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ꯅꯍꯥꯛꯀꯤ ꯑꯉꯥꯡ ꯑꯗꯨꯒꯤ ꯃꯁꯂꯁꯤꯡ ꯑꯗꯨ ꯁꯣꯟꯊꯔꯀꯄꯥ ꯎꯕꯥ ꯐꯪꯕ꯭ꯔꯥ? ꯗꯨꯆꯦꯟ ꯃꯁꯜ ꯗꯤꯁ꯭ꯠꯔꯣꯐꯤ (DMD)ꯒꯤ ꯃꯔꯃꯗꯥ ꯈꯪꯖꯤꯅꯕꯤꯌꯨ

ꯅꯍꯥꯛꯀꯤ ꯑꯉꯥꯡ ꯑꯗꯨꯒꯤ ꯃꯁꯂꯁꯤꯡ ꯑꯗꯨ ꯁꯣꯟꯊꯔꯀꯄꯥ ꯎꯕꯥ ꯐꯪꯕ꯭ꯔꯥ? ꯗꯨꯆꯦꯟ ꯃꯁꯜ ꯗꯤꯁ꯭ꯠꯔꯣꯐꯤ (DMD)ꯒꯤ ꯃꯔꯃꯗꯥ ꯈꯪꯖꯤꯅꯕꯤꯌꯨ

ꯅꯍꯥꯛꯀꯤ ꯑꯉꯥꯡ ꯑꯗꯨꯅꯥ ꯂꯥꯟꯊꯦꯡꯅꯔꯤꯉꯩ ꯑꯃꯁꯨꯡ ꯁꯥꯟꯅꯔꯀꯄꯗꯒꯤ ꯈꯣꯡꯅꯥ ꯆꯠꯄꯥ ꯑꯃꯁꯨꯡ ꯊꯣꯡꯅꯥꯎ ꯍꯥꯡꯗꯣꯀꯄꯗꯥ ꯑꯋꯥꯕꯥ ꯍꯧꯔꯀꯄꯥ ꯍꯧꯔꯀꯄꯗꯨ ꯅꯍꯥꯛꯅꯥ ꯈꯪꯂꯃꯒꯅꯤ꯫ ꯅꯠꯔꯒꯥ ꯃꯈꯣꯌꯅꯥ ꯂꯦꯞꯄꯥ ꯂꯩꯇꯅꯥ ꯁꯣꯀꯄꯥ ꯑꯃꯁꯨꯡ ꯌꯥꯝꯅꯥ ꯋꯥꯅꯥ ꯊꯣꯀꯄꯥ ꯐꯥꯑꯣꯔꯤꯕꯔꯥ? ꯍꯥꯌꯔꯤꯕꯁꯤꯡ ꯑꯁꯤ ꯑꯩꯈꯣꯌꯅꯥ ꯌꯥꯝꯅꯥ ꯃꯤꯠꯌꯦꯡ ꯆꯪꯗꯕꯥ ꯑꯄꯤꯀꯄꯥ ꯋꯥꯐꯃꯁꯤꯡ ꯑꯣꯏꯅꯥ ꯎꯕꯥ ꯌꯥꯏ, ꯑꯗꯨꯕꯨ ꯃꯈꯣꯌ ꯑꯁꯤ ꯑꯔꯨꯕꯥ ꯐꯤꯚꯃꯁꯤꯡꯒꯤ ꯇꯣꯏꯅꯥ ꯊꯣꯀꯄꯥ ꯈꯨꯗꯃꯁꯤꯡ ꯑꯣꯏꯕꯥ ꯌꯥꯏ꯫ ꯉꯁꯤ ꯑꯩꯈꯣꯌꯅꯥ ꯋꯥꯔꯤ ꯁꯥꯅꯔꯤꯕꯥ ꯑꯁꯤ ꯇꯁꯦꯡꯅꯥ ꯃꯗꯨꯅꯤ, ꯃꯔꯨꯑꯣꯏꯅꯥ ꯅꯨꯄꯥꯃꯆꯥꯁꯤꯡꯗꯥ ꯃꯁꯂꯁꯤꯡ ꯇꯞꯅꯥ ꯇꯞꯅꯥ ꯁꯣꯀꯍꯜꯂꯤꯕꯥ ꯂꯥꯌꯅꯥ ꯑꯃꯅꯤ꯫

ꯗꯨꯆꯦꯟ ꯃꯁꯜ ꯗꯤꯁ꯭ꯠꯔꯣꯐꯤ (DMD) ꯍꯥꯌꯕꯁꯤ ꯀꯔꯤꯅꯣ?

ꯌꯥꯝꯅꯥ ꯂꯥꯏꯅꯥ ꯍꯥꯌꯔꯕꯗꯥ, ꯗꯨꯆꯦꯟ ꯃꯁꯜ ꯗꯤꯁ꯭ꯠꯔꯣꯐꯤ ꯅꯠꯠꯔꯒꯥ ꯊꯣꯏꯗꯣꯀꯄꯥ ꯃꯑꯣꯡꯗꯥ ꯗꯤ.ꯑꯦꯝ.ꯗꯤ . ꯃꯁꯤ ꯈ꯭ꯕꯥꯏꯗꯒꯤ ꯀꯃꯟ ꯑꯣꯏꯕꯥ ꯑꯃꯁꯨꯡ ꯁꯥꯊꯤꯕꯥ ꯃꯈꯂꯒꯤ ꯃꯁꯜ ꯗꯤꯁ꯭ꯠꯔꯣꯐꯤꯅꯤ .

ꯃꯁꯤꯒꯤ ꯃꯇꯥꯡꯗꯥ ꯑꯁꯤꯒꯨꯝꯅꯥ ꯈꯟꯊꯕꯤꯌꯨ: ꯑꯩꯈꯣꯌꯒꯤ ꯃꯁꯂꯁꯤꯡ ꯑꯁꯤ ꯏꯂꯥꯁ꯭ꯇꯤꯛ ꯔꯕ꯭ꯕꯔ ꯕꯦꯟꯗꯁꯤꯡꯒꯨꯝꯅꯥ ꯑꯣꯏ꯫ ꯂꯥꯌꯅꯥ ꯑꯁꯤꯗꯥ, ꯏꯂꯥꯁ꯭ꯇꯤꯛ ꯃꯁꯂꯁꯤꯡ ꯑꯗꯨꯒꯤ ꯃꯄꯥꯉ꯭ꯒꯜ ꯍꯟꯊꯔꯀꯏ ꯑꯃꯁꯨꯡ ꯃꯈꯣꯌꯅꯥ ꯃꯑꯣꯡ ꯆꯨꯝꯅꯥ ꯊꯕꯛ ꯇꯧꯕꯥ ꯉꯃꯗ꯭ꯔꯦ꯫ ꯃꯇꯃꯒꯤ ꯃꯇꯨꯡꯏꯟꯅꯥ, ꯀꯟꯗꯤꯁꯟ ꯑꯁꯤ ꯍꯦꯟꯅꯥ ꯐꯠꯆꯤꯜꯂꯛꯇꯕꯥ ꯅꯠꯇꯅꯥ ꯍꯦꯟꯅꯥ ꯐꯠꯆꯤꯜꯂꯀꯏ꯫

ꯗꯤ.ꯑꯦꯝ.ꯗꯤ.ꯅꯥ ꯑꯌꯥꯝꯕꯅꯥ ꯖꯦꯅꯦꯇꯤꯛ ꯑꯣꯏ, ꯍꯥꯌꯕꯗꯤ ꯃꯁꯤ ꯃꯤꯔꯣꯜ ꯑꯃꯗꯒꯤ ꯃꯤꯔꯣꯜ ꯑꯃꯗꯥ ꯌꯧꯍꯜꯂꯤ . ꯃꯔꯨꯑꯣꯏꯅꯥ ꯃꯁꯤ ꯑꯦꯛꯁ-ꯂꯤꯉ꯭ꯛ ꯇꯧꯔꯕꯥ ꯔꯤꯁꯦꯁꯤꯕ ꯇ꯭ꯔꯦꯠ ꯑꯃꯥ ꯑꯣꯏꯅꯥ ꯇ꯭ꯔꯥꯟꯁꯃꯤꯠ ꯇꯧꯏ . ꯃꯁꯤꯅꯥ ꯇꯥꯀꯄꯗꯤ ꯀꯔꯤꯒꯨꯝꯕꯥ ꯃꯃꯥ ꯑꯗꯨꯅꯥ ꯂꯥꯌꯅꯥ ꯑꯁꯤꯒꯤ ꯀꯦꯔꯤꯌꯔ ꯑꯣꯏꯔꯕꯗꯤ ꯃꯍꯥꯛꯀꯤ ꯑꯉꯥꯡ ꯑꯗꯨꯅꯥ ꯃꯍꯥꯛꯀꯤ ꯃꯐꯃꯗꯒꯤ ꯂꯧꯕꯥ ꯌꯥꯏ꯫ ꯑꯗꯨꯝ ꯑꯣꯏꯅꯃꯛ, ꯀꯦꯁ ꯈꯔꯗꯗꯤ, ꯆꯥꯎꯔꯥꯛꯅꯥ ꯀꯦꯁ 30%ꯗꯤ, ꯀꯟꯗꯤꯁꯟ ꯑꯁꯤ ꯑꯅꯧꯕꯥ ꯖꯦꯅꯦꯇꯤꯛ ꯃ꯭ꯌꯨꯇꯦꯁꯟ ꯑꯃꯅꯥ ꯃꯔꯝ ꯑꯣꯏꯗꯨꯅꯥ ꯊꯣꯀꯍꯅꯕꯥ ꯌꯥꯏ , ꯀꯔꯤꯒꯨꯝꯕꯥ ꯏꯃꯨꯡ ꯑꯗꯨꯒꯤ ꯀꯅꯥꯒꯨꯝꯕꯥ ꯑꯃꯠꯇꯅꯥ ꯃꯃꯥꯡꯗꯥ ꯂꯥꯌꯅꯥ ꯑꯁꯤ ꯂꯩꯔꯃꯗ꯭ꯔꯕꯁꯨ꯫ ꯃꯁꯤꯅꯥ ꯇꯥꯀꯄꯗꯤ ꯀꯔꯤꯒꯨꯝꯕꯥ ꯃꯇꯃꯗꯥ ꯃꯁꯤ ꯔꯦꯟꯗꯝ ꯑꯣꯏꯅꯥ ꯊꯣꯀꯄꯥ ꯌꯥꯏ꯫

DMD ꯀꯟꯗꯤꯁꯟ ꯑꯁꯤꯅꯥ ꯀꯅꯥꯅꯥ ꯈ꯭ꯕꯥꯏꯗꯒꯤ ꯍꯦꯟꯅꯥ ꯁꯣꯀꯍꯜꯂꯤꯕꯒꯦ?

ꯗꯨꯆꯦꯟ ꯃꯁꯜ ꯗꯤꯁ꯭ꯠꯔꯣꯐꯤꯅꯥ ꯃꯔꯨꯑꯣꯏꯅꯥ ꯅꯨꯄꯥꯃꯆꯥꯁꯤꯡꯗꯥ ꯁꯣꯀꯍꯜꯂꯤ . ꯑꯗꯨꯝ ꯑꯣꯏꯅꯃꯛ, ꯂꯥꯌꯅꯥ ꯑꯁꯤ ꯊꯣꯀꯍꯜꯂꯤꯕꯥ ꯖꯤꯅꯒꯤ ꯀꯦꯔꯤꯌꯔ ꯑꯣꯏꯔꯤꯕꯥ ꯅꯨꯄꯤꯃꯆꯥꯁꯤꯡꯗꯥ ꯀꯔꯤꯒꯨꯝꯕꯥ ꯃꯇꯃꯗꯥ ꯃꯌꯥꯏ ꯑꯣꯏꯕꯥ ꯂꯥꯏꯑꯣꯡ ꯎꯠꯄꯥ ꯌꯥꯏ꯫ ꯑꯗꯨꯝ ꯑꯣꯏꯅꯃꯛ ꯃꯁꯤ ꯌꯥꯝꯅꯥ ꯀꯃꯟ ꯑꯣꯏꯗꯦ꯫

ꯃꯁꯜ ꯁꯣꯟꯊꯕꯒꯤ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯑꯁꯤ ꯃꯍꯧꯁꯥꯅꯥ ꯆꯍꯤ 2 ꯑꯃꯁꯨꯡ 4ꯒꯤ ꯃꯔꯛꯇꯥ ꯍꯧꯏ, ꯑꯗꯨꯕꯨ ꯑꯉꯥꯡ ꯈꯔꯗꯤ ꯆꯥꯎꯔꯥꯛꯅꯥ ꯆꯍꯤ 6 ꯁꯨꯗ꯭ꯔꯤꯉꯩꯗꯥ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯑꯁꯤ ꯎꯠꯄꯥ ꯍꯧꯔꯀꯄꯥ ꯌꯥꯏ꯫ ꯃꯔꯝ ꯑꯗꯨꯅꯥ ꯀꯔꯤꯒꯨꯝꯕꯥ ꯅꯍꯥꯛꯅꯥ ꯆꯤꯡꯅꯕꯥ ꯂꯩꯔꯕꯗꯤ ꯃꯦꯗꯤꯀꯦꯂꯒꯤ ꯄꯥꯎꯇꯥꯛ ꯂꯧꯕꯅꯥ ꯈ꯭ꯕꯥꯏꯗꯒꯤ ꯐꯩ꯫

DMD ꯑꯁꯤ ꯀꯌꯥꯝ ꯀꯃꯟ ꯑꯣꯏꯕꯒꯦ?

ꯃꯁꯤ ꯌꯥꯝꯅꯥ ꯁꯥꯊꯤꯕꯥ ꯀꯟꯗꯤꯁꯟ ꯑꯃꯅꯤ ꯍꯥꯌꯔꯕꯁꯨ, ꯃꯁꯤ ꯀꯅꯥꯒꯨꯝꯕꯥ ꯑꯃꯅꯥ ꯈꯜꯂꯤꯕꯥ ꯑꯗꯨꯒꯨꯝꯅꯥ ꯌꯥꯝꯅꯥ ꯊꯨꯅꯥ ꯊꯣꯀꯄꯥ ꯅꯠꯇꯦ꯫ ꯁ꯭ꯇꯦꯇꯤꯁ꯭ꯇꯤꯀꯦꯂꯅꯥ ꯇꯥꯛꯂꯤ ꯃꯗꯨꯗꯤ ꯃꯥꯂꯦꯝ ꯁꯤꯅꯕꯥ ꯊꯨꯡꯅꯥ ꯅꯨꯄꯥ ꯑꯉꯥꯡ ꯳꯶꯰꯰ꯒꯤ ꯃꯅꯨꯡꯗꯥ ꯆꯥꯎꯔꯥꯛꯅꯥ ꯑꯃꯥ ꯗꯤ.ꯑꯦꯝ.ꯗꯤ. DMD ꯑꯁꯤ ꯌꯥꯝꯅꯥ ꯁꯥꯊꯤꯕꯥ, ꯏꯅꯍꯦꯔꯤꯇꯦꯗ ꯃꯥꯌꯣꯄꯦꯊꯤꯁꯤꯡ , ꯅꯠꯠꯔꯒꯥ ꯁ꯭ꯀꯦꯂꯦꯇꯜ ꯃꯁꯂꯁꯤꯡꯒꯤ ꯂꯥꯌꯅꯥꯁꯤꯡꯒꯤ ꯃꯅꯨꯡꯗꯥ ꯈ꯭ꯕꯥꯏꯗꯒꯤ ꯀꯃꯟ ꯑꯣꯏꯕꯥ ꯑꯃꯅꯤ꯫

DMD ꯑꯁꯤ ꯁꯤꯍꯅꯕꯥ ꯌꯥꯕꯥ ꯂꯥꯌꯅꯥ ꯑꯃꯅꯤ ꯍꯥꯌꯕꯁꯤꯅꯤ?

ꯍꯣꯌ, ꯅꯨꯡꯉꯥꯏꯇꯕꯥ ꯋꯥꯐꯝ ꯑꯃꯅꯥ, ꯗꯤ.ꯑꯦꯝ.ꯗꯤ .ꯑꯇꯣꯞꯄꯥ ꯂꯥꯌꯅꯥ ꯑꯃꯅꯤ꯫ ꯀꯟꯗꯤꯁꯟ ꯑꯁꯤꯅꯥ ꯅꯥꯕꯥ ꯃꯤꯑꯣꯏ ꯀꯌꯥꯗꯤ ꯂꯪꯁ ꯑꯃꯁꯨꯡ ꯍꯥꯔꯇꯇꯥ ꯂꯩꯕꯥ ꯀꯃꯞꯂꯤꯀꯦꯁꯅꯁꯤꯡꯅꯥ ꯁꯤꯍꯜꯂꯤ꯫ ꯑꯗꯨꯕꯨ ꯋꯥꯈꯜ ꯋꯥꯕꯥ ꯂꯩꯔꯣꯏꯗꯕꯅꯤ, ꯍꯧꯖꯤꯛ ꯂꯩꯔꯤꯕꯥ ꯂꯥꯌꯦꯡꯁꯤꯡ ꯑꯁꯤꯒꯥ ꯂꯣꯌꯅꯅꯥ ꯅꯍꯥꯛꯀꯤ ꯄꯨꯟꯁꯤ ꯁꯥꯡꯗꯣꯀꯄꯥ ꯑꯃꯁꯨꯡ ꯄꯨꯟꯁꯤꯒꯤ ꯈꯔꯥ ꯐꯕꯥ ꯃꯒꯨꯟ ꯑꯃꯥ ꯊꯝꯅꯕꯒꯤ ꯄꯥꯝꯕꯩꯁꯤꯡ ꯂꯩꯔꯤ꯫

DMDꯒꯤ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯑꯗꯨ ꯀꯔꯤꯅꯣ?

