Nu i nih angin i naute piang thar chu kut zungtang pahnih emaw a aia tam emaw a inzawm tih i hriat chuan i lungkham deuh mai thei. He natna hi damdawi lamah chuan `(Syndactyly)` emaw Sinhala tawngin ``fingers stuck together'' tih mai mai emaw a ni. Hei hi naute piang thar zingah piansualna hmuh tur awm fo a ni. Chuvangin, hlauthawng lova kan hriat chian a pawimawh.
Syndactyly chu eng nge ni?
A awlsam zawngin ``(Syndactyly)`` chu naute kut emaw ke emaw kut zungtang pahnih emaw a aia tam emaw vun emaw, a chang chuan ruh emaw hmanga inzawm khawm, web ang chi a ni. Hei hi naute kut leh keah hmuh tur a awm fo a, an pian tirh atangin hmuhchhuah a ni fo bawk .
I doctor emaw, midwife emaw chuan i naute a pian veleh he natna hi a hmuchhuak nghal mai thei. I enkawl dan tur chu i naute ke ruh engzat nge fuse tih leh engzat nge fuse tih ah a innghat ang.
`(Syndactyly)` leh `(Polydactyly)` hi eng nge an danglamna?
Heng thu pahnih hi i hriat chuan thil inangah i ngai mai thei. Mahse, an pahnih inkarah hian danglamna tlem a awm.
- Syndactyly tih awmzia chu kut zungtangte chu kan sawi angin, kan inzawm khawm tihna a ni.
- Polydactyly tih awmzia chu naute hian an kut emaw ke emaw ah kut zungtang emaw ke ruh emaw extra a nei tihna a ni.
A châng chuan heng dinhmun pahnih hi a awm dun thei a, chu chu naute chu kut zungtang inzawmkhawm laiin kut zungtang dang neiin a piang thei tihna a ni. Hei hi ``Polysyndactyly'' an ti a.
Mahse a pawimawh ber chu heng natna pathumte hi a pian tirh atangin hriat theih vek a ni tlangpui a, a hun takah enkawl a nih chuan naute chungah hun rei tak nghawng nei lovin tihdam theih a ni
He dinhmun hian tute nge a nghawng ber?
He natna hi ``Syndactyly'' tia koh hi naute piang thar apiangah a awm thei a ni. Mahse, zirchianna thenkhatah chuan:
- He natna hi naute hmeichhia aiin naute mipa zingah a let hnih velin a tam zawk a ni .
- Hnam thenkhatah chuan a dang aiin tlemin hmuh a tam zawk.
I chhungkuaa mi tu emaw, i nu leh pa, i pi leh pu, i unaute emaw, hetiang taka kut zungtang inzawm khawm hmanga piang emaw, chhungkuaah hian genetic disorder a awm chuan i naute pawhin he natna hi a neih theihna chance a awm thei.
Mahse hre reng ang che, naute hian syndactyly a neih vang mai mai hian hmasawnna lama harsatna dang emaw natna dang emaw an nei hauh lo.
`(Syndactyly)` hi engtiang chiahin nge a awm?
Statistics atanga a lan dan chuan kum tin naute piang 2,000 zinga pakhat vel chuan syndactyly chi khat emaw an nei dawn a ni. Kut zungtang aiin ke ruh ah a tam zawk.
A tam zawkah chuan 50% velin he natna hi kut pahnih emaw ke pahnih emaw (bilaterally) ah hmuh a ni.
Hei hi nau piangsual zinga mi ni mah se, a pumpuiah chuan hengte hi a tlem hle. I naute hian he natna a neih chungchangah hian ngaihtuahna i neih chuan doctor nen inbiakna neih a tha ber.
Hetiang dinhmun hian ka naute taksa hi engtin nge a nghawng?
Naute kut zungtangte chu a inzawm khawm a, a bik takin kut zungtangte chu enkawl loh chuan naute tan chuan chu kut zungtang chu hman a harsa deuh thei a, a lo puitlin rualin nitin hna a thawk thei bawk. Ngaihtuah teh, kut zungtangte hi zalen taka an che thei lo a nih chuan thil chelh leh ziak ang chi thil a nghawng dawn a ni lawm ni?
Mahse a tam zawkah chuan `(Syndactyly)` natna hi naute kum khat vel a nih laiin enkawl a ni a, chu chu kum naupang takah tihna a ni . Chuvângin, naute chu a lo puitlin hunah chuan a nei tih pawh a hre lo mai thei. Tin, a kut leh ke hnathawh pawh a nghawng lo thei bawk.
Mahse, naute chu syndactyly nen hian genetic disorder dang emaw, piansualna dang emaw a vei tih hmuhchhuah a nih chuan, chutiang dinhmun chuan naute thanlenna leh thanlennaah hun rei tak chhung nghawng a nei thei a ni.
`(Syndactyly)` natna lan chhuah dan chu engte nge ni?
`(Syndactyly)` chhinchhiahna awmchhun chu naute a pian hian kut zungtang emaw ke ruh pahnih emaw a aia tam emaw a inzawm khawm a, hmuh theih a ni . Naute kut zungtang inzawmkhawm dan hi a `(Syndactyly)` chi hrang hrang a zirin a danglam thei.
