Skip to main content

Mwana wako mudiki ane kukwenya kusinganzwisisike here? (West Syndrome) Ngatikurukurei nezvazvo!

Mwana wako mudiki ane kukwenya kusinganzwisisike here? (West Syndrome) Ngatikurukurei nezvazvo!

Wakamboona mwana wako achingoerekana asvetuka-svetuka, sekunge arohwa nemheni here? Maoko ake nemakumbo zvinongoerekana zvapetana, kana kuti anozvikanda kumashure. Kunyangwe izvi zvikaitika kwemasekonzi mashoma chete, kana zvikaitika kakawanda zvakateerana, zvinogona kutyisa mubereki wese anozviona. Tiri kuzotaura nezvechirwere chinotyisa kudaro, asi zvakakosha kuti chizivikanwe nekukurumidza. Ndiyo West Syndrome.

Zvichitaurwa zviri nyore, chii chinonzi West Syndrome?

West Syndrome chirwere chisingawanzoitiki chinobata vana vadiki, kunyanya vari pasi pegore rimwe chete . Chinonzi zita rachiremba akatanga kuchiwana.

Izvi zvine mazita akati wandei pakati pevanachiremba. Unogona kunzwa zita rekuti `Infantile Spasms (IS)`. Izvi zvinoreva ``baby spasms.'' Inonziwo `Epileptic Spasms.'' Kunyange zvazvo paine mazita akawanda, ese anotaura nezvechirwere chimwe chete.

Ndezvipi zviratidzo zvechirwere ichi?

Chinhu chikuru cheizvi kusvetuka-svetuka kwatakataura nezvako kare. Izvi zvinonzi `kusvetuka-svetuka`. Kusvetuka-svetuka uku kune hunhu hwakasiyana-siyana:

  • Mabatiro anoita dumbu: Mwana anongoerekana akotama mberi (sepaanenge achirwadziwa nemudumbu) kana kuti anodzokera shure. Maoko nemakumbo zvinongoerekana zvaoma uye zvichigwinha.
  • Nguva: Kurova kamwe chete kunongotora masekondi mashoma chete.
  • Maboka: Maboka aya haauye kamwe chete uye haamire. Anouya nenzira inoenderera mberi, yakaungana . Kubatana kumwe kunoteverwa nerimwe, uye rimwezve, uye rimwezve, kusvika pa150 muboka. Kune vacheche vane maboka akadaro anosvika makumi matanhatu pazuva.
  • Nguva: Unogona kuona mafambiro aya mwana paanongomuka kubva kuhope.

Kuwedzera kune kudedera uku, zvimwe zviratidzo zvinogona kuonekwa.

Chiratidzo Tsananguro
Kugara uchichema/kutsamwa (Crankiness) Mwana anogara achichema pasina chikonzero uye zvakaoma kumunyaradza.
Kurasikirwa nechido chekudya Deredza kana kuramba kunwa mukaka.
Kuchinja kwehope Kurara zvishoma husiku, kurara zvakanyanya masikati.
Kumira kwekukura kana kudzokera shure Uhu hunhu hunokosha zvikuru. Mwana, uyo aimboita zvinhu zvakaita sekuseka, kutamba, uye kuziva amai vake, anorega zvishoma nezvishoma kuita zvinhu izvozvo. Anokanganwa zvinhu zvaakadzidza kare.

Sei izvi zvichiitika kuvana vacheche?

Chirwere cheWest Syndrome chirwere chisingawanzoitiki. Chinobata vana vanosvika 6 pavana 10,000. Chinowanzobata vana vari pakati pemwedzi mina nesere. Kunyange hazvo chikonzero chaicho chisingazivikanwi nguva dzose, zvikonzero zvikuru zvakawanda zvakawanikwa.

  • Matambudziko europi: Chero zvikanganiso zvinoitika panguva yekukura kana kuumbwa kweuropi.
  • Kuchinja kwemajini: Dambudziko iri rinogona kukonzerwa nekuchinja kwemajini emwana.
  • Kukuvara kwehuropi: Kunokonzerwa nekushaikwa kweokisijeni kuuropi panguva yekuzvarwa kana pane imwe nguva, senge tsaona.
  • Matambudziko emetabolism: Nekuda kwemamwe matambudziko nemaitiro emakemikari emuviri.
  • Utachiona hwehuropi: Matambudziko ehutachiona anokanganisa uropi.
  • Tuberous Sclerosis Complex: Chirwere chemajini umo bundu risiri rekenza rinokura mumuviri nemuuropi.

