I taksaah, a bik takin i ruhah natna leh natna i nei fo thin em? A nih loh leh i ruhte chu thil tenawm ber pawha a chhe vek ang maiin i hria em? Heng thil hnung lamah hian kan sawi vak loh condition a awm mai thei, mahse hriat a pawimawh hle. Chutiang dinhmun pakhat chu `(Osteitis Fibrosa Cystica - OFC)` a ni. He hming hi a buaithlak deuhin lang mahse, awlsam takin han sawifiah ila.
Osteitis Fibrosa Cystica (OFC) hi eng nge ni?
A awlsam zawngin sawi ila, `(Osteitis Fibrosa Cystica - OFC)` hi natna hmuh tur awm lo tak a ni a, kan ruhte a nghawng a ni. Kan taksa chhunga parathyroid glands te nen a inzawm tlat a ni. Thyroid gland chungchang hi i hre tawh a. A hnung lamah hian heng parathyroid gland pali te hi an awm a. Heng gland te hian parathyroid hormone (`Parathyroid Hormone - PTH`) an siam chhuak thin.
He `(PTH)` hormone hi kan ruh nghet leh hrisel taka vawn nan a pawimawh hle. Thisen a calcium level control nan a pui bawk. Mahse, han ngaihtuah teh, he `(PTH)` hormone hi siam chhuah tam lutuk, chu chu siam chhuah tam lutuk a nih chuan eng nge thleng ang? Chutah chuan buaina chu a intan ta a ni. Chu `(PTH)` tam lutuk avang chuan ruhte chu tihchak ai chuan zawi zawiin an chak lo tan ta zawk a ni . Hun kal zelah ruhte pianzia a danglam thei a, a chhungah hian khur ang chi thil (tui khat cyst ang chi) pawh a lo awm thei bawk.
He PTH tam lutuk hian thisenah calcium level a tisang thei a, chu chuan kal (kidney stone) a siam thei a, thisen sang (hypertension), leh heart failure a thlen thei bawk.
Condition hi hming dang engemaw zatin `(OFC)` an ti a. Heng hmingte hi i hre tawh mai thei:
- ``Von Recklinghausen-a ruh natna''.
- `Osteitis fibrosa` tih a ni
- `Cystica chu a tlangpuiin a awm`
- `Osteodystrophia fibrosa` tih a ni
- Brown tumor of bone a awm a . He hming hian hlauthawng suh. `(Tumor)` tih ziak ni mah se, ``Cancerous`` a ni lo. He hming hi `(OFC)` vei te hian an ruh chhunga thisen chhuak leh fibrous tissue avanga rawn lang brown spot an neih vang a ni. Mahse a takah chuan cancer natna `(Tumor)` a ni lo.
"(Osteitis Fibrosa Cystica)" tih thumal hian 'ruh hmin leh cyst siam' ang chi a kawk a ni. Chuvangin, `(PTH)` level a san chuan ruh chu engtik lai pawhin a chhe thei a ni. Mahse, he natna `(Hyperparathyroidism)` (i.e. `(PTH)` siam chhuah tam lutuk) hi hriat hmasak a, enkawl hmasak a nih chuan `(OFC)` natna hi tihdam emaw, a lo awm loh nan emaw a veng thei a ni.
Hetiang (OFC) dinhmun hi engtiang chiahin nge a awm?
Tunah chuan he natna hi engtiang chiahin nge a hluar tih i ngaihtuah mai thei. Dik tak chuan, hriselna lama enkawlna tha nei ramteah chuan a tlem hle . Entirnan, United States-ah pawh hian hyperparathyroidism vei zinga 5% aia tlem chuan OFC an vei a ni. Hyperparathyroidism na tak nei, hun rei tak enkawl lohte zingah a lang tam ber.
Mahse tun hma chuan hei hi a tam zawk hle. Kum sawmnga vel kalta khan ``Hyperparathyroidism'' vei zinga 69% vel chuan he ruh natna hi an nei a. Mahse medical science hmasawnna avang hian, a bik takin ``Routine Blood Tests'' a lo chhuah tak avangin heng natna te hi rang zawkin hriatchhuah leh enkawl theih a ni ta a ni. Chu chu thil ropui tak a ni lo maw?
