Ngaihtuah teh, i fa, a bîk takin naupang tê chu ni tam tak chhung chu a muhil ṭan nghal a. Kaihthawh i tum a nih pawhin a mu leh mai thin. Chaw ei leh bathroom kal tih loh chu a muhil reng a ni. Nu emaw pa emaw tu pawhin hetiang thil hi an hmuh chuan an hlau ang em? Hei hi rilru lam harsatna nge natna dang a ni tih hriat a har khawp mai. Vawiin hian thil mak tak mai, ni tam tak chhung mutthilh lutukna thlentu, thil mak tak mai kan sawi dawn a ni. Chu chu Kleine-Levin Syndrome, a tawi zawngin KLS a ni.
Kleine-Levin Syndrome (KLS) hi eng nge ni tak tak?
A awlsam zawngin sawi ila, Kleine-Levin Syndrome (KLS) hi mutna lama harsatna awm lo tak a ni. Tlangval naupangte zingah a tam ber . Hetiang natna vei zinga 70% chu he category-ah hian an tel a ni.
He natna lan chhuah dan ber chu mut tam lutuk hi a hun takah a awm thin a ni. Heng hun chhung hian damlo chu hrisel tak leh pangngai takin a lang thei a ni. Chu chu symptom engmah nei lo tihna a ni.
Heng symptoms te hi kan thluak hmun pawimawh tak nen a inzawm tlat a ni. Chu chu hypothalamus a ni . He hmun tenau tak hian kan mut, riltam, tuihal, ei duhna, leh mipat hmeichhiatna lama kan duhna ang chi thil tam tak a thunun a ni. KLS-ah chuan he hypothalamus hnathawh hi hun engemaw chen a tichhe niin an ngai.
Damdawi lamah chuan KLS hi hypersomnia an tih angin an dah a, chu chu mutthilh lutuk tihna a ni. Mahse, a symptom thenkhat chu rilru natna nen a inang avangin, a chang chuan depression ang chi condition anga hriat sual a ni.
Thu lawmawm tak chu kum upat deuh deuh hian heng symptoms te hi a tlahniam zauh zauh thin. Kum 50 chunglam zingah KLS symptoms hmuh tur a awm lo hle.
KLS hi a chhan bik a awm em?
Zirchiangtute chuan a chhan chu eng nge ni tih chiang takin an la sawi thei lo a, mahse thil engemaw chu an ringhlel hle.
Vawi tam tak chu, he natna episode pakhat hi a hnuaia damdawi lam dinhmun, khawsik, flu, a nih loh leh virus infection dang .
Chu bâkah, zirchiangtu ṭhenkhat chuan lu hliam, natna hrik, a nih loh leh autoimmune disorder a awm thei niin an ngai bawk. Amaherawhchu, thlahtu natna a ni lo. Chhungkaw khata mi engemaw zatin he natna hi an vei hi a tlem hle.
KLS natna lanchhuahna chu engte nge ni?
Kan sawi tawh ang khan he natnaah hian a lan chhuah dan chu ‘sudden’ episode angin a lang thin. Episode pakhat hi kar khat atanga thla hnih thleng a awh thei . A vaiin kum khatah hetiang episode 2 leh 12 inkar a awm thei.
Hemi hun chhung hian damlo nungchang leh taksaah inthlak danglamna lian tak tak tam tak i hmu thei a ni. Mut tam lutuk bakah hian symptom dang tam tak a lang chhuak thin.
