He raruraru kei te hāora i roto i te toto? Me ako tātou mō te methemoglobinemia!

Kua kite koe i te kiri me ngā ngutu o tētahi tangata e huri whakarere ana i te tae kikorangi rerekē? Kua rongo rānei koe he kikorangi te whānautanga o ētahi pēpi? Ko tētahi take mō tēnei he mate toto tino onge, engari he kino pea. I tēnei rā ka kōrero tātou mō tētahi o aua mate , ko te methemoglobinemia . Ka kiia hoki e ētahi ko te "blue baby syndrome".

He aha tonu te methemoglobinemia?

I te whakarapopototanga, ko te methemoglobinemia he āhuatanga e kore ai e taea e ngā toto whero o roto i ō tātou toto te kawe i te hāora ki ētahi atu pūtau me ngā kiko o te tinana. Whakaarohia, ko ngā toto whero te mea e āwhina ana ki te kawe i te hāora puta noa i ō tātou tinana, tika? Kei roto i ēnei toto whero he pūmua motuhake e kiia nei ko te hemoglobin . He rite ki te pahi, ā, ko tēnei hemoglobin te kawe i te hāora puta noa i te tinana.

Heoi, i roto i tēnei āhuatanga e kiia nei ko te "Methemoglobinemia", ko te mea ka tupu ko te "Hemoglobin" e kawe ana i te hāora ka huri hei momo mea rerekē e kiia nei ko te "Methemoglobin ." Ko te raruraru, kāore e taea e tēnei "Methemoglobin" te kawe hāora. He rite ki te pahi e kawe ana i te hāora ka pakaru, ā, kāore e taea te kawe i ngā pāhihi.

Ka taea te tuku iho i tēnei āhuatanga (mā te ira) i roto i ētahi tāngata. Engari i te nuinga o te wā ka puta mai i ētahi rongoā e whakamahia ana e tātou, i ngā raau taero whakangahau, i te pānga rānei ki ētahi matū . I ētahi wā ka morearea te ora, inā koa i roto i ngā pēpi i whānau mai me te momo mate kino me te hunga e whakamahi ana i ngā raau taero. Heoi, i te nuinga o te wā, ka taea e ngā tākuta te tohu rongoā hei whakaiti i te taumata o te "Methemoglobin" me te whakakore i ngā tohu.

He aha te pānga o tēnei ki tōku tinana?

He maha ngā tāngata e pāngia ana e te methemoglobinemia ka pāngia e te mate e kiia nei ko te cyanosis . Ko te cyanosis te wā e huri ai ō maikuku, arero, ngutu, me te kiri ki te kikorangi mārama, ki te papura rānei. Ka puta tēnei ina kore e nui te hāora i roto i ō toto. E ai ki taku kōrero i mua, ko ngā toto whero ngā mea e kawe ana i te hāora puta noa i te tinana. He pūmua e kiia nei ko te hemoglobin hei āwhina i tēnei.

I roto i te methemoglobinemia, ka puta te "Methemoglobinemia" ina huri te "Hemoglobin" hei "Methemoglobin", nā te whakarerekētanga ira, nā tētahi atu take o waho rānei. Nā te mea kāore e taea e te "Methemoglobin" te kawe hāora, ka heke te nui o te hāora i roto i te toto, ā, ka pāngia koe e te "Cyanosis".

He aha ngā tohu o te Methemoglobinemia?

Ka rerekē ngā tohu i ia tangata, i ia tangata, ā, ka whakawhirinaki anō hoki ki te momo mate kei a koe. Me titiro tātou ki te āhua o te putanga mai o ēnei tohu.

Ngā Tohu o te Methemoglobinemia i Whiwhi

He tokomaha te hunga ka pāngia e tēnei mate i muri i te tango i ētahi rongoā whakamamae mamae, i ētahi rongoā rānei, i te pānga rānei ki ngā matū paitini . Ka kiia tēnei ko te methemoglobinemia kua whiwhihia. Ko ngā tohu ka puta ko:

• Kiri mā (kiri kōwhai)
• Te tino ngenge (te ngenge nui)
• ngoikore
• Ānini

I ētahi wā, ka pāngia te hunga whai methemoglobinemia e ngā tohu kino e hiahia ana kia aro wawe atu ki te hauora . Kei roto i ēnei ko:

• Whakapairuaki me te ruaki.
• Te hiamoe nui, te kōrero pōturi, me te puhoi o te urupare: He tohu pea ēnei nō te pouri o te pūnaha io matua .
• Te ngaronga o te māramatanga, ngā nekehanga tinana kāore e taea te whakahaere (pēnei i te haurangi): He tohu ēnei o te haurangi haurangi .
• Te tere o te manawa, te tere o te manawa, me te pōhēhē: He tohu ēnei o te mate e kiia nei ko te metabolic acidosis .

