Lu chhungah emaw, thluak chhungah emaw, gland te tak te tak, mahse pawimawh tak tak – pituitary gland bulah hian tumor mak tak mai a lo thang lian tih i hre tawh em ? Hei hi craniopharyngioma an ti a. A nihna takah chuan a tlem deuh a, chu chu mi zawng zawng tuar thei natna a ni lo tihna a ni. Mahse he tumor te tak te hian i mit leh i endocrine system ah hetiang hian nghawng lian tak a nei thei a ni . Chuvangin vawiin hian he thu hi chipchiar deuhin han sawi ila, okay?
Craniopharyngioma tih hi eng nge ni?
A awlsam zawngin sawi ila, craniopharyngioma hi a awm lo hle a, cancer ni lo (benign) tumor a ni. I pituitary gland bulah a lo thang lian thin. Tumor chu a lo thang zauh zauh a. Mahse, i cranial nerves , a bik takin i mit hmuhna nena inzawm nerve te a nghawng thei a ni. I taksaa hormone awmte control tu i endocrine system pawh a nghawng thei bawk.
Hei hi enkawlna ber chu surgery leh radiation therapy te hi a ni . A châng chuan, chemotherapy hi tumor chi khat, papillary subtype-ah pawh hman a ni.
Thu lawmawm tak chu he tumor vei zinga 90% aia tam hi an hmuhchhuah atanga kum nga hnuah an dam thei a ni. Mahse, he tumor hi chronic condition anga ngaih a ni . A chhan chu enkawlna hian he tumor avanga natna dangte hi a tidam ngai lo va, he tumor chi hi a lo lang leh mai thei bawk.
Tute nge craniopharyngioma vei?
Kum tinin mi maktaduai khatah mi pahnih velin craniopharyngioma chi hnih zinga pakhat an vei a: adamantinomatous leh papillary . Kum hnih ah an tam ber a:
- Naupang kum 5 leh 14 inkar
- Puitling kum 50 leh 74 inkar
Kum eng pawha adamantinomatus type hi a lo awm thei a, papillary subtype hi puitlingah hmuh tur a awm tam ber.
He craniopharyngioma hi engtiang chiahin nge a nasat?
Dik tak chuan craniopharyngioma hi damdawi lam natna khirh tak a ni. Damdawi lam dam chhung zawnga enkawl a ngai thei a ni. Surgery hmanga lak chhuah vek tumor zinga a chanve vel chu hun engemaw chen hnuah a lo let leh ang. Heng tumor avanga hriselna lama harsatna awm thenkhat hi chu tumor lakchhuah hnuah pawh a awm reng thei a ni.
Craniopharyngioma leh Pituitary Adenoma hi eng nge an danglamna?
Heng pahnih hian hormone hnathawh a tichhe thei a ni.Pituitary adenoma hi i pituitary gland-a lo awm thin tumor chi khat a ni. Mahse, craniopharyngioma hi gland bulah a lo awm thin. Tumor chi hnih hi benign ni mahse, craniopharyngioma hi pituitary adenoma aiin a na zawk tlangpui.
Craniopharyngioma natna lan chhuah dan chu engte nge ni?
Craniopharyngioma symptoms hi thil engemaw takin i emaw i fa emaw pituitary gland, hypothalamus gland, optic nerves , leh thluak a nghawng hian a lo awm thinna nen a inzawm a ni.
- Naupang tan: Hei hian naupangte thanlenna leh thanlenna a nghawng thei a ni. Hei hi puitling craniopharyngioma vei aiin naupangte zingah a langsar zawk.
- Naupang leh puitling tan: Mit hmuhna a nghawng thei. A bik takin peripheral vision a tlahniam thei.
Amaherawhchu, hêng chhinchhiahnate hi natna dangte nên a inang thei avângin, doctor-te tân chuan he natna hrik avânga lo awm a ni tih hi rang taka sawi chhuah a harsa thei a ni.
