I mit lamah pawh hetiang harsatna hi i nei em? Retinoschisis dinhmun hi i zir dawn teh ang!

I mit chhunga retina, i mit screen ang maia kan hmuh lem siamtu chu rang takin layer hnih emaw a aia tam emaw-ah a inthen tih i hre ngai em? Chu chu thil mak tak ni mahse hriat tur pawimawh tak a ni. Hei hi Doctor ten `(Retinoschisis)` an tih chu a ni. Ngaihtuah buai suh, awlsam takin sawi ila.

Retinoschisis chu eng nge ni? A awlsam zawngin i hrethiam ang u.

A awlsam zawngin, `(Retinoschisis)` chu i mit chhunga retina chu layer hrang hranga a inthen hian a ni. A dik tak chuan layer hnih emaw a aia tam emaw-ah a inthen a. I hria em, kan retina hi membrane complex tak a ni. Light sensitive layer a nei a, `optic nerve` kaltlangin thluaka signal phur thei cell layer a nei bawk. Chuvangin, heng layer te hi hetianga an inthen hian i mit hmuhna a nghawng thei a ni. Lehkhabu phek chu glue-a inzawm lo leh inthen ang maiin han ngaihtuah teh. Heng inthenna te hi retina lai takah a awm thei a, mahse a tam zawk chu a sir lamah, chu chu `periphery`-ah a thleng thin.

Retinoschisis chi hrang hrangte chu engte nge ni?

Hetiang dinhmun, ``Retinoschisis'' hi a awm lo deuh. Mahse hei hi chi hnih lian tak a awm. Pakhat chu acquired a ni a , pakhat chu congenital a ni .

A hnu lama lo awm tan Retinoschisis (Acquired Retinoschisis) .

Hei hi `degenerative retinoschisis` an ti bawk. Chu chu kum upat ruala thil thleng, a chhe deuh deuh nena inzawm thil a ni tihna a ni. A tam zawkah chuan hei hi kum 50, 60, 70 vel ah hmuh a ni a, chuvang chuan mi thenkhat chuan `senile retinoschisis` an ti bawk. Mahse, a chang chuan naupang zawkte pawhin he natna hi an nei thei a ni.

Degenerative retinoschisis hi chi hnih a awm a. Pakhat chu typical type a ni a, pakhat chu bullous emaw reticular type emaw a ni. Bullous type-ah chuan retina-ah hian tui ang chi hnah te te a lo awm thin. A chi hnih hi thliar hran a harsa deuh. Mahse, bullous type hian retinal holes leh retinal detachment a nei tam zawk.

Myopic macular schisis chi dang a awm bawk . Myopic traction maculopathy emaw myopic foveoschisis emaw an ti bawk. Retina lairil, macula , an tihah a awm a, a bik takin macula lairil, fovea tia koh-ah a awm bawk. Myopia na tak emaw, mitdelna emaw nei te zingah a lang tam ber.

Pianpui atanga lo chhuak Retinoschisis

I hria em, pianpui thil kan sawi hian kan pian tirh atanga kan taksa chhunga thil awm tihna a ni. Hetiang chi `(Retinoschisis)` hi `juvenile X-linked retinoschisis` an ti a.Kum naupan lai, emaw, naupan lai atanga intan, X chromosome nena inzawm, natna a ni. Mit pahnih a nghawng fo thin.

He natna, `juvenile X-linked retinoschisis` hian mipa naupang a nghawng tam ber. An nu hian a gene hi an keng tel a, mahse a tam zawkah chuan nute hian he natna hi an nei lo.

Retinal Detachment leh Retinoschisis hi eng nge an danglamna?

Heng pahnih hi ri inang mahse, a danglamna tlem a awm. Ngaihtuah teh, retinal detachment chu retina chu a supporting tissue atanga a inthen vek a, a chhuak ta a ni. Wall atanga poster rawn chhuak ang mai a ni.

Retinoschisis hi retina detachment a ni lo va, retina chu layer hrang hranga inthen darh a ni zawk. Hetiang dinhmun hi a chang chuan hriat harsa tak a ni thei a, mit lam doctor tan pawh a harsa thei hle. Mahse, special test hmangin i doctor chuan eng nge a nih chiah tih a hriat theih nan a pui thei a ni.

A châng chuan heng dinhmun pahnih, `(Retinal detachment)` leh `(Retinoschisis)` te hi a rualin a thleng thei a ni. He risk hi a bik takin nau piang laia `(congenital)` type `(Retinoschisis)` i neih chuan a sang hle.

He natna hi Retinoschisis an tih hi engtiang chiahin nge a awm?

