Kei te piki haere tō ngenge me tō ngoikore i ia rā, i ia rā? Haunga te mamae o te puku me te whakapairuaki, kei te hiahia kē koe ki ngā kai tote i ētahi wā? Ahakoa he āhua noa ēnei, tera pea kei muri i tēnei he mate kāore anō kia rangona nuitia, engari me whakahaere tika. I tēnei rā kei te kōrero tātou mō tētahi o aua mate, arā, te mate a Addison.
He aha tonu te mate a Addison?
He māmā noa iho, he mate mau tonu te mate a Addison e puta ana ina kore e nui ngā homoni matua e rua e whakaputaina ana e ngā repe adrenal i roto i te tinana, arā, ko te cortisol me te aldosterone .
Tērā pea kei te whakaaro koe he aha ngā repe adrenal. He repe iti, tapatoru ēnei e rua e tū ana i runga i ō tātou whatukuhu, pērā i te taupoki. He wāhanga nui ēnei o te pūnaha endocrine o tō tātou tinana.
- Cortisol: He mea nui tēnei homoni ki ō tātou oranga. Whakaarohia mēnā ka pāngia koe e te mate, ka pāngia rānei koe e te aituā, ka pokanga rānei, ka nui te ahotea o tō tinana. I ēnei wā, ka āwhina te homoni cortisol i te tinana ki te aro atu ki taua ahotea. Ehara i te mea koinā anake, engari ka āwhina anō hoki ki te whakahaere i te toto toto, te mahi o te ngākau, te pūnaha ārai mate, me ngā taumata huka toto.
- Aldosterone: Ka whakahaere tēnei homoni i te taurite o te konutai (tote) me te pāhare pākawa i roto i ō tātou toto. Ka whakahaere hoki i te nui o te wai ka tukuna e ō tātou whatukuhu hei mimi. Ka pā tika tēnei ki te nui o te toto me te toto toto.
E mōhiotia ana hoki te mate a Addison ko te koretake o te adrenal tuatahi . Tērā tētahi atu āhuatanga e pā ana ki tēnei āhuatanga, ko te koretake o te adrenal tuarua . I roto i tēnei āhuatanga, kāore te repe pituitary i roto i te roro e whakaputa i te nui o te homoni e kiia nei ko te ACTH . Mā tēnei homoni, ACTH, ka whakaoho i ngā repe adrenal ki te whakaputa i te cortisol.
He aha te rerekētanga i waenga i te mate a Addison me te mate a Cushing?
Kaua e whakapoauau i ngā mea e rua. He tino māmā noa iho.
- Te Mate a Addison: Kāore i te rawaka te cortisol (me te aldosterone) i roto i te tinana.
- Te Mate a Cushing: Ka nui ake te cortisol i roto i te tinana.
Ko wai te mea tino tūpono ka pāngia e tēnei mate?
Ahakoa ka taea te mate a Addison i ngā tau katoa, ko te nuinga o te wā ka pāngia e te mate i waenga i te 30 me te 50 tau.I roto i te iwi. He tino onge tēnei mate.
Waihoki, he nui ake te tūponotanga o te hunga whai mate ārai mate ki te pāngia e tēnei mate. Ko te mate ārai mate ko te wā e whakaeke hē ai te pūnaha ārai mate o tō tātou tinana i ō tātou pūtau hauora. He nui ake te tūponotanga o te hunga whai mate e whai ake nei ki te pāngia e te mate a Addison:
- Mate huka momo I
- Te mate toto kino
- Te mate o Graves
- Te mate tairoiti mau tonu
- Te kiri herpetiformis
- Te kiriuhi
- Te mate pāwera
He aha ngā tohu o te mate a Addison?
I roto i tēnei mate, ka puta mārire te kino o ngā repe adrenal, i roto i te wā. Nō reira, ka puta mārire ngā tohu. Ka rerekē ēnei tohu i ia tangata, i ia tangata.