He (OFC) natna lan chhuah dan hi engte nge ni?
Okay, tunah chuan `(Osteitis Fibrosa Cystica)` condition ah hian eng symptoms nge a awm theih tih kan en ang.
A lan chhuah dan ber chu:
- Ruh natna . Hei hi mi tam zawkin an hriat hmasak ber a ni. A châng chuan, ruh khawih pawh a na thei.
- Fractures te chu a awm . Ruh, a bik takin kut, ke emaw, ruhro emaw a awmte chu awlsam takin a chhe thei a ni. Tlu tenau pawhin ruh a tikehsawm thei.
Hetiang dinhmun tir lamah hian a hnuaia chhinchhiahna te hi a awm thei bawk (hengte hi ``Hyperparathyroidism'' chhinchhiahna pawh a ni thei):
- Chau tih hriat reng (`Fatigue`).
- Chaklohna.
- Nausea leh luak chhuak.
- Ek khal.
- A tlangpui aia tam zun chhuah (`Polyuria`). Hei hian toilet-a kal tam a ngai tihna a ni.
Heng symptoms te hi i neih chuan nangmah ngeiin, "Aw, hei hi `(OFC)' a ni," tiin thutlukna siam suh. A chhan chu heng symptoms te hi natna dangah pawh a awm thei a ni. Mahse hengte hi hriat chian a, doctor hnena hrilh a pawimawh hle.
(OFC) awm chhante chu engte nge ni?
Eng thilin nge Osteitis Fibrosa Cystica hi a thlen? Ka sawi tawh ang khan hei hi a chhan ber chu enkawl loh Hyperparathyroidism . Chu chu kan Parathyroid glands te hian PTH an siam tam lutuk tihna a ni. Hei hi kawng lian pahnihin a thleng thei a ni:
1. Primary Hyperparathyroidism: Hei hi i parathyroid glands-a harsatna awm vang a ni. Heng glands te hi cancer (cancerous) emaw, noncancerous growth (adenoma ang chi) nei emaw, PTH tam lutuk siamtu an ni thei bawk. A nih loh leh gland palite hi a lian vek (hyperplasia) a, hormone tam lutuk a siam chhuak thei bawk.
2. Secondary Hyperparathyroidism: Hei hi hriselna lama harsatna dang vang a ni. Entirnan, miin kal natna rei tak a neih chuan a taksaa calcium leh vitamin D balance chu a tibuai a ni. Tichuan, a chhanna atan chuan parathyroid glands te chuan PTH tam zawk an siam tan ta a ni. Tin, vitamin D tlakchhamna nasa tak a awm chuan thisen calcium level a hniam avangin parathyroid glands te hian calcium level tihsan nan an thawkrim zawk thin. Chutih lai chuan PTH hormone pawh a pung a, hun kal zelah Osteitis Fibrosa Cystica a lo awm thei bawk.
Ngaihtuah teh, kan pi Kamala hian hun rei tak chhung chu kal lam harsatna a nei tawh a. Chumi atan chuan damdawi dik tak a ei lo. Hun engemaw chen hnuah a `(Parathyroid)` glands te chuan a taksa chhunga calcium awm chu thunun tumin an bei nasa hle a, an tih tur aia tam `(PTH)` an siam chhuak ta a ni. A tawpah chuan aunt Kamala chuan ruh na nen `(OFC)` a nei ve ta a. A inzawmna chu i hrethiam em?
(OFC) avanga harsatna awm thei te chu engte nge ni?
Hyperparathyroidism enkawl loh leh OFC avanga harsatna lian ber chu ruh nena inzawm a ni. Hei hian natna, ruh chhiatna (a pianzia inthlak), leh ruh tliak awlsam tihna a ni . Hengte hi a lang nghal mai thin a ni. Mi chu a san zawng pawh a tlahniam thei.
Mahse, hei bakah hian harsatna dang a awm thei bawk. Anni chu:
- Kidney lung (kidney stone) siam chhuah.
- Kidney tha lo a awm.
- Energy hniam, hah reng.
- Pum natna.
