Reka twige ku rukingo rwa Pegvaliase rwa PKU.

Ese wowe cyangwa umuntu wo mu muryango wawe ufite indwara yitwa Phenylketonuria? Niba ari uko bimeze, muganga wawe ashobora kuba yarakwandikiye umuti witwa Pegvaliase. Kubera ko uyu ari umuti udasanzwe, ni ibisanzwe kugira ibibazo n'impungenge kuri wo. None rero uyu munsi, reka tuganire kuri uyu muti n'ibintu ugomba kumenya mugihe uwukoresha.

Uru rukingo rwa Pegvaliase ni uruhe?

Muri make, Phenylketonuria (PKU) ni indwara aho umubiri wacu udashobora gusya neza aside amine yitwa phenylalanine. Ibi ni ibintu bikunze kuboneka mu biribwa bikungahaye kuri poroteyine turya. Iyo iyi phenylalanine yirundanyije mu mubiri w'umuntu urwaye PKU, ikomeza kwiyongera mu maraso kandi ishobora kwangiza, cyane cyane ubwonko, uko igihe kigenda gihita.

Rero, icyo uru rushinge rwa Pegvaliase rukora ni ukugabanya urugero rw'umusemburo wa phenylalanine udakenewe kandi urenze urugero mu maraso. Akenshi uza ku izina rya Palynziq.

Ibintu ugomba kubwira muganga wawe mbere yo gufata umuti

Mbere yo gutangira uyu muti, ni ngombwa cyane kuganira na muganga wawe kuri ibi bintu mu buryo busobanutse neza kandi mu buryo buboneye. Ntugahishe ikintu icyo ari cyo cyose.

• Tubwire niba ufite aleriji kuri Pegvaliase cyangwa undi muti, ibiryo, cyangwa irangi.
• Niba utwite cyangwa wifuza gusama, menya neza ko ubivuze.
• Niba uri umubyeyi wonsa, menyesha muganga wawe na byo.

Dukurikije aya makuru, bizoroha ko muganga afata icyemezo niba uyu muti ukubereye cyangwa utakubereye.

Ni gute wakoresha urukingo neza?

Uru ni urushinge rwo mu mubiri. Muganga wawe cyangwa umuforomo wawe azajya aguha amabwiriza asobanutse neza y'uko warutanga mu rugo. Ni ngombwa cyane gukurikiza aya mabwiriza neza.

• Fata ingano ikwiye, mu gihe gikwiye: Fata umuti gusa mu gihe kandi mu rugero rukwiye nk'uko muganga wawe yabigutegetse. Ntukigere ufata ingano irenze iyategetswe.
• Shyira inshinge n'inshinge neza: Ntukigere ujugunya inshinge n'inshinge zakoreshejwe mu myanda. Ahubwo, zishyire mu kintu cyabigenewe gikoreshwa mu gukaraba. Niba udafite, saba muganga wawe.
• Agatabo k'amakuru yihariye (MedGuide):Mbere ya buri buryo bwo kuvurwa, uzahabwa agapapuro kabigenewe 'MedGuide', agapapuro karimo ibisobanuro birambuye ku muti. Buri gihe ujye usoma witonze.

Bite se nintakaza urugero rw'umuti?

Niba ubuze dose mu buryo butunguranye, ntugahangayike. Ntugafate dose yabuze. Fata dose ikurikira ku gihe cyawe gisanzwe. Ntugafate dose ebyiri.

Bite ho nindamuka nkoresheje imiti irenze urugero?

Niba ubona ko wafashe imiti myinshi cyane, hamagara ikigo cy’igihugu gishinzwe amakuru ku burozi mu bitaro by’igihugu bya Colombo, cyangwa ujye mu ishami rishinzwe kuvura byihutirwa (ETU) ry’ibitaro biri hafi yawe. Iki ni ikibazo cyihutirwa, ntutinde.

Ibintu ugomba kwitondera cyane cyane mu gihe ukoresha uyu muti:

Iki gice ni ingenzi cyane. Ugomba kwitondera ibi bintu mu gihe cyose ukoresha uyu muti.

