Heng thilte hi i chungah a thleng ngai em? Chanchinbu i chhiar hian lehkhate chu a inzawm khawm ang maiin a lang a, a nih loh leh mi i hriat chian em em i hmuh chuan rang takin i hre thei lo. A nih loh leh in lama kawngkhar, dawhkan, leh ṭhutphah i tawk fo em? I hmu tha thei a, mahse thil awm danah thil mak tak i nei a, chutih rual chuan hlauhna emaw, lungkhamna emaw tlem i neih chuan tunlaia kan sawi tak `(Posterior Cortical Atrophy)` tih hi i hriat chian a pawimawh hle.
Posterior Cortical Atrophy (PCA) hi eng nge ni?
A awlsam zawngin, `(Posterior Cortical Atrophy)` emaw `(PCA)` emaw hi kan thluak nena inzawm natna zual zel, leh a tlem deuh hlek a ni. Hei hi `(neurodegenerative disorder) kan ti a ni.` Heta thil thleng hi kan thluak hnunglam cortex, chu chu `(posterior cerebral cortex)` a bik takin kan thil hmuh hriatthiam leh thlirletna tura min puitu part-a thluak cell, ` (neurons),` te chu a chhe zauh zauh a ni. He thluak peng hian kan `(parietal lobes)` leh `(occipital lobes)` te a huam a ni. Heng cell te tihchhiat avang hian chu thluak hmun chu a lo tlem zauh zauh thin. Hei hi `(atrophy) .` kan ti bawk
A pawimawh ber chu, hei hi mit hmuh lohna a ni lo. Mit hian thluak lam pan a, thluak pawhin ‘hei hi ka hmuh chu a ni’ tia a hriatthiamna kawngah harsatna a ni. Camera tha tak hmanga thlalak lak ang mai a ni a, mahse chu thlalak entu computer processor a chhiat chuan thlalak chu a lang dik lo.
Hei hi eng symptoms nge ni?
Heng symptoms te hi kum 50 leh 60 inkar atanga tan a ni tlangpui a, mit hmuhna lama harsatna nei hi a tam ber. Eng nge an nih i han thlir teh ang.
1. Chhiar harsa: 1.1.
Chanchinbu emaw, hetiang lehkhabu emaw i chhiar angin han mitthla teh. Tichuan, rang takin lehkhabute chu pakhat chungah pakhatin a kal ang maiin i hria mai thei a, line-te chu a hnung leh hnung lamah a zuang chhuak ang maiin i inhria mai thei . Mi thenkhat chuan thumal leh hawrawpte chu a inzawm tlat a, a inzawm tlat niin an hria. Mi dangte chuan, ‘Aw doctor, chhiar ka tum hian lehkhabu chu phek a\angin a tla thla ang maiin ka hria’ an ti. Hei hian i thil chhiar chu hriatthiam a har a, i chhiar chhunzawm thei lo bawk.
2. Hmun hlat zawng hriat theih lohna:
Hei pawh hi mi tam tak rilrua buaina lo lang thin a ni. Entîr nân, step-te chu eng chen nge a inhlat tih chiang taka an hriat loh avângin stairs-a chho emaw, chhuk emaw chu an hlau mai thei. A nih loh leh, curb lam an pan chuan tire leh curb inkar hlat zawng an hre thei lo. Mi thenkhat chuan engtikah nge ke pen tur tih leh khawiah nge an pen dawn tih an hriat theih loh avangin escalator-a chhoh an hlau bawk.
3. Hmasawnna tur hriatthiam harsa: 1.1.
‘Dinglam hawi’ emaw, veilamah kal’ tih ang chi kawng awlsam tak hrilh che pawh ni se, chu chu hriatthiam leh tih a harsa thei hle. Eng nge dik leh eng nge vei tih i hre thei lo ang maiin i inhria nghal a .
4. Hmêl, thil leh hmun hriat theih lohna:
Hei hi a pawi deuhin a lang thei a, mahse a tir lamah chuan a thleng thei. I hriat chian tak tak i hmu a nih pawhin, ‘Aw... hei hi tu nge ni?’ tih hi i hre nghal thei lo. A châng chuan thil hriat lar tak hriat theih nân hun rei tak a ngai a, chu chu in lama i neih tawh thil pawh ni se. A châng chuan i awmna hmun pawh hian mak tak maiin i hre nghal thei.