| Tohu | Whakaahuatanga |
|---|---|
| Te ahua o te ngenge nui | He tohu noa tēnei, ā, ka piki haere haere. |
| Ngā ira pango o te kiri (Hyperpigmentation) | Te pōuri o te kiri, inā koa ki ngā patunga, ngā koha, ngā whāriki kiri (ngā tuke, ngā turi), me ngā kapia. |
| Mamae puku, whakapairuaki, me te ruaki | Ngā raruraru o te pūnaha nakunaku. |
| Pupuhi (korere) | Ngā mamae puku maha me te korere. |
| Te ngaronga o te hiahia kai me te mate taimaha | Te ngaronga o te hiahia kai me te taumaha, kāore he take e kitea ana. |
| Mamae uaua me ngā hononga | Ngā āhuatanga pēnei i te mamae o te tinana me te kōpeketanga o ngā uaua. |
| Te toto toto iti | Te pōuri me te ngoikore i te tū. |
| Te hiahia nui ki te tote | He tohu e hua mai ana i te hekenga o te taumata tote i roto i te tinana. |
| Te huka toto iti (Hypoglycemia) | Tērā pea ka puta ngā tohu pēnei i te mamae o te tinana me te werawera. |
| Ngā huringa hinengaro | Te riri kāore i te mārama, te pouri, me te uaua ki te arotahi. |
Mena kei te pāngia ngā wāhine e tēnei mate, ka pāngia pea rātou e ngā tohu pēnei i te huringa paheketanga koretake, te ngaronga o te huruhuru o te tinana, me te hekenga o te hiahia moepuku.
Āhuatanga ohorere: He aha te āhua o te raruraru Addisonian?
I ētahi wā, inā koa i ngā wā tino taumaha o te tinana (hei tauira, he mate kino, he aituā), ka tere te kino haere o ngā tohu, ā, ka noho hei mōrearea ki te ora. Ka kiia tēnei he raruraru Addisonian , he ngoikore rānei o te adrenal .
He āhuatanga ohorere hauora tēnei. Ki te kore e rongoatia tika, ka pā mai pea te ohorere, tae atu ki te mate.
Mena kei a koe, kei tētahi atu rānei e mōhio ana koe, ēnei tohu e whai ake nei, haria tonutia ia ki te Tari Ohotata (ETU) o te hōhipera tata.
| Ngā tohu whakatūpato o te raruraru Addisonian | |
|---|---|
| 1. | Te ngenge nui me te ngoikore ohorere. |
| 2. | Te mamae ohorere, te mamae nui i te puku o raro, i te tuara, i ngā waewae rānei. |
| 3. | Te ruaki nui me te korere, ka hua ake te matewai. |
| 4. | Te hekenga o te toto toto ki raro rawa. |
| 5. | Te āhua o te rangirua hinengaro, te kore okiokinga, te wehi rānei. |
| 6. | Te ngaronga o te māramatanga. |
He aha te take o te mate a Addison?
Ko te tino take o te mate a Addison he urupare ā-tinana . I roto i ngā kupu māmā, ka whakaekea hētia e te pūnaha ārai mate o tō tātou tinana (te pūnaha ārai mate) ō tātou kiko hauora. I roto i tēnei mate, ka whakaekea e te pūnaha ārai mate te wāhanga o waho o ngā repe adrenal (te adrenal cortex). Koinei te wāhi e puta ai te cortisol me te aldosterone. Kāore e puta ngā tohu tae noa ki te 90% o tēnei kino kua pā mai. Ka roa pea tēnei i ngā marama, i ngā tau rānei. Koinei te take o te 75% o ngā tūroro a Addison.
I ngā wā o mua, ko te mate kohi te tino take o tēnei, ā, he tino take tonu tēnei i ngā whenua whakawhanake.
Tērā atu anō ētahi take onge:
- Ngā mate urutā pēnei i te HIV/AIDS me ngā mate harore.
- Te horapa o ngā pūtau matepukupuku mai i ētahi atu wāhi ki ngā repe adrenal.
- Te toto ki roto i ngā repe adrenal (te totohu).
- Te tango pokanga i ngā repe adrenal.
- Nga mate penei i te amyloidosis.
Me pēhea te tautuhi a te tākuta i tēnei mate?
Nā te mea ka puta mārire ngā tohu, ā, he mea noa hoki ki te maha atu o ngā mate, he uaua ki te tautuhi tika i tēnei mate.
He maha ngā wā ka whakapae te tākuta ina whakaatuhia e te whakamātautau toto o ia rā he iti te konutai , he nui rānei te pāhare pāporo i roto i te toto. Ko ngā ira pango i runga i te kiri tētahi atu tohu nui e whakapae ai te tangata i tēnei.
Mena kei te whakapae tō tākuta kei a koe te mate a Addison i runga i ō tohumate, ka tonoa e rātou ētahi atu whakamātautau hei whakaū i te mate.
- Ngā whakamātautau toto: Ka ine ēnei i ngā taumata o te konutai, te pāhare pāporo, te cortisol, me ngā homoni ACTH i roto i ō toto.
