Ingaba izihlunu zakho ziyathamba kancinci kancinci? Ngaba oku kungaba yiPrimary Lateral Sclerosis (PLS)?

Ngaba ngamanye amaxesha uziva ngathi imilenze yakho inzima kancinci, ngathi yenziwe ngamatye? Okanye uziva ngathi ulahlekelwa yibhalansi yakho xa uhamba, okanye amalungu akho aphelelwa ngamandla kancinci? Ukuba ezi mpawu aziveli ngequbuliso, kodwa ziyanda kancinci kancinci, kunokuba kubalulekile ukuba uqaphele le meko ibizwa ngokuba yiPrimary Lateral Sclerosis (PLS). Ungakhathazeki, siza kuthetha ngayo yonke into ngokulula.

Ngamafutshane, yintoni isifo se-primary lateral sclerosis (PLS)?

I-Primary Lateral Sclerosis, okanye i-PLS ngamafutshane, sisifo esichaphazela imithambo-luvo kunye nemisipha yethu. Sibangela ukuba imisipha yethu ibe buthathaka kancinci kancinci, okanye kancinci kancinci, kwaye/okanye iqine.

Amaxesha amaninzi, ezi mpawu ziqala emilenzeni yakho. Ekuhambeni kwexesha, obu buthathaka kunye nokuqina kwazo kunokusasazeka kwezinye izihlunu emzimbeni wakho. Le yimeko eqhubekayo , nto leyo ethetha ukuba iimpawu ziya zisiba mandundu ngokuhamba kwexesha.

Akukho nyango lukhethekileyo lwale meko (PLS), ngoko ke unyango lujolise kakhulu ekulawuleni iimpawu nokukunceda ukuba wenze imisebenzi yemihla ngemihla ngokulula. Umzekelo, ukusebenzisa isixhobo sokuncedisa esifana nomsimelelo okanye isixhobo sokuhamba .

Le yimeko engaqhelekanga kakhulu, oko kuthetha ukuba ayiqhelekanga ukubonwa kuluntu.

Yintoni umahluko phakathi kwe-PLS kunye ne-ALS?

Mhlawumbi ukhe weva ngemeko ebizwa ngokuba yi -Amyotrophic Lateral Sclerosis (ALS) . Nangona zombini ezi zifo zibandakanya imithambo-luvo kunye nemisipha, kukho umahluko ocacileyo phakathi kwezi zimbini. Ukuze siqonde oku, masiqale sijonge indlela imizimba yethu elawula ngayo intshukumo.

Kukho uhlobo oluthile lweeseli zemithambo-luvo ezithwala imiyalezo esuka engqondweni yethu ukuya kwizihlunu zethu, sizibiza ngokuba zii-motor neurons . Zimbini iintlobo zezi:

1. Ii-Upper Motor Neurons (UMN): Ezi 'ziingcingo eziphambili' ezithwala imiyalezo esuka engqondweni ukuya kumqolo.

2. IiLower Motor Neurons (LMN): Ezi 'zii-sub-neurons' ezithwala imiyalezo ngqo ukusuka kwi-spinal cord ukuya kwimisipha.

Ngoku kubaluleke kakhulu ukuqonda lo mahluko.

Iimpawu zokuqala ze-ALS zinokufana kakhulu nezo ze-PLS. Ngoko ke ngamanye amaxesha ugqirha unokukuqala akuxilonge nge-PLS aze ayitshintshe ibe yi-ALS xa kuvela iimpawu ezichaphazela ne-LMN. Ngenxa yesi sizathu, ukuze kuqinisekiswe ngokuqinisekileyo i-PLS, iimpawu kufuneka zibonwe ubuncinane iminyaka emithathu ukuya kwemine .

Zithini iimpawu ze-PLS?

Iimpawu ze-PLS ziqala kancinci kakhulu. Nazi ezinye zeempawu zokuqala onokuzibona:

• Ukuqina kwemisipha emilenzeni.
• Ubuthathaka bemisipha emilenzeni.
• Ubunzima bokuhamba okanye ukuba nengxaki yokugcina ulungelelwano.
• Ukuqhaqhazela kwemisipha okanye ukuqaqamba okanye ukuqaqamba okubuhlungu.

Njengoko isifo siqhubeka, ezinye iimpawu zinokuvela:

• Ukuqina kwemisipha kunye nobuthathaka kwiminwe, izandla, kunye neengalo.
• Ubunzima bokulawula umchamo(Imfuneko engxamisekileyo yokuchama kunye nokuvuza komchamo).
• Intlungu yomqolo nentamo.

