Wake wazizwa sengathi amhlophe amehlo akho nesikhumba sakho aphenduka abe phuzi kancane? Kuyesabeka kancane ukubona lokho, akunjalo? Ungase ucabange ukuthi uhlobo oluthile lwesifo sesibindi. Esinye isizathu esingaba khona salokhu yisimo esibizwa ngokuthi i-Gilbert's syndrome. Kodwa ungesabi uma uzwa igama, aliyona ingozi njengoba ungase ucabange. Eqinisweni, kuyisimo sofuzo kunokuba yisifo.
Kalula nje, iyini i-Gilbert's syndrome?
I-Gilbert's syndrome iyisimo esivame kakhulu esithinta imindeni yethu, okungukuthi, siwufuzo. Umuntu onalesi sifo unomkhiqizo omningi kakhulu obizwa ngokuthi i-bilirubin egazini lakhe.
Manje cishe uyazibuza ukuthi iyini i-bilirubin. Kulula kakhulu. Amaseli abomvu egazi emzimbeni wethu nawo anesikhathi sokuphila. Uma leso sikhathi sokuphila sesiphelile, ayaphuka. I-Bilirubin iyi-pigment ephuzi, noma umkhiqizo ongcolile, owakheka lapho amaseli abomvu egazi ephuka. Ngokuvamile, isibindi sethu sithatha le bilirubin, siyicubungule, bese siyisusa emzimbeni nge-bile.
Kodwa kubantu abane-Gilbert's syndrome, isibindi asikhiqizi ngokwanele i-enzyme ekhethekile eyenza lo msebenzi. Ngakho-ke i-bilirubin ayikwazi ukusulwa ngokuphelele, futhi enye yayo ihlala egazini. Lapho izinga le-bilirubin egazini landa, ngezinye izikhathi amehlo nesikhumba kuba phuzi. Lokhu sikubiza nangokuthi i-jaundice .
Into ebalulekile ukuthi i-Gilbert's syndrome ayiyona ingozi. Ayidingi ukwelashwa. Ngeke ibangele umonakalo wesikhathi eside empilweni yakho.
Iyini imbangela yalesi simo?
Lokhu kungenxa yomehluko omncane ezizakhini zethu zofuzo. Njengoba nje sizuza izinto ezifana nombala wesikhumba kanye nokuthungwa kwezinwele kubazali bethu, nalokhu kuyiqiniso.
Kukhona isakhi sofuzo emzimbeni wethu esibizwa ngokuthi i-UGT1A1 . Lesi sakhi sofuzo sisiyala ukuba senze i-enzyme yesibindi engikhulume ngayo ekuqaleni ehlanza i-bilirubin. I-Gilbert's syndrome ibangelwa ukuguquka okuncane kwalesi sakhi sofuzo.
Ukuze ube nalesi simo, udinga amakhophi amabili esakhi sofuzo esiguquliwe. Lokhu kusho ukuthi kufanele uthole isakhi sofuzo kumama wakho nakubaba wakho . Kodwa-ke, noma ngabe unazo zombili izakhi zofuzo, akuwona wonke umuntu ozobonisa izimpawu ze-Gilbert's syndrome. Futhi, lesi simo sivame kakhulu kwabesilisa kunakwabesifazane.
Ziyini izimpawu ze-Gilbert's syndrome?
Eqinisweni, abantu abaningi abane-Gilbert's syndrome abanazo nhlobo izimpawu . Banama-enzyme esibindi anele ukulawula amazinga e-bilirubin emizimbeni yabo.
Uphawu oluyinhloko futhi ngezinye izikhathi uphawu olulodwa kuphela ukuba phuzi kwamehlo nesikhumba, okwaziwa ngokuthi i-jaundice. Uma uzwa ukuba phuzi kwamehlo, kubalulekile ukubona udokotela ukuze akuhlole , njengoba kungase kube nezinye izimbangela.
Abanye abantu bangase babe nezimpawu ezilandelayo kanye nokuphuzi kwamehlo:
- Ukuhlanza kanye nokuphazamiseka kwesisu
- Ukungakhululeki kwesisu
- Ukuzizwa ukhathele kakhulu (ukukhathala)
- Umchamo omnyama
Kungani amehlo ami ephenduka aphuzi ngezinye izikhathi kuphela, hhayi njalo?
Lona umbuzo omuhle. Kunezinto ezithile ezingabangela amazinga ethu e-bilirubin ukuba akhuphuke. Yilapho sivame ukubona khona ukuphuzi kwamehlo.
| Amacala lapho amazinga e-bilirubin enyuka khona futhi kungase kube khona i-jaundice | |
|---|---|
| Ukucindezeleka | Ngenxa yezivivinyo, izinkinga emsebenzini, njll. |
| Ukuphelelwa amanzi emzimbeni | Ukungaphuzi amanzi anele umzimba. |
| Ukweqa ukudla | Ukungadli isidlo sasekuseni noma sasemini. |
| Ukuzivocavoca ngokweqile | Ukwenza ukuzivocavoca okunzima kakhulu, njengokugoba phansi. |
| Izimo ezithathelwanayo | Uma uthola isifo esifana nomkhuhlane noma umkhuhlane. |
| Ukuphuza utshwala | Utshwala bubeka umthwalo owengeziwe esibindini. |
| Eminye imithi | Ukuthatha imithi ethile ethinta isibindi. |
| Ukuya esikhathini kwabesifazane | Ngezinsuku zomjikelezo wokuya esikhathini wanyanga zonke. |
Ungasibona kanjani lesi simo?
