Ndeapi matombo aya eitsvo aunowanawo? (Cystine Stones) Ngatidzidzei nezvawo zviri nyore!

Wakambopinda muchipatara uine matombo eitsvo uye kurwadziwa kusingatsungiririki kumusana, pasi pedumbu, kana parutivi here? Kana kuti wakambonzwa nezvemumwe munhu waunoziva akambova nedambudziko rakadaro here? Matombo eitsvo chiitiko chinorwadza zvechokwadi. Matombo aya anogona kuumbwa nenzira dzakasiyana-siyana. Nhasi tichataura nezverudzi rwematombo eitsvo asingawanzoitiki, asi anogona kukonzera matambudziko kana akasarapwa nemazvo, kunyanya pakati pevechidiki, anonzi matombo ecystine .

Matombo aya e cystine chii?

Zvichitaurwa zviri nyore, matombo ecystine rudzi rwematombo eitsvo. Matombo eitsvo masumbu akaomarara anoumbwa kana makemikari akasiyana-siyana ari muweti yako aungana, sematombo madiki. Matombo ecystine anoumbwa nekemikari inonzi cystine . Iyi cystine iamino acid inowanikwa mumiviri yedu. Kazhinji, chinofanira kuitika ndechekuti iyi cystine inodzoserwa mumuviri neitsvo. Asi dzimwe nguva, kana izvi zvikasaitika zvakanaka, cystine inoungana muweti yogadzira matombo.

Matombo aya e cystine anowanzova makuru . Saka dzimwe nguva kuvhiyiwa kunodiwa kuti abviswe kudzivirira kukuvara kweitsvo kana nzira yeweti. Chinosuwisa ndechekuti, vanhu vazhinji vanowana matombo e cystine vanogona kuwana matombo aya kakawanda muhupenyu hwavo. Asi musazvidya moyo, kune nzira dzekurapa chirwere ichi pasina kuvhiyiwa. Semuenzaniso, munogona kudzora chirwere ichi nekuchinja kudya kwenyu kana kushandisa mishonga inoenzanisa pH yeweti yenyu.

Saka chii chinonzi Cystinuria?

Cystinuria chirwere chisingawanzoitiki, chinogara nhaka . Apa ndipo apo kemikari inonzi cystine inoungana muweti yako. Munhu mumwe chete pavanhu zviuru gumi vane chirwere ichi. Kana uine cystinuria, muviri wako unonetseka nekunyungudutsa cystine. Apa ndipo painoungana uye inoumba matombo ecystine. Cystinuria inogona kukonzera kuti uve nematombo eitsvo kakawanda muhupenyu hwako hwese.

Izvi zvinokonzerwa nerudzi rwejini rinonzi (autosomal recessive gene) . Izvi zvinoreva kuti kana mwana akagara nhaka jini iri kubva kuna amai nababa, mwana achava nechirwere che cystinuria. Ichi chirwere chehupenyu hwese uye hachigone kurapwa zvachose. Zvisinei, chinogona kudzorwa zvakanaka nekurapwa kwakakodzera .

Matombo eitsvo e cystine haawanzo kuwanikwa kakawanda sei?

Zvichienzaniswa nedzimwe mhando dzematombo eitsvo, matombo ecystine anowanikwa chete mu1% kusvika 2% yezviitiko. Izvozvo hazviwanzoitiki. Asi zvinoshamisa kuti, 6% kusvika 8% yematombo eitsvo muvana imatombo ecystine . Kutaura zvazviri, 80% yevanhu vanogadzira matombo ecystine vanogadzira dombo ravo rekutanga vasati vasvitsa makore makumi maviri.Zvisinei, zvinokwanisika kugadzira rimwe kana akawanda ematombo aya pazera ripi zvaro.

Ndezvipi zviratidzo zvematombo e cystine?

Zviratidzo zvematombo e cystine zvakafanana zvikuru nezvemamwe matombo eitsvo. Unotanga kunzwa zviratidzo kana dombo raumbwa.

