I rilru a buai ang maiin, i ruhkawr a na ang maiin, i vun chu a hring emaw, a hring emaw chi hrang hrang a awm ang maiin i inhriat ngai em? Heng thilte hi thil pangngai anga ngaihin kan theihnghilh fo thin. Mahse, a châng chuan heng chhinchhiahna tenau tak takte hnuaiah hian kan hriat ngai loh natna khirh zawk a awm thei a ni. Vawiin hian chutiang natna pakhat, Vasculitis , chungchang kan sawi dawn a ni. He hming hi i tan chuan thil thar a ni mai thei. Mahse hei hi hriat chian a pawimawh hle.
Vasculitis hi eng nge ni? A awlsam zawngin i hrethiam ang u.
A awlsam zawngin, Vasculitis chu i thisen kalna kawng, chu chu thisen kalna kawng a inflammation emaw swelling emaw a ni . Tunah chuan heng thisen kalna kawngte hi eng nge ni tih i ngaihtuah mai thei. Chu chu tlem han sawifiah ila.
Kan taksaa thisen kalna kawng (blood vessel system) hi Sri Lanka ram pum huapa kawngpui network angin han ngaihtuah teh. Heng kawngte hian kan taksa cell tinah oxygen leh nutrients a phur a. He kawngpui network hi chi thum a awm a, chungte chu:
- Arteries: Hengte hi main highway ang mai a ni. Heng thisen kalna lian tak takte hian thinlung atanga thisen thianghlim taksa pum puiah an phur a.
- Veins: Hengte hi thisen hman tawh, chu chu thisen bawlhhlawh, thinlunga hruai kir lehtu kawngte an ni.
- Capillaries: Hengte hi kawngpui lian leh kawngpui dang inzawmkhawmna byway te te an ni. Taksa chhunga cell tin hian heng thisen kalna kawng te tak te hmang hian thisen atang hian nutrients an dawng vek a.
Tunah chuan i hrethiam em? Vasculitis hian thisen kalna kawng network a nghawng a. He natna hi a lo awm chuan thisen kalna bangte chu a lo hring a, a thim bawk. Kawngpui chu a zim a, lirthei tan a harsat ang bawkin, heng thisen kalna kawng zim tak tak kal tlang hian thisen kal a harsa ta hle a ni.
Hetianga thisen kal dan a tihbuai chuan chu thisen kalna kawng (entir nan, kal, lung, vun) te chawmtu taksa peng te chu a chhe tan thin. A châng chuan thisen kalna kawng bangte chu a chak lo thei a, balloon ang maiin a bulh thei bawk. Hei hi aneurysm kan ti a . Condition hlauhawm tak a ni.
Mi tam tak chuan damdawi hmangin heng symptoms te hi an control thei a ni. Mahse, taksa peng pawimawh tak takte thisen kal chu tihtawp a nih chuan hei hi nunna atana hlauhawm tak a ni thei .
Khawiah nge vasculitis hian taksa a nghawng?
Dik tak chuan taksa peng eng pawh thisen kalna kawng nei te chu a nghawng thei a ni. Chumi awmzia chu lu atanga ke thlengin taksa peng eng pawh a nghawng thei tihna a ni.
Hengte hi nghawng a neih theihna hmunpui thenkhat chu hetiang hi a ni:
- Vun
- Chuap
- Thinlung
- Nerves a awm
- Mit
- Kidney a ni
- Thluak
- Sinus a awm
- Pum leh Intestines (Stomach) .
- Kut leh ke
Vasculitis natna lan chhuah dan tlangpui chu engte nge ni?
He natna lan chhuah dan hi mi hrang hrangah a inang lo thei hle. Thisen kalna kawngte hian eng organ nge a nghawng tih leh engtiang chiahin nge a inflammation nasat tih ah a innghat. Entirnan, mi pakhatin an vunah thisen kalna kawng a nghawng a nih chuan a vunah vun rawng leh sen hring a awm thei. Mi dangin kal natna an neih chuan an zun-ah thisen a awm thei.
Mahse, he natna chi hrang hrang ni lo, symptoms tlanglawn thenkhat a awm. Heng symptoms engemaw zat hi in tawn dun a nih chuan doctor pan ngei ngei tur a ni.
| Symptom a ni | A awlsam zawngin... |
|---|---|
| Thiltih dan tlangpui | Khawsik, hahna, taksa rihna tlahniam, taksa na. |
| Vun nena inzawm natna lan chhuah dan | Vunah sen emaw, sen emaw, eczema, leh hliam pawh a awm thei. |
| Nerve nena inzawm natna lan chhuah dan | Numbness, tingling, taksa peng hrang hranga chak lohna. |
| Respiratory system nena inzawm natna lan chhuah dan | Thâwk harsa, khuh (thisen nen pawh a ni thei). |
| Kidney nena inzawm symptoms te | Zun thim, zun chhunga thisen. |
| Thil dang pawh a awm | Thil awmdan hrang hrang, ruh natna, pum na, leh stroke te. |
Engvangin nge he Vasculitis hi a lo awm?
Hei hi zawhna buaithlak deuh a ni. Vasculitis hi autoimmune natna a ni a . Hei hian eng nge a awmzia?
Kan taksa hian defence system fing tak a nei a. Immune system kan ti a. A hna chu taksaa lut natna hrik (virus, bacteria) do a, natna laka min humhim hi a ni. Mahse, autoimmune disease-ah chuan he defense system hi a dik lo a, ramdang invader ni lovin kan cell hrisel tak takte chu a bei tan ta a ni.
Vasculitis-ah chuan i immune system hian nangmah ngeiin i thisen kalna kawng a bei thin . Scientist-te chuan hetiang thil hi a thlen chhan chiang takin an la hre lo.
