So wo koma ntini ayɛ den? Momma yɛnka restrictive cardiomyopathy ho asɛm.

So woasusuw nea ɛbɛba ho pɛn sɛ adan nketewa a ɛwɔ wo koma mu no gyae adwumayɛ yiye a? Ɛtɔ da bi a, yɛn koma ntini yɛ den na entumi nhyɛ mogya ma yiye. Ɛno na yebetumi anya nea yɛrebɛka ho asɛm no: restrictive cardiomyopathy. Mma ɛnhaw wo, momma yɛmma ɛnyɛ mmerɛw.

Dɛn ne Restrictive Cardiomyopathy?

Sɛ yɛbɛka no tiawa a, eyi yɛ tebea a ɛfa koma ntini no ho. Ntini a ɛwɔ adan abien a ɛwɔ yɛn koma ase a wɔfrɛ no ventricles , no mu yɛ den. Ɛnte sɛ rɔba a ɛsan twa ne ho bere a woatrɛw mu no, nanso ntini no ntumi nkɔ fam yiye. Eyi kyerɛ sɛ saa adan yi nni baabi a ɛdɔɔso a mogya bɛhyɛ mu ma yiye. Sɛ eyi ba a, mogya a ɛsen fa koma no mu no sɛe.

Edin afoforo wɔ hɔ a wɔde frɛ eyi, na ɛtɔ mmere bi a nnuruyɛfo betumi de din ahorow yi adi dwuma:

• `Idiopathic anohyeto cardiomyopathy`
• Infiltrative cardiomyopathy (koma ntini mu yare a nneɛma afoforo a ɛkɔ ntini no mu de ba) .

Hena na ɛda adi kɛse sɛ obenya saa yare yi? Ɛtaa ba dɛn?

Ɛwom sɛ obiara betumi anya saa tebea yi, `(Restrictive Cardiomyopathy)` de, nanso ɛtaa ba nnipa binom mu esiane tebea horow bi a ɛhyɛ ase nti. Sɛ nhwɛso no, `(Sarcoidosis)` (a ebetumi nso de `(Restrictive Cardiomyopathy)`) abu so kɛse wɔ mmea a wofi mmusuakuw bi mu mu.

Koma mu ntini mu yare yɛ tebea a ɛtaa ba. Ɛka nnipa 500 biara mu bɛyɛ 1. Nanso, koma ne ntini mu yare yi ne nea ɛntaa nsi . Ɛyɛ bɛyɛ 5% wɔ koma ne ntini mu yare nyinaa mu. Enti, eyi yɛ biribi a wɔntaa nte ho asɛm, nanso ɛfata sɛ yehu.

Ɔkwan bɛn so na restrictive cardiomyopathy ka koma no?

Yɛn koma yɛ akwaa a ɛyɛ nwonwa. Ɛwɔ adan anan, na wɔde ntini na ɛyɛ titiriw. Saa adan yi de mogya nam denam twetwe so. Wɔfrɛ atifi dan abien no `Atria` , na wɔfrɛ ase dan abien no `Ventricles` .

Nea ɛkɔ so wɔ saa `(Restrictive Cardiomyopathy)` tebea yi mu ne sɛ ntini a ɛwɔ fam (`Ventricles`) no yɛ den na ɛhwere ne ahoɔden. Afei saa adan no ntumi mfa mogya nhyɛ mu ma koraa. Fa no sɛ ɛte sɛ nea worebɔ balloon mu mframa, sɛ wɔanhyɛ balloon no mu yiye a, mframa kakraa bi pɛ na ɛbɛkura mu. Saa na ɛkɔ so wɔ ha nso. Eyi ma ɔkwan a mogya fa koma no mu no nyinaa siw kwan.

Dɛn ne sɛnkyerɛnne ahorow no? So wobetumi ahu wɔn ntɛm?

Ɛtɔ mmere bi a, ebia yare no ho sɛnkyerɛnne biara nni hɔ , titiriw wɔ mfiase no. Nanso bere a yare no kɔ so no, komayare betumi aba.Nsɛnkyerɛnne a ɛte sɛ atiridii no fi ase da adi. Saa sɛnkyerɛnne ahorow no bi ni:

• Yafunu a ɛyɛ ma anaasɛ akisikuru.
• Koko mu yaw (a ebetumi aba bere a wɔagye wɔn ahome anaa bere a wɔreyɛ apɔw-mu-teɛteɛ).
• Adwene a ɛyɛ basaa anaasɛ obi a ɔtotɔ piti.
• Nan ne anan a ɛho ahonhon (`Edema`).
• Ɔbrɛ a wɔte nka bere nyinaa (`Ɔbrɛ`).
• Koma a ɛbɔ a ɛnteɛ (`Koma a ɛbɔ`).
• Ɔhome a ɛyɛ den (Dyspnea), ɛtɔ mmere bi mpo a sɛ ɔbɔ mmɔden kakra.
• Mu duru a ɛkɔ soro mpofirim.

