Doctor-in i naute hian a taksa hnuai lam, chu chu a hnungzang hnuai lam, a ke, emaw, fecal leh urinary system-ah emaw thil danglam tak a nei tih a hrilh che chuan, nu emaw, pa emaw chuan a hriat chuan a mangang hle ang. ‘Caudal Regression Syndrome’ tih hming hi i hre tawh mai thei em? Hei hi damdawi lama harsatna awm lo, mahse hriat tur pawimawh tak a ni. Vawiin hian he thu hi awlsam takin, i hriatthiam theih dan tur angin kan sawi dawn a ni.
Caudal Regression Syndrome hi eng nge ni?
A awlsam zawngin sawi ila, hei hi pian tirh (na piansualna)-a awm, thil awm lo tak a ni. Kan taksaah chuan ‘caudal’ tih awmzia chu tail lam hawi tihna a ni a, chu chu taksa peng hnuai ber tihna a ni. ‘Regression’ tih hian thanlenna tihkhawtlai emaw, hnungtawlh emaw tihna a ni. Chuvangin he dinhmunah hian thil thleng chu naute chu nausen pum chhunga a lo seilian lai hian taksa hnuai lam a lo thang tha lo a ni.
Hei hian taksa peng tam tak a nghawng thei a, chung zingah chuan hnungzang hnuai lam, ruhro, ke, chaw ei kawng hnuai lam (intestines, rectum), leh zun kawng (kidney, bladder) te pawh a tel. Hetiang dinhmun hi ‘sacral syndrome’ an ti \hin.
Hetiang dinhmun hi engte nge ni?
Doctor-te chuan he natna hi a chhan pakhat, 100% chiang tak an la hmu thei lo. Mahse, tunah chuan environment leh genetic factors inzawmkhawm hian he natna thlentuah hian chanvo a nei thei niin an ngai. A chhan nia rinhlelh ber berte hi han thlir ila.
| Thiltihtheihna thlentu factor | A sawifiahna awlsam tak |
|---|---|
| Nu hriselna dinhmun | A bik takin naupai laiin nu zunthlum hi a thunun tha lo a nih chuan thisen sugar level sang chuan nausen pum chhunga naute thanlenna a tichhe thei a ni. Mahse, he natna hi zunthlum vei nu naute zawng zawngah a awm vek lo. Zunthlum vei lo nu nauteah pawh a awm thei bawk. He inzawmna chungchangah hian zirchianna an la nei reng a ni. |
| Genetic Factors te hi a ni | Hei hi genetic influence vang pawh a ni thei tih theory a awm. Chu chu, thlah kal zelah gene inthlak danglamna engemaw zat chu a mawhphurtu a ni thei tihna a ni. |
| Embryo hmasa berah harsatna a awm thin | Naupai thla khatna chhung hian naute taksa kalphung a lo piang tan a. Hetih hun chhung hian nausen pum chhunga nghawng emaw, harsatna emaw eng pawh hian naute ruh, chaw ei dan leh zun kawng hmasawnna a tibuai thei a ni. |
| Thisen supply lama harsatna a awm | Theory dang pakhat chu he natna hi nausen pum chhunga lo seilian taksa hnuai lam thisen pek tlem vang a ni tih a ni. Thisen atanga oxygen leh nutrients tlahniam hian thanlenna a nghawng a ni. |
| Nausen tissue-a harsatna awm | Naute pian tirh kar hmasa berah hian tissue layer lian pathum a awm a. Tissue layer lai tak, mesoderm an tih hian taksa hnuai lam ruh, ruh leh kal tam tak a siam chhuak a ni. Chuvangin scientist-te chuan he mesoderm lo pian chhuahnaah hian harsatna a awm a nih chuan he dinhmun hi a lo awm thei niin an ngai. |
A langsar ber berte chu engte nge ni?
