Kua pāngia koe e te mataku mō te rongoā whakamoe e hoatu ana ki a koe mō te pokanga? He mea noa ki ētahi tāngata te whakaaro pēnā. Engari whakaarohia te mea ka tupu mēnā kāore ētahi o ngā rongoā whakamoe e hoatu ana ki a koe i te tino tika mō tō tinana. I tēnei rā ka kōrero tātou mō tētahi āhuatanga onge, engari he mea tino nui kia mōhio koe. Koia tētahi āhuatanga e kiia nei ko te `(Pseudocholinesterase Deficiency)`.
He aha te `(Pseudocholinesterase Deficiency)`? Me mārama noa iho, me pēhea?
Āe, he roa te ahua o tēnei ingoa, kāore? Kia māmā noa iho. Ko te '(Pseudocholinesterase)' he whākōkī motuhake '(Enzyme)' i roto i tō tātou tinana. Ko tētahi o ngā mahi matua o tēnei '(Enzyme)' ko te wawahi (arā, '(metabolize)') i roto i te tinana ētahi o ngā rongoā e hoatu ana hei whakangāwari i ngā uaua , inā koa ka whakamoea tātou (e kiia ana ēnei e mātou ko '(Choline esters)'). Whakaarohia, i te wā o te pokanga, me pararutiki ō uaua mō tētahi wā. Koinei ngā rongoā e hoatu ana mō tēnā.
I roto i tētahi āhuatanga e kiia nei ko te `(Pseudocholinesterase Deficiency)`, ko te mea ka tupu ko tēnei `(Enzyme)` e kiia nei ko te `(Pseudocholinesterase)` i roto i tō tinana kāore i te nui te hanga , kāore rānei i te mahi tika . He aha te mea ka tupu? Ko ngā rongoā e hoatu ana hei whakangāwari i ngā uaua (`(Succinylcholine)` me te `(Mivacurium)` he tauira e rua o tēnei) kāore e tangohia wawetia mai i te tinana. Ka noho roa ki roto i te tinana.
Nā reira, ka noho ngoikore pea ō uaua mō te wā roa i muri i te rongoā whakamoe, ā, ka uaua pea koe ki te manawa. Ko te tikanga o tēnei, kāore pea koe e taea te neke, te manawa rānei i a koe anō kia memeha rā anō ngā pānga o te rongoā.
He pēhea te noa o tēnei āhuatanga?
Ko te tikanga, ehara tēnei āhuatanga e kiia nei ko te `(Pseudocholinesterase Deficiency)` i te mea noa . I te toharite, kotahi noa iho i roto i te 3,200, 5,000 rānei o te taupori ka pāngia e tēnei āhuatanga. Arā, he tino tokoiti.
He aha ngā tohu? Me pēhea e mōhio ai koe ki tēnei?
Ko te nuinga o te hunga whai mate pēnei kāore e mōhio kia whiwhi rā anō rātou i te momo rongoā whakangote i kōrerotia e au i mua ake nei, e kiia nei ko ngā "Choline esters." Koinei te wā e puta ai ngā tohu matua:
- Ngā uaua e tino wātea rawa ana (arā, kāore he ora) mō te wā roa atu i te mea e tika ana.
- Ahakoa ngā uaua e āwhina ana i a koe ki te manawa ka kore e mahi mō tētahi wā .
Tērā pea ka roa pea ētahi hāora ka memeha haere ēnei tohu. He rerekē tēnei wā i ia tangata, i ia tangata. I tēnei wā, ka noho tonu koe i raro i te rongoā whakamoe a tō rōpū hauora, ā, ka āwhina i a koe ki te manawa mā te "pūwero manawa", he mīhini manawa horihori, kia taea rā anō e koe te manawa ko koe anake.
He aha ngā take? Me pēhea tēnei e puta ai?
Ka taea tēnei āhuatanga (Pseudocholinesterase Deficiency) te tuku iho (arā, he mea tuku iho), ka taea rānei te whanake i muri mai i te ao..
