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Ganda remwana wako rakakwinya here? Ngatikurukurei nezvePrune Belly Syndrome

Ganda remwana wako rakakwinya here? Ngatikurukurei nezvePrune Belly Syndrome

Wakambotarisa dumbu remwana wako achangoberekwa ukaona ganda rake rakakombama, semuchero wakaomeswa here? Kana kuti rinonzwa risina simba uye risina nyama here? Zvakajairika kuti utye saamai paunoona zvinhu zvakadai. Asi izvi zvinogona kuva chiratidzo chekusakwana kwekuzvarwa kunonzi Prune Belly Syndrome. Nhasi, tichataura nezvazvo nenzira iri nyore yaunogona kunzwisisa.

Chii chinonzi Prune Belly Syndrome?

Zvichitaurwa zviri nyore, chirwere chePrune Belly Syndrome chirwere chisingawanzoitiki chinoitika pakuzvarwa. Chinonziwo Eagle-Barrett syndrome. "Prune" muchero unoita semazambiringa akaomeswa kana plum. Zita iri rinobva pakuti vana ava vane chitarisiko chakakwenyana padumbu ravo.

Chirwere ichi chine zviratidzo zvikuru zvitatu, ndosaka dzimwe nguva chichinzi "triad syndrome."

1. Kusavapo kana kuti tsandanyama dzemudumbu dzisina simba: Ichi ndicho chiratidzo chikuru chekunze. Tsandanyama dzemudumbu hadzina kukura zvakanaka, izvo zvinoita kuti ganda riri padumbu riite serakatetepa uye rakakwenya.

2. Machende asina kudzika: Chirwere ichi chinonyanya kubata vakomana. Machende avo anoramba ari mudumbu, pane kudzika mudumbu.

3. Matambudziko edundira nehurongwa hweweti zvisina kujairika: Iri ndiro dambudziko guru rechirwere ichi. Dundira rinokura zvakanyanya, zvichikonzera matambudziko makuru nehurongwa hweweti.

Matambudziko aya emushonga weti anotadzisa mwana kubvisa tsvina yese mudundira, itsvo, nemachubhu anotakura weti kubva muitsvo kuenda mudundira (ureters).

Kana mwana akazvarwa aine chirwere ichi, anogona kunge aine zvimwe zvinhu zvisina kumira zvakanaka muweti. Semuenzaniso, urethra inogona kukura zvisina kujairika, weti inogona kuungana yozadzwa, uye weti inogona kuyerera ichidzokera kumashure ichienda kuitsvo (backflow).

Chirwere chePrune Belly Syndrome chinogonawo kukonzera zvimwe zvikanganiso zvekuzvarwa nazvo. Izvi zvinosanganisira zvikanganiso mumapapu, mwoyo, ura, uye mapfupa. Kunyangwe chirwere ichi chisingawanzo kanganisa vasikana, 95% yezviitiko zvinoonekwa muvakomana.

Sei izvi zvichiitika? Ndezvipi zvikonzero?

Kutaura zvazviri, vanachiremba havasati vawana chikonzero chaicho chePrune Belly Syndrome, asi kune dzidziso dzakawanda dzinoratidza kuti ingave ndiyo inokonzera.

  • Pfungwa yekutanga:Mwana paanokura mudumbu, zvinofungidzirwa kuti pane kuvharika kwedundira kana urethra. Izvi zvinodzivirira weti kuti isabude mumuviri, zvichiita kuti dundira, ureter, neitsvo zvikure. Kana dundira rava guru zvakanyanya, kumanikidzwa kwarinoita kunodzivirira tsandanyama dzemudumbu kukura uye machende kuti asaburuke.
  • Pfungwa yechipiri: Nekuti tsandanyama dzemudumbu hadzisi kukura zvakanaka, zvinonetsa kuti mwana aite weti. Izvi zvinokonzera kuti weti izvimbe, zvichikonzera hutachiona nematambudziko.
  • Pfungwa yechitatu: Pamwe kusasimba kwetsandanyama uku nematambudziko emudumbu pamwe nehurongwa hweweti zvine chimwe chinhu chakafanana, uye panogona kunge paine chikonzero chatisingazive (semuenzaniso, dambudziko riri muhurongwa hwetsinga).

Sezvo paine mishumo yakati wandei yekuti chirwere ichi chinoitika muhama dzemumhuri imwe chete, tsvakiridzo iri kuitwawo kuti ione kana paine hukama hwemajini neizvi.

Ndezvipi zviratidzo zvechirwere ichi?