| Symptom a ni | Hrilhfiahna |
|---|---|
| Mut tam lutuk | Ni khatah darkar 20 vel mut a, thil pawimawh tak tak ei emaw, bathroom kal emaw tih loh chu harh loh. |
| Nungchang a inthlak danglam thin | Chhan awm lova thinrim, tharum thawh, midang ngaihsak loh, lungngaihna leh lungkhamna te. |
| Ei duh lutuk | I ei tlangpui aia tam ei. A châng chuan thil danglam tak tak ei tûrin thlêmna i nei hial thei bawk. |
| Mipat hmeichhiatna hmansual (hypersexuality). | Mipat hmeichhiatna lama duhna danglam tak pung leh chumi chungchang sawi fo emaw, nungchang emaw tih fo thin. |
| Buaina leh thil tak tak atanga tlanchhuahna | Harh lai pawhin rilru hah, buai leh mumang ang maia awm. A châng chuan, thil awm lo (hallucinations) pawh i hmu mai thei. |
| Hriatrengna leh ngaihvenna | Thil thleng theihnghilh, thil pakhata ngaihtuahna seng thei lo. |
Because these episodes can start suddenly, without any warning , KLS vei tam tak chuan an dinhmun chipchiar taka tarlanna medical jewelry ang chi thil an ha thin.
He natna hi engtin nge kan hriat theih ang? (Diagnosis) tih a ni.
Hei hi diagnose hi a harsa deuh a, a chhan chu thisen test emaw scan emaw bik a awm loh vang a ni. Chuvangin doctor-te chuan natna dang, chutiang bawka chhinchhiahna nei chu paih chhuah an tum ṭhin. Hei hi ‘ruling out’ kan ti a ni.
KLS natna hi heng dinhmunte nen hian a inzawm thei fo thin:
- Depression emaw Bipolar Disorder emaw a ni thei
- Narcolepsy, mut natna dang
- Epilepsy natna a ni
- Multiple Sclerosis natna a ni
- Thluak natna (brain tumor) a awm
- Migraine natna (Migraine) a awm
- Damdawi thenkhat (e.g., Benzodiazepines) emaw damdawi emaw avanga side effects
Chuvangin, i doctor chuan nangmah chauh ni lovin, he natna tawk tawh i nu leh pa leh chhungte nen pawh inbiakna hmangin thutlukna dik tak a siam ang.
KLS enkawl dan tur chu engte nge ni?
KLS damdawi a la awm lo. Mahse, natna lan chhuah dan control thei tur leh episode inkar hun pawh ti sei thei tur enkawlna a awm. Enkawlna tum ber chu symptoms tihziaawm hi a ni.
Mut tam lutuk control nan doctor-te chuan stimulant an pe thei a. Entir nan:
- Amphetamines a awm bawk
- Methylphenidate a ni
- Modafinil a ni
Tin, damdawi lithium hi hlawhtling taka hman a ni fo bawk a, symptoms control nan leh episode inkar hun rei zawk atan hman a ni bawk. Lithium hi rilru lam natna enkawlna atana hman thin damdawi a ni bawk. He damdawi hi KLS leh rilru lam natna thenkhat inanna a awm avangin a tangkai hle niin an ngai.
Mahse hei hi i ngaihtuah reng tur a ni . Doctor thurawn tel lo chuan heng damdawi te hi hman a tha lo . Doctor chauhvin natna hi dik takin a hmuchhuak thei a, damdawi dik tak chu a dose dik takah a pe thei bawk.
Take-Home Thuchah a ni
- Kleine-Levin Syndrome (KLS) hi natna hlauhawm tak a ni a, mipa naupangte a nghawng ber a, ni tam tak chhung mutthilh lutuk a thlen thin.
- A lan chhuah dan chu mut tam lutuk mai ni lovin, nungchang inthlak danglam, ei duh lutuk leh buaina te pawh a ni.
- Hei hi rilru lam natna a ni lo va, thluak hypothalamus inrawlhna neurological condition a ni.
- Natna hriatchhuah hi a buaithlak a, natna dang, a lan chhuah dan inang lote chu paih chhuah a ngai a ni.
- Nangmah emaw, i hriat miin emaw heng symptoms te hi i hriat chuan hlau suh la, a rang thei ang bera doctor thiam tak hnenah doctor thurawn la rawh.
- Symptoms control nan damdawi tha tak tak a awm a, mahse doctor rawtna ang chauha ei tur a ni.











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