Nea ɛho hia: Sɛ wowɔ saa sɛnkyerɛnne yi mu biako anaa nea ɛboro saa a, nsusuw sɛ ɛyɛ `Restrictive Cardiomyopathy`. Nanso, ɛbɛyɛ papa sɛ wobɛkɔ oduruyɛfo nkyɛn akɔhwehwɛ afotu.

Dɛn nti na tebea yi ba? Dɛn ne nea enti a ɛte saa?

Nneɛma atitiriw pii na ɛde koma mu ntini mu yare a anohyeto wom ba. Ɛne sɛ, ebetumi afi aduruyɛ mu tebea afoforo mu aba.

• `Amyloidosis` : Eyi ne bere a protein bi gu koma ntini mu.
• Connective tissue diseases : Nyarewa a ɛka nipadua no mu ntini ahorow.
• Hemochromatosis (iron overload) : Dade a ɛboaboa ano dodo wɔ nipadua no mu.
• Sarcoidosis : Nkwammoaa nketenkete a wɔfrɛ no granulomas a ɛba nipadua no akwaa ahorow mu.

Nea ɛka ho no, ebetumi aba sɛ tebea yi bɛba bere a wɔayɛ kokoram ayaresa bi akyi:

• Nnuru a wɔde sa yare
• Mframa a wɔde sa yare

Ɔkwan bɛn so na nnuruyɛfo hu yare yi pɛpɛɛpɛ? (Nyare a Wɔahu) .

Sɛ wokɔ oduruyɛfo nkyɛn a, obedi kan abisa wo wo yare no ho sɛnkyerɛnne, ayɛ wo nipadua mu nhwehwɛmu, atie wo koma bɔ, na wahwɛ wo mogya mmoroso.

Afei, sɛnea ɛbɛyɛ na wɔakyerɛ sɛ wɔahu yare no na wɔahwɛ sɛ koma no mu adan (ventricles) no reyɛ adwuma yiye anaa no, wɔyɛ echocardiogram (koma mu nhwehwɛmu). Eyi betumi ahwɛ nneɛma te sɛ sɛnea koma no yɛ adwuma ne sɛnea ntini no mu yɛ duru.

Ebia wo duruyɛfo nso bɛkamfo nhwehwɛmu afoforo pii akyerɛ de ahwɛ sɛ ebia tebea afoforo a ɛda adi a ebetumi de Restrictive Cardiomyopathy aba anaa. Eyinom bi ne:

• Mogya ne nsu mu nhwehwɛmu.
• Koko so X-ray a wɔyɛ.
• `CT` scan a wɔde hwɛ koma no (`Cardiac CT scan`).
• Apɔw-mu-teɛteɛ adwennwen sɔhwɛ.
• Koma mu MRI.
• Koma mu PET scan.
• Koma nifa a wɔde hyɛ nipadua no mu.
• Myocardial biopsy - Eyi hwehwɛ sɛ wɔfa koma ntini ketewaa bi na wɔsɔ hwɛ.
• Awosu mu nhwehwɛmu.

So ayaresa wɔ hɔ? Ɔkwan bɛn so na wodi ho dwuma?

Nea ɛyɛ awerɛhow no, saa tebea yi a wɔfrɛ no `Restrictive Cardiomyopathy' no yɛ tebea yi pɔtee.Aduru biara nni hɔ de besi nnɛ. Nanso, nnuruyɛfo betumi asa nea ɛde ba no na wɔadi sɛnkyerɛnne ahorow no so.

Sɛ wowɔ sɛnkyerɛnne ahorow a ɛfa komayare ho a, wo duruyɛfo betumi akamfo ayaresa ahorow a edidi so yi akyerɛ wo:

• Corticosteroids (nnuru a ɛte sɛ steroid) sɛ wowɔ sarcoidosis a.
• Diuretics (nnuru a ɛma obi tow nsu kɛse) a ɛma nsu a ɛboro so wɔ nipadua no mu no so tew.
• Nnuru a wɔde sa koma a ɛyɛ den a ɛnkɔ so pɛpɛɛpɛ (e.g. `Antiarrhythmics`, `Beta-blockers` anaa `Calcium channel blockers`).
• Phlebotomy a wɔde sa yare yɛ aduru a wɔde sa nnipa a wɔwɔ hemochromatosis (dade a ɛboro so).
• Nnuru pɔtee a wɔde sa `(Amyloidosis)` ahorow bi.

Ebia awiei koraa no, nnipa binom behia sɛ wɔyɛ wɔn koma foforo oprehyɛn bere a yare no mu yɛ den no. Wobetumi nso de wɔn akɔma ayaresabea a wɔde brɛ wɔn ho ase na ama wɔadi yare no ho sɛnkyerɛnne ahorow so na wɔakura asetra pa mu.

Dɛn ne nsɛnnennen a ebetumi afi yare yi mu aba?

