Ingaba nawe unemithambo yegazi emincinci emiphungeni yakho? Masithethe ngePulmonary Arterial Hypertension (PAH)!

Ngaba ngamanye amaxesha uziva uphelelwa ngumphefumlo? Okanye uzive udiniwe ngokungaqhelekanga nangona uhamba umgama omfutshane? Ngaba wakha waphawula ukuba iminwe yakho kunye nemilebe yakho zijika zibe luhlaza okwesibhakabhaka kunye nokuqina okanye intlungu esifubeni sakho? Musa ukuzithatha njengezizinto eziqhelekileyo. Kuba ngamanye amaxesha, emva kwezi mpawu, kunokubakho imeko yempilo efuna ingqalelo ethile. Enye yezi meko yiPulmonary Arterial Hypertension (PAH) . Nangona igama lisenokuvakala lisoyikisa kancinci, masithethe ngalo ngokulula nangendlela onokuyiqonda.

Yintoni i-Pulmonary Arterial Hypertension (PAH)? Ngamafutshane...

Ngamafutshane, i-Pulmonary Arterial Hypertension (PAH) yimeko apho imithambo yegazi emincinci emiphungeni yakho (imithambo yegazi yemiphunga) incipha. Yicinge njengombhobho wamanzi ovalekileyo, kwaye kunzima ukuba amanzi adlule kuwo. Xa le mithambo yegazi incipha, igazi alikwazi ukuhamba kakuhle emiphungeni yakho. Oku kubangela ukuba uxinzelelo olungaphakathi kwezi mithambo yegazi, okanye uxinzelelo lwegazi, lube phezulu kakhulu . Le mithambo yegazi yileyo ithwala igazi elingenaoksijini ukusuka entliziyweni yakho ukuya emiphungeni yakho, apho licocwa khona.

Kuthekani ke xa oku kusenzeka? Icala lasekunene lentliziyo yakho kufuneka lisebenze nzima kunesiqhelo ukupompa igazi liye emiphungeni. Kufana nokuphakamisa umthwalo onzima nokunyuka intaba. Xa intliziyo kufuneka ithwale lo mthwalo wongezelelweyo ngokuhamba kwexesha, iqala ukuba buthathaka kancinci kancinci. Ukuba ayinyangwa kakuhle, le meko, i-PAH, inokubangela uthotho lweengxaki kungekuphela nje entliziyweni yakho nakwimiphunga, kodwa nakumzimba wakho wonke.

Khumbula, i-PAH luhlobo oluthile lwe- pulmonary hypertension , oluyimeko apho uxinzelelo kwimithambo yegazi yemiphunga lunyuka ngenxa yesizathu esithile.

I-PAH iyichaphazela njani umzimba wakho?

Uxinzelelo lwegazi oluphezulu lwemithambo yegazi (i-PAH) lubeka uxinzelelo kwicala lasekunene lentliziyo yakho. Oku kungenxa yokuba le nxalenye yentliziyo ihambisa igazi elingenaoksijini ukuya emiphungeni. Ekuhambeni kwexesha, olu xinzelelo luphezulu lunokubangela ukuba intliziyo ingasebenzi kakuhle kwicala lasekunene .

Ayipheleli apho, i-PAH ikwacothisa ukuhamba kwegazi phakathi kwentliziyo nemiphunga. Oku kuthetha ukuba igazi elincinci lifikelela emiphungeni ukuze kufumaneke ioksijini entsha. Ngenxa yoko, ioksijini encinci ithunyelwa kwamanye amalungu kunye nezicubu emzimbeni wakho. Enyanisweni, lonke ilungu lomzimba wethu lifuna ioksijini ukuze liphile. Ukuba ayifumani ngokwaneleyo, kuvela iingxaki.

Ingaba le meko ibizwa ngokuba yi-PAH iyingozi kangakanani?

I-Pulmonary Arterial Hypertension (PAH) yimeko embi kakhulu, ngamanye amaxesha ebeka ubomi esichengeni . Nangona kunjalo, ukuba ifunyenwe kwangethuba kwaye inyangwa ngokukhawuleza, ungaphila ubomi obude nobungcono. Yiyo loo nto kubalulekile ukuqaphela iimpawu.

