Na sɛ wɔannya komayare bi a wɔde awo obi no yare nso ɛ? Sua Eisenmenger Syndrome ho ade

So woate sɛ wɔwo nkokoaa a tokuru wɔ wɔn koma mu pɛn? Mpɛn pii no, sɛ wɔsa no ntɛm a, eyi nyɛ ɔhaw. Nanso, ɛtɔ mmere bi a, sɛ wɔansa tebea horow yi a, ebetumi abɛyɛ nsɛnnennen a emu yɛ den yiye bere a bere kɔ so no. Ɛno ne nea yɛfrɛ no Eisenmenger Syndrome. Ɛwom sɛ eyi yɛ asɛmti a ɛyɛ den kakra de, nanso yɛbɛka ho asɛm tiawa koraa nnɛ, wɔ ɔkwan a wubetumi ate ase so.

Sɛ yɛbɛka no tiawa a, dɛn ne Eisenmenger yare no?

Sɛ yɛbɛte eyi ase a, momma yenni kan nkae sɛnea koma no yɛ adwuma. Fa no sɛ yɛn koma te sɛ ofie a ɛwɔ adan anan. Pia abien a ɛwɔ soro ne adan abien a ɛwɔ fam. Mogya "a ɛho agu fĩ" a akɔ so adi akɔneaba wɔ nipadua no mu nyinaa, a oxygen kakraa bi na ɛwom wɔ koma no nifa so . Ɛsɛ sɛ "wɔtew" mogya yi ho denam nea wɔde bɛkɔ ahurututu no mu ma wɔanya oxygen no so. Mogya "a ɛho tew" a akɔ so afi ahurututu no mu, a oxygen ahyɛ mu ma wɔ koma no benkum so. Wɔde mogya yi kɔ nipadua no mu nyinaa. Mpɛn pii no, mogya nfrafra afã abien yi ntam.

Afei, fa no sɛ wɔawo wo a tokuru bi wɔ ɔfasu no mu wɔ koma no mu adan ntam (sɛ nhwɛso no). Nhyɛso a ɛwɔ koma no benkum so no dɔɔso sen nea ɛwɔ nifa so no. Enti, wɔ mfiase no, mogya a oxygen pii wom no bi fa saa tokuru no mu kɔ nifa so na ɛne mogya a oxygen nnim no fra. Yɛfrɛ eyi sɛ shunt a ɛkɔ benkum kɔ nifa . Eyi ma mogya dodow a ɛkɔ ahurututu mu no kɔ soro a ɛho nhia.

Awiei koraa no, nhyɛso a ɛwɔ ahurututu no mu no kɔ soro araa ma nhyɛso a ɛwɔ koma no nifa so no kɔ soro sen benkum so. Dɛn na ɛba saa bere no? Mogya a ɛsen no dan kɔ koraa. Ɛno kyerɛ sɛ seesei mogya "a ɛho agu fĩ" a oxygen sua no nkɔ ahurututu mu na wɔrehohoro ho, na mmom ɛrefa saa tokuru no mu tẽẽ akɔ benkum so na wɔrebɔ no akɔ nipadua no nyinaa mu. Yɛfrɛ eyi sɛ nifa so kɔ benkum so shunt .

Saa sɛnkyerɛnne ne nsɛnnennen a wɔaboaboa ano a mogya a oxygen nnim a wɔde kɔ nipadua no mu de ba yi ne nea yɛfrɛ no Eisenmenger Syndrome .

Dɛn ne tebea yi ho sɛnkyerɛnne?

Nsɛnkyerɛnne titiriw ne nea efi oxygen a ɛdɔɔso a wonnya nkɔ nipadua no mu (hypoxemia) mu ba. Saa sɛnkyerɛnne ahorow yi taa da adi wɔ mmerantebere ne mmabaabere anaa mpanyin afe so, nanso ɛtɔ mmere bi a ebetumi afi ase wɔ mmofraase.

Dɛn nti na eyi ba? Dɛn ne koma mu sintɔ ahorow a ɛhyɛ ase?