ꯑꯩꯈꯣꯌꯅꯥ ꯃꯃꯥꯡꯗꯥ ꯍꯥꯌꯈꯤꯕꯒꯨꯝꯅꯥ, DMDꯒꯤ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯑꯁꯤ ꯃꯍꯧꯁꯥꯅꯥ ꯆꯍꯤ 2 ꯑꯃꯁꯨꯡ 4ꯒꯤ ꯃꯔꯛꯇꯥ ꯍꯧꯏ, ꯑꯗꯨꯕꯨ ꯀꯔꯤꯒꯨꯝꯕꯥ ꯃꯇꯃꯗꯥ ꯃꯈꯣꯌ ꯑꯁꯤ ꯑꯉꯥꯡ ꯑꯣꯏꯔꯤꯉꯩꯗꯥ ꯍꯧꯔꯀꯄꯥ ꯌꯥꯏ, ꯅꯠꯠꯔꯒꯥ ꯑꯉꯥꯡ ꯑꯣꯏꯔꯤꯉꯩꯗꯥ ꯇꯨꯡꯗꯥ ꯐꯥꯎꯕꯥ ꯂꯥꯀꯄꯥ ꯌꯥꯏ꯫

DMDꯅꯥ ꯃꯇꯃꯒꯤ ꯃꯇꯨꯡꯏꯟꯅꯥ ꯃꯁꯜ ꯁꯣꯟꯊꯍꯅꯕꯅꯥ ꯃꯔꯝ ꯑꯣꯏꯗꯨꯅꯥ, ꯈ꯭ꯕꯥꯏꯗꯒꯤ ꯀꯃꯟ ꯑꯣꯏꯕꯥ ꯂꯥꯏꯑꯣꯡꯁꯤꯡꯗꯤ:

  • ꯃꯁꯜ ꯁꯣꯟꯊꯕꯥ ꯑꯃꯁꯨꯡ ꯃꯥꯡ-ꯇꯥꯛꯅꯤꯡꯉꯥꯏ ꯑꯣꯏꯕꯥ (muscle atrophy) ꯍꯥꯌꯕꯁꯤ ꯇꯞꯅꯥ ꯇꯞꯅꯥ ꯍꯦꯅꯒꯠꯂꯀꯄꯥ, ꯈꯣꯡ ꯑꯃꯁꯨꯡ ꯈꯣꯡꯗꯥ ꯍꯧꯔꯀꯄꯥ꯫ ꯀꯟꯗꯤꯁꯟ ꯑꯁꯤꯅꯥ ꯃꯈꯨꯠ, ꯈꯣꯡ ꯑꯃꯁꯨꯡ ꯍꯀꯆꯥꯡꯒꯤ ꯑꯇꯩ ꯁꯔꯨꯀꯁꯤꯡꯗꯥ ꯌꯥꯝꯅꯥ ꯅꯦꯝꯅꯥ ꯁꯣꯀꯍꯜꯂꯤ꯫
  • ꯀꯥꯜꯐ ꯃꯁꯜ ꯍꯥꯏꯄꯔꯠꯔꯣꯐꯤ (ꯃꯁꯤꯅꯥ ꯇꯥꯀꯄꯗꯤ ꯀꯥꯜꯐ ꯃꯁꯜ ꯑꯗꯨ ꯍꯦꯟꯅꯥ ꯆꯥꯎꯈꯠꯂꯀꯏ)꯫ ꯃꯁꯤ ꯃꯁꯜ ꯐꯤꯕꯔꯁꯤꯡ ꯑꯁꯤ ꯐꯦꯇꯤ ꯇꯤꯁꯨ ꯑꯃꯁꯨꯡ ꯀꯅꯦꯛꯇꯤꯚ ꯇꯤꯁꯨꯁꯤꯡꯅꯥ ꯃꯍꯨꯠ ꯁꯤꯜꯂꯀꯄꯥ ꯃꯇꯃꯗꯥ ꯊꯣꯀꯏ꯫
  • ꯊꯣꯉꯅꯥꯑꯣꯗꯥ ꯆꯠꯄꯗꯥ ꯑꯋꯥꯕꯥ꯫
  • ꯃꯇꯃꯒꯤ ꯃꯇꯨꯡꯏꯟꯅꯥ ꯈꯣꯡꯅꯥ ꯆꯠꯄꯗꯥ ꯑꯋꯥꯕꯥ꯫
  • ꯆꯥꯡ ꯅꯥꯏꯅꯥ ꯁꯣꯀꯄꯥ꯫
  • ꯋꯥꯗꯂꯤꯡ ꯒꯦꯠ ꯑꯃꯥ꯫
  • ꯈꯣꯡꯗꯥ ꯆꯠꯄꯥ꯫
  • ꯊꯨꯅꯥ ꯋꯥꯈꯜ ꯇꯥꯗꯕꯥ (fatigue)꯫

ꯈꯅꯕꯤꯌꯨ, ꯀꯔꯤꯒꯨꯝꯕꯥ ꯅꯍꯥꯛꯀꯤ ꯃꯆꯥꯅꯨꯄꯥ ꯑꯗꯨꯅꯥ ꯐ꯭ꯂꯣꯔꯗꯥ ꯁꯥꯟꯅꯕꯗꯒꯤ ꯊꯣꯔꯛꯇꯨꯅꯥ, ꯃꯍꯥꯛꯀꯤ ꯃꯈꯨꯠꯁꯤꯡ ꯑꯗꯨ ꯐ꯭ꯂꯣꯔꯗꯥ ꯆꯦꯠꯅꯥ ꯊꯃꯖꯤꯜꯂꯕꯗꯤ, ꯃꯗꯨꯒꯤ ꯃꯇꯨꯡꯗꯥ ꯃꯍꯥꯛꯀꯤ ꯃꯈꯨꯠ ꯑꯗꯨ ꯃꯍꯥꯛꯀꯤ ꯈꯨꯎꯗꯥ ꯊꯃꯖꯤꯜꯂꯕꯗꯤ, ꯑꯃꯁꯨꯡ ꯃꯍꯥꯛꯀꯤ ꯍꯀꯆꯥꯡ ꯑꯗꯨ ꯌꯥꯝꯅꯥ ꯋꯥꯅꯥ ꯇꯞꯅꯥ ꯇꯞꯅꯥ ꯊꯃꯖꯤꯜꯂꯕꯗꯤ, ꯃꯗꯨꯁꯨ ꯂꯥꯌꯅꯥ ꯑꯁꯤꯒꯤ ꯂꯥꯏꯑꯣꯡ ꯑꯃꯥ ꯑꯣꯏꯕꯥ ꯌꯥꯏ (ꯃꯁꯤꯕꯨ ꯒꯧꯔꯁꯀꯤ ꯂꯥꯏꯑꯣꯡꯁꯨ ꯀꯧꯏ)꯫

ꯃꯁꯤꯒꯤ ꯃꯊꯛꯇꯥ, DMDꯅꯥ ꯑꯇꯩ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯊꯣꯀꯍꯅꯕꯥ ꯌꯥꯏ:

  • ꯍꯥꯔꯠ ꯃꯁꯂꯒꯤ ꯂꯥꯌꯅꯥ (Cardiomyopathy)꯫
  • ꯁ꯭ꯕꯔ ꯍꯣꯅꯕꯥ ꯋꯥꯕꯥ ꯑꯃꯁꯨꯡ ꯁ꯭ꯕꯔ ꯍꯣꯅꯕꯥ ꯋꯥꯕꯥ꯫
  • ꯀꯣꯒꯅꯤꯇꯤꯚ ꯏꯝꯄꯥꯌꯔꯃꯦꯟꯇ ꯑꯃꯁꯨꯡ ꯂꯔꯅꯤꯡꯒꯤ ꯈꯦꯠꯅꯕꯥ ꯂꯩꯕꯥ꯫
  • ꯋꯥ ꯉꯥꯡꯕꯥ ꯑꯃꯁꯨꯡ ꯂꯣꯜ ꯁꯦꯃꯒꯠꯄꯗꯥ ꯊꯦꯡꯊꯕꯥ꯫
  • ꯗꯤꯚꯦꯂꯄꯃꯦꯟꯇꯗꯥ ꯊꯦꯡꯊꯕꯥ꯫
  • ꯁ꯭ꯀꯣꯂꯤꯑꯣꯁꯤꯁ (Scoliosis)꯫
  • ꯁꯣꯔꯠ ꯁ꯭ꯇꯦꯆꯔ꯫

DMD (ꯀꯦꯔꯤꯌꯔ) ꯊꯣꯀꯍꯜꯂꯤꯕꯥ ꯖꯤꯟ ꯑꯁꯤ ꯄꯨꯔꯤꯕꯥ ꯅꯨꯄꯤꯃꯆꯥꯁꯤꯡꯒꯤ ꯃꯅꯨꯡꯗꯥ 2.5% ꯑꯃꯁꯨꯡ 20%ꯒꯤ ꯃꯔꯛꯇꯥ ꯃꯌꯥꯏ ꯑꯣꯏꯕꯥ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯂꯥꯀꯄꯥ ꯌꯥꯏ, ꯑꯗꯨꯕꯨ ꯃꯍꯧꯁꯥꯅꯥ ꯃꯈꯣꯌ ꯑꯁꯤ ꯌꯥꯝꯅꯥ ꯁꯥꯊꯤꯕꯥ ꯑꯣꯏꯗꯦ꯫

ꯀꯔꯤꯒꯤꯗꯃꯛ ꯑꯁꯤꯒꯨꯝꯕꯥ ꯗꯤ.ꯑꯦꯝ.ꯗꯤ.

ꯗꯤ.ꯑꯦꯝ.ꯗꯤ.ꯒꯤ ꯃꯔꯨꯑꯣꯏꯕꯥ ꯃꯔꯃꯗꯤ ꯑꯩꯈꯣꯌꯒꯤ ꯃꯁꯂꯁꯤꯡꯕꯨ ꯍꯀꯆꯥꯡ ꯐꯅꯥ ꯊꯝꯅꯕꯒꯤꯗꯃꯛ ꯇꯉꯥꯏ ꯐꯗꯕꯥ ꯄ꯭ꯔꯣꯇꯤꯟ ꯑꯃꯥ ꯑꯣꯏꯔꯤꯕꯥ ꯗꯤꯁ꯭ꯠꯔꯣꯐꯤꯟ ꯄꯨꯊꯣꯀꯄꯒꯤ ꯀꯣꯗ ꯇꯧꯔꯤꯕꯥ ꯖꯤꯅꯗꯥ ꯃ꯭ꯌꯨꯇꯦꯁꯟ ꯇꯧꯕꯅꯤ꯫ ꯃꯁꯤꯒꯤ ꯄ꯭ꯔꯣꯇꯤꯟ ꯑꯁꯤ ꯗꯤꯁ꯭ꯠꯔꯣꯐꯤꯟ ꯑꯁꯤ ꯃꯁꯂꯁꯤꯡꯒꯤ ꯁ꯭ꯠꯔꯀꯆꯔꯦꯜ ꯌꯨꯅꯤꯠ ꯑꯃꯥ ꯑꯣꯏꯅꯥ ꯊꯕꯛ ꯇꯧꯕꯥ ꯗꯤꯁ꯭ꯠꯔꯣꯐꯤꯟ-ꯒ꯭ꯂꯥꯏꯀꯣꯞꯔꯣꯇꯤꯟ ꯀꯃꯞꯂꯦꯛꯁ (ꯗꯤ.ꯖꯤ.ꯁꯤ.) ꯒꯤꯗꯃꯛꯇꯥ ꯌꯥꯝꯅꯥ ꯃꯔꯨꯑꯣꯏ꯫

DMDꯗꯥ, ꯗꯤꯁ꯭ꯠꯔꯣꯐꯤꯟ ꯑꯃꯁꯨꯡ DGC ꯄ꯭ꯔꯣꯇꯤꯟ ꯑꯅꯤꯃꯛ ꯃꯥꯡꯈꯤ, ꯑꯃꯁꯨꯡ ꯑꯔꯣꯏꯕꯗꯥ ꯃꯁꯜ ꯁꯦꯜ ꯁꯤꯍꯅꯕꯥ (necrosis) ꯊꯣꯀꯍꯜꯂꯤ꯫DMDꯅꯥ ꯅꯥꯕꯥ ꯃꯤꯑꯣꯏ ꯑꯃꯗꯥ ꯍꯀꯁꯦꯜ ꯐꯕꯥ ꯃꯁꯂꯁꯤꯡꯒꯤꯗꯃꯛ ꯃꯊꯧ ꯇꯥꯕꯥ ꯗꯤꯁ꯭ꯠꯔꯣꯐꯤꯅꯒꯤ ꯆꯥꯡꯒꯤ 5%ꯗꯒꯤ ꯇꯥꯅꯥ ꯂꯩ꯫

DMDꯅꯥ ꯅꯥꯕꯥ ꯃꯤꯑꯣꯏꯁꯤꯡꯅꯥ ꯆꯍꯤ ꯌꯥꯃꯈꯠꯂꯀꯄꯒꯥ ꯂꯣꯌꯅꯅꯥ, ꯃꯈꯣꯌꯒꯤ ꯃꯁꯂꯁꯤꯡꯅꯥ ꯑꯁꯤꯕꯥ ꯁꯦꯂꯁꯤꯡ ꯑꯁꯤ ꯑꯅꯧꯕꯥ ꯁꯦꯂꯁꯤꯡꯅꯥ ꯃꯍꯨꯠ ꯁꯤꯅꯕꯥ ꯉꯃꯗꯦ꯫ ꯃꯗꯨꯒꯤ ꯃꯍꯨꯠꯇꯥ , ꯀꯅꯦꯛꯇꯤꯕ ꯇꯤꯁꯨ ꯑꯃꯁꯨꯡ ꯑꯦꯗꯤꯄꯣꯖ ꯇꯤꯁꯨꯅꯥ ꯃꯁꯜ ꯐꯤꯕꯔꯒꯤ ꯃꯍꯨꯠ ꯁꯤꯜꯂꯤ꯫

ꯑꯩꯈꯣꯌꯅꯥ ꯃꯃꯥꯡꯗꯥ ꯍꯥꯌꯈꯤꯕꯒꯨꯝꯅꯥ ꯗꯤ.ꯑꯦꯝ.ꯗꯤ.ꯅꯥ ꯑꯦꯛꯁ-ꯂꯤꯉ꯭ꯛ ꯇꯧꯕꯥ ꯔꯤꯁꯦꯁꯤꯕ ꯀꯟꯗꯤꯁꯟ ꯑꯃꯅꯤ꯫ ꯑꯗꯨꯝ ꯑꯣꯏꯅꯃꯛ, ꯆꯥꯎꯔꯥꯛꯅꯥ ꯀꯦꯁ 30%ꯗꯥ, ꯃꯁꯤ ꯔꯦꯟꯗꯝ ꯑꯣꯏꯅꯥ, ꯏꯃꯨꯡꯒꯤ ꯍꯤꯁ꯭ꯇꯔꯤ ꯑꯃꯠꯇꯥ ꯌꯥꯎꯗꯅꯥ ꯊꯣꯀꯄꯥ ꯌꯥꯏ꯫

"ꯑꯦꯛꯁ-ꯂꯤꯉ꯭ꯛ" ꯍꯥꯌꯕꯁꯤꯅꯥ ꯗꯤ.ꯑꯦꯝ.ꯗꯤ.ꯒꯤ ꯗꯥꯌꯠꯕ ꯂꯧꯔꯤꯕꯥ ꯖꯤꯟ ꯑꯁꯤ ꯑꯦꯛꯁ ꯀ꯭ꯔꯣꯃꯣꯖꯣꯃꯗꯥ ꯂꯩ ꯍꯥꯌꯕꯅꯤ꯫ ꯑꯗꯣꯝꯅꯥ ꯈꯉꯕꯤꯔꯤꯕꯥ ꯑꯗꯨꯅꯤ ꯅꯨꯄꯥꯁꯤꯡꯗꯥ X ꯀ꯭ꯔꯣꯃꯣꯖꯣꯝ ꯑꯃꯥ ꯑꯃꯁꯨꯡ Y ꯀ꯭ꯔꯣꯃꯣꯖꯣꯝ ꯑꯃꯥ ꯂꯩ, ꯑꯃꯁꯨꯡ ꯅꯨꯄꯤꯁꯤꯡꯗꯥ X ꯀ꯭ꯔꯣꯃꯣꯖꯣꯝ ꯑꯅꯤ ꯂꯩ꯫

"ꯔꯤꯁꯦꯁꯤꯚ" ꯍꯥꯌꯕꯁꯤꯅꯥ ꯃꯤꯑꯣꯏ ꯑꯃꯅꯥ ꯂꯥꯌꯅꯥ ꯑꯁꯤ ꯊꯣꯀꯍꯜꯂꯤꯕꯥ ꯖꯤꯅꯒꯤ ꯀꯣꯄꯤ ꯑꯅꯤ ꯂꯩꯔꯕꯈꯛꯇꯗꯥ ꯂꯥꯌꯅꯥ ꯑꯁꯤ ꯂꯥꯛꯀꯅꯤ ꯍꯥꯌꯕꯅꯤ꯫ ꯑꯗꯨꯕꯨ ꯅꯨꯄꯥꯁꯤꯡꯗꯥ X ꯀ꯭ꯔꯣꯃꯣꯖꯣꯝ ꯑꯃꯥ ꯂꯩ꯫ ꯑꯗꯨꯅꯥ ꯀꯔꯤꯒꯨꯝꯕꯥ DMD ꯊꯣꯀꯍꯜꯂꯤꯕꯥ ꯖꯤꯟ ꯃ꯭ꯌꯨꯇꯦꯁꯟ ꯑꯗꯨ X ꯀ꯭ꯔꯣꯃꯣꯖꯣꯝ ꯑꯗꯨꯗꯥ ꯂꯩꯔꯕꯗꯤ ꯃꯈꯣꯌꯅꯥ DMD ꯐꯪꯒꯅꯤ꯫ ꯅꯨꯄꯤꯃꯆꯥ ꯑꯃꯅꯥ DMD ꯂꯧꯅꯕꯒꯤꯗꯃꯛ, ꯃꯍꯥꯛꯀꯤ X ꯀ꯭ꯔꯣꯃꯣꯖꯣꯝ ꯑꯅꯤꯃꯛꯇꯥ ꯖꯤꯟ ꯃ꯭ꯌꯨꯇꯦꯁꯟ ꯑꯁꯤ ꯂꯩꯒꯗꯕꯅꯤ꯫ ꯃꯗꯨ ꯌꯥꯝꯅꯥ ꯊꯦꯡꯅꯩ꯫ ꯑꯗꯨꯕꯨ ꯀꯔꯤꯒꯨꯝꯕꯥ ꯃꯍꯥꯛꯀꯤ ꯃ꯭ꯌꯨꯇꯦꯁꯟ ꯑꯗꯨ ꯑꯦꯛꯁ ꯀ꯭ꯔꯣꯃꯣꯖꯣꯝ ꯑꯃꯈꯛꯇꯗꯥ ꯂꯩꯔꯕꯗꯤ ꯃꯍꯥꯛ ꯂꯥꯌꯅꯥ ꯑꯁꯤꯒꯤ ꯀꯦꯔꯤꯌꯔ ꯑꯃꯥ ꯑꯣꯏꯒꯅꯤ꯫

DMD ꯑꯁꯤ ꯀꯔꯝꯅꯥ ꯈꯪꯗꯣꯀꯄꯒꯦ?

ꯀꯔꯤꯒꯨꯝꯕꯥ ꯅꯍꯥꯛꯀꯤ ꯑꯉꯥꯡ ꯑꯗꯨꯅꯥ DMDꯒꯤ ꯈꯨꯗꯃꯁꯤꯡ ꯎꯕꯥ ꯐꯪꯂꯕꯗꯤ, ꯗꯣꯛꯇꯔ ꯑꯗꯨꯅꯥ ꯑꯍꯥꯅꯕꯗꯥ ꯐꯤꯖꯤꯀꯦꯜ ꯑꯦꯀꯖꯥꯃꯤꯅꯦꯁꯟ , ꯅ꯭ꯌꯨꯔꯣꯂꯣꯖꯤꯀꯦꯜ ꯑꯦꯀꯖꯥꯃꯤꯅꯦꯁꯟ ꯑꯃꯁꯨꯡ ꯃꯁꯜ ꯑꯦꯀꯖꯥꯃꯤꯅꯦꯁꯟ ꯑꯃꯥ ꯄꯥꯡꯊꯣꯛꯀꯅꯤ꯫ ꯃꯈꯣꯌꯅꯥ ꯅꯍꯥꯛꯀꯤ ꯑꯉꯥꯡ ꯑꯗꯨꯒꯤ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯑꯃꯁꯨꯡ ꯃꯦꯗꯤꯀꯦꯜ ꯍꯤꯁ꯭ꯇꯔꯤꯒꯤ ꯃꯇꯥꯡꯗꯁꯨ ꯍꯪꯒꯅꯤ꯫

ꯀꯔꯤꯒꯨꯝꯕꯥ ꯗꯣꯛꯇꯔ ꯑꯗꯨꯅꯥ ꯑꯉꯥꯡ ꯑꯗꯨꯗꯥ DMD ꯂꯩꯔꯦ ꯍꯥꯌꯅꯥ ꯆꯤꯡꯅꯔꯕꯗꯤ ꯃꯈꯥꯗꯥ ꯄꯤꯔꯤꯕꯥ ꯇꯦꯁ꯭ꯇꯁꯤꯡ ꯑꯁꯤ ꯄꯥꯡꯊꯣꯀꯄꯥ ꯌꯥꯏ:

