Bere a oduruyɛfo no ka kyerɛɛ wo sɛ ɛsɛ sɛ wo ba kumaa no yɛ ‘Glenn’ oprehyɛn esiane komayare nti no, ɛbɛyɛ sɛ wotee ehu ne ahodwiriw kɛse nka. Ɛsɛ sɛ wunya nsɛmmisa pii wɔ w’adwene mu, te sɛ nea ɛyɛ ‘Glenn Procedure’, nea ɛka ho, ne nea enti a wɔreyɛ. Nha wo ho. Saa nkate ahorow no yɛ nea ɛfata koraa. Momma yɛnka eyinom nyinaa ho asɛm tiawa, wɔ ɔkwan a wubetumi ate ase so.
Sɛ yɛbɛka no tiawa a, dɛn ne Glenn Adeyɛ no?
Susuw ho hwɛ, yɛn koma ne motor a ɛma mogya fa nipadua no nyinaa mu. Ɛwɔ afã anan (dan anan). Wɔwo nkokoaa binom a saa adan yi mu biako nnyinii koraa anaasɛ ɛyɛ ketewaa koraa. Sɛ ɛba saa a, koma no ntumi mfa mogya nkɔ yiye.
Sɛ yɛbɛka no tiawa a, Glenn kwan no yɛ ‘bypass’ adeyɛ a ɛboa koma a ɛyɛ mmerɛw te sɛ eyi.
Ɛha no, nnuruyɛfo a wɔyɛ oprehyɛn no de mogya ntini titiriw (superior vena cava) a ɛde mogya a mframa pa nnim, a ɛho ntew fi akokoaa no atifi fam no kɔ ahurututu mu ntini no mu tẽẽ, sen sɛ wɔde bɛkɔ koma no mu.
Eyi te sɛ ɔkwan foforo a ɛnyɛ den sɛ wɔde bedi dwuma a woretwa kwan a nnipa pii fa so ho. Eyi ma mogya a ɛsɛ sɛ enya mframa pa no twa koma no fã a ɔhaw wom no ho na ɛkɔ ahurututu no mu tẽẽ.
Mpɛn pii no, eyi ne oprehyɛn a ɛto so abien a akokoaa yɛ. Wɔyɛ oprehyɛn foforo wɔ mfe kakraa bi akyi na ama wɔanya tebea no ano aduru a ɛtra hɔ daa.
Mmofra bɛn na wɔyɛ wɔn oprehyɛn yi?
Wɔyɛ Glenn oprehyɛn no wɔ mmofra a wɔde awo wɔn koma mu dɛmdi titiriw. Ɛho hia titiriw ma mmofra nkumaa paa, anaa wɔn a koma no mu adan atitiriw abien (ventricles) a ɛma mogya no mu biako nyɛ adwuma yiye no. Wɔfrɛ saa tebea yi ‘ventricle defect biako’.
Ase hɔ no yɛ komayare atitiriw a ɛhwehwɛ sɛ wɔyɛ Glenn oprehyɛn no bi.
| Komayare no din (Aduruyɛ Tebea) . | Nkyerɛkyerɛmu a ɛnyɛ den |
|---|---|
| Hypoplastic Koma Benkum mu Yare a Ɛyare | Koma no benkum (benkum so ventricle, valves) ntumi nkɔ yiye. |
| Tricuspid Atresia a ɛwɔ nipadua no mu | Tricuspid valve a ɛwɔ adan a ɛwɔ koma no nifa so no ntam no, wɔanhyehyɛ no yiye. |
| Ahurututu mu Atresia | Ahurututu mu ntini a ɛde mogya kɔ ahurututu mu no asiw. |
| Double Inlet Benkum anaa Nifa Ventricle | Koma no atifi adan abien (atria) no ka biako a ɛwɔ fam (venttricle) ho. |
Bere bɛn na wɔtaa yɛ Glenn oprehyɛn?
Nnuruyɛfo taa kamfo oprehyɛn yi kyerɛ bere a akokoaa no adi asram 3 kosi 6 no . Wɔtaa yɛ no sɛ oprehyɛn a ɛto so abien, bere a wɔayɛ akokoaa no oprehyɛn a edi kan de ama mogya no akɔ yiye (te sɛ Blalock-Taussig (BT) shunt) wɔ awo akyi.
Dɛn na ɛba ansa na wɔayɛ oprehyɛn ne bere a wɔreyɛ no oprehyɛn?
Ansa na wɔreyɛ no oprehyɛn
Ansa na wobɛyɛ oprehyɛn no, wo duruyɛfo no bɛyɛ nhwehwɛmu pii de ahwɛ sɛnea wo ba no koma te yiye.
- Cardiac Catheterization: Wɔyɛ sɔhwɛ yi de susuw nhyɛso ne oxygen dodow a ɛwɔ koma no mu na wɔhwɛ sɛnea koma no te.
- Koma MRI: Eyi boa ma wonya koma no ho mfonini a ɛkɔ akyiri a ɛwɔ afã abiɛsa.
- Ɛho hia yiye sɛ wobɛbɔ oduruyɛfo no amanneɛ wɔ nnuru (a vitamin ne nnuru a wɔde ma ka ho) a wo ba no renom nyinaa ho .
Bere a wɔreyɛ oprehyɛn no
Mpɛn pii no, c-section gye bɛyɛ nnɔnhwerew anan , nanso saa bere yi betumi ayɛ soronko a egyina akokoaa no tebea so.
