Kodi khungu lanu likukulirakulira ndipo likulimba? Tiyeni tiphunzire za Scleroderma!

Kodi nthawi zina mumamva ngati khungu lanu ndi lolimba komanso lolimba kuposa masiku onse? Kapena muli ndi ululu wa mafupa kapena kuuma kwa m'mawa? Izi ndi zinthu zomwe sitingaziganizire kwambiri. Komabe, zitha kukhalanso zizindikiro za matenda osowa otchedwa Scleroderma . Tiyeni tikambirane za izi mwatsatanetsatane lero, sichoncho?

Kodi Scleroderma ndi chiyani?

Mwachidule, Scleroderma ndi matenda osowa omwe minofu ya thupi lanu imakhala yolimba komanso yolimba kuposa yachibadwa. Nthawi zambiri, imakhudza khungu. Koma nthawi zina, vutoli lingakhudze minofu ina iliyonse m'thupi.

Kwenikweni ili ndi vuto la autoimmune . Tsopano mwina mukudabwa kuti 'autoimmune disorder' ndi chiyani. Thupi lathu lili ndi dongosolo lofanana ndi la asilikali lomwe limatiteteza ku matenda, lotchedwa chitetezo chamthupi. Koma mu mkhalidwe uwu, dongosolo limenelo limalakwika, ndipo m'malo molimbana ndi majeremusi akunja, limayamba kuukira maselo athu abwino. Zili ngati sitingathe kudziwa omwe ali athu ndi omwe ali mdani. Ngakhale madokotala sakudziwabe chifukwa chake izi zimachitika.

Ngati muli ndi scleroderma, chitetezo chanu cha mthupi chimauza maselo a thupi lanu kuti apange puloteni yochuluka yotchedwa collagen . Matupi athu amafunikiradi collagen. Ndi chomwe chimapanga minofu yolumikizana yamphamvu komanso yathanzi yomwe imathandizira ziwalo zathu. Koma ikachuluka kwambiri, khungu ndi minofu ina imakhala yokhuthala komanso yolimba kuposa masiku onse.

Matenda a scleroderma ndi matenda osatha . Izi zikutanthauza kuti mungakhale ndi zizindikirozi kwa nthawi yayitali, mwina kwa moyo wanu wonse. Komanso, ngati zimakhudza minofu ya ziwalo zanu zamkati, zingayambitse mavuto omwe angakupheni. Ngati mukumva ngati muli ndi vuto la mtima, mukuvutika kupuma, kapena mukuvutika kumeza, imbani 911 (kapena nambala yanu yadzidzidzi yapafupi) nthawi yomweyo, kapena pitani kuchipatala chadzidzidzi.

Ngati muli ndi ululu kapena kuuma kwa mafupa anu, makamaka pafupi ndi zala zanu ndi zala zanu, muyenera kuwona dokotala.

Kodi mitundu ikuluikulu ya Scleroderma ndi iti?

Madokotala amagawa scleroderma m'magulu awiri akuluakulu:

1. Localized Scleroderma: 'Localized' amatanthauza kutsekeredwa pamalo amodzi. Mtundu uwu umakhudza gawo limodzi lokha la thupi (nthawi zambiri khungu). Umayambitsa mawanga kapena mizere ya khungu lokhuthala komanso lofanana ndi sera. Chabwino kwambiri ndichakuti localized scleroderma nthawi zina imatha yokha . Komanso nthawi zambiri sifalikira ku ziwalo zina za thupi.

2.Systemic Sclerosis: Mtundu uwu ungakhudze ziwalo zina kuwonjezera pa khungu. Ungakhudze dongosolo lanu la kupuma (chiwalo chomwe chimakuthandizani kupuma ndi kununkhiza) ndi dongosolo lanu la m'mimba (chiwalo chomwe chimasintha chakudya chomwe timadya kukhala mphamvu). Ngati scleroderma imakhudza mphamvu yanu yopumira kapena kuyamwa zakudya, mumakhala ndi mwayi waukulu wopeza mavuto aakulu. Ikhozanso kupha. Systemic Sclerosis ilinso ndi mitundu itatu - diffuse, limited, ndi sine sclerosis.