Zirchiangtute chuan pianpui natna `juvenile X-linked retinoschisis` hi mi 5,000 zinga pakhat emaw, mi 25,000 zinga pakhat emaw-ah a awm niin an sawi. Chu chu percentage hniam tak a ni.

Kum 40 chunglam zinga 4% velin Degenerative retinoschisis a vei nia chhut a ni a, zirchianna dang pakhatah chuan kum 50 chunglam zinga 1% leh 4% inkar velin a vei thei niin an sawi.

Retinoschisis natna lan chhuah dan chu engte nge ni? Nang pawhin hengte hi i nei em?

Mak tak mai chu a chang chuan he natna hi engmah chhinchhiahna awm lovin i nei thei thin . Mahse, symptom i neih chuan eng nge a nih i en ang.

Congenital `juvenile X-linked retinoschisis` i neih chuan heng ang symptoms hi i hmu thei ang:

• Mit chu hnar lam hawiin a lang (`crossed eyes` ang chi).
• Mit chu hmun khatah a awm lo va, a kal leh haw (nystagmus).
• Retinal tear awmna hmun azirin central emaw foveal vision emaw peripheral vision emaw a hloh thei.
• Distance vision lama harsatna (a tam zawkah chuan hla tak atanga thlir theihna).

Retinoschisis i neih chuan a hnuaia mite hi i tawk thei ang:

• Kawng lehlamah chiang taka hmuh theih loh (peripheral vision hloh).
• A châng chuan, symptoms a awm thei lo.

Mahse, i retinoschisis a nasat chuan, a nih loh leh retinal detachment a awm chuan, hetiang hian symptoms i nei thei a ni:

• Mit hmaa thil dum te te (`floaters`) lo inhnim pil hmuh leh êng rawn chhuak nghal (`flashers`) tawn.
• Thil inzawm leh tihdanglam (`distorted images`) hmuh.
• Retinal tear awmna hmun azirin central emaw peripheral vision emaw a hloh thei bawk.

Pawimawh: Heng symptoms te hi i neih chuan mit doctor pan nghal tur a ni. A chhan chu mit lama harsatna nei tan chuan enkawl hmasak a pawimawh hle a ni.

Engvangin nge Retinoschisis hi a lo awm? A chhante chu engte nge ni?

Congenital retinoschisis hi genetic mutation avanga lo awm a ni fo thin . X-linked a nih thu kan sawi tawh a, chu chu nu atanga rochun genes nen a inzawm tihna a ni.

Mahse, scientist-te chuan he natna hi a chhan dik tak an la hmu lo ``acquired retinoschisis.`` Mahse, kum upat rualin a vei theihna a sang chho zel tih hmuhchhuah a ni a, a bik takin kum 40 an tlin hnuah a ni.

Engtin nge Retinoschisis i vei tih chiang taka i hriat theih ang? (Diagnosis) tih a ni.

He natna hi mit lama mithiam (ophthalmologist) ten an hmuchhuak fo thin . Mit enfiahna uluk tak (mit enfiahna kimchang) hnuah a hnuaia test te hi tih theih a ni a, chu chu a natna hriat chian nan a ni:

• Ophthalmoscopy emaw fundoscopy: Hemiah hian doctor chuan hmanraw bik (ophthalmoscope) hmangin i mit chhung lam, a bik takin retina chu a enfiah thin.
• Optical Coherence Tomography (OCT): Hei hi non-invasive test a ni a, light hmangin i mit chhung leh hnunglam thlalak chiang tak a siam a ni. Retina layer te chu chiang takin a hmu thei a ni.
• B-scan ultrasonography: Hei hi non-invasive ultrasound test a ni bawk a, sound wave hmangin mit chhung lam thlalak a la thin.
• Electroretinography (ERG): He test hian i mitin êng a rawn chhuah nghal zat a chhan dan a teh a ni. Hei hian retina hnathawh dan tehna atan a pui thin.
• Angiography: He test hian i retina chhunga thisen kalna kawngte thlalak a la a. Dye bik fluorescein emaw indocyanine green emaw a hmang thin.
• Genetic testing: I doctor chuan pianpui natna, juvenile X-linked retinoschisis an tih i neih a rinhlelh chuan he test hi an rawt thei ang.

Retinoschisis hi eng enkawlna nge ni? Dam theih a ni em?

Dik tak chuan, dinhmun `(Retinoschisis)`A dam kim thei lo. Mahse, enkawl theih a ni. Doctor-te chuan i mit hmuhna tichak turin glasses emaw, mitdelna hmanrua dang emaw an rawt thei ang.