`(Syndactyly)` tih chi hrang hrangte chu engte nge ni?
I doctor chuan i naute kut zungtang-a he natna hi sawina atan hian thumal thenkhat a hmang thei ang. I naute hian syndactyly chi a neih dan chu eng kut zungte nge a nghawng tih leh a kut zungtang engzat nge adhesion-a inrawlh tih ah a innghat.
- Simple syndactyly: Hei hian kut zungtang chu vun chauhvin a inzawm khawm tihna a ni , kut zungtang inkarah hian membrane te tak te awm ang maiin.
- Complex syndactyly: Hetiang a nih chuan vun bakah hian naute kut zungtangte hian ruh, nerve, leh thisen kalna kawngte pawh a inzawm khawm thei bawk . Hei hi simple syndactyly aiin a tlem zawk.
Chu bâkah, naute chu syndactyly kimchang emaw, tling lo emaw neiah dah a ni bawk.
- Complete syndactyly: Hei hian kut zungtang bul atanga nail thlengin kut zungtang te chu a inzawm khawm tihna a ni.
- Incomplete syndactyly: Hetah hian kut zungtang thenkhat chauh fuse , kut zungtang pum pui ni lovin.
Heng thute i hriat hian hlauthawng suh. Heng thumalte hi Doctor ten an hman thin thumal a ni. I naute hian eng type pawh nei se, doctor chuan a enkawl dan tur a hrilhfiah ang che.
`(Syndactyly)` awm chhante chu engte nge ni?
Syndactyly hi naute nu pum chhunga an lo thanglian laia an genes-a inthlak danglamna emaw, tihbuai emaw engemaw zat avanga lo awm a ni.Genes hi a awlsam zawngin sawi ila, nu leh pa atanga fate hnena pek chhuah biological blueprints a ni a, chu chuan taksa chhunga cell tinte chu an lo thang lian a, an thawk thei ang.
Naute lo thanglian zel angin heng genes te hi thil pakhatin a nghawng a nih chuan, chu chu tihbuai a awm chuan naute taksaah inthlak danglamna engemaw zat a thlen thei tihna a ni. Inthlâk danglamna ṭhenkhat chu kan hmuh ngai loh thilte pawh a ni. Mahse a chang chuan `(Syndactyly)` ang chi piansualna a thlen thei bawk.
Naute kut, ke leh kut hmasawnna control tu genes te a nghawng chuan syndactyly nei a piang thei a ni. Heng genes te hi genetic disorders , chutiang bawkin environmental factors (naupai laiin i emaw i chhehvela mi emaw chunga thil thleng) te pawhin a nghawng thei bawk.
Syndactyly thlen thei genetic natna lian ber ber thenkhat chu:
- `Down syndrome` tih a ni
- `Apert syndrome` tih a ni
- `Poland syndrome` tih a ni
`(Syndactyly)` hi dominant emaw recessive trait emaw a ni em?
Zirna hrang hrangah syndactyly hi genetic trait lian ber a ni tih hmuhchhuah a ni . Chumi awmzia chu nu leh pa zinga pakhatin a gene a neih chuan an fate pawhin he natna hi an nei tam zawk tihna a ni.
Engtin nge `(Syndactyly)` hi kan hriat theih ang?
I naute a pian veleh i doctor chuan syndactyly a nei tih a hmuchhuak nghal ang. A kut zungtang emaw ke ruh emaw fused eng pawh a zawng ang a, eng syndactyly nge a nih tih a hre chhuak ang.
`(Syndactyly)` tih hriat nan eng test nge hman thin?
A tlangpuiin `(Syndactyly) hriat theihna turin test bik a ngai lo.` Naute kut zungtang leh ke ruhte chu chiang takin a lang . Dik tak chuan, a châng chuan doctor chuan naute pian hma pawhin he natna hi a hre thei a, naupai laiin ``ultrasound`` test pawh a nei thei a ni .
Mahse, syndactyly enkawl hmain naute kut emaw ke emaw X-ray lak a ngai mai thei. Hei hian a chhunga ruhte chu engtin nge an inzawm tih chiang taka hriat theih nan a pui thei a ni.
Genetic testing neih a ni
I chhungkuaa mi pakhatin genetic condition a neih chuan genetic counseling hian genetic testing neih tur nge tih i rel thei ang. Hei hian harsatna hrang hrang a enfiah thei a, chung zingah chuan syndactyly thlentu genetic mutations te pawh a tel.
A tam zawkah chuan, genetic mutation carrier i nih chuan i fate hian genetic disease an nei dawn tihna a ni hauh lo. Genetic counselor chuan i risk chu a hrilhfiah thei a, i hriselna humhimna tur emaw, i fate hnena genetic problem thenkhat i thlen theihna tur tihtlem nan emaw eng step nge i tih theih tih a hrilh thei bawk.
Syndactyly hi engtin nge enkawl a nih?
Syndactyly hi kut zungtang inzawm khawm te chu surgery hmanga then hran a ni . Naute tam zawk chuan kum khat vel an nih laiin he surgery hi an nei thin .