Ngubani ochaphazeleka kakhulu yi-PAH?

I-PAH inokuchaphazela abantu abadala bayo nayiphi na iminyaka. Nangona kunjalo, ixhaphake kakhulu kubasetyhini , abadla ngokufunyaniswa bephakathi kweminyaka engama-30 nama-60 ubudala. Kukwafunyaniswe ukuba amadoda angaphezu kweminyaka engama-65 ubudala afumana i-PAH anokuba sengozini enkulu yokuhlaselwa sesi sifo.

Le meko inokuchaphazela neentsana ezincinci. Xa isenzeka kwiintsana ezisandul’ ukuzalwa, siyibiza ngokuba yiPersistent Pulmonary Hypertension in the Neonate (PPHN) .

Ixhaphake kangakanani i-PAH?

Xa kuthelekiswa nezinye iintlobo ze-pulmonary hypertension, ezifana ne-pulmonary hypertension ebangelwa sisifo sentliziyo okanye isifo semiphunga, i-PAH ayisiyonto ixhaphakileyo . Kwanakwilizwe elifana ne-United States, zi-500 ukuya kwi-1,000 kuphela iimeko ezintsha ze-PAH ezifunyaniswa minyaka le. Kumazwe aseNtshona, ukwenzeka kwazo kumalunga nama-25 kwisigidi.

Zithini iimpawu ze-Pulmonary Arterial Hypertension (PAH)?

Usenokungabi nazo naziphi na iimpawu kwisigaba sokuqala se-PAH. Uninzi lwabantu luqala ukuzifumana iimpawu njengoko isifo siqhubeka. Ezinye zezi mpawu ziquka:

• Ukutshintsha kombala oluhlaza okwesibhakabhaka kwiminwe okanye imilebe: Ngokungathi igazi alinawo umoya-mpilo.
• Intlungu yesifuba okanye ukuxinana: Njengokungathi kukho umntu ocinezela isifuba sakho.
• Ukudinwa okanye ukuquleka: Oku kunokwenzeka xa ukuhamba kwegazi ukuya engqondweni kuncipha.
• Ukudinwa: Ukuziva udiniwe kakhulu , kungekuphela nje ukudinwa.
• Ukubetha kwentliziyo okukhawulezayo okanye okuhlabayo.
• Ukuphefumla kancinci: Oku kuyanda ngokuhamba kwexesha. Nokuba ukwenza imisebenzi emincinci kunokubangela ukuphefumla kancinci.
• Ukudumba (Ukudumba): Ukudumba kungaqala emilenzeni nasemaqatheni, kuze kudlulele esiswini nasentanyeni.

Ukuba azinyangwa, ezi mpawu ze-PAH ziya kuba mandundu ngokuhamba kwexesha. Usenokuzifumana ungakwazi ukwenza imisebenzi yemihla ngemihla esisiseko ngaphandle kokuphefumla okanye ukuphumla.

Zithini izizathu ze-Pulmonary Arterial Hypertension (PAH)?

Eyona nto ibangela i-PAH kukonakala kwemithambo yegazi emiphungeni yakho. Nangona kunjalo, akusoloko kucaca ukuba yintoni ebangela lo monakalo.

Amatyala apho kungafumaneki sizathu (i-Idiopathic PAH)

Ngamanye amaxesha, akukho sizathu sithile sifumanekayo . Thina oogqirha sikubiza ngokuba yi- “idiopathic” pulmonary arterial hypertension . Kufana nemfihlakalo.

Izizathu ezaziwayo

Nangona kunjalo, ngamanye amaxesha, kukho izizathu ezicacileyo. Ezinye zezizathu ezaziwayo ze-PAH ziquka:

• Ezinye iimeko zonyango:
• Isifo sentliziyo esizalwa naso
• Izifo zokugcina iGlycogen
• Usulelo lwe-HIV
• Isifo sesibindi
• Izifo ezizikhuselayo emzimbeni ezifana ne -lupus
• Uxinzelelo lwegazi oluphezulu lwe-portal (uxinzelelo olongezelelekileyo kwimithambo yegazi ekhokelela esibindini)
• I-hemangiomatosis ye-pulmonary capillary (ukukhula okungaqhelekanga kwe-capillaries emiphungeni)
• Isifo se-pulmonary veno-occlusive disease (ukuvaleka kwemithambo emiphungeni)
• I-Schistosomiasis (usulelo olubangelwa yiparasite)
• I-Scleroderma (ukuqina kolusu kunye nezicubu ezinxibelelanayo)

