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Yintoni iLennox-Gastaut Syndrome (LGS)? Makhe sithethe ngayo!

Yintoni iLennox-Gastaut Syndrome (LGS)? Makhe sithethe ngayo!

Ngaba umntwana wakho unesifo sokuxhuzula rhoqo? Ngaba unezinguqu ezinkulu ekufundeni nasekuziphatheni? Ukuba kunjalo, into endizakuyithetha inokuba ibaluleke kakhulu kuwe. Namhlanje siza kuthetha ngeLennox -Gastaut Syndrome , okanye (LGS) ngamafutshane, isifo sokuxhuzula esinzima nesinzima ukunyanga. Oku kunokuqala ebuntwaneni. Kodwa ungakhathazeki, amayeza amatsha kunye nonyango ngoku luyafumaneka.

Yintoni kanye kanye iLennox-Gastaut syndrome (LGS)? Ngubani oyifumanayo?

Ngamafutshane, i-LGS luhlobo olubi lwesifo sokuwa oluqala ebuntwaneni, ngesiqhelo ngaphambi kokuba sibe neminyaka eli-10, ngakumbi phakathi kweminyaka emi-3 nemi-5. Sixhaphake kancinci kubafana. Nangona kunjalo, asiyongxaki ixhaphakileyo. Sichaphazela malunga nomntu omnye ukuya kwabababini kwisigidi. Malunga ne-1% ukuya kwi-2% yazo zonke izigulana zesifo sokuwa zine-LGS.

Oku kuyichaphazela njani imizimba yethu?

Isifo sokuwa sisifo apho imiqondiso yombane yengqondo, okanye ulwazi, ludluliselwa phakathi kweeseli. (LGS) luhlobo olubi kakhulu lwesifo sokuwa. Kukho izizathu ezahlukeneyo:

  • Kwi-LGS, kukho iintlobo ezingaphezu kwesinye zokuxhuzula. Ezinye zezi ntlobo zokuxhuzula zinokubangela ukwenzakala okukhulu emntwaneni.
  • Ezi zixhuzula zingonakalisa ingqondo ngokwayo. Abantwana abane-LGS banokuba nomonakalo omkhulu engqondweni, ubunzima bokufunda, kunye nokulibaziseka kokukhula. Oku kuthetha ukuba umntwana unokulahlekelwa okanye alibale izinto asele ezifundile, ezifana nokuhamba nokuthetha. Le yimeko ebuhlungu kakhulu.
  • (LGS) idla ngokuxhathisa kakhulu kunyango. Oku kuthetha ukuba kunzima ukuyilawula ngamayeza. Amayeza lunyango lokuqala, kodwa kudla ngokunikezelwa iintlobo ezininzi zamayeza ngaxeshanye. Nokuba anikwa, amayeza ewodwa awakwazi ukuyiphelisa ngokupheleleyo i-seizures.

Zithini iimpawu ze (LGS)?

Umntwana one-LGS unokubonakalisa iimpawu ezahlukeneyo. Ezinye zazo ziyabonakala kubomi bemihla ngemihla nakwimisebenzi yakhe, ngelixa ezinye zibonakala kuphela ngexesha lokuxhuzula.

Iingxaki zokufunda nokuziphatha

Kuqhelekile ukuba abantwana abane-LGS babe neengxaki zokufunda kunye neengxaki zokuziphatha . Ezi zinokuvela kungekudala emva kokuba ziqalile ukuxhuzula, kwaye zinokuba mandundu njengoko ukuxhuzula kuqhubeka. Ezi ngxaki zokufunda kunye nengqondo zihlala zihlala zihleli, oko kuthetha ukuba zinokuqhubeka zize zibe ngabantu abadala.

Abantwana abane-LGS banengxaki yokufunda, ukwenza abahlobo, kunye nokunxibelelana nabanye. Basenokuba nobunzima bokulawula iimvakalelo zabo. Abanye abantwana banokubonisa iimpawu ezifana nezo zabantwana abane-Autism Spectrum Disorder .

Isigaba sokubanjwa

Ukuxhuzula ngokuqhelekileyo kunokwenzeka ngamanqanaba amathathu:

1. I-Prodrome okanye i-aura: Le yinto abanye abantu abayifumanayo ngaphambi kokuba baxhuzule, nangona ingabi njalo. Oku kungaba yimvakalelo engathandekiyo kancinci. Utshintsho embonweni, utshintsho kwezinye iimvakalelo, okanye utshintsho kwimo okanye kwindlela yokuziphatha lunokwenzeka ngeli xesha.

2. Ukuxhuzula: Kulapho kuvela khona ukuxhuzula. Oku kunokwahluka ngokuxhomekeke kuhlobo lokuxhuzula (siza kuxoxa ngeentlobo ezahlukeneyo zokuxhuzula ngezantsi).

3. Ukuchacha emva kokuba umntu ebanjwe sisifo: Eli lixesha emva kokuba umntu ephelile ukubanjwa sisifo. Eli lixesha apho umntu ebuyela engqondweni ngokupheleleyo.

Iintlobo zokuxhuzula ezibonwa kwi-LGS

Kukho iintlobo ezininzi eziphambili ze-seizures ezibonwa kwi-LGS. Ezona ntlobo zixhaphakileyo ze-seizures kunye nemiphumo yazo zezi zilandelayo:

  • Ukuxhuzula kweAtonic:
  • Ukulahlekelwa kulawulo lwemisipha/ukutyhafa: Oku kukwabizwa ngokuba "luhlaselo lokuwa" kuba kubandakanya ukulahlekelwa kulawulo ngequbuliso nokuwa phantsi, njengopopi oneentambo eziphukileyo. Oku kuyingozi kakhulu kuba umntwana akanalawulo xa ewa kwaye unokubandezeleka kakhulu, nokuba yingozi ebomini, ukwenzakala entloko, entanyeni, esifubeni nasemqolo.
  • Ukulahlekelwa yingqondo okuncinci: Oku kuxhuzula kusenokungabangeli ukulahlekelwa yingqondo ngokupheleleyo.
  • Ixesha elifutshane: Ezi zixhuzula zihlala ixesha elifutshane kakhulu, njengemizuzwana embalwa.
  • Ukuxhuzula kweTonic:
  • Ukuqina/ukuqandisa umzimba wonke: Kulapho zonke izihlunu zomzimba ziqhawuka ngequbuliso, nto leyo eyenza umzimba uqine ngokupheleleyo ngokungathi ujike waba lilitye.
  • Indlela ekhethekileyo yokuma: Xa besemhlabeni, imilenze namagxa abo esemhlabeni, umqolo wabo unokugoba. Iingalo zinokwandiswa ngaphezu kweentloko zabo, okanye iingalo zinokolulwa kwaye iingqiniba zijonge emacaleni, kwaye amanqindi anokuba kufutshane nezinqe.
  • Izihlandlo ezininzi zenzeka xa ulele: Ezi zihlandlo ezininzi zenzeka xa ulele. Kodwa zinokwenzeka nasemini. Ukuba oku kwenzeka xa umntwana evukile, kukho umngcipheko wokwenzakala kuba umntwana angawa.
  • Ubude obufutshane: Oku kukwathatha imizuzwana embalwa ukuya kumzuzu omnye.
  • Ukuxhuzula okungaqhelekanga kokungabikho:
  • Amehlo avuleka aze ajonge ngaphandle kwesizathu: Kule ngxaki, ingqondo iyalahleka, kodwa amehlo ahlala evulekile. Ke ngoko, oku kunokuphambukiswa njengokuphupha emini, ukungakwazi ukugxila, kunye nokuziva ngathi awukho kwindawo efanelekileyo.
  • Iintshukumo eziphindaphindayo: Ngexesha lokuxhuzula, unokubona iintshukumo zamehlo nomlomo. Kunokubakho neentshukumo zezandla.
  • Ubude obufutshane: Oku akudluli kwimizuzwana embalwa.