Kufalikira kwa Sclerosis

'Diffuse' amatanthauza 'kufalikira'. Mu mkhalidwe uwu, diffuse sclerosis imachitika mwadzidzidzi m'malo akuluakulu a thupi. Mwachitsanzo:

• Chifuwa
• Mimba
• Matchafu
• Manja
• Miyendo
• Nkhope

Komanso, imatha kukhudza ziwalo zingapo nthawi imodzi. Izi zikutanthauza:

• Dongosolo la m'mimba (Gawo la m'mimba - njira ya m'mimba)
• Impso
• Mtima
• Mapapu

Matenda a CREST (Limited Sclerosis)

Madokotala nthawi zambiri amatcha matenda a CREST otchedwa Limited Scleroderma. Chilembo chilichonse mu CREST chimayimira chizindikiro chomwe chimayamba chifukwa cha matendawa:

• C - Calcinosis: Kuchuluka kwa calcium m'thupi. Kungawoneke ngati mabala ang'onoang'ono oyera pakhungu.
• R - Matenda a Raynaud: Kusintha mtundu ndi dzanzi la zala ndi zala. Zitha kuoneka zotumbululuka, zabuluu, kapena zofiira zikakhudzidwa ndi kuzizira.
• E - Kulephera kwa m'mero: Kuvuta kumeza ndi acid reflux.
• S - Sclerodactyly: Kulimba kwa khungu pa zala, zomwe zimapangitsa kuti zikhale zovuta kupindika ndi kuwongola zala.
• T - Telangiectasias: Madontho ang'onoang'ono, ofiira kapena osintha mtundu pakhungu. Izi zitha kuwoneka ngati ukonde wa akangaude.

Sine Sclerosis

Pankhani ya Sine Sclerosis, zizindikiro za Limited Sclerosis zomwe tatchula kale zimawonekera, koma khungu silikhudzidwa . Izi zikutanthauza kuti, mungakhale ndi zizindikiro zina zomwe zatchulidwa mu CREST syndrome, koma palibe kukhuthala kooneka kwa khungu.

Kodi matenda a Scleroderma ndi ofala bwanji?

Scleroderma ndi matenda osowa kwambiri.Akatswiri akuti anthu pafupifupi 250 pa anthu miliyoni ku United States ali ndi mitundu yonse itatu ya scleroderma. Mwa anthu amenewa, anthu pafupifupi 100,000 ali ndi matenda a systemic sclerosis.

Kodi zizindikiro za Scleroderma ndi ziti?

Anthu ena omwe ali ndi scleroderma sangakhale ndi zizindikiro zilizonse kumayambiriro. Komabe, kwa ambiri, chizindikiro chachikulu ndikuwoneka ngati mawanga okhuthala kapena mizere pakhungu. Kuphatikiza apo, palinso zizindikiro zina zodziwika bwino:

• Kupweteka kwa mafupa
• Kuuma , makamaka m'mawa mukadzuka
• Kutopa (kumva kutopa kwambiri nthawi zonse)
• Kuchepetsa thupi kosamveka bwino

Zizindikiro zina zomwe mumakumana nazo (ndi komwe zimakukhudzani) zimadalira mtundu wa scleroderma yomwe muli nayo.

Zizindikiro za Localized Scleroderma

Anthu omwe ali ndi matenda a scleroderma nthawi zambiri amaona kuti khungu lawo likukhuthala . Kukhuthala kumeneku kungachitike m'dera limodzi kapena m'mabala. Kungakhudze madera otsatirawa a khungu:

• Chifuwa
• Mimba (malo ozungulira mimba)
• Manja ndi miyendo (Manja ndi miyendo yanu)
• Manja ndi zala
• Mapazi ndi zala

Komabe, matenda a scleroderma omwe amakhudza ziwalo zamkati mwa thupi ndi osowa kwambiri .

Zizindikiro za Systemic Sclerosis

Matenda a systemic sclerosis angayambitse zizindikiro zosiyanasiyana. Izi zimapangitsanso kuti khungu likhale lolimba, koma nthawi zambiri m'malo akuluakulu komanso m'mabala. Makamaka pankhope ndi m'manja. Khungu lolimba likhoza kuyamba m'zala ndi zala kenako n'kufalikira m'thupi lonse. Ngati muli ndi matenda a Raynaud , zala ndi zala za mwendo zomwe zakhudzidwa zimatha kusintha mtundu zikakhudzidwa ndi kuzizira (nthawi zambiri zimakhala zoyera, zofiira, kapena zabuluu wofiirira).

