I fa tê tê chu a ke leh a hnungzang-ah rawng te te, sen hring hring a lo awm thut chuan i hlau tawh em? Pum na leh ruh natna an complain pawh a ni thei. Nu leh pa tu pawhin hetiang thil an hmuh hian an buaipui hi thil pangngai tak a ni. Mahse a tam zawkah chuan a serious lo . Heng symptoms te hi Henoch-Schönlein Purpura (HSP) tih hming pu, tuna IgA Vasculitis an tih ang chi natna avanga lo awm thei a ni. A awlsam zawngin sawi ila.
A awlsam zawngin, Henoch-Schönlein Purpura (HSP) hi eng nge ni?
Henoch-Schönlein Purpura (HSP) hi, damdawi lam atanga thlir chuan ``Vasculitis.`` chi khat a ni.Vasculitis chu kan taksa chhunga thisen kalna kawng, thisen phur tube te tak te ang maia awmte chu a chhung atanga a lo hring chhuak thin hi a ni. Kan vun a hliam a a hring ang bawkin thisen kalna kawng chhungah pawh a hring chhuak thin.
HSP-ah chuan he hliam hi vun hnuaia thisen kalna kawng te tak te, te tak teah a awm ber a ni. Mahse, a châng chuan he nghawng hi kal, intestines leh joint-a thisen kalna kawngah pawh a thleng thei bawk.
Hei hi a chhan chu kan taksa immune system (chu chu natna laka min vengtu system)-a tel, `(Immunoglobulin A)` emaw `(IgA)` emaw tia koh protein (antibody) bik chu thisen kalna kawngah a awm khawm vang a ni. Hetianga `(IgA)` a pung khawm chuan thisen kalna kawng a chhe a, a puak a, vun hnuaiah thisen tlem a leak thin. Chuvang chuan pawn lamah purple leh red spot kan hmu thin. Hriselna te tak te ang maiin.
Hetiang dinhmun hi `(IgA) Vasculitis` an ti bawk a, a chhan chu `(IgA)` antibody a inrawlh vang a ni. Kum eng pawha lo awm thei mah se, naupangte zingah a lang tam ber .
A pawimawh ber chu HSP hi a tlangpuiin natna khirh tak a ni lo. Naupang tam zawk hi enkawl ngai lovin an dam vek. Mahse, puitlingah chuan a na zawk thei.
Eng symptoms nge kan hmuh?
HSP symptoms hian naupang vun, ruhkawr, intestine, leh kidney te a nghawng ber a ni. A lan chhuah dan langsar leh langsar ber chu vunah purple-red spot lo lang hi a ni. Heng symptoms te hi a hranin han en ila.
| Symptom a ni | Hrilhfiahna |
|---|---|
| Vun a hring chhuak | Hei hi a symptom ber a ni. Vun chung lamah hian a sen emaw, a sen emaw a siam a, chu chu vun chung lamah a sang deuh hlek a ni. A chang chuan spot tlemte chauh a awm a, a chang chuan a tam thei bawk. Hengte hi a tlangpuiin itchy emaw na emaw an ni lo . Naupang ke leh a hnuteah an hmu tam ber . |
| Joint na leh a hring | Joints, a bik takin khup leh ke ruhte chu a lo hring a, a na bawk. Naupangin kal a harsat phah thei bawk. |
| Pum a na | Pum natna a lo thleng thei a, a kal lo thei bawk. Naupang thenkhat chuan luak chhuak leh luak chhuak an nei thei bawk. |
| Thil dang pawh a awm | A tlem hle a, ek chhungah thisen emaw, zun chhunga thisen (red/brown urine) emaw hmuh tur a awm thei. Hengte hi kal emaw, intestinal lama harsatna nei chhinchhiahna a ni thei. |
Engvangin nge hetiang hi a lo awm? A chhan engte nge ni?
HSP hi autoimmune natna a ni a . A awlsam zawngin kan taksa "sipai" (immune system) hian tihsualin a thisen kalna hrisel tak takte chu a rawn bei tan ta a ni. Hetiang thil a thlen chhan hi zirchiangtute chuan an la hre chiang lo.
Mahse thil pakhat a chiang a ni: HSP vei naupang 50% vel chuan heng symptoms lo lang hma ni engemaw zat chhungin upper respiratory infection, rilru na emaw, khawsik emaw an nei tawh a ni
HSP tichhuak thei thil dang (Triggers) .
A châng chuan HSP hi immune system-in a chhanna dik lo angin a lo awm thei bawk a:
- Bacteria infection, entirnan strep throat.
- Viral natna hrik kai te.
- Chaw thenkhat.
- Insect te hian an seh thin.
- Damdawi thenkhat.
- Vaccine chi thenkhat (hei hi a tlem hle).
He natna hi tuin nge vei tam ber?
IgA vasculitis hi kum eng pawhah a awm thei a, mahse naupang kum 3 leh 10 inkar ah hian 90% aia tam an awm tih hmuhchhuah a ni .
Risk factor dangte chu:
- Chhungkaw chanchin: 1.1.I chhungkuaa mi pakhatin HSP a lo vei tawh a nih chuan i fa pawhin a vei theihna chance a sang deuh hlek a ni.
- Genetic influence: He natna hi Europe leh Asian hnam chhuak zingah a awm fo tih hmuhchhuah a ni.
HSP vang hian harsatna a awm thei em?
