So woahu anaa woate tebea bi a nnipa binom, titiriw mmofra nkumaa, tew mogya a ano yɛ den mpofirim, wɔte nka sɛ wɔabrɛ paa, na ɛtɔ mmere bi a ebetumi de wɔn nkwa ato asiane mu pɛn? Ɛno yɛ tebea horow a anibere wom a yɛrebɛka ho asɛm nnɛ no mu biako, a wɔfrɛ no aplastic crisis . Ɛwom sɛ ebia edin yi bɛyɛ te sɛ nea ɛyɛ hu kakra de, nanso sɛ yenim a, yebetumi agyina tebea yi ano yiye.
Dɛn ankasa ne saa aplastic ahokyere yi?
Sɛ yɛbɛka no tiawa a, aplastic crisis yɛ bere a nnompe mu ntini a ɛwɔ yɛn nipadua mu no gyae mogya mu nkwammoaa kɔkɔɔ foforo a ɛyɛ mpofirim no . Afei ebia woresusuw sɛ, "Enti sɛ mogya mu nkwammoaa kɔkɔɔ a wɔyɛ no gyae a, dɛn na ɛba?" Saa mogya mu nkwammoaa kɔkɔɔ yi na ɛde mframa pa kɔ yɛn nipadua mu nyinaa. Enti sɛ wogyae awo a, mogya mu nkwammoaa kɔkɔɔ dodow a ɛwɔ nipadua no mu no so tew kɛse, na ɛde mogya a ɛtɔ kɔ nipadua no mu kɛse ba . Eyi yɛ tebea a ebetumi de nkwa ato asiane mu.
Mpɛn pii no aplastic ahokyere ka nnipa a wɔwɔ mogya mu yare te sɛ sickle cell anemia . Nea ɛde eyi ba titiriw ne ɔyare mmoawa a wɔtaa nya a wɔfrɛ no Parvovirus B19 . Mma ɛnnyɛ wo nwonwa, ɛwom sɛ saa mmoawa yi ka nnipa pii de, nanso aplastic crisis ba bere a nnipa a wɔwɔ mogya mu haw no nya saa mmoawa yi nkutoo. Saa tebea yi taa ba mmofra nkumaa mu, titiriw nkokoaa. Nanso asɛmpa bi wɔ hɔ, ayaresa ahorow bi wɔ hɔ a wɔde sa eyi te sɛ mogya a wɔde ma ne immunoglobulin a wɔde fa ntini mu (IVIG) .
So eyi yɛ yare a ɛka obiara?
Dabi, ɛnte saa koraa. Sɛnea madi kan aka no, Parvovirus B19 yɛ mmoawa a abu so yiye. Nanso, ɛnyɛ obiara a ɔwɔ saa mmoawa yi na onya aplastic crisis. Eyi ba bere a obi a ɔwɔ mogya mu yare pɔtee bi anya Parvovirus B19 nkutoo.
Nkokoaa a wɔawo wɔn foforo, nkokoaa, ne mmofra a mogya atɔ wɔn wɔ sickle cell mu titiriw na wɔwɔ asiane mu. Nnipa a wɔwɔ tebea afoforo a ɛma mogya mu nkwammoaa kɔkɔɔ sɛe ne mogya a ɛtɔ kɔ mogya mu a ɛma mogya tu no nso wɔ asiane kɛse mu sɛ sɛ wonya parvovirus B19 a, wobenya aplastic ahokyere. Tebea horow yi bi ne:
- Awosu mu Spherocytosis
- Hemoglobin C yare no
- Thalassemia a ɛwɔ nipadua no mu
- G6PD a enni nipadua mu ho yare
- Pyruvate Kinase a enni nipadua no mu
- Autoimmune Hemolytic Mogya a Ɛma Nnipa Nyinaa
- Paroxysmal Anadwo Hemoglobinuria a ɛma mogya tu
- Elliptocytosis a wonya fi awo mu
Sɛ wo anaa wo ba wɔ mogya mu yare a ɛte sɛɛ a, ɛho hia paa sɛ wohwɛ eyi so titiriw.
Dɛn ne aplastic ahokyere ho sɛnkyerɛnne?