• Utshintsho lwemfuza:
• Amaxesha amaninzi, oku kungenxa yokuguquka kwejini yakho ye-BMPR2 . Le jini ilawula inani leeseli kwezinye izicwili emzimbeni wethu. Ngoko ke, xa le jini itshintshatshintsha, iiseli kwimithambo yegazi emincinci emiphungeni yakho zinokukhula kakhulu. Xa ezi seli zizala, imingxuma kwimithambo yegazi iba mxinwa.
• I-PAH ingasebenza kwiintsapho. Siyibiza ngokuba yi-PAH ezuzwa njengelifa . Malunga nama-80% abantu abanale meko baneziguquguquko kwi-gene ye-BMPR2.
• Abanye abantu bathwala olu tshintsho lwejini, kodwa abaze bavelise i-PAH.
• Abanye abantu banokuba ne-PAH nangona kungekho mntu kwintsapho yabo onayo, ngenxa yotshintsho lwemfuza. Oku kubizwa ngokuba yi -PAH engaqhelekanga .

• Amanye amayeza kunye neziyobisi:
• Ezinye iipilisi zokunciphisa umzimba , njengeyeza elidala elithi “fen-phen,” ngoku azivumelekanga, kodwa zisenokubangela i-PAH emva kweminyaka emininzi zisetyenziswa.
• Iziyobisi zokuzonwabisa , umzekelo i-cocaine kunye ne-methamphetamine.

Ifunyanwa njani i-Pulmonary Arterial Hypertension (PAH)?

I-PAH inokuba nzima ukuyifumanisa kuba iimpawu ze-PAH ziyafana nezezinye izifo ezininzi. Ugqirha wakho uza kwenza uvavanyo lomzimba aze athethe nawe ngeempawu zakho kunye nembali yakho yezonyango. Baza kwenza uvavanyo oluninzi (kuquka uvavanyo lwemifanekiso kunye novavanyo lwegazi) ukuze bafumane ukuba unesifo segazi esingaphezulu kweqondo loxinzelelo lwegazi emaphaphu, kwaye ukuba kunjalo, loluphi uhlobo lwaso.

Ugqirha wakho angakuthumela kwingcali yezifo zamaphaphu okanye kwingcali yentliziyo . Ezi ngcali ziya kwenza uvavanyo olukhethekileyo ukujonga ukusebenza kwentliziyo nemiphunga yakho. Ziya kugqiba ukuba ngaba une-PAH okanye olunye uhlobo lwe-pulmonary hypertension. Ziya kuhlola nokuba imeko yakho imbi kangakanani.

Kukho unyango oluthile lwe-PAH olungekhoyo kwezinye iintlobo ze-pulmonary hypertension. Ke ngoko, iqela lakho lezonyango kufuneka lazi kangangoko kunokwenzeka malunga nokuba kwenzeka ntoni emiphungeni nasentliziyweni yakho. Olu lwazi luya kubanceda baphuhlise isicwangciso sonyango esifanelekileyo kuwe.

Zeziphi iimvavanyo ezisetyenziswayo ukufumanisa i-PAH?

Iqela lakho lezonyango liza kusebenzisa indibaniselwano yovavanyo ukuze liqinisekise ukuba akukho ezinye izifo kwaye lixilonge i-PAH.

Ukuba ugqirha wakho ukrokrela ukuba usenokuba ne-PAH emva kovavanyo lwakho lomzimba, uvavanyo lokuqala aza kuluyalela yi- transthoracic echocardiogram . Olu vavanyo luvavanya ulwakhiwo kunye nomsebenzi wentliziyo yakho iyonke.