Nsɛnnennen afoforo pii betumi aba esiane `Restrictive Cardiomyopathy` nti. Eyinom ne:

• Koma a ɛnyɛ adwuma yiye : Koma a ɛbɔ a ɛnteɛ daa.
• Koma a entumi nyɛ adwuma yiye : Koma no ntumi mfa mogya a ɛdɔɔso nkɔ nipadua no mu.
• Mogya a ɛtɔ ne akisikuru (`Thromboembolism` anaa `Stroke`) : Mogya a ɛtwetwe no betumi ama obi anya akisikuru.

Dɛn na yebetumi ayɛ de atew asiane no so?

Saa tebea yi, ``Restrictive Cardiomyopathy,'' kyerɛ sɛ ɛsɛ sɛ wo koma yɛ adwumaden de bɔ mogya. Enti, ɛho hia sɛ wo ne wo duruyɛfo kasa fa nea wubetumi ayɛ de atew adwuma a ɛda wo koma so no so.

Bere a ɛyɛ den sɛ wubesiw aduruyɛ mu tebea horow a ɛde Restrictive Cardiomyopathy ba no ano no, wubetumi ayɛ nea edidi so yi na ama wo koma atra apɔw:

• Di wo mogya mmoroso so .
• Kura mu duru a ɛfata mu .
• Tew adwennwen so .

Dɛn na ɛsɛ sɛ wohwɛ kwan bere a wo ne yare yi te ase no?

Restrictive Cardiomyopathy yɛ tebea a emu yɛ den, enti ɛho hia sɛ wo ne wo duruyɛfo kasa daa fa anammɔn a wubetumi ayɛ na ama wo koma anya apɔwmuden ho.

Bere tenten a wubetumi de yare yi atra ase no gu ahorow wɔ onipa biara mu. Wo duruyɛfo bɛkyerɛkyerɛ sɛnea yare no bɛkɔ so ne nea ɛsɛ sɛ wohwɛ kwan mu akyerɛ wo ne w’abusua.

Ɔkwan bɛn so na ɛsɛ sɛ mehwɛ me ho? (Ne ho a wɔhwɛ) .

Ade a ɛho hia sen biara ne sɛ wubedi wo duruyɛfo akwankyerɛ akyi pɛpɛɛpɛ na woanom nnuru a wɔakyerɛw ama wo nyinaa wɔ bere ano. Nea ɛka ho no, ebia wo duruyɛfo nso bɛka akyerɛ wo sɛ yɛ nsakrae wɔ w’asetra mu te sɛ:

• Aduan a ahoɔden wom a nkyene nnim (a sodium nnim) .Sɛ wobɛfa.
• Apɔw-mu-teɛteɛ (sɛnea wo duruyɛfo afotu ama wo nkutoo).

Bere bɛn na ɛsɛ sɛ wohwehwɛ aduruyɛ mu afotu ntɛm ara?

Sɛ wote nka sɛ wo komayare ho sɛnkyerɛnne no reyɛ kɛse, anaasɛ wunya sɛnkyerɛnne foforo a, frɛ wo duruyɛfo ntɛm ara .

Afei nso, sɛ tebea a egye ntɛmpɛ te sɛ eyi si a, kɔ ayaresabea ntɛm ara (sɛ wowɔ Sri Lanka a, frɛ nɔma a egye ntɛmpɛ te sɛ 1990):

• Sɛ wowɔ koko mu yaw a emu yɛ den a .
• Sɛ wo totɔ piti a .
• Sɛ mpofirim ara ɛyɛ den ma wo kɛse sɛ wobɛhome a .

Kae: Koma yɛ akwaa a ɛho hia paa wɔ yɛn asetra mu, enti ɛho hia paa sɛ yɛhwɛ so.

Nkrasɛm a Wɔde Kɔ Fie

Okay, enti nneɛma a ɛnyɛ den bi a ɛsɛ sɛ yɛkae fa `(Restrictive Cardiomyopathy)` a yɛkaa ho asɛm no ho ni:

• Nea ɛba wɔ eyi mu ne sɛ ntini a ɛwɔ koma no ase adan (venttricles) no mu yɛ den na ɛmma wontumi nyɛ nsakrae .
• Enti, saa nkwammoaa no ntumi nhyɛ mogya ma yiye .
• Afei ɛsɛ sɛ koma no yɛ adwumaden de pam mogya kɔ nipadua no mu, na ebetumi ama ``Koma no ayɛ adwuma yiye``.
• Ɛwom sɛ wonni aduru pɔtee biara a wɔde sa eyi de, nanso wodi ho dwuma denam nea ɛde ba no a wɔsa ne sɛnkyerɛnne ahorow a wodi so so .
• Sɛ wowɔ nsɛmmisa anaa adwenem naayɛ bi wɔ eyi ho a, nsuro sɛ wo ne wo duruyɛfo bɛkasa .

Yɛrepɛ sɛ mo akwahosan pa!

` Restrictive Cardiomyopathy, komayare, koma ntini mu yare, ahome a ɛyɛ tiaa, koko mu yaw, komayare, aduruyɛ