5. Kawngkhar leh furniture-a bang:
Chiang taka hmu thei mah la, i hmaa kawngkhar, dawhkan, leh ṭhutphah ang chi thilte chu a awmna hmun dik tak i hriat theih loh avangin i tawk fo mai thei. ‘Engvangin nge engkim ka tawk?’ tih hi i ngaihtuah mai thei.
6. Number hmanga hnathawh harsatna:
I ṭhian ṭha ber phone number chu i zir chhuak ang tih han ngaihtuah teh. Mahse phone i pick up a, dial i tum chuan phone-a digit awmte chu i hmu thei lo. Digit te chu i hmu thei a, mahse i thluak chuan a man thei lo niin a lang.
7. Appliances leh switch hman harsatna:
Blender emaw rice cooker ang chi inchhung bungrua-a ‘on/off’ switch awmna hmun chu ‘hmu’ thei mah la, i thluak hian a awmna dik tak a hriat theih loh avangin hman a harsa thei hle.
8. A chhan awm lova lungkhamna:
Heng thilte bakah hian PCA vei te hian an naupan lai atang tawhin sawifiah theih loh khawpa lungkhamna leh lungkhamna an nei thei bawk. Zirchiangtu thenkhat chuan he natna hian kan hriatna, rilru leh ngaihtuahna inzawmkhawmtu thluak network a nghawng a, chu chuan he lungkhamna hi a thlen niin an ngai. Theory dang pakhat chu miten thil dik lo nia an hriat a, mahse thumal hmanga sawi theih loh avangin lungkhamna an nei tih hi a ni. Mahse, he lungkhamna danglam tak hi doctor-te’n PCA an hmuhchhuah huna an ngaihtuah thin symptom a ni bawk.
Hei hian eng harsatna nge a thlen theih?
PCA hi natna zual zel a nih avangin a tir lama a lan chhuah dan chu hun kal zelah a zual thei a, a lan chhuah dan thar a lo lang thei bawk. Harsatna lo awm thei lian ber berte chu hetiang hi a ni:
- Functional blindness: Mit tha tak ni mahse thluak hian thil hmuh chu a hrilhfiah thei lo va, chu mi chu mitdel ang maiin a siam a ni.
- Depression leh lungkhamna: Natna nen hian rilru lama harsatna a awm thei a, lungngaihna leh lungkhamna ang chi dinhmun a pung thei bawk.
- Tlu hlauhawmna a tipung: Hetiang dinhmun hian taksa balance a tichhe thei bawk a, chu chuan a tlu fo thin.
- In lama accident pung: Entirnan, stove control panel pan a, stove hmun lum tak khawih avanga i kut hal ang chi accident hi thluak hian i thil hmuh dik tak chu khawiah nge a awm tih a hriatthiam loh vang a ni thei.
Eng thilin nge hei hi a thlen?
PCA thlentu ber chu thluak tibuaitu neurodegenerative natna dang a awm vang a ni. PCA vei te hian Alzheimer natna emaw Lewy body dementia emaw an nei fo bawk.Natna pakhat an tih hi a awm a. Hengte hi a chhan tam ber a ni.
Mahse, a tlem hle a, damdawi lam thil dang pawhin PCA a thlen thei bawk. Chung zingah chuan:
- `(Creutzfeldt-Jakob natna)`
- `(Corticobasal tihchhiatna)`
PCA hi Alzheimer natna zinga mi a ni em?
Ni e, PCA hi a takah chuan Alzheimer natna chi khat anga ngaih theih a ni . Alzheimer natna kan ngaihtuah hian hriatrengna lama harsatna kan ngaihtuah hmasa ber thin. Amaherawhchu Alzheimer natna bul tan tirh lamah chuan thluak hmun dang, hriatrengna nena inzawm lote pawh a nghawng thei bawk. Doctor-te chuan heng dinhmunte hi Alzheimer natna atypical variant an ti a. Posterior Cortical Atrophy hi chutiang Alzheimer natna chi khat a ni.
He natna hi engtin nge an hriat chhuah?
Doctor-te chuan PCA dik taka hriat theih nan test eng emaw zat an nei a, heng symptoms te hi chhan dang avanga lo awm thei a nih avangin, paih chhuah a ngai a ni.
