I naute a pian hunah, doctor-in a enfiah hunah, beng pakhat chu a dang aiin a te zawk tih a hriat chuan, a nih loh leh a siam kim lo tih a hriat chuan i mangang a, i hlauthawng thei bawk. Hei hi a hluar hle. Damdawi lamah chuan he natna hi Microtia kan ti a. He hming i hriat hian hlauthawng suh. Hei hi nu leh pa tam takin an hmachhawn thin a ni. Fiah tak leh awlsam takin sawi ila.
Microtia chu eng nge ni?
A awlsam zawngin sawi ila, microtia hi kan beng pawn lam (kan hmuh thin earlobe)-a pianpui ( congenital developmental abnormality) a ni. Nausen pum chhunga a la awm laiin beng a lo thang tha lo tihna a ni.
He hming hi Latin tawng pahnih atanga lak a ni. ‘Micro’ tih awmzia chu ‘tlem’ tihna a ni a, ‘otia’ tih awmzia chu ‘beng’ tihna a ni. Hei hian ‘beng te tak te’ tihna a ni .
Hetiang dinhmun hi thil danglam deuh atanga beng awm lohna tluantling thlengin a awm thei. A châng chuan beng pawn lam chauh ni lovin, beng kawng pawh a bo thei bawk. Chutiang a nih chuan naute hian hriatna lama harsatna a nei thei a, khawi atanga ri lo chhuak nge tih hriat a harsat phah thei bawk.
A tam zawkah chuan he natna hian beng pakhat chauh a nghawng a, mahse a tlem berah chuan, beng pahnih a nghawng thei. Naupai thla thum khatna chhunga beng hmasawnna lama harsatna awm vang a ni fo.
Microchia hi engtin nge an classified?
Doctor-te chuan he natna hi a nasat dan a zirin chi paliah an ṭhen a. He classification hian i naute hian eng ang dinhmun nge a neih tih hriatthiamna a pe ang che.
| Pawl | Hrilhfiahna |
|---|---|
| Type 1 a ni | Pawn lam beng hi a tlangpui aiin a te deuh a, mahse beng peng zawng zawng deuhthaw chu a lang vek. Deformities tenau te chauh a awm. |
| Type 2 a ni | Beng pawn lam a\anga a \hen chauh a lo piang \hin. A te hle bawk. Ear canal chu a zim emaw, a block emaw pawh a ni thei. |
| Type 3 a ni | Hei hi a tam ber chi a ni. Tissue hmun te tak te, mumal lo tak chauh hmuh tur a awm a, beng ang chi a nei lo. Ear canal leh eardrum a awm lo vek thei. |
| Type 4 a ni | Beng pawn lam awm lohna tluantling. Hei hi anotia an ti a. Hei hi thil awm lo tak a ni. |
Hetiang dinhmun hi engtiang chiahin nge a awm?
Khawvel pum huap data-a a lan dan chuan he natna hian nau piang nung 10,000 zinga 1 leh 5 inkar a nghawng a ni. Hmeichhia aiin mipaah a tam zawk. Tin, beng veilam aiin beng dinglam a nghawng nasa zawk bawk.
Microtia natna lan chhuah dan chu engte nge ni?
Chumi chhinchhiahna ber leh awmchhun chu naute beng lo lang hi a ni. Natna dang angin natna leh hrehawmna dang a thlen lo. A lan chhuah dan ber chu:
- Beng hi a pianzia danglam tak a ni.
- Beng pangngai aia te zawk.
- Pawn lam beng (Anotia) awm lohna tluantling.
A pawimawh ber chu a kaihhnawih hriatna hloh , beng hmel eng pawh ni se, enfiah a ni.
Microtia vei naute hian a hre tha thei em?
Hei hi nu leh pa tan harsatna lian ber a ni. Naupang microtia vei chuan a beng natnaah hian eng emaw chen chu hriatna a hloh thei a ni. Hei hi beng lairil emaw, beng kawngkhar emaw hmasawnna lama harsatna a awm chuan a dik hle.
Mahse a tha ber chu a tam zawkah chuan beng chhung lam hi a pangngaiin a lo thang lian thei vek a ni. Kan beng hi sound system angin han ngaihtuah teh. Pawn lam beng leh beng kawng chu microphone ang mai a ni. Beng chhung lam chu amplifier leh speaker ang mai a ni. Microtia-ah chuan he microphone hi a nghawng fo thin. Chuvangin, sound lut tur a tibuai thei a, mahse a chhung lam a thawk tha a nih chuan sound luh theihna tur kawng a awm.
Chuvangin i naute hian microtia a nei a nih chuan hriatna test neih a pawimawh hle. Hriatna lama harsatna tlem te pawh hi enkawl loh chuan naupang thusawi hmasawnna a nghawng thei a ni.
Eng thilin nge microtia hi a thlen?
A tam zawkah chuan microtia awm chhan chiang tak hmuh a harsa thin. Chumi awmzia chu nu leh pa sual vang a ni lo tihna a ni. Naupai thla thum hmasa berah beng a lo thang lian zel laiin random occurrence a ni.
Mahse, a then phei chuan hei hi nghawng thei thil engemaw zat hmuhchhuah a ni a:
- Genetic causes: A chang chuan hei hi thlahtute atanga lo chhuak a ni thei a, mahse a tlem hle.