Kubalulekile: Abantwana abane-LGS banokuba nokuxhuzula "kwii-clusters," oko kuthetha ukuba ukuxhuzula okuninzi kwenzeka ngexesha elifutshane. Ngaphezulu kwesibini kwisithathu sabantwanaKuvela imeko ebizwa ngokuba yi "Status Epilepticus" . Le yimeko efuna unyango olungxamisekileyo!

Yintoni iStatus Epilepticus?

Oku kuthetha enye yezinto ezimbini:

  • Ukuxhuzula kube kanye, okuhlala ixesha elide phakathi kwemizuzu emi-5 ukuya kwengama-30.
  • Ukuxhuzula okungaphezulu kwesinye kwimizuzu engama-30, kwaye umntu akabuyi engqondweni ngokupheleleyo ngexesha lokuxhuzula.

I-status epilepticus yimeko engxamisekileyo yezonyango. Iyingozi kakhulu kuba inokubangela umonakalo ongunaphakade engqondweni kwanokufa.

Ezinye iimpawu kunye neentlobo zokuxhuzula ezinxulumene nazo

  • Ukuxhuzula kwe-Tonic-clonic: Ukuxhuzula kwe-Tonic-clonic (eyayisakuba yi-"grand mal") kuqala ngendlela efanayo nokuxhuzula kwe-tonic, kodwa kunesigaba esongezelelweyo. Isigaba se-clonic kuxa umzimba ushukuma, uphawu oluqhelekileyo lokuxhuzula, luvela. Ukuxhuzula kwe-Tonic kunye ne-tonic-clonic kudla ngokuthatha malunga nemizuzu emibini.
  • Iintshukumo ezikhawulezayo nezimfutshane nezixhaphakileyo: Ukuxhuzula kwe-Myoclonic ziintshukumo ezixhaphakileyo nezixhaphakileyo. Zihlala imizuzwana embalwa kuphela, kodwa ngamanye amaxesha zinokuhlala ixesha elide. Abantu abangenazo iintshukumo banokuba nezi ntlobo "zeentshukumo ze-myoclonic." Umzekelo, zinokubangela ii-hiccups okanye zivuke ngequbuliso ebuthongweni.
  • Iimpawu zokuva, zengqondo, okanye ezinye iimpawu: Ukuxhuzula okungaphelelanga okanye okujoliswe kuko kuchaphazela kuphela inxalenye ethile yomzimba.

Zithini izizathu ze-LGS?

Kukho izizathu ezininzi ezinokubangela iLennox-Gastaut syndrome. Ezinye zezizathu zikhona ngaphambi kokuba umntwana azalwe. Ezinye zibangelwa ziziganeko ezenzeka ebuntwaneni. Kwicala lesine lamatyala e-``(LGS)``, akukho sizathu sicacileyo sinokuchongwa.

Nazi ezinye zezizathu ezichongiweyo:

  • Iingxaki zophuhliso lobuchopho ngaphambi kokuzalwa.
  • Ukulimala kakhulu entloko (ukulimala kwengqondo okanye ukuxhuzula ingqondo).
  • Iintsholongwane ezonakalisa ingqondo, ezifana ne-meningitis okanye i-encephalitis.
  • Izifo ze-metabolic ezizuzwe njengelifa, umzekelo `(Izifo ze-Mitochondrial)`.
  • Ukonakala kwengqondo okubangelwa kukungabikho komoya-mpilo ngaphambi okanye ngexesha lokuzalwa (i-cerebral hypoxia).
  • Isifo se-Tuberous sclerosis.
  • Iithumba zobuchopho.
  • I-West syndrome (le yenye uhlobo lwesifo sokuwa, esinokuthi kamva sibe yi-LGS).

Abaphandi bafumanise ukuba "i-de novo mutations" ixhaphakile kubantu abane-LGS.Igama elithi De novo lithetha "ukususela ekuqaleni." Ezi ziziphene kwi-`(DNA)` yomntu ezenzeka ngequbuliso, ngokungacwangciswanga. Oko kukuthi, utshintsho lubangelwa sisiphene kwi-`(DNA)` yesidoda okanye iqanda elivelise umntu, kodwa asisiphene kwi-`(DNA)` yomzali ngamnye.

Nangona kunjalo, kunokubakho impembelelo yemfuza kwesi sifo. Malunga nama-30% abantu abane-LGS banembali yentsapho yesifo sokuwa. Nangona kunjalo, kufuneka uphando oluthe kratya ukuze kuchongwe ukuba esi sifo sibangelwa yintoni na.

Ingaba oku kuyasulela?

Hayi, i-Lennox-Gastaut syndrome ayosuleli. Ayisasazeki ukusuka komnye umntu ukuya komnye. Nangona kunjalo, ezinye izifo ezisulelayo zinokubangela umonakalo engqondweni kwaye zibangele "LGS". Nangona kunjalo, ayinguye wonke umntu onezo zifo oza kuba "LGS".

Ifunyanwa njani iLennox-Gastaut syndrome (LGS)?

Kudla ngokwenziwa uvavanyo oluninzi ukuze kufunyaniswe i-LGS, kwaye ugqirha uya kwenza uvavanyo lwe-neurological. Ugqirha wezingane unokurhanela ukuba le meko isekelwe kwinto ethethwa ngabazali malunga neempawu zomntwana wabo, ingakumbi ukuba umntwana unengxaki yokufunda okanye yokuziphatha.

Zeziphi iimvavanyo ezenziwayo ukufumanisa oku?