Sɛnea yɛadi kan aka ho asɛm no, komayare bi a wɔde awo obi a wɔansa no na ɛde tebea yi ba. Nhwɛso ahorow bi ni:

• Atrial septal defect ( ASD ): Tokuru a ɛwɔ ɔfasu no mu wɔ koma no atifi adan abien (atria) ntam.
• Ventricular septal dɛmdi ( VSD ): Ɔde ne nsa kyerɛɛ ne so.Tokuru a ɛwɔ ɔfasu no mu wɔ koma no ase adan (dan) abien no ntam.
• Patent ductus arteriosus (PDA): Nkitahodi a ɛnteɛ a ɛda aorta ne ahurututu mu ntini a ɛsɛ sɛ wɔto mu wɔ awo akyi.
• Atrioventricular septal defect: Tokuru kɛse bi a ɛwɔ koma no mfinimfini, ne ɔhaw ahorow a ɛwɔ koma no ntini ahorow mu .
• Single-ventricle defect: Koma no ase adan abien no mu biako pɛ na ɛyɛ adwuma yiye.

Nsɛnnennen afoforo a ebetumi aba esiane tebea yi nti:

Eisenmenger yare no nka koma ne ahurututu nkutoo. Oxygen a ɛba nipadua no mu a ɛba fam no betumi de nsɛnnennen afoforo pii aba.

• Erythrocytosis a ɛto so abien: Nipadua no ma mogya mu nkwammoaa kɔkɔɔ pii sen nea ehia na ɛde oxygen asi ananmu, na ebetumi ama mogya no ayɛ den na ama asiane a ɛwɔ hɔ sɛ mogya no bɛtɔ no ayɛ kɛse.
• Mogya a ɛtɔ a ɛnyɛ ne kwan so: Nneɛma te sɛ mogya a ɛfefe, hwene mu mogya, brayɛ a emu yɛ duru, ne anom a mogya tu.
• Koma a ɛbɔ a ɛnteɛ (Arrhythmias): Koma a ɛbɔ ntɛmntɛm.
• Mogya a ɛtwetwe: Sɛ mogya a ɛtwetwe yi kɔ amemene no mu a, tebea horow a emu yɛ den te sɛ akisikuru betumi aba.
• Amemene mu akisikuru.
• Nsateaa a wɔde nhama ayɛ.
• Asaabo dwumadi a asɛe.
• Koma a entumi nyɛ adwuma yiye.
• Koma mu yare (infective endocarditis).
• mogya a ɛtɔ kɔ nipadua mu a dade nnim.

Asiane kɛse wɔ nyinsɛn mu

Eyi yɛ asɛm a ɛho hia paa. Ɔbea a ɔwɔ Eisenmenger yare no nyinsɛn yɛ asiane kɛse, na ɛde ne nkwa mpo to asiane mu . Koma ne mogya a ɛkɔ nipadua no mu no ntumi nni adwennwen a ɛba bere a wɔyem no ho dwuma, na ɛno betumi ama ɛna no anaa akokoaa no awu, anaa n’abien nyinaa mpo.

Ɔkwan bɛn so na nnuruyɛfo hu eyi?

Ebia wo duruyɛfo begyina wo yare no ho sɛnkyerɛnne ne w’aduruyɛ ho abakɔsɛm so asusuw eyi ho. Wɔbɛyɛ sɔhwɛ ahorow pii de asi so dua.

• Mogya mu nhwehwɛmu:Sɛnea ɛbɛyɛ a wubesua mogya mu nkwammoaa kɔkɔɔ dodow ne nsɛnnennen afoforo ho ade.
• Echocardiogram (Echo): Scan a ɛhwɛ sɛnea koma no yɛ adwuma, sɛnea ɛte, ne baabi a tokuru no wɔ.
• Electrocardiogram (ECG/EKG): Sɛnea ɛbɛyɛ a wɔbɛhwɛ sɛnea anyinam ahoɔden yɛ adwuma ne sɛnea koma no yɛ adwuma.
• Koma mu Catheterization: Sɔhwɛ a ɛho hia yiye a ɛfa sɛ wɔde afiri ketewaa bi hyɛ koma no ne ahurututu mu de susuw nhyɛso a ɛwɔ hɔ no pɛpɛɛpɛ.
• Pulse oximetry: Wɔde afiri ketewaa bi a wɔde abata nsateaa ho susuw oxygen dodow a ɛwɔ mogya no mu.
• Apɔw-mu-teɛteɛ mu adwennwen sɔhwɛ: Sɛnea koma ne oxygen dodow sesa bere a wɔreyɛ apɔw-mu-teɛteɛ no a wɔbɛhwɛ.

