I fate mitmeng kha ngun takin i en ngai em? A chang chuan mit chhunga êng luhna hmun thianghlim, zungbun (cornea) chu a lian lutuk deuh tih kan hmu thei. A nih loh leh doctor-in ``Megalocornea'' tih thumal a hrilh che khan i buai deuh pawh a ni thei. ``Megalocornea'' hi eng nge ni tak tak? Ngaihtuah buai suh, i hriatthiam theih tur awlsam takin kan sawi dawn a ni.
`(Megalocornea)` hi eng nge ni tak tak?
A awlsam zawngin, `(Megalocornea)` chu mit hma lama transparent membrane, cornea kan tih hmun chu a tlangpui aia lian a nih chuan a ni. Ngaihtuah teh, kan mit hi camera ang a nih chuan he cornea hi chu camera lens hma lama venhimna glass ang a ni. Hemi hmang hian mit chhungah êng a lut thin. `(Megalocornea)` ah chuan he mit (cornea) diameter (chu chu a sir lehlamah a hlat zawng) hi millimeter 13 aia tam a ni. A tlangpuiin naupang te tak teah chuan hetiang size hi a te zawk hle.
Chutianga thil thleng dang chu mitmeng leh mit rawng (iris kan tih), anterior chamber tia koh inkar, tuiin a khat hmun chu a tlangpui aia thuk zawk a ni.
A pawimawh ber chu `(Megalocornea)` hi `(congenital)` condition a ni . Chumi awmzia chu naute chu heng features te nen hian a piang tihna a ni. A tam zawkah chuan Doctor-te hian kum naupan lai atang tawhin an hre chiang thin. Mi tam zawk chuan hei vang hian mit lama harsatna lian tham an nei lo va, hun kal zelah a na zual zel `(progressive)` condition a ni lo. Chumi awmzia chu a tam zawk chu a nihna ang chiah a ni tihna a ni. Hei hi `(Microcornea)` tih dinhmun nen a inkalhin a ni. `(Microcornea)` ah chuan mitmeng hi a pangngai lo takin a te a.
Mahse a chang chuan he `(Megalocornea)` dinhmun hi natna dang nen pawh a inzawm thei. Entirnan, `(Marfan syndrome)` ang chi connective tissue natna nen hmuh tur a awm. Chutiang a nih chuan i fa chu mit natna dang, mitdel ang chi a vei thei a ni. Chuvangin `(Megalocornea)` dinhmun hi hriat hmasak a pawimawh hle. Tichuan doctor-te chuan naupang mit leh mit hmuh dan chu ngun takin an en thei ang.
Doctor-te chuan he natna hi hming dang engemaw zat an hmang a:
- Hma lam megalophthalmos a awm
- Congenital hmalam megalophthalmia a awm thin
- A pianpui megalocornea chu a hranpaa awm
- Macrocornea tih a ni
Engtin nge Megalocornea hian mit a nghawng?
A tam zawkah chuan ``Megalocornea'' natna hian mit pahnih a nghawng thin. A bik takin kawng hnih in:
1. Mit (cornea) diameter (a sir lehlamah teh) chu a pangngai aia lian (13 millimeter aia tam) a ni.
2. Mit hma lam, tui thianghlim, tui ang maia luang chhuak (anterior chamber) chu a tlangpui aia thuk zawk a ni.
Heng inthlak danglamna te hian pawn lam atanga mit chu tlem a lian deuhin a lantir a ni.
Hetiang dinhmun hian tute nge a nghawng nasa ber?
Megalocornea hi mipa naupangah hmuh tam ber a ni . Hei hi a chhan chu megalocornea vei zinga 90% aia tam chu X chromosome-a genetic mutation vang a ni. Heng X-linked condition te hian hmeichhia aiin mipa naupang a nghawng nasa zawk.
Hei hi a awm lo hle a ni . Researcher-te chuan mi engzat nge piang chhuak tih chiang takin an sawi thei lo a, mahse underdiagnosed a nih a rinawm thu an sawi.
`(Megalocornea)` chi hrang hrangte chu engte nge ni?
`(Megalocornea)` hi chi hnih a awm a:
1. Isolated or simple megalocornea : Hei hian mit lam chauh a nghawng a, natna dang nen a inzawm lo.
2. Anterior megalophthalmos : Hetiang chi hi a hnuaia awm (underlying condition) nen a inzawm a, chuvangin naupang mit hmun dang emaw, taksa peng dang emaw a nghawng thei a ni.
