Ɛtɔ da bi a, sɛ yɛhwɛ mogya ho amanneɛbɔ bi a, yehu nsɛm a yennim wɔ mu, ɛnte saa? Sɛ oduruyɛfo bi ka asɛm bi te sɛ eyi a, yɛte nka sɛ yɛpɛ sɛ yehu biribi kakra, ebia ehu ka yɛn kakra mpo. Edin a ɛte saa no mu biako ne ‘Heinz Bodies’. Enti ɛnnɛ, momma yɛnka nea eyi yɛ ankasa ho asɛm, so ɛyɛ yare, anaasɛ yare bi ho sɛnkyerɛnne. Sɛ wote eyi ase pɛpɛɛpɛ a, wo suro befi hɔ.
Sɛ yɛbɛka no tiawa a, dɛn ne Heinz Nipadua yi?
Sɛ yɛbɛka no tiawa a, Heinz Nipadua nyɛ yare. Wɔyɛ sɛnkyerɛnne ara kwa a ɛkyerɛ sɛ wo mogya mu nkwammoaa kɔkɔɔ no asɛe. Te sɛ bere a yehu sɛ kar mu asɛe a, yenim sɛ wɔabɔ no wɔ baabi, na saa ara na eyi nso te.
Eyinom yɛ nsensanee nketenkete a ɛwɔ yɛn mogya mu nkwammoaa kɔkɔɔ no so. Nnuruyɛfo (titiriw ɔyare ho animdefo) betumi ahu wɔn bere a wɔde aduru titiriw bi a wɔde yɛ nneɛma di dwuma na wɔde afiri a wɔde hwɛ nneɛma nketenkete hwɛ wɔn nkutoo. Protein bi a wɔfrɛ no hemoglobin a asɛe na ɛyɛ saa nsensanee yi ankasa. Enti, sɛ wuhu eyinom wɔ mogya mu nhwehwɛmu mu a, ɛkyerɛ sɛ biribi asɛe wɔ mogya mu nkwammoaa kɔkɔɔ no ho. Ebetumi ayɛ tebea bi te sɛ mogya a ɛtɔ kɔ nipadua mu ho sɛnkyerɛnne.
Momma yɛnte sɛnea wɔhyehyɛ eyinom ase?
Sɛ yɛbɛte eyi ase a, ɛsɛ sɛ yedi kan hu yɛn mogya mu nkwammoaa kɔkɔɔ no ho asɛm kakra.
Susuw mogya mu nkwammoaa kɔkɔɔ ho sɛ ɛyɛ adwuma a ɛde mframa pa kɔ yɛn nipadua nyinaa mu. Nneɛma a ɛwɔ kar a wɔde fa nneɛma yi mu ne hemoglobin. Saa hemoglobin yi na ɛgye mframa pa na ɛde fi ahurututu mu kɔ nipadua no afã horow nyinaa. Saa hemoglobin yi na ɛma yɛn mogya kɔla kɔkɔɔ.
Mpɛn pii no, nkwammoaa bi a ɛwɔ yɛn nipadua mu wɔ nuklea. Nanso, mogya mu nkwammoaa kɔkɔɔ a ɛho akokwaw nni nuklea. Enti, ebetumi akura hemoglobin molecule ɔpepem pii mu.
Sɛ biribi nti saa hemoglobin ahorow yi sɛe (oxidative damage) , a, ɛnyɛ adwuma yiye. Wɔboaboa wɔn ho ano na wɔboaboa wɔn ho ano. Yɛfrɛ saa hemoglobin asinasin a ayɛ akuwakuw na asɛe no Heinz Bodies. Sɛ eyi ba a, mogya mu nkwammoaa kɔkɔɔ no ntumi mfa mframa pa nkɔ yiye. Afei nso, wofi ase sɛe na wɔsɛe no ntɛmntɛm sen sɛnea ɛte daa. Wɔ nnuruyɛ mu no, wɔfrɛ mogya mu nkwammoaa kɔkɔɔ a ɛpaapae ntɛmntɛm yi hemolysis .