Bere a wɔreyɛ oprehyɛn no, wɔma akokoaa no aduru a wɔde kum nipadua no, enti akokoaa no nte ɛyaw biara. Akokoaa no da kɛse. Wɔde mmofra binom bata afiri titiriw bi a egye koma ne ahurututu adwuma bere tiaa bi bere a wɔreyɛ oprehyɛn no ho. Wɔfrɛ eyi afiri a wɔde twa koma ne ahurututu mu . Afei, sɛnea yɛadi kan aka no, oduruyɛfo a ɔyɛ oprehyɛn no yɛ mogya ntini a ɛsan ka bom no ne koma no foforo siesie sɛ ɛho hia a.
Mfaso a ɛwɔ oprehyɛn mu ne asiane ahorow a ebetumi aba
Te sɛ oprehyɛn biara no, mfaso ne asiane ahorow wɔ Glenn oprehyɛn no so. Ɛho hia sɛ awofo hu eyinom.
| Mfaso a ɛwɔ so | Asiane/nsɛnnennen a ebetumi aba |
|---|---|
| Koma dan biako pɛ a ɛyɛ adwuma (ventricle) no mu duru a ɛso tew. | Oxygen dodow a ɛso tew wɔ mogya no mu. |
| Koma no a ɛrentrɛw esiane adwuma a ɛboro so nti a wosiw ano. | Mogya mmoroso. |
| Fontan oprehyɛn a ɛreba no bɛyɛ mmerɛw. | Pleural effusions a ɛma mogya tu. |
| Hokwan a ɛkɔ soro sɛ obegye abofra no nkwa wɔ Fontan oprehyɛn akyi. | Ɛsɛ sɛ wɔma wɔn aduan fa tube mu esiane adidi a ɛyɛ den nti. |
| Sɛ́ ɛbɛyɛ ɔkwan foforo a wɔbɛfa so ama mmofra a wonhia anaasɛ wontumi nyɛ Fontan oprehyɛn no. | Ɛsɛ sɛ wɔyɛ no oprehyɛn foforo. |
Ade a ɛho hia sen biara ne sɛ abofra no nkwagye dodow wɔ Glenn oprehyɛn no akyi no dɔɔso yiye. Ɛyɛ bɛyɛ 99% . Eyi yɛ oprehyɛn a edi mu yiye.
Dɛn na ɛba wɔ oprehyɛn no akyi?
Sɛ wɔyɛ oprehyɛn no wie a, wɔde akokoaa no bɛkɔ ayaresabea a wɔhwɛ wɔn a wɔyare denneennen (ICU). Ebia wobɛte ehu nka bere a wuhu sɛ wɔde nsu afiri ne nneɛma a wɔde hwɛ nneɛma so abata akokoaa no nipadua ho no. Nanso ɛno yɛ ade a ɛfata. Aduruyɛ kuw no bɛhwɛ akokoaa no so yiye.
Akokoaa no bɛtra baabi a wɔhwɛ wɔn a wɔyare denneennen no bɛyɛ nnansa, afei wɔde no bɛkɔ baabi a wɔhwɛ wɔn a wɔyare daa. Ebia ebegye adapɛn pii ansa na akokoaa no ho atɔ no koraa na wakɔ fie.
Mmofra pii, wɔ Glenn oprehyɛn no akyi mfe kakraa bi, bere a wofi ase nantew no, ebehia sɛ wɔyɛ anammɔn a edi hɔ, Fontan oprehyɛn , a ɛma koma no mogya a ɛkɔ nipadua no mu no ano aduru a ɛtra hɔ daa kɛse.
Bere bɛn na ɛsɛ sɛ wokɔ oduruyɛfo nkyɛn bere a woakɔ fie awie no?
Ɛho hia paa sɛ wohwɛ wo ba no yiye bere a woakɔ fie awie no. Sɛ wuhu sɛnkyerɛnne ahorow a edidi so yi mu biara a , frɛ wo duruyɛfo ntɛm ara.
- Sɛ akokoaa no nya atiridii a.
- Sɛ mogya anaa nsu foforo bi retu afi kuru a wɔayɛ no oprehyɛn no mu a.
- Sɛ ɛyɛ den ma wo sɛ wobɛnom nufusu a.
- Sɛ wowɔ ɔhaw bi a ɛfa wo mu duru a ɛkɔ soro ho a.
Ɛho behia sɛ wo ba no kɔ komayare ho ɔyaresafo ayaresabea na ɔnom nnuru bere tenten. Ɛno yɛ akwantu yi fã.
Nkrasɛm a Wɔde Kɔ Fie
- Glenn Adeyɛ no yɛ oprehyɛn a wɔayɛ ho nhyehyɛe, a ɛto so abien a wɔyɛ nkokoaa a wɔwɔ komayare a emu yɛ den a wɔde awo wɔn.
- Eyi kyerɛ sɛ wɔde mogya a oxygen nnim kɔ ahurututu no mu tẽẽ, twa koma no ho hyia, na ɛma adwuma a ɛwɔ koma no so no so tew.
- Oprehyɛn yi nkonimdi dodow yɛ kɛse yiye (bɛyɛ 99%). Enti mma nsuro.
- Sɛ wɔyɛ abofra no oprehyɛn wie a, ebehia sɛ oduruyɛfo hwɛ no bere tenten ne nnuru, enti ɛho hia paa sɛ odi oduruyɛfo no akwankyerɛ akyi.
- Wo ne wo duruyɛfo nka nsɛmmisa anaa ehu biara a wowɔ ho asɛm pefee. Wɔwɔ hɔ sɛ wɔbɛboa wo.











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