- Brain scan (MRI - magnetic resonance imaging): Hei hian hnunglam cerebral cortex-a atrophy awm leh awm loh a enfiah thei a ni.
- Mit enfiahna: Hei hi mit natna dang avanga lo awm a nih leh nih loh hriat nan a pawimawh hle.
- Neurological exam: Hei hian nervous system hnathawh dan a enfiah thin.
- Neuropsychological assessment: Hei hian thluak hnathawh hrang hrang, hriatrengna, ngaihtuahna, tawng thiamna, leh mit hmuhna te a test thin.
- `(PET scan - positron emission tomography scan)`: Hei hi thluak hnathawh leh Alzheimer natnaah inthlak danglamna a awm em tih hriat nan pawh hman theih a ni.
- Lumbar puncture / spinal tap: Hei hian thluak leh ruh chhunga tui awmte chu Alzheimer natna nena inzawm protein awm leh awm loh a test thin.
Hei hi eng enkawl dan nge ni ang?
Dik tak chuan PCA hi damdawi a la awm lo. Mahse, lungngai suh. Natna lan chhuah dan tur enkawl dan tur, natna zual zel tur tihkhawtlai nan leh nun awlsam zawka siam turin thil i tih theih a awm.
Doctor-te chuan he natna chhan bulpui ber, Alzheimer natna emaw Lewy body dementia emaw te hi an hre hmasa ber a ni. Tichuan, a hnuaia awm chu an enkawl ta a ni. US Food and Drug Administration-in a pawmpui damdawi a awm a, hei hian natna a zual zel tihziaawmna tur a pui a ni.
Mite chu natna lan chhuah dan nena nunpui tura puitu programme leh service hrang hrang a kawk bawk.
- Damdawi: 1.1.
- `(Donepezil)` (Donepezil) chuan a rawn ti a.
- `(Rivastigmine)` (Rivastigmine) tih a ni.
- `(Galantamine)` (Galantamine) tih a ni.
- `(Lecanemab)` (Lecanemab) tih a ni.
Hengte hi Alzheimer natna atana damdawi pek tlanglawn tak takte an ni.
Anxiety emaw depression ang chi condition i neih chuan chutiang tan chuan damdawi (anti-anxiety medication, antidepressants) pek i ni thei bawk.
- Enkawlna leh rawngbawlna dangte:
- Cognitive rehabilitation: Hriatrengna leh ngaihvenna ang chi thil tihchangtlunna tura puitu exercise leh technique te i zir thei.
- Occupational therapy: Hei hian coping strategies zir turin a pui che a, nitin hna i thawh theih nan i environment i siamrem thei bawk.
- Physical therapy: Hei hian balance leh kea kal ang chi thila pui thei exercise a pe a.
- Mental health counseling: He natna nena lo awm thin stress leh lungkhamna te hi enkawl nan counselling hi a pawimawh hle.
I hmangaih tak hian PCA a vei a nih chuan eng nge i beisei ang?
PCA hi hun kal zelah a na zual zel a ni. Chuvangin, i hmangaih tak symptoms chu zawi zawiin a zual zel i beisei thei ang. A tâwpah chuan, Alzheimer natna zual tak vei tawhte nêna inang tak tak an nei thei a ni. Hei hi hriat a lungchhiatthlak laiin, hmachhawn tur chuan kan inpeih a ngai a ni.
PCA vei dam rei zawng chu engzat nge ni ang?
PCA vei dam rei zawng hi a tlangpuiin Alzheimer natna vei dam rei zawng nen a inang hle. Alzheimer natna lan chhuah hmasak ber a nih hnuah mi tam zawk chu kum 10 atanga kum 12 vel an dam .
Mahse, hei hi hriat reng a pawimawh: Hei hi kaihhruaina tlangpui chauh a ni. Mi tin a inang lo thei. I dinhmun chu a danglam thei. Chuvang chuan doctor hnenah hemi chungchang hi zawt la a tha ber.
PCA vei ka hmangaih tak chu engtin nge ka enkawl ang?
I hmangaih tak hian PCA a vei a nih chuan enkawl hi mawhphurhna lian tak a ni a, hmangaihna nasa tak a mamawh a ni. An tih hmasak ber chu khawvel an hmuh dan hriatthiam tum hi a ni.