Eng thilin nge Megalocornea hi a thlen?
Megalocornea hi CHRDL1 gene-a genetic mutation avanga lo awm a ni a, hei hian mit thanna control nan a pui a ni. Zirchiangtute chuan he mutation hian mit chhunga awm optic cup , chu a tlangpui aia lianin a ti lian niin an ngai. Hei hi mit (cornea) lian tham chhan ber a ni.
`(Megalocornea)` natna lanchhuahna chu engte nge ni?
Thu lawmawm tak chu Megalocornea vei piang tam zawk hian symptom an nei lo . Nun pangngaiin an khawsa thei a ni.
Mahse naupang thenkhat chuan hetiang symptom hi an nei thei a ni:
- Astigmatism vangin mit a danglam zauh zauh emaw, mit a fiah lo emaw. (Astigmatism hi mit chhunga mit (cornea) chu a zungbun (performat spherical) a nih loh avangin mit chhunga hmun khatah êng a focus lo tihna a ni.)
- Sensitivity to bright light (photophobia) - Chumi awmzia chu ni eng emaw, eng eng emaw kan hmuh chuan mit a sen vek tihna a ni.
- Hmuh rei lo tak (myopia).
Mahse, natna dang ``Megalocornea'' hi natna dang nena inzawm a nih chuan naupang chuan natna lan chhuahna na zawk a nei thei a, chungte chu:
- Mit (cataract) a awm.
- Coloboma (mit hmun thenkhat a lo thang tha lo).
- Lens hring (ectopia lentis) emaw phacondonesis emaw a awm thei.
- Glaucoma (mit pressure sang vanga mit chhiatna).
- Mit lens vel ring (ciliary body band) chu a tlangpui aia lian a ni.
- Mit hmuhna a hniam.
- Retinal atanga chhuak (retinal detachment) a awm.
Pawimawh: I fain heng symptoms te hi a neih chuan mit doctor pan nghal rawh. Hriat hmasak chu enkawl a awlsam zawk.
Engtin nge `(Megalocornea)` hi kan hriat theih ang?
Doctor te chuan megalocornea hi naupan lai atanga an hmuhchhuah tlangpui thin . Mit lam doctor-te chuan mit enfiahna hmangin an nemnghet a, a tul chuan genetic test hmangin an nemnghet bawk.
Hei hi dik taka hriat a pawimawh hle a, natna khirh tak dang, glaucoma ang chi te nen pawh a danglam thei a, enkawlna dik tak kaihhruaina atan pawh a pawimawh hle.
I doctor chuan test dang a ti thei bawk a, chungte chu:
- Glaucoma test neih a ni.
- Gonioscopy (mit hmalam chamber angle enfiahna).
- Optical coherence tomography (OCT) (mit layer hrang hrangte thlalak lakna).
- Tonometry (mit pressure tehna) hmanga siam a ni.
- Ultrasound hmanga enfiah a ni.
- Mit chhunga tui awm zat tehna tur vitreous index chhut.
`(Megalocornea)` tihdamna a awm em?
Vanduaithlak takin Megalocornea hi damdawi a awm lo . Mahse, lungngai suh! Enkawlna hian i fate mit hmuhna a humhim thei a, a hnuaia dinhmun dangte pawh a enkawl thei a, harsatna awm thei tur pawh a veng thei bawk. I fate mamawh enkawlna dik tak i hmuh theihna tur kawng tha ber chu a hmaa hriatchhuah hi a ni.
I doctor chuan naupang mit lam doctor hnenah a refer thei che a ni. I fa hian natna dang a neih chuan specialist dang i pan a ngai mai thei.
`(Megalocornea)` enkawl dan tur chu engte nge ni?
A tam zawkah chuan megalocornea hian enkawlna bik a mamawh lo , a bik takin i fate mit hmuh dan a pangngai a, mit chhunga pressure a normal a nih chuan. I fa doctor chuan "watchful waiting" tih dan tur a rawt mai thei. Hei hian i fa mit hriselna enfiah fo a, a danglamna eng pawh enfiah reng tihna a ni.
Mahse, i fain symptoms emaw, a hnuaia thil dang emaw a neih chuan, chu chu enkawl turin enkawlna a mamawh mai thei. Surgery ni lo enkawlnaah chuan:
- Damdawi, entirnan mittui tlakna.
- Visual aids (eyeglasses emaw a bik taka siam contact lens emaw).
