I mit chhungah thil tenawm tak tak a lo chhuak thei a, harsatna a thlen thei tih i ngaihtuah ngai em? Dik tak chuan kan mit chhunga pigment particle te hi a chang chuan a lo chhuak thei a, mit chhunga tui awmte kalna tur kawng a tikhawlo thei bawk. Chutiang a nih chuan mit chhunga pressure a sang a, chu chuan natna hlauhawm tak, glaucoma , a thlen thei a ni. Vawiin hian chutiang dinhmun pakhat, Pigment Dispersion Syndrome (PDS) leh chuta lo awm thei Pigmentary Glaucoma (PG) chungchang kan sawi dawn a ni.
Pigment dispersion syndrome (PDS) leh pigmentary glaucoma (PG) te hi eng nge ni?
A awlsam zawngin, hengte hi natna inang vei pahnih an ni. Pigment Dispersion Syndrome (PDS) chu i mit rawng pe thei i iris -a pigment awm chu a te tea a inthen a, i mit chhunga tuiah a lo inhnim tan a ni. Thing hlui atanga paint chhuak ang maiin han ngaihtuah teh.
He PDS natna hi rei tak, kum tam tak emaw, kum sawm tam tak emaw pawh ni se, pigmentary glaucoma (PG) tih natnaah a lo chang thei a ni. PDS nei zawng zawng hian PG an nei vek dawn lo . Mahse, PDS i neih rei poh leh PG vei theihna a sang zawk.
Engtin nge pigment dispersion syndrome (PDS) hian glaucoma a thlen?
Hei hi hrethiam tur chuan mit chhunga thil thleng hi tlem kan hriat hmasak a ngai a ni. I mit iris hi zungbun ang maia zau, zungbun ang maia lian a ni a, chutah chuan melanin , an tih pigment a awm a, chu chuan i mit chu a rawng a pe a ni. He iris hian a hma leh a hnung lamah hmun hnih a nei a. Heng hmunte hi aqueous humor an tih tuiin a khat a ni . He tui pressure hian mit chu a zungbun (spherical) a ti reng a ni.
PDS i neih chuan i iris hian a pianzia a vawng tha thei tawh lo va, a hnunglam atanga hla lutukin a ben thei tawh bawk. Chumi hnuah chuan iris hnunglam chuan mit lens pianzia controltu muscle fibers te chu a rawn hrual a. I iris a zau a, a inzawm khawm (i.e., iris chu êng awm theihna turin a inzawm a, a inzawm khawm) chuan iris chhunga pigment granules te chu a lo chhuak ta a ni.
A dik tak chuan heng pigment te hi an peel off a, chu chu a rawng chuan thingphel a peel ang bawkin.
Loose pigment particles te hi aqueous humor ah an float a, mit hmun dangah an phur lut thin. He aqueous humor hi mit atanga a chhuah theih nan drainage system a awm a. Trabecular meshwork an ti a . He trabecular meshwork -ah hian loose pigment particle te hi a pungkhawm thei a, a tichhia thei bawk. Chutiang a nih chuan aqueous humorMit atang hian tui a chhuak tha thei lo. Hei hian mit chhunga pressure a tipung a ni. Hei hi ocular hypertension an ti a . Chutianga a kal zel chuan a tâwpah chuan glaucoma . Glaucoma hi enkawl a nih loh chuan tihdanglam theih loh, mitdelna nasa tak leh mitdelna thlengin a thlen thei a ni.
PDS leh PG hi eng symptoms nge ni?
A tam zawkah chuan PDS hian symptoms a nei lo. Chuvangin mi tam tak chuan he natna hi an nei tih pawh an hre lo. Mahse, a lan chhuahna a awm a nih chuan, glaucoma natna lan chhuah dân tlangpui nên a inang tlangpui . Chung zingah chuan:
- Mit na a na
- Mit a sen vek
- Eng laka hriatna ( photophobia ) .