  • ꯀ꯭ꯔꯤꯌꯦꯇꯤꯟ ꯀꯤꯅꯥꯁ (CK) ꯕ꯭ꯂꯗ ꯇꯦꯁ꯭ꯠ (CK) ꯕ꯭ꯂꯗ ꯇꯦꯁ꯭ꯠ: ꯃꯁꯂꯁꯤꯡ ꯁꯣꯀꯍꯜꯂꯕꯥ ꯃꯇꯃꯗꯥ ꯀ꯭ꯔꯤꯌꯦꯇꯤꯟ ꯀꯤꯅꯥꯁ ꯀꯧꯕꯥ ꯑꯦꯅꯖꯥꯏꯝ ꯑꯃꯥ ꯏꯗꯥ ꯁꯦꯃꯒꯠꯂꯀꯏ꯫ ꯃꯔꯝ ꯑꯗꯨꯅꯥ, ꯀꯔꯤꯒꯨꯝꯕꯥ ꯁꯤ.ꯀꯦ.ꯒꯤ ꯊꯥꯛ ꯑꯁꯤ ꯋꯥꯡꯈꯠꯂꯕꯗꯤ, ꯃꯁꯤ ꯗꯤ.ꯑꯦꯝ.ꯗꯤ.ꯒꯤ ꯈꯨꯗꯝ ꯑꯃꯥ ꯑꯣꯏꯕꯥ ꯌꯥꯏ꯫ ꯃꯁꯤꯒꯤ ꯊꯥꯛ ꯑꯁꯤ ꯃꯍꯧꯁꯥꯅꯥ ꯆꯍꯤ 2ꯒꯤ ꯃꯅꯨꯡꯗꯥ ꯈ꯭ꯕꯥꯏꯗꯒꯤ ꯋꯥꯡꯕꯥ ꯑꯣꯏ, ꯑꯃꯁꯨꯡ ꯅꯣꯔꯃꯦꯂꯗꯒꯤ ꯁꯔꯨꯛ 10-20 ꯍꯦꯟꯅꯥ ꯋꯥꯡꯕꯥ ꯌꯥꯏ꯫
  • ꯖꯦꯅꯦꯇꯤꯛ ꯕ꯭ꯂꯗ ꯇꯦꯁ꯭ꯠ: ꯗꯤꯁ꯭ꯠꯔꯣꯐꯤꯟ ꯖꯤꯟ ꯑꯗꯨ ꯃꯄꯨꯡꯐꯥꯅꯥ ꯅꯠꯠꯔꯒꯥ ꯁꯔꯨꯛ ꯈꯔꯗꯤ ꯃꯥꯡꯈꯤꯕꯥ ꯎꯠꯄꯥ ꯖꯦꯅꯦꯇꯤꯛ ꯇꯦꯁ꯭ꯠ ꯑꯃꯅꯥ ꯗꯤ.ꯑꯦꯝ.ꯗꯤ.
  • ꯃꯁꯜ ꯕꯥꯏꯑꯣꯞꯁꯤ (muscle biopsy) : ꯗꯣꯛꯇꯔꯅꯥ ꯅꯍꯥꯛꯀꯤ ꯑꯉꯥꯡ ꯑꯗꯨꯒꯤ ꯃꯄꯥꯟꯊꯪꯕꯥ ꯁꯔꯨꯛ ꯅꯠꯠꯔꯒꯥ ꯈꯣꯡꯄꯥꯛ ꯑꯗꯨꯗꯒꯤ ꯃꯁꯂꯒꯤ ꯑꯄꯤꯀꯄꯥ ꯁꯦꯝꯄꯜ ꯑꯃꯥ ꯂꯧꯕꯥ ꯌꯥꯏ꯫ ꯁ꯭ꯄꯦꯁꯤꯑꯦꯂꯤꯁ꯭ꯠ ꯑꯃꯅꯥ ꯁꯦꯝꯄꯜ ꯑꯗꯨ ꯃꯥꯏꯛꯔꯣꯁ꯭ꯀꯣꯄꯀꯤ ꯃꯈꯥꯗꯥ ꯌꯦꯡꯗꯨꯅꯥ ꯗꯤ.ꯑꯦꯝ.ꯗꯤ.ꯒꯤ ꯈꯨꯗꯝ ꯑꯃꯠꯇꯥ ꯂꯩꯕ꯭ꯔꯥ ꯍꯥꯌꯕꯗꯨ ꯌꯦꯡꯒꯅꯤ꯫
  • ꯏꯂꯦꯛꯠꯔꯣꯀꯥꯔꯗꯤꯑꯣꯒ꯭ꯔꯥꯐ (EKG): DMDꯅꯥ ꯑꯌꯥꯝꯕꯥ ꯃꯇꯃꯗꯥ ꯍꯥꯔꯇꯇꯥ ꯁꯣꯀꯍꯅꯕꯅꯥ ꯃꯔꯝ ꯑꯣꯏꯗꯨꯅꯥ, ꯗꯣꯛꯇꯔꯅꯥ DMDꯒꯤ ꯑꯀꯛꯅꯕꯥ ꯂꯥꯏꯑꯣꯡ ꯑꯃꯠꯇꯥ ꯂꯩꯕ꯭ꯔꯥ ꯍꯥꯌꯕꯗꯨ ꯌꯦꯡꯁꯤꯟꯅꯕꯥ ꯑꯃꯁꯨꯡ ꯍꯥꯔꯇꯀꯤ ꯍꯀꯁꯦꯜ ꯑꯗꯨ ꯌꯦꯡꯁꯤꯟꯅꯕꯥ EKG ꯑꯃꯥ ꯄꯥꯡꯊꯣꯛꯀꯅꯤ꯫

ꯃꯁꯤꯒꯤ ꯂꯥꯏꯌꯦꯡꯁꯤꯡ ꯑꯁꯤ ꯀꯔꯤꯅꯣ?

ꯅꯨꯡꯉꯥꯏꯇꯕꯥ ꯋꯥꯐꯝ ꯑꯃꯅꯥ ꯍꯧꯖꯤꯛꯀꯤ ꯑꯣꯏꯅꯥ ꯗꯤ.ꯑꯦꯝ.ꯗꯤ . ꯃꯔꯝ ꯑꯗꯨꯅꯥ ꯂꯥꯏꯌꯦꯡꯕꯒꯤ ꯃꯔꯨꯑꯣꯏꯕꯥ ꯄꯥꯟꯗꯃꯗꯤ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯀꯟꯠꯔꯣꯜ ꯇꯧꯕꯥ ꯑꯃꯁꯨꯡ ꯑꯉꯥꯡ ꯑꯗꯨꯒꯤ ꯄꯨꯟꯁꯤꯒꯤ ꯃꯒꯨꯟ ꯑꯗꯨ ꯌꯥꯔꯤꯕꯃꯈꯩ ꯈ꯭ꯕꯥꯏꯗꯒꯤ ꯐꯕꯥ ꯃꯑꯣꯡꯗꯥ ꯊꯝꯕꯅꯤ꯫

ꯃꯈꯥꯗꯥ ꯄꯤꯔꯤꯕꯥ ꯑꯁꯤ ꯗꯤ.ꯑꯦꯝ.ꯗꯤ.ꯒꯤ ꯁꯄꯣꯔꯇꯤꯕ ꯇ꯭ꯔꯤꯠꯃꯦꯟꯇꯁꯤꯡꯅꯤ:

  • ꯀꯣꯔꯇꯤꯀꯣꯁ꯭ꯇꯦꯔꯣꯏꯗꯁꯤꯡ: ꯄ꯭ꯔꯦꯗꯅꯤꯁꯣꯂꯣꯟ ꯑꯃꯁꯨꯡ ꯗꯦꯐ꯭ꯂꯥꯖꯥꯀꯣꯔꯇꯒꯨꯝꯕꯥ ꯁ꯭ꯇꯦꯔꯣꯏꯗ ꯍꯤꯗꯥꯀꯁꯤꯡꯅꯥ ꯃꯁꯜ ꯁꯣꯟꯊꯍꯅꯕꯗꯥ ꯃꯇꯦꯡ ꯄꯥꯡꯏ, ꯂꯪꯁꯀꯤ ꯐꯉ꯭ꯀꯁꯟ ꯐꯒꯠꯍꯅꯕꯗꯥ ꯃꯇꯦꯡ ꯄꯥꯡꯏ, ꯁ꯭ꯀꯣꯂꯤꯑꯣꯁꯤꯁ ꯇꯞꯅꯥ ꯇꯞꯅꯥ ꯁꯣꯀꯍꯜꯂꯤ, ꯍꯥꯔꯇꯀꯤ ꯃꯁꯜ ꯁꯣꯟꯊꯕꯒꯤ ꯆꯥꯡ ꯍꯟꯊꯍꯜꯂꯤ (ꯀꯥꯔꯗꯤꯑꯣꯃꯥꯌꯣꯄꯦꯊꯤ) ꯑꯃꯁꯨꯡ ꯄꯨꯟꯁꯤ ꯁꯥꯡꯗꯣꯀꯍꯜꯂꯤ꯫
  • ꯀꯥꯔꯗꯤꯑꯣꯃꯥꯌꯣꯄꯦꯊꯤꯒꯤ ꯍꯤꯗꯥꯀꯁꯤꯡ: ꯑꯦꯁꯤꯏ ꯏꯅꯍꯤꯕꯤꯇꯔꯁꯤꯡ ꯑꯃꯁꯨꯡ/ꯅꯠꯠꯔꯒꯥ ꯕꯦꯇꯥ-ꯕ꯭ꯂꯣꯀꯔꯁꯤꯡꯒꯨꯝꯕꯥ ꯍꯤꯗꯥꯀꯁꯤꯡ ꯉꯟꯅꯥ ꯍꯧꯗꯣꯀꯄꯅꯥ ꯍꯥꯔꯠ ꯃꯁꯜ ꯁꯣꯟꯊꯕꯥ ꯀꯟꯠꯔꯣꯜ ꯇꯧꯕꯥ ꯉꯝꯃꯤ ꯑꯃꯁꯨꯡ ꯍꯥꯔꯠ ꯑꯦꯇꯦꯀꯁꯤꯡ ꯊꯤꯡꯕꯥ ꯉꯝꯃꯤ꯫
  • ꯐꯤꯖꯤꯀꯦꯜ ꯊꯦꯔꯥꯄꯤ: ꯐꯤꯖꯤꯀꯦꯜ ꯊꯦꯔꯥꯄꯤꯒꯤ ꯃꯔꯨꯑꯣꯏꯕꯥ ꯄꯥꯟꯗꯃꯗꯤ ꯃꯁꯂꯁꯤꯡ, ꯇꯦꯟꯗꯣꯅꯁꯤꯡ ꯑꯃꯁꯨꯡ ꯈꯣꯡꯗꯥ ꯃꯇꯝ ꯆꯨꯞꯄꯒꯤ ꯑꯣꯏꯅꯥ ꯇꯞꯅꯥ ꯇꯞꯅꯥ ꯁꯣꯀꯄꯥ ꯀꯟꯠꯔꯦꯀꯆꯔꯁꯤꯡ ꯊꯤꯡꯕꯅꯤ꯫ ꯃꯁꯤꯗꯥ ꯃꯍꯧꯁꯥꯅꯥ ꯑꯀꯛꯅꯕꯥ ꯁ꯭ꯠꯔꯦꯆꯤꯡ ꯑꯦꯛꯁꯔꯁꯥꯏꯖꯁꯤꯡ ꯌꯥꯎꯏ꯫
  • ꯁ꯭ꯄꯥꯏꯅꯦꯜ ꯁ꯭ꯇꯦꯅꯣꯁꯤꯁ ꯑꯃꯁꯨꯡ ꯃꯁꯜ ꯁꯣꯟꯊꯕꯒꯤ ꯁꯔꯖꯔꯤ: ꯁꯥꯊꯤꯕꯥ ꯀꯦꯁꯁꯤꯡꯗꯥ, ꯃꯁꯜ ꯁꯣꯟꯊꯕꯥ ꯊꯤꯡꯅꯕꯥ ꯁꯔꯖꯔꯤ ꯇꯧꯕꯥ ꯃꯊꯧ ꯇꯥꯕꯥ ꯌꯥꯏ꯫ ꯁ꯭ꯄꯥꯏꯅꯦꯜ ꯁ꯭ꯇꯦꯅꯣꯁꯤꯁ ꯀꯣꯀꯍꯟꯅꯕꯥ ꯁꯔꯖꯔꯤꯅꯥ ꯂꯪꯁꯀꯤ ꯐꯉ꯭ꯀꯁꯟ ꯑꯃꯁꯨꯡ ꯁ꯭ꯕꯔ ꯍꯣꯅꯕꯥ ꯐꯒꯠꯍꯅꯕꯥ ꯉꯝꯃꯤ꯫
  • ꯑꯦꯛꯁꯔꯁꯥꯏꯖ: ꯅꯍꯥꯛꯀꯤ ꯑꯉꯥꯡꯒꯤ ꯗꯣꯛꯇꯔꯅꯥ ꯑꯌꯥꯝꯕꯥ ꯃꯇꯃꯗꯥ ꯃꯈꯥ ꯇꯥꯅꯥ ꯃꯁꯜ ꯁꯣꯟꯊꯕꯥ ꯊꯤꯡꯅꯕꯥ ꯇꯞꯅꯥ ꯇꯞꯅꯥ ꯑꯦꯛꯁꯔꯁꯥꯏꯖ ꯇꯧꯅꯕꯥ ꯄꯥꯎꯇꯥꯛ ꯄꯤꯒꯅꯤ꯫ ꯃꯁꯤ ꯃꯍꯧꯁꯥꯅꯥ ꯄꯨꯜ ꯑꯦꯛꯁꯔꯁꯥꯏꯖ ꯑꯃꯁꯨꯡ ꯔꯤꯛꯔꯤꯌꯦꯁꯅꯦꯜ ꯑꯦꯛꯇꯤꯚꯤꯇꯤꯁꯤꯡꯒꯥ ꯂꯣꯌꯅꯅꯥ ꯄꯥꯡꯊꯣꯀꯏ꯫

ꯑꯇꯣꯞꯄꯥ ꯁꯄꯣꯔꯇꯤꯕ ꯇ꯭ꯔꯤꯠꯃꯦꯟꯇꯁꯤꯡꯒꯤ ꯃꯅꯨꯡꯗꯥ ꯃꯈꯥꯗꯥ ꯄꯤꯔꯤꯕꯁꯤꯡ ꯑꯁꯤ ꯌꯥꯑꯣꯔꯤ:

  • ꯃꯣꯕꯤꯂꯤꯇꯤ ꯑꯦꯗꯁꯤꯡ: ꯕ꯭ꯔꯦꯁ, ꯀꯦꯟ, ꯑꯃꯁꯨꯡ ꯍꯨꯏꯂꯆꯦꯌꯥꯔ꯫
  • ꯔꯦꯁ꯭ꯄꯤꯔꯦꯇꯔꯤ ꯄ꯭ꯔꯣꯕ꯭ꯂꯦꯃꯁꯤꯡꯒꯤꯗꯃꯛ ꯇ꯭ꯔꯦꯀꯤꯑꯣꯁ꯭ꯇꯣꯃꯤ ꯑꯃꯁꯨꯡ ꯑꯦꯁꯤꯁ꯭ꯇꯦꯟꯇ ꯚꯦꯟꯇꯤꯂꯦꯁꯟ꯫

ꯍꯧꯈꯤꯕꯥ ꯆꯍꯤ ꯇꯔꯥꯒꯤ ꯈꯨꯖꯤꯡ ꯈꯔꯁꯤꯗꯥ, ꯁꯄꯣꯔꯇꯤꯚ ꯀꯦꯌꯔ ꯁꯔꯚꯤꯁꯁꯤꯡꯗꯥ ꯑꯍꯣꯡꯕꯥ ꯂꯥꯀꯄꯒꯥ ꯂꯣꯌꯅꯅꯥ DMDꯅꯥ ꯅꯥꯕꯥ ꯃꯤꯑꯣꯏꯁꯤꯡꯒꯤ ꯄꯨꯟꯁꯤ ꯃꯍꯤꯡ ꯑꯁꯤ ꯌꯥꯝꯅꯥ ꯍꯦꯅꯒꯠꯂꯛꯂꯤ꯫

ꯍꯧꯖꯤꯛ ꯑꯅꯧꯕꯥ ꯗ꯭ꯔꯒ ꯀꯌꯥ ꯑꯃꯥ ꯀ꯭ꯂꯤꯅꯤꯀꯦꯜ ꯇꯦꯁ꯭ꯇꯤꯡ ꯇꯧꯔꯤ ꯃꯗꯨꯅꯥ ꯗꯤ.ꯑꯦꯝ.ꯗꯤ. "ꯑꯦꯛꯁꯣꯟ ꯁ꯭ꯀꯤꯄꯤꯡ" (ꯗꯤꯁ꯭ꯠꯔꯣꯐꯤꯟ ꯖꯤꯅꯒꯤ ꯃꯥꯡꯈꯤꯕꯥ ꯅꯠꯠꯔꯒꯥ ꯃ꯭ꯌꯨꯇꯦꯁꯟ ꯇꯧꯔꯕꯥ ꯁꯔꯨꯛ ꯑꯃꯥ "ꯁ꯭ꯞꯂꯥꯏꯁ" ꯇꯧꯕꯥ ꯃꯦꯊꯗ ꯑꯃꯥ)ꯒꯨꯝꯕꯥ ꯑꯅꯧꯕꯥ ꯂꯥꯌꯦꯡ ꯀꯌꯥ ꯑꯃꯥ ꯍꯟꯗꯛꯇꯥ ꯑꯦꯐ.ꯗꯤ.ꯑꯦ.(ꯐꯨꯗ ꯑꯃꯁꯨꯡ ꯗ꯭ꯔꯒ ꯑꯦꯗꯃꯤꯅꯤꯁ꯭ꯠꯔꯦꯁꯟ)ꯅꯥ ꯑꯌꯥꯕꯥ ꯄꯤꯈ꯭ꯔꯦ꯫ ꯑꯗꯨꯝ ꯑꯣꯏꯅꯃꯛ, ꯂꯥꯏꯌꯦꯡꯁꯤꯡ ꯑꯁꯤ ꯌꯥꯝꯅꯥ ꯑꯀꯛꯅꯕꯥ ꯖꯦꯅꯦꯇꯤꯛ ꯃ꯭ꯌꯨꯇꯦꯁꯟ ꯂꯩꯕꯥ ꯃꯤꯑꯣꯏ ꯈꯔꯈꯛꯇꯗꯥ ꯁꯤꯖꯤꯟꯅꯕꯥ ꯌꯥꯏ꯫ ꯂꯥꯌꯦꯡꯁꯤꯡ ꯑꯁꯤꯅꯥ ꯃꯁꯂꯁꯤꯡꯗꯥ ꯗꯤꯁ꯭ꯠꯔꯣꯐꯤꯟ ꯄ꯭ꯔꯣꯇꯤꯅꯒꯤ ꯆꯥꯡ ꯍꯦꯅꯒꯠꯂꯕꯁꯨ, ꯃꯈꯣꯌꯅꯥ ꯍꯧꯖꯤꯛ ꯐꯥꯑꯣꯕꯥ ꯄꯥꯉ꯭ꯒꯜ ꯑꯃꯁꯨꯡ ꯍꯀꯆꯥꯡꯒꯤ ꯊꯕꯛ ꯊꯧꯔꯃꯗꯥ ꯃꯁꯛ ꯊꯣꯀꯄꯥ ꯑꯍꯣꯡꯕꯥ ꯄꯨꯔꯀꯄꯥ ꯉꯃꯗ꯭ꯔꯤ꯫

ꯃꯁꯤꯒꯤ ꯗꯤ.ꯑꯦꯝ.ꯗꯤ.ꯒꯤ ꯀꯟꯗꯤꯁꯟ ꯑꯁꯤ ꯊꯤꯡꯕꯥ ꯉꯃꯒꯗ꯭ꯔꯥ?

DMD ꯑꯁꯤ ꯍꯦꯔꯤꯇꯦꯖ ꯀꯟꯗꯤꯁꯟ ꯑꯃꯅꯤ ꯃꯔꯝ ꯑꯗꯨꯅꯥ ꯃꯁꯤ ꯊꯤꯡꯅꯕꯥ ꯅꯍꯥꯛꯅꯥ ꯇꯧꯕꯥ ꯌꯥꯕꯥ ꯀꯔꯤꯁꯨ ꯂꯩꯇꯦ . ꯀꯦꯁꯁꯤꯡꯒꯤ ꯆꯥꯎꯔꯥꯛꯅꯥ ꯁꯔꯨꯛ ꯑꯍꯨꯝ ꯊꯣꯀꯄꯒꯤ ꯑꯃꯗꯤ ꯔꯦꯟꯗꯝ ꯑꯣꯏꯅꯥ ꯊꯣꯀꯏ, ꯏꯃꯨꯡꯒꯤ ꯍꯤꯁ꯭ꯇꯔꯤ ꯑꯃꯠꯇꯥ ꯂꯩꯇꯦ꯫

ꯀꯔꯤꯒꯨꯝꯕꯥ ꯅꯍꯥꯛꯅꯥ ꯑꯉꯥꯡ ꯑꯃꯥ ꯄꯣꯛꯅꯕꯥ ꯍꯣꯠꯅꯗ꯭ꯔꯤꯉꯩꯗꯥ ꯅꯍꯥꯛꯀꯤ ꯑꯉꯥꯡꯁꯤꯡꯗꯥ DMD ꯅꯠꯠꯔꯒꯥ ꯑꯇꯩ ꯖꯦꯅꯦꯇꯤꯛ ꯀꯟꯗꯤꯁꯅꯁꯤꯡ ꯄꯤꯕꯒꯤ ꯔꯤꯁ꯭ꯛ ꯂꯩꯔꯕꯗꯤ, ꯖꯦꯅꯦꯇꯤꯛ ꯀꯥꯎꯟꯁꯦꯂꯤꯡꯒꯤ ꯃꯇꯥꯡꯗꯥ ꯈꯟꯅꯕꯤꯌꯨ꯫ꯃꯁꯤꯒꯤ ꯃꯇꯥꯡꯗꯥ ꯅꯍꯥꯛꯀꯤ ꯗꯣꯛꯇꯔꯒꯥ ꯇꯥꯟꯅꯧ꯫ ꯀꯦꯁ ꯈꯔꯗꯗꯤ, ꯃꯤꯔꯣꯜꯂꯤꯉꯩ ꯃꯇꯃꯗꯥ ꯇꯣꯏꯅꯥ ꯄ꯭ꯔꯤꯅꯦꯇꯦꯜ ꯇꯦꯁ꯭ꯠ ꯇꯧꯕꯅꯥ ꯗꯤ.ꯑꯦꯝ.ꯗꯤ.

