Kana wava neronda diki, kubuda ropa kunomira mushure mechinguva, handiti? Izvi zvinokonzerwa nekudzivirira kunoshamisa mumuviri wedu. Asi kune vamwe vanhu, maitiro aya ekugwamba kweropa haaitike nemazvo. Kunyangwe ronda diki rinogona kukonzera kubuda ropa nguva dzose. Nhasi tiri kutaura nezve hemophilia, chirwere chinogara nhaka chinokonzera kusagwamba kweropa zvakanaka.
Ndingaziva sei kana ndine hemophilia?
Zvichitaurwa zviri nyore, miviri yedu painotanga kubuda ropa, maitiro emakemikari anotanga kuimisa. Mugumisiro weizvi kuumbwa kweropa rakagwamba (Fibrin clot). Mapuroteni akawanda akakosha muropa redu anobatsira kuumba ropa iri. Tinodaidza kuti "zvinhu zvinogwamba" kana kuti Zvinhu Zvinogwamba .
Hemophilia chirwere chinogara nhaka umo chimwe chezvinhu zvinokonzera kugonya ropa, zvikuru Factor VIII kana Factor IX, chinoshaikwa kana kuderera muhuwandu. Izvi zvinoreva kuti ropa harigwambi zvakanaka.
Kana chiremba akafungidzira kuti une hemophilia, achakupa bvunzo dzeropa dzakawanda kuti aone kuti ropa rako ragwamba zvakadii. Miedzo iyi inosanganisira:
- Muenzaniso weropa rako unotorwa, wosanganiswa nemakemikari akakosha murabhoritari, wozoongororwa kuti uone kana ropa rakagwamba, uye kana zvakadaro, kuti rinokurumidza sei kuumbwa.
- Kana bvunzo idzi dzisina kujairika, uchazoongororwa ropa rakasiyana-siyana kuti uzive huwandu hweFactor VIII neFactor IX muropa rako.
Miedzo iyi ichabatsira chiremba wako kuona kuti rudzii rwehemophilia yaunayo (A kana B) uye kuti yakanyanya sei.
Ndeipi mishonga yekurapa hemophilia?
Kune nzira dzakasiyana-siyana dzekurapa hemophilia. Rudzi rwekurapwa kwaunoda runoenderana nerudzi rwehemophilia yaunayo uye kuoma kwayo.
Semuenzaniso, kana uine hemophilia isina kunyanya kuoma, ungangoda kurapwa chete kana uine kukuvara kana paunenge uchigadzirira kuvhiyiwa. Zvisinei, kana uine hemophilia yakanyanya uye uchibuda ropa kakawanda, ungangoda kurapwa nguva nenguva kudzivirira kubuda ropa uye kudzivirira majoini ako kubva pakuremara uye kuremara.
Nzira huru dzekurapa ndeidzi dzinotevera:
| Nzira yekurapa | Tsananguro iri nyore |
|---|---|
| Kupa zvinhu zvinogwamba ropa (Factor Replacement Therapy) | Kurapa ropa risingawanikwe kana kuti risina kuzara (Factor VIII kana IX) kuburikidza netsinga (inopinzwa mutsinga) ndiyo nzira huru yekurapa. |
| Mamwe marudzi emishonga | Kupa mimwe mishonga yekubatsira kudzora kubuda ropa, kungave nezvinhu zvinokonzera kugomara kweropa kana kuti pasina. |
| Kurapa majoini anobuda ropa nezvimwe zvinetso | Kudzora kukuvara kwemajoini kunokonzerwa nekubuda ropa nguva nenguva, physiotherapy, uye kuchinja mararamiro. |
Ngatinyatsoongorora mishonga chaiyo inoshandiswa.
Vanhu vane hemophilia A vanopihwa factor VIII, uye vanhu vane hemophilia B vanopihwa factor IX. Zvinhu izvi zvinogadzirwa nenzira mbiri huru:
1. Plasma yeropa inopihwa
2. DNA yakagadzirwa ne synthetic/Recombinant
Zvinhu zvitsva zvino zvagadzirwa kuti zvigare mumuviri kwenguva yakareba, zvichireva kuti majekiseni mashoma anodiwa kupfuura kare.
