Fa no sɛ worehwɛ ahwehwɛ mu na woahu kwan tẽẽ bi a ɛkɔ w’anim mfinimfini, ɔfã biako yɛ kɔkɔɔ kɛse na fifiri ayɛ no, na ɔfã foforo no yɛ nea ɛfata, ebia ɛyɛ mmerɛw kakra... So ɛno nyɛ hu na ɛnyɛ nwonwa kakra? Anaasɛ sɛ wuhu sɛ wo ba a wɔawo no foforo no nipadua no fã biako dan kɔkɔɔ mpofirim na ɔfã foforo no yɛ nea ɛfata nso ɛ? Eyi ne nea yɛfrɛ no Harlequin Sign wɔ aduruyɛ mu. Esiane sɛ edin no yɛ nwonwa kakra nti, momma yɛnhwehwɛ ho nsɛm pii ne sɛ ebia eyi yɛ biribi a ɛsɛ sɛ yesuro ankasa anaa.
Dɛn ankasa ne Harlequin Nsɛnkyerɛnne yi?
Sɛ yɛbɛka no tiawa a, Harlequin Sign yɛ bere a wo nipadua anaa w’anim fã biako nya nsakrae wɔ honam ani kɔla mu (ɛyɛ kɔkɔɔ anaasɛ ɛyɛ tuntum), bere a ɔfã foforo no kɔ so yɛ pɛ, ɛtɔ mmere bi mpo a ɛyɛ mmerɛw. Ɛte sɛ nea wɔde nsensanee tẽẽ bi atew saa afã abien yi ntam, a ɛkɔ nipadua no mfinimfini pɛɛ.
Nea ɛka nsonsonoe a ɛwɔ honam ani kɔla mu yi ho no, wotumi hu nneɛma afoforo wɔ afã abien no nyinaa.
- Kɔkɔɔ: Saa beae yi betumi ayɛ hyperhidrosis (fifiri a ɛboro so). Ebia honam ani hwɛbea a ɛwɔ saa beae no nso bɛte nka sɛ ɛyɛ hyew kakra bere a wɔde wɔn nsa ka no.
- Pale/Normal Side: Saa ɔfã yi ntumi fifiri. Sɛ woka honam ani nso a, ɛbɛyɛ nwini.
Ɛwom sɛ ɛtɔ mmere bi a saa Harlequin Nsɛnkyerɛnne yi betumi ayɛ aduruyɛ tebea bi te sɛ `Harlequin syndrome` ho sɛnkyerɛnne de, nanso mpɛn pii no ɛnyɛ bɔne na ɛkɔ kɛkɛ.
Dɛn ne ade titiriw nti a ɛte saa?
Ɛnyɛ bere nyinaa na ɛyɛ yiye sɛ wubehu biribi pɔtee bi a ɛde eyi ba. Ade titiriw nti a eyi ba ne nkitahodi ho haw bi a ɛwɔ yɛn nipadua no ntini a ɛma ɛyɛ adwuma no mu. Fa eyi sɛ yɛn nipadua "auto-pilot" nhyehyɛe. Saa nhyehyɛe yi di nneɛma a yennim sɛ yɛwɔ so, te sɛ yɛn home, yɛn koma bɔ, ne yɛn fifiri.
Enti, sɛ ntini kwan a ɛde nkrasɛm fi amemene (hypothalamus) mu fa akyi berɛmo mu kɔ anim ne nipadua no atifi no mu a, ebia wɔremfa nkrasɛm no nkɔ nipadua no fã biako pɛ yiye. Eyi nti na mogya ntini a ɛwɔ ɔfã biako no trɛw na ɛdan kɔkɔɔ, bere a ɔfã foforo no nnya nkrasɛm no na ɛkɔ so yɛ nea ɛfata no.
So eyi to nkokoaa a wɔawo wɔn foforo nso?
Yiw, eyi yɛ biribi a wohu wɔ nkokoaa a wɔawo wɔn foforo mu. Sɛnea nhwehwɛmu ahorow kyerɛ no, nkokoaa a wɔwɔ apɔwmuden bɛyɛ 10% betumi anya saa Harlequin Nsɛnkyerɛnne yi. Enti, sɛ wo ba no wɔ eyi a, mma ɛnhaw wo.