ꯇꯨꯡꯗꯥ ꯀꯔꯤ ꯃꯈꯂꯒꯤ ꯐꯤꯚꯝ ꯂꯥꯛꯀꯅꯤ ꯍꯥꯌꯅꯥ ꯊꯥꯖꯕꯥ ꯌꯥꯕꯒꯦ (ꯄ꯭ꯔꯣꯒ꯭ꯅꯣꯁꯤꯁ)?

ꯗꯤ.ꯑꯦꯝ.ꯗꯤ.ꯅꯥ ꯅꯥꯕꯥ ꯃꯤꯑꯣꯏꯁꯤꯡꯗꯥ ꯑꯌꯥꯝꯕꯅꯥ ꯄ꯭ꯔꯣꯒ꯭ꯔꯦꯁꯤꯚ ꯄ꯭ꯔꯣꯒ꯭ꯅꯣꯁꯤꯁ ꯑꯁꯤ ꯌꯥꯝꯅꯥ ꯐꯠꯇꯦ . ꯃꯁꯤꯅꯥ ꯄ꯭ꯔꯣꯒ꯭ꯔꯦꯁꯤꯚ ꯗꯤꯁꯑꯦꯕꯤꯂꯤꯇꯤ ꯊꯣꯀꯍꯜꯂꯤ, ꯑꯃꯁꯨꯡ DMDꯅꯥ ꯅꯥꯕꯥ ꯑꯉꯥꯡ ꯀꯌꯥꯗꯤ ꯆꯍꯤ 12 ꯁꯨꯔꯀꯄꯗꯥ ꯍꯨꯏꯂꯆꯦꯌꯥꯔꯗꯥ ꯆꯠꯂꯤ, DMDꯅꯥ ꯉꯟꯅꯥ ꯁꯤꯍꯅꯕꯁꯨ ꯌꯥꯏ꯫

DMDꯅꯥ ꯅꯥꯕꯥ ꯃꯤꯑꯣꯏ ꯑꯃꯒꯤ ꯄꯨꯟꯁꯤꯒꯤ ꯃꯇꯝ ꯑꯁꯤ ꯀꯌꯥꯅꯣ?

DMDꯅꯥ ꯅꯥꯕꯥ ꯃꯤꯑꯣꯏꯁꯤꯡꯅꯥ ꯑꯌꯥꯝꯕꯗꯤ ꯆꯍꯤ 25 ꯁꯨꯔꯀꯄꯗꯥ ꯀꯟꯗꯤꯁꯟ ꯑꯁꯤꯅꯥ ꯁꯤꯕꯥ ꯌꯥꯏ, ꯑꯗꯨꯕꯨ ꯁꯄꯣꯔꯇꯤꯚ ꯀꯦꯌꯔꯗꯥ ꯑꯍꯣꯡꯕꯥ ꯂꯥꯀꯄꯅꯥ ꯃꯔꯝ ꯑꯣꯏꯗꯨꯅꯥ ꯍꯧꯖꯤꯛꯇꯤ ꯃꯤꯑꯣꯏ ꯀꯌꯥꯅꯥ ꯍꯦꯟꯅꯥ ꯍꯤꯡꯂꯤ꯫

ꯁꯤꯕꯥ ꯑꯁꯤ ꯑꯌꯥꯝꯕꯗꯤ ꯁ꯭ꯕꯔ ꯍꯣꯅꯕꯥ ꯋꯥꯕꯥ (breathing) ꯅꯠꯠꯔꯒꯥ ꯀꯥꯔꯗꯤꯌꯦꯛ ꯀꯃꯞꯂꯤꯀꯦꯁꯅꯁꯤꯡꯅꯥ ꯊꯣꯀꯍꯅꯕꯅꯤ꯫ ꯅ꯭ꯌꯨꯃꯣꯅꯤꯌꯥ, ꯆꯤꯟꯖꯥꯀꯒꯨꯝꯕꯥ ꯃꯄꯥꯅꯒꯤ ꯄꯣꯠꯁꯛ ꯑꯃꯒꯤ ꯑꯦꯁ꯭ꯄꯤꯔꯦꯁꯟ, ꯅꯠꯠꯔꯒꯥ ꯑꯦꯌꯔꯋꯦ (airway obstruction) ꯑꯁꯤꯅꯁꯨ ꯁꯤꯍꯅꯕꯥ ꯌꯥꯏ꯫

DMDꯅꯥ ꯅꯥꯕꯥ ꯃꯤꯑꯣꯏ ꯑꯃꯕꯨ ꯀꯔꯝꯅꯥ ꯌꯦꯡꯁꯤꯅꯕꯤꯒꯅꯤ?

ꯀꯔꯤꯒꯨꯝꯕꯥ ꯅꯍꯥꯛꯅꯥ DMDꯅꯥ ꯅꯥꯕꯥ ꯃꯤꯑꯣꯏ ꯑꯃꯕꯨ ꯌꯦꯡꯁꯤꯜꯂꯤꯕꯥ ꯑꯣꯏꯔꯕꯗꯤ, ꯃꯈꯣꯌꯒꯤꯗꯃꯛꯇꯥ ꯑꯦꯗꯣꯕꯣꯛꯁ ꯇꯧꯕꯥ ꯍꯥꯌꯕꯁꯤ ꯌꯥꯝꯅꯥ ꯃꯔꯨꯑꯣꯏ, ꯃꯈꯣꯌꯕꯨ ꯈ꯭ꯕꯥꯏꯗꯒꯤ ꯐꯕꯥ ꯃꯦꯗꯤꯀꯦꯜ ꯀꯦꯌꯔ ꯑꯃꯁꯨꯡ ꯊꯦꯔꯥꯄꯤ ꯐꯪꯍꯅꯕꯗꯥ ꯃꯇꯦꯡ ꯄꯥꯡꯏ , ꯃꯔꯝ ꯑꯗꯨꯅꯥ ꯃꯈꯣꯌꯅꯥ ꯈ꯭ꯕꯥꯏꯗꯒꯤ ꯐꯕꯥ ꯄꯨꯟꯁꯤꯒꯤ ꯃꯒꯨꯟ ꯂꯩꯕꯥ ꯉꯃꯒꯅꯤ꯫

ꯅꯍꯥꯛ ꯑꯃꯁꯨꯡ ꯅꯍꯥꯛꯀꯤ ꯏꯃꯨꯡ-ꯃꯅꯨꯡꯅꯥ ꯆꯞ ꯃꯥꯟꯅꯕꯥ ꯑꯦꯛꯁꯄꯔꯤꯌꯦꯟꯁ ꯂꯩꯔꯕꯥ ꯑꯇꯩ ꯃꯤꯑꯣꯏꯁꯤꯡꯒꯥ ꯎꯅꯅꯕꯥ ꯁꯄꯣꯔꯠ ꯒ꯭ꯔꯨꯞ ꯑꯃꯗꯥ ꯌꯥꯎꯕꯥ ꯍꯥꯌꯕꯁꯤꯁꯨ ꯑꯐꯕꯥ ꯋꯥꯈꯜꯂꯣꯟ ꯑꯃꯥ ꯑꯣꯏꯕꯥ ꯌꯥꯏ꯫ ꯅꯍꯥꯛ ꯅꯁꯥꯃꯛ ꯅꯠꯇꯕꯥ ꯅꯠꯇꯦ ꯍꯥꯌꯕꯥ ꯈꯉꯕꯗꯁꯨ ꯑꯆꯧꯕꯥ ꯄꯨꯛꯅꯤꯡ ꯊꯧꯒꯠꯄꯥ ꯑꯃꯥ ꯑꯣꯏꯕꯥ ꯌꯥꯏ꯫

ꯑꯩꯒꯤ ꯑꯉꯥꯡ ꯑꯗꯨꯅꯥ DMDꯒꯤ ꯃꯇꯥꯡꯗꯥ ꯀꯗꯥꯏꯗꯥ ꯗꯣꯛꯇꯔꯒꯥ ꯇꯥꯟꯅꯒꯗꯒꯦ?

ꯀꯔꯤꯒꯨꯝꯕꯥ ꯅꯍꯥꯛꯀꯤ ꯑꯉꯥꯡ ꯑꯗꯨ DMD ꯂꯩꯔꯦ ꯍꯥꯌꯅꯥ ꯈꯪꯂꯕꯗꯤ, ꯃꯈꯣꯌꯅꯥ ꯂꯥꯏꯌꯦꯡꯅꯕꯥ ꯑꯃꯁꯨꯡ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯌꯦꯡꯁꯤꯟꯅꯕꯥ ꯃꯈꯣꯌꯒꯤ ꯃꯦꯗꯤꯀꯦꯜ ꯇꯤꯃꯗꯥ ꯆꯥꯡ ꯅꯥꯏꯅꯥ ꯌꯦꯡꯁꯤꯅꯕꯥ ꯃꯊꯧ ꯇꯥꯒꯅꯤ꯫

ꯅꯍꯥꯛꯀꯤ ꯑꯉꯥꯡ ꯑꯗꯨꯒꯤ DMD ꯀꯟꯗꯤꯁꯟ ꯑꯗꯨ ꯈꯪꯖꯤꯅꯕꯗꯥ ꯅꯍꯥꯛꯀꯤꯗꯃꯛꯇꯥ ꯑꯋꯥꯕꯥ ꯑꯣꯏꯕꯥ ꯌꯥꯏ꯫ ꯑꯗꯨꯕꯨ ꯅꯍꯥꯛꯀꯤ ꯃꯦꯗꯤꯀꯦꯜ ꯇꯤꯃꯅꯥ ꯅꯍꯥꯛꯀꯤ ꯑꯉꯥꯡꯒꯤ ꯂꯥꯏꯑꯣꯡꯁꯤꯡꯒꯥ ꯆꯨꯅꯕꯥ ꯁ꯭ꯠꯔꯀꯆꯔꯦꯜ ꯃꯦꯅꯦꯖꯃꯦꯟꯇ ꯄ꯭ꯂꯥꯟ ꯑꯃꯥ ꯄꯤꯒꯅꯤ꯫ ꯅꯍꯥꯛꯀꯤ ꯑꯉꯥꯡ ꯑꯗꯨꯒꯤ ꯍꯀꯁꯦꯂꯗꯥ ꯃꯤꯠꯌꯦꯡ ꯊꯝꯕꯥ ꯑꯃꯁꯨꯡ ꯃꯈꯣꯌꯅꯥ ꯃꯊꯧ ꯇꯥꯕꯥ ꯁꯄꯣꯔꯠ ꯑꯗꯨ ꯁꯣꯌꯗꯅꯥ ꯐꯪꯍꯅꯕꯥ ꯍꯥꯌꯕꯁꯤ ꯌꯥꯝꯅꯥ ꯃꯔꯨꯑꯣꯏ꯫ ꯅꯤꯡꯁꯤꯡꯕꯤꯌꯨ, ꯅꯍꯥꯛꯀꯤ ꯃꯦꯗꯤꯀꯦꯜ ꯇꯤꯃꯅꯥ ꯃꯇꯝ ꯄꯨꯝꯅꯃꯛꯇꯥ ꯅꯍꯥꯛ, ꯅꯍꯥꯛꯀꯤ ꯏꯃꯨꯡ-ꯃꯅꯨꯡ ꯑꯃꯁꯨꯡ ꯅꯍꯥꯛꯀꯤ ꯑꯉꯥꯡ ꯑꯗꯨꯕꯨ ꯃꯇꯦꯡ ꯄꯥꯡꯅꯕꯥ ꯂꯩꯔꯤ꯫

ꯑꯔꯣꯏꯕꯗꯥ, ꯃꯁꯤ ꯅꯤꯡꯁꯤꯡꯕꯤꯌꯨ (ꯇꯦꯛ-ꯍꯣꯝ ꯃꯦꯁꯦꯖ)

ꯗꯨꯆꯦꯟ ꯃꯁꯜ ꯗꯤꯁ꯭ꯠꯔꯣꯐꯤ (DMD) ꯑꯁꯤ ꯌꯥꯝꯅꯥ ꯁꯥꯊꯤꯕꯥ, ꯄꯨꯟꯁꯤ ꯆꯨꯞꯄꯥ ꯂꯥꯀꯄꯥ ꯀꯟꯗꯤꯁꯟ ꯑꯃꯅꯤ꯫ ꯑꯗꯨꯝ ꯑꯣꯏꯅꯃꯛ, ꯑꯦꯋꯥꯔꯅꯦꯁ, ꯉꯟꯅꯥ ꯈꯪꯗꯣꯀꯄꯥ, ꯑꯃꯁꯨꯡ ꯃꯇꯤꯛ ꯆꯥꯕꯥ ꯃꯦꯗꯤꯀꯦꯜ ꯑꯦꯗꯚꯥꯏꯖꯔꯤ ꯑꯃꯁꯨꯡ ꯁꯄꯣꯔꯇꯤꯚ ꯀꯦꯌꯔ ꯄꯤꯕꯅꯥ ꯑꯉꯥꯡ ꯑꯃꯒꯤ ꯄꯨꯟꯁꯤꯒꯤ ꯃꯒꯨꯟ ꯑꯗꯨ ꯌꯥꯔꯤꯕꯃꯈꯩ ꯋꯥꯡꯅꯥ ꯊꯝꯕꯗꯥ ꯃꯇꯦꯡ ꯄꯥꯡꯏ꯫

ꯅꯤꯡꯁꯤꯡꯕꯤꯌꯨ: ꯅꯍꯥꯛ ꯅꯁꯥꯃꯛ ꯅꯠꯇꯦ꯫ ꯗꯣꯛꯇꯔꯁꯤꯡ, ꯐꯤꯖꯤꯀꯦꯜ ꯊꯦꯔꯥꯄꯤꯁ꯭ꯇꯁꯤꯡ, ꯀꯥꯎꯟꯁꯦꯂꯔꯁꯤꯡ ꯑꯃꯁꯨꯡ ꯑꯇꯩ ꯁꯄꯣꯔꯠ ꯒ꯭ꯔꯨꯄꯁꯤꯡꯅꯥ ꯅꯍꯥꯛ ꯑꯃꯁꯨꯡ ꯅꯍꯥꯛꯀꯤ ꯑꯉꯥꯡ ꯑꯗꯨꯕꯨ ꯃꯇꯦꯡ ꯄꯥꯡꯅꯕꯥ ꯂꯩ꯫ ꯑꯅꯧꯕꯥ ꯂꯥꯌꯦꯡꯁꯤꯡꯒꯤ ꯃꯇꯥꯡꯗꯥ ꯔꯤꯁꯔꯆ ꯇꯧꯕꯥ ꯑꯁꯤ ꯃꯇꯝ ꯄꯨꯝꯅꯃꯛꯇꯥ ꯆꯠꯊꯔꯤ꯫ ꯃꯔꯝ ꯑꯗꯨꯅꯥ ꯑꯥꯁꯥ ꯊꯥꯗꯣꯛꯂꯣꯏꯗꯕꯅꯤ꯫ ꯈ꯭ꯕꯥꯏꯗꯒꯤ ꯃꯔꯨꯑꯣꯏꯕꯥ ꯋꯥꯐꯃꯗꯤ ꯅꯍꯥꯛꯀꯤ ꯑꯉꯥꯡ ꯑꯗꯨꯕꯨ ꯅꯨꯡꯁꯤꯕꯥ, ꯌꯦꯡꯁꯤꯅꯕꯥ ꯑꯃꯁꯨꯡ ꯄꯨꯛꯅꯤꯡ ꯊꯧꯒꯠꯄꯥ ꯑꯁꯤꯅꯤ꯫

ꯀꯔꯤꯒꯨꯝꯕꯥ ꯅꯍꯥꯛꯀꯤ ꯑꯉꯥꯡ ꯑꯗꯨꯒꯤ ꯃꯁꯂꯁꯤꯡ ꯅꯠꯠꯔꯒꯥ ꯈꯣꯡꯅꯥ ꯆꯠꯄꯒꯤ ꯑꯋꯥꯕꯥ ꯑꯃꯥ ꯂꯩꯔꯕꯗꯤ, ꯃꯗꯨ ꯑꯄꯤꯀꯄꯥ ꯋꯥꯐꯝ ꯑꯃꯥ ꯑꯣꯏꯅꯥ ꯂꯧꯔꯣꯏꯗꯕꯅꯤ꯫ꯄꯥꯎꯇꯥꯛ ꯂꯧꯅꯕꯒꯤꯗꯃꯛ ꯈꯨꯗꯛꯇꯥ ꯀ꯭ꯕꯥꯂꯤꯐꯥꯏꯗ ꯗꯣꯛꯇꯔ ꯑꯃꯒꯥ ꯇꯥꯟꯅꯧ꯫ ꯂꯥꯌꯅꯥ ꯑꯁꯤ ꯉꯟꯅꯥ ꯈꯪꯗꯣꯀꯄꯥ ꯃꯇꯃꯗꯥ, ꯃꯁꯤꯕꯨ ꯍꯦꯟꯅꯥ ꯂꯥꯌꯊꯣꯀꯍꯜꯂꯒꯅꯤ꯫


` ꯗꯨꯆꯦꯟ ꯃꯁꯜ ꯗꯤꯁ꯭ꯠꯔꯣꯐꯤ, ꯗꯤ.ꯑꯦꯝ.ꯗꯤ., ꯃꯁꯜ ꯁꯣꯟꯊꯕꯥ, ꯖꯦꯅꯦꯇꯤꯛ ꯂꯥꯌꯅꯥ, ꯅꯨꯄꯥꯃꯆꯥꯒꯤ ꯂꯥꯌꯅꯥ, ꯗꯤꯁ꯭ꯠꯔꯣꯐꯤꯟ, ꯑꯉꯥꯡꯁꯤꯡꯒꯤ ꯍꯀꯁꯦꯜ꯫

Frequently Asked Questions (FAQ)

DMDꯅꯥ ꯅꯥꯕꯥ ꯃꯤꯑꯣꯏ ꯑꯃꯒꯤ ꯄꯨꯟꯁꯤꯒꯤ ꯃꯇꯝ ꯑꯁꯤ ꯀꯌꯥꯅꯣ?