Kuongororwa kwechirwere kunoitwa sei?

Kana ukaona mwana wako achibatwa nechirwere chakadai, unofanira kuona chiremba wevana nekukurumidza .

Zvakakosha: Usati waenda kunoona chiremba wako, zvinobatsira zvikuru kana ukakwanisa kutora vhidhiyo yekurwadziwa kwemwana wako. Izvi zvinogona kutorwa se colic, saka zvinobatsira zvikuru kuti chiremba aone vhidhiyo iyi kuti abatsire kuona chirwere chacho.

Chiremba anonyanya kutaura nezvemiedzo iyi:

  • EEG (Electroencephalogram): Iyi ndiyo bvunzo inonyanya kukosha. Muchidimbu, inonyora mashandiro emagetsi muuropi sepattern. Mwana ane West Syndrome acharatidza pattern isina kujairika inonzi `Hypsarrhythmia` paEEG. Ichi ndicho chiratidzo chikuru chechirwere ichi.
  • MRI kana CT scan:Kuongororwa uku kunobatsira kuona kana paine matambudziko, kukuvara, kana kusarongeka muchimiro cheuropi.
  • Kuongororwa kweropa, weti, uye cerebrospinal fluid (CSF): Kuongororwa uku kunobatsira kuona kana chikonzero chekudedera kwacho chiri dambudziko remajini kana kuti remetabolism.

Ndezvipi zvinorapwa izvi?

Zvakakosha zvikuru kutanga kurapwa nekukurumidza mushure mekunge West Syndrome yaonekwa, nekuti kudzora pfari kunobatsira kuderedza kukuvara kwehuropi hwemwana.

Mishonga

Mushonga unonyanya kushandiswa pakurapa izvi.

  • ACTH: Iyi ihormone. Inopihwa sejekiseni. Inoshanda zvikuru mukudzora kurova kwemoyo.
  • Vigabatrin (Sabril): Uyu mushonga wekurapa pfari zvakare. Unoshanda zvakanyanya kuvana vane West Syndrome, chirwere chinokonzerwa neTuberous Sclerosis.
  • MaSteroids: MaSteroids akaita se'Prednisone' anoshandiswawo.

Mishonga iyi inogona kuva nemigumisiro yakadai sekudzikira kwemasoja emuviri, kuwedzera kweBP, uye matambudziko ekuona. Saka, chiremba anogara achiongorora mwana uye achimurapa zvichienderana nezvakanakira nenjodzi.

Kudya kweKetogenic

Kune vamwe vacheche, kana mishonga isingakwani kudzora manyoka avo, chiremba anogona kukurudzira kudya uku kwakakosha. Uku kudya kune mafuta akawanda uye kusina makabhohaidhiretsi akawanda .

Yambiro: Usamboedza kuita izvi uri kumba wega. Izvi zvinowanzo tangwa muchipatara, uchibatsirwa nachiremba uye nyanzvi yezvekudya/yezvekudya.

Kuvhiya

Kana MRI scan ikaratidza pachena kuti sitiroko yacho inokonzerwa negomarara rakati muuropi, chiremba anogona kukurudzira kubviswa kwenzvimbo iyoyo nekuvhiyiwa. Izvi hazvisi zvinhu zvinogona kuitwa nemunhu wese. Zvinosarudzwa nechikwata chekurapa.

Chii chaungati nezveramangwana? (Outlook)

Kunyange zvazvo mubvunzo uyu wakaoma kubvunza, zvakakosha kuziva chokwadi. Remangwana reWest Syndrome richasarudzwa nezvinhu zvakakosha zvakawanda.