Iimvavanyo ezisetyenziswa kakhulu zezi:

  • I-Electroencephalogram (EEG): Oku kuquka ukubeka ii-electrodes ezininzi entlokweni ngejeli yokuhambisa umbane ukulinganisa umsebenzi wombane wengqondo. I-EEG ibalulekile ekuchongeni i-LGS kuba ibonisa ipatheni yombane eyahlukileyo kumaza obuchopho.
  • I-Magnetic Resonance Imaging (MRI): Le mifanekiso isebenzisa imagnethi enamandla kunye nekhompyutha ukuthatha imifanekiso ecacileyo yangaphakathi lomzimba, ingakumbi ingqondo. Oku kunceda kakhulu ekufumaneni iingxaki zophuhliso lobuchopho.
  • Uvavanyo lwelebhu: Olu vavanyo lujonga igazi nomchamo ukuze lubone ukuba kukho ezinye izizathu ezinokubangela ukuxhuzula. Lujonga izinto ezifana nekhemistri yegazi, ii-enzymes zesibindi, kunye nokusebenza kwezintso. Nangona olu vavanyo lungenako ukuxilonga ngokuqinisekileyo i-LGS, lunokunceda ekuthinteleni ezinye iimeko ezinokufana ne-LGS.
  • Uvavanyo lwe-genetic: Oku kunokunceda ekuqinisekiseni ukuba kukho iimeko ezizuzwe njengelifa ezinokubangela i-LGS, okanye ukuba kukho utshintsho oluzenzekelayo.

Ukongeza, kunokwenziwa olunye uvavanyo ukuze kuthintelwe iimeko ezifanayo. Ugqirha wakho uza kukuxelela okungakumbi ngale nto.

Inganyangwa njani le nto? Ngaba inganyangeka?

Kukho iindlela ezahlukeneyo zonyango lwe-LGS. Nangona kunjalo, le meko inzima kakhulu ukuyinyanga. Kwiimeko ezininzi, olunye okanye indibaniselwano yezi ndlela zonyango ingasetyenziswa:

  • Amayeza
  • Unyango lokutya
  • Utyando lobuchopho okanye izixhobo ezifakelweyo

Amayeza

I-Lennox-Gastaut syndrome idla ngokuxhathisa kakhulu amayeza. Yiyo loo nto kunzima ukuyilawula. Kwiimeko ezininzi, kufuneka amayeza amaninzi. Enye into ebangela ubunzima kukuba amanye amayeza okuthintela ukuxhuzula, alawula ezinye iintlobo zokuxhuzula, anokunyusa ukuxhaphaka kwezinye iintlobo zokuxhuzula.

Xa imeko ingavumi kunyango, oogqirha banokuzama ukuthintela iintlobo ezithile zokuxhuzula okanye ukunciphisa ukuxhaphaka kwazo. Umzekelo, ukuxhuzula okubangelwa yi-atonic kubaluleke kakhulu ukuthintela, njengoko kunxulunyaniswa nomngcipheko omkhulu wokwenzakala ngenxa yokuwa.

Unyango lokutya

Kwabaninzi abantu abanesifo sokuwa esinzima, utshintsho kwindlela yokutya lunokunceda ekunciphiseni ukuxhaphaka kokuwa okanye ukukuyekisa ngokupheleleyo. Ukutya okune-ketogenic kwisifo sokuwa – ukutya okuneproteni eninzi kunye namafutha kunye ne-carbohydrate ephantsi – kudla ngokucetyiswa ngoogqirha. Kungaba lukhetho olufanelekileyo xa amayeza engasebenzanga.

Nangona ukutya kwe-ketogenic kunyango oludumileyo lwesifo sokuwa esinzima, kuneengxaki ezimbalwa. Olu hlobo lokutya lusebenza kuphela ukuba ululandela ngokuchanekileyo. Oku kungenxa yokuba ukutya iicarbohydrate ezininzi, ezifana neswekile kunye nokutya okunesitatshi, kunokubangela ukuxhuzula. Nangona kunjalo, ezinye iindlela zokutya ezilungisiweyo nazo zinokunceda. Ukuba unomdla, ugqirha wakho unokukunceda uzame enye yezi ndlela zokutya.

Utyando lobuchopho kunye nezixhobo ezifakelweyo

Kwezinye iimeko, ingakumbi xa ezinye iindlela zonyango zingasebenzanga, utyando lolona khetho lungcono. Nazi ezinye iintlobo zotyando:

  • Ukukhuthazwa kweNerve yeVagus (VNS): Oku kuquka ukufaka isixhobo emzimbeni esihambisa umbane ophantsi kwi-nerve ye-10th cranial, i-vagus nerve - edibene ngqo nengqondo. Lo mbane unokunciphisa ukuxhaphaka kunye nobunzima bokuxhuzula. Ngokuhamba kwexesha, iziphumo zawo ziyanda. Oku kuthetha ukuba ukuxhuzula okuncinci kunye nokuxhuzula okuncinci kakhulu. Ukufakelwa esi sixhobo yinkqubo eguqukayo, enemingcipheko ephantsi kunye nexesha elifutshane lokuchacha, ngoko ke kudla ngokuqwalaselwa ngaphambi kotyando olukhulu.
  • I-Corpus callosotomy: I-corpus callosum yinxalenye yengqondo esebenza njengebhulorho phakathi kwe-hemispheres yasekhohlo neyasekunene. Xa i-corpus callosum inqunyulwe, imiqondiso engaqhelekanga ebangela ukuxhuzula ayisayi kuphinda ibuyele umva. Oku kunokunciphisa ukuxhaphaka kokuxhuzula, okanye kumise ukuxhuzula okunzima, okuphazamisa ngokupheleleyo.
  • I-Hemispherectomy `(I-Hemispherectomy)`:Oku kuquka ukususwa kwelinye icala lobuchopho ngotyando. Nangona oku kunokubonakala kugqithisile, iingcali zingakusebenzisa ukunqanda ukuxhuzula okungalawulekiyo. Kamva, unyango lomzimba lunokunceda ingqondo ukuba ilungele utshintsho. Ingqondo iyazilungisa, kwaye inxalenye eseleyo ithatha imisebenzi yenxalenye esusiweyo.
  • Ukususwa kwesisu: Ukungasebenzi kakuhle kwesakhiwo sengqondo ngamanye amaxesha kunokubangela i-LGS. Ukuba oogqirha banokufumanisa ukuba oku kungaqhelekanga, banokukwazi ukususa izicubu zengqondo ezonakeleyo okanye ezigulayo baze bayeke ukuxhuzula. Nangona kunjalo, kuba kwi-LGS, umsebenzi wokuxhuzula ukwiindawo ezingaphezu kwesinye zobuchopho, oku akusoloko kuyindlela ephumelelayo kwi-LGS.