- Rilru lama harsatna, depression ang chi te.
- Hriatrengna leh ngaihvenna lama harsatna.
Hmun khata buaina intan chu eng chen nge a kal theih tih hi han en teh. Kan taksa system pakhata harsatna awm hian system dang pawh a nghawng thei a ni. Chuvang chuan a hmaa hriatchhuah leh enkawl a pawimawh.
Engtin nge OFC hi hmuhchhuah a nih?
Okay, tunah chuan engtin nge doctor hian he natna `(Osteitis Fibrosa Cystica)` hi a hriat theih ang?
A hmasain, i doctor chuan i hriselna chanchin kimchang takin a ziak ang . Heng symptoms te hi eng chen nge i neih tawh tih te, i PTH level tichhe thei damdawi dang (kidney disease ang chi) i neih leh neih loh te, eng damdawi nge i ei tih te a zawt ang che. Tichuan, ruh na, a hring, a nih loh leh a piansual loh enfiah turin taksa enfiahna an nei ang.
Natna finfiah nan doctor-te chuan test ang chi te hi an hmang thei ang:
- Thisen test: Hengte hian hormone leh mineral inthlauhna a enfiah thin. A bik takin parathyroid hormone (PTH) level, calcium level, phosphorus level, vitamin D level leh alkaline phosphatase (ruh atanga enzyme chhuak) te an enfiah thin. OFC-ah chuan PTH leh alkaline phosphatase level a sang thei hle.
- Zun test: I zun a calcium awm zat pawh i en thei bawk.
- Imaging test hrang hrang:
- X-ray: Hengte hian ruh te hi eng ang taka sei nge a nih tih te, cyst ang chi thil te, ruh chhunga break tenau tak tak (microfractures) emaw, characteristic change (subperiosteal resorption ang chi) emaw a awm leh awm loh a tarlang thei a ni.
- CT Scan (`CT - Computed Tomography scans`) emaw MRI Scan (`MRI - Magnetic Resonance Imaging scans`): Hengte hian X-ray aiin ruh dinhmun chipchiar zawkin a tarlang a ni.
(OFC) enkawlna tur engte nge ni?
Awle, tunah chuan `(Osteitis Fibrosa Cystica)` enkawlna chungchang hi han sawi ila. Enkawlna chu `(OFC)` thlentu `(Hyperparathyroidism)` chi leh nasat danah a innghat a ni.
- Primary hyperparathyroidism hi a chhan a nih chuan:
- A tam zawkah chuan he `(OFC)` dinhmun lo awm chhan hi `(Parathyroid)` gland (tumor ang chi) hnathawh dan pangngai lo a nih chuan, standard treatment chu gland emaw, gland thenkhat emaw surgery hmanga lakchhuah (`Parathyroidectomy`) a ni . He surgery hian ruh hring hring a titawp thei a, ruh chhiatna lo awm tawh thenkhat chu a siam tha leh thei bawk (`remineralization`). A tlangpuiin `(Parathyroid)` gland pali kan nei a. Chuvangin, buaina nei gland chu lakchhuah a nih chuan gland la awmte chuan taksa mamawh `(PTH)` hormone chu an siam chhuak thei a ni.
- Operation nei thei lo emaw, secondary hyperparathyroidism nei emaw tan:
- A chhan bulpui enkawl dan: Entirnan, a chhan chu vitamin D tlakchham vang a nih chuan vitamin D supplement pek thin a ni. Kidney natna a nih chuan a tul anga enkawl a ni.
- Calcimimetics: Heng damdawi te hian i thisen a calcium awm chu an entawn thin. I parathyroid gland chu PTH tlem zawk siam turin an "trick" thin. Cinacalcet hi chutiang damdawi pakhat chu a ni.
- Bisphosphonates: Heng damdawi te hian ruh hloh rate tihziaawmna hmangin hna an thawk a ni. A tlangpuiin ruh natna vei tan an pe thin. Mahse, OFC vei tan pawh hun rei lote chhungin an pui thei a, a bik takin operation hmaa ruh tichak turin an pui thei bawk.
- Vitamin D leh calcium supplement: Hengte hi a tul angin pek thin a ni. Mahse, thisen calcium level a san chuan calcium supplement pek a ni lo.