Zvinhu zvakadai zvinogona kuitika:

• Kurwadziwa kwakanyanya kubaya parutivi rumwe rwemuviri wako (kumusana) .
• Kunzwa kurwadziwa muhudyu kana pasi pedumbu.
• Kuona ropa muweti .
• Kurutsa uye dumbu rinogumbuka (kuda kurutsa).
• Kurwadziwa pakuita weti (izvi zvinoitika kana dombo riri pedyo nedundira).

Dzimwe nguva, dombo re cystine rinogona kunamira rokonzera chirwere chemudumbu (UTI) . Nekuti matombo e cystine akakura zvishoma pane mamwe matombo, ane mukana mukuru wekukonzera matambudziko akadaro.

Sei matombo aya e cystine achiumbwa?

Sezvatakambotaura, matombo e cystine anowanzoonekwa muvanhu vane chirwere chisingawanzoitiki chinonzi cystinuria . Cystinuria inokonzerwa nekuchinja kwemajini eSLC3A1 neSLC7A9 . Chirwere ichi chinoita kuti muviri wako usakwanise kushandisa amino acid cystine nemazvo. Chinobva chaungana uye chagadzira matombo. Matombo aya anogona kugara chero kupi zvako muweti yako, senge mudundira rako kana itsvo.

Zvichitaurwa zviri nyore, dambudziko iri rinokonzerwa nemajini. Izvi zvinoreva kuti harisi mhosva yako.

Matombo e cysteine ​​​​anogadzirwa nei?

Matombo eCystine anoumbwa necystine . Sezvatakambotaura, cystine iamino acid . Amino acids rudzi rweprotein. Anobatsira muviri wedu kugadzirisa nyama, kuvaka tsandanyama, uye kurwisa hutachiona. Vanhu vane cystinuria vane matambudziko neitsvo dzavo dzinotora kana kushandisa amino acid iyi.

Ndezvipi zvinetso zvinogona kuitika nekuda kwematombo e cystine?

Cystinuria chirwere chinogara kwenguva refu. Chiremba wako anogona kukubatsira kugadzirisa dambudziko iri nemishonga, kuchinja zvekudya, uye pamwe nekuvhiyiwa. Zvisinei, une mukana wekuva nematombo ecystine muhupenyu hwako hwese. Matombo aya anogona kurwadza zvikuru paanenge achipera.

Matombo eCystine anogona kukonzera matambudziko akadai se:

• Utachiona hweitsvo .
• Kuvharika kweureter (chubhu inotakura weti kubva kuitsvo kuenda kudundira).
• Utachiona hweWeti (UTIs) .
• Kukuvara kweitsvo.

Unoziva sei kana uine matombo e cystine?

Chiremba wako achaongorora matombo e cystine nekuteerera zviratidzo zvako uye kutora nhoroondo yako yese yehutano, kusanganisira kana paine mumwe munhu mumhuri yako akambova nezvirwere izvi. Pamusoro pezvo, unogona kuita zvinotevera:

• Miedzo yekufungidzira , yakaita se ultrasound scans ne CT scans , uye bvunzo dzeweti.
• Kutumira dombo kurabhoritari kunoongororwa. Kana zvichikwanisika, tora dombo rakabuda weti yako, uye chiremba wako anogona kuritumira kurabhoritari kunoongororwa. Nenzira iyi, vanogona kuziva kuti dombo racho rakagadzirwa nemakemikari akaita sei.

Cystinuria inorapwa sei?

Chinhu chinonyanya kukosha pakurapa matombo e cystine ndechekuedza kudzivirira kuti asaumbwe pakutanga . Imwe yenzira dzakanakisisa dzekuita izvi ndeyekuderedza huwandu hwe cystine muweti yako. Chiremba wako angangoshandisa musanganiswa wemishonga nekuchinja kwekudya kuti abatsire kuderedza huwandu hwematombo aunoumba. Kana mishonga nekuchinja kwekudya zvikasamisa matombo, kana kana matombo acho akakura zvikuru, kuvhiyiwa ndeimwe sarudzo.

