So woate pɛn sɛ retina a ɛwɔ w’aniwa mu, w’aniwa fã a ɛte sɛ screen a ɛyɛ mfonini ahorow a yehu no mu paapae mpofirim yɛ abien anaa nea ɛboro saa? Ɛno yɛ tebea a ɛyɛ nwonwa nanso ɛho hia a ɛsɛ sɛ wuhu ho asɛm. Eyi ne nea nnuruyɛfo frɛ no `(Retinoschisis)`. Mma ɛnhaw wo, momma yɛnka ho asɛm tiawa.
Dɛn ne Retinoschisis? Momma yɛnte ase tiawa.
Sɛ yɛbɛka no tiawa a, `(Retinoschisis)` yɛ bere a retina a ɛwɔ w’ani mu no mu paapae yɛ no ntoatoaso. Sɛ yɛbɛka no pɛpɛɛpɛ a, ɛpaapae mu abien anaa nea ɛboro saa. So wunim, yɛn retina yɛ ntini a ɛyɛ den yiye. Ɛwɔ ɔfa bi a ɛte hann nka, ne nkwammoaa a ɛde nsɛnkyerɛnne fa `optic nerve` so kɔ amemene no mu. Enti, sɛ saa ntoatoaso yi mu paapae saa a, ebetumi aka w’anisoadehu. Susuw ho te sɛ nhoma bi nkratafa a wɔmfa gluu nhyɛ mu na wɔatew mu. Saa mpaapaemu yi betumi aba wɔ retina no mfinimfini, nanso mpɛn pii no ɛba wɔ anoano, kyerɛ sɛ, wɔ `periphery`.
Dɛn ne retinoschisis ahorow atitiriw?
Saa tebea yi, ``Retinoschisis'', yɛ nea ɛntaa nsi kakra. Nanso eyi ahorow atitiriw abien na ɛwɔ hɔ. Baako yɛ nea wonya , na biako nso yɛ nea wonya fi awo mu .
Retinoschisis (Retinoschisis a Wonya) a efi ase akyiri yi .
Wɔsan frɛ eyi sɛ `degenerative retinoschisis` . Ɛno kyerɛ sɛ ɛyɛ biribi a ɛba bere a obi nyin, biribi a ɛne ɔporɔw kakra wɔ abusuabɔ. Mpɛn pii no, wohu eyi bɛyɛ mfe 50, 60, anaa 70. Ɛno nti na nnipa binom nso frɛ no `senile retinoschisis` . Nanso, ɛtɔ mmere bi a, mmerante ne mmabaa nso betumi anya saa tebea yi.
Retinoschisis a ɛma nipadua no sɛe no gu ahorow abien. Baako yɛ nea wɔtaa de di dwuma, na biako nso yɛ nea ɛyɛ bullous anaa reticular . Wɔ bullous type no mu no, akisikuru nketenkete a nsu wom ba retina no so. Ɛyɛ den kakra sɛ yebehu nsonsonoe a ɛda ahorow abien no ntam. Nanso, bullous type no taa nya retina ntokuru ne retina detachment.
Myopic macular schisis foforo nso wɔ hɔ . Wɔsan frɛ no myopic traction maculopathy anaa myopic foveoschisis . Ɛba retina no mfinimfini fã a wɔfrɛ no macula , ne titiriw wɔ macula no mfinimfini a wɔfrɛ no fovea . Wɔtaa hu no kɛse wɔ nnipa a wɔn ani da hɔ kɛse anaasɛ wontumi nhu ade yiye no mu.
Retinoschisis a Wɔde Awo Wɔn
Wunim, sɛ yɛka biribi a ɛyɛ awosu a, ɛkyerɛ biribi a ɛwɔ yɛn nipadua mu bere a wɔawo yɛn. Saa `(Retinoschisis)` yi na wɔfrɛ no `mmofra X-linked retinoschisis`.Ɛyɛ tebea a efi ase wɔ mmofraase, anaa mmofraase, na ɛne X chromosome no wɔ abusuabɔ. Ɛtaa ka aniwa abien no nyinaa.
Saa tebea yi, `juvenile X-linked retinoschisis`, ka mmarimaa kɛse. Wɔn maamenom kura awosu mu abɔde a ɛma wonya no, nanso mpɛn pii no, ɛnanom nnya tebea no.
Nsonsonoe bɛn na ɛda Retinal Detachment ne Retinoschisis ntam?
Ɛwom sɛ nnyigyei abien yi yɛ pɛ de, nanso nsonsonoe kakra wɔ mu. Susuw ho hwɛ, retina a ɛpaapae ne bere a retina no tetew ne ho fi ntini a ɛboa no ho koraa na efi mu ba. Ɛte sɛ poster bi a efi ɔfasu bi so reba.