Ezinye iimvavanyo zingabandakanya:

• Uvavanyo lwegazi: Jonga ukusebenza kwamalungu omzimba, amanqanaba ehomoni, kwaye uchonge izifo ezisisiseko. Ingakumbi uvavanyo olufana ne-complete metabolic panel kunye ne -complete blood count .
• I-CT scan yesifuba: Ukujonga nokuthintela ezinye iimeko ezifana nesifo sezintso. (Mhlawumbi isifo sezintso kwinqaku lokuqala kufuneka sibe sisifo semiphunga. I-CT chest scan ijonga imiphunga kunye namalungu esifubeni. Masithi sijonga imeko yemiphunga.
• I-X-ray yesifuba: Ukujonga ukuba imithambo yentliziyo okanye yemiphunga yakho inkulu kuneqhelekileyo.
• I-MRI yentliziyo: Hlola imeko ye-ventricle yasekunene yentliziyo yakho (eli ligumbi lentliziyo elipompa igazi ukuya emiphungeni).
• I-Polysomnogram (PSG): Ukuhlolwa kwe-sleep apnea, nto leyo enokwenza i-PAH ibe mandundu. I-PSG luhlobo lovavanyo lokulala olwenziwa ebusuku.
• Uvavanyo lokusebenza kwephaphu: Jonga ukuba imiphunga yakho isebenza kakuhle kangakanani.
• Iskeni yokungenisa umoya/ukukhupha igazi kwimiphunga: Ijonga ukuba akukho mahlwili egazi emiphungeni. Olu vavanyo lunokuthintela imeko ebizwa ngokuba yi -chronic thromboembolic pulmonary hypertension .
• Ukufakwa kwe-catheter yentliziyo ekunene: Kulinganisa uxinzelelo kwimithambo yegazi kwimiphunga yakho (uxinzelelo lwemithambo yegazi yepulmonary). Olu vavanyo lubalulekile ukuze kufunyaniswe ngokucacileyo i-PAH.
• Uvavanyo lokuhamba ngeenyawo lwemizuzu emithandathu: Jonga ukuba ungawunyamezela umthambo ongakanani kunye nokuba ingakanani ioksijini ejikeleza egazini lakho xa ushukuma.

Thetha nogqirha wakho malunga novavanyo ekufuneka ulwenze kunye nendlela yokuzilungiselela.

Ziziphi iindlela zokuchonga uxinzelelo lwegazi lwe-Pulmonary Arterial?

Oogqirha baxilonga uxinzelelo lwegazi oluphezulu lwemiphunga ngokulinganisa uxinzelelo olukwimithambo yegazi emiphungeni yakho. Iindlela zokuxilonga zezokuba uxinzelelo lwemithambo yegazi emiphungeni yakho lungaphezulu kwe-20 millimeters yemercury (20 mmHg) xa uphumle . Eli xabiso lilinganiswa nge- catheterization yentliziyo ekunene .

Ziziphi iindlela zonyango lwe-Pulmonary Arterial Hypertension (PAH)?

Iinjongo eziphambili zonyango lwe-PAH kukulawula ukuqhubela phambili kwesi sifo kunye nokukunika ubomi obungcono. Akukho nyango lufanayo lwe-PAH. Ugqirha wakho uza kusebenza nawe ukumisela unyango olulungele iimfuno zakho ezithile.

Isicwangciso sakho sonyango lwe-PAH singabandakanya:

• I-Balloon atrial septostomy (BAS): Le nkqubo idla ngokwenziwa kwiintsana ezineziphene zentliziyo ezizalwa nazo, kodwa ngamanye amaxesha isetyenziswa kubantu abadala abane-PAH. I-septostomy inceda ekunciphiseni uxinzelelo kwicala lasekunene lentliziyo, ivumela ioksijini engaphezulu ukuba ijikeleze egazini. Ingenziwa njengebhulorho eya kufakelo lwemiphunga.
• Izithinteli zeCalcium channel: La mayeza anceda ekunciphiseni uxinzelelo lwegazi kwimithambo yegazi yemiphunga yakho nakuwo wonke umzimba wakho.
• I-Diuretics: Ekwaziwa ngokuba "ziipilisi zamanzi," la mayeza anceda ukususa ulwelo olugqithisileyo emzimbeni kwaye anciphise ukudumba.
• Unyango lweoksijini: Olu nyango lunokufuneka ukuba awunaoksijini eyaneleyo egazini lakho. Ioksijini eyongezelelweyo inokukunceda xa uphumle, ulele, okanye uzilolonga.
• Ii-vasodilator zemiphunga: La mayeza anceda imithambo yegazi emiphungeni yakho (imithambo yemiphunga) ukuba iphumle kwaye ivuleke ngokubanzi. Oku kunciphisa uxinzelelo entliziyweni yakho kwaye kunceda ekunciphiseni iimpawu zakho.

