Naute ruhro hi pianpui harsatna a ni em? Myelomeningocele chungchang hi han sawi ila!

Aw, i pum chhunga i fa te tak te ngaihtuah chu a va ropui tak em! Mahse a chang chuan, kan fate hi he khawvelah hian beisei loh hriselna lama harsatna neiin an lo kal thin. Vawiin hian naute chu nausen pum chhunga a la awm laiin ruhro, a nih loh leh ruhro (spinal cord) lo pian chhuah laia lo piangsual (complex birth defect) chungchang kan sawi dawn a ni. Hei hi myelomeningocele an ti a. ``Open Spina Bifida'' tih pawh i hre tawh mai thei. Hei hi a takah chuan naute ruhro, a nih loh leh ruhro (spinal canal) a khar tha lo tihna a ni.

Myelomeningocele hi eng nge ni tak tak?

A awlsam zawngin, myelomeningocele hi piansualna a ni a, i naute ruhro leh ruhro (spinal canal) chu a pian hmain, nausen pum chhungah a khar kim lo. Hei hi neural tube defect (NTD) chi khat a ni. He hming hi lam harsa i ti mai thei, a dik em? ‘My-e-lo-men-in-go-ceil’ angin a lam chhuak thin.

Myelomeningocele hi naupai atanga kar li chhungin a awm thin. Hei hi naute neural tube a khar tha lo a, chu chuan naute ruh hnunglam atanga tuiin a khat sac a rawn chhuah tir thin a ni . A bik takin, sac-ah hian:

• An ruhro (spinal cord) hmun thenkhat
• Meninges - an ruhro khuh tu tissue te
• Nerves a awm
• Cerebrospinal fluid (CSF) hi thluak leh ruhroa awm, tui pawimawh tak a ni.

Myelomeningocele hi naute ruhro hmun apiangah a awm thei a, mahse a hnungzang hnuai lam (lumbar leh sacral areas) , chu chu a kawrfual (waist area)-ah hmuh a ni tam ber .

Lungchhiatthlak tak chu spinal cord leh sac chhunga nerve te a chhiat vang a ni. Hei hian a tlangpuiin sac hnuaia taksa peng hrang hrangah chak lohna emaw hriatna hloh emaw a thlen thin . A then phei chuan sac chu a chhe thei bawk. Hei hi naute pum chhunga a chet dan pangngai vang a ni thei a, a pian tirh lamah pawh a thleng thei bawk.

Myelomeningocele hi spina bifida natna khirh ber a ni a, rualbanlo nasat lutuk a thlen thei bawk. Entirnan, taksa ruh chak lohna, bladder emaw bowel control theih lohna, leh/ emaw paralysis . Mahse, naute ruh hnuai lama nei te hian ruhro sang zawka he natna nei naute aiin symptom an nei tlem zawk tlangpui.

Neural tube defect tih hi eng nge ni?

Neural Tube Defects (NTDs) hi nau piangsual (congenital conditions) thluak, ruhro emaw, ruhro emaw a ni. Naupai thla hmasa chhungin an thleng fo thin – a chang chuan naupai i hriat hma pawhin an awm thin. Neural tube defect chi hnih lian ber chu spina bifida leh anencephaly te an ni.

Hei hi a tlangpuiin a thleng thin: Naupai thla hmasa berah hian nausen ruhro kil hnih chu a inzawm khawm a, ruhro, ruhro, ruhro (spinal nerve) leh meninges (spinal cord khuh tu tissue) te tan venhimna khuhna a siam a ni. Hetih lai hian nausen thluak lo thang lian leh ruhro (spinal cord) chu neural tube an ti a.

Chuvangin, he neural tube siamnaah hian tihsual emaw, harsatna emaw a awm chuan neural tube defect an ti a ni.

Spina Bifida leh Myelomeningocele hi eng nge an danglamna?

`Spina Bifida` tih hian piansualna eng pawh a kawk a, chutah chuan ruhro vel a neural tube chu a khar kim lo.

Spina Bifida hi naute ruhro khawi hmunah pawh a awm thei a, a hmaa kan sawi tawh ang khan, utero-ah neural tube a khar kim lo a nih chuan. Chutiang a nih chuan ruhro (spinal cord) vengtu ruh (spinal cord) chu a khar tha lo hle. Hei hian naute ruhro leh nerve a tichhia thei a ni.

Myelomeningocele hi spina bifida chi khat a ni a – a na ber bawk. Naute hnungzang atanga chhuak, tuiin a khat bawm a ni a, chutah chuan ruhro leh nerve thenkhat a awm a ni. Spina bifida chi dangte chu meningocele leh spina bifida occulta te an ni.

Meningocele leh Myelomeningocele hi eng nge an danglamna?