Iingxaki/iziphumo ebezingalindelekanga zonyango

Iingxaki zonyango zixhomekeke kunyango ngalunye. Ke ngoko, kungcono ukuthetha nogqirha wakho malunga neengxaki kunye nemiphumo emibi yonyango olufumana wena okanye umntwana wakho. Ugqirha angakunika ulwazi olufanelekileyo kwimeko yakho, iimeko zakho, kunye nezinye iimeko zonyango.

Ndiza kuziva bhetele nini emva konyango? Kuza kuthatha ixesha elingakanani ukuze ndiphile?

Ixesha lokuchacha emva konyango liyahluka kakhulu ngokuxhomekeke kwiindlela zonyango ezisetyenzisiweyo kunye nemeko yakho iyonke. Ugqirha wakho ngumntu ofanelekileyo ukukuxelela into omawuyilindele kunye nexesha eliza kuthatha ukuchacha.

Ngaba i-Lennox-Gastaut syndrome (LGS) ingathintelwa?

Kwiimeko ezininzi, i-LGS ayisiyongxaki inokuthintelwa. Kwaye nomngcipheko wokuyifumana awunakuncitshiswa. Okukodwa kukuthintela ukwenzakala entloko nasengqondweni okunokubangelwa yi-LGS. Eyona ndlela yokuthintela le meko kukuba abantwana bakho banxibe izigcina-ntloko ezivunyiweyo neziqinisekisiweyo.

Yintoni endimele ndiyilindele ukuba mna okanye umntwana wam sinale meko?

Isifo sikaLennox-Gastaut sisifo esidla ngokuba nemiphumo emibi kakhulu. Abantwana abaninzi abanale meko bakhula nokukhubazeka kokufunda kunye nokonakala kwengqondo okuhlala kuhleli okuthintela amandla abo engqondo. Kwakhona, kuba ukuxhuzula (ukuhlaselwa ngamaconsi) kuxhaphakile, kwaye kudla ngokukhokelela ekuweni, abantwana abanale meko basengozini enkulu yokwenzakala.

Le meko ikwanzima ukuyinyanga. Abantwana abaninzi abanayo bafuna ukhathalelo olukhethekileyo ubomi babo bonke kuba abakwazi ukuzinyamekela. Nangona kunjalo, abanye abantu abanale meko banomonakalo omncinci engqondweni, nto leyo ethetha ukuba banokuphila ngokuzimela.

Ihlala ixesha elingakanani (LGS)?

Ngaphandle kokuba unyango lunikwe ukunqanda ngokupheleleyo ukuxhuzula (okungaqhelekanga kakhulu), i-LGS yimeko ehlala ubomi bonke.

Iyintoni ikamva lale meko?

Eyona mingcipheko mikhulu yesifo seLennox-Gastaut kukulimala kwengqondo ngenxa yokuxhuzula okungalawulekiyo, okanye ukuwa okubangelwa kukuxhuzula. Ngenxa yezo mingcipheko, izinga lokufa kwabantu abane-"LGS" kwiminyaka eli-10 emva kokufunyaniswa kwesi sifo liphakathi kwe-3% ne-7%.

Kwezinye iimeko, iinkqubo zonyango zinokumisa ukuxhuzula okubangelwa yi-LGS. Oku kuyayimisa le meko, kodwa akunakulungisa umonakalo engqondweni obangelwe kukuxhuzula kwangaphambili.

Ndingazinyamekela njani? / Ndingamnyamekela njani umntwana wam?

Ukuba wena okanye umntu omthandayo une-LGS, kubaluleke kakhulu ukulandela imiyalelo kagqirha wakho ngokuchanekileyo. Oku kuquka:

  • Ukuthatha amayeza njengoko kuchaziwe.
  • Ukuya kugqirha njengoko kucetyisiwe.
  • Ukubeka esweni ukuxhuzula kunye nokuphepha izinto ezinokubangela ukuxhuzula okanye iimeko ezinokubangela ukuxhuzula.

Ndifanele ndimbone nini ugqirha?

Ugqirha wakho okanye womntwana wakho uza kukuxelela ukuba uze kutyelelo olulandelayo xa kufuneka. Kufuneka ubone ugqirha wakho ukuba iimpawu zakho zokuxhuzula zitshintsha kakhulu okanye ukuba zichaphazela indlela oqhele ukwenza ngayo imihla ngemihla kunye nemisebenzi yakho.

Ndingaya nini kwiYunithi yoNyango oluNgxamisekileyo (i-ETU) ?

Ukuba wena okanye umntwana wakho unesithuthwane okanye isithuthwane esiphindaphindeneyo esihlangabezana neemfuno zengxamiseko yezonyango ebizwa ngokuba yi-status epilepticus , kufuneka uye kwigumbi likaxakeka kwisibhedlele esikufutshane nawe. Oku kuthetha ukuba kwezi meko zilandelayo:

  • Ukuba ukuxhuzula kube kanye kuthatha imizuzu emi-5 ukuya kwengama-30.
  • Ukuba umntu uxhuzula kabini okanye ngaphezulu kwimizuzu engama-30 aze angabuyi engqondweni ngokupheleleyo ngexesha lokuxhuzula.

Umyalezo Wokuya Ekhaya

I-Lennox-Gastaut syndrome (LGS) luhlobo olubi kakhulu lwesifo sokuwa esiqala kwangethuba. Sidla ngokuba nefuthe elinzulu, ngamanye amaxesha ubomi bonke bomntwana. Nangona kunzima ukunyanga, amayeza amatsha, utyando, kunye nonyango lunokunceda ukunciphisa ubunzima besifo kunye nokunciphisa ukusasazeka kwaso. Amaxesha amaninzi, unyango lunokunyanga ngokupheleleyo esi sifo. Nangona kunjalo, uphando oluthe kratya luyadingeka ukuze kuqinisekiswe ukuba esi sifo sinokunyangwa okanye sinyangwe na. Ukuba umntwana wakho unezinye zezi mpawu, kungcono ukubona ugqirha ngokukhawuleza.


Isifo sikaLennox -Gastaut, i-LGS, isifo sokuwa, ukuxhuzula, abantwana, iingxaki zobuchopho, izifo zemithambo-luvo

Frequently Asked Questions (FAQ)

Yintoni iStatus Epilepticus?

Oku kuthetha enye yezinto ezimbini:

Zeziphi iimvavanyo ezenziwayo ukufumanisa oku?

Iimvavanyo ezisetyenziswa kakhulu zezi:

Iyintoni ikamva lale meko?

Eyona mingcipheko mikhulu yesifo seLennox-Gastaut kukulimala kwengqondo ngenxa yokuxhuzula okungalawulekiyo, okanye ukuwa okubangelwa kukuxhuzula. Ngenxa yezo mingcipheko, izinga lokufa kwabantu abane-"LGS" kwiminyaka eli-10 emva kokufunyaniswa kwesi sifo liphakathi kwe-3% ne-7%.

⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

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Yintoni iLennox-Gastaut Syndrome (LGS)? Makhe sithethe ngayo!
Izifo kunye neemekoJulayi 16, 2026

Yintoni iLennox-Gastaut Syndrome (LGS)? Makhe sithethe ngayo!

Ngaba umntwana wakho unesifo sokuxhuzula rhoqo? Ngaba unezinguqu ezinkulu ekufundeni nasekuziphatheni? Ukuba kunjalo, into endizakuyithetha inokuba ibaluleke kakhulu kuwe. Namhlanje siza kuthetha ngeLennox -Gastaut Syndrome , okanye (LGS) ngamafutshane, isifo sokuxhuzula esinzima nesinzima ukunyanga. Oku kunokuqala ebuntwaneni. Kodwa ungakhathazeki, amayeza amatsha kunye nonyango ngoku luyafumaneka.

Yintoni kanye kanye iLennox-Gastaut syndrome (LGS)? Ngubani oyifumanayo?

Ngamafutshane, i-LGS luhlobo olubi lwesifo sokuwa oluqala ebuntwaneni, ngesiqhelo ngaphambi kokuba sibe neminyaka eli-10, ngakumbi phakathi kweminyaka emi-3 nemi-5. Sixhaphake kancinci kubafana. Nangona kunjalo, asiyongxaki ixhaphakileyo. Sichaphazela malunga nomntu omnye ukuya kwabababini kwisigidi. Malunga ne-1% ukuya kwi-2% yazo zonke izigulana zesifo sokuwa zine-LGS.

Oku kuyichaphazela njani imizimba yethu?

Isifo sokuwa sisifo apho imiqondiso yombane yengqondo, okanye ulwazi, ludluliselwa phakathi kweeseli. (LGS) luhlobo olubi kakhulu lwesifo sokuwa. Kukho izizathu ezahlukeneyo:

  • Kwi-LGS, kukho iintlobo ezingaphezu kwesinye zokuxhuzula. Ezinye zezi ntlobo zokuxhuzula zinokubangela ukwenzakala okukhulu emntwaneni.
  • Ezi zixhuzula zingonakalisa ingqondo ngokwayo. Abantwana abane-LGS banokuba nomonakalo omkhulu engqondweni, ubunzima bokufunda, kunye nokulibaziseka kokukhula. Oku kuthetha ukuba umntwana unokulahlekelwa okanye alibale izinto asele ezifundile, ezifana nokuhamba nokuthetha. Le yimeko ebuhlungu kakhulu.
  • (LGS) idla ngokuxhathisa kakhulu kunyango. Oku kuthetha ukuba kunzima ukuyilawula ngamayeza. Amayeza lunyango lokuqala, kodwa kudla ngokunikezelwa iintlobo ezininzi zamayeza ngaxeshanye. Nokuba anikwa, amayeza ewodwa awakwazi ukuyiphelisa ngokupheleleyo i-seizures.

Zithini iimpawu ze (LGS)?

Umntwana one-LGS unokubonakalisa iimpawu ezahlukeneyo. Ezinye zazo ziyabonakala kubomi bemihla ngemihla nakwimisebenzi yakhe, ngelixa ezinye zibonakala kuphela ngexesha lokuxhuzula.

Iingxaki zokufunda nokuziphatha

Kuqhelekile ukuba abantwana abane-LGS babe neengxaki zokufunda kunye neengxaki zokuziphatha . Ezi zinokuvela kungekudala emva kokuba ziqalile ukuxhuzula, kwaye zinokuba mandundu njengoko ukuxhuzula kuqhubeka. Ezi ngxaki zokufunda kunye nengqondo zihlala zihlala zihleli, oko kuthetha ukuba zinokuqhubeka zize zibe ngabantu abadala.

Abantwana abane-LGS banengxaki yokufunda, ukwenza abahlobo, kunye nokunxibelelana nabanye. Basenokuba nobunzima bokulawula iimvakalelo zabo. Abanye abantwana banokubonisa iimpawu ezifana nezo zabantwana abane-Autism Spectrum Disorder .

Isigaba sokubanjwa

Ukuxhuzula ngokuqhelekileyo kunokwenzeka ngamanqanaba amathathu:

1. I-Prodrome okanye i-aura: Le yinto abanye abantu abayifumanayo ngaphambi kokuba baxhuzule, nangona ingabi njalo. Oku kungaba yimvakalelo engathandekiyo kancinci. Utshintsho embonweni, utshintsho kwezinye iimvakalelo, okanye utshintsho kwimo okanye kwindlela yokuziphatha lunokwenzeka ngeli xesha.

2. Ukuxhuzula: Kulapho kuvela khona ukuxhuzula. Oku kunokwahluka ngokuxhomekeke kuhlobo lokuxhuzula (siza kuxoxa ngeentlobo ezahlukeneyo zokuxhuzula ngezantsi).

3. Ukuchacha emva kokuba umntu ebanjwe sisifo: Eli lixesha emva kokuba umntu ephelile ukubanjwa sisifo. Eli lixesha apho umntu ebuyela engqondweni ngokupheleleyo.

Iintlobo zokuxhuzula ezibonwa kwi-LGS

Kukho iintlobo ezininzi eziphambili ze-seizures ezibonwa kwi-LGS. Ezona ntlobo zixhaphakileyo ze-seizures kunye nemiphumo yazo zezi zilandelayo:

  • Ukuxhuzula kweAtonic:
  • Ukulahlekelwa kulawulo lwemisipha/ukutyhafa: Oku kukwabizwa ngokuba "luhlaselo lokuwa" kuba kubandakanya ukulahlekelwa kulawulo ngequbuliso nokuwa phantsi, njengopopi oneentambo eziphukileyo. Oku kuyingozi kakhulu kuba umntwana akanalawulo xa ewa kwaye unokubandezeleka kakhulu, nokuba yingozi ebomini, ukwenzakala entloko, entanyeni, esifubeni nasemqolo.
  • Ukulahlekelwa yingqondo okuncinci: Oku kuxhuzula kusenokungabangeli ukulahlekelwa yingqondo ngokupheleleyo.
  • Ixesha elifutshane: Ezi zixhuzula zihlala ixesha elifutshane kakhulu, njengemizuzwana embalwa.
  • Ukuxhuzula kweTonic:
  • Ukuqina/ukuqandisa umzimba wonke: Kulapho zonke izihlunu zomzimba ziqhawuka ngequbuliso, nto leyo eyenza umzimba uqine ngokupheleleyo ngokungathi ujike waba lilitye.
  • Indlela ekhethekileyo yokuma: Xa besemhlabeni, imilenze namagxa abo esemhlabeni, umqolo wabo unokugoba. Iingalo zinokwandiswa ngaphezu kweentloko zabo, okanye iingalo zinokolulwa kwaye iingqiniba zijonge emacaleni, kwaye amanqindi anokuba kufutshane nezinqe.
  • Izihlandlo ezininzi zenzeka xa ulele: Ezi zihlandlo ezininzi zenzeka xa ulele. Kodwa zinokwenzeka nasemini. Ukuba oku kwenzeka xa umntwana evukile, kukho umngcipheko wokwenzakala kuba umntwana angawa.
  • Ubude obufutshane: Oku kukwathatha imizuzwana embalwa ukuya kumzuzu omnye.
  • Ukuxhuzula okungaqhelekanga kokungabikho:
  • Amehlo avuleka aze ajonge ngaphandle kwesizathu: Kule ngxaki, ingqondo iyalahleka, kodwa amehlo ahlala evulekile. Ke ngoko, oku kunokuphambukiswa njengokuphupha emini, ukungakwazi ukugxila, kunye nokuziva ngathi awukho kwindawo efanelekileyo.
  • Iintshukumo eziphindaphindayo: Ngexesha lokuxhuzula, unokubona iintshukumo zamehlo nomlomo. Kunokubakho neentshukumo zezandla.
  • Ubude obufutshane: Oku akudluli kwimizuzwana embalwa.