Sɛ Heinz Bodies wɔ hɔ a, sɛnkyerɛnne bɛn na ebetumi aba?
Ɛnyɛ Heinz Nipadua no na ɛde sɛnkyerɛnne ahorow no ba ankasa, na mmom tebea a ɛwɔ ase a ɛde ba, a ɛne mogya mu nkwammoaa kɔkɔɔ dodow a ɛba fam (nemia). Sɛ wo mogya mu nkwammoaa kɔkɔɔ dodow sua koraa a, ebia worennya yare no ho sɛnkyerɛnne biara koraa. Mpɛn pii no, wo nipadua no nnya mframa pa a ɛdɔɔso na ɛde saa sɛnkyerɛnne ahorow yi ba.
| Nsɛnkyerɛnne a ɛkyerɛ | Nkyerɛkyerɛmu a ɛnyɛ den |
|---|---|
| Ɔbrɛ | Ɔbrɛ a ɛtra so a wɔte nka sɛ wonyɛ hwee mpo. |
| Adwene a ɛyɛ basaa | Nkate a ɛma obi ho dwiriw no na ɔnkari pɛ. |
| Wora a ɛyɛ mmerɛw | Wora ne anofafa a ɛyɛ mmerɛw esiane mogya a enni mu nti. |
| Koma a ɛbɔ ntɛmntɛm (Tachycardia) . | Koma a ɛbɔ ntɛmntɛm, a ɛte sɛ nea wo moma so rebɔ. |
| Ɔhome a ɛyɛ den (Dyspnea) . | Ɔhome a ɛyɛ tiaa, sɛ ɔbɔ mmɔden kakra mpo a, ɔte nka sɛ watɔ piti. |
| Jaundice a ɛyɛ mmerɛw | Wora a ɛyɛ kɔkɔɔ ne aniwa fitaa. |
| Splenomegaly a ɛyɛ kɛse | Akisikuru a ɛtrɛw, a eyi mogya mu nkwammoaa kɔkɔɔ a asɛe no fi hɔ. |
Wobɛyɛ dɛn ahu eyinom?
Nnuruyɛfo de nhwehwɛmu bi a wɔfrɛ no peripheral blood smear hu Heinz Nipadua yi . Nea ɛka eyi ho ne sɛ wubeyi mogya ketewaa bi afi wo nsateaa mu na wode apete ahwehwɛ a wɔde twetwe nneɛma so, de aduru titiriw bi aka ho, na wode afiri a wɔde hwɛ nneɛma nketenkete ahwɛ mu.
Nea ɛyɛ nwonwa ankasa ne sɛ ɛtɔ mmere bi a mogya mu nkwammoaa kɔkɔɔ a ɛwɔ Heinz Bodies yi te sɛ nea obi aka nkwammoaa no fã bi. Yɛfrɛ eyinom "nkwaboaa a ɛka."
Sɛnea ɛyɛ adwuma ni: Sɛ mogya mu nkwammoaa kɔkɔɔ a asɛe fa yɛn akyi berɛmo mu a, akyi berɛmo no yɛ adwuma te sɛ nea wɔde yiyi mu. Ɛ "we" Heinz Bodies a asɛe no. Mogya mu nkwammoaa kɔkɔɔ a aka no te sɛ aduan bi a obi awe.
Dɛn ne aduruyɛ mu tebea atitiriw a wohu Heinz Nipadua wɔ mu?
