Moms and Dads u, in fa thisen report in hmuh khan doctor pakhatin ‘Low neutrophils’ emaw ‘Low white blood cells’ emaw a tih khan i hlau deuh mai thei, a dik em? A nih loh leh, i fa chu a damlo fo a nih chuan, hei hi a chhan a ni em tih i ngaihtuah mai thei. Chuvangin vawiin hian `(Neutropenia)` (pronounced: neutro-pe-nia) tih condition chungchang kan sawi dawn a ni. Hei hi dik taka i hriatthiam chuan a tul lova hlauhna nei lova uluk taka i enkawl theih nan tanpuina ropui tak a ni ang.
`(Neutropenia)` tih awmzia chu eng nge ni?
A awlsam zawngin `(Neutropenia)` tih hian kan thisenah thisen var chi khat bik kan nei tling lo tihna a ni. Heng thisen var te hi `(Neutrophils)` kan ti a. Heng `(Neutrophils)` te hi kan taksa chhunga sipai te tak te angin han ngaihtuah teh. An hna ber chu kan taksaa hrik lut `(Bacteria)` ang chi hrik do a, natna laka min humhim hi a ni. `(Bacteria)` hi hrik chi khat a ni a, natna chi hrang hrang min thlentu an ni.
Chuti a nih chuan, heng sipai `(Neutrophils)` an tihte hi kan thisenah kan hloh tawk a nih chuan eng nge thleng thin? Kan taksa invenna (defence system) a chak lo hle. Tichuan natna hrik te chu awlsam takin taksaah a lut thei a, natna khirh tak tak a thlen thei a ni. Chuvangin naupang `(Neutropenia)` vei chuan khawsik a neih a, a hliam chhehvel a senna chhinchhiahna a neih chuan, a nih loh leh a khawsik leh a khur a nih chuan damdawi lam thurawn lak nghal a pawimawh Mahse lungngai suh, inenkawlna i hmuh vat chuan `(Neutropenia)` vei naupang zinga hri kai tam zawk hi tihdam theih a ni.
Naupang ``(Neutropenia)'' vei hian eng natna nge a neih?
Naupang ``(Neutropenia)`` vei chuan naupang hrisel dang aiin natna a vei tam zawk. Tin, heng hri kai te hi:
- A thleng fo thei.
- A pawi zawk pawh a ni thei.
- A na zual thuai thei.
Symptoms chu i fain natna a neih chi hrang hrangah a innghat a ni. Entirnan, naupang beng natna nei chuan beng na a nei thei. A châng chuan natna lan chhuahna tlangpui, khawsik, taksa na, leh ei duh lohna te pawh an nei thei bawk.
Engvangin nge hetiang `(Neutropenia)` hi a lo awm? A chhante chu engte nge ni?
Tunah chuan ``Neutropenia`` hi thisen a ``Neutrophils`` awm zat tlahniam vang a ni tih kan hre ta. Hei hi thil engemaw zat a awm a, chungte chu:
- Infection hrang hrang: Viral emaw bacteria emaw infection thenkhat chuan ``(Neutrophils)'' hi hun eng emaw chen atan a tihtlem thei.
- Damdawi: Chemotherapy, a bik takin cancer cell tihhlumna atana hman damdawi te hian ruhro a nghawng thei a, neutrophils siam chhuah a ti tlem thei bawk. Damdawi dang thenkhat pawhin hetiang hi a thlen thei bawk.
- Radiation therapy: Cancer cell tihchhiatna atana hman radiation therapy hian ruhro a tichhe thei bawk a, neutrophils siamchhuahna a tichhe thei bawk.
- Genetic lama harsatna awmte: 1.1.Naupang thenkhat chu an pian tirh atanga awm thin genetic condition vangin ``Neutropenia`` an nei thei bawk. Hei hi ``Congenital neutropenia`` an ti bawk.
- Bone marrow dysfunction: Bone marrow hi kan ruh chhunga sponge ang chi a ni. Hei hi kan thisen cell siamna hmun a ni. Chuvangin, he ruhroah hian harsatna eng pawh hian `(Neutrophils)` siam chhuah a tihtlem phah thei a ni.