Mi tam zawk chu thla khat emaw thla thum chhungin engmah enkawl ngai lovin an dam vek. A châng chuan natna hi a lo lang leh thei a, mahse chu pawh chu a mah chauhin a reh fo ṭhin.
Mahse, a tlem hle, a bik takin puitling zingah chuan HSP hi a nasat phah thei a, harsatna a thlen thei bawk.
- Kal chhiatna: Hun rei tak chhung kal natna a awm thei. Hei hi HSP-a fimkhur tur complication ber a ni.
- Intestine-a thisen chhuak.
- Intestine chhia emaw block emaw.
- Naupai laiin thisen sang (hmeichhia tan).
Engtin nge hei hi i hmuh theih, Doctor?
I fa chu naupang enkawltu hnena i hruai dawn chuan uluk takin i fa chu a enfiah hmasa ang a, a bik takin vun natna leh ruh hring eng emaw zat a enfiah hmasa ang. Tichuan, i fate natna lan chhuah dan leh tun hnaia natna i neih apiang an zawt ang che.
Diagnosis finfiah tur leh damdawi lam dinhmun dang tihbo nan doctor chuan test thenkhat a ti thei ang.
- Urinalysis: Kal (kidney) a nghawng tawh em tih hriat nan zun chu thisen emaw protein emaw a awm leh awm loh enfiah thin a ni.
- Thisen test: Infection emaw taksaa harsatna dang a awm leh awm loh enfiah nan.
- Kidney ultrasound: Kal dinhmun enfiah thin ang che.
- Abdominal ultrasound: Pum na chhan zawng chhuak rawh.
- Skin biopsy: A then phei chuan vun te tak te tak te chu mole awmna hmun atang hian lakchhuah a ni a, enfiahin a natna hriat chian a ni.
- Kidney biopsy: Kal chhiatna nasa tak a awm nia rinhlelhna a awm chauhvin test tih a ni.
HSP enkawlna tur engte nge ni?
A tam zawkah chuan HSP hian enkawlna bik a mamawh lo. A pawimawh ber chu in lama symptoms enkawl hi a ni.
Joint na leh swelling atan chuan doctor-in a tih angin paracetamol (Tylenol®) emaw NSAID pain reliever (Advil®) emaw i ei thei bawk.
Mahse, pum na ang chi symptoms a nasat chuan doctor chuan steroid damdawi prednisone ang chi a pe thei a ni. Vun rawng leh natna dang a awm reng chuan i fa doctor pan ngei ngei tur a ni.
HSP hi natna na lo tak a ni fo thin tih hre reng ang che, a mah chauhin a reh thei. Mahse a tlem berah chuan harsatna lian tak tak a thlen thei a, chu chu kal leh intestinal lama harsatna a thlen thei a ni. Chuvangin naupang thenkhat chuan an taksa hriselna (immune system) tha taka a thawh theih nan damdawi an ei a ngai mai thei. Heng damdawi te leh an side effect te hi i doctor nen sawiho rawh.
Engtikah nge Doctor kan hmuh ang?
I fain heng symptoms a neih veleh doctor pan vat a tha ber. Tin, enkawl lai emaw, natna a dam lai emawa a hnuaia symptoms te hi a lo lang a nih chuan doctor pan leh tur a ni.
| Damdawi lam thurawn lak nghal tur | |
|---|---|
| 1. 1. A rilru a hah lutuk chuan a rilru a buai em em a. | Thil danglam tak a awm chuan. |
| 2. 2. A rilru a hah lutuk chuan a rilru a buai em em a. | Naupang chu tuar theih loh khawpa natna emaw, nuam lo emaw a nih chuan. |
| 3. A rilru a hah lutuk chuan a rilru a buai em em a. | Kar 12 aia rei symptoms a awm chuan. |
| 4. 4. A rilru a hah lutuk chuan a rilru a buai em em a. | Symptoms a lo tha a, a lo lang leh a nih chuan. |
| 5. A rilru a hah lutuk. | Nitin a natna lan chhuah dan a na zual zel a nih chuan, a dam lehzual ai chuan. |
HSP hi dam chhung zawnga awm tur a ni lo. Thla khat emaw thla thum emaw chhungin a reh tlangpui. Naupang thenkhat chuan second episode an nei thei a, mahse a symptoms hi a na lo zawk tlangpui.
A tawp berah chuan HSP hian i fa chu a ti na thei a, a ti hrehawm thei bawk. Nu leh pate tan chuan an fa hrehawm lai hmuh a harsa thei hle. Mahse, naupang tam zawk chu hun rei tak chhunga harsatna awm lovin an dam vek tih hre reng ang che.Doctor chuan naupang chu a kal dinhmun enfiah turin hun engemaw chen a enkawl a ngai mai thei. Hei hi a pawimawh hle.
Take-Home Thuchah a ni
- Henoch-Schönlein Purpura (HSP) hi vun hnuaia thisen kalna kawng te te a lo hring chhuak a, ke leh hnuteah hian purple-red spot a awm thin.
- Hei hi naupangte zingah hmuh tur a tam ber a, a tlangpuiin natna khirh tak a ni lo.
- Hei nen hian ruh natna leh pum na ang chi symptoms te pawh a awm thei bawk.
- Naupang tam zawk chu thla 1-3 chhungin enkawlna bik nei lovin an dam vek.
- I fa vunah heng hmunte hi i hmuh chuan doctor pan vat a pawimawh hle a, kal (kidney) a nghawng tlem avangin.
- Doctor thupek zawm a, checkup neih reng a pawimawh.











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