Nu ni tur i nih chuan i naute piang lai hriselna tur i ngaihtuah a ni mai thei. A chang chuan scan zawhah doctor-in thil pawi tak a sawi a, hlauhna leh lungkhamna nasa tak nei hi thil pangngai a ni. Vawiin hian piansualna hmuh tur awm lo tak, hlauhawm deuh, mahse uluk taka enkawl a nih chuan rah tha tak a chhuah thei chungchang kan sawi dawn a ni. Hetiang dinhmun hi Gastroschisis (GAS-tro-schi-sis) an ti a.
A awlsam zawngin, Gastroschisis chu eng nge ni?
Gastroschisis hi naute chu an pum hnuai lam chiaha khur neia piang a ni a, chuta tang chuan intestines leh a chang chuan taksa peng dang, liver leh stomach te chu a chhuak chhuak thin. Ngaihtuah teh, nausen pum chhunga a lo seilian hmasak ber hian pum ruhte hi a thang tha lo hle. He gap te tak te hian heng organ te hi a lo chhuak thei a ni.
Hetiang natna vei naute hi an pian tirh atangin operation neih a ngai a ni. Tin, Neonatal Intensive Care Unit-ah pawh surgery hma leh operation zawhah rei vak lo an awm a ngai bawk. Nu leh pa kan nih angin hei hi thil hlauhawm tak a ni thei a, mahse naute tam zawk chu operation hnuah an dam tha hle.
Gastroschisis leh Omphalocele hi eng nge an danglamna?
Heng pahnih hi naute pum chhunga khur atanga taksa peng hrang hrang lo chhuahna hmun tlemte a ni. Mahse an pahnih inkarah hian danglamna chiang tak a awm. A danglamna hre turin a hnuaia table hi en la.
| Mihring ziarang | Gastroschisis natna (Gastroschisis) a awm | Omphalocele tih a ni |
|---|---|---|
| Khawiah nge khur a awm | Belly button bulah chuan . | Hole chhungah chuan a lut nghal. |
| Organ hrang hrang khuh | Protective membrane hmanga khuh loh . | Protective film hmanga khuh a ni (mahse he film hi a chang chuan a chhe thei). |
| Risk lian ber | Naute chhehvel amniotic fluid-a intestine a awm chuan a hring leh a chhe thei a ni. | Nau piangsual dang (a bik takin thinlung natna leh genetic problems) nen a inzawm zawk a ni. |
I obstetrician chuan naupai laiin routine scan hmangin heng zinga pakhat tal hi a hmuchhuak thei a ni.
Hetiang natna lan chhuah dan hi engte nge ni?
Naupai lai hian symptom engmah i nei lo mai thei . Hei hi naute scan hmang chauha hriat theih a ni. Doctor chuan scan laiin hetiang thil hi a hmu thei a ni:
- Naute taksa peng hrang hrang, intestine leh pum te chu taksa pawnah a inphah chhuak niin a lang.
- Intestines chu a hring emaw, a inzawm khawm emaw a ni.
- A chang chuan naute taksa lumna a tlahniam (Hypothermia).
Gastroschisis hi engte nge ni?
Hei hi a chhan chiang tak pakhat mah a la awm lo. A tam zawkah chuan thil hrang hrang inzawmkhawm avanga lo awm a ni. Hengte hi a hlauhawmna tipungtu nia hriat chhuah thenkhat chu a ni:
- Kum naupang takah naupai: A bik takin nu tleirawlte tan chuan a hlauhawmna a sang hle.
- Meizial zuk: Naupai laia meizuk, a bik takin thla tir lamah.
- Zu in: Naupai laia zu in.
- Damdawi emaw damdawi emaw thenkhat hman.
- Low maternal body mass index (BMI): Naupai laiin nu taksa rihna a tlahniam dan pangngai lo.
- Urinary tract infection ang chi infection: Nu hian naupai hma thla 3 emaw, naupai thla 3 hmasa berah emaw urinary tract infection ang chi condition a nei tawh a.
- Naute gene emaw chromosome emaw inthlak danglamna.
Mahse heng risk factors nei zawng zawng hian he natna hi an nei vek dawn lo. Tin, heng risk factors zinga pakhat mah nei lo pawhin he natna hi a nei thei bawk. Chuvangin he thil chungchangah hian a tul lovah inthiam lohna nei suh.
Engtin nge he dinhmun hi kan hriat theih ang?
Hetiang dinhmun hi naupai kar 18 leh kar 20 inkar scan-ah hriat theih a ni fo. Chumi atana test hman berte chu:
- Ultrasound: Hei hi natna hriat dan ber a ni. Naute taksa peng hrang hrangte chu a pum chhungah chiang takin a inphah chhuak tih hmuh theih a ni.
- Nu thisen test dan:A châng chuan nu thisenah hian protein pakhat alpha-fetoprotein (AFP) an tih chu an enfiah ṭhin. Level a sang hle a nih chuan gastroschisis rinhlelh a ni. Hei hi scan hmangin a nemnghet leh thin.