• Retinoschisis i neih chuan enkawlna engmah i mamawh lo mai thei. I doctor chuan hei hi benign condition, enkawl ngai loah a ngai mai thei. Mahse, refractive error, nearsightedness emaw farsightedness emaw i neih chuan glasses i mamawh mai thei.
• Congenital `juvenile X-linked retinoschisis` i neih chuan mit lama harsatna nei tan pawh glasses i hman a ngai dawn a ni.

A chang chuan mit chhunga thisen kalna kawngte chu a chhe thei a, mit chhungah thisen a chhuak thei bawk. Chutiang a nih chuan i doctor chuan thisen chhuah tihtawp nan cryoablation emaw laser therapy emaw a rawt thei ang.

A pawimawh ber chu retinal detachment i neih chuan retina reattach turin operation i mamawh ngei ang.

Researcher-te chuan juvenile X-linked retinoschisis enkawlna thar an la zawng mek a, chung zingah chuan gene therapy , stem-cell therapy , leh damdawi dorzolamide tih te pawh a tel.

Retinoschisis laka inven dan tur a awm em?

Vanduaithlak takin ``Retinoschisis'' lo awm tur hi ven theih a ni lo .

Acquired retinoschisis hi a chhan hriat a la ni lo va, chuvangin ven theih a ni lo. Mahse, i chhungkuaa mi tu emaw chuan juvenile X-linked retinoschisis a vei tawh a nih chuan, i doctor hnenah genetic counselor nena inbiakna chungchang zawh a tha.

Retinoschisis i neih chuan eng nge i beisei theih ang?

Kan sawi tawh ang khan he natna hi damdawi a awm lo. A châng chuan mitdelna nasa tak a thlen thei a, a châng chuan dân anga mitdel pawh a thlen thei bawk. Mahse, mi thenkhat chuan enkawlna engmah an mamawh lo mai thei. I dinhmun nasat dan leh chi hrang hrangah a innghat.

Retinoschisis ka neih chuan engtin nge ka in enkawl ang?

`(Retinoschisis)` i neih chuan thil pawimawh engemaw zat tih theih a awm a:

• Mit enfiah fo thin ang che. Hei hi a pawimawh ber a ni. I mit chu a hun takah enfiah tir rawh , i doctor-in a rawt angin.
• Mitdelna (low vision aids) hmang ang che.Tin, nitin hna awlsam zawka thawk thei tur adaptive technology chungchang pawh zir bawk ang che. Hei hi nang leh i fate tan he natna hi an neih chuan a pawimawh hle.
• I mit hmuh danah danglamna i hmuh chuan doctor hnenah hrilh nghal rawh. Hrilhfiahna tenau te pawh ngaihthah suh.

Mit tlemte pawh hloh chu a hlauhawm thei hle. Mahse, nangmah chauhin i enkawl vek a ngai lo tih hre reng ang che. I mit doctor nen inzawmna nei reng rawh. I medical team-te hnenah support group leh resource dangte zawt rawh. An service pek te hi hmang tangkai rawh. Zirna an pe thei che a, mi dangte hnena thil tawn inhrilhhriatna an pe thei che a, technical assistance an pe thei bawk.

Kan sawi tawh atanga i hriat reng tur pawimawh ber (Take-Home Message)

Okay, chuti a nih chuan, kan sawi tawh atang chuan hengte hi kan ngaihtuah tur pawimawh ber berte chu an ni:

• Retinoschisis hi retina chu layer-ah a inthen a, chu chuan mit hmuhna a tichhe thei a ni.
• Hei hi chi hnih a awm a, chungte chu kum lama inzawm leh pianpui (congenital) te an ni.
• Mi thenkhat chuan symptoms an nei lo mai thei , mahse thenkhat chuan mitdelna leh mit tichhe ang chi symptoms an nei thei bawk.
• Hei hi damdawi famkim awm lo mah se, enkawl theih a ni. Chumi atan chuan damdawi lam thurawn mumal leh test neih a pawimawh hle.
• Nangmah emaw i chhungte zinga tu emaw hian he natna hi i neih chuan mit doctor pan fo a, an thurawn zawm fo a pawimawh hle .
• I mit hmuh danah inthlak danglamna i hmuh chuan damdawi lam thurawn la nghal rawh. A hmaa hriatchhuah leh enkawl a nih chuan natna a zual zel loh nan a veng thei a ni.
• Nangmah chauh i ni lo, tanpuina dawn theihna hmun leh kawng hrang hrang a awm.

Chuvangin, he thu hi i tan a tangkai ngei ka beisei. I mit kha fimkhur rawh!

` Retinoschisis, retinal detachment, mit natna, mit hmuh lohna, mit hriselna, genetic natna, mit test