Retinoschisis nyɛ retina a ɛpaapae, na mmom ɛyɛ retina a ɛpaapae mu yɛ no ntoatoaso. Ɛtɔ mmere bi a, ebetumi ayɛ den sɛ wobehu tebea yi, wɔ aniwa ho oduruyɛfo mpo fam. Nanso, nhwehwɛmu titiriw betumi aboa wo duruyɛfo ma wahu nea ɛyɛ pɛpɛɛpɛ.
Ɛtɔ da bi a, saa tebea mmienu yi nyinaa, a ɛne `(Retinal detachment)` ne `(Retinoschisis)`, tumi ba bere koro mu. Saa asiane yi yɛ kɛse titiriw sɛ wowɔ `(congenital)` type `(Retinoschisis)` a ɛwɔ hɔ wɔ awo mu a.
Tebea yi a wɔfrɛ no Retinoschisis abu so dɛn?
Nhwehwɛmufo ka sɛ awo mu tebea `juvenile X-linked retinoschisis` no ba bɛyɛ nnipa 5,000 biara mu biako anaa nnipa 25,000 biara mu biako mu. Ɛno yɛ ɔha biara mu nkyem a ɛba fam koraa.
Wobu akontaa sɛ degenerative retinoschisis, tebea a ɛba bere a obi nyin no, ka nnipa a wɔadi boro mfe 40 bɛyɛ 4%. Nhwehwɛmu foforo kyerɛ sɛ ebetumi aka nnipa a wɔadi boro mfe 50 no mu 1% kosi 4%.
Dɛn ne Retinoschisis ho sɛnkyerɛnne ahorow? So wowɔ eyinom nso?
Nea ɛyɛ nwonwa ne sɛ ɛtɔ mmere bi a wubetumi anya saa tebea yi a wunnya sɛnkyerɛnne biara . Nanso sɛ wowɔ sɛnkyerɛnne ahorow a, ma yɛnhwɛ nea ɛyɛ.
Sɛ wowɔ awosu mu `juvenile X-linked retinoschisis` a, ebia wubehu sɛnkyerɛnne te sɛ eyinom:
- Ɛte sɛ nea aniwa no adan akɔ hwene no so (te sɛ `ani a wɔatwa`).
- Aniwa no ntra baabi biako na ɛkɔ anim ne akyi (nystagmus).
- Ɛdenam beae a retina no tetew no so no, ebia mfinimfini anaa foveal anisoadehu anaa akyi anisoadehu bɛyera.
- Ɔhaw ahorow a ɛfa akyirikyiri anisoadehu ho (mpɛn pii no, obi a ɔhwɛ akyirikyiri).
Sɛ woanya retinoschisis a, ebia wubehyia nea edidi so yi:
- Sɛ wontumi nhu ade yiye wɔ afã abien no nyinaa (anisoadehu a ɛyera wɔ akyirikyiri).
- Ɛtɔ da bi a, yare no ho sɛnkyerɛnne biara ntumi mma.
Nanso, sɛ wo retinoschisis no mu yɛ den, anaasɛ retina a ɛpaapae ka ho a, wubetumi anya sɛnkyerɛnne ahorow te sɛ:
- Sɛ wuhu nneɛma nketenkete tuntum a ɛrehuruhuruw wɔ aniwa no anim (`floaters`) na wunya hann a ɛhyerɛn mpofirim (`flashers`).
- Nneɛma a wɔatrɛw mu na wɔakyinkyim (`mfonini ahorow a wɔakyinkyim`) a wubehu.
- Ɛdenam beae a retina no tetew no so no, ebia mfinimfini anaa akyi anisoadehu bɛyera.
Nea ɛho hia: Sɛ wowɔ saa sɛnkyerɛnne yi bi a, kɔ aniwa ho oduruyɛfo nkyɛn ntɛm ara. Efisɛ ayaresa a wɔde ma ntɛm ho hia yiye ma aniwa mu haw ahorow.
Dɛn nti na Retinoschisis ba? Dɛn na ɛde ba?
Mpɛn pii no awosu mu nsakrae bi na ɛde retinoschisis a wonya fi awo mu ba . Yɛadi kan aka sɛ ɛne X wɔ abusuabɔ, a ɛkyerɛ sɛ ɛne awosu mu nkwaadɔm a wonya fii ɛna no hɔ wɔ abusuabɔ.
Nanso, nyansahufo nnya nhuu nea ɛde tebea no ba ankasa ``acquired retinoschisis.`` Nanso, wɔahu sɛ asiane a ɛwɔ hɔ sɛ wobenya bi no kɔ soro bere a obi nyin, titiriw wɔ mfe 40 akyi.