He mea nui: Ki te whakaatu tetahi i tō taha i tētahi o ēnei tohu o te mate haurangi, arā, te `(Metabolic Acidosis)` me te `(Central Nervous System Depression)` rānei, me waea tonu atu koe ki te 1990 ka waea atu ki tētahi waka tūroro .

Ngā Tohu o te Methemoglobinemia Whakatupu

He tino onge te mate methemoglobinemia whānau. He torutoru noa ngā kēhi kua pūrongohia puta noa i te ao. I runga i aua kōrero, kua wehea e ngā tākuta kia toru ngā momo matua: Momo 1, Momo 2, me te mate Hemoglobin M (HbM) .

• He maha ngā wā ka pāngia te hunga whai mate hemoglobin M (HbM) e te cyanosis (kiri kikorangi), engari he hauora tonu rātou i te nuinga o te wā.
• Ahakoa he cyanosis anō hoki te hunga whai methemoglobinemia Momo 1 (Momo 1 MetHb) , he onge tonu ētahi atu raruraru hauora nui.
• Heoi, ka taea e ngā pēpi i whānau mai me te momo methemoglobinemia momo 2 (Momo 2 MetHb) te whakawhanake i ngā raruraru pūnaha io kino i te wā e 9 marama te pakeke. Heoi, kāore ēnei pēpi e ora roa.

He aha te take e puta ai te methemoglobinemia?

Ka taea tēnei mate te tuku iho, e ai ki taku kōrero i mua ake nei, ka taea hoki te puta i muri mai i ētahi rongoā, ngā rongoā, ngā matū paitini rānei.

Ngā Take o te Methemoglobinemia i Whiwhi

• Ka taea tēnei e ngā rongoā mamae pēnei i te benzocaine me te lidocaine (ina koa ko ērā e kitea ana i roto i ngā kirimi me ngā rehu pani) me te paturopi dapsone .
• Ngā nitrates e whakamahia ana i roto i ētahi rongoāKo ngā nitrites, kei roto pea i ngā mea tiaki kai me ētahi wai puna, me te pānga ki ētahi patu taru e whakamahia ana i roto i te ahuwhenua, ētahi atu o ngā take.
• Ko te hunga e whakamahi ana i ngā raau taero whakangahau pēnei i te amyl nitrite (e mōhiotia ana ko ngā poppers), te nitrous oxide (hau kata), me ētahi rongoā whakangote i konatunatua ki ngā raau taero pēnei i te cocaine, kei te nui ake te mōrearea o ngā raruraru hauora e morearea ana ki te ora nā te nui rawa o te methemoglobin.

Ngā Take o te Methemoglobinemia Whakatupu

E rua ngā whakarerekētanga ira e puta ai te methemoglobinemia whānau (MetHb whānau).

• I ngā momo 1 me te 2 , ka whakararu te whakarerekētanga ira CYB5R i te taurite i waenga i te hemoglobin me te methemoglobin i roto i ngā toto toto whero.
• Ko te mate Hemoglobin M (HbM) ka puta mai i ngā whakarerekētanga ira i roto i ētahi ira Hemoglobin M.

He mate tuku iho ā-ira-ira te methemoglobinemia whānau. Ki te kī ngāwari, kia pāngia ai te tamaiti e te mate, me kawe e ngā mātua e rua te whakarerekētanga ira, ā, me riro mai i te tamaiti te whakarerekētanga ira mai i a rāua.

He mate tino rangatira te mate Hemoglobin M (HbM). Ko te tikanga ka taea e te tamaiti te pāngia e te mate ahakoa ka riro mai i a ia te whakarerekētanga ira mai i te mātua kotahi anake.