Nakuba i-Gilbert's syndrome iyisimo sokuzalwa, ivame ukutholakala kubantu abaneminyaka engu-20 noma engu-30. Nalokho kwenzeka ngengozi.
Ake sithi uhlolwa igazi ngesizathu esithile. Udokotela wakho ube esebona ukuthi izinga le-bilirubin egazini lakho liphakeme kancane kunokuvamile. Khona-ke angase asole ukuthi unesifo sikaGilbert.
Bese, ukuqinisekisa ukuthi azikho ezinye izifo zesibindi eziyingozi, udokotela angenza izivivinyo eziningana, njengokuthi:
- Ukuhlolwa Kokusebenza Kwesibindi (LFT): Lokhu ukuhlolwa kwegazi okuvamile.
- I-Ultrasound Yesibindi: Ukuhlola ezinye izinkinga zesibindi.
- Ukuhlolwa Kwezakhi Zofuzo: Qinisekisa ukuthi une-UGT1A1 gene mutation.
- Ukuhlolwa Kwesibindi: Lokhu akwenziwa njalo.
Ukwelashwa nalokho esingakwenza thina ngokwethu
Izindaba ezinhle ukuthi abantu abaningi abane-Gilbert's syndrome abadingi ukwelashwa , futhi ukuphuzi kwamehlo akho ngeke kukubangele izinkinga zesikhathi eside.
Ngakho-ke okudingeka sikwenze ukuhlala kude ngangokunokwenzeka nezinto engizikhulumile ekuqaleni ezikhulisa amazinga e-bilirubin.
- Ungayeki ukudla, ikakhulukazi uma uzila ukudla.
- Phuza amanzi amaningi kanye noketshezi. Ungavumeli umzimba wakho uphelelwe amanzi emzimbeni.
- Lawula ukucindezeleka. Yenza okuthile okuphumuzayo njengokuzindla, ukulalela umculo, noma ukuzibandakanya entweni oyithandayo.
- Lala kahle. Lala okungenani amahora angu-7-8 ngosuku.
- Nciphisa noma uyeke ngokuphelele ukuphuza utshwala .
- Gwema ukuzivocavoca okunzima. Ukuzivocavoca okulingene kulungile, kodwa ungazicindezeli ngaphezu kwemingcele yakho.
Okudingeka ukwazi uma uthatha imithi!
Lokhu kubaluleke kakhulu. Uma unesifo sikaGilbert, kudingeka uqaphele lokhu ngaphambi kokuthatha noma yimuphi umuthi omusha.
I-enzyme efanayo ehlanza i-bilirubin esibindini sethu iyasiza nasekuhlukaniseni nasekususeni eminye imithi emzimbeni. Ngakho-ke, ngenxa yokuthi unesifo sikaGilbert, umsebenzi waleyo enzyme uyancipha kancane. Ngakho-ke, uma uthatha imithi enjalo, iqoqana emzimbeni ngokweqile.Ingozi yemiphumela emibi iphezulu.
Isibonelo, bheka le mithi:
- I-Acetaminophen - (Iqukethe i-Panadol, i-Paracetamol)
- I-Irinotecan - umuthi osetshenziselwa ukwelapha umdlavuza
- Eminye imithi ye-HIV kanye ne-hepatitis C (ama-Protease inhibitors)
Ngakho-ke, kungakhathaliseki ukuthi uthatha muphi umuthi omusha, qiniseka ukuthi utshela udokotela wakho ukuthi unesifo sikaGilbert. Angakunikeza umuthi ophephile ofanele wena. Ungalokothi uthathe noma yimuphi umuthi udokotela angakawuniki noma uphuze ngaphezu komthamo onconywayo.
Umlayezo Wokuya Nawe Ekhaya
- I-Gilbert's syndrome iyisifo esivamile, esingeyona ingozi, esidluliselwa ngofuzo. Akusona isifo okufanele sesatshwe.
- Amehlo nesikhumba kuba phuzi (i-jaundice) ngenxa yamazinga aphezulu e-bilirubin egazini. Lokhu kuvame ukubangelwa ukucindezeleka noma ukugula.
- Akukho ukwelashwa okuqondile okudingekayo kulokhu. Into engcono kakhulu ongayenza ukugwema izinto ezandisa amazinga e-bilirubin.
- Okubaluleke kakhulu: Uma unesifo sikaGilbert, qiniseka ukuthi utshela udokotela wakho ngaphambi kokuthatha noma yimuphi umuthi omusha.











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