- Light chhehvel halo emaw glare emaw hmuh
Mi thenkhat chuan hun eng emaw chen chu mit pressure a sang thei a, mit a fiah lo thei a, light chhehvelah halo a awm thei a, chu chu exercise neih lai ang chi hi a ni. Mahse hengte hi rei vak lo hnuah a bo ang.
PDS awm chhante chu engte nge ni?
Mithiamte chuan PDS thlentu hi eng nge ni tih chiang takin an la hre lo a, mahse a thlentu tur thil engemaw zat an hmuchhuak a ni.
- Genetics: Research chuan DNA mutation thenkhat leh PDS/PG te hi inzawmna a nei tih hmuhchhuah a ni. Hei vang hian PDS leh PG hi chhungkuain a kal thei a ni. Mahse, engtin nge a lo than chhoh zel dawn tih erawh sawi lawk a har hle.
- Kum: PDS hi kum 20 leh 50 inkar ah hmuhchhuah a ni tlangpui.
- Sex: PDS leh PG condition hian mipa a nghawng nasa zawk.
- Hnam: Mihring dum emaw Asian emaw hnam chhuakte hian PDS leh PG vei an nei tlem zawk. Mihring varte hi an hlauhawm zawk.
- Nearsightedness (Myopia): Myopia , chu chu hla tak tak hmu thei lo tihna nei te hian PDS leh PG vei an hlauhawm zawk. Hmun hnai zawka i awm poh leh PDS i vei theihna a sang zawk a, a nih loh leh PG ah a chang thei bawk.
- Mit structure: I anterior chamber a thuk chuan PDS leh PG i vei theihna a sang zawk. Hei hi a chhan chu chamber a thuk chuan a chhungah tui tam zawk a awm khawm thei a ni. Hei hian iris chu hnunglam hawiin, lens lam hawiin a "bend" thei a ni. Tin, mit (cornea) flattened pawh hi a puitu a ni thei bawk.
- Activity level tam lutuk: Exercise tam lutuk emaw taksa tihchak lutuk lehResearch atanga a lan dan chuan PDS/PG te hi inzawmna a awm a ni. PDS emaw PG emaw i neih chuan i mit doctor chuan i taksa tihchak dan a zawt mai thei. I activity level hian he condition hi a nghawng a nih chuan tihtlem turin an fuih mai thei che.
Secondary Pigment Dispersion tih hi eng nge ni?
I iris-a pigment a hloh theihna chhan dang pawh a awm bawk. Hei hi "secondary PDS" an ti a. Hei hi "primary PDS" nen a danglam hle. Primary PDS chu PDS hi a hnuaia damdawi lam dinhmun dang awm lovin a lo awm hian a ni. Mahse, secondary PDS-ah pawh PG hi a awm thei bawk.
Secondary PDS thlen thei thil thenkhat chu:
- Mit tan hlauhawmna
- Mit chhunga tumor (growths) lo awm thin
- Mit chhunga lens (IOL ) atanga inthlak danglamna .
PDS leh PG hi engtin nge kan hriat theih ang?
PDS natna lan chhuah hmaa hriat theih dan tha ber chu mit enfiah dan pangngai neih hi a ni . PDS emaw PG emaw avanga mit endik laiin mit chhunga inthlak danglamna hmuh tur thenkhat chu:
- Krukenberg spindle: Hei hi line te tak te, dinglam hawia i iris -a rawng inang ang maia lang a ni a, i mitmeng hmaah a lang thei. Mit chhunga pressure a san chuan fluid hmalam pan a nih chuan a lo awm a, chu chuan loose pigment granules chu cornea chhungah a innghat a ni.
- Radial iris defects: Hei hi iris-a pigment line te tak te lo lang thin a ni. Bicycle ke spoke ang mai an ni. Mit lama mithiam chuan hengte hi lighting technique bik hmangin a hmu thei a ni.
- Iris pawn lam kil hnaihah pigmentation: I mit specialist chuan gonioscopy tih test hmangin chutah chuan pigmented granules awm chu a hmu thei ang.