Hunhu uye kuoma kwezviratidzo zvinogona kusiyana kubva pamwana kuenda kumwana ane Prune Belly Syndrome. Zvisinei, pane zvimwe zviratidzo zvakajairika. Ona tafura iri pazasi.

Chiratidzo Tsananguro iri nyore
Dumbu rakakwinya Ganda racho rinoita serakatetepa uye rakaoma nekuda kwekushaya tsandanyama mudumbu.
Kuzvimba mudumbu rezasi Dumbu repazasi rinoita serakazvimba nekuda kwekukura kwedundira.
Kubuda kweura Chimiro cheura chinoonekwa nepaganda nekuda kwekusasimba kwemukati medumbu.
Utachiona hwemunzira weti hunowanzoitika (UTIs) Kutapurirana hutachiona hunowanzoitika nekuda kwekuita weti isina kunaka.
Kuomerwa nekugara nekufambaKutadza kudzora muviri nekuda kwekushaya simba remuviri.
Kuburitsa maburi paganda remazamu Machende evana vechirume haawanikwe mudumbu.

Pamusoro pezvo, vamwe vana vanogonawo kuva netsoka dzakakombama, chirwere chekuti tsoka inozvarwa yakatarira mukati, uye spina bifida , chirwere chekuzvarwa nacho umo tsinga dzemusana dzisingakure zvakanaka.

Ungaziva sei chirwere ichi?

Kazhinji, vanachiremba vanogona kuona chirwere ichi panguva yekuongorora ultrasound panguva yekuzvitakura kwako. Kana zvisina kudaro, zviratidzo izvi zvichaonekwa zvakajeka panguva yekuongororwa kwekutanga kwechiremba mushure mekuzvarwa kwemwana.

Chiremba wako anogona kuita bvunzo dzinoverengeka kuti asimbise chirwere chacho uye kuti chirwere chacho chakanyanya kuoma sei.

  • Ultrasound Scan: Izvi zvinobatsira kuona mamiriro eitsvo nedzimwe nhengo dzemuviri weti.
  • Kuongororwa kweX-ray: Kune mhando mbiri dzeX-ray dzinoshandisa dhayi yakakosha kuti ibayiwe mumuviri. Imwe iPyelogram yemutsinga (IVP) uye imwe iVoiding Cystourethrogram (VCUG). Izvi zvinogona kuratidza zvakajeka kuvharika nematambudziko ari muhurongwa hweweti.
  • Kuongororwa kweropa: Kuongororwa uku kunobatsira kuona kuti itsvo dzemwana wako dziri kushanda zvakanaka sei.

Ndezvipi zviri kurapwa?

Nekuti zviratidzo uye kuoma kwechirwere chePrune Belly Syndrome zvinosiyana, kune nzira dzakasiyana dzekurapa. Chiremba ndiye achasarudza kurapwa kwakakodzera zvichienderana nemamiriro emwana. Kazhinji, kuvhiyiwa kakawanda kunodiwa.

Zita rekuvhiyiwa (Izwi reChirungu) Zvichitaurwa zviri nyore, izvi zvinorevei?
Kuvhiyiwa kweVesicostomy Kaburi kadiki kanoburitswa nedumbu kachipinda mudundira, zvichiita kuti weti ipfuure zviri nyore.
OrchiopexyMachende ari mudumbu anounzwa mudumbu obva agadziriswa.
Cystoplasty Uku kuvhiyiwa kwekuvakazve kana kugadzirazve dundira.
Kuwedzera kwe detrusor Kuvhiyiwa kwekusimbisa tsandanyama dzedundira. Dzimwe nguva, kunyange chikamu chetsandanyama kubva munharaunda yehudyu chinogona kushandiswa.
Kuisirwa itsvo Muzviitiko zvakakomba, kana itsvo dzikatadza kushanda, mwana anogona kuda kuisirwa itsvo.

Remangwana remwana richava rakaita sei? (Kufungidzira)

Zvakaoma kupa mhinduro imwe chete kumubvunzo uyu, nekuti ramangwana remwana rinoenderana nekuoma kwechirwere, zera remwana, uye hutano hwake hwese.

Kune dzimwe nguva apo vamwe vana vanofira mudumbu (vakaberekwa vakafa). Vamwe vana vanogona kufa mukati memwedzi mishomanana yekuzvarwa. Iyi inyaya inonetsa zvikuru zvechokwadi.