Me pēhea te tautuhi a ngā tākuta i tēnei?

Ka tātaritatia tēnei mate e ngā tākuta mā te tango i tō hītori hauora katoa me te whakahaere i tētahi whakamātautau tinana . Mena he tohu kei te tangata kua pāngia e te methemoglobinemia, ka pātai pea rātou mō ngā rongoā e whakamahia ana e rātou, ngā matū paitini rānei kua pāngia pea rātou.

He aha ngā whakamātautau e mahia ana hei tautuhi i tēnei?

Ko te tikanga ka mahia ēnei whakamātautau:

• Ngā Whakamātautau Toto: Ko te toto i tangohia mai i ngā uaua o te hunga whai mate pēnei he parauri pouri te tae. Ko te tikanga o tēnei tae parauri pouri kāore ngā uaua e kawe tika ana i te hāora i roto i te toto.
• Whakamātautau taumata Methemoglobin (MetHb): Mā tēnei ka ine i te nui o te methemoglobin i roto i tō toto.
• Te ngohe o te whākōkī CYB5R: Mena he iti iho i te tikanga te ngohe o tēnei whākōkī, he tohu tēnei nō te methemoglobinemia whānau mai.
• Te Tātaitanga Ira Tangata: Ki te whakapae koe he methemoglobinemia whānau tōu, ka tirohia tō DNA mō ngā huringa ira hei whakaū i te mate. Ka āwhina hoki tēnei ki te tautuhi i te momo mate.
• Te Hikohiko o te Hemoglobin:He tikanga tēnei mō te whakamātautau i te "Hemoglobin" i roto i ngā toto whero. Ka taea te whakamahi i tēnei whakamātautau hei tātaritanga i te mate hemoglobin M "(HbM).

Me pēhea te rongoā mō tēnei?

He rerekē ngā kōwhiringa maimoatanga i runga i te momo methemoglobinemia kei a koe. Hei tauira, he tino rerekē te maimoatanga mō tētahi pēpi hou i whānau mai me te momo 2 i te maimoatanga mō tētahi i pāngia e te mate nā te pānga ki tētahi matū paitini, ki te whakamahinga tarukino rānei.

• Kāore pea e hiahiatia he rongoā mō te hunga whai Methemoglobinemia Momo 1, te mate Hemoglobin M rānei . Mēnā e tika ana, ka whakamahia pea e ngā tākuta ēnei rongoā hei whakaheke i ngā taumata Methemoglobin:
• Methylene Blue: Koinei te rongoā matua mō te methemoglobinemia.
• Huaora C me te huaora B2.

Te Maimoatanga mō te Methemoglobinemia i Whiwhihia

I runga i te āhua o te mate, ka taea e te methemoglobinemia te noho hei āhuatanga ohorere hauora. I roto i ēnei āhuatanga, me whai wai māori me te hāora i roto i te uaua . He maha ngā wā, ka hoatu he methylene blue ki te hunga whai methemoglobinemia.

He aha ngā raruraru o te maimoatanga?

Mena ka tukuna tonutia te rongoā methylene blue ki tētahi tangata he mate G6PD (he mate ira anō hoki), ka puta pea he mate e kiia nei ko te hemolysis . Ko te hemolysis te pakaru wawe, te pakaru koretake rānei o ō toto whero.

Ka taea e au te whakaiti i te mōrearea o te whakawhanake i te methemoglobinemia?

• Ko te hunga kua riro mai i a rātou tētahi momo ira o tēnei mate, me karo i ngā matū paitini (hei tauira, ngā patu pepeke), ētahi rongoā, me ngā rongoā whakamoe ā-rohe maha ka taea te whakanui ake i ngā taumata methemoglobin. Mena kei a koe tēnei mate, pātai atu ki tō tākuta mō ngā mea ka pāwera pea koe.
• Ko te hunga e whakamahi ana i ngā raau taero pēnei i te amyl nitrite, te cocaine rānei, ka nui ake te tūponotanga o te whakawhanake i te methemoglobinemia. Mena kei te whakamahi koe i ēnei raau taero, ā, me āwhina koe ki te whakamutu, kōrero ki te tākuta mō ngā maimoatanga e wātea ana.

Ka aha mēnā kei ahau tēnei āhuatanga?