Kubalulekile: Abantwana abane-LGS banokuba nokuxhuzula "kwii-clusters," oko kuthetha ukuba ukuxhuzula okuninzi kwenzeka ngexesha elifutshane. Ngaphezulu kwesibini kwisithathu sabantwanaKuvela imeko ebizwa ngokuba yi "Status Epilepticus" . Le yimeko efuna unyango olungxamisekileyo!

Yintoni iStatus Epilepticus?

Oku kuthetha enye yezinto ezimbini:

  • Ukuxhuzula kube kanye, okuhlala ixesha elide phakathi kwemizuzu emi-5 ukuya kwengama-30.
  • Ukuxhuzula okungaphezulu kwesinye kwimizuzu engama-30, kwaye umntu akabuyi engqondweni ngokupheleleyo ngexesha lokuxhuzula.

I-status epilepticus yimeko engxamisekileyo yezonyango. Iyingozi kakhulu kuba inokubangela umonakalo ongunaphakade engqondweni kwanokufa.

Ezinye iimpawu kunye neentlobo zokuxhuzula ezinxulumene nazo

  • Ukuxhuzula kwe-Tonic-clonic: Ukuxhuzula kwe-Tonic-clonic (eyayisakuba yi-"grand mal") kuqala ngendlela efanayo nokuxhuzula kwe-tonic, kodwa kunesigaba esongezelelweyo. Isigaba se-clonic kuxa umzimba ushukuma, uphawu oluqhelekileyo lokuxhuzula, luvela. Ukuxhuzula kwe-Tonic kunye ne-tonic-clonic kudla ngokuthatha malunga nemizuzu emibini.
  • Iintshukumo ezikhawulezayo nezimfutshane nezixhaphakileyo: Ukuxhuzula kwe-Myoclonic ziintshukumo ezixhaphakileyo nezixhaphakileyo. Zihlala imizuzwana embalwa kuphela, kodwa ngamanye amaxesha zinokuhlala ixesha elide. Abantu abangenazo iintshukumo banokuba nezi ntlobo "zeentshukumo ze-myoclonic." Umzekelo, zinokubangela ii-hiccups okanye zivuke ngequbuliso ebuthongweni.
  • Iimpawu zokuva, zengqondo, okanye ezinye iimpawu: Ukuxhuzula okungaphelelanga okanye okujoliswe kuko kuchaphazela kuphela inxalenye ethile yomzimba.

Zithini izizathu ze-LGS?

Kukho izizathu ezininzi ezinokubangela iLennox-Gastaut syndrome. Ezinye zezizathu zikhona ngaphambi kokuba umntwana azalwe. Ezinye zibangelwa ziziganeko ezenzeka ebuntwaneni. Kwicala lesine lamatyala e-``(LGS)``, akukho sizathu sicacileyo sinokuchongwa.

Nazi ezinye zezizathu ezichongiweyo:

  • Iingxaki zophuhliso lobuchopho ngaphambi kokuzalwa.
  • Ukulimala kakhulu entloko (ukulimala kwengqondo okanye ukuxhuzula ingqondo).
  • Iintsholongwane ezonakalisa ingqondo, ezifana ne-meningitis okanye i-encephalitis.
  • Izifo ze-metabolic ezizuzwe njengelifa, umzekelo `(Izifo ze-Mitochondrial)`.
  • Ukonakala kwengqondo okubangelwa kukungabikho komoya-mpilo ngaphambi okanye ngexesha lokuzalwa (i-cerebral hypoxia).
  • Isifo se-Tuberous sclerosis.
  • Iithumba zobuchopho.
  • I-West syndrome (le yenye uhlobo lwesifo sokuwa, esinokuthi kamva sibe yi-LGS).

Abaphandi bafumanise ukuba "i-de novo mutations" ixhaphakile kubantu abane-LGS.Igama elithi De novo lithetha "ukususela ekuqaleni." Ezi ziziphene kwi-`(DNA)` yomntu ezenzeka ngequbuliso, ngokungacwangciswanga. Oko kukuthi, utshintsho lubangelwa sisiphene kwi-`(DNA)` yesidoda okanye iqanda elivelise umntu, kodwa asisiphene kwi-`(DNA)` yomzali ngamnye.

Nangona kunjalo, kunokubakho impembelelo yemfuza kwesi sifo. Malunga nama-30% abantu abane-LGS banembali yentsapho yesifo sokuwa. Nangona kunjalo, kufuneka uphando oluthe kratya ukuze kuchongwe ukuba esi sifo sibangelwa yintoni na.

Ingaba oku kuyasulela?

Hayi, i-Lennox-Gastaut syndrome ayosuleli. Ayisasazeki ukusuka komnye umntu ukuya komnye. Nangona kunjalo, ezinye izifo ezisulelayo zinokubangela umonakalo engqondweni kwaye zibangele "LGS". Nangona kunjalo, ayinguye wonke umntu onezo zifo oza kuba "LGS".

Ifunyanwa njani iLennox-Gastaut syndrome (LGS)?

Kudla ngokwenziwa uvavanyo oluninzi ukuze kufunyaniswe i-LGS, kwaye ugqirha uya kwenza uvavanyo lwe-neurological. Ugqirha wezingane unokurhanela ukuba le meko isekelwe kwinto ethethwa ngabazali malunga neempawu zomntwana wabo, ingakumbi ukuba umntwana unengxaki yokufunda okanye yokuziphatha.

Zeziphi iimvavanyo ezenziwayo ukufumanisa oku?