Kwabanye abantu abane-PAH enzima , ukufakelwa imiphunga kungaba lolona khetho lokugqibela. Olu tyando lunokukunika umphunga omnye okanye emibini emitsha. Ukufakelwa intliziyo nemiphunga kunokukunika intliziyo entsha.

Ngawaphi amayeza anikwa i-PAH?

Amayeza okunyanga i-PAH aza ngeendlela ezahlukeneyo:

• Amayeza omlomo: La mayeza anceda ekuphumzeni imithambo yegazi emiphungeni kwaye ayithintele ukuba inciphe. La mayeza anokukunceda ukuba usebenze ngokomzimba.
• Amayeza afunxwayo: Nyanga ubunzima bokuphefumla.
• Impompo yokufunxa ephathwayo: Oku kunokunceda ukuvula imithambo yegazi nokunyusa ukuhamba kwegazi. Oku kunokunceda ukuphucula iimpawu zakho.
• Amayeza afakwa kwimithambo yegazi: Avula imithambo yegazi aze anciphise iimpawu ezifana neentlungu zesifuba kunye nobunzima bokuphefumla.

Nazi ezinye zezonyango ezivunyiwe yi-US Food and Drug Administration (FDA) kwizigulana ze-PAH:

• I-Ambrisentan (ngomlomo)
• I-Bosentan (ngomlomo)
• I-Epoprostenol (IV)
• I-Iloprost (ukuphefumla)
• IMacitentan (ngomlomo)
• I-Riociguat (ngomlomo)
• I-Selexipag (ngomlomo)
• I-Sildenafil (eyomlomo)
• I-Tadalafil (ngomlomo)
• Treprostinil (ngomlomo, ukuphefumla, impompo, IV)

Iziphumo ebezingalindelekanga zamayeza e-PAH

Ezinye iziphumo ebezingalindelekanga eziqhelekileyo zamayeza asetyenziswa ukunyanga i-PAH ziquka:

• Ukuziva unesizungu okanye utyhafile.
• Ukuziva ufudumele ebusweni, entanyeni, okanye ezandleni (ukuhlanjwa).
• Iimpawu zesisu ezifana nokudumba, isicaphucaphu, ukuhlanza, kunye norhudo.
• Intloko ebuhlungu (intloko ebuhlungu).
• Uxinzelelo lwegazi oluphantsi (Hypotension) .
• Ukudumba kwemilenze namaqatha (iPedal edema) .
• Ukuqhambuka kwesikhumba.
• Ukuziva ngathi uxinana kwindlela yokuphefumla ephezulu.

Amanye amayeza anokuba nemiphumo emibi eyongezelelweyo. Thetha nogqirha wakho malunga nendlela yokulawula nayiphi na imiphumela emibi. Kwezinye iimeko, ugqirha wakho unokufuna ukutshintsha umthamo wamayeza akho.

Ngaba i-Pulmonary Arterial Hypertension (PAH) inganyangeka ngokupheleleyo?

Nangona amayeza akhoyo ngoku anokulawula ukuqhubela phambili kwe-PAH, awanakukwazi ukubuyisela umva umonakalo osele ukho . Nangona kunjalo, abaphandi baphanda amayeza amatsha abacinga ukuba angayibuyisela umva i-PAH. La mayeza anokulungisa umonakalo kwiiseli ze-endothelial ezijikeleze imithambo yegazi emiphungeni yakho.

Thetha nogqirha wakho ukuze ufunde okungakumbi ngophando lwamva nje kunye novavanyo lweklinikhi lonyango lwe-PAH.

Zeziphi izinto ezibangela ukuba umntu abe sengozini yokuba ne-Pulmonary Arterial Hypertension (PAH)?