- Syndrome dang: A châng chuan microsomia hi syndrome lian zawk chhinchhiahna pakhat chauh a ni thei a, chu chu hemifacial microsomia ang chi hi a ni a, chu chu hmai sir khata lo ṭhang ṭhat lohna a ni.
- Naupai laiin nghawng a nei: Naupai lai damdawi thenkhat ei emaw, nu zunthlum vei emaw ang chi thilte pawhin nghawng tlemte a nei thei tih ngaihdan a awm. Mahse, hengte hi zirchianna stage-ah an la awm a ni.
Engtin nge hei hi kan hriat theih ang?
Hei hi hriat chian nan hian test bik neih a ngai lo. Hei hi naute pian veleh doctor in a hmu nghal thei a ni. Hetiang dinhmun hi beng hmel enin hriat theih a ni.
Mahse, beng chhung leh beng lai tak insiam dan hriat nân, i doctor chuan CT scan neih a rawt thei ang . Hei hian beng chhunga dinhmun chiang zawk a pe thei a ni.
Microtia enkawl dan tur chu engte nge ni?
Hetah hian thil pahnih kan ngaihtuah a ngai a, pakhat chu beng lan dan a ni a, pakhat chu hriatna a ni.
Beng hmel enkawl leh enkawl loh chu nu leh pa leh naupang mimal duhdan a ni. Mahse , hriatna lama harsatna a awm chuan enkawl a pawimawh hle.
Enkawlna kawng hnih a awm ber.
1. Ear Prosthetics hman tur
Hengte hi silicone hmanga siam beng siam (artificial ears) a ni a, beng dang nen a inang hle. Lu-ah hian special adhesives emaw magnet emaw hmangin an bun theih bawk. Surgery an mamawh loh avangin duhthlan tur tha tak an ni. Mahse, enkawl a ngai a, hun kal zelah thlak a ngai a, naupang thenkhat tan chuan a tangkai lo thei bawk.
2. Surgical hmanga beng siam thar lehna
Hei hi a chinfelna nghet ber a ni. Surgery hmanga beng thar siam a ngai a ni. Doctor-te chuan naupang kum 6 leh 9 inkar tan he surgery hi an rawt tlangpui a, hei hi a chhan chu chu kum a lo thlen chuan naupang taksa chu a lo thang tha tawh a, surgery atana mamawh cartilage pawh a lo thang tha tawk tawh a ni.
He surgery hi tih dan tlangpui pahnih a awm a, chungte chu:
- Naupang ruh atanga cartilage hmanga beng siam:Hetah hian surgeon chuan naupang ruh atanga cartilage te tak te a la a, beng angin a siam a, vun hnuaiah a dah a ni. Hei hi naupang taksa peng a nih avangin taksain a hnar lovang. Mahse, hei hi surgery complex tak a ni a, stage engemaw zatah tih a ni.
- Synthetic Material hman dan: Hetah hian beng implant, synthetic material bik hmanga siam hman a ni. Hei hi naupang tissue ngeiin a khuh a ni.
Eng ang operation pawh ni se, plastic surgeon leh beng, hnar leh kawr (ENT) surgeon te nen uluk taka sawiho hnuah thutlukna siam tur a ni.
Harsatna awm thei leh thlirna
Microtia natna thlentu ber chu hriatna hloh hi a ni. Uluk taka enkawl a nih chuan naupang tawng leh tawng thiamnaah harsatna a awm lovang.
Chu bâkah, naupang chu a lo upa deuh a, a ṭhiante nêna an inhnial chuan, a beng lan dân chuan rilru lama harsatna engemaw zât, mualphona, a nih loh leh mahni inngaihsakna hniam tak a nei thei a ni Nu leh pa i nih angin, hetiang hunah hian i fate chu rilru lama chakna tha tak i pek a ngai a ni. A tul chuan counselling service-a refer a pawimawh hle bawk.
Microtia vei naupang tam tak chu a danglamna chu hrisel, active leh normal takin an nung tih hre reng ang che.
I fa doctor hnena zawh tur zawhna
I fa hian hetiang dinhmun hi a nei a nih chuan heng zawhnate hi doctor hnenah zawh leh sawifiah a pawimawh hle.
- Doctor, ka naute dinhmun hi engtiang chiahin nge a pawi? Hei hi eng chi nge a nih?
- Harsatna dang kan hriat tur chhinchhiahnate chu engte nge ni?
- Ka fa tan eng enkawlna nge tha ber?
- Kan naute hriatna enfiah turin tute nge kan hmuh ang?
Chûng zawhnate chhânna chuan i tih tûr chu a hrethiam zâwk ang che.
Take-Home Thuchah a ni
- Microtia hi beng pawn lam pianpui (congenital deformity) a ni. I sualna a ni lo.
- I tih hmasak ber leh pawimawh ber chu a rang thei ang bera naute hriatna test tir hi a ni.
- Hriatna hloh enkawl hi naupang tawng leh tawng thanlenna atan a pawimawh hle.
- Beng hmel siamthat nan surgical option a awm bawk. Hei hi naupang chu a lo upa deuh tawh chuan specialist te nen sawiho theih a ni.
- Damdawi lam enkawlna dik leh nu leh pate hmangaihna leh puihna a awm chuan microtia vei naupang chuan nun hrisel tak, hlim tak a nei thei a ni.











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