Mishonga

Kana chiremba wako achifunga kuti kunwa mvura yakawanda kunobatsira kuti dombo ribude roga, anogona kunyora mishonga yekurwadziwa isingatengeswi nechiremba (OTC) yekurapa marwadzo. Vanogonawo kunyora mishonga yakaita setiopronin ned-penicillamine kuti vabatsire kudzivirira kuumbwa kwematombo mune ramangwana.

Chirongwa Chekudya

Chiremba wako anogona kukukurudzira kuti uchinje maitiro ako ekudya kuti udzivise kuumbwa kwematombo. Zvimwe zvacho zvinosanganisira:

• Kunwa mvura yakawanda. Izvi zvinogona kubatsira kunyungudutsa matombo e cystine. Chiremba wako anogona kukuudza kuti unwe ma ounces 96 (anenge marita 2.8) emvura pazuva, inwa girazi remvura awa yega yega, kana kunwa mvura paunomuka husiku.
• Deredza huwandu hwemunyu (sodium) waunodya. Izvi zvinoreva kuti unofanira kurega kudya chikafu chakaomeswa nechando kana chemumagaba. Kwete munyu watinoisa mumupunga watinodya chete, asiwo kune munyu wakavanzika muzvinhu zvakaita semapickle, mapickle, masosi, chikafu chakapetwa, uye chikafu chinotengwa muchitoro. Saka unofanirawo kungwarira nezvazvo.
• Mapuroteni emhuka , zvinoreva kudya nyama shoma uye panzvimbo pezvo kudya mapuroteni anobva muzvirimwa. Semuenzaniso, unogona kuwedzera zvinhu zvakaita sechizi, nyemba, uye soya pakudya kwako pachinzvimbo chenyama nehove.

Kuvhiya

Matombo makuru anogona kukuvara kana akasapfuudzwa nenzira yeweti. Matombo aya anogona kurwadza zvikuru uye anogona kudzivirira kuyerera kweweti mumuviri. Pane nzira dzakawanda dzingashandiswa nachiremba kubvisa dombo:

• Kamera diki, inochinjika inopfuudzwa muurethra yako, kuburikidza nedundira neurethra, kuti iwane dombo uye ibvise (ureteroscopy) .
• Kuchekwa kudiki kunoitwa paganda remusana wako, pombi inopinzwa nepakati payo ichipinda muitsvo, uye dombo rinobviswa.(percutaneous nephrolithotomy).

Unoziva sei kana kurapwa kwacho kwabudirira?

Chiremba wako anogona kuraira kuti uongorore weti yako nguva nenguva kuti aone huwandu hwe cystine yako. Kuongororwa uku kuchamubatsira kuona kana chirongwa chako chekurapa chiri kushanda kana kwete.

Matombo e cystine anogona kunyungudutswa here?

Ehe, dombo re cystine rinogona kupfuudzwa. Asi rinoda kutariswa nekungwarira uye kurapwa nguva dzose . Pane kunyungudika zvachose, rinogona kuitwa diki uye nyore kupfuudzwa.

Ndezvipi zvekudya zvinobatsira ne cystinuria?

Ongororo yakaratidza kuti vanhu vane cystinuria vanogona kubatsirwa nekuchinja zvekudya. Zvimwe zvacho zvinosanganisira kunwa mvura yakawanda, kudya michero nemiriwo yakawanda, uye kudya chikafu chine munyu mushoma. Michero yeCitrus yakaita semarangi nemaremoni, miriwo yakasvibira, nemiriwo yemashizha zvakanaka zvikuru.

Matombo e cystine anogona kudzivirirwa here?

