Kodi mtima wanu ukugunda mofulumira mwadzidzidzi? Izi zitha kukhala CPVT (Catecholaminergic Polymorphic Ventricular Tachycardia)!

Nthawi zina, mukatopa kwambiri, kapena mukamva chinthu chachikulu mumtima mwanu, monga chisangalalo chachikulu, chisoni, kapena mantha, kodi mtima wanu umagunda mofulumira mwadzidzidzi ndipo chifuwa chanu chimamveka cholimba? Mwina maso anu amasanduka abuluu ndipo mukumva chizungulire? Musadabwe, zinthuzi zingachitike ngakhale kwa mwana wamng'ono. Lero tikambirana za vuto lapadera lomwe limachitika mu kugunda kwa mtima, lomwe ndi losowa koma lofunika kwambiri kudziwa.

Kodi CPVT (Catecholaminergic Polymorphic Ventricular Tachycardia) ndi chiyani?

Mwachidule, CPVT (Catecholaminergic Polymorphic Ventricular Tachycardia) ndi vuto lomwe limachitika mu kayimbidwe ka mtima. Pankhaniyi, magawo apansi a mtima wanu, omwe ndi zipinda zapansi za mtima, kapena monga momwe madokotala amawatchulira, ma ventricles , mwadzidzidzi amayamba kugunda mofulumira kwambiri komanso modabwitsa mukamachita masewera olimbitsa thupi, kusewera, kapena kumva kupsinjika kwambiri, monga chisangalalo chachikulu, mantha, kapena chisangalalo.

Taganizirani izi motere: mtima wathu uli ngati pampu yamadzi. Ndi womwe umapopa magazi m'thupi lonse. Chifukwa chake, mtima uwu ukagunda mofulumira kwambiri, ndiko kuti, mu kayimbidwe kosayenera, umavutika kupopa magazi moyenera ndikutumiza ku ziwalo zonse za thupi. Izi ndi zomwe zimachitika mu CPVT.

Kodi vuto limeneli lotchedwa CPVT ndi lofala bwanji?

Ndipotu, vuto limeneli lotchedwa CPVT ndi losowa kwambiri . Malinga ndi akatswiri azachipatala, akuti munthu m'modzi yekha mwa anthu 10,000 (10,000) ali ndi vutoli. Choncho, si aliyense amene anamvapo za vutoli.

N’chifukwa chiyani CPVT imeneyi imachitika? Kodi chifukwa chake n’chiyani?

Anthu ambiri ali ndi funso lakuti, "N'chifukwa chiyani izi zimachitika?" Chifukwa chachikulu cha CPVT ndi kusintha kwa majini athu, kusintha kwa majini . Mukudziwa, chilichonse m'thupi lathu chimalamulidwa ndi majini awa.

• Nthawi zambiri, mutha kulandira majini osiyanasiyana kuchokera kwa amayi anu kapena abambo anu, kapena onse awiri.
• Koma nthawi zambiri, ndiko kuti, nthawi zambiri, kusintha kwa majini kumeneku kungachitike m'thupi la munthu watsopano mwachisawawa , popanda chikoka chilichonse cha majini kuchokera kwa makolo.

Chifukwa chake, kusintha kwa majini kumeneku kumayambitsa vuto pa momwe ma calcium ions amalamuliridwira mkati mwa maselo a mtima. Ndicho chifukwa chachikulu chomwe mtima umagunda mofulumira mtima ukakhala ndi nkhawa kapena panthawi yochita masewera olimbitsa thupi.

Kodi zizindikiro za CPVT ndi ziti? Kodi timazizindikira bwanji ?

Zizindikiro za CPVT nthawi zambiri zimayamba ali mwana, nthawi zambiri pakati pa zaka 7 ndi 12. Zizindikiro nthawi zambiri zimayamba munthu akathamanga kwambiri komanso kusewera , kapena munthu akamamva chisoni kwambiri , monga chisangalalo, mantha, mkwiyo, kapena chisangalalo.

Nazi zina mwa zizindikiro za CPVT:

• Kuposa munthu wambaMungagwe mphwayi pafupipafupi, kapena kumva chizungulire kapena mutu wopepuka. Nthawi zina mungataye mwadzidzidzi chikumbumtima popanda chifukwa chomveka ndikugwa.
• Kugunda kwa mtima ndi kugunda kwadzidzidzi, kwachangu kwambiri, komwe kumamveka ngati wina akuthamanga m'chifuwa mwanu.
• Anthu ena amathanso kudwala matenda monga khunyu . Izi zimachitika chifukwa kuchuluka kwa magazi omwe amafika muubongo kumachepa pamene mtima supompa magazi moyenera.