Matenda a systemic sclerosis angayambitsenso zizindikiro m'ziwalo ndi minofu yanu ina. Mwachitsanzo:

• Minofu: Kusanza ndi kutupa, makamaka m'manja ndi m'mapazi (kumapeto kwa miyendo yanu).
• Mafupa: Kuuma, kutupa, ndi kulephera kuyenda.
• Mapapo: Chifuwa ndi kuvutika kupuma (kupuma movutikira).
• Matenda a m'mimba: dysphagia, kutentha pamtima, kudzimbidwa, kudzimbidwa, ndi kutsegula m'mimba.
• Mtima:Kugunda kwa mtima kosazolowereka (arrhythmia), madzi ozungulira mtima (pericardial effusion), ndi kukhuthala kwa minofu ya mtima (fibrosis).
• Impso: Kulephera kwa impso (izi zitha kupha munthu).
• Ziwalo zoberekera: Kulephera Kugonana (ED) mwa amuna ndi kuuma kwa nyini mwa akazi.

Kodi n’chiyani chimayambitsa matenda a scleroderma?

Ndipotu, madokotala sakudziwabe chomwe chimayambitsa matenda a scleroderma.

Kafukufuku wina wapeza kuti imatha kuchitika m'mabanja mpaka pamlingo winawake (kutanthauza kuti imatha kufalikira kuchokera kwa makolo kupita kwa ana), koma ndi yosowa kwambiri kotero kuti palibe umboni wokwanira wotsimikizira kuti ndi matenda a majini .

Zinthu Zoopsa za Scleroderma

Aliyense akhoza kudwala scleroderma, koma magulu ena ali pachiwopsezo chachikulu:

• Azimayi ali ndi mwayi wochuluka wopeza matendawa nthawi zinayi kuposa amuna.
• Kawirikawiri imapezeka mwa anthu azaka zapakati pa 30 ndi 50. Scleroderma ndi yosowa kwambiri kwa anthu osakwana zaka 30.
• Anthu akuda ali ndi mwayi waukulu wopeza matenda a scleroderma. Amakondanso kudwala matendawa msanga, amakhala ndi mwayi waukulu wopeza zizindikiro zomwe zimakhudza mapapo, komanso amakhala ndi zizindikiro zoopsa pakhungu.

Kodi mavuto omwe angakhalepo chifukwa cha Scleroderma ndi ati?

Anthu omwe ali ndi scleroderma ali pachiwopsezo chachikulu chotenga matenda ena awiri: Raynaud's syndrome ndi Sjögren's syndrome .

Matenda a Raynaud amakhudza mitsempha yaing'ono yamagazi m'zala zanu ndi zala zanu (madigiri anu). Anthu omwe ali ndi vutoli amakumana ndi zizindikiro zina (nthawi zina zimatchedwa 'kuukira'). Apa ndi pamene mitsempha yamagazi m'zala zanu imagwedezeka mwadzidzidzi kwambiri. Izi zingapangitse khungu m'zala zomwe zakhudzidwa kukhala lofiirira, kapena lopepuka kuposa mtundu wa khungu lanu lachilengedwe. Nthawi zina, limatha kuoneka ngati labuluu.

Matenda a Sjögren amachititsa kuti tiziwalo tina ta m'thupi lanu tipange chinyezi chochepa - nthawi zambiri tinthu ta m'kamwa mwanu ndi tinthu ta misozi m'maso mwanu. Anthu ena omwe ali ndi matenda a Sjögren amamvanso kupweteka kwa minofu ndi mafupa.