Mpɛn pii no, mpanyimfo, ne mmofra ne nkokoaa a wɔwɔ aplastic haw no taa nya sɛnkyerɛnne ahorow a ɛfa mogya a ɛtɔ kɔ nipadua mu a emu yɛ den ho. Ebia nkokoaa ne mmofra nkumaa bɛyɛ basabasa anaasɛ wɔn bo afuw sen sɛnea wɔtaa yɛ no. Sɛ nhwɛso no, sɛ wo ba no resu pii, n’ani nnye biribiara ho, anaa ɛte sɛ nea ne bo fuw bere nyinaa a, eyi betumi ayɛ biribi a ɛte sɛɛ ho sɛnkyerɛnne.
Nsɛnkyerɛnne atitiriw no bi ni:
- Ɔbrɛ: Ɔbrɛ a ɛtra so, a ontumi nyɛ hwee.
- Atiridii: Nipadua mu hyew betumi adu digrii Celsius 38 (digrii Fahrenheit 101) anaa nea ɛboro saa.
- Adwene a ɛyɛ wo yaw: Ɛte sɛ nea wo ti twitwa, na w’ani betumi ayɛ bruu mpo.
- Ahome a ɛyɛ tiaa / ahome a ɛyɛ den: Ahome a ɛyɛ tiaa mpo bere a woretu kakra, ɔbrɛ kɛse nka bere a woreforo antweri no.
- Koma a ɛbɔ a ɛnteɛ anaasɛ ɛbɔ ntɛmntɛm: Ebia koma no bɔ ntɛmntɛm sen sɛnea ɛte daa, anaasɛ ebia ɛremmɔ koraa, nanso ebetumi ayɛ nea ɛnbɔ daa.
- Pallor: Wora, anofafa, anom, anaa nnadewa no yɛ fitaa sen sɛnea ɛtaa yɛ. Eyi ne kɔla a wohu bere a mogya nni hɔ no.
Sɛ wuhu saa sɛnkyerɛnne ahorow yi mu biako anaa nea ɛboro saa, titiriw sɛ wo anaa wo ba wɔ mogya mu yare bi a, ɛho hia yiye sɛ wohwehwɛ aduruyɛfo afotu ntɛm ara .
Dɛn nti na aplastic ahokyere yi ba? Dɛn na ɛde ba?
Asɛmfua "aplastic" kyerɛ sɛ biribi a ɛwɔ wo nipadua mu agyae adwumayɛ. Ɛno ne nea ɛkɔ so wɔ aplastic ɔhaw yi mu. Wo nnompe mu ntini ntumi mma mogya mu nkwammoaa kɔkɔɔ a ɛte apɔw. Nea enti a ɛte saa ne Parvovirus B19 a madi kan aka ho asɛm no. Saa mmoawa yi de n’ani si mogya mu nkwammoaa kɔkɔɔ a ennyinii a ennya nnyinii no so tẽẽ. Ɛsɛe wɔn.
Yɛn nipadua no nya nneɛma te sɛ mogya mu nkwammoaa kɔkɔɔ, mogya mu nkwammoaa fitaa bi, ne plasma fi nnompe mu. Enti sɛ mogya mu nkwammoaa kɔkɔɔ a ɛkɔ so yɛ no gyae a, wunya mogya a ɛtɔ kɔ wo mu a emu yɛ den . Fa no sɛ, eyi ne nea ɛba bere a yɛn nipadua mu mogya adwumayɛbea no gyae adwumayɛ mpofirim no.
Dɛn ne nsɛnnennen a ebetumi afi tebea yi mu aba?
Aplastic ahokyere betumi de nsɛnnennen ahorow aba, titiriw wɔ nnipa a wɔwɔ sickle cell anemia mu . Eyinom nso yɛ aniberesɛm paa.
- Vaso-occlusive crisis (VOC) a ɛkyɛ:VOC yɛ ɛyaw a emu yɛ den mpofirim a ɛba nnipa a wɔwɔ sickle cell anemia so. Saa ɛyaw yi betumi akyɛ esiane aplastic ahokyere nti.
- Myocarditis: Eyi yɛ koma ntini a ɛyɛ hyew, na ɛyɛ tebea a ɛte sɛ nea ɛho ahonhon.
- Splenetic sequestration: Mogya mu nkwammoaa kɔkɔɔ a ɛnyɛ ne kwan so no kyere wɔ ahurututu no mu, na ɛma akyi berɛmo no yɛ kɛse.