Ngā take tuku iho
Ko te hunga whānau mai me tēnei mate, he huringa, he whakarerekētanga rānei kei roto i tētahi ira e kiia nei ko te `(BCHE)`. Ko tēnei ira `(BCHE)` te mea e kī ana ki tō tātou tinana kia hanga te whākōkī `(Pseudocholinesterase)`. Nō reira, ina he huringa kei roto i tēnei ira, he iti noa iho tēnei whākōkī e hangaia ana e tō tinana, kāore rānei e taea te hanga i te katoa.
Ngā take e puta ake ana i te wā e ora ana (I whiwhi)
I ētahi wā, ka puta pea tēnei āhuatanga (Pseudocholinesterase Deficiency) puta noa i te oranga. Ka puta pea i ngā mate maha me ētahi rongoā.
Ko ētahi mate ka pā mai ki tēnei āhuatanga:
- Te kore kai
- Ngā whara nui o te wera
- mate whatukuhu
- Mate ate
- Te ngoikore o te tairoi (te ngoikore o te mahi o te tairoi)
- Matepukupuku
- Te haputanga
Ko ētahi rongoā ka taea te whakanui ake i te mōrearea o tēnei mate ko:
- Ko nga aukati MAO (hei tauira, Phenelzine (Nardil®))
- Ngā pire ārai whānau (ngā ārai hapūtanga ā-waha)
- Ngā pata kanohi Echothiophate
- Metoclopramide
- Cyclophosphamide
- Piridostigmina
Me pēhea te tautuhi a ngā tākuta i tēnei?
Mena he uaua ki a koe te whakahaere i ō uaua, te manawa rānei i muri i te rongoā whakamoe whānui, tera pea ka whakapae tō tākuta kei te ngoikore te pseudocholinesterase. Hei whakaū i tēnei, ka taea e rātou te whakahaere i tētahi whakamātautau toto hei tirotiro i ō taumata o te whākōkī pseudocholinesterase.
Mena kei roto i tō whānau tēnei mate, ka taea e te tākuta te whakahaere whakamātautau ira hei kimi mēnā kei a koe anō hoki. Ko te tikanga o tēnei ko te tango i tētahi tauira toto me te tirotiro mēnā kei a koe te whakarerekētanga ira (BCHE).
Ki te whakapae tō tākuta kei a koe tēnei mate, ka whakamahia e rātou ētahi atu momo rongoā whakangāwari uaua kāore e whakawhirinaki ana ki te whākōkī "Pseudocholinesterase".
He aha te maimoatanga?
Ki te puta mai ngā tohu o te `(Pseudocholinesterase Deficiency)` i muri i te hoatutanga o te rongoā whakamoe whānui ki a koe, me tere pea te rapu awhina hauora. Ka tirotirohia koe e te tīma hauora kia ora ra ano koe. Ki te tika, ka noho tonu koe i raro i te rongoā whakamoe, ā, ka whakamahia he mīhini ``mīhini whakaea manawa`` hei āwhina i a koe ki te manawa kia taea ra ano e koe te manawa ko koe anake.
He aha ngā mea me tumanako atu mēnā kei a koe tēnei āhuatanga?
Mena kua tāpaetia koe kei te mate koe i te `(Pseudocholinesterase Deficiency)`, ko te mea pai rawa atu māu ko te whakamōhio atu ki ō tākuta – inā koa ko ngā tākuta ka kite i a koe mō te pokanga .
Me kōrero anō hoki e koe tēnei ki tō whānau., kātahi ka taea hoki te whakamātautau i a rātou kia kitea ai mēnā kei a rātou te whakarerekētanga ira `(BCHE)`. Mēnā koinā, me whakamōhio atu hoki rātou ki ā rātou tākuta i mua i te pokanga.
He mea pai anō hoki te mau i tētahi poroporo tohu hauora kia mōhio ai ngā tākuta mēnā me mahi pokanga ohorere koe.