Eyi taa ba wɔ akokoaa no awo akyi nna abien kosi anum, nanso ɛtɔ mmere bi a ebetumi aba akyiri adapɛn abiɛsa.
Ade a ɛho hia sen biara ne Harlequin Sign yi a nkokoaa a wɔawo wɔn foforo wɔ no.Ɛnyɛ asiane biara koraa. Saa kɔla a ɛsakra yi yera wɔ sikani 30 pɛ mu. Ɛtɔ mmere bi a, etumi di simma 20. Ebia ɛbɛsan apue bere a wɔde akokoaa no si n’afã no.
Nea ɛho hia yiye: Ɛnsɛ sɛ wɔde tebea a wɔfrɛ no Harlequin Sign yi frafra `Harlequin ichthyosis`, awosu mu tebea a ɛyɛ hu yiye, ɛde nkwa to asiane mu na ɛntaa nsi koraa. `Harlequin ichthyosis` yɛ tebea a ɛma akokoaa no nipadua nyinaa kata nsenia a ɛyɛ den a ɛte sɛ mprɛte so, na mpaapaemu a emu dɔ wɔ ntam. Ɛyɛ biribi soronko koraa.
Nyarewa afoforo a ɛbata ho
Ɛtɔ mmere bi a Harlequin Sign no betumi ada adi sɛ aduruyɛ mu tebea afoforo ho sɛnkyerɛnne.
Harlequin Yare a Wɔde Yɛ Adwuma
Eyi yɛ tebea a ɛka yɛn ntini a ɛma yɛte nka no. Saa ntini nhyehyɛe yi na ɛhwɛ yɛn "ako-anaa-guan" mmuae so, a ɛyɛ nsakrae a ɛba nipadua no mu bere a yɛn ani agye, ehu aka yɛn, anaa yɛreteɛteɛ yɛn apɔw mu. Bere biara a wɔbɛma nhyehyɛe yi ayɛ adwuma wɔ obi a ɔwɔ Harlequin Syndrome mu (sɛ nhwɛso no, bere a ɔreyɛ apɔw-mu-teɛteɛ) no, anim ne nipadua no fã biako bɛyɛ kɔkɔɔ na fifiri ayɛ no, bere a ɔfã foforo no rennyɛ saa.
Horner Syndrome a Ɛyɛ Fɛ
Eyi nso yɛ ntini mu yare a ɛntaa nsi. Ɛka aniwa ne ntini a atwa ho ahyia wɔ anim no fã biako. Wɔsan frɛ no `oculosympathetic palsy`. Ɛnam ntini kwan a efi amemene no mu kɔ aniwa ne anim no a asiw so. Ɛha nso, anim no fã a ɛka no betumi ayɛ kɔkɔɔ.
| Gyinabea | Henanom na ɛka wɔn? | Nneɛma atitiriw a ɛwom | Aniberesɛm? |
|---|---|---|---|
| Harlequin Sign (wɔ mmofra a wɔawo wɔn foforo mu) . | Nkokoaa a wɔawo wɔn foforo a wɔwɔ apɔwmuden (bɛyɛ 10%) . | Nipadua no fã biako a ɛyɛ kɔkɔɔ bere tiaa bi. | Dabi, asiane biara nni ho koraa na ɛno nkutoo bɛkɔ. |
| Harlequin Yare a Wɔde Yɛ Adwuma | Wɔ obiara a wadi mfe biara fam | Kɔkɔɔ ne fifiri a ɛba ɔfã biako bere a woreteɛteɛ w’apɔw mu anaasɛ w’ani agye no. | Egyina nea ɛde ba no so. Mpɛn pii no, ɛnyɛ asiane biara. |
| Horner Syndrome a Ɛyɛ Fɛ | Wɔ obiara a wadi mfe biara fam | Aniwa a ɛwɔ fam wɔ anim no fã biako, aniwa tuntum ketewaa bi, fifiri a ɛso tew, ne anim a ɛyɛ kɔkɔɔ. | Nea ɛde ba titiriw (sɛ nhwɛso no, akisikuru) betumi ayɛ aniberesɛm. Aduruyɛ mu nhwehwɛmu ho hia. |
Ɔkwan bɛn so na wɔsa?
Ayaresa no gyina nea ɛde Harlequin Nsɛnkyerɛnne no ba so.