Surgeon chuan naute kut zungtang inzawm (fused fingers) (leh ruh leh tissue dang inzawm khawm te pawh a then thei bawk). A tlangpuiin, skin graft , a nih loh leh naute taksa peng dang aṭanga lak chhuah vun chi khat chu kut zungtang inthen tawhte khuh nân an hmang ṭhin.
Operation hnuah i naute chuan kut zungtang emaw ke ruh emaw inthen tawhte thlawp turin splint emaw cast emaw a bun a ngai mai thei. Operation hnua an kut emaw ke emaw chakna leh hnathawh theihna tura pui turin physical therapy engemaw zat an mamawh thei bawk.
I doctor emaw surgeon emaw chuan i naute hian eng ang surgery nge a neih a ngai tih leh fused fingers te i then hnua i tih tur te chu a hrilhfiah vek ang che.
Syndactyly natna vei hi non-surgical treatment a ni
Naute ṭhenkhat, a bîk takin ke ruh-a syndactyly na lo tak neite chuan operation an mamawh ngai lo mai thei . Mahse hei hi i doctor-in thutlukna a siam tur a ni.
Kut zungtang hian zai ngai lo hi a tlem hle a, a chhan chu kut zungtang chetna tikhawtlai thei thil eng pawh hian naute kut pum hnathawh a nghawng a ni.
`(Syndactyly)` enkawlna atanga dam leh theih nan eng chen nge a duh?
Hei hi i naute hian eng ang surgery nge a neih tih ah a innghat tak zet a ni. A tlangpuiin syndactyly surgery atanga dam leh hun chhung hi a rei lo va, dam lehna pawh a rang hle . I doctor emaw surgeon emaw chuan i naute inthen hnua a kut emaw ke emaw enkawl dan tur a hrilh ang che.
Syndactyly hi a veng thei ang em?
Naupai laiin `(Syndactyly)` ang chi genetic condition lo awm tur hi kan veng thei lo . Mahse, `(Syndactyly)` leh genetic condition dangte chu environment factor thenkhat nen a inzawm tih hmuhchhuah a ni. Naupai lai hian hengte hi pumpelh a pawimawh:
- Zu in a in thin.
- Meizial zu emaw, zuk leh hmuam hman emaw.
- Dan loa ruihhlo hman.
Naupai laia ei leh in loh tur chungchang doctor nen sawiho rawh.
Ka naute hian `(Syndactyly)` a neih chuan eng nge ka beisei ang?
I naute chu an fused fingers then hran nan operation hnuah a dam kim theih beisei tur a ni . I naute hian syndactyly chi hrang hrang nei mahse, a siamthatna tur surgery hian an hmalam hun atana an thanlenna leh an thanlenna chu a nghawng dawn lo. Dik tak chuan, surgery hian kut zungtang inzawm (fused fingers) neia piang hian hun rei tak chhunga nghawng a neih loh nan an thang tha hle ang.
Mahse, i naute syndactyly hi piansualna emaw, genetic condition dang emaw avanga lo awm (a nih loh leh a vei tih hmuhchhuah a nih chuan) i naute hian enkawlna emaw enkawlna chi hrang hrang a mamawh thei a ni. Hemi chungchang hi i doctor nen sawiho rawh.
Engtik hunah nge ka doctor ka hmuh ang?
I naute zai zawhah an kut emaw keah emaw danglamna i hmuh chuan Doctor pan rawh. A bik takin i naute kut zungtang inthen te hian heng symptoms te hi a neih chuan doctor pan nghal rawh:
- Thisen chhuak
- A rawng a inthlak (e.g. a sen, a dum) .
- Vung
- Fluid chhuah emaw, leak emaw
- I naute chu a na ang tih a hriat chuan
Doctor hnenah eng zawhna nge ka zawh ang?
Hetiang thil hriat hian zawhna tam tak a siam thei che a ni. I doctor hnenah heng thilte hi zawh theihnghilh suh:
- Ka naute hian eng chi syndactyly nge a neih?
- Genetic condition dang a nei em?
- Engtikah nge i naute kut zungtang i then ang?
- Surgery zawhah engtin nge a kut/ke chu ka enkawl ang?
Take-Home Thuchah a ni
I naute hian piansualna a nei tih hriat chu thil mak tak a ni thei. A tam hle mai. Mahse syndactyly hi, thil buaithlak takah pawh, enkawl theih a ni . I naute chu a kut zungtang leh ke ruh thliar hrang tura operation hnuah a dam thuai ang a, nakin lawkah a kut leh ke hman theihna a nghawng dawn lo. Dik tak chuan he enkawlna hian hun rei tak chhunga nghawng tha lo nei lovin an thang lian thei a, an thanglian tha thei bawk.
I doctor nen genetic conditions chungchang sawi la, test neih a ngai em tih zawt rawh. I naute pian hmaa i hriat tur thil hrang hrangah an pui thei che a ni. A pawimawh ber chu hlauthawng lo tur leh doctor thupek zawm hi a ni.
` Syndactyly, kut zungtang fusion, piansualna, naute hriselna, surgery, genetic natna, ke leh ke leh ke thanna











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