Pituitary gland-a pressure avanga awm dinhmun
I emaw i fa emaw pituitary gland hian taksa hormone hnathawh tam tak a thunun a ni. Craniopharyngioma hian he gland hi a press chuan a hnuaia thil awmte hi a lo awm thei a ni:
- Growth Hormone (GH) tlakchhamna: Hei hian naupangte thanlenna a tikhawlo thei a ni. Puitlingah chuan GH tlakchhamna hian chak lohna, ruh natna ( ruh hring), taksa ruh chakna tlahniam, LDL cholesterol tihpun, leh thinlung natna a thlen thei a ni.
- Gonadotropin tlakchhamna: Hetiang natna vei te hian puitlin hun rei tak an nei thei. Hmeichhia chuan thlasik an chawlhsan thei a, chu chu amenorrhea an ti a ni.
- Adrenocorticotropic hormone (ACTH) tlakchhamna: Hei hian chak lohna leh hahna a thlen thei. Tin, taksa rihna tlahniam, ei duh lohna, taksa ruh chak lohna, luak leh luak chhuak, thisen sang ( hypotension ) te a thlen thei bawk.
- Thyroid Stimulating Hormone (TSH) tlakchhamna: TSH hniam nei te hian hahna, period mumal lo, leh theihnghilh te ang chi symptoms an nei thei.
- Central Diabetes Insipidus (CDI): He natna hi tuihal lutuk ( polydipsia ) leh zun tam lutuk ( polyuria ) vang a ni.) thleng. CDI vei te hian dehydration , thinlung thawk mumal lo, khawsik, vun leh mucous membrane vawt, buai, leh seizures ang chi dinhmun an nei thei.
Hypothalamus-a pressure avanga awm dinhmun
I fa emaw i fa emaw hypothalamus hian taksa kalphung, mood, riltam leh tuihal, mut dan, leh mipat hmeichhiatna hman dan te a thunun a ni. Craniopharyngioma tumor-in hypothalamus a press chuan a hnuaia thil awmte hi a thleng thei a ni:
- Hypothalamic obesity: Hei hian calorie tihtlem, exercise leh diet control-na nei chung pawha thau lutuk tihna a ni.
- Froehlich’s syndrome: Hetiang natna vei te hian eng ang pawhin ei mah se riltam an nei a, chu chuan thau lutuk a thlen thin. Froehlich’s syndrome vei naupangte chu naupang dang aiin an lo thang zawi zawk thei. Naupang thenkhat chu mitdelna leh rilru lama harsatna nei te pawh an awm thei bawk.
- Non-24-hour sleep-wake syndrome: Hei hi mut harsatna a ni a, mut dan pangngai zawm thei lo tura siam a ni. Mi thenkhat chuan mut harsatna nasa tak an nei thei bawk .
He tumor hian engtin nge i emaw i fa emaw mit hmuhna a nghawng?
Craniopharyngioma tumor hi i emaw i fa emaw mit nerve hnaih takah a lo awm fo thin . Heng nerve te hi compress a nih chuan mit a fiah lo emaw, peripheral vision-ah harsatna a thlen thei a ni.
Eng thilin nge craniopharyngioma hi a thlen?
Zirchiangtute chuan a chhan dik tak chu an la hre lo a, mahse heng tumor te hi i emaw i fa emaw pituitary gland siam tura puitu cell atanga lo piang chhuak niin an ngai. Eng emaw chhan vangin heng cell te hi a pangngai lo a, an pung a, an thang lian a ni.
Engtin nge doctor te hian Craniopharyngioma hi an hriat theih?
Hetiang tumor chi hi i enfiah a nih chuan i doctor chuan i medical history leh taksa thanlenna chungchang a zawt thei ang. I fa chu enfiah a nih chuan, a taksa thanlenna te, a rilru lama hmasawnna te, a mit hmuh dan te, leh a tuihalna danglam tak tak emaw, zun tam a ngai emaw tih te an zawt thei a ni.
Eng ang test nge tih thin?
Doctor-te chuan hetiang test hi an ti thei ang:
- Thisen test: Hengte hian hormone level thenkhat a teh thin.
- Urinalysis: Kal lama harsatna awm leh awm loh a enfiah thin.