Hetiang natna vei naupang zawng zawng hian symptom inang an nei vek lo. Naupang thenkhat chuan symptoms na lo tak tak an nei thei a, thenkhat erawh chuan harsatna lian tak an nei thei thung. A lan chhuah dan tlangpui thenkhat han thlir ila.
| Taksa peng a nghawng | Hmuh theih thil chi hrang hrang |
|---|---|
| Spine a ni | Scoliosis hi hnungzang hnuai lam vertebrae awm lo emaw, a inmil lo emaw a awm a ni. Hei hian rilru insiam dan a nghawng thei a, thawk harsatna a thlen thei bawk. |
| Taksa hnuai lam | Hip ruh te te, a hnute a flat. Ke ruh lo awm dan pangngai lo. Khup chu a sir lehlamah a hawi emaw, ke chu a in/out emaw a ni. Kea hriatna hloh. |
| Kidney leh urinary system te a ni | Kidney pakhat emaw pahnih emaw a bo emaw, kal pahnih inzawmkhawm emaw a ni. Hei hian zun kawng infection emaw kidney failure emaw a thlen fo thei. Bladder chhunga nerve chhiat avanga zun control harsa. |
| Mipat hmeichhiatna lam | Mipa naupangah chuan zunthlum (urethra) hi penis hnuaiah a awm emaw, taksa atanga testicles a chhuak lo emaw a ni. Hmeichhiaah chuan vagina leh anus inzawmna pangngai lo a awm a. Naupang \henkhatah chuan serh (genitals) hi a lo thang kim lo. |
| Chaw ei dan (digestive system) a ni | Harsatna hrang hrang, intestinal torsion, blocked anus, leh constipation te. |
Engtin nge enkawl a nih?
Hei hi enkawlna pakhat chauh a awm lo. Naupang tin dinhmun a inang lo vek avangin, naupangin harsatna a neih bikte a zirin enkawl dan tur ruahman a ni. Chumi atan chuan field hrang hranga specialist team te thawhhona tha tak neih a ngai a ni.
Hetiang natna nei naupang tan hian a rang thei ang bera hriatchhuah leh enkawl tan a pawimawh hle. Hei hian naupang nunphung nasa takin a tichangtlung thei a ni.
A tlangpuiin, enkawlna team-ah hian specialist te pawh an tel thei a, chungte chu:
- Naupang enkawltu doctor te
- Neurosurgeon te an ni
- Neurologist te an ni
- Urologist (urinary system lama tui tak surgeon) te chuan an .
- Orthopaedic surgeon te an ni
- Cardiologist te an ni
- Nephrologist te an ni
Naupang zun kawng, ruhro, thinlung, rectum, emaw ke leh ke leh ke ruh chungchanga harsatna awmte siamthat nan kum naupan laia operation neih thinThil engemaw zat tih a ngai mai thei. Tin, zun kawng lama harsatna nei tan damdawi bik pek theih a ni a, dam chhung zawnga physiotherapy, rilru lam puihna leh puihna service dangte pawh a ngai thei bawk.
I fa hian he natna hi a nei emaw, rinhlelhna a neih emaw chuan a tha ber chu hlauthawng lovin, i doctor nen inbia a, a tul anga specialist te hnena refer hi a ni.
Take-Home Thuchah a ni
- Caudal Regression Syndrome hi nausen piansualna hmuh tur awm lo tak a ni a, naupang taksa hnuai lam hmasawnna a tichhe thei a ni.
- Hei hi a chhan dik tak hriat chhuah ni lo mah se, naupai laia nu hriselna (a bik takin zunthlum thunun theih loh) leh genetic factors hian hmun a chang thei a ni.
- Naupang tin hian natna lan chhuah dan a inang lo. Spine, ke, kidney, bladder, leh intestines te a nghawng thei a ni.
- Enkawlna atan hian specialist chi hrang hrang team a ngai a, naupang mamawh ang zelin enkawl tura ruahman a ni.
- I fate nunphung tha tak neih theih nan a hmaa natna hriatchhuah leh enkawlna ruahmanna kimchang siam tan a pawimawh hle. I doctor nen harsatna awm apiang sawipui rawh.











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