Wobɛyɛ dɛn ahu no yiye sɛ wowɔ Retinoschisis? (Nyare a Wɔahu) .
Mpɛn pii no , aniwa ho ɔbenfo (aniwa ho oduruyɛfo) na ohu tebea yi . Bere a wɔayɛ aniwa mu nhwehwɛmu a edi mũ (aniwa mu nhwehwɛmu a edi mũ) akyi no, wobetumi ayɛ nhwehwɛmu ahorow a edidi so yi de asi so dua sɛ wɔahu yare no:
- Ophthalmoscopy anaa fundoscopy: Wɔ saa adeyɛ yi mu no, oduruyɛfo no de adwinnade titiriw bi (ophthalmoscope) hwehwɛ w’ani mu, titiriw retina.
- Optical Coherence Tomography (OCT): Eyi yɛ sɔhwɛ a ɛnyɛ nea wɔde hyɛ mu a wɔde hann di dwuma de yɛ w’ani mu ne akyi mfonini a emu da hɔ. Etumi hu retina no ntoatoaso no pefee.
- B-scan ultrasonography: Eyi nso yɛ ultrasound sɔhwɛ a ɛnyɛ nea wɔde hyɛ nipadua mu a wɔde nnyigyei asorɔkye di dwuma de twa aniwa no mu mfonini.
- Electroretinography (ERG): Saa sɔhwɛ yi susuw sɛnea w’ani yɛ n’ade bere a hann a ɛhyerɛn mpofirim no. Eyi boa ma wosusuw sɛnea retina no yɛ adwuma.
- Angiography: Saa nhwehwɛmu yi twa mogya ntini a ɛwɔ wo retina mu no mfonini. Ɛde nnuru soronko te sɛ fluorescein anaa indocyanine green na edi dwuma.
- Awosu mu nhwehwɛmu: Sɛ wo duruyɛfo susuw sɛ wowɔ awo mu yare bi a wɔfrɛ no juvenile X-linked retinoschisis a, ebia ɔbɛhyɛ nyansa sɛ wɔnyɛ nhwehwɛmu yi.
Dɛn ne nnuru a wɔde sa Retinoschisis? So wobetumi asa no yare?
Sɛ yɛbɛka nokware a, tebea no `(Retinoschisis)`Wontumi nsa koraa. Nanso, wobetumi adi ho dwuma. Ebia nnuruyɛfo bɛkamfo ahwehwɛ anaa nneɛma afoforo a ɛboa ma wunhu ade yiye a ɛbɛboa wo ma woahu ade yiye.
- Sɛ woanya retinoschisis , ebia wunhia ayaresa biara. Ebia wo duruyɛfo bebu eyi sɛ tebea a ɛnyɛ hu a enhia sɛ wɔsa. Nanso, sɛ wowɔ mfomso ahorow a ɛma wotumi hu ade te sɛ nea wutumi hu ade yiye anaasɛ wutumi hu ade akyirikyiri a, ebia wubehia ahwehwɛ.
- Sɛ wowɔ congenital `juvenile X-linked retinoschisis` , ɛho behia nso sɛ wode ahwehwɛ di dwuma ma aniwa mu haw ahorow.
Ɛtɔ mmere bi a, mogya ntini a ɛwɔ retina no mu no betumi apaapae na ama mogya atu aniwa no mu. Sɛ eyi ba a, ebia wo duruyɛfo bɛkamfo akyerɛ sɛ wɔmfa cryoablation anaa laser therapy nni dwuma na ama mogya no agyae.
Ade a ɛho hia sen biara ne sɛ, sɛ w’aniwa no ayɛ mmerɛw a, akyinnye biara nni ho sɛ wubehia oprehyɛn na ama w’aniwa no asan abata ho.
Nhwehwɛmufo da so ara rebɔ mmɔden sɛ wobenya ayaresa foforo a wɔde sa mmofra retinoschisis a ɛne X wɔ abusuabɔ, a awosu mu nkwaadɔm a wɔde sa yare , ntini mu nkwammoaa a wɔde sa yare , ne aduru bi a wɔfrɛ no dorzolamide ka ho.
So ɔkwan bi wɔ hɔ a wɔbɛfa so asiw retinoschisis ano?
Nea ɛyɛ awerɛhow no, ɛrentumi nyɛ yiye sɛ wobesiw ``Retinoschisis'' a ɛbɛba no ano .