Ka taea te ārai i tēnei?
He mate whānau te ngoikore o te pseudocholinesterase, kāore e taea te ārai. Heoi, ki te pāngia tētahi o tō whānau e tēnei mate, ka taea te whakamātautau i a koe mō te whakarerekētanga ira BCHE i mua i te whakamoe whānui. Ka āwhina tēnei ki te ārai i ngā raruraru i te wā o te pokanga.
Mena kei a koe te whakarerekētanga ira, tera pea ka mahue i tō tākuta ngā Choline esters ka whiriwhiri i tētahi atu rongoā whakangote. Ko te Rocuronium te rongoā whakangote e whakamahia whānuitia ana mō te hunga whai Pseudocholinesterase Deficiency.
Tērā pea ka taea e koe te whakaiti i tō tupono ki te whakawhanake i te Acquired Pseudocholinesterase Deficiency i muri mai i te oranga mā te rongoā i ngā mate taketake, pērā i te kore kai pai, te mate tākihi mau tonu rānei (CKD). Waihoki, ki te mea kei te tango koe i ētahi rongoā e whakaiti ana i te hanga o te whākōkī Pseudocholinesterase, me kōrero pea koe ki tō tākuta mō te whakarerekē i tō rongoā.
He aha ngā ārai, arā, he aha ngā rongoā kāore e pai hei whakamahi mā te hunga whai mate pēnei?
Mena kua tāpaetia koe kei te pāngia e te `(Pseudocholinesterase Deficiency)`, me karo koe i ngā momo rongoā whakangote e whai ake nei :
- Succinylcholine `(Succinylcholine)`
- Mivacurium
- Procaine
- Koroporokāina
- Benzocaine
- Tetracaine
Ngā pātai hei pātai atu ki tō tākuta
Mena kei a koe tētahi āhuatanga e kiia nei ko te "Pseudocholinesterase Deficiency", ahakoa i whānau mai koe me tēnei āhuatanga, i pāngia rānei koe e tēnei āhuatanga i muri mai, me pātai atu pea koe ki tō tākuta i ētahi pātai pēnei i:
- He aha ngā ārai tika mōku, arā, he aha ngā rongoā me karo e au?
- Nōku whānau mai tēnei mate, nō tētahi atu mate rānei i puta ai?
- He whakaaro pai rānei kia whakahaerehia he whakamātautau ira mō tōku whānau?
He āhua taumaha te haere ki te pokanga. He tokomaha o tātou e aro nui ana ki te pokanga, kāore e whakaaro ki te tūponotanga o tētahi pānga kino ki te rongoā whakamoe. Kāore he rongoā mō te Pseudocholinesterase Deficiency. Heoi, mā te mōhio mēnā kei a koe tēnei mate ka āwhina i a koe ki te karo i te ngoikore o te uaua me ngā uauatanga manawa poto ka puta i muri i te pokanga. Mena kei a koe te Pseudocholinesterase Deficiency, kōrerotia ki ō whānau. Ka taea hoki e rātou te whakamātau i te ira me te karo i ngā raruraru koretake ka puta i roto i tā rātou haerenga hauora.
Hei whakamutunga, ngā mea hei maumahara
Nō reira, he ingoa whakamataku te `(Pseudocholinesterase Deficiency)`, engari he mea nui kia mōhio koe ki tēnei. Ina koa mēnā kei te haere koe ki te pokanga, mēnā rānei kua pāngia tētahi o tō whānau e tēnei āhuatanga , he mea pai kia kōrero koe ki ō tākuta mō tēnei. Kia maumahara, ko te mōhiotanga te whakangungu pai rawa atu hei whakaora i a tātou i ngā raruraru koretake!
` Te rongoā whakamoe, te pseudocholinesterase, te ngoikore o te whākōkī, ngā raruraru pokanga, te āhua ira, te ngoikore o te uaua, ngā rongoā whakamoe











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