Ngaihtuah teh, dawhkan pakhatah a tlu lut a. Dawhkan a ‘hmu’ loh vang a ni lo. A mit chuan a thluak hnenah dawhkan chu a awm tih signal a thawn a, mahse thluak chuan a hrethiam tawk lo va, ‘Chutah chuan dawhkan a awm a, kawng i siam a ngai’ tiin a chhang let vang a ni.
Hetiang hun lai hian a chinfel dan pakhat chu room inkar kawngpui chu chiang taka dah hi a ni. Thil tul lo chu i paih chhuak thei a, a tlu theihna pawh i ti tlem thei bawk. Hei hi rawtna pakhat chauh a ni. I hmangaih tak enkawltu medical team chuan in leh hmun dangah him taka an awm theih nân leh, mahni inrintawkna neia an hna an thawh theih nân rawtna dang tam tak an pe ang che
- Dawhthei rawh: Thil hrethiam tur leh thil tihfel theih nan hun rei tak a mamawh thei a ni.
- Fiah takin thu sawi la, awlsam takin:Vawi khata thu tam lutuk sawi ai chuan thil pakhat sawi mai mai rawh.
- Environment him siam: Hmun hnim leh hnim hringte tihtlem. Zanah light on reng tur a ni.
- An rilru put hmang hrethiam rawh: Hei hi an tan pawh thil harsa tak a ni. An lungngaihna leh thinrimna hrethiam rawh.
- Nangmah pawh enkawl rawh: Hmangaih tak i enkawl dawnin mahni rilru leh taksa hriselna vawng reng a pawimawh hle.
Engtikah nge Doctor ka hmuh ang?
PCA symptoms hi hun kal zelah a na zual zel thin. Hetiang dinhmun hi i neih chuan i doctor nen thla leh kum lo awm turtea i beisei tur chungchang sawipui rawh.
Tin, i dinhmun a chhe zual zel tih hriat theihna tur symptom eng emaw zat zawt la, i hriat chuan doctor i biak tur em tih te zawt bawk ang che. Symptom thar i neih emaw, symptom awmsa chu a zual thut a nih chuan doctor thurawn la nghal rawh.
Doctor hnenah eng zawhna nge ka zawh ang?
PCA hi thil awm lo tak a nih avangin zawhna tam tak i nei mai thei. Doctor hnenah engkim zawh hlau suh. Entir nan:
- 'Doctor, engtin nge `(Posterior Cortical Atrophy)` ka nei tih chiang taka i hriat?'
- 'Eng thilin nge ka thluak hnathawh a tihdanglam chhan?'
- 'Tuna ka symptoms te hi engtin nge ka tih theih ang?'
- 'Heng symptoms tihziaawm thei damdawi a awm em?'
- 'He dinhmun hian engtin nge ka nitin nun a nghawng ang?'
- 'Thla engemaw zat, kum lo awm turah hian eng inthlak danglamna nge ka beisei ang?'
- 'Ka tan chuan hmalam hun atana ruahmanna siam dan tha ber chu eng nge ni?'
He thawnthu atang hian eng thuchah nge in lama kan hruai duh?
Posterior Cortical Atrophy (PCA) hi a harsa thei hle a, i nunah nghawng lian tak a nei thei bawk. I thluak in i thil hmuhte a process dan a inthlak danglam avangin nitin hna, lehkha chhiar te, number hmanga hnathawh te, leh hlat zawng tehna te tih a harsa thei a ni. Hei hian lungkhamna leh hlauhna nasa tak a thlen thei a ni. I hna chu nangmah chauhin i thawk thei dawn lo niin i inhria thei bawk.
Hetiang dinhmun hi damdawi awm lo mah se, nangmah chauhin i hmachhawn a ngai lo. I natna lan chhuah dan enkawl dan tur te, he nunphung thara insiamrem tur te, leh a theih ang anga rei tak mahni inrintawkna neia nung tur hian thil tam tak i tih theih a ni. PCA i neih chuan i healthcare team nen sawiho rawh. Anni chuan an ṭanpui che a, i mamawh thilte chu an pe che a, an hlim hle ang. I mamawh thlawpna leh fuihna nen chuan he zinkawng hi i zawh thei ang.
` Posterior Cortical Atrophy, PCA, Thluak Natna, Mit lama harsatna, Alzheimer’s, Dementia, Thluak lam natna











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