Izinto ezininzi ezonyusa umngcipheko wokufumana i-PAH zezi:

• Isifo sezicubu ezidityanisiweyo .
• Isifo seDown .
• Imbali yosapho ye-pulmonary hypertension.
• Usulelo lwe-HIV .
• Ukusebenzisa amayeza okunciphisa umzimba afana ne-“fen-phen” (dexfenfluramine kunye ne-phentermine).
• Ukusetyenziswa kweziyobisi ezingekho mthethweni (iziyobisi zasesitalatweni).

Ukuba kukho umntu kusapho lwakho one-PAH, buza ugqirha wakho malunga novavanyo lwemfuza. Ukuba ufunyaniswe une-PAH, kungcono ukucela usapho lwakho ukuba nalo lucinge ngovavanyo lwemfuza.

Ungayithintela njani i-Pulmonary Arterial Hypertension (PAH)?

Asinakulawula ezinye izinto ezibangela umngcipheko we-PAH (ezifana notshintsho lwemfuza). Nangona kunjalo, ukuhlala kude neziyobisi ezingekho mthethweni kunokunciphisa umngcipheko wakho kungekuphela nje we-PAH, kodwa nezinye iingxaki ezininzi zempilo. Kwakhona, thetha nogqirha wakho ngaphambi kokuba uthathe naliphi na iyeza lokunciphisa umzimba.

Ngokuxhomekeke kwizinto ezikubangela umngcipheko, ugqirha wakho unokucebisa ukuba uhlolwe i-PAH ngokuthintela.

Iyintoni ikamva labantu abane-Pulmonary Arterial Hypertension (PAH)?

Ngenxa yokuqhubela phambili kunyango, abantu abane-PAH baphila ixesha elide kunangaphambili. Ubungakanani bobomi bakho buxhomekeke kwizinto ezininzi, kuquka ubukhali bemeko yakho kunye nokuba uxilongwa kwangethuba kangakanani. Thetha nogqirha wakho ngemeko yakho ethile.

Eyona nto ibalulekileyo kukuqhuba unyango lwakho kwaye ulandele imiyalelo kagqirha wakho ngononophelo. Kukho izinto ezimbalwa onokuzenza ukuphucula amathuba akho okusinda:

• Yenza ikhithi yongxamiseko. Kukho izinto ezithile kunye nolwazi ekufuneka uhlale unalo. Buza ugqirha wakho ukuba uza kufaka ntoni kwikhithi yakho, kwaye ungaze uphume ekhaya ungayisebenzisi.
• Fumana izitofu zamaxesha onyaka njengoko ugqirha wakho ecebisile. Kubaluleke kakhulu ukuzikhusela kumkhuhlane kunye ne-pneumonia.
• Gcina onke amadinga okulandela. Ukuhlolwa rhoqo kubalulekile ukujonga ukusebenza kwemiphunga yakho kunye nentliziyo yakho kunye nokulinganisa inkqubela yonyango lwakho.
• Sela amayeza akho kanye njengoko ugqirha wakho ekuyalele, ngexesha elifanayo yonke imihla. Musa ukutshintsha indlela othatha ngayo amayeza akho ngaphandle kwengcebiso kagqirha wakho.

Zeziphi iinguqu zendlela yokuphila ekufuneka ndizenze?

Landela icebiso likagqirha wakho malunga naluphi na utshintsho kwindlela ophila ngayo ofuna ukulwenza. Ngokubanzi, nazi ezinye iingcebiso ezibalulekileyo:

• Ziphephe iibhafu ezishushu, ii-sauna, kwaye uhambe uye kwiindawo eziphakamileyo.
• Cinga ngolawulo lokuzala. Ukukhulelwa kunokuba yingozi kubantu abane-PAH. Thetha nogqirha wakho ukuba uceba ukukhulelwa okanye ukuba ungakhulelwa.
• Zilolonge kwaye uhlale usebenza kangangoko unako. Thetha nogqirha wakho malunga nokuba zeziphi imithambo ekhuselekileyo kuwe kunye nokuba ungakanani umsebenzi omele uwenze yonke imihla. Buza ugqirha wakho ngaphambi kokuba uqalise inkqubo entsha yokuzilolonga.
• Landela ukutya okunempilo kwentliziyo. Oku kuquka ukutya okunamafutha agcweleyo aphantsi, amafutha e-trans, kunye ne-sodium.
• Yeka ukutshaya nokusebenzisa iimveliso zecuba. Kwakhona, kuphephe ukutshaya umsi osetyenziswa ngabanye abantu.
• Funa inkxaso, ungazami ukuhamba wedwa kuhambo lwakho lwe-PAH. Buza ugqirha wakho malunga namaqela enkxaso kunye nezixhobo.

