Èse dɔléle aɖe si woyɔna be Fibromuscular Dysplasia (FMD) ŋu nya kpɔa? Ðewohĩ menye nenemae o. Enye nɔnɔme si mebɔ o vie. Gake ate ŋu anɔ vevie ŋutɔ be míanya nu tso eŋu. Elabena edo ƒome kple ʋu ƒe sisi le míaƒe ŋutilã me. Eyata egbea, mina míaƒo nu tso FMD sia ŋu le mɔ bɔbɔe aɖe si gɔme nàte ŋu ase nu.
Nukae nye Fibromuscular Dysplasia (FMD) ƒe dɔléle?
Kpuie ko la, Fibromuscular Dysplasia , alo FMD abe alesi míeyɔnɛ ene, nye lãmenugbagbeviwo ƒe tsitsi si mesɔ o le ʋuka siwo le míaƒe ŋutilã me ƒe gliwo me. Fifia ɖewohĩ ànɔ nusi ʋukawo nye ŋu bum. Ʋukawoe nye ʋuka siwo tsɔa ʋu tso míaƒe dzi me yia lãmenugbagbevi bubu siwo katã le míaƒe ŋutilã me. Abe alesi ko pɔmpi si tsɔa tsi tso tsigoe me yia aƒea ƒe akpa sia akpa ene la, ʋuka siawo hã naa ʋu yia míaƒe ŋutilã me.
Eyata le FMD-nɔnɔme sia ta la, wò ʋukawo, si nye ʋukawo, ate ŋu axe, avuvu, alo adze abe ka ene, axe le teƒe aɖewo eye woavuvu le teƒe aɖewo . Tsɔe be ne woxe tsi ƒe pɔmpi eye wogbãe ɖe teƒe aɖewo la, axe mɔ na tsi ƒe sisi, eye FMD sia ate ŋu axe mɔ na ʋu ƒe sisi hã.
Ʋuka kawoe FMD ate ŋu akpɔ ŋusẽ ɖo?
Nɔnɔme sia si woyɔna be FMD ate ŋu agblẽ nu le ʋuka siwo le míaƒe ŋutilã ƒe akpa vovovowo ŋu. Ʋukawo ƒomevi vevi geɖe li siwo ŋu wòate ŋu agblẽ nu le:
- Carotid arteries: Esiawo le wò kɔ me. Ʋuka siawo tsɔa ʋu tso wò dzi me yia wò ahɔhɔ̃ me. Ne nane dzɔ ɖe ʋuka siawo dzi la, ʋu si yina wò ahɔhɔ̃ me ate ŋu aɖe akpɔtɔ.
- Ayiku ƒe ʋukawo: Ʋuka siawo tsɔa ʋu tso wò dzi me yia wò ayiku me, siwo nye ŋutinu vevi siwo ɖea gbeɖuɖɔwo ɖa le míaƒe ŋutilã me.
- Coronary arteries: Esiawoe nye ʋuka siwo naa ʋu yia dzia ŋutɔ me. Ele be ʋuka siawo nanɔ lãmesẽ me hafi dzia nate ŋu awɔ dɔ nyuie.
- Mesenteric arteries: Ʋuka siawo tsɔa ʋu yia wò dɔgbowo me. Ele be woawɔ dɔ nyuie hafi nuɖuɖu siwo míeɖuna la naɖu.
- Ʋuka Bubuwo: Tsɔ kpe ɖe esia ŋu la, FMD ate ŋu akpɔ ŋusẽ ɖe ʋuka siwo tsɔa ʋu yia wò afɔwo, abɔwo, alo wò ŋutilã ƒe akpa bubuwo hã dzi.
Amekawoe le afɔku gã me be woaxɔ FMD?
FMD ate ŋu adze ame sia ame dzi, gake ame aɖewo ya ate ŋu axɔ dɔlélea. Nukutɔe la, FMD dɔnɔ siwo wu 90% nye nyɔnuwo . Ebɔ ɖe amesiwo xɔ tso ƒe 40 va ɖo ƒe 70 hã dzi wu .