Myelomeningocele leh meningocele hi spina bifida chi hnih a ni a, mahse a danglamna tlem a awm.

Meningocele hi naute hnungzang kawngkhar atanga tui khata khat bawm a chhuak a, mahse chu bawm chhungah chuan naute ruhro (spinal cord) a awm lo Hei hian nerve a tichhe tlem emaw, a tichhe lo emaw a ni tlangpui.

Mahse myelomeningocele -ah chuan chu bawm chhungah chuan ruhro leh nerve thenkhat a awm a, an chhe vek a ni . Chu chuan a ti na zual sauh a ni.

Myelomeningocele hian tute nge a nghawng?

Myelomeningocele hian nausen eng pawh a nghawng thei. Scientist-te chuan eng thil nge a thlen tih hre chiang lo mah se, nautein he natna a vei theihna tipungtu genetic, environmental, leh nutritional factor ṭhenkhat an hmuchhuak a ni.

Hetiang dinhmun hi engtiang chiahin nge a awm?

Myelomeningocele hi central nervous system-a awm a ni a, a natna hi a ni.Pianpui natna (birth defect) awm tam ber. Entirnan, he natna hian United States-ah kum tin nau piang 1,645 vel a nghawng a ni. Sri Lanka ramah pawh hetiang natna nei hian naupang an piang bawk.

Myelomeningocele natna lan chhuah dan chu engte nge ni?

Myelomeningocele vei naute chuan a hnungzang lai tak atanga ruhro hnuai lam atanga tuiin a khat sac a nei a . Doctor-te chuan naupai laiin ultrasound scan hmangin he natna hi an hre thei fo.

Naute myelomeningocele vei hian piansualna dang a nei thei bawk . Hetiang natna vei naute 10 zinga 8 vel chuan hydrocephalus an tih natna an nei bawk a, chu chu thluaka tui awmkhawm a ni .

Myelomeningocele nena inzawm thei, spinal cord emaw musculoskeletal system-a harsatna dangte chu:

• Syringomyelia (spinal cord chhunga tui awmna cyst) .
• Hip a hring chhuak

Myelomeningocele hi engte nge ni?

Doctor leh scientist-te chuan myelomeningocele awm chhan dik tak chu an la hre lo a , mahse , genetic, nutritional, leh environmental factors inzawmkhawm avanga natna khirh tak a nih an ring

A bik takin, naupai hma leh naupai laia nu taksaa folic acid level hniam hian he piansualna chi hi a thlen thei tih hmuhchhuah a ni. Folic acid (folate tia hriat bawk) hi nausen thluak leh ruhro (spinal cord) hmasawnna atan a pawimawh hle.

Naute pian hmain Myelomeningocele hi engtin nge an hriat theih?

Vawi tam tak (mahse a ni lo) doctor-te chuan naupai laiin nausen myelomeningocele an hmuchhuak thei. Heng test te hi an hmang thin:

• Thisen test: I doctor chuan naupai kar 16 leh kar 18 inkarah thisen test a ti ang a, chu chuan alpha-fetoprotein (AFP) an tih thil pakhat a teh ang. Hmeichhe naupai zingah spina bifida vei naute phur zinga 75% atanga 80% vel chuan he AFP hi a tlangpui aia sang an nei a ni. I level pawh a sang a nih chuan i doctor chuan naute chu enfiah lehzual turin test dang, ultrasound scan ang chi tih a ti ang.
• Fetal prenatal ultrasound: Naupai laiin ultrasound scan hi myelomeningocele hriat dan dik ber a ni. Doctor-te chuan ultrasound scan hi first trimester (kar 11-14) leh second trimester (kar 18-22)-ah an rawt tlangpui. Second trimester scan hian a natna chu a dik berin a hriat theih a ni.
• Amniocentesis test hmanga enfiah a ni:Nausen ultrasound scan hmanga myelomeningocele a awm tih a chiang a nih chuan i doctor chuan amniocentesis test neih a rawt thei ang. Hei hi myelomeningocele nena inzawm genetic condition rare tak tak awm leh awm loh enfiah nan tih a ni. Hei hian doctor chuan needle hmangin nausen chhehvel amniotic sac atanga tui sample lak a huam a ni. He test hian hlauhawmna engemaw zat a nei a, chuvangin hei hi doctor nen sawiho a pawimawh hle.

Naupai laia hmuhchhuah a nih loh chuan naute pian hnuah myelomeningocele hi imaging test MRI (Magnetic Resonance Imaging) scan emaw CT (Computed Tomography) scan emaw hmangin hmuhchhuah a ni.

Myelomeningocele hi eng enkawlna nge ni?

Myelomeningocele enkawlna tlangpui chu naute ruhro (spinal cord) kawngkhar hawnna kha khar tura operation tih a ni .