Mahse, thil engemaw tak chuan he natna hi a thlen thei tih hmuhchhuah a ni.
- Infection: He natna hi virus emaw bacteria emaw infection thenkhat hnuah a awm thei.
- Autoimmune natna dang: Autoimmune natna dang, rheumatoid arthritis ang chi i neih tawh chuan vasculitis i vei theihna a sang zawk.
- Damdawi thenkhat: A tam lo hle a, hei hi damdawi thenkhat avanga thil thleng angin a thleng thei bawk.
- Cancer chi thenkhat: Hetiang dinhmun hi thisen cancer ang chi thil vang pawh a ni thei.
He natna chi hrang hrang a awm em?
Ni e, hei hi chi 30 chuang a awm. Thisen kalna kawng (liar, medium, small) leh an awmna hmun a zirin an thliar hrang ber a ni. Heng chi hrang hrang hi sawi ta ila, nang leh kei hi kan bo vek ang. Chuvangin chi hrang hrang sawiho zinga tlemte hming chauh han sawi ila.
- ANCA-associated vasculitis: Hei hian subtype engemaw zat a nei a.
- Giant cell arteritis: Hei hi kum 50 chunglamte vei tam ber a ni a, lu leh kawr chhunga thisen kalna kawng lian tak takte a nghawng nasa ber a ni.
- Takayasu arteritis: Hei hi arteries lian tak tak tuar thei chi a ni bawk.
- Polyarteritis nodosa natna (polyarteritis) a ni
- Kawasaki natna: Hei hi naupang tê tête zingah a awm tam ber chi a ni.
- IgA vasculitis (Henoch-Schönlein purpura): Hei hi naupang zingah pawh a hluar hle.
Heng hmingte hi i hriat reng a ngai lo. A pawimawh ber chu doctor-in eng chi nge i neih tih chiang taka a hriat chian a ngai a, a chhan chu chutiang chiah chuan enkawl dan tur a innghat dawn a ni.
He natna hi engtin nge doctor hian a hriat theih ang?
Vasculitis hmuhchhuah hi a harsa deuh thei a, a chhan chu a natna lan chhuah dan hi natna dang tam tak nen a inang a ni. Chuvangin doctor chuan vasculitis a ti nghal mai lovang.
Doctor i pan hunah i natna lan chhuah dan a ngaithla hmasa ang a, a chanchin a hre hmasa ang. Tichuan i taksa chu a enfiah ang. Hei bakah hian a natna hmuhchhuah a nih leh nih loh finfiah nan test eng emaw zat a ti dawn bawk.
- Thisen test: Hengte hian taksaa inflammation awm leh awm loh (ESR, CRP ang test), leh ANCA ang chi antibody bik awm leh awm loh enfiah nan a pui thin.
- Zun test: Hengte hian kal (kidney) a nghawng em tih hriat theih nan a pui thei a ni.
- Biopsy: Hei hi natna finfiah dan tha ber a ni. Hei hian taksa peng (e.g. vun, kal) atanga tissue te tak te tak tak lak a, microscope hmanga enfiah a ni.
- Angiogram: Hei hi X-ray ang chi test bik a ni a, i thisen kalna kawng chhung lam a en thin. I thisen kalna kawng a zim emaw, a hring emaw a enfiah thei.
Heng test i neih zawh hian hetiang ang natna hrik (inflammatory diseases) lama tui doctor, rheumatologist .
Vasculitis enkawlna tur engte nge ni?
Vasculitis enkawlna kawngah hian tum lian tak pahnih a awm a.
1. Inflammation control dan.
2. Immune system hnathawh that lohna tihtawp.
Hemi atan hian damdawi hman a ni ber.
- Corticosteroids: Hei hi damdawi chak tak a ni a, inflammation a control nghal vat a ni. He class-a damdawi hman tam ber chu Prednisolone a ni.
- Immunosuppressants: Heng damdawi te hian immune system hnathawh a control a, chu chuan taksa a bei sual a ni.
He enkawlna dan hi i doctor-in i dinhmun chi leh nasat dan a zirin a ruat ang. A châng chuan thisen kalna kawngah chhiatna nasa tak a awm chuan siam ṭhat nân operation neih a ngai mai thei.
A pawimawh ber chu Doctor-in damdawi a pek, a dose dik leh a hun dik taka ei hi a ni. A chanve vel tihtawp chuan chhiatna nasa tak a thlen thei a ni.
Engtikah nge damdawi lam thurawn ka lak ang?
He thuziak hi a pawimawh ber a ni. I taksa chu ngun takin ngaithla rawh. Thil danglam emaw, thil danglam emaw i hriat chuan ngaihthah suh.
| Ngaihtuah vat ngai dinhmunte | |
|---|---|
| I doctor hmu rawh... |
|
| Hospital-a Emergency Treatment Unit (ETU)-ah kal nghal rawh... |
|
Take-Home Thuchah a ni
- Vasculitis hi thisen kalna kawng a inflammation a ni. Autoimmune natna a ni.
- He natna lan chhuah dan hi a inang lo hle. A natna lan chhuah dan tlangpui, khawsik leh malaise atanga natna khirh zawk, vun natna leh thawk harsa zawk thlengin a awm thei.
- He natna hi a dam kim thei lo. Amaherawhchu, uluk taka enkawl a nih chuan symptoms te chu control theih a ni a, nun pangngaia nunpui theih a ni.
- I taksaa natna lan chhuah thar emaw, a zual zel emaw chu ngaihthah ngai suh. I doctor hnenah hriattir nghal rawh.
- Thâwk harsat, heart attack symptoms i neih emaw, mitdel nghal mai emaw i neih chuan hreh lovin damdawi in hnai ber Emergency Department (ETU)-ah kal rawh.











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