Cystinuria chirwere chinogara nhaka, saka hachigone kudzivirirwa. Zvisinei, nekutevera chirongwa chekurapa chaunopihwa nachiremba wako , unogona kudzivirira kuumbwa kwematombo ecystine . Kureva kuti, unogona kudzora kuumbwa kwematombo.

Cystinuria inotyisidzira hupenyu here?

Izvi hazviwanzo konzera njodzi kuhupenyu . Vanhu vazhinji havaiti zvirwere zvakakomba zvakaita sekutadza kushanda kweitsvo. Chinhu chakakosha kushanda nachiremba wako kuti uwane mushonga unoshanda kwauri. Vanhu vazhinji vanobvuma kurapwa zvakanaka. Zvinokwanisikawo kuwana mushonga usingakuvadzi itsvo, dundira, kana nzira yeweti.

Ndeipi tarisiro yeramangwana yematombo echisistine?

Matombo eCystine anogona kuumbwa kakawanda muhupenyu hwako. Kana uine cystinuria, uchafanira kuramba uchichinja zvekudya uye kutora mishonga yekudzivirira kuumbwa kwematombo eCystine. Chiremba wako achakutarisa uye achave nechokwadi chekuti uri kurapa zvakanaka chero matombo matsva eCystine anoumbwa. Izvi zvinoitirwa kudzivirira kukuvara kwenzira yako yeweti, itsvo, uye dundira.

Ndinofanira kuona chiremba rini?

Kana uine zviratidzo zvedombo reitsvo, iva nechokwadi chekuona chiremba . Heano mamwe ezviratidzo zvinonyanya kuzivikanwa:

• Kurwadziwa mudumbu, parutivi rwemusana, kana pahudyu.
• Kusvotwa nekurutsa.
• Kurwadziwa kana uchiita weti.

Cystinuria chirwere chinogara kwenguva refu chinoita kuti matombo ecystine aumbe. Shanda nachiremba wako kuti mugadzire hurongwa hwekurapa kudzivirira matombo kuti asaumbe. Nekuti chirwere ichi ndechemajini, vanhu vane cystinuria vangada kufunga nezvemajini ekurapa kana vachifunga nezvekutanga mhuri.Zvinogonawo kubatsira kuzviwana. Mashoko akanaka ndeekuti chirwere ichi chinogona kudzorwa nekurapwa uye hachikonzeri kutadza kushanda kweitsvo kana kukuvara kwakanyanya kwenzira yeweti.

Zvinhu zvakakosha zvekurangarira (Mharidzo Yekuenda Kumba)

Zvakanaka, ngatipfupisei zvimwe zvezvinhu zvaunofanira kurangarira kubva pane zvatataura nezvazvo:

• Matombo eCystine rudzi rwematombo eitsvo anoumbwa nekuda kwechirwere chemajini chinonzi cystinuria .
• Izvi zvinogona kuva zvakakura uye zvinogona kuitika kakawanda muhupenyu hwese.
• Zviratidzo zvinogona kusanganisira kurwadziwa kwakanyanya, ropa muweti, uye kurutsa .
• Kurapa kunosanganisira kunwa mvura yakawanda, kuderedza munyu nemapuroteni emhuka, uye, kana zvichidikanwa, mishonga nekuvhiyiwa .
• Kunyange hazvo cystinuria isingarapike zvachose, nekurapwa kwakakodzera, kuumbwa kwematombo kunogona kudzorwa uye hupenyu hwemazuva ese hunogona kuraramwa.
• Kana uine zviratidzo zvematombo muitsvo , usapedza nguva woenda kuna chiremba.

Ndapota cherechedzai kuti ruzivo urwu nderwekupa ruzivo chete uye harufanirwe kutorwa semazano ekurapa. Nguva dzose zvakanaka kubvunza chiremba kana paine chero dambudziko rehutano.

Matombo eitsvo , matombo ecystine, cystinuria, matombo emuweti, zvirwere zveitsvo, zvirwere zvemajini, hutachiona hwenzira yeweti