Zvisinei, kunyangwe kana vakarapwa, vamwe vana vanogona kutadza kushanda zvakanaka kweitsvo . Kutadza kushanda zvakanaka kweitsvo kunoitika kana itsvo dzikarasikirwa ne85-90% yebasa radzo, kusvika padzisisakwanise kushanda zvakanaka. Zvadaro, tsvina nemvura yakawanda zvinoungana mumuviri, zvichiita kuti mwana arware zvikuru. Zviratidzo zvinosanganisira kuneta, kurasikirwa nechido chekudya, kuvaviwa, uye kuzvimba makumbo.

Kana itsvo dzikatadza kushanda, kurapwa kwacho ndekwe dialysis kana kuisirwa itsvo .

Chekupedzisira, kana uine kakufungira kuti mwana wako ari kuratidza chimwe chezviratidzo izvi, enda kuna chiremba nekukasika . Kuongororwa nekukurumidza uye kutanga kurapwa kwakakodzera kunogona kutungamira kumhedzisiro iri nani kumwana wako.

Mharidzo Yekuenda Nayo Kumba

  • Chirwere chePrune Belly chirwere chisingawanzoitiki chinowanzo kanganisa vana vechirume.
  • Zviratidzo zvikuru zvitatu zvechirwere ichi ganda rakakombama padumbu, tsandanyama dzisina simba, uye matambudziko enzira yeweti.
  • Kunyangwe chikonzero chaicho cheizvi chisati chawanikwa, zvinofungidzirwa kuti zvinogona kunge zvichikonzerwa nekuvharika kwenzira yeweti panguva yekuzvitakura.
  • Izvi zvinogona kuonekwa kuburikidza nekuongororwa panguva yekuzvitakura kana mushure mekuzvarwa kwemwana.
  • Kuvhiyiwa kunowanzo diwa sekurapa. Kana chirwere chacho chakanyanya, pane mukana wekuti itsvo dzishande zvisina kunaka.
  • Kana mwana wako aine chimwe chezviratidzo izvi, usanonoka wobva waona chiremba wako nekukasika . Kupindira nekukurumidza kwakakosha zvikuru.

Chirwere chePrune Belly, dumbu remwana rinokwinya, matambudziko ekuita weti yemwana, kuremara kwekuzvarwa, chirwere cheitsvo, zvirwere zvevana, chirwere cheEagle-Barrett
⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

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Ganda remwana wako rakakwinya here? Ngatikurukurei nezvePrune Belly Syndrome

Ganda remwana wako rakakwinya here? Ngatikurukurei nezvePrune Belly Syndrome

Wakambotarisa dumbu remwana wako achangoberekwa ukaona ganda rake rakakombama, semuchero wakaomeswa here? Kana kuti rinonzwa risina simba uye risina nyama here? Zvakajairika kuti utye saamai paunoona zvinhu zvakadai. Asi izvi zvinogona kuva chiratidzo chekusakwana kwekuzvarwa kunonzi Prune Belly Syndrome. Nhasi, tichataura nezvazvo nenzira iri nyore yaunogona kunzwisisa.

Chii chinonzi Prune Belly Syndrome?

Zvichitaurwa zviri nyore, chirwere chePrune Belly Syndrome chirwere chisingawanzoitiki chinoitika pakuzvarwa. Chinonziwo Eagle-Barrett syndrome. "Prune" muchero unoita semazambiringa akaomeswa kana plum. Zita iri rinobva pakuti vana ava vane chitarisiko chakakwenyana padumbu ravo.

Chirwere ichi chine zviratidzo zvikuru zvitatu, ndosaka dzimwe nguva chichinzi "triad syndrome."

1. Kusavapo kana kuti tsandanyama dzemudumbu dzisina simba: Ichi ndicho chiratidzo chikuru chekunze. Tsandanyama dzemudumbu hadzina kukura zvakanaka, izvo zvinoita kuti ganda riri padumbu riite serakatetepa uye rakakwenya.

2. Machende asina kudzika: Chirwere ichi chinonyanya kubata vakomana. Machende avo anoramba ari mudumbu, pane kudzika mudumbu.

3. Matambudziko edundira nehurongwa hweweti zvisina kujairika: Iri ndiro dambudziko guru rechirwere ichi. Dundira rinokura zvakanyanya, zvichikonzera matambudziko makuru nehurongwa hweweti.

Matambudziko aya emushonga weti anotadzisa mwana kubvisa tsvina yese mudundira, itsvo, nemachubhu anotakura weti kubva muitsvo kuenda mudundira (ureters).

Kana mwana akazvarwa aine chirwere ichi, anogona kunge aine zvimwe zvinhu zvisina kumira zvakanaka muweti. Semuenzaniso, urethra inogona kukura zvisina kujairika, weti inogona kuungana yozadzwa, uye weti inogona kuyerera ichidzokera kumashure ichienda kuitsvo (backflow).