Indwara ikomeye ya ubwivumbure

Ingaruka zikomeye kandi zikomeye z'uyu muti ni uko ushobora kugira allergie ikomeye, cyangwa mu buryo bw'ubuvuzi, anaphylaxis. Iki ni ikibazo gishyira ubuzima mu kaga.

Kubera iyo mpamvu, muganga wawe akunze kukwandikira inshinge zidasanzwe za epinephrine, inshinge zidasanzwe zishobora gukoreshwa mu gihe cy’impanuka. Ugomba kuzigumana buri gihe.

Tekereza utewe urushinge hanyuma mu gihe gito, ukagira ikibazo cyo guhumeka, isura n'iminwa bikabyimba, kandi ukumva uzunguza umutwe. Ibyo bishobora gusobanura ko ufite ubwivumbure bukomeye. Niba ibyo bibaye, ugomba guhita uterwa urwo rukingo rwa epinephrine hanyuma ukajya mu cyumba cy’ubutabazi bw’ibanze cy’ibitaro (ETU) vuba bishoboka.

Kubera iyi ngaruka, muganga wawe akunze kukubwira ko ugomba kuba uri kumwe n'umuntu mu gihe cyo guterwa urushinge ndetse n'isaha imwe nyuma yo guterwa urushinge. Ibi ni ukugira ngo niba ufite ubwivumbure bukomeye, uwo muntu agufashe kandi akujyane kwa muganga vuba.

Kwisuzumisha kwa muganga buri gihe no kugenzura indyo

• Ibizamini by'ubuvuzi: Muganga wawe azagukurikirana buri gihe mu gihe ufata uyu muti. Azagutegeka kandi gupima amaraso buri gihe (amaraso) kugira ngo arebe urugero rwa phenylalanine mu maraso yawe. Ntukabireke.
• Indyo: Wibuka igihe twavugaga ku ndyo yihariye ugomba gukurikiza kuri PKU? Mu gihe ufata uyu muti, ugomba no gukurikiza indyo yihariye wahawe. Ntugahindure iyo ari yo yose ku mirire yawe utabanje kugisha inama muganga wawe.

Ingaruka mbi z'umuti

Kimwe n'indi miti iyo ari yo yose, iyi ishobora kugira ingaruka mbi. Ntugahangayike, ariko ni ngombwa kubimenya.

Ese hari ibibazo bishobora kubaho ku yindi miti?

Yego, imiti imwe n'imwe ishobora kugira ingaruka ku rukingo. Urugero, ibintu nk'urukingo rwa medroxyprogesterone acetate, rukoreshwa mu kuboneza urubyaro cyangwa mu kuvura imisemburo.

Uru si urutonde rwuzuye. Kubwibyo, bwira muganga wawe imiti yose ufata (harimo na vitamine, imiti y'ibimera, n'inyongeramusaruro). Nanone, bwira muganga wawe niba unywa itabi cyangwa unywa inzoga.

Ni gute wabika imiti neza?

Ibi nabyo ni ingenzi cyane. Kugira ngo umuti ukomeze kuba mwiza, ugomba kubikwa neza.

• Koresha: Bika umuti muri firigo ku bushyuhe buri hagati ya dogere selisiyusi 2 na 8. Ntuzigere uwubika muri firigo.
• Ubushyuhe bw'icyumba: Niba bibaye ngombwa, uyu muti ushobora kuwubika ku bushyuhe bw'icyumba (dogere selisiyusi 20-25) kugeza ku minsi 30.
• Icy'ingenzi kurushaho: Ni ngombwa cyane kudasubiza umuti muri firigo nyuma yo kuwukura muri firigo. Niba ubitse ku bushyuhe bw'icyumba, ugomba gukoreshwa mu minsi 30. Nyuma y'iminsi 30, jugunya umuti usigaye mu buryo bwizewe.
• Ntugakoreshe umuti warengeje igihe.