Chiropa chimwe chezvikamu zvakakosha mumuviri wako. Chakafanana nefekitori hombe. Chinoita basa rakawanda rakakosha, sekubvisa chepfu kubva muchikafu chatinodya, kuchengetedza simba, uye kugadzira bile, izvo zvinotibatsira kugaya chikafu. Saka, kuchengetedza fekitori iyi ichishanda zvakanaka kwakakosha zvikuru pahutano hwemuviri wedu wese. Asi dzimwe nguva kune zvirwere zvinokanganisa chiropa chinyararire, zvirwere zvatisinganzwi zvakawanda nezvazvo. Nhasi tichataura nezvechimwe chirwere chakadaro. Icho chinonzi Primary Biliary Cholangitis, kana kuti PBC sezvatinochidana muchidimbu.
Zvichitaurwa zviri nyore, chii chinonzi PBC?
Zvakanaka, ngatirambei tichiita izvi zviri nyore. Sezvandambotaura, chiropa chinoburitsa mvura inonzi bile . Izvi ndizvo zvinotibatsira kugaya mafuta ari muchikafu chatinodya, kunwa mavhitamini akati wandei, uye kubvisa cholesterol isingadiwe nehupfu mumuviri.
Fungidzira, mukati mechiropa mune network yenzira dzemudumbu, dzakaita senzira yemudumbu mudiki. Nyoka inoitwa nechiropa inofamba nemachubhu madiki aya uye inochengetwa imomo, ichibatsira kugaya chikafu kana zvichidikanwa. Chinoitika muPBC ndechekuti nzira dzemudumbu idzi dzinokuvadzwa.
Kana migero iyi yakuvara, bile haigone kuyerera zvakanaka uye inotanga kuungana mukati mechiropa. Zvakafanana nepombi yemvura yakatyoka ichizadza imba nemvura. Bile rinoungana nenzira iyi rinotanga kukuvadza masero echiropa. Kana kukuvara uku kukaitika nekufamba kwenguva, mavanga anotanga kuumbwa panzvimbo pemasero echiropa ane hutano. Tinowanzoti chirwere ichi cirrhosis . Kana chiropa chikava nemavanga nenzira iyi, kushanda kwacho kwakajairika kunenge kwava kukanganiswa zvachose.
Matanho mana echirwere chePBC
PBC hainyanyi kuipa panguva imwe chete. Inokura zvishoma nezvishoma, kuburikidza nematanho akati wandei. Kazhinji pane matanho makuru mana.
| Danho | Chii Chinoitika |
|---|---|
| Danho 1 (Danho rePortal) | Iri ndiro danho rekutanga. Chinoitika pano kuzvimba, uko kuri kuzvimba, kwakakomberedza ducts dze bile. Kuchinja uku kunotanga munzvimbo yepasuo rechiropa uko tsinga dzeropa neducts dze bile zvinobatana. |
| Danho rechipiri (Periportal Stage) | Iye zvino kuzvimba kwapararira zvishoma uye kwava kutanga kubuda mumigero yenyongo. Panguva iyi ndipo panotanga kuumbwa mavanga madiki (fibrosis). |
| Danho rechitatu (Danho reGunyana) | Pari zvino, mavanga iwayo apararira zvakanyanya, zvichiita kuti pave nekubatana pakati pezvikamu zvechiropa. Zvakafanana nedandemutande remavanga anopararira muchiropa chose. |
| Danho rechina (Biliary Cirrhosis) | Iri ndiro danho rakanyanya kuoma uye rekupedzisira rechirwere. Panguva ino, mavanga apararira muchiropa chose, zvichiita kuti chiropa chiwedzere kukora uye zvikaita mapundu. Dambudziko iri rinonzi cirrhosis. Panguva ino, mashandiro echiropa anokanganiswa zvikuru. |
Chii chinokonzera PBC chaizvo?
Iri idambudziko rine vanhu vazhinji. Kutaura zvazviri, vanachiremba havasati vawana chikonzero chaicho chePBC. Zvisinei, maonero aripo pari zvino ndeekuti chirwere chinokonzerwa ne autoimmune chinokonzerwa nekusanganiswa kwezvinhu zvemajini uye zvakatipoteredza .
Zvakanaka, chii chinonzi chirwere ichi che autoimmune?
Zvichitaurwa zviri nyore, izvi zvinokonzerwa nekusashanda zvakanaka kwemuviri wedu. Kazhinji, masero edu machena eropa (kunyanya masero eT) anorwisa utachiona hunokonzera zvirwere. Asi muPBC, masero aya ekudzivirira muviri anova asina simba uye anotanga kurwisa masero emudumbu ane hutano muchiropa. Zvakafanana neuto redu richirwisa vanhu vedu zvisizvo.
Ndipo apo masero edu anoramba achirwisa ducts dze bile nenzira iyi ndipo panotanga kukuvara kwandataura pakutanga.