Doctor-te chuan he surgery hi naute pian hmain (fetal surgery) emaw, a pian hnu lawkah (postnatal surgery) emaw an ti thei a ni.

Myelomeningocele vei naute hian hydrocephalus (thluaka tui awmkhawm) an neih fo avangin, naute thluak atanga tui tam zawk lakchhuah nan ventriculoperitoneal (VP) shunt pawh a ngai thei bawk.

Naupang tam tak chuan an ruhro leh nerve chhiatna avanga harsatna awmte enkawl turin dam chhung enkawlna an mamawh dawn a ni. Enkawlna tlangpui chu natna hrik laka invenna atana antibiotics, meningitis (brain infection) emaw, urinary tract infection (UTIs) leh physical therapy te a ni.

Nausen chu myelomeningocele a awm avangin operation neih a ni

Fetal surgery hi myelomeningocele nasat dan leh nu naupai hriselna a zirin duhthlan tur a ni. Hetiang surgery hi a tam chho zel a.

He surgery hian natna lan chhuahna a tizual lo thei a, mahse , ruhro emaw, nerve emaw-a chhiatna thleng tawh chu a siam ṭha thei lo .

Pawimawh: Heng nausen surgery-te hian harsatna a awm a, chu chu nau neih hmaa nau neih theihna a sang leh uterine dehiscence a ni.

Nau neih hnua myelomeningocele natna avanga operation neih a ni

I naute hian spina bifida siamthat nan nausen surgery a neih loh chuan a pian hnuah a rang thei ang bera operation tih tur a ni – a tha ber chu a pian atanga darkar 48 hmasa berah – natna kai theihna tur a tihziaawm theih nan.

Myelomeningocele vei ka fa hian eng doctor nge a hmuh ang?

Myelomeningocele vei naupang tam tak chuan an enkawlna leh enkawl dan tur inrualrem turin multidisciplinary team puihna an dawng a ni. I fa enkawlna kawnga inrawlh thei specialist-te chu:

• Neurologist a ni
• Neurosurgeon a ni
• Nausen (fetal surgeon) a ni
• Urologist (Urologist) a ni
• Orthopedist doctor a ni
• Vun lam doctor
• Taksa lam enkawltu a ni

Myelomeningocele vei theihna tur risk factors te chu engte nge ni?

Vanduaithlak takin, myelomeningocele ang chi nau piangsual hi pumpelh theih a ni lo – a hlauhawmna chu tihtlem theih chauh a ni . A tam zawkah chuan he natna hi a awm fo thin. Mahse scientist-te chuan he natna nena inzawm risk factor engemaw zat an hmuchhuak a ni. Anni chu:

• Folate (folic acid) tlakchhamna: Nausen hrisel taka thanlenna atan Vitamin B9 natural form folate hi a pawimawh hle. Folate tlakchhamna hian spina bifida leh neural tube defects (NTDs) dang a thlen theihna a tipung a ni. Naupai emaw, naupai tum emaw i nih chuan naupai hmaa vitamin ei a pawimawh a, chu chuan naupai hrisel tak neih theihna tura i mamawh folate (folic acid) leh nutrient dangte i dawng tih chian a pawimawh hle.
• Chhungkaw history-a neural tube defects nei: Naupang pakhat neural tube defect nei tawhte chuan fa pahnihna neural tube defect nei an neih theihna chance chu 3% velin an pung a ni. Tin, hmeichhia neural tube defect (NTD) nei tawhte chuan he natna nei lote aiin myelomeningocele vei fa an nei tam zawk bawk. Mahse, myelomeningocele vei naute tam zawk hi nu leh pa, chhungkaw history nei lo atanga piang an ni.
• Anti-seizure damdawi: Anti-seizure damdawi thenkhat chu naupai laiin ei hian neural tube defects a tipung tih hmuhchhuah a ni.
• Zunthlum: Hmeichhe naupai, zunthlum control tha lote chuan myelomeningocele vei naute an neih theihna a sang hle.
• Thau lutuk: Hmeichhia naupai hmaa thau lutuk te chuan naute neural tube defect nei, myelomeningocele te pawh nei an neih theihna a sang hle.
• Taksa lumna sang: 1.1.Naupai kar tir lama core body temperature (hyperthermia) a san chuan, khawsik chhunzawm zel vang emaw, sauna emaw hot tub hman vang emaw pawh ni se, myelomeningocele vei theihna a tisang deuh tih hmuhchhuah a ni.

Myelomeningocele vei naute neih hi i sualna a ni lo tih hre reng ang che. Nau neih kum tling tawh zawng zawng hi piansualna avanga naupai theihna hlauhawm tak an ni.

Myelomeningocele hi eng prognosis nge ni?