DMDꯅꯥ ꯅꯥꯕꯥ ꯃꯤꯑꯣꯏꯁꯤꯡꯅꯥ ꯑꯌꯥꯝꯕꯗꯤ ꯆꯍꯤ 25 ꯁꯨꯔꯀꯄꯗꯥ ꯀꯟꯗꯤꯁꯟ ꯑꯁꯤꯅꯥ ꯁꯤꯕꯥ ꯌꯥꯏ, ꯑꯗꯨꯕꯨ ꯁꯄꯣꯔꯇꯤꯚ ꯀꯦꯌꯔꯗꯥ ꯑꯍꯣꯡꯕꯥ ꯂꯥꯀꯄꯅꯥ ꯃꯔꯝ ꯑꯣꯏꯗꯨꯅꯥ ꯍꯧꯖꯤꯛꯇꯤ ꯃꯤꯑꯣꯏ ꯀꯌꯥꯅꯥ ꯍꯦꯟꯅꯥ ꯍꯤꯡꯂꯤ꯫

⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

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ꯅꯍꯥꯛꯀꯤ ꯑꯉꯥꯡ ꯑꯗꯨꯒꯤ ꯃꯁꯂꯁꯤꯡ ꯑꯗꯨ ꯁꯣꯟꯊꯔꯀꯄꯥ ꯎꯕꯥ ꯐꯪꯕ꯭ꯔꯥ? ꯗꯨꯆꯦꯟ ꯃꯁꯜ ꯗꯤꯁ꯭ꯠꯔꯣꯐꯤ (DMD)ꯒꯤ ꯃꯔꯃꯗꯥ ꯈꯪꯖꯤꯅꯕꯤꯌꯨ

ꯅꯍꯥꯛꯀꯤ ꯑꯉꯥꯡ ꯑꯗꯨꯒꯤ ꯃꯁꯂꯁꯤꯡ ꯑꯗꯨ ꯁꯣꯟꯊꯔꯀꯄꯥ ꯎꯕꯥ ꯐꯪꯕ꯭ꯔꯥ? ꯗꯨꯆꯦꯟ ꯃꯁꯜ ꯗꯤꯁ꯭ꯠꯔꯣꯐꯤ (DMD)ꯒꯤ ꯃꯔꯃꯗꯥ ꯈꯪꯖꯤꯅꯕꯤꯌꯨ

ꯅꯍꯥꯛꯀꯤ ꯑꯉꯥꯡ ꯑꯗꯨꯅꯥ ꯂꯥꯟꯊꯦꯡꯅꯔꯤꯉꯩ ꯑꯃꯁꯨꯡ ꯁꯥꯟꯅꯔꯀꯄꯗꯒꯤ ꯈꯣꯡꯅꯥ ꯆꯠꯄꯥ ꯑꯃꯁꯨꯡ ꯊꯣꯡꯅꯥꯎ ꯍꯥꯡꯗꯣꯀꯄꯗꯥ ꯑꯋꯥꯕꯥ ꯍꯧꯔꯀꯄꯥ ꯍꯧꯔꯀꯄꯗꯨ ꯅꯍꯥꯛꯅꯥ ꯈꯪꯂꯃꯒꯅꯤ꯫ ꯅꯠꯔꯒꯥ ꯃꯈꯣꯌꯅꯥ ꯂꯦꯞꯄꯥ ꯂꯩꯇꯅꯥ ꯁꯣꯀꯄꯥ ꯑꯃꯁꯨꯡ ꯌꯥꯝꯅꯥ ꯋꯥꯅꯥ ꯊꯣꯀꯄꯥ ꯐꯥꯑꯣꯔꯤꯕꯔꯥ? ꯍꯥꯌꯔꯤꯕꯁꯤꯡ ꯑꯁꯤ ꯑꯩꯈꯣꯌꯅꯥ ꯌꯥꯝꯅꯥ ꯃꯤꯠꯌꯦꯡ ꯆꯪꯗꯕꯥ ꯑꯄꯤꯀꯄꯥ ꯋꯥꯐꯃꯁꯤꯡ ꯑꯣꯏꯅꯥ ꯎꯕꯥ ꯌꯥꯏ, ꯑꯗꯨꯕꯨ ꯃꯈꯣꯌ ꯑꯁꯤ ꯑꯔꯨꯕꯥ ꯐꯤꯚꯃꯁꯤꯡꯒꯤ ꯇꯣꯏꯅꯥ ꯊꯣꯀꯄꯥ ꯈꯨꯗꯃꯁꯤꯡ ꯑꯣꯏꯕꯥ ꯌꯥꯏ꯫ ꯉꯁꯤ ꯑꯩꯈꯣꯌꯅꯥ ꯋꯥꯔꯤ ꯁꯥꯅꯔꯤꯕꯥ ꯑꯁꯤ ꯇꯁꯦꯡꯅꯥ ꯃꯗꯨꯅꯤ, ꯃꯔꯨꯑꯣꯏꯅꯥ ꯅꯨꯄꯥꯃꯆꯥꯁꯤꯡꯗꯥ ꯃꯁꯂꯁꯤꯡ ꯇꯞꯅꯥ ꯇꯞꯅꯥ ꯁꯣꯀꯍꯜꯂꯤꯕꯥ ꯂꯥꯌꯅꯥ ꯑꯃꯅꯤ꯫

ꯗꯨꯆꯦꯟ ꯃꯁꯜ ꯗꯤꯁ꯭ꯠꯔꯣꯐꯤ (DMD) ꯍꯥꯌꯕꯁꯤ ꯀꯔꯤꯅꯣ?

ꯌꯥꯝꯅꯥ ꯂꯥꯏꯅꯥ ꯍꯥꯌꯔꯕꯗꯥ, ꯗꯨꯆꯦꯟ ꯃꯁꯜ ꯗꯤꯁ꯭ꯠꯔꯣꯐꯤ ꯅꯠꯠꯔꯒꯥ ꯊꯣꯏꯗꯣꯀꯄꯥ ꯃꯑꯣꯡꯗꯥ ꯗꯤ.ꯑꯦꯝ.ꯗꯤ . ꯃꯁꯤ ꯈ꯭ꯕꯥꯏꯗꯒꯤ ꯀꯃꯟ ꯑꯣꯏꯕꯥ ꯑꯃꯁꯨꯡ ꯁꯥꯊꯤꯕꯥ ꯃꯈꯂꯒꯤ ꯃꯁꯜ ꯗꯤꯁ꯭ꯠꯔꯣꯐꯤꯅꯤ .

ꯃꯁꯤꯒꯤ ꯃꯇꯥꯡꯗꯥ ꯑꯁꯤꯒꯨꯝꯅꯥ ꯈꯟꯊꯕꯤꯌꯨ: ꯑꯩꯈꯣꯌꯒꯤ ꯃꯁꯂꯁꯤꯡ ꯑꯁꯤ ꯏꯂꯥꯁ꯭ꯇꯤꯛ ꯔꯕ꯭ꯕꯔ ꯕꯦꯟꯗꯁꯤꯡꯒꯨꯝꯅꯥ ꯑꯣꯏ꯫ ꯂꯥꯌꯅꯥ ꯑꯁꯤꯗꯥ, ꯏꯂꯥꯁ꯭ꯇꯤꯛ ꯃꯁꯂꯁꯤꯡ ꯑꯗꯨꯒꯤ ꯃꯄꯥꯉ꯭ꯒꯜ ꯍꯟꯊꯔꯀꯏ ꯑꯃꯁꯨꯡ ꯃꯈꯣꯌꯅꯥ ꯃꯑꯣꯡ ꯆꯨꯝꯅꯥ ꯊꯕꯛ ꯇꯧꯕꯥ ꯉꯃꯗ꯭ꯔꯦ꯫ ꯃꯇꯃꯒꯤ ꯃꯇꯨꯡꯏꯟꯅꯥ, ꯀꯟꯗꯤꯁꯟ ꯑꯁꯤ ꯍꯦꯟꯅꯥ ꯐꯠꯆꯤꯜꯂꯛꯇꯕꯥ ꯅꯠꯇꯅꯥ ꯍꯦꯟꯅꯥ ꯐꯠꯆꯤꯜꯂꯀꯏ꯫

ꯗꯤ.ꯑꯦꯝ.ꯗꯤ.ꯅꯥ ꯑꯌꯥꯝꯕꯅꯥ ꯖꯦꯅꯦꯇꯤꯛ ꯑꯣꯏ, ꯍꯥꯌꯕꯗꯤ ꯃꯁꯤ ꯃꯤꯔꯣꯜ ꯑꯃꯗꯒꯤ ꯃꯤꯔꯣꯜ ꯑꯃꯗꯥ ꯌꯧꯍꯜꯂꯤ . ꯃꯔꯨꯑꯣꯏꯅꯥ ꯃꯁꯤ ꯑꯦꯛꯁ-ꯂꯤꯉ꯭ꯛ ꯇꯧꯔꯕꯥ ꯔꯤꯁꯦꯁꯤꯕ ꯇ꯭ꯔꯦꯠ ꯑꯃꯥ ꯑꯣꯏꯅꯥ ꯇ꯭ꯔꯥꯟꯁꯃꯤꯠ ꯇꯧꯏ . ꯃꯁꯤꯅꯥ ꯇꯥꯀꯄꯗꯤ ꯀꯔꯤꯒꯨꯝꯕꯥ ꯃꯃꯥ ꯑꯗꯨꯅꯥ ꯂꯥꯌꯅꯥ ꯑꯁꯤꯒꯤ ꯀꯦꯔꯤꯌꯔ ꯑꯣꯏꯔꯕꯗꯤ ꯃꯍꯥꯛꯀꯤ ꯑꯉꯥꯡ ꯑꯗꯨꯅꯥ ꯃꯍꯥꯛꯀꯤ ꯃꯐꯃꯗꯒꯤ ꯂꯧꯕꯥ ꯌꯥꯏ꯫ ꯑꯗꯨꯝ ꯑꯣꯏꯅꯃꯛ, ꯀꯦꯁ ꯈꯔꯗꯗꯤ, ꯆꯥꯎꯔꯥꯛꯅꯥ ꯀꯦꯁ 30%ꯗꯤ, ꯀꯟꯗꯤꯁꯟ ꯑꯁꯤ ꯑꯅꯧꯕꯥ ꯖꯦꯅꯦꯇꯤꯛ ꯃ꯭ꯌꯨꯇꯦꯁꯟ ꯑꯃꯅꯥ ꯃꯔꯝ ꯑꯣꯏꯗꯨꯅꯥ ꯊꯣꯀꯍꯅꯕꯥ ꯌꯥꯏ , ꯀꯔꯤꯒꯨꯝꯕꯥ ꯏꯃꯨꯡ ꯑꯗꯨꯒꯤ ꯀꯅꯥꯒꯨꯝꯕꯥ ꯑꯃꯠꯇꯅꯥ ꯃꯃꯥꯡꯗꯥ ꯂꯥꯌꯅꯥ ꯑꯁꯤ ꯂꯩꯔꯃꯗ꯭ꯔꯕꯁꯨ꯫ ꯃꯁꯤꯅꯥ ꯇꯥꯀꯄꯗꯤ ꯀꯔꯤꯒꯨꯝꯕꯥ ꯃꯇꯃꯗꯥ ꯃꯁꯤ ꯔꯦꯟꯗꯝ ꯑꯣꯏꯅꯥ ꯊꯣꯀꯄꯥ ꯌꯥꯏ꯫

DMD ꯀꯟꯗꯤꯁꯟ ꯑꯁꯤꯅꯥ ꯀꯅꯥꯅꯥ ꯈ꯭ꯕꯥꯏꯗꯒꯤ ꯍꯦꯟꯅꯥ ꯁꯣꯀꯍꯜꯂꯤꯕꯒꯦ?

ꯗꯨꯆꯦꯟ ꯃꯁꯜ ꯗꯤꯁ꯭ꯠꯔꯣꯐꯤꯅꯥ ꯃꯔꯨꯑꯣꯏꯅꯥ ꯅꯨꯄꯥꯃꯆꯥꯁꯤꯡꯗꯥ ꯁꯣꯀꯍꯜꯂꯤ . ꯑꯗꯨꯝ ꯑꯣꯏꯅꯃꯛ, ꯂꯥꯌꯅꯥ ꯑꯁꯤ ꯊꯣꯀꯍꯜꯂꯤꯕꯥ ꯖꯤꯅꯒꯤ ꯀꯦꯔꯤꯌꯔ ꯑꯣꯏꯔꯤꯕꯥ ꯅꯨꯄꯤꯃꯆꯥꯁꯤꯡꯗꯥ ꯀꯔꯤꯒꯨꯝꯕꯥ ꯃꯇꯃꯗꯥ ꯃꯌꯥꯏ ꯑꯣꯏꯕꯥ ꯂꯥꯏꯑꯣꯡ ꯎꯠꯄꯥ ꯌꯥꯏ꯫ ꯑꯗꯨꯝ ꯑꯣꯏꯅꯃꯛ ꯃꯁꯤ ꯌꯥꯝꯅꯥ ꯀꯃꯟ ꯑꯣꯏꯗꯦ꯫

ꯃꯁꯜ ꯁꯣꯟꯊꯕꯒꯤ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯑꯁꯤ ꯃꯍꯧꯁꯥꯅꯥ ꯆꯍꯤ 2 ꯑꯃꯁꯨꯡ 4ꯒꯤ ꯃꯔꯛꯇꯥ ꯍꯧꯏ, ꯑꯗꯨꯕꯨ ꯑꯉꯥꯡ ꯈꯔꯗꯤ ꯆꯥꯎꯔꯥꯛꯅꯥ ꯆꯍꯤ 6 ꯁꯨꯗ꯭ꯔꯤꯉꯩꯗꯥ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯑꯁꯤ ꯎꯠꯄꯥ ꯍꯧꯔꯀꯄꯥ ꯌꯥꯏ꯫ ꯃꯔꯝ ꯑꯗꯨꯅꯥ ꯀꯔꯤꯒꯨꯝꯕꯥ ꯅꯍꯥꯛꯅꯥ ꯆꯤꯡꯅꯕꯥ ꯂꯩꯔꯕꯗꯤ ꯃꯦꯗꯤꯀꯦꯂꯒꯤ ꯄꯥꯎꯇꯥꯛ ꯂꯧꯕꯅꯥ ꯈ꯭ꯕꯥꯏꯗꯒꯤ ꯐꯩ꯫

DMD ꯑꯁꯤ ꯀꯌꯥꯝ ꯀꯃꯟ ꯑꯣꯏꯕꯒꯦ?

ꯃꯁꯤ ꯌꯥꯝꯅꯥ ꯁꯥꯊꯤꯕꯥ ꯀꯟꯗꯤꯁꯟ ꯑꯃꯅꯤ ꯍꯥꯌꯔꯕꯁꯨ, ꯃꯁꯤ ꯀꯅꯥꯒꯨꯝꯕꯥ ꯑꯃꯅꯥ ꯈꯜꯂꯤꯕꯥ ꯑꯗꯨꯒꯨꯝꯅꯥ ꯌꯥꯝꯅꯥ ꯊꯨꯅꯥ ꯊꯣꯀꯄꯥ ꯅꯠꯇꯦ꯫ ꯁ꯭ꯇꯦꯇꯤꯁ꯭ꯇꯤꯀꯦꯂꯅꯥ ꯇꯥꯛꯂꯤ ꯃꯗꯨꯗꯤ ꯃꯥꯂꯦꯝ ꯁꯤꯅꯕꯥ ꯊꯨꯡꯅꯥ ꯅꯨꯄꯥ ꯑꯉꯥꯡ ꯳꯶꯰꯰ꯒꯤ ꯃꯅꯨꯡꯗꯥ ꯆꯥꯎꯔꯥꯛꯅꯥ ꯑꯃꯥ ꯗꯤ.ꯑꯦꯝ.ꯗꯤ. DMD ꯑꯁꯤ ꯌꯥꯝꯅꯥ ꯁꯥꯊꯤꯕꯥ, ꯏꯅꯍꯦꯔꯤꯇꯦꯗ ꯃꯥꯌꯣꯄꯦꯊꯤꯁꯤꯡ , ꯅꯠꯠꯔꯒꯥ ꯁ꯭ꯀꯦꯂꯦꯇꯜ ꯃꯁꯂꯁꯤꯡꯒꯤ ꯂꯥꯌꯅꯥꯁꯤꯡꯒꯤ ꯃꯅꯨꯡꯗꯥ ꯈ꯭ꯕꯥꯏꯗꯒꯤ ꯀꯃꯟ ꯑꯣꯏꯕꯥ ꯑꯃꯅꯤ꯫

DMD ꯑꯁꯤ ꯁꯤꯍꯅꯕꯥ ꯌꯥꯕꯥ ꯂꯥꯌꯅꯥ ꯑꯃꯅꯤ ꯍꯥꯌꯕꯁꯤꯅꯤ?

ꯍꯣꯌ, ꯅꯨꯡꯉꯥꯏꯇꯕꯥ ꯋꯥꯐꯝ ꯑꯃꯅꯥ, ꯗꯤ.ꯑꯦꯝ.ꯗꯤ .ꯑꯇꯣꯞꯄꯥ ꯂꯥꯌꯅꯥ ꯑꯃꯅꯤ꯫ ꯀꯟꯗꯤꯁꯟ ꯑꯁꯤꯅꯥ ꯅꯥꯕꯥ ꯃꯤꯑꯣꯏ ꯀꯌꯥꯗꯤ ꯂꯪꯁ ꯑꯃꯁꯨꯡ ꯍꯥꯔꯇꯇꯥ ꯂꯩꯕꯥ ꯀꯃꯞꯂꯤꯀꯦꯁꯅꯁꯤꯡꯅꯥ ꯁꯤꯍꯜꯂꯤ꯫ ꯑꯗꯨꯕꯨ ꯋꯥꯈꯜ ꯋꯥꯕꯥ ꯂꯩꯔꯣꯏꯗꯕꯅꯤ, ꯍꯧꯖꯤꯛ ꯂꯩꯔꯤꯕꯥ ꯂꯥꯌꯦꯡꯁꯤꯡ ꯑꯁꯤꯒꯥ ꯂꯣꯌꯅꯅꯥ ꯅꯍꯥꯛꯀꯤ ꯄꯨꯟꯁꯤ ꯁꯥꯡꯗꯣꯀꯄꯥ ꯑꯃꯁꯨꯡ ꯄꯨꯟꯁꯤꯒꯤ ꯈꯔꯥ ꯐꯕꯥ ꯃꯒꯨꯟ ꯑꯃꯥ ꯊꯝꯅꯕꯒꯤ ꯄꯥꯝꯕꯩꯁꯤꯡ ꯂꯩꯔꯤ꯫

DMDꯒꯤ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯑꯗꯨ ꯀꯔꯤꯅꯣ?