- Whakamātautau whakaohooho ACTH: Kei roto i tēnei ko te werohanga i tētahi homoni ACTH hangai, me te tirotiro mēnā ka puta te cortisol i roto i ō repe adrenal hei whakautu. Ko ngā taumata cortisol iti pea he tohu kāore i te kaha te mahi a ngā repe.
- Whakamātautau huka toto i puta mai i te insulin: Ka tirohia tēnei mēnā he hononga tō raruraru ki te repe pituitary.
- Matawai CT: Ka taea e tēnei te tirotiro mēnā he kino ki ngā repe adrenal, he mate pāwera rānei.
He aha ngā maimoatanga mō tēnei?
Ka rongoātia te mate a Addison mā te whakakapi i ngā homoni ngaro o te tinana ki ngā rongoā hangai.
- Ka hoatu he rongoā e kīia ana ko te hydrocortisone hei whakakapi mō te cortisol.
- Ka whakakapia te aldosterone ki tētahi rongoā e kiia nei ko te fludrocortisone .
He mate mau tonu te mate a Addison, nō reira me tango e koe ēnei rongoā mō te toenga o tō oranga .
He rerekē te horopeta o tēnei rongoā i ia tangata, i ia tangata. Waihoki, ka whakanuia pea e tō tākuta te horopeta o te rongoā hei ārai i te raruraru Addisonian mēnā ka pāngia koe e te ahotea, pērā i te mate urutā, te aituā, te pokanga rānei.
Mena kei a koe te mate a Addison, me pēhea koe e tiaki ai i a koe anō?
Mena kei a koe tēnei mate, he mea tino nui kia tiakina koe.
- Me mau tonu he kāri tuakiri, he poroporo whakatūpato hauora rānei, kia mōhio ai ngā tohunga hauora ki tō āhua mēnā ka puta he āhuatanga ohorere.
- Kōrero ki tō tākuta mō te mea me mahi koe ina pāngia koe e te mate, ina pāngia rānei koe e te ahotea nui, nā te mea me whakarerekē pea te horopeta o tō rongoā i ēnei wā.
- Mō tētahi āhuatanga ohorerePātai atu ki tō tākuta mō te pupuri i tētahi werohanga cortisol me te whakaako i tētahi mema o te whānau me pēhea te hoatu ki a koe.
Āhea koe me toro atu ki tō tākuta?
Mena kei a koe te mate a Addison, me toro atu koe ki tō tākuta (he tākuta endocrinologist) i ia wā, kia mōhio ai koe kei te tika te horopeta o tō rongoā mōu.
Ki te pāngia koe e tētahi āhuatanga taumaha nui, pērā i tētahi aituā, i tētahi mate, i te matenga rānei o tētahi e arohaina ana e koe, waea atu ki tō tākuta nā te mea me whakarerekē pea te horopeta o tō rongoā.
Ki te puta ngā tohu o te raruraru Addisonian (pēnei i te ngoikore ohorere, te mamae nui), haere tonu ki te Tari Ohotata (ETU) o te hōhipera kia whiwhi maimoatanga hauora.
He mea whakapouri te hinengaro mēnā kei a koe tētahi mate pūmau. Engari ko te rongo pai, ka taea te whakahaere angitu i te mate a Addison mā te rongoā. Mā te toro atu ki tō tākuta i ia wā, te tango i te horopeta rongoā tika, me te tiaki i a koe anō, ka taea e koe te noho hauora, noho noa.
Karere Tangohia ki te Kāinga
- He mate onge, he mate mau tonu te mate a Addison, ā, kāore e nui te whakaputanga a ngā repe adrenal i ngā homoni cortisol me te aldosterone.
- Ko ngā tohu matua ko te ngenge haere, ngā wāhi pouri o te kiri (ina koa ko te wāhi e piko ai te kiri), me te hiahia nui ki ngā kai tote.
- He āhuatanga ohorere hauora e morearea ana pea te mate o te mate urutā Addisonian, ā, ki te puta ngā tohu, me haere tonu koe ki te tari ohorere o te hōhipera (ETU).
- Ko te maimoatanga e hiahiatia ana he rongoā whakakapinga homoni mo te wa katoa.
- Mā te whai i ngā tohutohu hauora tika, me te tango i ō rongoā kia rite ki ngā tohutohu, ka taea e koe te ora i tētahi oranga hauora, ā, he āhua noa iho.











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