- Wɔ mmofra a wɔawo wɔn foforo fam no: Ayaresa biara ho nhia. Ɛno ankasa bɛkɔ wɔ sikani anaa simma kakraa bi mu.
- Wɔ Harlequin Syndrome ho: Ɛnyɛ bere nyinaa na ɛho hia sɛ wɔsa yare. Ɛtɔ mmere bi a, tebea yi ankasa betumi ayɛ yiye. Nanso, sɛ wo duruyɛfo no susuw sɛ ɛho hia sɛ wɔsa yare a, obegyina nea ɛde ba no so akyerɛw ayaresa ahorow ama wo. Eyinom bi ne:
- Wɔde aduru bi a wɔfrɛ no `Stellate ganglion block` di dwuma de siw honam ani kɔla a ɛsakra no ano.
- Botulinum awuduru a wɔde twitwiw fifiri mu.
- Sɛ akisikuru bi wɔ ase a, wobetumi ayɛ oprehyɛn anaa denam mframa a wɔde sa yare so ayi afi hɔ.
- Afotu a wɔde ma wɔ adwene mu dadwen a saa anim a ɛda adi yi de ba ho.
- Wɔ Horner Syndrome ho: Sɛ ɛyaw biara nni hɔ a, ebia ɛho renhia sɛ wɔsa yare. Sɛ ɛba saa a, oduruyɛfo no bɛsa nea ɛde ba no.
Bere bɛn na ɛsɛ sɛ wokɔ oduruyɛfo nkyɛn?
Sɛ wo anaa obi a ɔwɔ w’abusua mu hu Harlequin Sign a ɛyɛ kɔkɔɔ, fifiri ayɛ no ma, na ɛyɛ hyew wɔ nipadua no fã biako a, ade a eye sen biara a ɛsɛ sɛ woyɛ ne sɛ wobɛkɔ akɔhwɛ oduruyɛfo na woakɔhwɛ.
Wo duruyɛfo bɛhwɛ wo, abisa wo yare no ho sɛnkyerɛnne, na sɛ ɛho hia a, ɔbɛyɛ nhwehwɛmu ahorow bi de ayi tebea afoforo afi hɔ. Ɛwom sɛ ɛntaa nsi koraa de, nanso ɛho hia sɛ wopow akisikuru anaa tebea foforo bi, efisɛ eyi betumi de aba.
Sɛ sɛnkyerɛnne afoforo a emu yɛ den ka saa sɛnkyerɛnne ahorow yi ho mpofirim (sɛ nhwɛso no, tiyɛ a emu yɛ den, aniwa a ɛsakra, adwenem naayɛ) a, ɛho hia yiye sɛ wobɛkɔ ayaresabea a ɛbɛn wo no Dwumadibea a Ɛhwɛ Ntɛmntɛm (ETU) ntɛm ara .
Nkrasɛm a Wɔde Kɔ Fie
- Harlequin Sign yɛ tebea a nipadua anaa n’anim fã biako yɛ kɔkɔɔ na ɔfã foforo no yɛ mmerɛw. Mpɛn pii no, eyi nyɛ asiane.
- Eyi abu so wɔ nkokoaa a wɔawo wɔn foforo mu. Ɛno ankasa kɔ, wɔ simma kakraa bi mu, a wonnya ayaresa biara, na ɛnyɛ biribiara a ɛsɛ sɛ ɛhaw adwene. Kae sɛ eyi nyɛ `Harlequin ichthyosis` yare a ɛyɛ hu no.
- Sɛ eyi ba mpanyimfo mu a, ebetumi ayɛ ntini mu tebea bi te sɛ `Harlequin syndrome` anaa `Horner syndrome` ho sɛnkyerɛnne.
- Sɛ wo anaa wo ba no nya saa sɛnkyerɛnne yi a, nyansa wom sɛ ɛnsɛ sɛ wobɔ hu, na mmom wobɛkɔ wo duruyɛfo nkyɛn akɔhwɛ nea ɛde ba ankasa na woahwɛ ahu sɛ tebea foforo biara a emu yɛ den biara nni hɔ.
💬 Comments (0)
Wɔnnya nyɛɛ nsɛm biara. Fa wo nsɛm no ka ho wɔ ha nea edi kan.
Fa wo nsɛm no ka ho