Hazvigone kutaurwa kuti chirwere ichi chinopfuudzwa kubva kuchizvarwa kuenda kune chimwe kuburikidza nemajini. Kureva kuti, hapana mutemo wekuti nekuda kwekuti amai vanacho, mwanasikana wavo achachiwanawo. Zvisinei, kana mumwe munhu mumhuri, kunyanya hama yepedyo (amai, hanzvadzi, kana mukoma), aine PBC, njodzi yekuti vamwe vabatwe nechirwere ichi yakanyanya kupfuura munhuwo zvake. Saka, zvinogona kufungidzirwa kuti pane hukama hwemajini.
Ndiani ari panjodzi huru yekuva nePBC?
Kunyangwe munhu wese achigona kuva nePBC, vamwe vanhu vari panjodzi yakakura zvishoma. Ngatitarisei kuti ndivanaani.
| Chinhu Chinokonzera Njodzi | Zvimwe Zvakadzama |
|---|---|
| Murume/Mukadzi (Bonde) | Izvi zvinoshamisa. PBC inowanikwa zvakanyanya muvakadzi. Vakadzi vane mukana wekuwana chirwere ichi kanenge ka9 kusvika ka10 kupfuura varume. |
| Zera | Vanhu vazhinji vanoonekwa vaine chirwere ichi vane makore ari pakati pe30 ne60 , asi chinogonawo kuitika kuvanhu vadiki kana vakuru pane izvozvo. |
| Nhoroondo Yemhuri | Sezvandambotaura, kana mumwe munhu mumhuri yako (kunyanya amai vako kana hanzvadzi yako) aine PBC, uri panjodzi huru yekubatwa nechirwere ichi kupfuura vanhu vose. |
| Nhoroondo yeMajini | Pasi rose, chirwere ichi chinonyanya kutaurwa nevanhu vanobva kuNorthern Europe (senge Scotland nenyika dzeScandinavia). Zvisinei, chinogona kuitika munyika chero ipi zvayo uye muboka remadzinza pasi rose. |
Ndezvipi zviratidzo zvacho?
Ichi ndicho chinhu chinonyanya kukosha. Chinhu chinotyisa nezvePBC ndechekuti vanhu vazhinji havaratidzi zviratidzo pakutanga. Dzimwe nguva zvinoonekwa netsaona kana ropa raongororwa chimwe chirwere.
Asi sezvo chirwere ichi chichienderera mberi, zviratidzo zvakadai zvinogona kuoneka:
- Kuneta: Chiratidzo chikuru kunzwa kuneta zvakanyanya pasina chikonzero chakajeka, kunyangwe kana wakarara.
- Ganda Rinokwenya: Unogona kunzwa kuvaviwa kusingatsungiririki mumuviri wako wese, kunyanya pazvanza zvako nepasi.
- Maziso nemuromo zvakaoma: Kuderera kwemisodzi mumaziso nemate mumuromo, zvichikonzera kunzwa kuoma.
- Kurwadziwa kwemajoini nemapfupa.
- Kurwadziwa kudiki kana kusagadzikana kudivi rekumusoro rekurudyi redumbu.
Sezvo chirwere ichi chichienderera mberi (kusvika padanho rechirwere chetsinga), zviratidzo zvakaita sekuzvimba kwemakumbo, mvura mudumbu, uye kutsvuka kwemaziso neganda (jaundice) zvinogonawo kuitika.
Unofanira kuona chiremba rini?
Kana iwe, kunyanya kana uri mukadzi ari pakati pemakore makumi matatu nemakumi matanhatu, uchiona zviratidzo zvakaita sekuneta kunogara kwenguva refu uye ganda richikwenya pasina chikonzero chakajeka, usazviti "uri kungokura" kana kuti "kushanda zvakanyanya." Enda kuna chiremba wako nekukasika wotaura nezvazvo.
Chiremba achakuongorora uye, kana zvichidikanwa, acharaira kuongororwa ropa kakawanda. Chirwere ichi chinogona kuongororwa zviri nyore nekutarisa ma enzymes echiropa uye ma antibodies chaiwo (AMA - Antimitochondrial Antibodies). Saka usafuratira zviratidzo. Kana chikaonekwa nekukurumidza, mukana wekuti chirapwe uye chidzorwe zvakanyanya.
Mharidzo Yekuenda Nayo Kumba
- PBC chirwere chisingaperi chinokuvadza ducts diki dze bile muchiropa.
- Ichi hachisi chirwere chinotapuriranwa. Chinowanzo kukonzerwa nekutadza kuri mumasoja emuviri wedu (autoimmune).
- Pakutanga, panogona kunge pasina zviratidzo zvachose. Zviratidzo zvekutanga zvinowanzoonekwa kuneta uye ganda rinokwenya.
- Chirwere ichi chinowanzoitika kuvakadzi, kunyanya avo vane makore ari pakati pe30 ne60.
- Kana muine kusava nechokwadi kana zviratidzo nezveizvi, zviongororei (Mirai, ndizvozvo zvechiThai. Typo iri mukufunga kwangu. Ndinofanira kungwarira). Musazviongororei, asi edzai kuona chiremba ane hunyanzvi uye tsvagai mazano.

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