Iimvavanyo ezisetyenziswa kakhulu zezi:

  • I-Electroencephalogram (EEG): Oku kuquka ukubeka ii-electrodes ezininzi entlokweni ngejeli yokuhambisa umbane ukulinganisa umsebenzi wombane wengqondo. I-EEG ibalulekile ekuchongeni i-LGS kuba ibonisa ipatheni yombane eyahlukileyo kumaza obuchopho.
  • I-Magnetic Resonance Imaging (MRI): Le mifanekiso isebenzisa imagnethi enamandla kunye nekhompyutha ukuthatha imifanekiso ecacileyo yangaphakathi lomzimba, ingakumbi ingqondo. Oku kunceda kakhulu ekufumaneni iingxaki zophuhliso lobuchopho.
  • Uvavanyo lwelebhu: Olu vavanyo lujonga igazi nomchamo ukuze lubone ukuba kukho ezinye izizathu ezinokubangela ukuxhuzula. Lujonga izinto ezifana nekhemistri yegazi, ii-enzymes zesibindi, kunye nokusebenza kwezintso. Nangona olu vavanyo lungenako ukuxilonga ngokuqinisekileyo i-LGS, lunokunceda ekuthinteleni ezinye iimeko ezinokufana ne-LGS.
  • Uvavanyo lwe-genetic: Oku kunokunceda ekuqinisekiseni ukuba kukho iimeko ezizuzwe njengelifa ezinokubangela i-LGS, okanye ukuba kukho utshintsho oluzenzekelayo.

Ukongeza, kunokwenziwa olunye uvavanyo ukuze kuthintelwe iimeko ezifanayo. Ugqirha wakho uza kukuxelela okungakumbi ngale nto.

Inganyangwa njani le nto? Ngaba inganyangeka?

Kukho iindlela ezahlukeneyo zonyango lwe-LGS. Nangona kunjalo, le meko inzima kakhulu ukuyinyanga. Kwiimeko ezininzi, olunye okanye indibaniselwano yezi ndlela zonyango ingasetyenziswa:

  • Amayeza
  • Unyango lokutya
  • Utyando lobuchopho okanye izixhobo ezifakelweyo

Amayeza

I-Lennox-Gastaut syndrome idla ngokuxhathisa kakhulu amayeza. Yiyo loo nto kunzima ukuyilawula. Kwiimeko ezininzi, kufuneka amayeza amaninzi. Enye into ebangela ubunzima kukuba amanye amayeza okuthintela ukuxhuzula, alawula ezinye iintlobo zokuxhuzula, anokunyusa ukuxhaphaka kwezinye iintlobo zokuxhuzula.

Xa imeko ingavumi kunyango, oogqirha banokuzama ukuthintela iintlobo ezithile zokuxhuzula okanye ukunciphisa ukuxhaphaka kwazo. Umzekelo, ukuxhuzula okubangelwa yi-atonic kubaluleke kakhulu ukuthintela, njengoko kunxulunyaniswa nomngcipheko omkhulu wokwenzakala ngenxa yokuwa.

Unyango lokutya

Kwabaninzi abantu abanesifo sokuwa esinzima, utshintsho kwindlela yokutya lunokunceda ekunciphiseni ukuxhaphaka kokuwa okanye ukukuyekisa ngokupheleleyo. Ukutya okune-ketogenic kwisifo sokuwa – ukutya okuneproteni eninzi kunye namafutha kunye ne-carbohydrate ephantsi – kudla ngokucetyiswa ngoogqirha. Kungaba lukhetho olufanelekileyo xa amayeza engasebenzanga.

Nangona ukutya kwe-ketogenic kunyango oludumileyo lwesifo sokuwa esinzima, kuneengxaki ezimbalwa. Olu hlobo lokutya lusebenza kuphela ukuba ululandela ngokuchanekileyo. Oku kungenxa yokuba ukutya iicarbohydrate ezininzi, ezifana neswekile kunye nokutya okunesitatshi, kunokubangela ukuxhuzula. Nangona kunjalo, ezinye iindlela zokutya ezilungisiweyo nazo zinokunceda. Ukuba unomdla, ugqirha wakho unokukunceda uzame enye yezi ndlela zokutya.

Utyando lobuchopho kunye nezixhobo ezifakelweyo

Kwezinye iimeko, ingakumbi xa ezinye iindlela zonyango zingasebenzanga, utyando lolona khetho lungcono. Nazi ezinye iintlobo zotyando:

  • Ukukhuthazwa kweNerve yeVagus (VNS): Oku kuquka ukufaka isixhobo emzimbeni esihambisa umbane ophantsi kwi-nerve ye-10th cranial, i-vagus nerve - edibene ngqo nengqondo. Lo mbane unokunciphisa ukuxhaphaka kunye nobunzima bokuxhuzula. Ngokuhamba kwexesha, iziphumo zawo ziyanda. Oku kuthetha ukuba ukuxhuzula okuncinci kunye nokuxhuzula okuncinci kakhulu. Ukufakelwa esi sixhobo yinkqubo eguqukayo, enemingcipheko ephantsi kunye nexesha elifutshane lokuchacha, ngoko ke kudla ngokuqwalaselwa ngaphambi kotyando olukhulu.
  • I-Corpus callosotomy: I-corpus callosum yinxalenye yengqondo esebenza njengebhulorho phakathi kwe-hemispheres yasekhohlo neyasekunene. Xa i-corpus callosum inqunyulwe, imiqondiso engaqhelekanga ebangela ukuxhuzula ayisayi kuphinda ibuyele umva. Oku kunokunciphisa ukuxhaphaka kokuxhuzula, okanye kumise ukuxhuzula okunzima, okuphazamisa ngokupheleleyo.
  • I-Hemispherectomy `(I-Hemispherectomy)`:Oku kuquka ukususwa kwelinye icala lobuchopho ngotyando. Nangona oku kunokubonakala kugqithisile, iingcali zingakusebenzisa ukunqanda ukuxhuzula okungalawulekiyo. Kamva, unyango lomzimba lunokunceda ingqondo ukuba ilungele utshintsho. Ingqondo iyazilungisa, kwaye inxalenye eseleyo ithatha imisebenzi yenxalenye esusiweyo.
  • Ukususwa kwesisu: Ukungasebenzi kakuhle kwesakhiwo sengqondo ngamanye amaxesha kunokubangela i-LGS. Ukuba oogqirha banokufumanisa ukuba oku kungaqhelekanga, banokukwazi ukususa izicubu zengqondo ezonakeleyo okanye ezigulayo baze bayeke ukuxhuzula. Nangona kunjalo, kuba kwi-LGS, umsebenzi wokuxhuzula ukwiindawo ezingaphezu kwesinye zobuchopho, oku akusoloko kuyindlela ephumelelayo kwi-LGS.