ꯑꯩꯈꯣꯌꯅꯥ ꯃꯃꯥꯡꯗꯥ ꯍꯥꯌꯈꯤꯕꯒꯨꯝꯅꯥ, DMDꯒꯤ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯑꯁꯤ ꯃꯍꯧꯁꯥꯅꯥ ꯆꯍꯤ 2 ꯑꯃꯁꯨꯡ 4ꯒꯤ ꯃꯔꯛꯇꯥ ꯍꯧꯏ, ꯑꯗꯨꯕꯨ ꯀꯔꯤꯒꯨꯝꯕꯥ ꯃꯇꯃꯗꯥ ꯃꯈꯣꯌ ꯑꯁꯤ ꯑꯉꯥꯡ ꯑꯣꯏꯔꯤꯉꯩꯗꯥ ꯍꯧꯔꯀꯄꯥ ꯌꯥꯏ, ꯅꯠꯠꯔꯒꯥ ꯑꯉꯥꯡ ꯑꯣꯏꯔꯤꯉꯩꯗꯥ ꯇꯨꯡꯗꯥ ꯐꯥꯎꯕꯥ ꯂꯥꯀꯄꯥ ꯌꯥꯏ꯫

DMDꯅꯥ ꯃꯇꯃꯒꯤ ꯃꯇꯨꯡꯏꯟꯅꯥ ꯃꯁꯜ ꯁꯣꯟꯊꯍꯅꯕꯅꯥ ꯃꯔꯝ ꯑꯣꯏꯗꯨꯅꯥ, ꯈ꯭ꯕꯥꯏꯗꯒꯤ ꯀꯃꯟ ꯑꯣꯏꯕꯥ ꯂꯥꯏꯑꯣꯡꯁꯤꯡꯗꯤ:

  • ꯃꯁꯜ ꯁꯣꯟꯊꯕꯥ ꯑꯃꯁꯨꯡ ꯃꯥꯡ-ꯇꯥꯛꯅꯤꯡꯉꯥꯏ ꯑꯣꯏꯕꯥ (muscle atrophy) ꯍꯥꯌꯕꯁꯤ ꯇꯞꯅꯥ ꯇꯞꯅꯥ ꯍꯦꯅꯒꯠꯂꯀꯄꯥ, ꯈꯣꯡ ꯑꯃꯁꯨꯡ ꯈꯣꯡꯗꯥ ꯍꯧꯔꯀꯄꯥ꯫ ꯀꯟꯗꯤꯁꯟ ꯑꯁꯤꯅꯥ ꯃꯈꯨꯠ, ꯈꯣꯡ ꯑꯃꯁꯨꯡ ꯍꯀꯆꯥꯡꯒꯤ ꯑꯇꯩ ꯁꯔꯨꯀꯁꯤꯡꯗꯥ ꯌꯥꯝꯅꯥ ꯅꯦꯝꯅꯥ ꯁꯣꯀꯍꯜꯂꯤ꯫
  • ꯀꯥꯜꯐ ꯃꯁꯜ ꯍꯥꯏꯄꯔꯠꯔꯣꯐꯤ (ꯃꯁꯤꯅꯥ ꯇꯥꯀꯄꯗꯤ ꯀꯥꯜꯐ ꯃꯁꯜ ꯑꯗꯨ ꯍꯦꯟꯅꯥ ꯆꯥꯎꯈꯠꯂꯀꯏ)꯫ ꯃꯁꯤ ꯃꯁꯜ ꯐꯤꯕꯔꯁꯤꯡ ꯑꯁꯤ ꯐꯦꯇꯤ ꯇꯤꯁꯨ ꯑꯃꯁꯨꯡ ꯀꯅꯦꯛꯇꯤꯚ ꯇꯤꯁꯨꯁꯤꯡꯅꯥ ꯃꯍꯨꯠ ꯁꯤꯜꯂꯀꯄꯥ ꯃꯇꯃꯗꯥ ꯊꯣꯀꯏ꯫
  • ꯊꯣꯉꯅꯥꯑꯣꯗꯥ ꯆꯠꯄꯗꯥ ꯑꯋꯥꯕꯥ꯫
  • ꯃꯇꯃꯒꯤ ꯃꯇꯨꯡꯏꯟꯅꯥ ꯈꯣꯡꯅꯥ ꯆꯠꯄꯗꯥ ꯑꯋꯥꯕꯥ꯫
  • ꯆꯥꯡ ꯅꯥꯏꯅꯥ ꯁꯣꯀꯄꯥ꯫
  • ꯋꯥꯗꯂꯤꯡ ꯒꯦꯠ ꯑꯃꯥ꯫
  • ꯈꯣꯡꯗꯥ ꯆꯠꯄꯥ꯫
  • ꯊꯨꯅꯥ ꯋꯥꯈꯜ ꯇꯥꯗꯕꯥ (fatigue)꯫

ꯈꯅꯕꯤꯌꯨ, ꯀꯔꯤꯒꯨꯝꯕꯥ ꯅꯍꯥꯛꯀꯤ ꯃꯆꯥꯅꯨꯄꯥ ꯑꯗꯨꯅꯥ ꯐ꯭ꯂꯣꯔꯗꯥ ꯁꯥꯟꯅꯕꯗꯒꯤ ꯊꯣꯔꯛꯇꯨꯅꯥ, ꯃꯍꯥꯛꯀꯤ ꯃꯈꯨꯠꯁꯤꯡ ꯑꯗꯨ ꯐ꯭ꯂꯣꯔꯗꯥ ꯆꯦꯠꯅꯥ ꯊꯃꯖꯤꯜꯂꯕꯗꯤ, ꯃꯗꯨꯒꯤ ꯃꯇꯨꯡꯗꯥ ꯃꯍꯥꯛꯀꯤ ꯃꯈꯨꯠ ꯑꯗꯨ ꯃꯍꯥꯛꯀꯤ ꯈꯨꯎꯗꯥ ꯊꯃꯖꯤꯜꯂꯕꯗꯤ, ꯑꯃꯁꯨꯡ ꯃꯍꯥꯛꯀꯤ ꯍꯀꯆꯥꯡ ꯑꯗꯨ ꯌꯥꯝꯅꯥ ꯋꯥꯅꯥ ꯇꯞꯅꯥ ꯇꯞꯅꯥ ꯊꯃꯖꯤꯜꯂꯕꯗꯤ, ꯃꯗꯨꯁꯨ ꯂꯥꯌꯅꯥ ꯑꯁꯤꯒꯤ ꯂꯥꯏꯑꯣꯡ ꯑꯃꯥ ꯑꯣꯏꯕꯥ ꯌꯥꯏ (ꯃꯁꯤꯕꯨ ꯒꯧꯔꯁꯀꯤ ꯂꯥꯏꯑꯣꯡꯁꯨ ꯀꯧꯏ)꯫

ꯃꯁꯤꯒꯤ ꯃꯊꯛꯇꯥ, DMDꯅꯥ ꯑꯇꯩ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯊꯣꯀꯍꯅꯕꯥ ꯌꯥꯏ:

  • ꯍꯥꯔꯠ ꯃꯁꯂꯒꯤ ꯂꯥꯌꯅꯥ (Cardiomyopathy)꯫
  • ꯁ꯭ꯕꯔ ꯍꯣꯅꯕꯥ ꯋꯥꯕꯥ ꯑꯃꯁꯨꯡ ꯁ꯭ꯕꯔ ꯍꯣꯅꯕꯥ ꯋꯥꯕꯥ꯫
  • ꯀꯣꯒꯅꯤꯇꯤꯚ ꯏꯝꯄꯥꯌꯔꯃꯦꯟꯇ ꯑꯃꯁꯨꯡ ꯂꯔꯅꯤꯡꯒꯤ ꯈꯦꯠꯅꯕꯥ ꯂꯩꯕꯥ꯫
  • ꯋꯥ ꯉꯥꯡꯕꯥ ꯑꯃꯁꯨꯡ ꯂꯣꯜ ꯁꯦꯃꯒꯠꯄꯗꯥ ꯊꯦꯡꯊꯕꯥ꯫
  • ꯗꯤꯚꯦꯂꯄꯃꯦꯟꯇꯗꯥ ꯊꯦꯡꯊꯕꯥ꯫
  • ꯁ꯭ꯀꯣꯂꯤꯑꯣꯁꯤꯁ (Scoliosis)꯫
  • ꯁꯣꯔꯠ ꯁ꯭ꯇꯦꯆꯔ꯫

DMD (ꯀꯦꯔꯤꯌꯔ) ꯊꯣꯀꯍꯜꯂꯤꯕꯥ ꯖꯤꯟ ꯑꯁꯤ ꯄꯨꯔꯤꯕꯥ ꯅꯨꯄꯤꯃꯆꯥꯁꯤꯡꯒꯤ ꯃꯅꯨꯡꯗꯥ 2.5% ꯑꯃꯁꯨꯡ 20%ꯒꯤ ꯃꯔꯛꯇꯥ ꯃꯌꯥꯏ ꯑꯣꯏꯕꯥ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯂꯥꯀꯄꯥ ꯌꯥꯏ, ꯑꯗꯨꯕꯨ ꯃꯍꯧꯁꯥꯅꯥ ꯃꯈꯣꯌ ꯑꯁꯤ ꯌꯥꯝꯅꯥ ꯁꯥꯊꯤꯕꯥ ꯑꯣꯏꯗꯦ꯫

ꯀꯔꯤꯒꯤꯗꯃꯛ ꯑꯁꯤꯒꯨꯝꯕꯥ ꯗꯤ.ꯑꯦꯝ.ꯗꯤ.

ꯗꯤ.ꯑꯦꯝ.ꯗꯤ.ꯒꯤ ꯃꯔꯨꯑꯣꯏꯕꯥ ꯃꯔꯃꯗꯤ ꯑꯩꯈꯣꯌꯒꯤ ꯃꯁꯂꯁꯤꯡꯕꯨ ꯍꯀꯆꯥꯡ ꯐꯅꯥ ꯊꯝꯅꯕꯒꯤꯗꯃꯛ ꯇꯉꯥꯏ ꯐꯗꯕꯥ ꯄ꯭ꯔꯣꯇꯤꯟ ꯑꯃꯥ ꯑꯣꯏꯔꯤꯕꯥ ꯗꯤꯁ꯭ꯠꯔꯣꯐꯤꯟ ꯄꯨꯊꯣꯀꯄꯒꯤ ꯀꯣꯗ ꯇꯧꯔꯤꯕꯥ ꯖꯤꯅꯗꯥ ꯃ꯭ꯌꯨꯇꯦꯁꯟ ꯇꯧꯕꯅꯤ꯫ ꯃꯁꯤꯒꯤ ꯄ꯭ꯔꯣꯇꯤꯟ ꯑꯁꯤ ꯗꯤꯁ꯭ꯠꯔꯣꯐꯤꯟ ꯑꯁꯤ ꯃꯁꯂꯁꯤꯡꯒꯤ ꯁ꯭ꯠꯔꯀꯆꯔꯦꯜ ꯌꯨꯅꯤꯠ ꯑꯃꯥ ꯑꯣꯏꯅꯥ ꯊꯕꯛ ꯇꯧꯕꯥ ꯗꯤꯁ꯭ꯠꯔꯣꯐꯤꯟ-ꯒ꯭ꯂꯥꯏꯀꯣꯞꯔꯣꯇꯤꯟ ꯀꯃꯞꯂꯦꯛꯁ (ꯗꯤ.ꯖꯤ.ꯁꯤ.) ꯒꯤꯗꯃꯛꯇꯥ ꯌꯥꯝꯅꯥ ꯃꯔꯨꯑꯣꯏ꯫

DMDꯗꯥ, ꯗꯤꯁ꯭ꯠꯔꯣꯐꯤꯟ ꯑꯃꯁꯨꯡ DGC ꯄ꯭ꯔꯣꯇꯤꯟ ꯑꯅꯤꯃꯛ ꯃꯥꯡꯈꯤ, ꯑꯃꯁꯨꯡ ꯑꯔꯣꯏꯕꯗꯥ ꯃꯁꯜ ꯁꯦꯜ ꯁꯤꯍꯅꯕꯥ (necrosis) ꯊꯣꯀꯍꯜꯂꯤ꯫DMDꯅꯥ ꯅꯥꯕꯥ ꯃꯤꯑꯣꯏ ꯑꯃꯗꯥ ꯍꯀꯁꯦꯜ ꯐꯕꯥ ꯃꯁꯂꯁꯤꯡꯒꯤꯗꯃꯛ ꯃꯊꯧ ꯇꯥꯕꯥ ꯗꯤꯁ꯭ꯠꯔꯣꯐꯤꯅꯒꯤ ꯆꯥꯡꯒꯤ 5%ꯗꯒꯤ ꯇꯥꯅꯥ ꯂꯩ꯫

DMDꯅꯥ ꯅꯥꯕꯥ ꯃꯤꯑꯣꯏꯁꯤꯡꯅꯥ ꯆꯍꯤ ꯌꯥꯃꯈꯠꯂꯀꯄꯒꯥ ꯂꯣꯌꯅꯅꯥ, ꯃꯈꯣꯌꯒꯤ ꯃꯁꯂꯁꯤꯡꯅꯥ ꯑꯁꯤꯕꯥ ꯁꯦꯂꯁꯤꯡ ꯑꯁꯤ ꯑꯅꯧꯕꯥ ꯁꯦꯂꯁꯤꯡꯅꯥ ꯃꯍꯨꯠ ꯁꯤꯅꯕꯥ ꯉꯃꯗꯦ꯫ ꯃꯗꯨꯒꯤ ꯃꯍꯨꯠꯇꯥ , ꯀꯅꯦꯛꯇꯤꯕ ꯇꯤꯁꯨ ꯑꯃꯁꯨꯡ ꯑꯦꯗꯤꯄꯣꯖ ꯇꯤꯁꯨꯅꯥ ꯃꯁꯜ ꯐꯤꯕꯔꯒꯤ ꯃꯍꯨꯠ ꯁꯤꯜꯂꯤ꯫

ꯑꯩꯈꯣꯌꯅꯥ ꯃꯃꯥꯡꯗꯥ ꯍꯥꯌꯈꯤꯕꯒꯨꯝꯅꯥ ꯗꯤ.ꯑꯦꯝ.ꯗꯤ.ꯅꯥ ꯑꯦꯛꯁ-ꯂꯤꯉ꯭ꯛ ꯇꯧꯕꯥ ꯔꯤꯁꯦꯁꯤꯕ ꯀꯟꯗꯤꯁꯟ ꯑꯃꯅꯤ꯫ ꯑꯗꯨꯝ ꯑꯣꯏꯅꯃꯛ, ꯆꯥꯎꯔꯥꯛꯅꯥ ꯀꯦꯁ 30%ꯗꯥ, ꯃꯁꯤ ꯔꯦꯟꯗꯝ ꯑꯣꯏꯅꯥ, ꯏꯃꯨꯡꯒꯤ ꯍꯤꯁ꯭ꯇꯔꯤ ꯑꯃꯠꯇꯥ ꯌꯥꯎꯗꯅꯥ ꯊꯣꯀꯄꯥ ꯌꯥꯏ꯫

"ꯑꯦꯛꯁ-ꯂꯤꯉ꯭ꯛ" ꯍꯥꯌꯕꯁꯤꯅꯥ ꯗꯤ.ꯑꯦꯝ.ꯗꯤ.ꯒꯤ ꯗꯥꯌꯠꯕ ꯂꯧꯔꯤꯕꯥ ꯖꯤꯟ ꯑꯁꯤ ꯑꯦꯛꯁ ꯀ꯭ꯔꯣꯃꯣꯖꯣꯃꯗꯥ ꯂꯩ ꯍꯥꯌꯕꯅꯤ꯫ ꯑꯗꯣꯝꯅꯥ ꯈꯉꯕꯤꯔꯤꯕꯥ ꯑꯗꯨꯅꯤ ꯅꯨꯄꯥꯁꯤꯡꯗꯥ X ꯀ꯭ꯔꯣꯃꯣꯖꯣꯝ ꯑꯃꯥ ꯑꯃꯁꯨꯡ Y ꯀ꯭ꯔꯣꯃꯣꯖꯣꯝ ꯑꯃꯥ ꯂꯩ, ꯑꯃꯁꯨꯡ ꯅꯨꯄꯤꯁꯤꯡꯗꯥ X ꯀ꯭ꯔꯣꯃꯣꯖꯣꯝ ꯑꯅꯤ ꯂꯩ꯫

"ꯔꯤꯁꯦꯁꯤꯚ" ꯍꯥꯌꯕꯁꯤꯅꯥ ꯃꯤꯑꯣꯏ ꯑꯃꯅꯥ ꯂꯥꯌꯅꯥ ꯑꯁꯤ ꯊꯣꯀꯍꯜꯂꯤꯕꯥ ꯖꯤꯅꯒꯤ ꯀꯣꯄꯤ ꯑꯅꯤ ꯂꯩꯔꯕꯈꯛꯇꯗꯥ ꯂꯥꯌꯅꯥ ꯑꯁꯤ ꯂꯥꯛꯀꯅꯤ ꯍꯥꯌꯕꯅꯤ꯫ ꯑꯗꯨꯕꯨ ꯅꯨꯄꯥꯁꯤꯡꯗꯥ X ꯀ꯭ꯔꯣꯃꯣꯖꯣꯝ ꯑꯃꯥ ꯂꯩ꯫ ꯑꯗꯨꯅꯥ ꯀꯔꯤꯒꯨꯝꯕꯥ DMD ꯊꯣꯀꯍꯜꯂꯤꯕꯥ ꯖꯤꯟ ꯃ꯭ꯌꯨꯇꯦꯁꯟ ꯑꯗꯨ X ꯀ꯭ꯔꯣꯃꯣꯖꯣꯝ ꯑꯗꯨꯗꯥ ꯂꯩꯔꯕꯗꯤ ꯃꯈꯣꯌꯅꯥ DMD ꯐꯪꯒꯅꯤ꯫ ꯅꯨꯄꯤꯃꯆꯥ ꯑꯃꯅꯥ DMD ꯂꯧꯅꯕꯒꯤꯗꯃꯛ, ꯃꯍꯥꯛꯀꯤ X ꯀ꯭ꯔꯣꯃꯣꯖꯣꯝ ꯑꯅꯤꯃꯛꯇꯥ ꯖꯤꯟ ꯃ꯭ꯌꯨꯇꯦꯁꯟ ꯑꯁꯤ ꯂꯩꯒꯗꯕꯅꯤ꯫ ꯃꯗꯨ ꯌꯥꯝꯅꯥ ꯊꯦꯡꯅꯩ꯫ ꯑꯗꯨꯕꯨ ꯀꯔꯤꯒꯨꯝꯕꯥ ꯃꯍꯥꯛꯀꯤ ꯃ꯭ꯌꯨꯇꯦꯁꯟ ꯑꯗꯨ ꯑꯦꯛꯁ ꯀ꯭ꯔꯣꯃꯣꯖꯣꯝ ꯑꯃꯈꯛꯇꯗꯥ ꯂꯩꯔꯕꯗꯤ ꯃꯍꯥꯛ ꯂꯥꯌꯅꯥ ꯑꯁꯤꯒꯤ ꯀꯦꯔꯤꯌꯔ ꯑꯃꯥ ꯑꯣꯏꯒꯅꯤ꯫

DMD ꯑꯁꯤ ꯀꯔꯝꯅꯥ ꯈꯪꯗꯣꯀꯄꯒꯦ?

ꯀꯔꯤꯒꯨꯝꯕꯥ ꯅꯍꯥꯛꯀꯤ ꯑꯉꯥꯡ ꯑꯗꯨꯅꯥ DMDꯒꯤ ꯈꯨꯗꯃꯁꯤꯡ ꯎꯕꯥ ꯐꯪꯂꯕꯗꯤ, ꯗꯣꯛꯇꯔ ꯑꯗꯨꯅꯥ ꯑꯍꯥꯅꯕꯗꯥ ꯐꯤꯖꯤꯀꯦꯜ ꯑꯦꯀꯖꯥꯃꯤꯅꯦꯁꯟ , ꯅ꯭ꯌꯨꯔꯣꯂꯣꯖꯤꯀꯦꯜ ꯑꯦꯀꯖꯥꯃꯤꯅꯦꯁꯟ ꯑꯃꯁꯨꯡ ꯃꯁꯜ ꯑꯦꯀꯖꯥꯃꯤꯅꯦꯁꯟ ꯑꯃꯥ ꯄꯥꯡꯊꯣꯛꯀꯅꯤ꯫ ꯃꯈꯣꯌꯅꯥ ꯅꯍꯥꯛꯀꯤ ꯑꯉꯥꯡ ꯑꯗꯨꯒꯤ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯑꯃꯁꯨꯡ ꯃꯦꯗꯤꯀꯦꯜ ꯍꯤꯁ꯭ꯇꯔꯤꯒꯤ ꯃꯇꯥꯡꯗꯁꯨ ꯍꯪꯒꯅꯤ꯫

ꯀꯔꯤꯒꯨꯝꯕꯥ ꯗꯣꯛꯇꯔ ꯑꯗꯨꯅꯥ ꯑꯉꯥꯡ ꯑꯗꯨꯗꯥ DMD ꯂꯩꯔꯦ ꯍꯥꯌꯅꯥ ꯆꯤꯡꯅꯔꯕꯗꯤ ꯃꯈꯥꯗꯥ ꯄꯤꯔꯤꯕꯥ ꯇꯦꯁ꯭ꯇꯁꯤꯡ ꯑꯁꯤ ꯄꯥꯡꯊꯣꯀꯄꯥ ꯌꯥꯏ:

  • ꯀ꯭ꯔꯤꯌꯦꯇꯤꯟ ꯀꯤꯅꯥꯁ (CK) ꯕ꯭ꯂꯗ ꯇꯦꯁ꯭ꯠ (CK) ꯕ꯭ꯂꯗ ꯇꯦꯁ꯭ꯠ: ꯃꯁꯂꯁꯤꯡ ꯁꯣꯀꯍꯜꯂꯕꯥ ꯃꯇꯃꯗꯥ ꯀ꯭ꯔꯤꯌꯦꯇꯤꯟ ꯀꯤꯅꯥꯁ ꯀꯧꯕꯥ ꯑꯦꯅꯖꯥꯏꯝ ꯑꯃꯥ ꯏꯗꯥ ꯁꯦꯃꯒꯠꯂꯀꯏ꯫ ꯃꯔꯝ ꯑꯗꯨꯅꯥ, ꯀꯔꯤꯒꯨꯝꯕꯥ ꯁꯤ.ꯀꯦ.ꯒꯤ ꯊꯥꯛ ꯑꯁꯤ ꯋꯥꯡꯈꯠꯂꯕꯗꯤ, ꯃꯁꯤ ꯗꯤ.ꯑꯦꯝ.ꯗꯤ.ꯒꯤ ꯈꯨꯗꯝ ꯑꯃꯥ ꯑꯣꯏꯕꯥ ꯌꯥꯏ꯫ ꯃꯁꯤꯒꯤ ꯊꯥꯛ ꯑꯁꯤ ꯃꯍꯧꯁꯥꯅꯥ ꯆꯍꯤ 2ꯒꯤ ꯃꯅꯨꯡꯗꯥ ꯈ꯭ꯕꯥꯏꯗꯒꯤ ꯋꯥꯡꯕꯥ ꯑꯣꯏ, ꯑꯃꯁꯨꯡ ꯅꯣꯔꯃꯦꯂꯗꯒꯤ ꯁꯔꯨꯛ 10-20 ꯍꯦꯟꯅꯥ ꯋꯥꯡꯕꯥ ꯌꯥꯏ꯫
  • ꯖꯦꯅꯦꯇꯤꯛ ꯕ꯭ꯂꯗ ꯇꯦꯁ꯭ꯠ: ꯗꯤꯁ꯭ꯠꯔꯣꯐꯤꯟ ꯖꯤꯟ ꯑꯗꯨ ꯃꯄꯨꯡꯐꯥꯅꯥ ꯅꯠꯠꯔꯒꯥ ꯁꯔꯨꯛ ꯈꯔꯗꯤ ꯃꯥꯡꯈꯤꯕꯥ ꯎꯠꯄꯥ ꯖꯦꯅꯦꯇꯤꯛ ꯇꯦꯁ꯭ꯠ ꯑꯃꯅꯥ ꯗꯤ.ꯑꯦꯝ.ꯗꯤ.
  • ꯃꯁꯜ ꯕꯥꯏꯑꯣꯞꯁꯤ (muscle biopsy) : ꯗꯣꯛꯇꯔꯅꯥ ꯅꯍꯥꯛꯀꯤ ꯑꯉꯥꯡ ꯑꯗꯨꯒꯤ ꯃꯄꯥꯟꯊꯪꯕꯥ ꯁꯔꯨꯛ ꯅꯠꯠꯔꯒꯥ ꯈꯣꯡꯄꯥꯛ ꯑꯗꯨꯗꯒꯤ ꯃꯁꯂꯒꯤ ꯑꯄꯤꯀꯄꯥ ꯁꯦꯝꯄꯜ ꯑꯃꯥ ꯂꯧꯕꯥ ꯌꯥꯏ꯫ ꯁ꯭ꯄꯦꯁꯤꯑꯦꯂꯤꯁ꯭ꯠ ꯑꯃꯅꯥ ꯁꯦꯝꯄꯜ ꯑꯗꯨ ꯃꯥꯏꯛꯔꯣꯁ꯭ꯀꯣꯄꯀꯤ ꯃꯈꯥꯗꯥ ꯌꯦꯡꯗꯨꯅꯥ ꯗꯤ.ꯑꯦꯝ.ꯗꯤ.ꯒꯤ ꯈꯨꯗꯝ ꯑꯃꯠꯇꯥ ꯂꯩꯕ꯭ꯔꯥ ꯍꯥꯌꯕꯗꯨ ꯌꯦꯡꯒꯅꯤ꯫
  • ꯏꯂꯦꯛꯠꯔꯣꯀꯥꯔꯗꯤꯑꯣꯒ꯭ꯔꯥꯐ (EKG): DMDꯅꯥ ꯑꯌꯥꯝꯕꯥ ꯃꯇꯃꯗꯥ ꯍꯥꯔꯇꯇꯥ ꯁꯣꯀꯍꯅꯕꯅꯥ ꯃꯔꯝ ꯑꯣꯏꯗꯨꯅꯥ, ꯗꯣꯛꯇꯔꯅꯥ DMDꯒꯤ ꯑꯀꯛꯅꯕꯥ ꯂꯥꯏꯑꯣꯡ ꯑꯃꯠꯇꯥ ꯂꯩꯕ꯭ꯔꯥ ꯍꯥꯌꯕꯗꯨ ꯌꯦꯡꯁꯤꯟꯅꯕꯥ ꯑꯃꯁꯨꯡ ꯍꯥꯔꯇꯀꯤ ꯍꯀꯁꯦꯜ ꯑꯗꯨ ꯌꯦꯡꯁꯤꯟꯅꯕꯥ EKG ꯑꯃꯥ ꯄꯥꯡꯊꯣꯛꯀꯅꯤ꯫

ꯃꯁꯤꯒꯤ ꯂꯥꯏꯌꯦꯡꯁꯤꯡ ꯑꯁꯤ ꯀꯔꯤꯅꯣ?

ꯅꯨꯡꯉꯥꯏꯇꯕꯥ ꯋꯥꯐꯝ ꯑꯃꯅꯥ ꯍꯧꯖꯤꯛꯀꯤ ꯑꯣꯏꯅꯥ ꯗꯤ.ꯑꯦꯝ.ꯗꯤ . ꯃꯔꯝ ꯑꯗꯨꯅꯥ ꯂꯥꯏꯌꯦꯡꯕꯒꯤ ꯃꯔꯨꯑꯣꯏꯕꯥ ꯄꯥꯟꯗꯃꯗꯤ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯀꯟꯠꯔꯣꯜ ꯇꯧꯕꯥ ꯑꯃꯁꯨꯡ ꯑꯉꯥꯡ ꯑꯗꯨꯒꯤ ꯄꯨꯟꯁꯤꯒꯤ ꯃꯒꯨꯟ ꯑꯗꯨ ꯌꯥꯔꯤꯕꯃꯈꯩ ꯈ꯭ꯕꯥꯏꯗꯒꯤ ꯐꯕꯥ ꯃꯑꯣꯡꯗꯥ ꯊꯝꯕꯅꯤ꯫

ꯃꯈꯥꯗꯥ ꯄꯤꯔꯤꯕꯥ ꯑꯁꯤ ꯗꯤ.ꯑꯦꯝ.ꯗꯤ.ꯒꯤ ꯁꯄꯣꯔꯇꯤꯕ ꯇ꯭ꯔꯤꯠꯃꯦꯟꯇꯁꯤꯡꯅꯤ:

  • ꯀꯣꯔꯇꯤꯀꯣꯁ꯭ꯇꯦꯔꯣꯏꯗꯁꯤꯡ: ꯄ꯭ꯔꯦꯗꯅꯤꯁꯣꯂꯣꯟ ꯑꯃꯁꯨꯡ ꯗꯦꯐ꯭ꯂꯥꯖꯥꯀꯣꯔꯇꯒꯨꯝꯕꯥ ꯁ꯭ꯇꯦꯔꯣꯏꯗ ꯍꯤꯗꯥꯀꯁꯤꯡꯅꯥ ꯃꯁꯜ ꯁꯣꯟꯊꯍꯅꯕꯗꯥ ꯃꯇꯦꯡ ꯄꯥꯡꯏ, ꯂꯪꯁꯀꯤ ꯐꯉ꯭ꯀꯁꯟ ꯐꯒꯠꯍꯅꯕꯗꯥ ꯃꯇꯦꯡ ꯄꯥꯡꯏ, ꯁ꯭ꯀꯣꯂꯤꯑꯣꯁꯤꯁ ꯇꯞꯅꯥ ꯇꯞꯅꯥ ꯁꯣꯀꯍꯜꯂꯤ, ꯍꯥꯔꯇꯀꯤ ꯃꯁꯜ ꯁꯣꯟꯊꯕꯒꯤ ꯆꯥꯡ ꯍꯟꯊꯍꯜꯂꯤ (ꯀꯥꯔꯗꯤꯑꯣꯃꯥꯌꯣꯄꯦꯊꯤ) ꯑꯃꯁꯨꯡ ꯄꯨꯟꯁꯤ ꯁꯥꯡꯗꯣꯀꯍꯜꯂꯤ꯫
  • ꯀꯥꯔꯗꯤꯑꯣꯃꯥꯌꯣꯄꯦꯊꯤꯒꯤ ꯍꯤꯗꯥꯀꯁꯤꯡ: ꯑꯦꯁꯤꯏ ꯏꯅꯍꯤꯕꯤꯇꯔꯁꯤꯡ ꯑꯃꯁꯨꯡ/ꯅꯠꯠꯔꯒꯥ ꯕꯦꯇꯥ-ꯕ꯭ꯂꯣꯀꯔꯁꯤꯡꯒꯨꯝꯕꯥ ꯍꯤꯗꯥꯀꯁꯤꯡ ꯉꯟꯅꯥ ꯍꯧꯗꯣꯀꯄꯅꯥ ꯍꯥꯔꯠ ꯃꯁꯜ ꯁꯣꯟꯊꯕꯥ ꯀꯟꯠꯔꯣꯜ ꯇꯧꯕꯥ ꯉꯝꯃꯤ ꯑꯃꯁꯨꯡ ꯍꯥꯔꯠ ꯑꯦꯇꯦꯀꯁꯤꯡ ꯊꯤꯡꯕꯥ ꯉꯝꯃꯤ꯫
  • ꯐꯤꯖꯤꯀꯦꯜ ꯊꯦꯔꯥꯄꯤ: ꯐꯤꯖꯤꯀꯦꯜ ꯊꯦꯔꯥꯄꯤꯒꯤ ꯃꯔꯨꯑꯣꯏꯕꯥ ꯄꯥꯟꯗꯃꯗꯤ ꯃꯁꯂꯁꯤꯡ, ꯇꯦꯟꯗꯣꯅꯁꯤꯡ ꯑꯃꯁꯨꯡ ꯈꯣꯡꯗꯥ ꯃꯇꯝ ꯆꯨꯞꯄꯒꯤ ꯑꯣꯏꯅꯥ ꯇꯞꯅꯥ ꯇꯞꯅꯥ ꯁꯣꯀꯄꯥ ꯀꯟꯠꯔꯦꯀꯆꯔꯁꯤꯡ ꯊꯤꯡꯕꯅꯤ꯫ ꯃꯁꯤꯗꯥ ꯃꯍꯧꯁꯥꯅꯥ ꯑꯀꯛꯅꯕꯥ ꯁ꯭ꯠꯔꯦꯆꯤꯡ ꯑꯦꯛꯁꯔꯁꯥꯏꯖꯁꯤꯡ ꯌꯥꯎꯏ꯫
  • ꯁ꯭ꯄꯥꯏꯅꯦꯜ ꯁ꯭ꯇꯦꯅꯣꯁꯤꯁ ꯑꯃꯁꯨꯡ ꯃꯁꯜ ꯁꯣꯟꯊꯕꯒꯤ ꯁꯔꯖꯔꯤ: ꯁꯥꯊꯤꯕꯥ ꯀꯦꯁꯁꯤꯡꯗꯥ, ꯃꯁꯜ ꯁꯣꯟꯊꯕꯥ ꯊꯤꯡꯅꯕꯥ ꯁꯔꯖꯔꯤ ꯇꯧꯕꯥ ꯃꯊꯧ ꯇꯥꯕꯥ ꯌꯥꯏ꯫ ꯁ꯭ꯄꯥꯏꯅꯦꯜ ꯁ꯭ꯇꯦꯅꯣꯁꯤꯁ ꯀꯣꯀꯍꯟꯅꯕꯥ ꯁꯔꯖꯔꯤꯅꯥ ꯂꯪꯁꯀꯤ ꯐꯉ꯭ꯀꯁꯟ ꯑꯃꯁꯨꯡ ꯁ꯭ꯕꯔ ꯍꯣꯅꯕꯥ ꯐꯒꯠꯍꯅꯕꯥ ꯉꯝꯃꯤ꯫
  • ꯑꯦꯛꯁꯔꯁꯥꯏꯖ: ꯅꯍꯥꯛꯀꯤ ꯑꯉꯥꯡꯒꯤ ꯗꯣꯛꯇꯔꯅꯥ ꯑꯌꯥꯝꯕꯥ ꯃꯇꯃꯗꯥ ꯃꯈꯥ ꯇꯥꯅꯥ ꯃꯁꯜ ꯁꯣꯟꯊꯕꯥ ꯊꯤꯡꯅꯕꯥ ꯇꯞꯅꯥ ꯇꯞꯅꯥ ꯑꯦꯛꯁꯔꯁꯥꯏꯖ ꯇꯧꯅꯕꯥ ꯄꯥꯎꯇꯥꯛ ꯄꯤꯒꯅꯤ꯫ ꯃꯁꯤ ꯃꯍꯧꯁꯥꯅꯥ ꯄꯨꯜ ꯑꯦꯛꯁꯔꯁꯥꯏꯖ ꯑꯃꯁꯨꯡ ꯔꯤꯛꯔꯤꯌꯦꯁꯅꯦꯜ ꯑꯦꯛꯇꯤꯚꯤꯇꯤꯁꯤꯡꯒꯥ ꯂꯣꯌꯅꯅꯥ ꯄꯥꯡꯊꯣꯀꯏ꯫

ꯑꯇꯣꯞꯄꯥ ꯁꯄꯣꯔꯇꯤꯕ ꯇ꯭ꯔꯤꯠꯃꯦꯟꯇꯁꯤꯡꯒꯤ ꯃꯅꯨꯡꯗꯥ ꯃꯈꯥꯗꯥ ꯄꯤꯔꯤꯕꯁꯤꯡ ꯑꯁꯤ ꯌꯥꯑꯣꯔꯤ:

  • ꯃꯣꯕꯤꯂꯤꯇꯤ ꯑꯦꯗꯁꯤꯡ: ꯕ꯭ꯔꯦꯁ, ꯀꯦꯟ, ꯑꯃꯁꯨꯡ ꯍꯨꯏꯂꯆꯦꯌꯥꯔ꯫
  • ꯔꯦꯁ꯭ꯄꯤꯔꯦꯇꯔꯤ ꯄ꯭ꯔꯣꯕ꯭ꯂꯦꯃꯁꯤꯡꯒꯤꯗꯃꯛ ꯇ꯭ꯔꯦꯀꯤꯑꯣꯁ꯭ꯇꯣꯃꯤ ꯑꯃꯁꯨꯡ ꯑꯦꯁꯤꯁ꯭ꯇꯦꯟꯇ ꯚꯦꯟꯇꯤꯂꯦꯁꯟ꯫

ꯍꯧꯈꯤꯕꯥ ꯆꯍꯤ ꯇꯔꯥꯒꯤ ꯈꯨꯖꯤꯡ ꯈꯔꯁꯤꯗꯥ, ꯁꯄꯣꯔꯇꯤꯚ ꯀꯦꯌꯔ ꯁꯔꯚꯤꯁꯁꯤꯡꯗꯥ ꯑꯍꯣꯡꯕꯥ ꯂꯥꯀꯄꯒꯥ ꯂꯣꯌꯅꯅꯥ DMDꯅꯥ ꯅꯥꯕꯥ ꯃꯤꯑꯣꯏꯁꯤꯡꯒꯤ ꯄꯨꯟꯁꯤ ꯃꯍꯤꯡ ꯑꯁꯤ ꯌꯥꯝꯅꯥ ꯍꯦꯅꯒꯠꯂꯛꯂꯤ꯫

ꯍꯧꯖꯤꯛ ꯑꯅꯧꯕꯥ ꯗ꯭ꯔꯒ ꯀꯌꯥ ꯑꯃꯥ ꯀ꯭ꯂꯤꯅꯤꯀꯦꯜ ꯇꯦꯁ꯭ꯇꯤꯡ ꯇꯧꯔꯤ ꯃꯗꯨꯅꯥ ꯗꯤ.ꯑꯦꯝ.ꯗꯤ. "ꯑꯦꯛꯁꯣꯟ ꯁ꯭ꯀꯤꯄꯤꯡ" (ꯗꯤꯁ꯭ꯠꯔꯣꯐꯤꯟ ꯖꯤꯅꯒꯤ ꯃꯥꯡꯈꯤꯕꯥ ꯅꯠꯠꯔꯒꯥ ꯃ꯭ꯌꯨꯇꯦꯁꯟ ꯇꯧꯔꯕꯥ ꯁꯔꯨꯛ ꯑꯃꯥ "ꯁ꯭ꯞꯂꯥꯏꯁ" ꯇꯧꯕꯥ ꯃꯦꯊꯗ ꯑꯃꯥ)ꯒꯨꯝꯕꯥ ꯑꯅꯧꯕꯥ ꯂꯥꯌꯦꯡ ꯀꯌꯥ ꯑꯃꯥ ꯍꯟꯗꯛꯇꯥ ꯑꯦꯐ.ꯗꯤ.ꯑꯦ.(ꯐꯨꯗ ꯑꯃꯁꯨꯡ ꯗ꯭ꯔꯒ ꯑꯦꯗꯃꯤꯅꯤꯁ꯭ꯠꯔꯦꯁꯟ)ꯅꯥ ꯑꯌꯥꯕꯥ ꯄꯤꯈ꯭ꯔꯦ꯫ ꯑꯗꯨꯝ ꯑꯣꯏꯅꯃꯛ, ꯂꯥꯏꯌꯦꯡꯁꯤꯡ ꯑꯁꯤ ꯌꯥꯝꯅꯥ ꯑꯀꯛꯅꯕꯥ ꯖꯦꯅꯦꯇꯤꯛ ꯃ꯭ꯌꯨꯇꯦꯁꯟ ꯂꯩꯕꯥ ꯃꯤꯑꯣꯏ ꯈꯔꯈꯛꯇꯗꯥ ꯁꯤꯖꯤꯟꯅꯕꯥ ꯌꯥꯏ꯫ ꯂꯥꯌꯦꯡꯁꯤꯡ ꯑꯁꯤꯅꯥ ꯃꯁꯂꯁꯤꯡꯗꯥ ꯗꯤꯁ꯭ꯠꯔꯣꯐꯤꯟ ꯄ꯭ꯔꯣꯇꯤꯅꯒꯤ ꯆꯥꯡ ꯍꯦꯅꯒꯠꯂꯕꯁꯨ, ꯃꯈꯣꯌꯅꯥ ꯍꯧꯖꯤꯛ ꯐꯥꯑꯣꯕꯥ ꯄꯥꯉ꯭ꯒꯜ ꯑꯃꯁꯨꯡ ꯍꯀꯆꯥꯡꯒꯤ ꯊꯕꯛ ꯊꯧꯔꯃꯗꯥ ꯃꯁꯛ ꯊꯣꯀꯄꯥ ꯑꯍꯣꯡꯕꯥ ꯄꯨꯔꯀꯄꯥ ꯉꯃꯗ꯭ꯔꯤ꯫

ꯃꯁꯤꯒꯤ ꯗꯤ.ꯑꯦꯝ.ꯗꯤ.ꯒꯤ ꯀꯟꯗꯤꯁꯟ ꯑꯁꯤ ꯊꯤꯡꯕꯥ ꯉꯃꯒꯗ꯭ꯔꯥ?

DMD ꯑꯁꯤ ꯍꯦꯔꯤꯇꯦꯖ ꯀꯟꯗꯤꯁꯟ ꯑꯃꯅꯤ ꯃꯔꯝ ꯑꯗꯨꯅꯥ ꯃꯁꯤ ꯊꯤꯡꯅꯕꯥ ꯅꯍꯥꯛꯅꯥ ꯇꯧꯕꯥ ꯌꯥꯕꯥ ꯀꯔꯤꯁꯨ ꯂꯩꯇꯦ . ꯀꯦꯁꯁꯤꯡꯒꯤ ꯆꯥꯎꯔꯥꯛꯅꯥ ꯁꯔꯨꯛ ꯑꯍꯨꯝ ꯊꯣꯀꯄꯒꯤ ꯑꯃꯗꯤ ꯔꯦꯟꯗꯝ ꯑꯣꯏꯅꯥ ꯊꯣꯀꯏ, ꯏꯃꯨꯡꯒꯤ ꯍꯤꯁ꯭ꯇꯔꯤ ꯑꯃꯠꯇꯥ ꯂꯩꯇꯦ꯫

ꯀꯔꯤꯒꯨꯝꯕꯥ ꯅꯍꯥꯛꯅꯥ ꯑꯉꯥꯡ ꯑꯃꯥ ꯄꯣꯛꯅꯕꯥ ꯍꯣꯠꯅꯗ꯭ꯔꯤꯉꯩꯗꯥ ꯅꯍꯥꯛꯀꯤ ꯑꯉꯥꯡꯁꯤꯡꯗꯥ DMD ꯅꯠꯠꯔꯒꯥ ꯑꯇꯩ ꯖꯦꯅꯦꯇꯤꯛ ꯀꯟꯗꯤꯁꯅꯁꯤꯡ ꯄꯤꯕꯒꯤ ꯔꯤꯁ꯭ꯛ ꯂꯩꯔꯕꯗꯤ, ꯖꯦꯅꯦꯇꯤꯛ ꯀꯥꯎꯟꯁꯦꯂꯤꯡꯒꯤ ꯃꯇꯥꯡꯗꯥ ꯈꯟꯅꯕꯤꯌꯨ꯫ꯃꯁꯤꯒꯤ ꯃꯇꯥꯡꯗꯥ ꯅꯍꯥꯛꯀꯤ ꯗꯣꯛꯇꯔꯒꯥ ꯇꯥꯟꯅꯧ꯫ ꯀꯦꯁ ꯈꯔꯗꯗꯤ, ꯃꯤꯔꯣꯜꯂꯤꯉꯩ ꯃꯇꯃꯗꯥ ꯇꯣꯏꯅꯥ ꯄ꯭ꯔꯤꯅꯦꯇꯦꯜ ꯇꯦꯁ꯭ꯠ ꯇꯧꯕꯅꯥ ꯗꯤ.ꯑꯦꯝ.ꯗꯤ.

