Wake wezwa ngokujiya kwegazi? Lokhu kungase kube yinto entsha kuwe. Igazi emzimbeni wethu alilona uketshezi olufana namanzi, kodwa liyinto egobile kancane. Kodwa kuthiwani uma lokhu kugobile kuba phezulu kakhulu kunokudingekile? Yilapho-ke sithola khona isimo esizokhuluma ngaso esibizwa ngokuthi "i-Hyperviscosity Syndrome". Lokhu kwenzeka lapho igazi lakho ligobile kakhulu futhi lingakwazi ukugeleza kahle emithanjeni yakho yegazi.
Iyini i-Hyperviscosity Syndrome? Masiyiqonde kalula.
Kalula nje, `(Hyperviscosity Syndrome)` kusho ukuthi igazi lakho liba likhulu kakhulu . Cabanga ngalo njengoju. Uju lujiyile kunamanzi, futhi yilokho okwenzekayo nalapha. Igazi lethu liqukethe izinto ezifana namaseli abomvu egazi, amaseli amhlophe egazi, namaprotheni egazi. Uma noma yikuphi kwalokhu kwanda ngobuningi noma uma amaseli abomvu eba nesimo esingavamile, igazi lingaba likhulu kakhulu. Kufana nokufaka ufulawa omncane esitsheni bese liba likhulu.
Uma igazi liqina ngale ndlela, alihambi kalula emithanjeni yegazi ethambile emizimbeni yethu. Yilapho-ke izinkinga ziqala khona.
Ingabe lesi simo singaba yingozi?
Yebo, i-Hyperviscosity Syndrome iyisimo esibi kakhulu . Uyazi ukuthi siyini? Uma igazi lingahambi kahle, izitho zethu ezibalulekile (njengobuchopho, inhliziyo, nezinso) azitholi umoya-mpilo nezakhamzimba ezizidingayo. Lokhu kungaholela ekuvinjweni kwemithambo yegazi kanye nokungasebenzi kahle kwezitho zomzimba.
Uma ingane encane iba nalesi simo, singathinta ngqo ukukhula kwayo . Ngoba ngesikhathi lapho ubuchopho bayo nomzimba wayo kukhula ngokushesha, ukujikeleza kwegazi okuphazamisekile kuyinkinga enkulu. Ngakho-ke, kubaluleke kakhulu ukuqaphela lokhu.
Ubani onamathuba amaningi okuthola i-Hyperviscosity Syndrome?
Nakuba lesi simo singakhula kunoma ubani, abanye abantu basengozini enkulu. Abantu abanesimo esingavamile esibizwa ngokuthi i-Waldenstrom macroglobulinemia basengozini enkulu yokuthola i-Hyperviscosity Syndrome. Lokhu kwenzeka lapho uhlobo olukhethekile lweprotheni ebizwa ngokuthi i-macroglobulin egazini lethu luba phezulu kakhulu. Ngokwezibalo, abantu abangaphezu kuka-30% abane-Waldenstrom macroglobulinemia bazoba ne-Hyperviscosity Syndrome ngesikhathi esithile empilweni yabo.
Ziyini izimpawu ze-Hyperviscosity Syndrome? Masiqaphele!
Izimpawu zalesi simo zingahluka kumuntu nomuntu, kodwa singazihlukanisa zibe ezivamile nezingavamile.
Izimpawu ezivamile:
- Ubuhlungu bekhanda: Ubuhlungu bekhanda obuvame ukwenzeka, ngezinye izikhathi obukhulu.
- Ukuquleka: Abanye abantu bangase babe nezimo ezifana nokuquleka.
- Ibala lesikhumba elibomvu: Ngezinye izikhathi izindawo ezifana nobuso nezandla zingase zibonakale zibomvu.
Izimpawu ezingavamile, kodwa ezibalulekile:
- Ubuhlungu besifuba: Ubuhlungu besifuba bungenzeka, obufana nesifo senhliziyo.
- Ubunzima bokuhamba: Kungaba nzima ukuhamba, njengokungathi ulahlekelwe yibhalansi yakho.
- Izinkinga zokuzwa: Ungase uzizwe sengathi ulahlekelwa ukuzwa, noma ungase uzwe imisindo ehlukene ezindlebeni zakho.
- Ukopha okungajwayelekile: Isibonelo, ukopha kwezinsini kanye nokopha ekhaleni njalo.
- Ubunzima bokuphefumula (i-Dyspnea): Ungase uzizwe sengathi unenkinga yokuphefumula ngisho nalapho ukhuphuka izitebhisi noma wenza umsebenzi olula.
- I-Vertigo: Ungase uzizwe unesiyezi, sengathi ikhanda lakho liyazungeza, futhi ungakwazi ukuma.
- Ukushintsha kombono: Umbono ofiphele kanye nombono ophindwe kabili kungenzeka.
Uma uqhubeka nokuba nesinye noma ngaphezulu salezi zimpawu, kungcono kakhulu ukufuna iseluleko sezokwelapha. Ungesabi, kodwa ungazinaki futhi.