Myelomeningocele vei mi pahnih hi a inang lo hle. Hetiang dinhmun atana prognosis hi thil engemaw zatah a innghat a ni. Chung zingah chuan:

• An ruhro leh nerve te dinhmun hmasa ber.
• Spine-a opening chu engtiang chiahin nge a sang emaw a hniam emaw.
• Chu bag chu hawn nge khar?
• Nau piang hma emaw, pian hnu emawa operation an neih pawhin.

Spina bifida vei te thihna rate hi kum khatah kum 5 leh 30 inkar 1% vel a ni a, spinal cord a sang poh leh complication leh thihna a tam zawk.

Myelomeningocele hian side effect leh complication a neih hian nunphung a nghawng nasa hle thei a ni. Hetiang natna vei te hian lungngaihna, lungkhamna, leh risk-taking behavior an nei tam zawk .

Myelomeningocele natna hian eng harsatna nge a thlen?

Myelomeningocele natna avanga harsatna awm thei te chu:

• Fluid-filled sac (lesion) awmna hmun hnuaia taksa peng hrang hranga paralysis leh/ emaw, hriatna hloh.
• Muscle chak lohna avanga mobility tlahniam.
• Paralysis nena inzawm ruh lama harsatna , entirnan scoliosis (curvature of the spine), contractures, leh hip dislocation te.
• Bladder leh/ emaw bowel control hloh.
• Urinary tract infection (UTIs) a awm fo thin.
• Meningitis (thluak natna).
• Latex allergy nei a ni.
• Zirna inang lo emaw, hmasawnna tlai (cognitive impairments) emaw a awm thei.
• Epilepsy `(Seizures)` a ni.

Myelomeningocele vei ka naute hi engtin nge ka enkawl ang?

Hriat tur pawimawh ber chu myelomeningocele vei pahnih hi a inang lo tih hi a ni. I naute hian engtin nge a nghawng dawn tih chiang taka hriat theih a ni lo. I tih theih tha ber chu spina bifida leh myelomeningocele zirchianna leh enkawlna lama tui doctor nen inbiakna neih hi a ni.

I fa a lo seilian chhoh zel chuan specialist doctor team chuan an mamawh ngaihtuahsak turin an pui ang .A tangkai thei a ni.

Engtikah nge ka fa doctor hnenah myelomeningocele chungchang hi ka sawipui ang?

I fa chu myelomeningocele vei a piang a nih chuan a dam chhungin a doctor – emaw doctor team emaw – a hmuh fo a ngai dawn a ni.

A bik takin, hengte avang hian i fa doctor nen inbiakna neih a pawimawh hle:

• I fa chu kea kal tan a tlai lutuk emaw, a tlai lutuk emaw a nih chuan.
• I fain hydrocephalus symptoms a neih chuan, entirnan, a hmaiah hmun nem tak, thinrimna, mut tam lutuk, leh chaw pek harsatna te.
• I fain meningitis symptoms a neih chuan khawsik, kawr khauh, thinrimna leh tap sang tak a nei thei.

Myelomeningocele chungchangah hian ka doctor hnenah eng zawhna nge ka zawh tur?

I doctor-in myelomeningocele a rinhlelh chuan heng zawhnate hi zawh che a \angkai thei ang:

• Ka naupai chhung zawngin hrisel taka awm turin eng nge ka tih theih ang?
• Spina Bifida leh Myelomeningocele lama tui doctor leh specialist te i rawt thei ang em?
• Myelomeningocele hi eng enkawlna nge ni?
• Fetal repair surgery leh postnatal repair surgery te hian eng hlauhawmna leh hlawkna nge a neih?
• Myelomeningocele vei fa dang neih theihna hlauhawmah ka awm em?
• Myelomeningocele vei leh chutiang naupang nu leh pate tanpuitu pawl chungchang thu i nei em?

I naute hian damdawi lam natna khirh tak a nei tih hriat chu a buaithlak thei hle. Mahse nangmah chauh i ni lo tih hre reng ang che – nang leh i chhungte tanpui thei tur thil tam tak a awm. I naute a nghawng dan leh inbuatsaih dan tur hriat chian nan myelomeningocele chungchang hre chiang doctor nen inbiakna neih a pawimawh.

Kan hnen atanga Take-Home Message pakhat

Myelomeningocele hi nau piangsualna buaithlak tak a ni. Mahse, damdawi lam enkawlna dik, ṭanpuina, leh hmangaihna dik tak an neih chuan heng naupangte hian nun ṭha tak an nei thei a ni . Nausen chhunga he dinhmun hi hriat chian a, enkawl vat a pawimawh. Folic acid ei tam ang chi step lak hian he natna hi a tihziaawm thei bawk. Hemi chungchanga zawhna dang i neih chuan doctor nen inbiakna neih hreh suh.

` Myelomeningocele, Spina bifida, piansualna, neural tube chhiatna, ruhro, naute hriselna, naupai