(OFC) dinhmun thlirletna chu eng nge ni?
He `(OFC)` dinhmun hi eng nge beiseina awm? Dik tak chuan, enkawl leh enkawl dan dik tak chuan rah tha tak a chhuah thei a ni . Enkawlna hian ruh hring hring a titawp thei a, ruh a tichak bawk (`remineralize`). Ruh tliak chuan a tidam thei a, natna a tiziaawm thei bawk. Amaherawhchu, ruhte chu a chhe nasa hle a nih chuan a dam kim lo thei a ni.
(OFC) hi ven theih a ni em?
Hetiang natna `(Osteitis Fibrosa Cystica)` lo awm tur hi ven theih a ni em? Ni e, eng emaw chen chu a theih a ni. A bulpui ber chu `(Hyperparathyroidism)` natna hi hriat hmasak leh enkawl hmasak hi a ni.
- It is very important to have routine blood tests , a bik takin risk factors i neih chuan kidney disease ang chi i neih chuan. Hei hian i thisen calcium leh PTH level a inthlak danglam chuan chhiatna nasa tak a thlen hmain a hriat theih nan a pui ang.
- Tin, doctor nen inbia la, calcium leh vitamin D level tha tak vawng reng rawh.I tih tur chu ti rawh. Entirnan, thlasik laiin ni êng tlemna hmunah i awm a nih chuan vitamin D supplement i ei a ngai mai thei. I doctor chuan i ei leh in atanga i mamawh tur nutrients i hmuh theih dan tur a hrilh bawk ang che.
Hriat reng tur chu, natna `(Hyperparathyroidism)` hi hriatchhuah leh enkawl a nih hma chuan `(Osteitis Fibrosa Cystica)` a vei tlem zawk thin.
Engtikah nge Doctor ka hmuh ang?
Ruh na, tenderness, emaw ruh a chhe dawn nia i hriat chuan doctor pan nghal rawh. Tin, ka sawi tawh ang khan hyperparathyroidism symptom hmasa ber (chau lutuk, rilru hahna, leh zun tam lutuk ang chi) i neih chuan i doctor hnenah hrilh rawh. Hyperparathyroidism i nei tawh a nih chuan doctor-in a tih angin i thisen test fo a tha a, calcium leh PTH level enfiah a tha.
Doctor hnenah eng zawhna nge ka zawh ang?
`(Osteitis Fibrosa Cystica)` i vei tih hmuhchhuah i nih chuan i doctor hnenah heng zawhnate hi zawh a \angkai thei ang:
- Ka dinhmun hi engtiang chiahin nge a chhiat?
- Eng enkawlna kawng nge ka neih? An thatna leh that lohna chu engte nge ni?
- Supplements ei hi ka tan a pawi em? Eng ang nge?
- Surgery ka mamawh dawn em? Chutiang a nih chuan a hnuah eng nge ka beisei ang?
- Eng ei leh in lama inthlak danglamna nge ka tih theih ang a, chu chuan min pui thei ang?
- He dinhmun hian engtin nge ka nitin nun a nghawng ang?
A tawp berah chuan point pawimawh tlemte
Chuvangin, hei hi ka hrilh che a ngai a ni. Ruh chak lo leh natna hian kan nitin nunah nghawng lian tak a nei thei a ni. I ruhte a chhe awlsam chuan thiltih ṭhenkhat chu skip duhna pawh i nei thei. Chauhna, chak lohna, rilru hahna, leh zun tam lutuk ang chi symptom i neih chuan ``Hyperparathyroidism`` emaw a complication ``OFC`` emaw a ni thei.
Heng symptoms te hi i neih chuan Doctor rawn pan nghal mai tur a ni. Natna i hriat chian thuai a, i enkawl thuai poh leh i ruhte i tihchhiat a tlem phah a ni. I hriselna hi i tan a pawimawh hle. Chuvangin enkawl tha rawh.
` Osteitis Fibrosa Cystica, OFC, Ruh natna, Parathyroid, PTH Hormone, Hyperparathyroidism, Ruh Na











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