Chofunika: Ngati mwana wanu mwadzidzidzi akumva chizungulire akusewera, akuthamanga, kapena akudumpha, kapena ngati akudandaula kuti akuvutika kupuma, musangonyalanyaza. Ndikofunikira kufunafuna upangiri wa dokotala nthawi yomweyo.

Kodi dokotala amazindikira bwanji CPVT molondola?

Ngati inu kapena mwana wanu muli ndi zizindikiro izi, dokotala adzakuyesani mayeso angapo kuti atsimikizire ngati muli ndi CPVT.

• Echocardiogram - mayeso a echo: Izi zili ngati ultrasound scan ya mtima. Imagwiritsa ntchito mafunde a phokoso kuti ione bwino mawonekedwe a mtima wanu, momwe makoma a mtima akugwirira ntchito, ngati ma valve akugwira ntchito bwino, komanso momwe magazi akuyendera.
• ECG (Electrocardiogram): Kuyeza kumeneku kumatenga chithunzi cha zizindikiro zamagetsi za mtima wanu, kapena kayimbidwe ka mtima. Munthu amene ali ndi CPVT sangawonetse kusintha kulikonse kwakukulu pa ECG akakhala bwino.
• Mayeso Olimbitsa Thupi: Iyi ndi mayeso ofunikira kwambiri kuti muzindikire CPVT. Mukamathamanga pa treadmill kapena mukukwera njinga, kugunda kwa mtima wanu ndi ECG zimawunikidwa nthawi zonse. Anthu omwe ali ndi CPVT nthawi zambiri amakhala ndi kugunda kwa mtima mofulumira kwambiri panthawiyi.
• Mayeso ena ojambulira: Nthawi zina, dokotala wanu angakulangizeni kuti mufufuze bwino mtima wanu, monga MRI (Magnetic Resonance Imaging ), cardiac catheterization , kapena coronary angiography .
• Mayeso a Majini: Mayesowa amafufuza kusintha kwa majini komwe kumayambitsa CPVT m'magazi. Izi zitha kutsimikizira matendawa ndikuwona ngati achibale ena ali pachiwopsezo.

Nthawi zina dokotala wanu angakupatseni makina ang'onoang'ono omwe mungavale kwa masiku angapo kapena milungu ingapo. Izi zimatchedwa ambulatory monitor kapena Holter monitor.Imalemba momwe mtima wanu umagwirira ntchito tsiku lonse (24, 48, kapena kupitirira apo) pamene mukuchita ntchito zanu za tsiku ndi tsiku komanso ntchito zanu zapakhomo. Izi zimapatsa dokotala wanu lingaliro labwino la momwe mtima wanu ukugunda, ngakhale mutakhala kuti mulibe zizindikiro zilizonse.

Kodi mankhwala a CPVT ndi ati?

Ngati mtima wayamba kugunda mofulumira kwambiri, kutanthauza kuti, ngati wayamba kudwala matenda a ventricular tachycardia (Ventricular Tachycardia) , ukhoza kukhala pachiwopsezo cha moyo. Pazochitika zotere, kugwedezeka kwamagetsi (Cardioversion kapena Defibrillation) kungafunike kuti mtima ubwerere mwakale. Izi nthawi zambiri zimachitika ngati chithandizo chadzidzidzi.

Koma m'kupita kwa nthawi, cholinga chachikulu chochizira CPVT ndikuletsa kuti kugunda kwa mtima kusayende mofulumira kwambiri komanso kuti kugunda kwa mtima kukhale kwabwinobwino. Ndondomeko yanu ya chithandizo ikhoza kukhala ndi chimodzi kapena zingapo mwa izi:

• Mankhwala:
• Beta-blockers: (monga Lopressor®, Corgard®) Mankhwalawa amagwira ntchito pochepetsa mphamvu ya mahomoni monga adrenaline pamtima. Izi zimathandiza kuchepetsa kugunda kwa mtima kuti kusakwere panthawi yochita masewera olimbitsa thupi kapena kupsinjika maganizo. Uwu ndiye mtundu waukulu wa mankhwala operekedwa a CPVT.
• Zoletsa Njira za Calcium: (monga Cardizem®, Procardia®) Nthawi zina mankhwalawa amatha kuperekedwa limodzi ndi beta-blockers.
• Mankhwala ena oletsa kugunda kwa mtima: Anthu ena angapatsidwe mankhwala ena, monga flecainide.
• Chotsukira Moyo Chosalowa M'thupi (ICD): Ichi ndi chipangizo chaching'ono chogwiritsidwa ntchito ndi batire chomwe chimayikidwa opaleshoni pansi pa khungu la chifuwa. Chimayang'anira nthawi zonse kayendedwe ka mtima. Ngati kayendedwe ka mtima mwadzidzidzi kasinthasintha moopsa, chipangizocho chimadzibweretsera vuto lamagetsi kuti chibwezeretsedwe. Madokotala nthawi zambiri amalimbikitsa ICD kwa anthu omwe ali pachiwopsezo chachikulu komanso omwe kugunda kwa mtima wawo kumakhala kovuta kuwongolera ndi mankhwala okha.
• Kuchepetsa Kupweteka kwa Mtima Kumanzere (LCSD): Iyi ndi njira yochitira opaleshoni yomwe imachotsa mitsempha ina yomwe imapita kumtima. Izi zitha kuchepetsa kukondoweza kwa mtima ndikuchepetsa chiopsezo cha kugunda koopsa. Opaleshoni iyi ingaganizidwe kwa anthu omwe ali ndi ICD omwe nthawi zambiri amadabwa kapena omwe sakuyankha bwino mankhwala.

Kuphatikiza apo, muyenera kusintha zinthu zofunika kwambiri pa moyo wanu.

• Kuchita masewera olimbitsa thupi otopetsa , monga kuthamanga mofulumira kapena kunyamula zolemera, kuyenera kuchepetsedwa.
• Kwa mwana wamng'ono amene ali ndi CPVT, ndi bwino kupewa masewera ampikisano , chifukwa chisangalalo ndi kukakamizidwa kopambana mpikisano zingayambitse mtima kugunda mofulumira.
• Ndikofunikanso kwambiri kuchita njira zochepetsera kupsinjika maganizo.

Kodi tingaletse bwanji CPVT iyi kuti isachitike?

Popeza CPVT imayamba chifukwa cha kusintha kwa majini, palibe njira yoletsera kuti isachitike . Chifukwa si chinthu chomwe tingathe kuchilamulira.

Komabe, munthu akangozindikira CPVT, ngati yathandizidwa bwino, kutanthauza kuti, ngati mankhwala omwe dokotala wamupatsa agwiritsidwa ntchito moyenera, kusintha kwa moyo wake kumachitika monga momwe adanenera, ndipo kupita kwa dokotala nthawi zonse kumachitika, ngakhale munthu amene ali ndi CPVT akhoza kukhala ndi moyo wabwinobwino komanso wapamwamba.

Ngati wina m'banja mwanu wapezeka ndi CPVT, ndikofunikira kuganizira zoyezetsa majini ndi upangiri wa majini kwa anthu ena a m'banjamo, makamaka ana. Mlangizi wa majini angakuthandizeni kumvetsetsa bwino vutoli, kukambirana za mwayi woti ana anu adzalandira matendawa, ndikukambirana nkhani zofunika monga zomwe mungachite pa vutoli.

Kodi n’chiyani chingachitike kuti tipewe mavuto omwe angabwere chifukwa cha CPVT?

Ngati CPVT siilamulidwa bwino, mavuto ena oopsa angachitike. Mutha kuchita izi kuti muchepetse chiopsezo chanu:

• Lankhulani ndi dokotala wanu ndipo pangani dongosolo lotetezeka lochita masewera olimbitsa thupi lomwe lingagwire ntchito kwa inu. Simuyenera kusiya kuchita masewera olimbitsa thupi kotheratu, koma muyenera kudziwa masewera olimbitsa thupi omwe ndi abwino ndi omwe si abwino.
• Chepetsani kumwa zakumwa zokhala ndi caffeine monga khofi, tiyi, chokoleti, ndi zakumwa zina zoziziritsa kukhosi momwe mungathere, chifukwa caffeine imalimbitsa mtima wanu ndipo imatha kukweza kugunda kwa mtima.
• Nthawi zonse samalani ndi zizindikiro zanu . Ngati mukumva chizungulire, chifuwa chanu chikulimba, kapena mukuvutika kupuma, musanyalanyaze zizindikiro izi. Imbani dokotala wanu nthawi yomweyo.
• Musaphonye tsiku lililonse la mankhwala omwe dokotala wanu wakupatsani, imwani panthawi yoyenera komanso mu mlingo woyenera .
• Ndikofunikira kwambiri kuonana ndi dokotala nthawi yake ndikulandira mayeso ofunikira. Ichi ndi chinthu chomwe muyenera kuchita moyo wanu wonse.

Kodi munthu amene ali ndi CPVT angayembekezere tsogolo lotani?

Ngati sichinachiritsidwe, CPVT ingayambitse mavuto azaumoyo komanso mavuto ena. Mavuto ena, monga kulephera kwa mtima mwadzidzidzi , akhoza kukhala pachiwopsezo.

Koma nkhani yabwino ndi yakuti ndi chithandizo choyenera komanso moyo wathanzi, anthu ambiri omwe ali ndi CPVT amatha kusunga kugunda kwa mtima kwabwinobwino, kuchepetsa kwambiri chiopsezo cha mavutowa, ndikukhala ndi moyo wosangalala komanso wokhutiritsa.

Ngati muli ndi CPVT, muyenera kuthandizidwa ndi dokotala moyo wanu wonse kuti muwonetsetse kuti mtima wanu uli bwino.Ndikofunikira. Izi zikutanthauza kuti muyenera kupita kwa dokotala nthawi zonse ndikulandira mayeso ofunikira. Ngati zizindikiro za CPVT zikubwereranso, monga kumva chizungulire mutatha kuchita masewera olimbitsa thupi, funsani dokotala nthawi yomweyo.

Zinthu zoti mufunse dokotala wanu

Ngati inu kapena mwana wanu muli ndi zizindikiro izi, kapena ngati mwapezeka kale ndi CPVT, zingakhale zothandiza kwambiri kuti mufunse dokotala wanu momveka bwino za izi:

• Kodi chimayambitsa zizindikiro zimenezi ndi chiyani? Kodi ichi ndi CPVT?
• Ndi mayeso ena ati omwe ine kapena mwana wanga tiyenera kukhala nawo kuti titsimikizire ngati ndili ndi CPVT?
• Kodi njira zabwino zochiritsira CPVT ndi ziti? Ndi chithandizo chiti chomwe chili chabwino kwa ine/mwana wanga?
• Kodi ubwino ndi zotsatirapo zake ndi ziti?
• Kodi muyenera kuchita chiyani pakati pa kupita kwa dokotala, kuthetsa zizindikiro kunyumba, kapena pakagwa ngozi?
• Ndi kusintha kotani komwe ndikufunika kusintha pa moyo wanga (zakudya, masewera olimbitsa thupi)?
• Kodi achibale ena ali pachiwopsezo? Kodi nawonso ayenera kuyezedwa?

Pomaliza, zomwe muyenera kukumbukira (Uthenga Wopita Nawo Kunyumba)

Kotero, ngakhale kuti vuto lomwe takambirana mwatsatanetsatane, CPVT (Catecholaminergic Polymorphic Ventricular Tachycardia), lingawoneke loopsa pang'ono, chinthu chofunikira kwambiri ndikuzindikira msanga ndikuchiritsidwa bwino.

Ngati dokotala wanu akukupatsani chithandizo choyenera, kulandira chithandizo monga momwe mwalangizira, komanso kusintha moyo wanu mosavuta, ngakhale munthu amene ali ndi CPVT akhoza kukhala moyo wabwinobwino, wokangalika, komanso wokhutiritsa. Kumbukirani, ngati muli ndi zizindikiro, ndikofunikira kupita kwa dokotala mwamsanga popanda kuzinyalanyaza. Simuli nokha paulendowu, ndipo pali madokotala aluso ndi akatswiri azaumoyo omwe angakuthandizeni ndikusamalirani. Choncho musachite mantha, limbanani ndi izi molimba mtima.

CPVT , kugunda kwa mtima, kugunda kwa mtima, tachycardia ya ventricular, kusintha kwa majini, sitiroko, kuima kwa mtima mwadzidzidzi, thanzi la mwana