Thil engemaw takah chuan operation neih a ngai mai thei:
- Mitdel surgery emaw glaucoma enkawlna atana surgery emaw tih a ni.
- Photorefractive keratectomy (PRK) hi mit surgery a ni a, mit hmuhna hnai emaw, astigmatism emaw enkawl a ni.
Ka fa hian `(Megalocornea)` a vei a nih chuan eng nge ka beisei ang?
Naupang megalocornea vei tam zawk hi chu mit hmuhna tha tak neiin an seilian a . Mi dangte chuan an natna lan chhuah dan chu mit hmuhna hmanrua emaw, siamthatna lens emaw hmangin an enkawl thei bawk.
Mahse, he natna vei naupangte hmalam hun chu an natna awm dan leh a nasat danah a innghat a ni. If you feel that your symptoms are getting worse , i fa mit leh hriselna humhimna tur kawng tha ber berte chu i doctor nen sawiho rawh.
Ka fate Megalocornea vei theihna hi ka tihtlem thei ang em?
Dik tak chuan Megalocornea venna tur hian engmah tih theih a awm lo. Hei hi genetic condition a ni. Amaherawhchu, i fa mit venghim turin hma i la thei a ni.
Nangmah emaw i fain emaw a hnuaia thilte hi i tih hunah mit venna mitmeng vuah hmangin mitmeng chhiatna i veng thei ang:
- Bleach emaw chemical dang hmanga tihfai hunah.
- Pawn lama hnathawh lai, lawn sawh te.
- Electric hmanrua hman te, hammer emaw, paint hnawih emaw hmanga siamthat hna thawh laiin.
- Baseball emaw hockey emaw ang chi infiamnaah te.
I fain contact lens a bun a nih chuan mit emaw mit emaw a natna a veng loh nan a tihfai leh hrik paih dan tur thupek chu uluk takin zawm rawh. Don’t miss your eye doctor’s appointments , leh enkawlna kaihhruaina zawm la, harsatna awm lo tur leh i fate mit hmuhna humhim turin.
Engtikah nge he natna `(Megalocornea)` hi damdawi lam thurawn i lak ang?
Megalocornea hi a hmaa hriatchhuah a pawimawh a, chu chu enkawlna tha tak a ni. I fain mit a ti na lo, a na a, a mit a danglam a nih chuan i doctor rawn nghal rawh.
I doctor chuan i fate hahdamna tur leh mit hmuhna humhim turin enkawlna kawng \ha tak tak a pe thei ang.
Follow-up care hi a hnuaia awmte enkawl nan leh mitdel emaw glaucoma ang chi harsatna awm thei tur venna atan a pawimawh hle.
Megalocornea hi thil awm lo tak a ni a, mitmeng (cornea) a ti lian thin. Mahse chanchin lawmawm tak chu mi tam zawkin symptom an nei lo. Mi dangte chuan corrective lens hmangin an mit an humhim thei a, harsatna an veng thei bawk. Mit enfiah fo hian i fa chuan khawvel hi chiang takin a hmu thei a, nun chu a hlim thei hle!
I hriat tur thil (Take-Home Message) .
Okay, chuti a nih chuan tunah chuan kan sawi thin (Megalocornea) kha i hrethiam tawh hle. Hriat reng tur pawimawh thenkhat chu hetiang hi a ni:
- Megalocornea hi pianpui natna hmuh tur awm lo tak a ni a, mitmeng (cornea) chu a tlangpui aia lian a ni.
- Hei hian tlangvalte a nghawng nasa zawk fo thin.
- Hemi avang hian naupang tam zawk chuan mit lama harsatna lian tham an nei lo va, hun kal zelah a na zual lo.
- Mahse, a chang chuan damdawi lam thil dang nen pawh a inzawm thei bawk. Chuvangin natna hi hriat hmasak a pawimawh hle a, damdawi lam thurawn angin mit enfiah reng a pawimawh hle.
- Enkawlna hi a lan chhuah dan emaw, harsatna dang emaw a awm chauhvin enkawl a ngai a ni.
- Ngaihtuah buai suh, damdawi lam enkawlna mumal hnuaiah naupang chu mit hmuhna tha tak neiin nun pangngaiin a nung thei a ni.
Hemi chungchanga zawhna i la neih chuan i chhungkaw doctor emaw mit lam doctor emaw zawt hreh suh.
` Megalocornea, Corneal enlargement, Naupang mit natna, Congenital mit natna, Mit hmalam membrane, Mit test, CHRDL1 gene











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