| Zita remushonga uyu | Mashandisirwo uye mashandiro |
|---|---|
| Emicizumab-kxwh (HEMLIBRA) | Mushonga unopiwa kudzivirira kana kuderedza kubuda ropa muvanhu vane hemophilia A. Unoshanda nekutsiva missing factor VIII neimwe nzira. Unopiwa sejekiseni repasi pemuviri kamwe chete pasvondo. |
| Desmopressin (DDAVP) | Mushonga unopiwa vanhu vane hemophilia A isina kunyanya kuoma. Unowedzera huwandu hwe factor VIII muropa kwenguva pfupi. Unogona kupiwa netsinga, nekubaiwa jekiseni, kana semushonga wekupfapfaidza mhino. |
| Mishonga inorwisa fibrinolytic (semuenzaniso Tranexamic acid) | Iyi mishonga inogona kutorwa semapiritsi. Inoshanda nekudzivirira ropa kuti risanyungudike nekukurumidza. Mune zvimwe zviitiko, inoshandiswa pamwe chete nekurapa ne factor therapy. |
| Obizur | Iyi imhando yefactor VIII inowanikwa kubva kunguruve. Haishandiswi kurapa hemophilia inogarwa nhaka, asi kurapa chirwere chisingawanzoitiki, chinozotanga kunzi Acquired Haemophilia A. Chirwere ichi chinogona kukonzerwa nepamuviri, kenza, kana mimwe mishonga. |
Dzimwe nyaya nehutungamiriri
Tinofanirawo kutarisisa mamwe matambudziko akawanda anokonzerwa nehemophilia.
Majoini anobuda ropa
Iri ndiro dambudziko guru rehemophilia. Kana kubuda ropa kwaitika mumajoini akadai sebvi, gokora, kana chitsitsinho, zvakakosha kuwana rubatsiro rwezvinhu nekukurumidza. Kana izvi zvikasaitwa, joini rinogona kukuvara zvachose, zvichikonzera kurwadziwa, kuzvimba, uye kuoma kufamba nekufamba kwenguva. Kana kubuda ropa kwaitika, zorora woisa jira rechando mujoini sezvakarairwa nachiremba wako. Mushure mekunge kurwadziwa nekuzvimba zvapera, physiotherapy yakakosha zvikuru kuti uwanezve kufamba nesimba mujoini.
Mabasa emuviri
Kuva nehemophilia hazvirevi kuti unofanira kugara kumba nguva dzese. Zvisinei, kuchenjera kusaita mitambo inogona kukonzera kukuvara. Semuenzaniso, mitambo yakaita serugby neboxing haina kukodzera. Zvisinei, maekisesaizi akadai sekushambira, kufamba, uye kutasva bhasikoro (nenzira yakachengeteka) akanaka kwazvo kumuviri. Zvakanaka kutaura nachiremba wako nezve maekisesaizi akakodzera iwe uye ausingafaniri kuita.
Ndezvipi zvinetso zvinogona kuitika panguva yekurapwa?
Kunyange hazvo mishonga iripo yakachengeteka, pane matambudziko maviri ekuziva.
1. Zvirwere Zvinopararira Neropa: Kare, muma1970 nema1980, paiva nenjodzi huru yekutapurirana mavhairasi akaita seHIV nehepatitis kuburikidza nekurapwa neropa. Asi ikozvino hapana chikonzero chekunetseka nezvazvo.Mazuva ano, vanopa ropa vanoongororwa zvakanyanya. Ropa rese rinoongororwa mavhairasi uye rinorapwa nenzira dzakakosha kuti risashande risati rashandiswa mukurapa. Saka njodzi yacho yava shoma. Zvisinei, semunhu ane ropa rinobuda ropa, zvakakosha kuti upihwe majekiseni ekudzivirira hepatitis A neB.
2. Kuchinja kweSimba reMuviri (Inhibitors): Dzimwe nguva, immune system yemuviri wedu inokanganwa kuti protein yatinopa kubva kunze 'muvengi' uye inotanga kuirwisa. Tinoidaidza kuti kuumbwa kweinhibitors . Zvadaro kurapa kwatinoita hakushande nemazvo. Izvi zvakaoma zvishoma. Ndosaka chiremba wako achigara achiongorora ropa rako (kana remwana wako) kuti aone kana rudzi urwu rwemhinduro rukaitika.
Mharidzo Yekuenda Nayo Kumba
- Haemophilia chirwere chinogarwa nhaka chekugwamba kweropa. Mhando mbiri huru ndedzekuti haemophilia A (Factor VIII deficiency) uye haemophilia B (Factor IX deficiency).
- Chirwere ichi chinoonekwa kuburikidza nekuongororwa kweropa kwakananga.
- Kurapa kukuru ndekupa muviri chinhu chinovhara ropa chisingawanikwe kana kuti chakaderera kuburikidza netsinga.
- Kurapa kuri kushandiswa mazuva ano kwakachengeteka uye kunoshanda. Njodzi dzekare dzakanyangarika zvakanyanya.
- Kana ropa rikabuda mukati mejoini, zvakakosha kutsvaga rubatsiro rwechiremba nekukasika. Izvi zvinogona kubatsira kudzivirira kukuvara zvachose kwejoini.
- Gara uchikurukura nachiremba wako mararamiro ako uye maitiro ekurovedza muviri akakunakira. Zvakakosha kutevedzera zano rachiremba wako.
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