Tiyeni tiphunzire za katemera wapadera woperekedwa wa hemophilia A (Antihemophilic Factor, Porcine Sequence, Recombinant)

Kodi dokotala wanu wakupatsani jakisoni wapadera kuti muchepetse kutuluka magazi mwadzidzidzi kwa inu kapena wachibale wanu? Mungasokonezeke pang'ono ndi dzinalo. Koma musadandaule. Tikulankhula za mankhwala amenewo lero. Nthawi zambiri amagwiritsidwa ntchito pochepetsa kutuluka magazi mu vuto losowa lotchedwa Acquired Hemophilia A. Tiyeni tikambirane za izi mosavuta komanso momveka bwino.

Kodi Acquired Hemophilia A ndi chiyani?

Mwachidule, ili ndi vuto ndi njira yolumikizirana magazi m'thupi lathu. Nthawi zambiri, tikavulala, magazi athu amaundana ndipo magazi amasiya kutuluka. Izi zimathandizidwa ndi mapuloteni apadera m'magazi athu, monga Factor VIII .

Komabe, mu Acquired Hemophilia A, chitetezo chathu chamthupi chimayamba molakwika kuukira puloteni iyi yotchedwa Factor VIII. Timatchanso ma antibodies awa. Izi zimachepetsa mphamvu ya magazi kuundana, ndipo nthawi zina zimapangitsa kuti magazi azituluka kwambiri popanda chifukwa kapena ngakhale kuvulala pang'ono. Izi sizili ngati congenital hemophilia, koma vuto lomwe lingachitike nthawi iliyonse m'moyo.

Ndiye katemera uyu (OBIZUR) amagwira ntchito bwanji?

Tsopano mukumvetsa kuti vuto ndilakuti ma antibodies athu amaukira Factor VIII yathu. Choncho madokotala amapereka katemera wapaderayu ngati yankho la izi.

Ngakhale dzina la mankhwala awa ndi lalitali, zomwe akunena ndi zofunika kwambiri:

• Chinthu Choletsa Kutuluka kwa Magazi: Izi zikutanthauza chinthu chomwe chimalimbana ndi vuto la kuchepa kwa magazi m'thupi, kapena chomwe chimalimbikitsa magazi kuundana.
• Kutsatana kwa Nkhumba: Ichi ndi chinthu chapadera. "Nkhumba" imatanthauza chinthu chogwirizana ndi nkhumba. Katemerayu amapangidwa mwanjira yofanana ndi kutsatana kwa chinthu cholimbitsa magazi cha nkhumba. Nchifukwa chiyani chimachitidwa motero? Chifukwa, ngakhale kuti ma antibodies m'thupi lathu amazindikira ndikuukira Factor VIII ya anthu, sazindikira kapangidwe kofanana ndi chinthu cholimbitsa nkhumba ichi. Chifukwa chake, amatha kuthandiza njira yolimbitsa magazi popanda kuukira.
• Chophatikiza: Izi zikutanthauza kuti mankhwalawa sapezeka mwachindunji kuchokera ku nyama, koma amapangidwa mu labotale pogwiritsa ntchito biotechnology (ukadaulo wa DNA wophatikiza) mwanjira yoyera komanso yotetezeka.

Zinthu zomwe muyenera kuuza dokotala wanu musanamwe mankhwalawa

Popeza iyi ndi mankhwala apadera, ndikofunikira kwambiri kudziwitsa dokotala wanu mbiri yonse ya matenda anu musanayambe kulandira chithandizo.

Kodi mumagwiritsa ntchito bwanji mankhwalawa?

Iyi si mankhwala omwe mumameza ngati piritsi wamba. Iyi ndi jakisoni wolowetsedwa m'mitsempha . Mankhwalawa nthawi zambiri amaperekedwa kuchipatala kapena kuchipatala ndi dokotala kapena namwino wophunzitsidwa bwino. Izi zili choncho chifukwa muyenera kuyang'aniridwa mosamala pamene chithandizocho chikuperekedwa.