- CT scan (Computed Tomography - CT scan): X-ray hrang hrang leh computer hmangin tissue nem leh ruh te chu three-dimensional (3D) image siam nan an hmang thin.
- MRI Scan (Magnetic Resonance Imaging - MRI) hmanga tihchhuah a ni.Hei hi painless test a ni a, magnet lian tak, radio wave leh computer hmanga taksa peng leh insiam dan chi hrang hrang thlalak chiang tak tak siam a ni.
- Biopsy: Doctor-te chuan biopsy (tissue sample la) an ti a, microscope hmangin cell, tui, tissue emaw, a lo thang lian emaw an enfiah thin.
Craniopharyngioma hi enkawl theih a ni em?
Craniopharyngioma hi thluak surgery hmanga enkawl a ni tlangpui . Hei hi hnar atanga camera te tak te (scope) dah hmangin emaw, lu chhungah khur te tak te siamin ( craniotomy ) tih theih a ni. Surgery hian a tum ber chu tumor chu a tam thei ang ber paih chhuah a ni a, chutih rualin pituitary gland, hypothalamus emaw optic nerves emaw tihchhiat a tlem phah bawk. Mahse, mi thenkhat chuan operation hnuah hormone damdawi an ei a ngai mai thei. Tin, tumor hi him taka lak chhuah kim theih a nih loh chuan operation hnuah radiation therapy hman a tha thei bawk.
Surgery avanga side effect awm tlangpui te chu engte nge ni?
Craniopharyngioma surgery hi a harsa hle a ni . Pakhatnaah chuan, heng tumor te hi nerve nalh tak tak leh pituitary gland bulah an lo thang lian avangin an tihchhiat theihna a sang hle. Pahnihnaah chuan, craniopharyngioma lakchhuah chu envelope tichhe lovin envelope atanga sticker lakchhuah ang a ni. Hei hi a chhan chu heng tumor te hi pituitary gland leh mit hmuhna nena inzawm nerve te nen an inzawm tlat avangin a ni. Doctor thenkhat chuan heng tumor te lakchhuahna tur surgery hian tumor ngei ang bawkin a tichhe thei niin an ngai. Chuvangin, surgery neih chhan leh eng side effect nge beisei tur tih hi hriatthiam lawk a pawimawh hle.
Craniopharyngioma hi ven theih a ni em?
Vanduaithlak takin heng tumor te hi ven theih a ni lo. I emaw i fa emaw taksa lo thanglian zel chhunga cell inthlak danglamna avanga lo awm an ni.
Craniopharyngioma natna hi eng chen nge i dam theih ang?
Mi tam tak chu enkawl hnuah kum tam tak an dam. Mahse heng tumor te hi a lo lang leh thei fo. A pum puiin, operation hmanga tihbo vek tumor zinga 17% vel chu a lo kir leh ang. Hetiang zat hi tumor thenkhat chauh lakchhuah te tan chuan 25% atanga 63% ah a pung thin. Craniopharyngiomas lo kir leh tam zawk chu operation an neih atanga kum thum chhungin an lo kir leh ang.
Doctor thenkhat chuan craniopharyngioma hi natna khirh tak niin an ngai a, hun rei tak enkawl leh enkawl ngai a ni. Hei hi chhan hrang hrang a awm a:
- Nang emaw i fa emaw chuan tumor lo lang leh chu lakchhuah nan operation dang neih leh a ngai mai thei.
- Nangmah emaw i fate pituitary gland emaw hypothalamus emaw chu tumor emaw surgery emaw avanga nghawng a nih chuan hormone replacement therapy a ngai mai thei.
- Naupang tam tak, tumor vanga hypothalamic obesity nei te hi hriselna lama harsatna dang an neih theihna a sang hle. I fain hypothalamic obesity a neih chuan i fain ei tur tha a thlan theih nan leh exercise a tih fo theih nan tanpuina leh kaihhruaina i mamawh ang.
Engtikah nge kei/ka fa hian doctor a hmuh ang?