Iingxaki/iziphumo ebezingalindelekanga zonyango

Iingxaki zonyango zixhomekeke kunyango ngalunye. Ke ngoko, kungcono ukuthetha nogqirha wakho malunga neengxaki kunye nemiphumo emibi yonyango olufumana wena okanye umntwana wakho. Ugqirha angakunika ulwazi olufanelekileyo kwimeko yakho, iimeko zakho, kunye nezinye iimeko zonyango.

Ndiza kuziva bhetele nini emva konyango? Kuza kuthatha ixesha elingakanani ukuze ndiphile?

Ixesha lokuchacha emva konyango liyahluka kakhulu ngokuxhomekeke kwiindlela zonyango ezisetyenzisiweyo kunye nemeko yakho iyonke. Ugqirha wakho ngumntu ofanelekileyo ukukuxelela into omawuyilindele kunye nexesha eliza kuthatha ukuchacha.

Ngaba i-Lennox-Gastaut syndrome (LGS) ingathintelwa?

Kwiimeko ezininzi, i-LGS ayisiyongxaki inokuthintelwa. Kwaye nomngcipheko wokuyifumana awunakuncitshiswa. Okukodwa kukuthintela ukwenzakala entloko nasengqondweni okunokubangelwa yi-LGS. Eyona ndlela yokuthintela le meko kukuba abantwana bakho banxibe izigcina-ntloko ezivunyiweyo neziqinisekisiweyo.

Yintoni endimele ndiyilindele ukuba mna okanye umntwana wam sinale meko?

Isifo sikaLennox-Gastaut sisifo esidla ngokuba nemiphumo emibi kakhulu. Abantwana abaninzi abanale meko bakhula nokukhubazeka kokufunda kunye nokonakala kwengqondo okuhlala kuhleli okuthintela amandla abo engqondo. Kwakhona, kuba ukuxhuzula (ukuhlaselwa ngamaconsi) kuxhaphakile, kwaye kudla ngokukhokelela ekuweni, abantwana abanale meko basengozini enkulu yokwenzakala.

Le meko ikwanzima ukuyinyanga. Abantwana abaninzi abanayo bafuna ukhathalelo olukhethekileyo ubomi babo bonke kuba abakwazi ukuzinyamekela. Nangona kunjalo, abanye abantu abanale meko banomonakalo omncinci engqondweni, nto leyo ethetha ukuba banokuphila ngokuzimela.

Ihlala ixesha elingakanani (LGS)?

Ngaphandle kokuba unyango lunikwe ukunqanda ngokupheleleyo ukuxhuzula (okungaqhelekanga kakhulu), i-LGS yimeko ehlala ubomi bonke.

Iyintoni ikamva lale meko?

Eyona mingcipheko mikhulu yesifo seLennox-Gastaut kukulimala kwengqondo ngenxa yokuxhuzula okungalawulekiyo, okanye ukuwa okubangelwa kukuxhuzula. Ngenxa yezo mingcipheko, izinga lokufa kwabantu abane-"LGS" kwiminyaka eli-10 emva kokufunyaniswa kwesi sifo liphakathi kwe-3% ne-7%.

Kwezinye iimeko, iinkqubo zonyango zinokumisa ukuxhuzula okubangelwa yi-LGS. Oku kuyayimisa le meko, kodwa akunakulungisa umonakalo engqondweni obangelwe kukuxhuzula kwangaphambili.

Ndingazinyamekela njani? / Ndingamnyamekela njani umntwana wam?

Ukuba wena okanye umntu omthandayo une-LGS, kubaluleke kakhulu ukulandela imiyalelo kagqirha wakho ngokuchanekileyo. Oku kuquka:

  • Ukuthatha amayeza njengoko kuchaziwe.
  • Ukuya kugqirha njengoko kucetyisiwe.
  • Ukubeka esweni ukuxhuzula kunye nokuphepha izinto ezinokubangela ukuxhuzula okanye iimeko ezinokubangela ukuxhuzula.

Ndifanele ndimbone nini ugqirha?

Ugqirha wakho okanye womntwana wakho uza kukuxelela ukuba uze kutyelelo olulandelayo xa kufuneka. Kufuneka ubone ugqirha wakho ukuba iimpawu zakho zokuxhuzula zitshintsha kakhulu okanye ukuba zichaphazela indlela oqhele ukwenza ngayo imihla ngemihla kunye nemisebenzi yakho.

Ndingaya nini kwiYunithi yoNyango oluNgxamisekileyo (i-ETU) ?

Ukuba wena okanye umntwana wakho unesithuthwane okanye isithuthwane esiphindaphindeneyo esihlangabezana neemfuno zengxamiseko yezonyango ebizwa ngokuba yi-status epilepticus , kufuneka uye kwigumbi likaxakeka kwisibhedlele esikufutshane nawe. Oku kuthetha ukuba kwezi meko zilandelayo:

  • Ukuba ukuxhuzula kube kanye kuthatha imizuzu emi-5 ukuya kwengama-30.
  • Ukuba umntu uxhuzula kabini okanye ngaphezulu kwimizuzu engama-30 aze angabuyi engqondweni ngokupheleleyo ngexesha lokuxhuzula.

Umyalezo Wokuya Ekhaya

I-Lennox-Gastaut syndrome (LGS) luhlobo olubi kakhulu lwesifo sokuwa esiqala kwangethuba. Sidla ngokuba nefuthe elinzulu, ngamanye amaxesha ubomi bonke bomntwana. Nangona kunzima ukunyanga, amayeza amatsha, utyando, kunye nonyango lunokunceda ukunciphisa ubunzima besifo kunye nokunciphisa ukusasazeka kwaso. Amaxesha amaninzi, unyango lunokunyanga ngokupheleleyo esi sifo. Nangona kunjalo, uphando oluthe kratya luyadingeka ukuze kuqinisekiswe ukuba esi sifo sinokunyangwa okanye sinyangwe na. Ukuba umntwana wakho unezinye zezi mpawu, kungcono ukubona ugqirha ngokukhawuleza.


Isifo sikaLennox -Gastaut, i-LGS, isifo sokuwa, ukuxhuzula, abantwana, iingxaki zobuchopho, izifo zemithambo-luvo

Frequently Asked Questions (FAQ)

Yintoni iStatus Epilepticus?

Oku kuthetha enye yezinto ezimbini:

Zeziphi iimvavanyo ezenziwayo ukufumanisa oku?

Iimvavanyo ezisetyenziswa kakhulu zezi:

Iyintoni ikamva lale meko?

Eyona mingcipheko mikhulu yesifo seLennox-Gastaut kukulimala kwengqondo ngenxa yokuxhuzula okungalawulekiyo, okanye ukuwa okubangelwa kukuxhuzula. Ngenxa yezo mingcipheko, izinga lokufa kwabantu abane-"LGS" kwiminyaka eli-10 emva kokufunyaniswa kwesi sifo liphakathi kwe-3% ne-7%.

⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

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