Tlangval, hrisel, infiamna lama mi pakhat chu heart attack vangin a thi thut tih i hre ngai em? A lungchhiatthlak takzet. A tam zawkah chuan thinlung natna hi kum upat ruala thil thleng angin kan ngai thin. Mahse a châng chuan, heng thil thleng ngaihtuah phak loh thil thleng chhan hi kan hriat loh dinhmun tlemte chauh a ni. Vawiin hian chutiang thinlung natna pakhat, a bik takin thalai te nghawng thei tur chungchang kan sawi dawn a ni. Hei hi ARVC a ni.
ARVC hi eng nge ni tak tak?
A awlsam zawngin, ARVC hi thinlung natna hmuh tur awm lo tak a ni a, genetically inherited , chu chu thlah kal zelah a darh thei tihna a ni. Thil thleng chu kan thinlunga ruh (muscles) te hi a chhe ta a ni.
Kan thinlung hi pump chak tak, chamber pali atanga siam angin han ngaihtuah teh. Hei hi taksa pum puiah thisen pump chhuaktu a ni. Heng chamber pali zingah hian dinglam hnuai lam a awm chu Right Ventricle an ti a. ARVC-ah chuan he right ventricle-a heart muscle cell hrisel tak takte hi an thi a, chu chu thau leh fibrous tissue (scar tissue) -in a thlak a ni.
Bang tha tak atanga brick tla a, a gap te chu leivut in a khat ang mai a ni. Eng thil nge thleng? Chu thinlung pindan bang chu a hring a, a chak lo va, a inzawm khawm ta a ni. Tichuan a contract tha thei lo va, thisen a pump thei ta a ni. Hei hian thawk hah leh muhil ang chi thil a thlen thei a ni.
Chu aia hlauhawm zawk chu thau leh hliam tissue lo piang thar hian thinlung chhunga electrical signal awmte a tibuai a ni. Hei hian thinlung a thawk mumal lo a ti thin. Hei hi arrhythmia kan ti a ni . Hei hi he natnaah hian a hlauhawm ber a ni. A chhan chu cardiac arrest nghal a thlen thei a, thihna thlengin a thlen thei a ni.
He natna hi ARVC, Arrhythmogenic Right Ventricular Dysplasia (ARVD) an ti bawk. A chang chuan veilam ventricle a nghawng avangin Arrhythmogenic Cardiomyopathy (ACM) an ti bawk.
Hetiang natna lan chhuah dan hi engte nge ni?
He natna chungchanga harsatna pakhat chu a tir lamah chuan asymptomatic a ni thei a ni. Kum 40 an tlin hmain symptoms hi a lang tan fo thin a, a chang chuan puitling naupang takah pawh a lang tan thin.
Thil hlauhawm ber chu mi thenkhat tan chuan he natna hi an vei tih hriat theihna hmasa ber leh awmchhun chu rilru lam thihna (sudden cardiac death) hi a ni.
Chuvangin a hnuaia symptoms te hi kan hriat chian a pawimawh hle.
| Symptom a ni | A sawifiahna awlsam tak |
|---|---|
| Thinlung thawk mumal lo (Arrhythmias) . | Heart rate inthlak danglamna pangngai lo. A rilruah chuan fluttering emaw squeezing sensation ang maiin a awm thei. A bik takin (Atrial Fibrillation) ang chi dinhmunah chuan . |
| Luak chhuak emaw, muhil emaw | Thluak hian thisen a hmuh tlem avangin hriatna hloh ang mai a ni. |
| Chau | Taksain thisen a pump tha loh avangin chau lutuk tih hriat reng. |
| A rilru a na | Thinlung pressure avanga rilru natna. |
| Thâwk harsa | Thâwk lamah thisen a tlin tawk loh vanga thawk hah. |
| Taksa a hring chhuak | Ke, ke ruh, ke emaw, pum chhungah emaw a hring chhuak. |
| Lung lam chak lohna | Hun a kal zel a, thinlung pump theihna chu a tlahniam vek tawh mai. |
ARVC awm chhan leh a rochun dan
A tam zawkah chuan ARVC hi genetic variant avanga lo awm a ni . Hei hi kan taksa cell siamtu blueprint, a nih loh leh genes-a tihsual tlemte a ni. Hetiang dinhmun hi heart muscle cells inzawm tlat tura puitu proteins tichhe thei genes dik lo a awm hian a thleng thin.
He inzawmna hi a chak loh chuan heart muscle cell te chu an inthen tan a, an thi ta a ni. Hei hi a bik takin thinlunga harsatna awm lai, exercise lak lai ang chiah hian a thleng thei a ni.
ARVC vei zinga a chanve vel chu chhungkaw history-ah he natna hi an nei a ni. Hei hian genetic history a awm tihna a ni .
Chuvangin, i chhungkuaa mi tu emaw ARVC vei hmuhchhuah a nih chuan chu mi chu a chhungte hnai tak (nu leh pa, unau, fate, tu leh fate, a u, a pi, a farnu, a farnu) te chu medical examination an neih a pawimawh hle. Natna lanchhuahna a awm lo a nih pawhin naupang deuhte pawhin Doctor hmuin hemi chungchang hi sawipui mai tur a ni.
ARVC hi thlah kal zelah a kai darh theih dan tlangpui pahnih a awm a:
- Autosomal Dominant: Hei hi a tam ber chi a ni. Chumi awmzia chu nu leh pa zinga pakhat chuan gene mutation a nei tihna a ni. Tichuan an fain natna a rochun theihna chance 50% a nei a ni. Amaherawhchu, natna lan chhuah dan leh a lo intan kum hi chhungkaw member hrang hrangah a inang lo thei hle.