I te nuinga o te wā, ka taea e te maimoatanga te whakaora i ngā tohu. Ko te nuinga o te hunga whai mate Methemoglobinemia Momo 1, te mate Hemoglobin M rānei, he iti noa iho ngā tohu. I te nuinga o te wā ka ora rātou rite tonu ki te tangata kāore i te mate.

Me pēhea taku tiaki i ahau anō?

• I te nuinga o te wā, me tūpato te hunga i whānau mai me te momo "whanautanga" o te mate ki ngā rongoā me ngā matū ka taea te whakararu i te mate. Nā te mea he rerekē te āhua o te katoa, he pai ake te kōrero ki tō tākuta.
• Me karo rawa te hunga whai methemoglobinemia (Acquired MetHb) i ngā mea i puta ai te mate – pērā i ngā rongoā, ngā rongoā whakamamae mamae, ngā matū paitini rānei.

Āhea ahau me toro atu ki te tākuta?

• Mena he momo methemoglobinemia tuku iho tōu, tirohia he tākuta mēnā ka kite koe i ngā huringa o tō tinana, pērā i te ngenge, te ngoikore rānei. He tohu pea ēnei kua kore e taea e ō toto whero te kawe i te hāora puta noa i tō tinana.
• Mena ka pāngia koe e ngā tohu kino pēnei i te cyanosis (kiri kikorangi) me te haurangi, te hiamoe nui rānei, waea atu ki te 911 tonu atu, haere rānei ki te wāhanga ohorere o te hōhipera tata.

He aha ngā pātai me pātai atu e au ki te tākuta?

He mate toto tino onge te Methemoglobinemia. Ko ētahi tāngata ka pāngia e tēnei mate ira tuku iho (Congenital MetHb), engari ko te nuinga ka pāngia e tēnei mate i muri mai (Acquired MetHb). I runga i tō āhua, ka hiahia pea koe ki te pātai atu ki tō tākuta penei:

Mō te Methemoglobinemia i Whiwhi (MetHb i Whiwhi):

• He aha i pā ai tēnei ki ahau?
• Ka memeha atu rānei aku tohumate i te maimoatanga?
• Tērā pea ka hoki mai anō aku tohu?
• Me aha ahau kia kore ai e puta anō tēnei āhuatanga?

Mō te MetHb whānau Momo 1:

• He raruraru hauora nui te cyanosis (kiri kikorangi)?
• Me tango tonu rānei e au te rongoā methemoglobinemia (MetHb)?
• Tērā pea he tohu kē atu anō kei ahau?
• Ka taea e aku tamariki te tuku iho i tēnei mate?

Momo 2 o te MetHb whānau (mēnā he tamaiti):

• He aha te pānga o tēnei āhuatanga ki taku pēpi?
• He maimoatanga kei reira hei whakaiti i ngā tohumate o taku pēpi?
• He aha taku e taea ai hei āwhina i taku pēpi?
• Ki te mea he maha atu āku tamariki, ka pā anō tēnei ki a rātou?

Hei whakarāpopototanga (Karere hei tango ki te kāinga)

He mate toto onge te Methemoglobinemia e pā ana ki te kaha o ngā toto toto whero ki te kawe hāora puta noa i te tinana. Mō ētahi, he mea tuku iho, engari mō te nuinga o te tangata, nā ētahi rongoā, te pānga ki ngā matū paitini, te whakamahinga rānei o ngā raau taero whakangahau. I ētahi wā, ka pāngia te methemoglobinemia whānau (ina koa te momo 2) e ngā raruraru pūnaha io nui, engari i te nuinga o te wā kāore e pāngia e ngā raruraru hauora nui. Heoi, i ētahi wā, ka pāngia te ora e te methemoglobinemia kua riro (te methemoglobinemia kua riro).

Ko te mea nui, ki te whakaaro koe kei te tūpono koe ki te pangia e tēnei mate, kaua e wehi ki te kōrero ki te tākuta mō tēnei mea. Ka koa ia ki te āwhina i a koe.

Methemoglobinemia , Methemoglobinemia, Te mate pēpi kikorangi, Cyanosis, Te korenga o te hāora i roto i te toto, Hemoglobin, Ngā mate toto, Ngā mate ira