Ndifanele ndibize ugqirha wam nini?

Fowunela ugqirha wakho ukuba unemibuzo ethile kule:

• Ukuba isantya sentliziyo singaphezulu kwe-120 beats ngomzuzu (isantya sentliziyo esikhawulezayo).
• Ukuba usulelo okanye ukukhwehlela kuyanda.
• Ukuba uhlala uziva unesizungu okanye utyhafile.
• Ukuba ufumana iintlungu esifubeni okanye ukungakhululeki ngokwenza umthambo.
• Ukuba udinwa kakhulu okanye amandla akho okwenza imisebenzi eqhelekileyo ayancipha.
• Isicaphucaphu okanye ukungabi namdla wokutya.
• Ukungazoli okanye ukudideka.
• Ukuba ukuphefumla kwakho kuya kuba mandundu, ingakumbi ukuba uziva uphelelwa ngumphefumlo xa uvuka.
• Ukuba ukudumba emaqatheni akho, emilenzeni, okanye esiswini kuya kusiba mandundu.
• Ubunzima bokuphefumla xa usebenza okanye uphumle.
• Ukunyuka kobunzima (iikhilogram ezi-2 ngosuku okanye iikhilogram ezi-5 ngeveki).

Ndingaya nini kwiSebe leeNgxamiseko (i-ETU) ?

Ukuba unayo nayiphi na kwezi zinto, yiya kwigumbi likaxakeka okanye utsalele umnxeba kwinombolo yakho kaxakeka yasekuhlaleni:

• Ukuba izinga lentliziyo (120-150 beats ngomzuzu) alinciphi.
• Ukuquleka, okubangela ukulahlekelwa zingqondo.
• Iingxaki ezivela kwi-IV okanye kwi-infusion pump yakho (ezifana nosulelo, ukuphuma kwe-catheter, ukuvuza kwesisombululo, ukopha, ukungasebenzi kakuhle kwe-IV pump).
• Ukuba ukuphefumla okuncinci akupheli nokuba sele uphumle.
• Intlungu yesifuba ekhawulezileyo neqatha.
• Intloko ebuhlungu nengxamisekileyo.
• Ubuthathaka ngequbuliso okanye ukukhubazeka kweengalo okanye imilenze.

Okokugqibela, umyalezo ekufuneka uhlale uwukhumbula

I-Pulmonary Arterial Hypertension (PAH) sisifo esitshintsha ubomi. Ukuba wena okanye umntu omthandayo usandul' ukufunyanwa esi sifo, zinike ixesha lokufunda ngesi sifo kunye noko unokukulindela. Buza ugqirha wakho ngezixhobo ezichaza indlela i-PAH esebenza ngayo kunye nendlela unyango olunokunceda ngayo.

Esinye sezona zixhobo zixabisekileyo onokuba nazo kukuxhaswa ngabanye ebomini bakho. Musa ukuzama ukulawula le meko wedwa. Ukuba usapho lwakho nabahlobo bakho abakho, buza ugqirha wakho malunga namaqela enkxaso kunye nezibonelelo zoluntu.

Ukuba umntu omthandayo ufunyenwe enale sifo, yenza konke okusemandleni akho ukumenza azive exhaswa kwaye umncede adibane nabanye. Ukugula kunokusenza sizive sisodwa ngeendlela ezithile, kodwa kunokusenza sisondelelane. Sebenzisa eli xesha ukwakha uluntu olunokukunceda wena okanye umntu omthandayo ukuba aqhubele phambili.

Uxinzelelo lwegazi oluphezulu lwemithambo yemiphunga , i-PAH, uxinzelelo oluphezulu lwegazi oluphezulu lwemiphunga, ukuphefumla nzima, isifo sentliziyo, isifo semiphunga, iimpawu