Chirwere chePrune Belly Syndrome chinogonawo kukonzera zvimwe zvikanganiso zvekuzvarwa nazvo. Izvi zvinosanganisira zvikanganiso mumapapu, mwoyo, ura, uye mapfupa. Kunyangwe chirwere ichi chisingawanzo kanganisa vasikana, 95% yezviitiko zvinoonekwa muvakomana.

Sei izvi zvichiitika? Ndezvipi zvikonzero?

Kutaura zvazviri, vanachiremba havasati vawana chikonzero chaicho chePrune Belly Syndrome, asi kune dzidziso dzakawanda dzinoratidza kuti ingave ndiyo inokonzera.

  • Pfungwa yekutanga:Mwana paanokura mudumbu, zvinofungidzirwa kuti pane kuvharika kwedundira kana urethra. Izvi zvinodzivirira weti kuti isabude mumuviri, zvichiita kuti dundira, ureter, neitsvo zvikure. Kana dundira rava guru zvakanyanya, kumanikidzwa kwarinoita kunodzivirira tsandanyama dzemudumbu kukura uye machende kuti asaburuke.
  • Pfungwa yechipiri: Nekuti tsandanyama dzemudumbu hadzisi kukura zvakanaka, zvinonetsa kuti mwana aite weti. Izvi zvinokonzera kuti weti izvimbe, zvichikonzera hutachiona nematambudziko.
  • Pfungwa yechitatu: Pamwe kusasimba kwetsandanyama uku nematambudziko emudumbu pamwe nehurongwa hweweti zvine chimwe chinhu chakafanana, uye panogona kunge paine chikonzero chatisingazive (semuenzaniso, dambudziko riri muhurongwa hwetsinga).

Sezvo paine mishumo yakati wandei yekuti chirwere ichi chinoitika muhama dzemumhuri imwe chete, tsvakiridzo iri kuitwawo kuti ione kana paine hukama hwemajini neizvi.

Ndezvipi zviratidzo zvechirwere ichi?

Hunhu uye kuoma kwezviratidzo zvinogona kusiyana kubva pamwana kuenda kumwana ane Prune Belly Syndrome. Zvisinei, pane zvimwe zviratidzo zvakajairika. Ona tafura iri pazasi.

Chiratidzo Tsananguro iri nyore
Dumbu rakakwinya Ganda racho rinoita serakatetepa uye rakaoma nekuda kwekushaya tsandanyama mudumbu.
Kuzvimba mudumbu rezasi Dumbu repazasi rinoita serakazvimba nekuda kwekukura kwedundira.
Kubuda kweura Chimiro cheura chinoonekwa nepaganda nekuda kwekusasimba kwemukati medumbu.
Utachiona hwemunzira weti hunowanzoitika (UTIs) Kutapurirana hutachiona hunowanzoitika nekuda kwekuita weti isina kunaka.
Kuomerwa nekugara nekufambaKutadza kudzora muviri nekuda kwekushaya simba remuviri.
Kuburitsa maburi paganda remazamu Machende evana vechirume haawanikwe mudumbu.

Pamusoro pezvo, vamwe vana vanogonawo kuva netsoka dzakakombama, chirwere chekuti tsoka inozvarwa yakatarira mukati, uye spina bifida , chirwere chekuzvarwa nacho umo tsinga dzemusana dzisingakure zvakanaka.

Ungaziva sei chirwere ichi?

Kazhinji, vanachiremba vanogona kuona chirwere ichi panguva yekuongorora ultrasound panguva yekuzvitakura kwako. Kana zvisina kudaro, zviratidzo izvi zvichaonekwa zvakajeka panguva yekuongororwa kwekutanga kwechiremba mushure mekuzvarwa kwemwana.

Chiremba wako anogona kuita bvunzo dzinoverengeka kuti asimbise chirwere chacho uye kuti chirwere chacho chakanyanya kuoma sei.

  • Ultrasound Scan: Izvi zvinobatsira kuona mamiriro eitsvo nedzimwe nhengo dzemuviri weti.
  • Kuongororwa kweX-ray: Kune mhando mbiri dzeX-ray dzinoshandisa dhayi yakakosha kuti ibayiwe mumuviri. Imwe iPyelogram yemutsinga (IVP) uye imwe iVoiding Cystourethrogram (VCUG). Izvi zvinogona kuratidza zvakajeka kuvharika nematambudziko ari muhurongwa hweweti.
  • Kuongororwa kweropa: Kuongororwa uku kunobatsira kuona kuti itsvo dzemwana wako dziri kushanda zvakanaka sei.