  • Chikonzero: Chii chinokonzera pfari? Kana yakakonzerwa nekukuvara kwakanyanya kweuropi, mhedzisiro yacho inogona kunge isina kunaka. Kana yakakonzerwa pasina chikonzero chakajeka (idiopathic), mhedzisiro yacho yakanaka.
  • Nguva yekutanga kurapwa: Kana kurapwa kukatangwa mukati memwedzi mumwe chete mushure mekuongororwa, kukura kwemwana kunogona kudzokera kune zvakajairika.
  • Mhinduro yekurapwa: Kukurumidza kudzorwa kwepfari.

Kunyemwerera uku kunowanzo pera pazera remakore mana. Zvisinei,Vana vazhinji vanogona kuzova nemamwe marudzi epfari gare gare.

Vana vazhinji vane matambudziko ekudzidza kana kukura kwepfungwa. Zvisinei, nekurapwa kwakanakisa kuripo pakutanga, vanenge 20%-25% yevacheche vanogona kurarama hupenyu hwakajairika nehungwaru hwakajairika. Saka, kutora matanho nekukurumidza kwakakosha.

Mharidzo Yekuenda Nayo Kumba

  • Kana ukaona mwana wako achikwenya kamwe kamwe (kunyanya pakati pemwedzi 3-12), usazviregeredza.
  • Kana zvichibvira, tora vhidhiyo yekurwadziwa kwedumbu. Izvi zvichabatsira chiremba zvikuru.
  • Enda kuna chiremba wevana nekukasika. Kutambisa nguva kunogona kuwedzera kukuvara kwehuropi hwemwana.
  • West Syndrome chirwere chinorapika. Kurapwa nekukurumidza kunogona kudzora chirwere ichi uye kupa mwana mukana wakanakisisa wekukura mune ramangwana.
  • Rwendo urwu rwakaoma. Asi hausi wega. Taura nachiremba wako nguva dzose uwane rutsigiro rwaunoda.

West Syndrome, kurwadziwa kwevana vacheche, pfari, kurwadziwa kwevana, EEG, vana, zvirwere zveuropi
⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

💬 Comments (0)

Hapana zvakataurwa parizvino. Isa mhinduro yako pano kekutanga.

Wedzera zvaunofunga

Ndokumbira uverenge: 7 + 6 =
Mwana wako mudiki ane kukwenya kusinganzwisisike here? (West Syndrome) Ngatikurukurei nezvazvo!

Mwana wako mudiki ane kukwenya kusinganzwisisike here? (West Syndrome) Ngatikurukurei nezvazvo!

Wakamboona mwana wako achingoerekana asvetuka-svetuka, sekunge arohwa nemheni here? Maoko ake nemakumbo zvinongoerekana zvapetana, kana kuti anozvikanda kumashure. Kunyangwe izvi zvikaitika kwemasekonzi mashoma chete, kana zvikaitika kakawanda zvakateerana, zvinogona kutyisa mubereki wese anozviona. Tiri kuzotaura nezvechirwere chinotyisa kudaro, asi zvakakosha kuti chizivikanwe nekukurumidza. Ndiyo West Syndrome.

Zvichitaurwa zviri nyore, chii chinonzi West Syndrome?

West Syndrome chirwere chisingawanzoitiki chinobata vana vadiki, kunyanya vari pasi pegore rimwe chete . Chinonzi zita rachiremba akatanga kuchiwana.

Izvi zvine mazita akati wandei pakati pevanachiremba. Unogona kunzwa zita rekuti `Infantile Spasms (IS)`. Izvi zvinoreva ``baby spasms.'' Inonziwo `Epileptic Spasms.'' Kunyange zvazvo paine mazita akawanda, ese anotaura nezvechirwere chimwe chete.

Ndezvipi zviratidzo zvechirwere ichi?

Chinhu chikuru cheizvi kusvetuka-svetuka kwatakataura nezvako kare. Izvi zvinonzi `kusvetuka-svetuka`. Kusvetuka-svetuka uku kune hunhu hwakasiyana-siyana:

  • Mabatiro anoita dumbu: Mwana anongoerekana akotama mberi (sepaanenge achirwadziwa nemudumbu) kana kuti anodzokera shure. Maoko nemakumbo zvinongoerekana zvaoma uye zvichigwinha.
  • Nguva: Kurova kamwe chete kunongotora masekondi mashoma chete.
  • Maboka: Maboka aya haauye kamwe chete uye haamire. Anouya nenzira inoenderera mberi, yakaungana . Kubatana kumwe kunoteverwa nerimwe, uye rimwezve, uye rimwezve, kusvika pa150 muboka. Kune vacheche vane maboka akadaro anosvika makumi matanhatu pazuva.
  • Nguva: Unogona kuona mafambiro aya mwana paanongomuka kubva kuhope.