- Glomerulonephritis: Eyi yɛ asaabo mu yare a sɛ wɔansa no yiye a, ebetumi ama asaabo no ayɛ adwuma yiye.
Ɛno nti na yɛka sɛ ɛho hia paa sɛ yɛma yɛn ani da hɔ wɔ saa tebea yi ho.
Ɔkwan bɛn so na nnuruyɛfo hu eyi?
Sɛ wo anaa wo ba da saa nsɛnkyerɛnne yi adi a, sɛ wokɔ oduruyɛfo nkyɛn a, obedi kan abisa wo wo sɛnkyerɛnne ahorow no ho asɛm. Afei ɔbɛyɛ nipadua mu nhwehwɛmu. Nea ɛka ho no, wobetumi ayɛ nhwehwɛmu ahorow pii de asi tebea no so dua:
- Mogya Dodow a Edi Mu (CBC): Eyi hwɛ mogya mu nkwammoaa kɔkɔɔ, mogya mu nkwammoaa fitaa, ne mogya mu nkwammoaa dodow a ɛwɔ nipadua no mu. Wɔ aplastic ahokyere mu no, mogya mu nkwammoaa kɔkɔɔ dodow sua koraa.
- Reticulocyte dodow: Reticulocytes yɛ mogya mu nkwammoaa kɔkɔɔ a ennyinii. Saa nhwehwɛmu yi kyerɛ mogya mu nkwammoaa kɔkɔɔ foforo dodow a nnompe mu ntini no reyɛ. Wɔ aplastic ahokyere mu no, dodow yi nso sua koraa.
- Parvovirus B19 nhwehwɛmu: Wɔyɛ nhwehwɛmu yi de kyerɛ sɛ woanya saa mmoawa yi anaa.
Wɔ nhwehwɛmu ahorow yi akyi no, oduruyɛfo no betumi ahu no yiye sɛ ebia eyi yɛ aplastic ahokyere ampa anaa biribi foforo.
Dɛn ne ayaresa ahorow a wɔde sa eyi?
Ayaresa titiriw a wɔde sa aplastic ahokyere ne mogya a wɔde ma . Eyi kyerɛ sɛ wɔde mogya fi abɔnten bɛma. Eyi betumi ama nipadua no mogya mu nkwammoaa kɔkɔɔ dodow a ɛba fam no asan aba ntɛm. Nea ɛka ho no, wɔde aduru bi a wɔfrɛ no Intravenous Immunoglobulin (IVIG) ma. Wɔnam ntini bi so de eyi kɔ nipadua no mu (IV).
Ayarefo dodow no ara ho tɔ wɔn wɔ nnafua 10 kosi 14 akyi bere a wɔafi ayaresa ase no. Ade foforo a eye ne sɛ, sɛ obi nya parvovirus B19 pɛ a, onya ahoɔden a ɛko tia mmoawa no nkwa nna nyinaa. Eyi kyerɛ sɛ asiane a ɛwɔ hɔ sɛ obi benya aplastic crisis afi mmoawa no mu bio no so tew kɛse.
So ɔkwan bi wɔ hɔ a wɔbɛfa so asiw aplastic ahokyere ano?
Nokwarem no, ɛyɛ den kakra sɛ wobɛka. Efisɛ, aplastic crisis ba bere a obi a ɔwɔ mogya mu yare anya parvovirus B19 no . Parvovirus B19 yɛ mmoawa a abu so yiye, na wonnya nnyaa nnuru a wɔde ko tia no.
Nanso, wo ne wo ba no famSɛ wowɔ mogya mu yare te sɛ sickle cell anemia a, ɛho hia sɛ wubisa wo duruyɛfo nea wubetumi ayɛ de atew asiane a ɛwɔ hɔ sɛ wubenya parvovirus B19 no so. Sɛ nhwɛso no, nneɛma a ɛnyɛ den te sɛ twe a wobɛtwe wo ho afi mmeae a nnipa ahyɛ hɔ ma ne nsa a wobɛhohoro mpɛn pii no betumi ama woabɔ wo ho ban kakra.
Dɛn na ɛbɛba wɔ tebea yi akyi? (Nkɔmhyɛ) .