ꯇꯨꯡꯗꯥ ꯀꯔꯤ ꯃꯈꯂꯒꯤ ꯐꯤꯚꯝ ꯂꯥꯛꯀꯅꯤ ꯍꯥꯌꯅꯥ ꯊꯥꯖꯕꯥ ꯌꯥꯕꯒꯦ (ꯄ꯭ꯔꯣꯒ꯭ꯅꯣꯁꯤꯁ)?

ꯗꯤ.ꯑꯦꯝ.ꯗꯤ.ꯅꯥ ꯅꯥꯕꯥ ꯃꯤꯑꯣꯏꯁꯤꯡꯗꯥ ꯑꯌꯥꯝꯕꯅꯥ ꯄ꯭ꯔꯣꯒ꯭ꯔꯦꯁꯤꯚ ꯄ꯭ꯔꯣꯒ꯭ꯅꯣꯁꯤꯁ ꯑꯁꯤ ꯌꯥꯝꯅꯥ ꯐꯠꯇꯦ . ꯃꯁꯤꯅꯥ ꯄ꯭ꯔꯣꯒ꯭ꯔꯦꯁꯤꯚ ꯗꯤꯁꯑꯦꯕꯤꯂꯤꯇꯤ ꯊꯣꯀꯍꯜꯂꯤ, ꯑꯃꯁꯨꯡ DMDꯅꯥ ꯅꯥꯕꯥ ꯑꯉꯥꯡ ꯀꯌꯥꯗꯤ ꯆꯍꯤ 12 ꯁꯨꯔꯀꯄꯗꯥ ꯍꯨꯏꯂꯆꯦꯌꯥꯔꯗꯥ ꯆꯠꯂꯤ, DMDꯅꯥ ꯉꯟꯅꯥ ꯁꯤꯍꯅꯕꯁꯨ ꯌꯥꯏ꯫

DMDꯅꯥ ꯅꯥꯕꯥ ꯃꯤꯑꯣꯏ ꯑꯃꯒꯤ ꯄꯨꯟꯁꯤꯒꯤ ꯃꯇꯝ ꯑꯁꯤ ꯀꯌꯥꯅꯣ?

DMDꯅꯥ ꯅꯥꯕꯥ ꯃꯤꯑꯣꯏꯁꯤꯡꯅꯥ ꯑꯌꯥꯝꯕꯗꯤ ꯆꯍꯤ 25 ꯁꯨꯔꯀꯄꯗꯥ ꯀꯟꯗꯤꯁꯟ ꯑꯁꯤꯅꯥ ꯁꯤꯕꯥ ꯌꯥꯏ, ꯑꯗꯨꯕꯨ ꯁꯄꯣꯔꯇꯤꯚ ꯀꯦꯌꯔꯗꯥ ꯑꯍꯣꯡꯕꯥ ꯂꯥꯀꯄꯅꯥ ꯃꯔꯝ ꯑꯣꯏꯗꯨꯅꯥ ꯍꯧꯖꯤꯛꯇꯤ ꯃꯤꯑꯣꯏ ꯀꯌꯥꯅꯥ ꯍꯦꯟꯅꯥ ꯍꯤꯡꯂꯤ꯫

ꯁꯤꯕꯥ ꯑꯁꯤ ꯑꯌꯥꯝꯕꯗꯤ ꯁ꯭ꯕꯔ ꯍꯣꯅꯕꯥ ꯋꯥꯕꯥ (breathing) ꯅꯠꯠꯔꯒꯥ ꯀꯥꯔꯗꯤꯌꯦꯛ ꯀꯃꯞꯂꯤꯀꯦꯁꯅꯁꯤꯡꯅꯥ ꯊꯣꯀꯍꯅꯕꯅꯤ꯫ ꯅ꯭ꯌꯨꯃꯣꯅꯤꯌꯥ, ꯆꯤꯟꯖꯥꯀꯒꯨꯝꯕꯥ ꯃꯄꯥꯅꯒꯤ ꯄꯣꯠꯁꯛ ꯑꯃꯒꯤ ꯑꯦꯁ꯭ꯄꯤꯔꯦꯁꯟ, ꯅꯠꯠꯔꯒꯥ ꯑꯦꯌꯔꯋꯦ (airway obstruction) ꯑꯁꯤꯅꯁꯨ ꯁꯤꯍꯅꯕꯥ ꯌꯥꯏ꯫

DMDꯅꯥ ꯅꯥꯕꯥ ꯃꯤꯑꯣꯏ ꯑꯃꯕꯨ ꯀꯔꯝꯅꯥ ꯌꯦꯡꯁꯤꯅꯕꯤꯒꯅꯤ?

ꯀꯔꯤꯒꯨꯝꯕꯥ ꯅꯍꯥꯛꯅꯥ DMDꯅꯥ ꯅꯥꯕꯥ ꯃꯤꯑꯣꯏ ꯑꯃꯕꯨ ꯌꯦꯡꯁꯤꯜꯂꯤꯕꯥ ꯑꯣꯏꯔꯕꯗꯤ, ꯃꯈꯣꯌꯒꯤꯗꯃꯛꯇꯥ ꯑꯦꯗꯣꯕꯣꯛꯁ ꯇꯧꯕꯥ ꯍꯥꯌꯕꯁꯤ ꯌꯥꯝꯅꯥ ꯃꯔꯨꯑꯣꯏ, ꯃꯈꯣꯌꯕꯨ ꯈ꯭ꯕꯥꯏꯗꯒꯤ ꯐꯕꯥ ꯃꯦꯗꯤꯀꯦꯜ ꯀꯦꯌꯔ ꯑꯃꯁꯨꯡ ꯊꯦꯔꯥꯄꯤ ꯐꯪꯍꯅꯕꯗꯥ ꯃꯇꯦꯡ ꯄꯥꯡꯏ , ꯃꯔꯝ ꯑꯗꯨꯅꯥ ꯃꯈꯣꯌꯅꯥ ꯈ꯭ꯕꯥꯏꯗꯒꯤ ꯐꯕꯥ ꯄꯨꯟꯁꯤꯒꯤ ꯃꯒꯨꯟ ꯂꯩꯕꯥ ꯉꯃꯒꯅꯤ꯫

ꯅꯍꯥꯛ ꯑꯃꯁꯨꯡ ꯅꯍꯥꯛꯀꯤ ꯏꯃꯨꯡ-ꯃꯅꯨꯡꯅꯥ ꯆꯞ ꯃꯥꯟꯅꯕꯥ ꯑꯦꯛꯁꯄꯔꯤꯌꯦꯟꯁ ꯂꯩꯔꯕꯥ ꯑꯇꯩ ꯃꯤꯑꯣꯏꯁꯤꯡꯒꯥ ꯎꯅꯅꯕꯥ ꯁꯄꯣꯔꯠ ꯒ꯭ꯔꯨꯞ ꯑꯃꯗꯥ ꯌꯥꯎꯕꯥ ꯍꯥꯌꯕꯁꯤꯁꯨ ꯑꯐꯕꯥ ꯋꯥꯈꯜꯂꯣꯟ ꯑꯃꯥ ꯑꯣꯏꯕꯥ ꯌꯥꯏ꯫ ꯅꯍꯥꯛ ꯅꯁꯥꯃꯛ ꯅꯠꯇꯕꯥ ꯅꯠꯇꯦ ꯍꯥꯌꯕꯥ ꯈꯉꯕꯗꯁꯨ ꯑꯆꯧꯕꯥ ꯄꯨꯛꯅꯤꯡ ꯊꯧꯒꯠꯄꯥ ꯑꯃꯥ ꯑꯣꯏꯕꯥ ꯌꯥꯏ꯫

ꯑꯩꯒꯤ ꯑꯉꯥꯡ ꯑꯗꯨꯅꯥ DMDꯒꯤ ꯃꯇꯥꯡꯗꯥ ꯀꯗꯥꯏꯗꯥ ꯗꯣꯛꯇꯔꯒꯥ ꯇꯥꯟꯅꯒꯗꯒꯦ?

ꯀꯔꯤꯒꯨꯝꯕꯥ ꯅꯍꯥꯛꯀꯤ ꯑꯉꯥꯡ ꯑꯗꯨ DMD ꯂꯩꯔꯦ ꯍꯥꯌꯅꯥ ꯈꯪꯂꯕꯗꯤ, ꯃꯈꯣꯌꯅꯥ ꯂꯥꯏꯌꯦꯡꯅꯕꯥ ꯑꯃꯁꯨꯡ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯌꯦꯡꯁꯤꯟꯅꯕꯥ ꯃꯈꯣꯌꯒꯤ ꯃꯦꯗꯤꯀꯦꯜ ꯇꯤꯃꯗꯥ ꯆꯥꯡ ꯅꯥꯏꯅꯥ ꯌꯦꯡꯁꯤꯅꯕꯥ ꯃꯊꯧ ꯇꯥꯒꯅꯤ꯫

ꯅꯍꯥꯛꯀꯤ ꯑꯉꯥꯡ ꯑꯗꯨꯒꯤ DMD ꯀꯟꯗꯤꯁꯟ ꯑꯗꯨ ꯈꯪꯖꯤꯅꯕꯗꯥ ꯅꯍꯥꯛꯀꯤꯗꯃꯛꯇꯥ ꯑꯋꯥꯕꯥ ꯑꯣꯏꯕꯥ ꯌꯥꯏ꯫ ꯑꯗꯨꯕꯨ ꯅꯍꯥꯛꯀꯤ ꯃꯦꯗꯤꯀꯦꯜ ꯇꯤꯃꯅꯥ ꯅꯍꯥꯛꯀꯤ ꯑꯉꯥꯡꯒꯤ ꯂꯥꯏꯑꯣꯡꯁꯤꯡꯒꯥ ꯆꯨꯅꯕꯥ ꯁ꯭ꯠꯔꯀꯆꯔꯦꯜ ꯃꯦꯅꯦꯖꯃꯦꯟꯇ ꯄ꯭ꯂꯥꯟ ꯑꯃꯥ ꯄꯤꯒꯅꯤ꯫ ꯅꯍꯥꯛꯀꯤ ꯑꯉꯥꯡ ꯑꯗꯨꯒꯤ ꯍꯀꯁꯦꯂꯗꯥ ꯃꯤꯠꯌꯦꯡ ꯊꯝꯕꯥ ꯑꯃꯁꯨꯡ ꯃꯈꯣꯌꯅꯥ ꯃꯊꯧ ꯇꯥꯕꯥ ꯁꯄꯣꯔꯠ ꯑꯗꯨ ꯁꯣꯌꯗꯅꯥ ꯐꯪꯍꯅꯕꯥ ꯍꯥꯌꯕꯁꯤ ꯌꯥꯝꯅꯥ ꯃꯔꯨꯑꯣꯏ꯫ ꯅꯤꯡꯁꯤꯡꯕꯤꯌꯨ, ꯅꯍꯥꯛꯀꯤ ꯃꯦꯗꯤꯀꯦꯜ ꯇꯤꯃꯅꯥ ꯃꯇꯝ ꯄꯨꯝꯅꯃꯛꯇꯥ ꯅꯍꯥꯛ, ꯅꯍꯥꯛꯀꯤ ꯏꯃꯨꯡ-ꯃꯅꯨꯡ ꯑꯃꯁꯨꯡ ꯅꯍꯥꯛꯀꯤ ꯑꯉꯥꯡ ꯑꯗꯨꯕꯨ ꯃꯇꯦꯡ ꯄꯥꯡꯅꯕꯥ ꯂꯩꯔꯤ꯫

ꯑꯔꯣꯏꯕꯗꯥ, ꯃꯁꯤ ꯅꯤꯡꯁꯤꯡꯕꯤꯌꯨ (ꯇꯦꯛ-ꯍꯣꯝ ꯃꯦꯁꯦꯖ)

ꯗꯨꯆꯦꯟ ꯃꯁꯜ ꯗꯤꯁ꯭ꯠꯔꯣꯐꯤ (DMD) ꯑꯁꯤ ꯌꯥꯝꯅꯥ ꯁꯥꯊꯤꯕꯥ, ꯄꯨꯟꯁꯤ ꯆꯨꯞꯄꯥ ꯂꯥꯀꯄꯥ ꯀꯟꯗꯤꯁꯟ ꯑꯃꯅꯤ꯫ ꯑꯗꯨꯝ ꯑꯣꯏꯅꯃꯛ, ꯑꯦꯋꯥꯔꯅꯦꯁ, ꯉꯟꯅꯥ ꯈꯪꯗꯣꯀꯄꯥ, ꯑꯃꯁꯨꯡ ꯃꯇꯤꯛ ꯆꯥꯕꯥ ꯃꯦꯗꯤꯀꯦꯜ ꯑꯦꯗꯚꯥꯏꯖꯔꯤ ꯑꯃꯁꯨꯡ ꯁꯄꯣꯔꯇꯤꯚ ꯀꯦꯌꯔ ꯄꯤꯕꯅꯥ ꯑꯉꯥꯡ ꯑꯃꯒꯤ ꯄꯨꯟꯁꯤꯒꯤ ꯃꯒꯨꯟ ꯑꯗꯨ ꯌꯥꯔꯤꯕꯃꯈꯩ ꯋꯥꯡꯅꯥ ꯊꯝꯕꯗꯥ ꯃꯇꯦꯡ ꯄꯥꯡꯏ꯫

ꯅꯤꯡꯁꯤꯡꯕꯤꯌꯨ: ꯅꯍꯥꯛ ꯅꯁꯥꯃꯛ ꯅꯠꯇꯦ꯫ ꯗꯣꯛꯇꯔꯁꯤꯡ, ꯐꯤꯖꯤꯀꯦꯜ ꯊꯦꯔꯥꯄꯤꯁ꯭ꯇꯁꯤꯡ, ꯀꯥꯎꯟꯁꯦꯂꯔꯁꯤꯡ ꯑꯃꯁꯨꯡ ꯑꯇꯩ ꯁꯄꯣꯔꯠ ꯒ꯭ꯔꯨꯄꯁꯤꯡꯅꯥ ꯅꯍꯥꯛ ꯑꯃꯁꯨꯡ ꯅꯍꯥꯛꯀꯤ ꯑꯉꯥꯡ ꯑꯗꯨꯕꯨ ꯃꯇꯦꯡ ꯄꯥꯡꯅꯕꯥ ꯂꯩ꯫ ꯑꯅꯧꯕꯥ ꯂꯥꯌꯦꯡꯁꯤꯡꯒꯤ ꯃꯇꯥꯡꯗꯥ ꯔꯤꯁꯔꯆ ꯇꯧꯕꯥ ꯑꯁꯤ ꯃꯇꯝ ꯄꯨꯝꯅꯃꯛꯇꯥ ꯆꯠꯊꯔꯤ꯫ ꯃꯔꯝ ꯑꯗꯨꯅꯥ ꯑꯥꯁꯥ ꯊꯥꯗꯣꯛꯂꯣꯏꯗꯕꯅꯤ꯫ ꯈ꯭ꯕꯥꯏꯗꯒꯤ ꯃꯔꯨꯑꯣꯏꯕꯥ ꯋꯥꯐꯃꯗꯤ ꯅꯍꯥꯛꯀꯤ ꯑꯉꯥꯡ ꯑꯗꯨꯕꯨ ꯅꯨꯡꯁꯤꯕꯥ, ꯌꯦꯡꯁꯤꯅꯕꯥ ꯑꯃꯁꯨꯡ ꯄꯨꯛꯅꯤꯡ ꯊꯧꯒꯠꯄꯥ ꯑꯁꯤꯅꯤ꯫

ꯀꯔꯤꯒꯨꯝꯕꯥ ꯅꯍꯥꯛꯀꯤ ꯑꯉꯥꯡ ꯑꯗꯨꯒꯤ ꯃꯁꯂꯁꯤꯡ ꯅꯠꯠꯔꯒꯥ ꯈꯣꯡꯅꯥ ꯆꯠꯄꯒꯤ ꯑꯋꯥꯕꯥ ꯑꯃꯥ ꯂꯩꯔꯕꯗꯤ, ꯃꯗꯨ ꯑꯄꯤꯀꯄꯥ ꯋꯥꯐꯝ ꯑꯃꯥ ꯑꯣꯏꯅꯥ ꯂꯧꯔꯣꯏꯗꯕꯅꯤ꯫ꯄꯥꯎꯇꯥꯛ ꯂꯧꯅꯕꯒꯤꯗꯃꯛ ꯈꯨꯗꯛꯇꯥ ꯀ꯭ꯕꯥꯂꯤꯐꯥꯏꯗ ꯗꯣꯛꯇꯔ ꯑꯃꯒꯥ ꯇꯥꯟꯅꯧ꯫ ꯂꯥꯌꯅꯥ ꯑꯁꯤ ꯉꯟꯅꯥ ꯈꯪꯗꯣꯀꯄꯥ ꯃꯇꯃꯗꯥ, ꯃꯁꯤꯕꯨ ꯍꯦꯟꯅꯥ ꯂꯥꯌꯊꯣꯀꯍꯜꯂꯒꯅꯤ꯫


` ꯗꯨꯆꯦꯟ ꯃꯁꯜ ꯗꯤꯁ꯭ꯠꯔꯣꯐꯤ, ꯗꯤ.ꯑꯦꯝ.ꯗꯤ., ꯃꯁꯜ ꯁꯣꯟꯊꯕꯥ, ꯖꯦꯅꯦꯇꯤꯛ ꯂꯥꯌꯅꯥ, ꯅꯨꯄꯥꯃꯆꯥꯒꯤ ꯂꯥꯌꯅꯥ, ꯗꯤꯁ꯭ꯠꯔꯣꯐꯤꯟ, ꯑꯉꯥꯡꯁꯤꯡꯒꯤ ꯍꯀꯁꯦꯜ꯫

Frequently Asked Questions (FAQ)

DMDꯅꯥ ꯅꯥꯕꯥ ꯃꯤꯑꯣꯏ ꯑꯃꯒꯤ ꯄꯨꯟꯁꯤꯒꯤ ꯃꯇꯝ ꯑꯁꯤ ꯀꯌꯥꯅꯣ?

DMDꯅꯥ ꯅꯥꯕꯥ ꯃꯤꯑꯣꯏꯁꯤꯡꯅꯥ ꯑꯌꯥꯝꯕꯗꯤ ꯆꯍꯤ 25 ꯁꯨꯔꯀꯄꯗꯥ ꯀꯟꯗꯤꯁꯟ ꯑꯁꯤꯅꯥ ꯁꯤꯕꯥ ꯌꯥꯏ, ꯑꯗꯨꯕꯨ ꯁꯄꯣꯔꯇꯤꯚ ꯀꯦꯌꯔꯗꯥ ꯑꯍꯣꯡꯕꯥ ꯂꯥꯀꯄꯅꯥ ꯃꯔꯝ ꯑꯣꯏꯗꯨꯅꯥ ꯍꯧꯖꯤꯛꯇꯤ ꯃꯤꯑꯣꯏ ꯀꯌꯥꯅꯥ ꯍꯦꯟꯅꯥ ꯍꯤꯡꯂꯤ꯫

⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

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