- Immune system hian a mah ngeiin ``Neutrophils'' a bei a: Hei hi ``Autoimmune neutropenia'' an ti a. Heta thil thleng hi kan taksa chhunga hrik dotu immune system hian a tisual palh a, mahni ``Neutrophils'' cells te chu a tichhia a ni.
A châng chuan, neutropenia hi a lo thleng thei a, a lo kal thei bawk (cyclic neutropenia) . Chumi awmzia chu ni engemaw zat danah neutrophils level a tlahniam a, chutah chuan a pangngaiah a kir leh tihna a ni. Thil dang dangah chuan doctor-te chuan neutropenia (idiopathic neutropenia) awm chhan an hmu thei lo .
Engtin nge `(Neutropenia)` i vei tih i hriat theih ang?
Doctor-te chuan Neutropenia hi thisen test Complete Blood Count (CBC) an tih hmangin an hmuchhuak thin. Hei hian thisen chhunga cell chi hrang hrang awm zat a teh a ni.
Naupangin neutropenia a vei chhan dik tak hriat tumin, hematologist, thisen natna lama tui doctor chuan test dang engemaw zat a ti thei bawk. Chung zingah chuan:
- Naupang thisen microscopic hmanga enfiah.
- Bone marrow sample tlemte tak tak (`(Bone marrow biopsy)`) lak a, microscope hmanga enfiah.
- Infection chi hrang hrang testing neih a ni.
- Genetic test neih a ni.
Heng test te hian neutropenia awm chhan dik tak chu a tichiang a ni.
Neutropenia hi engtin nge enkawl a nih?
`(Neutropenia)` enkawl dan chu a natna chhan leh a nasat danah a innghat a ni. `(Neutropenia)` vei zawng zawng hi enkawl ngai a ni lo.
Doctor-te chuan enkawl dan tur thutlukna siam nan `ANC (Absolute Neutrophil Count)` tih hlutna an hmang a. `ANC` hi thisen chhunga `(Neutrophils)` cell awm zat tehna dik tak a ni. He value hi a hniam poh leh naupangin natna khirh tak a neih theihna a sang zawk.
Enkawl a ngai a nih chuan kawng hrang hrang a awm a:
1. `(Neutropenia)` dinhmun siamthatna:
- Granulocyte Colony-Stimulating Growth Factor (G-CSF) injection: Hengte hian ruhro chu neutrophils tam zawk siam turin a tichak a ni.
- Steroid damdawi: Heng damdawi te hi taksa hriselna (immune system)-in neutrophils (a bik takin autoimmune neutropenia) a tihchhiat loh nan a titawp a ni.
- White blood cell transfusions: Naupang chu natna hrik do turin cell dang pek belh.
- Stem cell thlak danglam dan:Hei hian thisen siamtu stem cell natna nei te chu donor atanga stem cell hrisel tak tak hmanga thlak a huam a ni. Hei hi thil pawi tak takah pawh tih a ni fo.
- Splenectomy: A chang chuan spleen hian neutrophils a tichhia a, chuvangin spleen lakchhuah hian neutrophils level a tisang thei a ni.
2. Hri kai venna leh enkawl dan:
- Antibiotics: Antibiotics hi natna a lo awm chuan enkawl nan emaw, a chang chuan natna laka inven nan emaw pek thin a ni.
3. Naupang neutrophil count hniam tak tak leh hri kai theihna sang tak nei te tan thupek bik:
Heng naupangte hi hri kai laka venhim nan a bik taka fimkhur a ngai a ni.
Pawimawh: Heng thupekte zawm hian i fa chu hri kai tam tak lakah a veng thei a ni.
- Mipui tamna hmun, sikul ang chite chu a theih ang angin pumpelh rawh.
- Mi damlote laka inthiarfihlim.
- Thil pawimawh tak tak avanga zin i nih chuan face mask vuah thin ang che.
- I kut chu uluk takin (sahbawn leh tui hmangin second 20 tal) sil fo thin ang che.
- Nitin ha sil leh flossing thin.