Nang emaw i fa emaw chu kum tam tak chhung chu craniopharyngioma nen an khawsa a ngai mai thei. Heng tumor te hi a lo thang leh thei a, enkawlna hian a symptom zawng zawng a ti bo vek lo thei bawk. I/i fa enkawl dan tur ruahmanna i siam hunah heng thilte hi ngaihtuah la:
- I emaw i fa emaw hriselna zawng zawng enfiah turin kum tin i doctor i pan tur a ni.
- I emaw, i fa emaw doctor chuan kum tin scan, a tlangpuiin MRI scan , chu tumor lo lang leh leh awm loh enfiah turin a ti mai thei.
- Nang emaw, i fa emaw chuan hormone tlakchhamna emaw, mitdelna emaw, operation hmanga siam ṭhat loh ang chi dinhmunte enkawlna kawngah ṭanpuina i mamawh mai thei.
Ka/ka fa doctor hnenah eng zawhna nge ka zawh ang?
Craniopharyngioma hi cancer awm lo, tumor awm lo tak ni mah se, hun rei tak enkawl ngai damdawi lama harsatna engemaw zat a thlen thei a ni. Nang emaw i fa emaw hian he tumor hi i nei a nih chuan he dam chhung zawnga natna hi enkawl dan tur i ngaihtuah mai thei. I emaw, i fa emaw doctor nena inbiakna neihpui thei tur zawhna ṭhenkhat chu hetiang hi a ni:
- He rah hi ka la hre ngai lo. Eng nge a nih i sawifiah thei ang em?
- He tumor hian kei/ka fa hian damdawi lama harsatna lian tak dang a thlen thei ang em?
- Engvangin nge kei/ka fa hian he tumor hi a neih?
- Eng enkawlna kawng nge awm?
- Enkawlna hlawhtlinna chance engzat nge awm?
- Enkawlna hian ka/ka fa natna lanchhuahna chu a ti bo dawn em ni?
- Enkawlna hian hun rei lote leh hun rei tak chhunga nghawng tha lo a neihte chu engte nge ni?
- Tumor chu a lo thang leh a nih chuan eng nge thleng ang?
Craniopharyngioma tihbo tumin operation i nei a nih pawhin, heng tumor awm lo, cancer ni lo, hun rei tak chhung chu nangmah emaw, i fa emaw chungah nghawng a nei thei a ni. Chu bâkah, nangmah emaw, i fa emaw chuan tumor vanga natna awmte chu damdawi lam enkawlna kalpui reng a ngai mai thei bawk. Kawng khatah chuan craniopharyngioma hi natna khirh tak a ni a, nangmah emaw i fa emaw chuan i dam chhung zawngin i enkawl a ngai dawn a ni. Doctor-te chuan an tidam kim thei lo nain, nang leh i fa chu he tumor hmuh tur awm lo tak nena nun harsatnate hmachhawn turin theihtawp an chhuah thei a ni.
A tawp berah chuan take-home message:
Craniopharyngioma hi natna khirh tak leh hmuh tur awm lo tak a ni a, mahse damdawi lam enkawlna dik leh hun rei tak chhunga ruahmanna siamin a enkawl theih a ni.
- Damdawi lam thurawn zawng fo rawh: I medical team nena inzawmna nei reng tur leh test leh appointment ruat saah te tel reng a pawimawh hle.
- Beiseina nei reng rawh: Hei hi zinkawng harsa tak ni mah se, nangmah chauh i ni lo. Doctor-te, chhungte leh ṭhiante ṭanpuinain hei hi paltlang theihna chakna i hmu ang.
- Hriat tur: He natna chungchang te, a enkawl dan te, leh harsatna awm thei te hriat chian chuan thutlukna dik siam turin a pui ang che.
He natna hi hlawhtling taka nun theihna kawng tha ber chu a hmaa hriatchhuah leh enkawl dan tha ber a ni tih hre reng ang che. Nang emaw i fa emaw hian heng symptoms te hi i neih chuan doctor pan hreh suh.
` Craniopharyngioma, thluaka natna hrik, pituitary gland, hormone, mit hmuhna, naupang hriselna, cancer ni lo tumor











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