I mit specialist-in a hman theih test te
PDS leh PG hriat theihna tur glaucoma test engemaw zat a awm a . Chung zinga ṭhenkhat chu mit enfiahna pangngai (routine eye exam) neih laiin tih a ni. Midang erawh chu a specialized deuh deuh bawk. I mit specialist chuan PDS leh PG diagnose emaw rule out emaw atana pui thei tur test eng nge tha ber tih a hrilh ang che .
Heng test-ah hian a tlangpuiin a hnuaia mi pakhat emaw, a aia tam emaw a tel thei:
- Slit lamp exam a ni
- Tonometry ( mit chakna tehna) .
- Optical coherence tomography (OCT) hmanga enfiah a ni.
- Pachymetry (mit leh mit thik zawng tehna) .
- Gonioscopy (mit atanga drainage angle enfiah) 1.1.
- Visual field testing ( peripheral vision testing) tih a ni.
PDS leh PG hi engtin nge enkawl an nih?
PDS leh PG enkawlna hi glaucoma chi dang enkawlna nen a inang hle a ni . Heng enkawlnaah hian a hnuaia mi pakhat emaw, a aia tam emaw pawh a tel thei a ni:
- Damdawi: Glaucoma damdawi hian kawng hrang hrangin mit chhunga pressure tihziaawmna hmangin hna a thawk a. Damdawi thenkhat chuan i mit chu a tizau a , aqueous humor drainage a tipung bawk . Mi dangte chuan aqueous humor siam chhuah tihtlem hmangin hna an thawk a ni . Hengte hi mittui tlakna atan a tam ber.
- Glaucoma surgery: Hetiang tih dan hian tui luang chhuak leh tui chhuah dan tihchangtlun tum a ni tlangpui. Entirnan , trabeculectomy , goniotomy, leh laser hmanga surgery thenkhat te hi a ni.
Vawi tam tak chu PDS leh PG vei te hian result tha ber an hmuh theih nan combination approach an hman a ngai thin. Entirnan, laser surgery leh damdawi nena inzawm. Damdawi chauh hian mit chhunga pressure a tihhniam tawk loh chuan he method hi a hlawk hle.
I mit specialist hi enkawlna kawng hrang hrang chungchang hriattirna pe theitu tha ber a ni. Ani chuan enkawlnate hian engtin nge a nghawng ang che tih te, i duhthlan turte leh eng side effect nge i beisei theih tih te a hrilh ang che.
Hetiang dinhmun hi ka neih chuan eng nge ka beisei ang?
PDS nei zawng zawng hian PG an nei vek dawn lo . Mahse, hun kal zelah a hlauhawmna a sang chho zel a ni. PDS vei zinga 10% velin kum 10 chhungin PG an nei ang. Kum 15 hnuah chuan chu chu 15%-ah a pung ta a ni. Nun chhungin he hlauhawmna hi 35% leh 50% inkar a ni.
PDS leh PG hi glaucoma chi dang aiin kum hmasa zawkah a intan tlangpui avangin, he natna hi a theih ang anga enkawl a pawimawh hle . Chumi zinga ṭhenkhat chu mit doctor pan chhunzawm zel leh follow-up neih chhunzawm zel hi a ni.
Heng appointment te hi thla thum atanga thla ruk danah emaw, kum khatah vawi khat emaw a ni thei a, chu chu i dinhmun a zirin a ni. Heng test te hian i doctor chu mit pressure sang zawng zawng a hriat theih nan a pui thei a, a chhiat loh nan emaw, a tlem berah chuan a na zual loh nan emaw enkawlna tur a rawt thei bawk.
Nangmah ta a niPDS emaw PG emaw enkawl leh enkawl chhunzawm zel hi i mit hmuhna humhalhna kawng pawimawh tak a ni. Permanent blindness hi an specialist thurawn zawmtu, check-up neih fo thin leh an dinhmun enkawltu zingah hian a tlem hle.