Ndezvipi zviri kurapwa?

Nekuti zviratidzo uye kuoma kwechirwere chePrune Belly Syndrome zvinosiyana, kune nzira dzakasiyana dzekurapa. Chiremba ndiye achasarudza kurapwa kwakakodzera zvichienderana nemamiriro emwana. Kazhinji, kuvhiyiwa kakawanda kunodiwa.

Zita rekuvhiyiwa (Izwi reChirungu) Zvichitaurwa zviri nyore, izvi zvinorevei?
Kuvhiyiwa kweVesicostomy Kaburi kadiki kanoburitswa nedumbu kachipinda mudundira, zvichiita kuti weti ipfuure zviri nyore.
OrchiopexyMachende ari mudumbu anounzwa mudumbu obva agadziriswa.
Cystoplasty Uku kuvhiyiwa kwekuvakazve kana kugadzirazve dundira.
Kuwedzera kwe detrusor Kuvhiyiwa kwekusimbisa tsandanyama dzedundira. Dzimwe nguva, kunyange chikamu chetsandanyama kubva munharaunda yehudyu chinogona kushandiswa.
Kuisirwa itsvo Muzviitiko zvakakomba, kana itsvo dzikatadza kushanda, mwana anogona kuda kuisirwa itsvo.

Remangwana remwana richava rakaita sei? (Kufungidzira)

Zvakaoma kupa mhinduro imwe chete kumubvunzo uyu, nekuti ramangwana remwana rinoenderana nekuoma kwechirwere, zera remwana, uye hutano hwake hwese.

Kune dzimwe nguva apo vamwe vana vanofira mudumbu (vakaberekwa vakafa). Vamwe vana vanogona kufa mukati memwedzi mishomanana yekuzvarwa. Iyi inyaya inonetsa zvikuru zvechokwadi.

Zvisinei, kunyangwe kana vakarapwa, vamwe vana vanogona kutadza kushanda zvakanaka kweitsvo . Kutadza kushanda zvakanaka kweitsvo kunoitika kana itsvo dzikarasikirwa ne85-90% yebasa radzo, kusvika padzisisakwanise kushanda zvakanaka. Zvadaro, tsvina nemvura yakawanda zvinoungana mumuviri, zvichiita kuti mwana arware zvikuru. Zviratidzo zvinosanganisira kuneta, kurasikirwa nechido chekudya, kuvaviwa, uye kuzvimba makumbo.

Kana itsvo dzikatadza kushanda, kurapwa kwacho ndekwe dialysis kana kuisirwa itsvo .

Chekupedzisira, kana uine kakufungira kuti mwana wako ari kuratidza chimwe chezviratidzo izvi, enda kuna chiremba nekukasika . Kuongororwa nekukurumidza uye kutanga kurapwa kwakakodzera kunogona kutungamira kumhedzisiro iri nani kumwana wako.

Mharidzo Yekuenda Nayo Kumba

  • Chirwere chePrune Belly chirwere chisingawanzoitiki chinowanzo kanganisa vana vechirume.
  • Zviratidzo zvikuru zvitatu zvechirwere ichi ganda rakakombama padumbu, tsandanyama dzisina simba, uye matambudziko enzira yeweti.
  • Kunyangwe chikonzero chaicho cheizvi chisati chawanikwa, zvinofungidzirwa kuti zvinogona kunge zvichikonzerwa nekuvharika kwenzira yeweti panguva yekuzvitakura.
  • Izvi zvinogona kuonekwa kuburikidza nekuongororwa panguva yekuzvitakura kana mushure mekuzvarwa kwemwana.
  • Kuvhiyiwa kunowanzo diwa sekurapa. Kana chirwere chacho chakanyanya, pane mukana wekuti itsvo dzishande zvisina kunaka.
  • Kana mwana wako aine chimwe chezviratidzo izvi, usanonoka wobva waona chiremba wako nekukasika . Kupindira nekukurumidza kwakakosha zvikuru.

Chirwere chePrune Belly, dumbu remwana rinokwinya, matambudziko ekuita weti yemwana, kuremara kwekuzvarwa, chirwere cheitsvo, zvirwere zvevana, chirwere cheEagle-Barrett
⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

💬 Comments (0)

Hapana zvakataurwa parizvino. Isa mhinduro yako pano kekutanga.

Wedzera zvaunofunga

Ndokumbira uverenge: 5 + 7 =