- Fetal Echocardiogram: Hei hi scan bik a ni bawk. Gastroschisis vei naute thenkhat pawhin thinlung lam harsatna an nei thei bawk. Chuvangin he scan hi naute thinlung hnathawh dan enfiah nan tih a ni.
Naute hian Gastroschisis a vei a nih chuan naupai laiin engtin nge enkawl a nih?
I naute hian he natna hi a vei tih hmuhchhuah a nih chuan nang leh i naute hian ngaihven bik i mamawh dawn a ni. I doctor chuan specialist team hnenah a refer ang che.
- Maternal-fetal medicine specialist: Naupai hlauhawm tak tak enkawltu doctor.
- Neonatologist: Nausen piang thar, a bik takin damlo emaw, nausen piang hma emaw enkawltu doctor.
- Pediatric surgeon: He doctor thurawn hi a pawimawh hle a, a chhan chu naute a pian veleh zai a ngai a ni.
Hemi chhung hian i naute hmasawnna enfiah nan scan nawn fo a ngai dawn a ni. Tin, ni khatah darkar hnih vel, kar 26 vel atanga tan tur, i naute chetna (a che vel zat) chhiar thin turin hriattir i ni thei bawk.
Engtin nge enkawl a nih?
Gastroschisis enkawlna chu operation a ni .
Vawi tam tak chu doctor-te chuan nau neih tir chu a tlangpui aia hma deuhin, kar 35 leh 37 inkarah an rel thin. Hetiang dinhmun hian cesarean section tihna a ni hauh lo va, mahse neonatal intensive care unit (NICU) awmna damdawi inah nau neih dan tur ruahmanna siam a pawimawh a, a chhan chu naute chu a pian veleh specialized care a mamawh dawn a ni.
Naute a pian veleh surgery an nei nghal a, taksa peng lo chhuak tawhte chu pum chhungah dah lehin a khur chu khar a ni. He surgery hi tih dan tlangpui pahnih a awm a.
1. Primary Repair (single surgery): Organ chhuak chhuak zat a tlem a, nasa taka a chhiat loh chuan nau piang veleh surgery vawi khatah dah leh nghal a, pum chu khar a ni.
2. Staged Repair: Hetiang tih dan hi taksa peng tam tak a chhuak emaw, a hring emaw a nih chuan hman thin a ni. Hetiang tih danah hian naute taksa peng hrang hrangte chu a pian hnu lawkah special protective plastic bag (‘ silo ’ an tih)-ah dah a ni. Hei hian taksa peng hrang hrangte a venghim a ni. Tichuan, taksa peng hrang hrangte chu ni engemaw zat chhung chu zawi zawiin pum chhungah an nawr lut leh thin. An dah kim hnuah chuan a khur chu surgery hmangin an khar a ni.
Surgery zawhah naute chu a pum chhunga pressure sang tak avangin thawk turin ventilator-ah dah a ni ang.Connect a ngai mai thei. Tin, intestine te hian hna a thawk tha tan hma chuan naute chu vein (IV) hmanga chaw pek a ngai dawn a ni. Hei hian naute chu damdawi inah kar engemaw zat a awm a ngai thei a, a aia rei pawh a awm thei bawk.
Hetiang dinhmun avang hian eng harsatna nge awm thei?
Amniotic fluid ei hian intestine a tichhe thei a ni. Chumi avang chuan naute thenkhat chuan harsatna an tawk thei a, chungte chu:
- Chaw ei harsa leh ei tur tha (nutrients) hip harsa.
- Intestinal atresia a awm thin.
- Intestines (Volvulus) a inzawm khawm (Volvulus).
- Intestine-a thisen kal dan block (infarction) avanga tissue chhiatna.
Surgery an neih hnuah pawh infection leh ei leh in harsatna ang chi harsatna a awm thei. Mahse, heng zawng zawng hi medical team-in uluk takin an vil reng a ni.
Take-Home Thuchah a ni
- Gastroschisis hi natna awm lo tak a ni a, naute chhungril leh taksa peng dangte chu taksa atanga rawn chhuakin a piang a ni.
- Hei hi naupai laiin scan hmangin hriat theih a ni tlangpui.
- Nu leh pate chuan he thu hi an hriat hian hlauthawng takin an awm thei a, mahse he natna vei naute 95% vel chu operation hnuah an dam kim vek a, nun pangngai an hmang thin.
- Naute a pian veleh zai a ngai a. Chumi atan chuan specialist doctor team enkawlna hnuaia damdawi ina dah a pawimawh hle.
- Naupai laia meizuk leh zu in pumpelh a, ei leh in inthlau tak ei hian heng piansualna te hi a tihziaawm thei a ni.
- Hemi chungchangah hian rinhlelhna emaw hlauhna emaw i neih chuan i doctor nen zalen takin inbia nghal ang che.











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