theih a ni bawk.
DVT hmanga zui a nih chuan
May-Turner syndrome avanga DVT i neih chuan a chunga kan sawi tak enkawlna bakah hian a hnuaia mite hi i tih a ngai bawk ang:
- Anticoagulants: Heng damdawi te hi thisen zam a lo awm loh nan leh thisen zam awmsa a lian loh nan pek thin a ni.
- Clot-dissolving medication: A chang chuan, damdawi chu catheter hmangin thisen zam chhungah direct-in an inject a, chu chu a dissolve a, a paih chhuak thin.
- Vena cava filter: Kan taksa chhunga thisen zam (inferior vena cava)-ah hian filter an tih hmanrua hi hun eng emaw chen emaw, a awm reng emaw dah a ni lo va, kea thisen zam chu a chhuak lo va, lungah a kal lo.
Harsatna hlauhawm ber chu: Pulmonary Embolism
May-Turner syndrome hlauhawm ber chu DVT lo awm hi a ni. Chu aia hlauhawm zawk chu chu DVT phek khat chu a inthen a, thisen nen a kal a, chutah chuan thisen kalna kawng khatah a inkhung ta a ni. Hei hi `Pulmonary Embolism` kan ti a ni.
Hei hi medical emergency pawi tak, nunna atana hlauhawm tak a ni! Nangmah emaw, i hriat miin emaw a hnuaia symptoms te hi a lo lang nghal a nih chuan damdawi in Emergency Department (ETU) -ah hruai nghal rawh.
- Thâwk harsa nghal (dyspnea) .
- Thâwk lak laiin rilru natna nasa tak a pung
- Thisen chhuah leh mucus
- Lung natna (palpitations) .
Risk tihtlem nan thil kan tih theihte
May-Turner syndrome hi ven dan tur chiang tak a awm lo a, a chhan dik tak hriat a la ni lo. Mahse, a hnuaia thilte hian i thisen kal dan a ti tha thei a, thisen zam i neih theihna a ti tlem thei bawk:
- Hun rei tak chu dinhmun inangah awm suh. A bik takin sedentary job i neih chuan tho la, darkar khatah vawi khat tal kal kual rawh.
- Tui tam tak in thin ang che.
- Exercise neih fo thin la, a bik takin aerobic exercise la.
- Natna dang, zunthlum emaw, hypertension emaw i neih chuan doctor thupek angin uluk takin control la.
- Meizial i zuk chuan chawlhsan nghal rawh.
- I doctor-in a rawt chuan special compression stockings ha la.
May-Turner syndrome chungchanga zawhna i neih belh chuan doctor zawt hreh suh. Engkim a hrilhfiah ang che.
Take-Home Thuchah a ni
- May-Turner syndrome hi ke dinglama thisen phurtu thisen kalna kawng leh ke veilam atanga thisen phurtu thisen kalna kawng (vein) te chu a compress a ni.
- Hei hian ke veilam a thisen kal chu a tikhawlo thei a, ke ruh na leh na ang chi symptoms a thlen thei a ni.
- He natna avanga harsatna lian ber leh hlauhawm ber chu deep vein thrombosis (DVT) lo awm hi a ni.
- Pulmonary embolism (DVT atanga clot chhuak a, lung chhunga awm) hi nunna atana hlauhawm emergency a ni.
- I ke veilam hi sawifiah theih loh khawpin a hring emaw, a na emaw, a rit emaw i neih chuan doctor lam pan a pawimawh hle.
- Hei hi enkawlna hmanga hlawhtling taka enkawl theih dinhmun a ni.











💬 Comments (0)
Comment a la awm lo. Hetah hian i comment hi a vawikhatna atan add rawh.
I comment kha add rawh