Kwiimeko ezingaqhelekanga kakhulu, izihlunu zolwimi nazo zinokuchaphazeleka. Kwimeko enjalo, ungabona iimpawu ezifana nezi:

• Intetho engacacanga (iDysarthria).
• Ubunzima bokuginya ukutya (i-Dysphagia).

Yintoni ebangela i-PLS?

Enyanisweni, asikazi ukuba yintoni kanye kanye imbangela ye-PLS kubantu abadala. Uninzi lwexesha, yenzeka ngokungacwangciswanga, ngaphandle kwesizathu esicacileyo.

Nangona kunjalo, kukho uhlobo olungaqhelekanga lwe-PLS oluchaphazela abantwana kunye nabantu abadala abancinci. Lubangelwa kukuguquka kwezakhi zofuzo (utshintsho kwi-DNA).

Into ebalulekileyo kukuba isifo se-PLS asiyosifo esidluliselwa kwilifa. Oku kuthetha ukuba ungaba naso nokuba akukho mntu kusapho lwakho owakha waba naso ngaphambili.

Ngubani osengozini enkulu?

Nabani na unokuba ne-PLS. Nangona kunjalo, izigulana zihlala zifunyaniswa ukuba zine-PLS xa zineminyaka engama-50 ubudala. Nangona kunjalo, zinokukhula nakubantu abancinci okanye abadala kunoko. Le meko ixhaphake kancinci kumadoda kunakwabasetyhini .

Ifunyaniswa njani le meko?

Emva kokufunda ngeempawu zakho, ugqirha wakho uza kwenza uvavanyo lomzimba nolwemithambo-luvo. Banokwenza novavanyo lokuthintela ezinye iimeko ezineempawu ezifana neze-PLS, ezifana ne-ALS okanye i-multiple sclerosis. Ezinye zezi vavanyo ziquka:

• Uvavanyo lwegazi: Jonga ezinye izizathu.
• Uvavanyo lwe-Electrodiagnostic: Olu vavanyo lulinganisa indlela esebenza ngayo imithambo-luvo kunye nemisipha yakho.
• I-MRI scan: Thatha imifanekiso eneenkcukacha zobuchopho kunye nomqolo ukuze ubone ukuba kukho naziphi na ezinye iingxaki.
• Ukubhobozwa kwethambo lomqolo (i-spinal tap): Oku kuquka ukuthatha ulwelo oluncinci kumqolo wakho uze ulujonge ukuba alunazo na iingxaki.

Zithini iindlela zonyango?

Njengoko besitshilo ngaphambili, akukho nyango luthile lwe-PLS. Unyango lujolise ekulawuleni iimpawu nokukunceda uphile ngokuzimela kangangoko unako.

• Amayeza: Amayeza anikwa ukunciphisa ukuqina kwemisipha, ukuqhwalela, kunye nobunzima bokuginya (umz. iBaclofen, iTizanidine, iQuinine, iDiazepam).
• Unyango lomzimba: Kucetyiswa ukuba umthambo unciphise ubuthathaka bemisipha, wonyuse ukuguquguquka, kwaye ugcine amalungu eshukuma kakuhle.
• Izixhobo zokuncedisa: Izixhobo ezifana nomsimelelo, i-walker , okanye isitulo esinamavili zisetyenziselwa ukukunceda uhambe wedwa.
• Unyango lokuthetha: Ukuba unengxaki yokuthetha, lunokukunceda.

Ufanele uye nini kugqirha?

Ukuba uvakalelwa kukuba ukuqina kwemisipha yakho okanye ubuthathaka buya bukhula kancinci kancinci, qiniseka ukuba ubona ugqirha wakho.

Kwakhona, ukuba sele ufunyenwe une-PLS kwaye amayeza owasebenzisayo enza iimpawu zakho zibe mandundu okanye abangela iziphumo ebezingalindelekanga, xelela ugqirha wakho ngaloo nto.

Ukuba wonzakele ngenxa yokuwa ngequbuliso okanye ingozi, yiya kwiYunithi yoNyango oluNgxamisekileyo (ETU) yesibhedlele ngoko nangoko.

Kuqhelekile ukuziva udandathekile njengoko amandla emisipha yakho ehla kancinci kancinci kwaye ungakwazi ukwenza izinto obuqhele ukuzenza. Ukuba uziva uxinezelekile malunga nolu tshintsho lomzimba, ukuthetha nomcebisi wezempilo yengqondo kunokukunceda.