PDS emaw PG emaw hi ven theih a ni em?
Vanduaithlak takin PDS leh PG venna atan engmah tih theih a awm lo. Beisei loh takin an thleng a, mi tam tak chuan heng natna hi an nei tih pawh an hre lo va, mit enfiah dan pangngaia specialist-in heng inthlak danglamna hi a hriat hma loh chuan, a nih loh leh symptoms a lo lan hma loh chuan.
PDS emaw PG emaw ka neih chuan engtin nge ka in enkawl ang?
PDS emaw PG emaw i neih chuan i mit hmuhna humhalh nan leh harsatna lian tak tak, mitdelna te laka invenna tur thil engemaw zat a awm a:
- A rawtna angin doctor hmu rawh. Checkup scheduled te pawh lo thlir ve suh.
- I damdawi ei tur chu a tih angin ei rawh. Damdawi hi a tih angin, a hun ruatah leh a zat tur angin hmang thin ang che.
- I mit specialist-in a rawt chuan i nunphung thlak danglam rawh. Entirnan, exercise tam lutuk tih tlem.
- I mit hmuh dan a danglam tih i hriat a, symptom thar i neih chuan emaw, i damdawi chungchanga zawhna i neih chuan i doctor ko nghal rawh.
Engtikah nge Emergency Treatment Unit (ETU) ah ka kal ang ?
Mit symptom thenkhat i neih chuan damdawi lam pan vat a ngai a ni. Enkawl loh chuan mit tihchhiat leh theih loh a awm thei. I natna hriat chhuah hnuah, i dinhmun bik a zirin eng natna lan chhuah dan nge i ngaihven ber tur tih leh heng chhinchhiahna zinga pakhat tal i neih chuan eng nge i tih tur tih te chu i mit lam doctor nen sawiho rawh.
Emergency medical attention mamawhna symptoms te chu:
- Mit a inthlak danglam a, chu chu mit a fiah nghal emaw, mit a tlahniam emaw a ni
- Halo thar emaw, a chhe zual emaw, light chhehvela glare emaw
- Mit na tak, na tak leh/ emaw lu na tak tak
- Mit hmuhna hloh nghal (a then emaw, a kim emaw) .
Doctor hnenah eng zawhna nge ka zawh ang?
I mit specialist i zawh theih tur zawhna thenkhat:
- Ka PDS dinhmun hi engtiang chiahin nge a nasat/a hmasawn? PG ah a chang tawh em ?
- Eng enkawlna tur nge i rawt?
- Enkawlna atang hian eng side effect nge ka beisei ang? Chutiang side effects te chu enkawl emaw, tihtlem emaw turin eng nge ka tih theih ang?
- Ka tih dân pangngai emaw, ka thiltih dân pangngaiah emaw inthlâk danglamna ka neih a ngai em?
A tawp berah chuan thil hriat reng tur (Take-Home Message) .
Pigment Dispersion Syndrome (PDS) emaw Pigmentary Glaucoma (PG) emaw i nei a ni.Glaucoma i vei tih hriat hian a tithinur deuh thei a, a bik takin kum naupan lai atanga i vei chuan. Glaucoma chi tam zawk hi nakin lawkah an lo awm laiin , PDS leh PG te hi a hma zawk hle. Hêng dinhmunte hian glaucoma chi dangte ang bawka hna an thawh laiin, danglamna pawimawh tak tak a awm a ni. Mahse a pawimawh ber chu damdawi lam enkawlna mumal leh enkawl dan dik tak a awm chuan PDS leh PG te hi enkawl theih a ni a, mitdel emaw mitdel emaw ang chi harsatna lian tak tak pawh a tlem emaw, a veng thei emaw a ni. Chuvangin, hlauthawng suh la, i doctor thurawn zawm rawh.
` Glaucoma, Pigment Dispersion Syndrome, Pigmentary Glaucoma, Mit hriselna, Mit Pressure, Mit hmuhna, Mit Natna











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