Nkɔmhyɛ ne nea wɔhwɛ kwan sɛ ebefi wo tebea no mu aba. Mpɛn pii no, nnipa a wɔwɔ aplastic ahokyere no ho tɔ wɔn wɔ nnafua 10 kosi 14 akyi bere a wɔafi ayaresa ase no. Nanso, ebia nnipa binom benya aplastic haw ahorow a ɛsan ba bio. Enti, ɛho hia sɛ wohwɛ yare no ho sɛnkyerɛnne ahorow no yiye na wudi wo duruyɛfo akwankyerɛ akyi.
Ɔkwan bɛn so na ɛsɛ sɛ mehwɛ me ho? / Ɔkwan bɛn so na ɛsɛ sɛ mehwɛ me ba?
Aplastic ahokyere yɛ nsɛnnennen pii a ebetumi aba wɔ mogya mu nyarewa te sɛ sickle cell anemia mu no mu biako pɛ . Ebia worentumi nsiw parvovirus B19 ano, nanso nneɛma bi wɔ hɔ a wubetumi ayɛ de akura w’akwahosan nyinaa mu:
- Kɔhwɛ wo daa: Sɛ wo ne wo duruyɛfo titiriw di nkitaho daa a, wubetumi ahu aduruyɛ mu nsɛnnennen a emu yɛ den ansa na aba.
- Tew asiane a ɛwɔ hɔ sɛ wubenya ɔyare no so: Wo ne wo duruyɛfo nkasa mfa akwan a wobɛfa so abɔ wo ho ban afi nyarewa a ɛtaa ba te sɛ atiridii ne atiridiinini ho.
- Di aduan a ahoɔden wom: Di aduan a ɛkari pɛ na nom nsu bɛyɛ nkuruwa 8-10 da biara.
- Apɔw-mu-teɛteɛ: Apɔw-mu-teɛteɛ a wobɛyɛ no daa betumi ama w’adwene ne w’akwahosan atu mpɔn. Nanso, fa no brɛoo, gye w’ahome bere a wote nka sɛ woabrɛ no, na kae sɛ wobɛnom nsu pii.
Saa nneɛma yi boa ma wo nipadua no mu tumi a ɛko tia nyarewa no yɛ den na ɛboa ma wotra apɔwmuden wɔ ɔkwan a ɛkɔ akyiri so.
Bere bɛn na ɛsɛ sɛ mekɔ oduruyɛfo nkyɛn?
Aplastic ahokyere yɛ aduruyɛ mu asɛm a egye ntɛmpɛ.
Sɛ wo anaa wo ba wɔ mogya mu yare bi te sɛ sickle cell anemia , na wuhu nsakrae mpofirim wɔ w’akwahosan mu, te sɛ mmerɛwyɛ anaa ɔbrɛ kɛse a wobɛte nka a, ɛsɛ sɛ wokɔ wo duruyɛfo nkyɛn ntɛm ara, a wontwentwɛn wo nan ase. Dodow a wufi ayaresa ase ntɛm no, dodow no ara na eye.
Nsɛm bɛn na ɛsɛ sɛ mibisa oduruyɛfo no?
Sɛ wo anaa wo ba wɔ aplastic crisis a, wubetumi abisa wo duruyɛfo nsɛm te sɛ eyinom:
- Bere bɛn na me/me ba no ho bɛtɔ me?
- Hokwan bɛn na ɛwɔ hɔ sɛ me/me ba no benya ɔhaw te sɛ eyi bio?
- Nneɛma bɛn na ɛsɛ sɛ mehwɛ yiye wɔ ho titiriw bere a me ne tebea yi te no?
Ɛho hia yiye sɛ wubebisa nsɛm te sɛ eyinom na woayi w’adwenem naayɛ no afi hɔ.
So aplastic crisis ne aplastic anemia yɛ ade koro?
Yiw, ɛwom sɛ tebea abien yi nyinaa ne mogya mu nkwammoaa kɔkɔɔ dodow a ɛso tew wɔ abusuabɔ de, nanso nsonsonoe da abien no ntam.
Aplastic crisis yɛ mogya mu nkwammoaa kɔkɔɔ dodow a ɛkɔ fam mpofirim .