Seesei yenim sɛ Heinz Nipadua yɛ yare bi ho sɛnkyerɛnne. Enti, tebea atitiriw a wohu wɔn wom no bi ni.
| Aduruyɛ mu tebea | Nkyerɛkyerɛmu a ɛnyɛ den |
|---|---|
| Mogya a Ɛma Mogya Mu | Mogya mu nkwammoaa kɔkɔɔ a ɛpaapae na ɛsɛe ntɛmntɛm sen sɛnea wɔyɛ no na ɛde mogya a ɛtɔ kɔ nipadua mu no ba. |
| G6PD a Ɛho Nhia | Eyi yɛ awosu mu tebea (a wonya fi awo mu). Enzyme G6PD a enni hɔ no ma asiane a ɛwɔ hɔ sɛ mogya mu nkwammoaa kɔkɔɔ bɛsɛe no yɛ kɛse. |
| Alpha-thalassemia a ɛwɔ nipadua no mu | Eyi nso yɛ awosu mu yare. Wɔ eyi mu no, nipadua no ntumi nyɛ hemoglobin a ahoɔden wom. |
| Akisikuru a Ɛyɛ Ntrɛwmu | Ɛsɛ sɛ akisikuru no yɛ adwumaden de yi mogya mu nkwammoaa kɔkɔɔ a asɛe pii fi hɔ, na ɛma ɛyɛ kɛse. |
Dɛn nti na Heinz Nipadua yi ba? Dɛn na ɛde ba?
Nneɛma atitiriw pii nti na ebetumi asɛe hemoglobin.
- Nnuru ne nnuru bi a wɔde di dwuma: Sɛ nhwɛso no, nnuru bi a wɔde sa nsu mu yare (UTIs) ne nnuru a wɔde sa kwata.
- Aboɔden abo a enni nipadua mu: Aboɔden abo a enni nipadua mu, titiriw selenium.
- Nnuan titiriw ma nnipa a G6PD nnim: Sɛ obi a G6PD nni no di nnuan te sɛ fava beans , ne mogya mu nkwammoaa kɔkɔɔ betumi asɛe na Heinz Bodies betumi ayɛ.
Ayaresa ne nea wɔde siw ano
Eyi yɛ ɔhaw a nnipa pii wɔ. Ayaresa pɔtee biara nni hɔ a wɔde sa Heinz Bodies. Efisɛ ɛnyɛ yare, na mmom ɛyɛ yare bi ho sɛnkyerɛnne. Nea ɛho hia ne sɛ wubehu tebea a ɛde ba no na woasa. Wo duruyɛfo bɛyɛ nhwehwɛmu a ɛho hia, ahu nea ɛde ba ankasa, na wakyerɛw aduru a ɛfata ama wo.
So wobetumi asiw ano? Yiw, wɔ nsɛm bi mu no, ebetumi aba saa.
Sɛ nhwɛso no, sɛ wunim sɛ wowɔ G6PD a enni wo mu a, ɛsɛ sɛ wokwati sɛ wubedi fava bankye koraa. Afei nso, sɛ worenom nnuru ama tebea foforo biara a, ɛho hia yiye sɛ woma wo duruyɛfo hu sɛ wowɔ G6PD a enni mu. Saa kwan no so no, wo duruyɛfo betumi akyerɛw aduru bi a ɛrempira wo.
Nkrasɛm a Wɔde Kɔ Fie
- Heinz Nipadua nyɛ yareɛ, ɛyɛ sɛnkyerɛnne ara kwa sɛ wo mogya mu nkwammoaa kɔkɔɔ no asɛe.
- Wɔnam nhwehwɛmu titiriw bi a wɔyɛ wɔ mogya a ɛtɔ gu fam (Peripheral Blood Smear) so na ehu eyinom.
- Eyinom betumi afi awosu mu tebea horow te sɛ G6PD a enni nipadua mu, thalassemia, anaa nnuru bi mu aba.
- Ayaresa pɔtee biara nni hɔ a wɔde sa Heinz Bodies. Wɔde ayaresa no kyerɛ tebea a ɛwɔ ase a ɛde wɔn bae no.
- Sɛ wowɔ din te sɛ eyi wɔ wo mogya ho amanneɛbɔ mu a, mma ɛnhaw wo, kɔ wo duruyɛfo nkyɛn ntɛm ara na ka ho asɛm. Ɔde afotu a wuhia nyinaa bɛma wo.











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