Yini ebangela i-Hyperviscosity Syndrome ezinganeni ezincane?
Kunezizathu eziningana eziqondile zokuthi kungani lesi simo singenzeka enganeni esanda kuzalwa:
- Izinkinga zofuzo: Isibonelo, izimo ezifana ne-"Down syndrome".
- Isifo sikashukela sokukhulelwa: Uma umama enesifo sikashukela ngesikhathi sokukhulelwa, singathinta ingane.
- Izinkinga ezibangelwa ufuzo: Uma othile emndenini eke waba nalezi zimo.
- Ukubopha kwentambo yenkaba ngemuva kwesikhathi: Lokhu kungaba yimbangela kwezinye izimo.
- I-Twin-to-twin transfusion syndrome: Lokhu kungenzeka lapho amawele afanayo enokuxhumana okungavamile kwemithambo yegazi ku-placenta phakathi kwawo.
Yiziphi izimbangela zalesi simo kubantu abadala?
Kwabantu abadala, njengoba kushiwo ngaphambili, `(i-Waldenstrom macroglobulinemia)` iyimbangela eyinhloko. Ngaphandle kwalokho, kungase kube nezinye izimbangela eziningana:
- Izinhlobo zomdlavuza wegazi: Isibonelo, `(Acute myeloid leukemia - AML)` kanye nezinye izinhlobo `(Leukemia)`.
- I-hypoxia engapheli: Lokhu kungabangelwa yizinto ezifana nezifo ezithile zokuphefumula.
- Izifo zezicubu ezixhumeneyo: Isibonelo, izifo ezifana `(Rheumatoid arthritis)` kanye `(Lupus)`.
- I-Cryoglobulinemia: Isimo lapho amaprotheni angajwayelekile akheka khona egazini.
- I-Essential thrombocythemia: Ukwanda okukhulu kwenani lama-platelet egazi.
- I-Multiple myeloma: Umdlavuza womnkantsha wamathambo.
- (Ama-syndrome e-paraneoplastic):Iqoqo lezimpawu ezibangelwa umdlavuza kwezinye izingxenye zomzimba.
- (I-Polycythemia vera): Ukwanda ngokweqile kwenani lamaseli abomvu egazi.
- (Sjögren's syndrome): Isimo esithinta izindlala ezikhiqiza umswakama emzimbeni.
- I-Myelodysplastic syndrome: Inkinga ngokukhiqizwa kwamaseli emnkantsheni wamathambo.
La magama angase abonakale edida kancane kuwe. Into ebalulekile okufanele uyikhumbule ukuthi akuzona zonke lezi zimo ezibangela i-Hyperviscosity Syndrome, kodwa ukuthi isimo sezokwelapha esingaphansi kwalesi singabangela ukujiya kwegazi.
Ungayithola kanjani i-Hyperviscosity Syndrome? (Ukuxilongwa)
Odokotela bavame ukuxilonga lesi simo ngokwenza ukuhlolwa kwegazi okuningana, okunye kwakho okuhlanganisa:
- Ukuhlolwa kwegesi yegazi lemithambo: Kuhlola amazinga omoya-mpilo kanye ne-carbon dioxide egazini.
- Ukuhlolwa kwe-Bilirubin: Kuhlola izinga le-bilirubin, into ephuzi ekhiqizwa lapho amangqamuzana abomvu ephuka.
- Ukuhlolwa koshukela egazini: Hlola izinga likashukela egazini (i-glucose).
- Ukubalwa kwegazi okuphelele (i-CBC): Kukala amazinga azo zonke izingxenye egazini, okuhlanganisa amangqamuzana abomvu egazi, amangqamuzana amhlophe egazi, namaprotheni.
- Ukuhlolwa kwe-Creatinine: Kuhlola ukuthi izinso zisebenza kahle kangakanani.
- Ukuhlolwa kokusebenza kwesibindi: Ukuhlolwa kwamaprotheni esibindi.
- Ukuhlolwa kwe-serum viscosity noma ukuhlolwa kwe-whole blood viscosity: Ukuhlolwa okulinganisa ngokunembile i-viscosity yegazi.
- Ukuhlolwa kwamaprotheni: Kala inani lamaprotheni ahlukahlukene egazini.
Kusekelwe emiphumeleni yalezi zivivinyo ukuthi udokotela angabona ngqo ukuthi une-"Hyperviscosity Syndrome" noma cha.
Yiziphi izindlela zokwelapha lokhu? (Izindlela zokwelapha)
Ukwelashwa kwe-"Hyperviscosity Syndrome" kungahlukahluka kuye ngokuthi imbangela iyini . Njengoba ukuphelelwa amanzi emzimbeni kungaba kubi kakhulu kulesi simo, udokotela angase ancome ukuthi kufakwe i-intravenous (IV) hydration .