Kuwedzera kune kudedera uku, zvimwe zviratidzo zvinogona kuonekwa.

Chiratidzo Tsananguro
Kugara uchichema/kutsamwa (Crankiness) Mwana anogara achichema pasina chikonzero uye zvakaoma kumunyaradza.
Kurasikirwa nechido chekudya Deredza kana kuramba kunwa mukaka.
Kuchinja kwehope Kurara zvishoma husiku, kurara zvakanyanya masikati.
Kumira kwekukura kana kudzokera shure Uhu hunhu hunokosha zvikuru. Mwana, uyo aimboita zvinhu zvakaita sekuseka, kutamba, uye kuziva amai vake, anorega zvishoma nezvishoma kuita zvinhu izvozvo. Anokanganwa zvinhu zvaakadzidza kare.

Sei izvi zvichiitika kuvana vacheche?

Chirwere cheWest Syndrome chirwere chisingawanzoitiki. Chinobata vana vanosvika 6 pavana 10,000. Chinowanzobata vana vari pakati pemwedzi mina nesere. Kunyange hazvo chikonzero chaicho chisingazivikanwi nguva dzose, zvikonzero zvikuru zvakawanda zvakawanikwa.

  • Matambudziko europi: Chero zvikanganiso zvinoitika panguva yekukura kana kuumbwa kweuropi.
  • Kuchinja kwemajini: Dambudziko iri rinogona kukonzerwa nekuchinja kwemajini emwana.
  • Kukuvara kwehuropi: Kunokonzerwa nekushaikwa kweokisijeni kuuropi panguva yekuzvarwa kana pane imwe nguva, senge tsaona.
  • Matambudziko emetabolism: Nekuda kwemamwe matambudziko nemaitiro emakemikari emuviri.
  • Utachiona hwehuropi: Matambudziko ehutachiona anokanganisa uropi.
  • Tuberous Sclerosis Complex: Chirwere chemajini umo bundu risiri rekenza rinokura mumuviri nemuuropi.

Kuongororwa kwechirwere kunoitwa sei?

Kana ukaona mwana wako achibatwa nechirwere chakadai, unofanira kuona chiremba wevana nekukurumidza .

Zvakakosha: Usati waenda kunoona chiremba wako, zvinobatsira zvikuru kana ukakwanisa kutora vhidhiyo yekurwadziwa kwemwana wako. Izvi zvinogona kutorwa se colic, saka zvinobatsira zvikuru kuti chiremba aone vhidhiyo iyi kuti abatsire kuona chirwere chacho.

Chiremba anonyanya kutaura nezvemiedzo iyi:

  • EEG (Electroencephalogram): Iyi ndiyo bvunzo inonyanya kukosha. Muchidimbu, inonyora mashandiro emagetsi muuropi sepattern. Mwana ane West Syndrome acharatidza pattern isina kujairika inonzi `Hypsarrhythmia` paEEG. Ichi ndicho chiratidzo chikuru chechirwere ichi.
  • MRI kana CT scan:Kuongororwa uku kunobatsira kuona kana paine matambudziko, kukuvara, kana kusarongeka muchimiro cheuropi.
  • Kuongororwa kweropa, weti, uye cerebrospinal fluid (CSF): Kuongororwa uku kunobatsira kuona kana chikonzero chekudedera kwacho chiri dambudziko remajini kana kuti remetabolism.

Ndezvipi zvinorapwa izvi?

Zvakakosha zvikuru kutanga kurapwa nekukurumidza mushure mekunge West Syndrome yaonekwa, nekuti kudzora pfari kunobatsira kuderedza kukuvara kwehuropi hwemwana.

Mishonga

Mushonga unonyanya kushandiswa pakurapa izvi.