Mitundu ina ya scleroderma ingayambitse mavuto aakulu . Ena mwa iwo ndi awa:

• Kulephera kwa impso
• Kuthamanga kwa magazi m'mapapo (kuthamanga kwa magazi m'mitsempha yomwe imanyamula magazi kuchokera pamtima kupita ku mapapo)
• Pulmonary fibrosis (mabala a minofu ya m'mapapo)
• Matenda a mtima (mavuto omwe amakhudza mtima wanu ndi mitsempha yamagazi)
• Kulephera kwa mtima, vuto la mtima
• Kusowa kwa chitetezo chamthupi
• Matenda a m'mimba (matenda omwe amakhudza momwe thupi limagwirira ntchito chakudya ndi kuyamwa zakudya)
• Khansa

Zina mwa zovutazi zimatha kupha . Ngati muwona zizindikiro zatsopano kapena zosintha, pitani kwa dokotala mwachangu momwe mungathere. Ngati mukuganiza kuti muli ndi zizindikiro za matenda a mtima, monga kuvutika kupuma kapena kumeza, imbani 911 (kapena nambala yanu yadzidzidzi yapafupi) nthawi yomweyo, kapena pitani kuchipatala.

Kodi matenda a scleroderma amachiritsidwa bwanji?

Dokotala amazindikira matenda a scleroderma kudzera mu mayeso a thupi ndi mayeso ena angapo.

Mungafunikenso kuonana ndi dokotala wa nyamakazi , dokotala amene amachiritsa matenda a chitetezo chamthupi. Iye adzakuyang'anirani ndikufunsani za zizindikiro zanu. Muyenera kuuza dokotala wanu zizindikiro zanu, nthawi yomwe zinayamba, komanso ngati pali chilichonse chomwe chikukupangitsani kukhala woipitsitsa.

Muyeneranso kuyesedwa kangapo kuti muwonetsetse kuti mulibe matenda ena omwe amayambitsa zizindikiro zofanana.

Kodi madokotala amagwiritsa ntchito mayeso otani kuti adziwe matenda a Scleroderma?

Kuzindikira matenda a scleroderma nthawi zambiri ndi gawo la njira yotchedwa 'differential diagnosis.' Izi zikutanthauza kuti dokotala wanu mwina adzachotsa matenda ena ndikuchita mayeso angapo kuti adziwe chomwe chikuyambitsa zizindikiro zanu asanakuzindikireni ndi scleroderma. Nazi zina mwa mayeso omwe mungakhale nawo:

• Kuyezetsa magazi kuti muwone momwe chitetezo cha mthupi lanu chikugwirira ntchito.
• Mayeso a ntchito ya m'mapapo kuti aone ngati mapapu anu kapena dongosolo lanu lopumira lakhudzidwa.
• Kujambula ndi njira yomwe chitsanzo chaching'ono cha khungu kapena minofu ina yomwe yakhudzidwa imatengedwa ndikuyesedwa mu labotale.
• Ngati muli ndi zizindikiro za kugaya chakudya (GI), endoscopy ndi mayeso omwe amayang'ana pansi pa pakhosi kapena m'mimba mwanu ndi kamera kakang'ono kolumikizidwa ku chubu chachitali komanso choonda.

Kuphatikiza apo, muyenera kuyesedwa zithunzi zingapo kuti mujambule zithunzi za mkati mwa thupi lanu. Izi zikuphatikizapo:

• Kadiyogramu ya Kadiyo (ECG)
• Echocardiogram (Echocardiogram - Echo)
• X-ray ya pachifuwa
• Kujambula kwa CT (Computed Tomography - CT scan)

Kodi matenda a scleroderma amachiritsidwa bwanji?

Palibe mankhwala a scleroderma , koma dokotala wanu angakuthandizeni kupeza njira zosiyanasiyana zomwe zingakuthandizeni kuchepetsa zizindikiro zanu ndikuchepetsa mphamvu zake pa moyo wanu watsiku ndi tsiku.

Mtundu wa chithandizo chomwe mukufuna chimadalira komwe zizindikiro zanu zili komanso momwe zilili zoopsa. Nazi njira zina zochizira matenda a scleroderma:

• Mankhwala a khungu: Muyenera kugwiritsa ntchito mafuta odzola ndi mafuta odzola kuti khungu lanu lisaume.
• Mankhwala Oletsa Kutupa kwa Thupi: Mankhwalawa amaletsa chitetezo cha mthupi lanu kuwononga maselo ndi minofu yathanzi.
• Mankhwala oletsa zizindikiro zinazake: Mwachitsanzo, mungafunike kumwa mankhwala oletsa kuthamanga kwa magazi, kupangitsa kupuma kukhala kosavuta, kuthana ndi kulephera kwa impso, kapena kuchepetsa zizindikiro za kugaya chakudya.
• Kuchiza thupi: Katswiri wa zamaganizo angakuthandizeni kukonza mayendedwe anu a thupi.
• Kuchiza ndi Phototherapy: Izi zimaphatikizapo kugwiritsa ntchito kuwala kowala komanso kolunjika kwa ultraviolet (UV) pochiza matenda a khungu. Izi zingathandize kuchiza khungu lokhuthala.
• Kusamutsa maselo oyambira: Anthu ena omwe ali ndi zizindikiro zoopsa angafunike kusamutsa maselo oyambira. Izi zimaphatikizapo kusintha maselo a magazi omwe awonongeka ndi maselo athanzi opereka magazi.

Ngati ndili ndi Scleroderma, ndiyenera kuyembekezera chiyani?

Muyenera kuyembekezera kuthana ndi matenda a scleroderma ndi zizindikiro zake kwa moyo wanu wonse . Ngakhale kuti palibe mankhwala okhalitsa, anthu ambiri amapeza njira zochiritsira komanso kusintha moyo wawo zomwe zingachepetse kukhudzidwa kwa zizindikiro zawo pa moyo wawo watsiku ndi tsiku.

Kukhala ndi matenda a nthawi yayitali kungakhale kokhumudwitsa nthawi zina. Funsani dokotala wanu za magulu othandizira kapena mwayi wophunzira kuti akuthandizeni kuthana ndi nkhawa zanu komanso thanzi lanu la maganizo.

Kodi Scleroderma ikhoza kupewedwa?

Popeza chifukwa chenicheni sichikudziwika, palibe njira yopewera scleroderma .

Kodi ndimadzisamalira bwanji? (Kudzisamalira)

Kuwonjezera pa mankhwala omwe mumagwiritsa ntchito nthawi zonse, mutha kuthana ndi zizindikiro zina mwa kusintha moyo wanu watsiku ndi tsiku. Zina mwa izi ndi izi:

• Kutsatira zakudya zabwino komanso dongosolo lochita masewera olimbitsa thupi lomwe likuyenererani.
• Kupewa kuchita masewera olimbitsa thupi kwambiri pamene simukumva bwino.
• Tetezani khungu lanu mwa kuvala zovala zoyenera malo anu ndikugwiritsa ntchito mafuta abwino oteteza ku dzuwa mukatuluka panja.
• Pitani kwa dokotala wa mano (wopereka chithandizo cha mano) kuti mukayeretse mano anu nthawi zonse komanso kuti mukayezedwe.

Ndiyenera kupita liti kwa dokotala wanga?

Scleroderma ingayambitse zizindikiro zosiyanasiyana, kotero nthawi zina zimakhala zovuta kuzizindikira poyamba. Ngati muli ndi ululu watsopano kapena zizindikiro zina, makamaka ngati zikuipiraipira, onani dokotala. Ngakhale zizindikiro zanu zitakhala chifukwa cha china chake, dokotala wanu akhoza kuzindikira chomwe chikuyambitsa ndikupangira chithandizo choziletsa.

Ngati chithandizo chanu cha scleroderma sichikugwira ntchito bwino, kapena ngati zizindikiro zanu zikusintha kapena kukulirakulira - makamaka ngati zikukhudza kupuma kwanu kapena kumeza - lankhulani ndi dokotala wanu.

Kodi ndiyenera kupita liti ku Emergency Treatment Unit (ETU) ?

Ngati muli ndi zizindikiro za matenda a mtima , monga kupweteka pachifuwa, kupuma movutikira, kapena ngati mukumva ngati simungathe kumeza, imbani 911 (kapena nambala yanu yadzidzidzi yapafupi) nthawi yomweyo, kapena pitani ku dipatimenti yadzidzidzi yachipatala.

Ndi mafunso ati omwe ndiyenera kufunsa dokotala wanga?

Musaiwale kufunsa mafunso awa mukapita kwa dokotala:

• Kodi ndili ndi Scleroderma kapena matenda ena?
• Kodi ndili ndi mtundu wanji wa Scleroderma?
• Kodi ndi chithandizo chamtundu wanji chomwe ndikufunika?
• Ndi mavuto ati omwe ndiyenera kuwadziwa bwino?