Kwezinye izimo ezinzima, odokotela bangase basebenzise izindlela zokwelapha ezifana nalezi:
- Ukumpontshelwa igazi ngokwengxenye: Lokhu kuhilela ukukhipha inani elincane legazi bese kufakwa isixazululo sikasawoti esikhundleni salo. Lokhu kungasiza ekunciphiseni ukujiya kwegazi.
- I-Plasmapheresis: Lokhu kuhilela ukususa inani elincane le-plasma, ingxenye ewuketshezi yegazi, bese kufakwa enye esikhundleni sayo. Lokhu kusiza ukususa amaprotheni ayingozi egazini futhi kunciphise ukujiya kwalo.
Lezi zindlela zokwelapha zinqunywa udokotela wakho, kuye ngesimo sakho kanye nembangela.
Ingabe zikhona izindlela zokuvimbela i-Hyperviscosity Syndrome?
Eqinisweni, ayikho indlela yokuvimbela ngokuphelele `(i-Hyperviscosity Syndrome)`. Kodwa-ke, uma ukhulelwe, kunezinto ezithile ongazenza ukuze unciphise ingozi yokuba ingane yakho ithole lesi simo :
- Thola ukuhlolwa kofuzo: Lokhu kuzokusiza uqonde amathuba okuba nengane enesifo sofuzo.
- Yidla ukudla okunomsoco futhi uvivinye umzimba njalo : Lokhu kunganciphisa ingozi yokuthola isifo sikashukela sokukhulelwa.
- Iya emitholampilo yezokwelapha bese uthola izivivinyo njengoba kuhleliwe: Kubaluleke kakhulu ukulandela iseluleko sezokwelapha phakathi nokukhulelwa kwakho.
Kwenzekani kumuntu one-Hyperviscosity Syndrome? (Ukulandelela)
I-Hyperviscosity Syndrome yisimo esidinga ukwelashwa okusheshayo . Uma singalashwa, singaholela ezinkingeni ezisongela ukuphila kanye nokwehluleka kwezitho zomzimba.
Izindaba ezinhle ukuthi izinsana nabantu abadala abathola ukwelashwa ngesikhathi bavame ukululama ngokuphelele kulesi simo . Kodwa-ke, uma i-hyperviscosity syndrome ibangelwa yisimo esingamahlalakhona esingaphansi, kungadingeka uqhubeke nokwelashwa ukuze uvimbele ukuthi singaphinde sivele.
I-Hyperviscosity Syndrome izwakala kanjani?
Lokhu kungahluka kumuntu nomuntu. Lapho igazi likhula, ukugeleza kwegazi kuya ebuchosheni kuyancipha, okungabangela ikhanda elibuhlungu, isiyezi, noma ngisho nokuquleka . Abanye abantu bangase babe nobunzima bokuphefumula noma ukubona okufiphele .
Yiziphi ezinye izinto ezithinta ukujiya kwegazi?
Kunezizathu eziningana zokuthi kungani igazi lakho lingaba likhulu. Igazi lakho lingaba likhulu uma amangqamuzana akho abomvu esesimweni esingajwayelekile . Lingaba likhulu futhi uma amazinga anoma yiziphi izingxenye zegazi lakho, njengamaseli abomvu egazi, amangqamuzana amhlophe egazi, noma amaprotheni egazini lakho, ephakeme ngendlela engajwayelekile .
Okokugcina, izinto okufanele uzikhumbule (Umyalezo Wokuya Ekhaya)
Kulungile, manje usuqonda kangcono lokho ebesikhuluma ngakho, "I-Hyperviscosity Syndrome." Khumbula, lokhu kwenzeka lapho igazi liqina futhi lingakwazi ukugeleza kahle emzimbeni wonke.
Lokhu kungenzeka kubantu abanezinkinga ezithile zegazi, kanye nasezinsaneni ezisanda kuzalwa ezinezifo ezithile zofuzo noma ezizuzwe njengefa.
Nakuba lesi kuyisimo esibucayi, uma sitholakale futhi selashwa kusenesikhathi, abantu abaningi bayalulama ngokuphelele. Ngakho-ke, uma wena noma ingane yakho ninezinkinga noma izimpawu, bonana nodokotela ngokushesha ukuze uthole iseluleko. Ungesabi, into ebaluleke kakhulu ukwaziswa.
Uma uneminye imibuzo, ungangabazi ukubuza udokotela wakho:
- Yini okungenzeka kakhulu ukuthi iyimbangela yalesi `(i-Hyperviscosity Syndrome)`?
- Yiziphi izivivinyo ezenziwayo ukuze kutholakale lokhu?
- Iphathwa kanjani?
- Ingabe kuzodingeka ngiqhubeke nokwelashwa?
- Uma nginenye ingane, kungenzeka yini ukuthi naye abe nalesi simo?
Buza imibuzo efana nale bese uxazulula zonke izinkinga engqondweni yakho.
I- Hyperviscosity syndrome, ukujiya kwegazi, izifo zegazi, izimpawu, ukwelashwa, impilo yengane, impilo yabantu abadala

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