Biribiara nni hɔ a wonim sɛ ɛde retinoschisis a wonya no ba, enti ɔkwan biara nni hɔ a wɔbɛfa so asiw ano. Nanso, sɛ obi wɔ w’abusua mu wɔ abakɔsɛm a ɛkyerɛ sɛ ɔwɔ mmofra a wɔfrɛ wɔn X-linked retinoschisis a, ɛbɛyɛ papa sɛ wubebisa wo duruyɛfo no sɛnea wo ne awosu ho ɔfotufo bi bɛkasa ho asɛm.
Sɛ wowɔ retinoschisis a, dɛn na wubetumi ahwɛ kwan?
Sɛnea yɛadi kan aka no, wonni saa tebea yi ano aduru. Ɛtɔ mmere bi a ebetumi ama n’ani so atew kɛse, na ɛtɔ mmere bi nso a ɛbɛma n’ani afura wɔ mmara kwan so. Nanso, ebia nnipa binom nhia ayaresa biara koraa. Egyina sɛnea wo tebea no mu yɛ den ne sɛnea ɛte so.
Sɛ mewɔ retinoschisis a, ɛsɛ sɛ meyɛ dɛn hwɛ me ho?
Sɛ wowɔ `(Retinoschisis)` a, nneɛma pii wɔ hɔ a ɛho hia a wubetumi ayɛ:
- Yɛ aniwa mu nhwehwɛmu daa. Eyi ne ade a ɛho hia sen biara. Ma wɔnhwɛ w’ani bere ne bere mu , sɛnea wo duruyɛfo kamfo kyerɛ no.
- Fa nneɛma a ɛboa ma wohu ade yiye di dwuma.Afei nso, sua mfiridwuma a ɛma wotumi sesa nneɛma a ebetumi aboa wo ma woayɛ da biara da nnwuma ntɛmntɛm no ho ade. Eyi ho hia ma wo ne wo ba no sɛ wɔwɔ saa tebea yi a.
- Sɛ wuhu nsakrae bi wɔ w’ani so a, ka kyerɛ wo duruyɛfo ntɛm ara. Mmu w’ani ngu nsakrae nketenkete mpo so.
Sɛ wohwere anisoadehu kakra mpo a, ebetumi ayɛ hu. Nanso kae sɛ, ɛnsɛ sɛ wo nkutoo di ne nyinaa ho dwuma. Kɔ so ne w’ani ho oduruyɛfo nni nkitaho. Bisa w’aduruyɛ kuw no fa akuw a wɔboa ne nneɛma afoforo ho. Fa nnwuma a wɔde ma no di dwuma. Wobetumi ama wo nhomasua, aka osuahu ahorow akyerɛ afoforo, ne mfiridwuma ho mmoa.
Ade a ɛho hia sen biara a ɛsɛ sɛ wokae fi nea yɛaka ho asɛm no mu (Take-Home Message) .
Okay, enti, sɛnea yɛaka ho asɛm no, eyinom ne nneɛma a ɛho hia sen biara a ɛsɛ sɛ yɛma ɛtra yɛn adwenem:
- Retinoschisis yɛ tebea a ɛma retina no mu paapae yɛ no ntoatoaso, na ebetumi aka anisoadehu.
- Eyi ahorow atitiriw abien na ɛwɔ hɔ: nea ɛfa mfe a obi adi ne nea efi awo mu.
- Ebia nnipa binom rennya yare no ho sɛnkyerɛnne biara , nanso afoforo betumi anya sɛnkyerɛnne te sɛ aniwa a ɛso tew ne aniwa a ɛtwetwe.
- Ɛwom sɛ wonni eyi ano aduru a edi mũ de, nanso wobetumi adi ho dwuma. Eyi nti, aduruyɛ mu afotu a ɛfata ne nhwehwɛmu ho hia.
- Sɛ wo anaa w’abusua mu obi wɔ saa tebea yi a, ɛho hia yiye sɛ wobɛkɔ aniwa ho oduruyɛfo nkyɛn daa na wudi wɔn afotu akyi .
- Sɛ wuhu nsakrae bi wɔ w’ani so a, hwehwɛ aduruyɛfo afotu ntɛm ara. Sɛ wohu ntɛm na wɔsa yare a, ebetumi asiw tebea no ano.
- Ɛnyɛ wo nko ara, mmeae ne akwan wɔ hɔ a wobɛfa so anya mmoa.
Enti, mewɔ anidaso sɛ saa nsɛm yi ho bɛba wo mfaso. Hwɛ w’ani so yiye!
` Retinoschisis, retina detachment, aniwa mu nyarewa, aniwa a ɛyera, aniwa akwahosan, awosu mu nyarewa, aniwa mu nhwehwɛmu











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