- Rectal thermometer hmangin khawsik a awm leh awm loh enfiah suh (hei hian hliam a thlen thei a, natna hrik a luhtir thei bawk).
- Hliam te tak te i neih chuan tifai vat la, plaster hnawih bawk ang che.
- Razor ang chi thil nalh tak tak hman loh tur (a tan chuan natna hrik a thlen theih avangin).
- Chaw thenkhat ei loh tur:
- Unpasteurized milk leh bawnghnute atanga siam ei tur.
- Thei, thlai, leh nut raw – an silfai leh a hmin tha a nih phawt chuan a pawi lo.
- Raw honey a ni.
- Heng chawte hi hrik a awm theih avangin ei loh tur a ni.
Nu leh pa angin engtin nge in tanpui theih?
I fain neutropenia a vei a nih chuan doctor thupek dik taka zawm a pawimawh.
- Ni ruat saah thisen test tir rawh.
- Damdawi pek chu dik tak leh a hun takah pe rawh.
- Infection laka invenna tur instruction pek ang chiah zawm rawh.
Heng thilte hi dik taka i tih chuan i fa dinhmun hi i enkawl tha thei ang.
Engtikah nge doctor i hmuh ang? (Emergency-ah chuan!)
Neutropenia vei naupangin hri kai chhinchhiahna a lan chhuah chuan damdawi lam pan vat a pawimawh hle. Enkawl vat a nih chuan naupang chu a dam thuai tlangpui.
A hnuaia symptoms te hi i neih chuan , i doctor hnenah hriattir nghal rawh:
- Khawsik hi 38 degree Celsius (100.4 Fahrenheit) aia sang a nih chuan.
- I vawt, i khur leh/ emaw i thawmhnaw i chhuah chuan.
- Khuh, thawk harsa.
- Kawng na, ril na.
- Zun laiin natna.
- Skin lesion vel a sen leh darh a awm chuan.
- Luak chhuak emaw, luak chhuak emaw.
- Natna thar engemaw zat.
Hetiang chhinchhiahna i hmuh chuan rei lovah Doctor pan rawh.
Thil hriat belh tur tam zawk...
Damdawi lam natna khirh tak nei fa neih chu chhungkaw eng tan pawh thil harsa tak a ni thei. Mahse, nangmah chauh i ni lo tih hre reng ang che. I fate medical team-a mi tu pawh biak la, i mamawh ṭanpuina i hmuh theih dan tur zawt rawh. Online-ah pawh damdawi lam website rintlak tak takah (e.g., World Health Organization website, damdawi in hmingthang website-ah) thu belhchian dawl zawk leh puihna i hmu thei bawk. Amaherawhchu, Internet-a thu hmuh chhuah zawng zawng hi a dik vek lo a, chuvangin doctor nena inbiakna neih a pawimawh a, chu chu a dik leh dik loh finfiah a pawimawh hle.
Hriat reng tur pawimawh ber berte (Take-Home Message) .
Okay, chuti a nih chuan, vawiin a kan sawiho atang hian `(Neutropenia)` hi hriatthiamna tha zawk in neih ka beisei.
Neutropenia chu thisenah thisen var neutrophils an tih tlem a ni. Hei hian natna hrik kai awlsam zawkin a siam thei che a ni.
A chhan tam tak a awm thei a, a chang chuan chhan pawh i hmu thei lo mai thei.
Thisen test hmanga diagnosis tih a ni.
Enkawlna chu a chhan leh a nasat danah a innghat. Mi zawng zawng hian enkawlna an mamawh vek lo.
A pawimawh ber chu hri kai chhinchhiahna fimkhur a, i hriat chuan damdawi lam thurawn la nghal a ni.
Damdawi lam thurawn dik tak zawm a, hri kai laka invenna hmanrua i hman chuan i fa chu i humhim thei a ni.
I fa chu dam thuai turin duhsakna hlanin! He thu hi in tan a tangkai ngei ka beisei.
` Neutropenia, neutropenia, thisen var zat tlem, naupang natna, hri kai, ANC, thisen natna, immunodeficiency











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