  • ACTH: Iyi ihormone. Inopihwa sejekiseni. Inoshanda zvikuru mukudzora kurova kwemoyo.
  • Vigabatrin (Sabril): Uyu mushonga wekurapa pfari zvakare. Unoshanda zvakanyanya kuvana vane West Syndrome, chirwere chinokonzerwa neTuberous Sclerosis.
  • MaSteroids: MaSteroids akaita se'Prednisone' anoshandiswawo.

Mishonga iyi inogona kuva nemigumisiro yakadai sekudzikira kwemasoja emuviri, kuwedzera kweBP, uye matambudziko ekuona. Saka, chiremba anogara achiongorora mwana uye achimurapa zvichienderana nezvakanakira nenjodzi.

Kudya kweKetogenic

Kune vamwe vacheche, kana mishonga isingakwani kudzora manyoka avo, chiremba anogona kukurudzira kudya uku kwakakosha. Uku kudya kune mafuta akawanda uye kusina makabhohaidhiretsi akawanda .

Yambiro: Usamboedza kuita izvi uri kumba wega. Izvi zvinowanzo tangwa muchipatara, uchibatsirwa nachiremba uye nyanzvi yezvekudya/yezvekudya.

Kuvhiya

Kana MRI scan ikaratidza pachena kuti sitiroko yacho inokonzerwa negomarara rakati muuropi, chiremba anogona kukurudzira kubviswa kwenzvimbo iyoyo nekuvhiyiwa. Izvi hazvisi zvinhu zvinogona kuitwa nemunhu wese. Zvinosarudzwa nechikwata chekurapa.

Chii chaungati nezveramangwana? (Outlook)

Kunyange zvazvo mubvunzo uyu wakaoma kubvunza, zvakakosha kuziva chokwadi. Remangwana reWest Syndrome richasarudzwa nezvinhu zvakakosha zvakawanda.

  • Chikonzero: Chii chinokonzera pfari? Kana yakakonzerwa nekukuvara kwakanyanya kweuropi, mhedzisiro yacho inogona kunge isina kunaka. Kana yakakonzerwa pasina chikonzero chakajeka (idiopathic), mhedzisiro yacho yakanaka.
  • Nguva yekutanga kurapwa: Kana kurapwa kukatangwa mukati memwedzi mumwe chete mushure mekuongororwa, kukura kwemwana kunogona kudzokera kune zvakajairika.
  • Mhinduro yekurapwa: Kukurumidza kudzorwa kwepfari.

Kunyemwerera uku kunowanzo pera pazera remakore mana. Zvisinei,Vana vazhinji vanogona kuzova nemamwe marudzi epfari gare gare.

Vana vazhinji vane matambudziko ekudzidza kana kukura kwepfungwa. Zvisinei, nekurapwa kwakanakisa kuripo pakutanga, vanenge 20%-25% yevacheche vanogona kurarama hupenyu hwakajairika nehungwaru hwakajairika. Saka, kutora matanho nekukurumidza kwakakosha.

Mharidzo Yekuenda Nayo Kumba

  • Kana ukaona mwana wako achikwenya kamwe kamwe (kunyanya pakati pemwedzi 3-12), usazviregeredza.
  • Kana zvichibvira, tora vhidhiyo yekurwadziwa kwedumbu. Izvi zvichabatsira chiremba zvikuru.
  • Enda kuna chiremba wevana nekukasika. Kutambisa nguva kunogona kuwedzera kukuvara kwehuropi hwemwana.
  • West Syndrome chirwere chinorapika. Kurapwa nekukurumidza kunogona kudzora chirwere ichi uye kupa mwana mukana wakanakisisa wekukura mune ramangwana.
  • Rwendo urwu rwakaoma. Asi hausi wega. Taura nachiremba wako nguva dzose uwane rutsigiro rwaunoda.

West Syndrome, kurwadziwa kwevana vacheche, pfari, kurwadziwa kwevana, EEG, vana, zvirwere zveuropi
⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

💬 Comments (0)

Hapana zvakataurwa parizvino. Isa mhinduro yako pano kekutanga.

Wedzera zvaunofunga

Ndokumbira uverenge: 7 + 6 =