Kawirikawiri, odwala ena amalangizidwa kulandira katemerayu kunyumba. Ngati ndi choncho, mudzalangizidwa momwe mungakonzekerere ndikubaya jakisoni moyenera. Musamwe mankhwala ochulukirapo kuposa momwe dokotala wanenera kapena kumwa mankhwalawo nthawi isanakwane nthawi yomwe mwapatsidwa.

Kodi mungachite chiyani ngati mlingo wa mankhwala wawonjezeka?

Ngati mukuganiza kuti mwamwa mankhwala ochulukirapo kuposa omwe mwapatsidwa, imbani nthawi yomweyo ku National Poisons Information Centre ku Colombo National Hospital kapena pitani ku Emergency Treatment Unit (ETU) ya chipatala chapafupi.

Nanga bwanji ngati ndaphonya mlingo?

Ndikofunikira kwambiri kumwa mlingo panthawi yake panthawi ya chithandizochi. Ngati mwaphonya nthawi yokumana ndi dokotala kuchipatala, imbani dokotala wanu nthawi yomweyo kuti akupatseni malangizo. Ngati mukumwa mankhwala kunyumba, imwani mlingo womwe mwaphonya nthawi yomweyo mukakumbukira. Komabe, ngati nthawi yatsala pang'ono yoti mutenge mlingo wotsatira, dumphani mlingo womwe mwaphonya ndikumwa mlingo wotsatira panthawi yomwe mwakonza. Musamwe kawiri pazifukwa zilizonse.

Zinthu zoti muziganizire panthawi ya chithandizo

• Kuyezetsa Magazi: Mukumwa mankhwalawa, dokotala wanu adzalamula kuti magazi aziyezedwe nthawi zonse kuti awone ngati akugwira ntchito bwino, momwe magazi anu akutsekerera magazi, komanso ngati thupi lanu likupanga ma antibodies atsopano motsutsana ndi mankhwalawa. Ndikofunikira kwambiri kuti musadumphe mayesowa.
• Kuyang'anira odwala: Mukakhala kuchipatala, ogwira ntchito zachipatala adzakuyang'anirani mosamala. Adzakhala akuyang'anirani nthawi zonse zizindikiro za kutuluka magazi ndi zomwe zimayambitsa ziwengo.
• ID ya Zachipatala: Ngati muli ndi hemophilia, ndikofunikira kwambiri kunyamula khadi la ID ya zachipatala kapena chibangili/unyolo womwe umalemba matenda anu, mankhwala omwe mumamwa, mlingo, ndi nthawi. Izi zingakuthandizeni kupulumutsa moyo wanu pakagwa ngozi.

Kodi zotsatirapo zake zingakhale zotani?

Monga mankhwala ena aliwonse, mankhwalawa angayambitse zotsatirapo zina, ngakhale kuti si aliyense amene amalandira. Ngati mukukumana ndi zizindikiro zotsatirazi, uzani dokotala kapena namwino nthawi yomweyo.

Ngati mukukumana ndi zizindikiro zina zachilendo zomwe sizinatchulidwe pamndandandawu, lankhulani ndi dokotala wanu za zizindikirozo.

Kuyanjana ndi mankhwala ena

Mankhwala ena omwe mukumwa angagwirizane ndi katemerayu, makamaka Factor VIIa.Muyenera kusamala kwambiri mukamagwiritsa ntchito izi pamodzi ndi mankhwala ena ochepetsa magazi, monga:

Choncho, perekani dokotala wanu mndandanda wathunthu wa mankhwala onse omwe mukumwa (mankhwala ochokera kwa dokotala, mavitamini, mankhwala ochokera ku zitsamba, ndi zowonjezera). Komanso, uzani dokotala wanu ngati mumasuta kapena kumwa mowa.