- Autosomal Recessive: Hei hi a tlem zawk. Hetah hian nu leh pa pahnih hian gene mutation an nei a, mahse symptom an nei lo. An fa hian he natna hi a vei theihna chance 25% a nei a ni. Hemi nena inzawm dinhmun bik pakhat chu Naxos disease , a ni a, chu chuan ke kutphah leh kephah vun a ti thim thei a, sam sei tak, vun ang maia lian a siam thei bawk.
Engtin nge natna hi kan hriat theih ang?
Doctor chuan ARVC hi i natna lan chhuah dan, chhungkaw chanchin leh damdawi lam test tlemte a zirin a hre thei a ni. ARVC hi diagnostic criteria bik engemaw zat a awm a. Doctor-te chuan heng criteria i tlin zat hi an en thin.
Doctor-te ngaihven ber berte chu:
- Right ventricular function dik lo enfiah nan ( Hei atan hian Echocardiogram emaw MRI test emaw hman a ni).
- Heart muscle-ah hian thau emaw scar tissue emaw a awm em tih en turin (hemi atan hian MRI hi a pawimawh hle).
- ECG test ( Electrocardiogram - ECG/EKG ) hmanga thil dik lo awm leh awm loh enfiah nan.
- Heart rhythm mumal lo, a bik takin exercise neih laiin.
- Chhungkaw zingah tu pawhin ARVC an nei em tih.
Heng thilte a\ang hian doctor chuan natna hi "dik tak zetin" i nei em tih, "a nei ngei ang" tih emaw, "i ve ngei ang tih emaw a rel ang. A tul chuan genetic testing atan pawh an refer thei bawk.
Test dang hman dan:
- Thinlung hi Cardiac Computed Tomography (CT ) hmanga enfiah a ni
- Exercise neih laiin ECG test ( Stress Test ) .
- Thinlung electric hnathawh dan zir chianna ( Electrophysiology Testing ) .
- Lung ruh te tak te enfiah nan lak ( Biopsy ) .
ARVC enkawl dan tur chu engte nge ni?
Vanduaithlak takin ARVC damdawi a awm lo. Mahse, i natna lan chhuah dan thunun thei tur, harsatna hlauhawm tak tak laka invenna tur leh nun pangngaia i nun theihna tur enkawlna tha tak tak a awm nual. I doctor thil tum ber chu heart rhythm leh heart conditions enkawl hi a ni.
| Enkawl dan tur | Eng thil nge thleng? |
|---|---|
| Damdawi chi hrang hrang | Heart rhythm mumal lo awm lo turin antiarrhythmic damdawi, beta-blockers , leh anticoagulants te pek thin a ni. |
| Catheter hmanga tihbo a ni | Damdawi hmanga control theih loh heartbeat mumal lo i neih chuan, chu chu heart-a electrical signal pangngai lo siamna hmunte halralna procedure a ni. |
| ICD hmanrua (Implantable Cardioverter-Defibrillator) hmanga siam theih a ni. | Hei hi enkawlna pawimawh ber pakhat a ni. Cardiac arrest nghal vanga thih hlauhawmna sang tak nei tan chuan an rilru vun hnuaiah hian hmanraw te tak te dah a ni. Heart rhythm disorder hlauhawm tak a awm chuan he device hian electric shock a pe a, chu chuan heart chu a normal angin a siam leh thin. |
| Lungphun thlak a ni | Enkawlna dang zawng zawng a hlawhchham chuan a tawp ber anga ngaih a ni a, mahse ARVC vei tam zawk chuan hetiang khawpa hla hi an kal a ngai lo. |
ARVC nena kan khawsak huna ngaihtuah tur thil
ARVC i vei tih hriat a nih veleh i nunphungah inthlak danglamna engemaw zat i siam a ngai dawn a ni. Heng thilte hian i thinlunga harsatna awm chu a tihziaawm thei a ni.
- Exercise tihtlem: ARVC hi exercise hmangin a ti na zual thei. Chuvangin, inelna infiamna hi i pumpelh vek a ngai mai thei. Nitin exercise i tih theih zat leh chi hrang hrangte chu i doctor hnenah sawipui ngei ang che.
- Nun hrisel tak: Zu in tlem te, zu in loh te, ei leh in tha tak ei te, caffeinated in tur (coffee, tea) te tihtlem a pawimawh hle.
- I damdawi ei tur chu a tih angin ei rawh: I doctor-in damdawi a pek chu ei loh ngai suh.
- Damdawi lam enfiah fo thin: I dam chhung zawng doctor i hmuh a ngai dawn a ni. ICD i neih chuan i check fo a ngai ang .
Lung natna i nei tih hriat chu thil harsa tak a ni thei a, a bik takin kum naupang takah chuan. Athlete i nih chuan chu identity chu i bânsan a ngai chu a pawi thei hle. Mahse, i nunna hi a hlu zawk hle tih hre reng ang che. Enkawlna dik leh nunphung dik tak nen chuan nun tha tak i hmang thei a ni.
Take-Home Thuchah a ni
- ARVC hi thil awm lo, thlahtute atanga lo chhuak a ni a, a bul berah chuan thinlung dinglam a nghawng a ni.
- He natna hlauhawm ber chu lungphu chawl thut leh chhinchhiahna awm lova thihna hlauhawm hi a ni.
- I rilru natna, luak chhuak, thawk harsa tih ang chi symptom i neih chuan doctor pan nghal rawh.
- I chhungkuaa mi pakhatin ARVC a neih chuan medical checkup i neih ngei ngei tur a ni.
- He natna hi tihdam kim theih ni lo mah se, damdawi, ICD hmanrua leh nunphung tihdanglamna hmangin hlawhtling taka thunun theih leh nunpui theih a ni.
- Heng damlote tan hian exercise hahthlak tak, inelna nei tak tak an tih loh a pawimawh hle.











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