Aplastic anemia yɛ tebea a ɛkɔ so nkakrankakra bere a bere kɔ so no. Wɔ eyi mu no, ɛnyɛ mogya mu nkwammoaa kɔkɔɔ nko na ebetumi atew, na mmom mogya mu nkwammoaa afoforo (mogya mu nkwammoaa fitaa, mogya mu nkwammoaa) nso betumi atew.
Sɛ yɛbɛka no tiawa a, Aplastic Crisis yɛ bere tiaa mu ɔhaw a emu yɛ den. Aplastic Anemia yɛ ɔhaw a ɛtra hɔ kyɛ, a ɛfa nnompe mu ntini pɔtee bi ho.
Awiei koraa no, nkrasɛm a wɔde kɔ fie
Okay, enti mewɔ anidaso sɛ seesei woanya ntease pa wɔ nea yɛkaa ho asɛm nnɛ, Aplastic Crisis no ho. Eyi yɛ ɔhaw a emu yɛ den a ebetumi aka nnipa a wɔwɔ mogya mu nyarewa te sɛ Sickle Cell Anemia . Nea ɛba ne sɛ wo anaa wo ba no nnompe mu ntini no gyae mogya mu nkwammoaa kɔkɔɔ a ɛba mpofirim, na ɛde mogya a ɛtɔ kɔ nipadua mu a emu yɛ den a ebetumi de ne nkwa ato asiane mu ba.
Aplastic ahokyere betumi ayɛ osuahu a ɛyɛ hu efisɛ sɛnkyerɛnne ahorow no betumi aba mpofirim na ayɛ kɛse. Nea eye ne sɛ, nnuruyɛfo betumi de mogya ne nnuru asa.
Sɛ wo anaa wo ba wɔ mogya mu yare bi a ɛma wo anaa wo ba no wɔ asiane kɛse mu sɛ wobenya aplastic crisis a, bisa wo duruyɛfo no sɛnkyerɛnne ahorow a ebetumi akyerɛ sɛ ɔhaw bi wɔ hɔ. Ebia worentumi nsiw aplastic ahokyere ano, nanso sɛ ɛba a, wubehu nea ɛsɛ sɛ woyɛ. Saa nhumu no ne ade a ɛho hia sen biara.
👩🏽 ⚕️ Nsɛmmisa foforo (FAQs)
💬 Dɛn ne Aplastic Crisis?
Wɔyɛ yɛn nipadua mu mogya mu nkwammoaa kɔkɔɔ no wɔ nnompe mu. Esiane biribi nti, titiriw wɔ ɔyare mmoawa (te sɛ Parvovirus B19) akyi no, mogya mu nkwammoaa kɔkɔɔ a ɛba mpofirim wɔ yɛn nnompe mu ntini mu nna pii no, wɔfrɛ no ‘aplastic crisis’.
💬 Sɛ nipadua no gyae mogya yɛ mpofirim a, dɛn na ɛba ɔyarefo no so?
Mogya mu nkwammoaa kɔkɔɔ de mframa pa kɔ nipadua no mu nyinaa. Sɛ wogyae a, ɔyarefo no nya mogya a ɛtɔ kɔ nipadua no mu denneennen. Anofafa, nnadewa, ne honam ani yɛ fitaa koraa (yɛ mmerɛw), koma no bɔ kɛse, anaasɛ ɔyarefo no ntumi nhu mpofirim esiane sɛ ɛyɛ den sɛ ɔbɛhome nti.
💬 Ayaresa bɛn na wɔde ma nnipa te sɛ yei, titire mmofra?
Saa tebea yi yɛ nea asiane wom kɛse ma mmofra a wɔwɔ sickle cell yare no. Sɛ wɔde wo kɔ ayaresabea esiane tebea yi nti a, ayaresabea no bɛma wo mogya ntɛm ara. Mpɛn pii no, wɔ mogya a wɔde ma yi akyi no, nnompe mu ntini no fi ase yɛ mogya sɛnea ɛsɛ bio wɔ bɛyɛ nnafua 10 kosi 14 mu.
` Aplastic Ahokyere, Mogya Nkwammoaa Kɔkɔɔ, Nnompe mu Ntini, Mogya a Wɔyare, Parvovirus B19, Sickle Cell Mogya Mu











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