Kodi munthu amene ali ndi matenda a Scleroderma amakhala ndi moyo wautali bwanji?

Anthu ambiri omwe ali ndi scleroderma sakumana ndi mavuto omwe angaike moyo pachiswe .

Komabe, ngati muli ndi matenda a systemic sclerosis, omwe amakhudza ziwalo zamkati, muli pachiwopsezo chachikulu cha mavuto aakulu. Dokotala wanu adzakuuzani zomwe mungayembekezere komanso ngati muli pachiwopsezo chachikulu cha mavuto oopsa.

Kodi Scleroderma ndi matenda oopsa?

Monga matenda ena aliwonse osatha, scleroderma ndi vuto lalikulu komanso loopsa.Izi zili choncho chifukwa mwina mudzayenera kuthana ndi zizindikirozo kwa moyo wanu wonse. Komabe, sizikutanthauza kuti Scleroderma idzalamulira moyo wanu. Zomwe aliyense amakumana nazo zimasiyana. Lankhulani ndi dokotala wanu za mantha anu, kukayikira kwanu, ndi nkhawa zanu.

Matenda a scleroderma angakhale vuto lokhumudwitsa kwambiri. Popeza madokotala sadziwa chomwe chimayambitsa matendawa ndipo palibe chithandizo chokwanira, zingatenge nthawi kuti mupeze chithandizo chomwe chingachepetse zizindikiro zanu bwino. Dokotala wanu adzakuthandizani panjira iliyonse.

Khulupirirani zomwe mukumva m'mimba mwanu, ndipo khulupirirani zomwe zikuoneka kuti 'sizili bwino'. Ngakhale kusintha pang'ono kwa zizindikiro kungakhale chizindikiro cha vuto lomwe liyenera kufufuzidwa ndi dokotala wanu. Musaope kufunsa mafunso ndikugawana malingaliro anu okhudza zizindikiro zanu kapena chithandizo chanu.

Kukhala ndi matenda osatha kungakhale kotopetsa kwambiri. Tengani nthawi yodzilemekeza ndi kuzindikira chifukwa cha ntchito yovuta yomwe mwagwira pothana ndi zizindikiro zanu.

Zinthu zofunika kuzikumbukira (Uthenga Wopita Nawo Kunyumba)

Chabwino, takambirana zambiri za Scleroderma tsopano. Pomaliza, nazi zina mwa zinthu zofunika kwambiri zomwe muyenera kukumbukira:

• Scleroderma ndi matenda osowa kwambiri, omwe amayambitsa chitetezo chamthupi chomwe thupi limapanga collagen yambiri, zomwe zimapangitsa kuti khungu ndi nthawi zina ziwalo zamkati zikhale zokhuthala.
• Pali mitundu iwiri ikuluikulu ya izi: ya m'deralo ndi ya m'thupi. Mtundu wa m'thupi ndi woopsa pang'ono chifukwa ungakhudzenso ziwalo zamkati.
• Zizindikiro zimasiyana. Zizindikiro zazikulu ndi monga kukhuthala kwa khungu, kupweteka kwa mafupa, kutopa, ndi matenda a Raynaud.
• Ngakhale kuti palibe mankhwala ochiritsira matenda, pali mankhwala othandiza oletsa zizindikiro. Lankhulani ndi dokotala wanu ndipo pangani dongosolo la chithandizo lomwe lingakuthandizeni.
• Kuzindikira msanga ndi kulandira chithandizo n'kofunika kwambiri, choncho ngati muli ndi zizindikiro izi, onetsetsani kuti mwapeza upangiri wa dokotala.
• Popeza vutoli ndi la nthawi yayitali, ndikofunikira kukhala olimba m'maganizo. Ngati kuli kofunikira, funani thandizo kuchokera ku magulu othandizira.

Musadandaule, simuli nokha. Ndi chidziwitso choyenera komanso upangiri wachipatala, mutha kukhala bwino ndi vutoli.

` Scleroderma, Scleroderma, Kukhuthala kwa khungu, Matenda a chitetezo chamthupi, Collagen, Raynaud's syndrome, Systemic sclerosis, Matenda a khungu