Ɔkwan bɛn so na wɔsa? So wobetumi asa eyi?

Ade a ɛho hia sɛ yɛte ase wɔ ha ne sɛ, sɛ Eisenmenger yare no nya nya nkɔso wie a, wontumi mfa oprehyɛn nto koma mu dɛmdi (tokuru) a ɛde bae mfiase no mu . Sɛ wɔyɛ saa a, koma no rentumi nnyina nhyɛso kɛse a ayɛ kɛse wɔ ahurututu mu dedaw no ano, na nsɛnnennen a emu yɛ den yiye ne owu mpo betumi aba.

Enti, ayaresa botae atitiriw ne sɛ wobedi yare no ho sɛnkyerɛnne ahorow so, ama asetra atu mpɔn, na wɔasiw nsɛnnennen ano.

• Ahurututu mu mogya mmoroso (PAH) ayaresa: Eyinom ne ayaresa titiriw. Saa nnuru yi brɛ nhyɛso a ɛwɔ mogya ntini a ɛwɔ ahurututu mu no ase, na ɛma yare no ho sɛnkyerɛnne te sɛ ahome a ɛyɛ tiaa no fi hɔ.
• Nnuru a ekum ɔyare mmoawa: Wɔde nnuru a ekum ɔyare mmoawa ma ansa na wɔayɛ aduruyɛ bi te sɛ sẽ a woyi, na amma ɔyare mmoawa no antrɛw akɔ koma no mu.
• Apɔw-mu-teɛteɛ wɔ oduruyɛfo hwɛ ase: Eyi betumi aboa ma wo home ne w’ahoɔden atu mpɔn. Mma w’ankasa nteɛteɛ w’apɔw mu da a wonkɔ wo duruyɛfo nkyɛn.
• Iron pills anaa injections: Sɛ wɔde sa iron a enni nipadua mu sɛ ɛba a.
• Oxygen a wɔde ka ho: Wɔkamfo eyi kyerɛ ayarefo bi a wɔapaw wɔn na ama oxygen dodow a ɛwɔ mogya no mu atu mpɔn.
• Nnuru a ɛma mogya yɛ mmerɛw: Eyi yɛ biribi a ɛsɛ sɛ wɔde ahwɛyiye kɛse di dwuma na wogye nnuruyɛfo afotu nkutoo.
• Koma anaa koma ne ahurututu a wɔde ma: Ade a wobetumi apaw ama ayarefo a wɔawie a wontumi mfa nnuru nni wɔn tebea no so.

Ɔkwan bɛn so na ɛsɛ sɛ mehwɛ me ho?

Bere a wo ne tebea yi te ase no, nneɛma kakraa bi wɔ hɔ a ɛsɛ sɛ woyɛ.

• Kwati sigaretnom koraa. Eyi bɛma tebea no asɛe kɛse.
• Nom nsu pii na amma wo ho atɔ wo.
• Di aduan a ahoɔden wom.
• Nya nnuru a ɛho hia a wɔde bɔ wo ho ban wɔ bere ano na ama woabɔ wo ho ban afi ɔyare mmoawa ho.
• Adwennwen a ɛwɔ yare a ɛte saa a ɛtra hɔ kyɛ mu a wobedi ho dwumaNya afotu .

Wobɛtena komayare ho oduruyɛfo ne ahurututu ho oduruyɛfo hwɛ ase wo nkwa nna nyinaa, enti ɛho hia yiye sɛ wudi wɔn akwankyerɛ akyi pɛpɛɛpɛ.