Azɔ hã, atikewɔwɔ me nɔnɔme bubu aɖewo li siwo ƒe dzesiwo ate ŋu asɔ kple FMD tɔ. Eyata ɖɔktawo hã tsia dzi ɖe nɔnɔme siawo ŋu:
- Ehlers-Danlos ƒe dɔlélea
- Loeys-Dietz ƒe dɔlélea
- Neurofibromatosis ƒomevi 1 lia
- Williams ƒe dɔlélea
- Ʋuka gãwo ƒe ʋukawo ƒe dɔléle (`Large vessel vasculitis`) .
- Ʋukawo ƒe ʋuʋu
- Systemic ʋukawo ƒe mediolysis
Aleke gbegbee FMD bɔe?
Le nyateƒe me la, esesẽna na dzɔdzɔmeŋutinunyalawo be woagblɔ ame agbɔsɔsɔme si tututu FMD le. Esi wònye be dzesi aɖeke mele ame geɖe ŋu o , alo wokpɔe le vo me le dodokpɔ siwo wowɔna le dɔléle bubu ŋu me ta la, dɔlélea ate ŋu anɔ ŋuwò, gake ɖewohĩ mènyae o.
Nukawoe nye FMD ƒomevi veviwo?
Woate ŋu ama FMD ɖe hatsotso vevi eve me le alesi ʋukaawo ƒe dzedzeme le ne ɖɔktawo le wo dom kpɔ nu.
1. Multifocal FMD: Esiae nye ƒomevi si bɔ wu . Le ƒomevi sia me la, ʋukaawo le abe ka si wotsɔ lãgbalẽ wɔe ene . Eyae nye be, ʋukaawo kekena ɖe teƒe aɖewo, emegbe wotsia, wogakekena, wogakekena ake... le nɔnɔme ma tɔgbe nu.
2. Focal FMD: Esia ƒomevi mebɔ kura o . Elɔ ʋukaa ƒe xexe alo lãkusi (abi) siwo mesɔ o ƒe wɔwɔ ɖe ʋukaa ƒe gliwo me ɖe eme.
Nukae hea FMD vɛ?
Nublanuitɔe la, dzɔdzɔmeŋutinunyalawo mekpɔ nya aɖeke koŋ si gbɔ FMD tsona haɖe o , gake wosusu be nu geɖee le eme:
- Domenyiŋusẽfianu: Le go aɖewo me la, esia ate ŋu atso domenyiŋusẽfianu me.
- Lãmetsiŋusẽ: Wosusui be tɔtrɔ siwo vaa ŋutilãa ƒe lãmetsiŋusẽ ƒe agbɔsɔsɔ me ate ŋu akpɔ gome le eme, vevietɔ esi wòbɔ ɖe nyɔnuwo dome wu ta.
- Nusiwo gblẽ le ʋukawo ƒe gli ŋu: Nusiwo abe ʋukawo ƒe tete enuenu ene ate ŋu agblẽ nu le ʋukawo ƒe gliwo ŋu.
- Nu aɖewo, abe atamanono ene, ate ŋu ana FMD nagado gã ɖe edzi. Eya ta ne ènoa atama la, ele vevie ŋutɔ be nàdzudzɔ.
Nukawoe nye FMD ƒe dzesiwo?
FMD ƒe dzesiwo toa vovo le ʋuka si ŋu dɔlélea le nu . Ðewohĩ dzesi aɖeke manɔ amesiwo ŋu FMD le dometɔ aɖewo ŋu kura o . Gake ame bubuwo ate ŋu akpɔ dzesi siwo tso mɔxexe ɖe ʋu ƒe sisi nu. Esiawo dometɔ aɖewoe nye:
- Bruit: Ne ɖɔkta tsɔ nuƒomɔ̃ ɖo to wò kɔ alo ƒodo la, wosea ‘swooshing’ ƒe gbeɖiɖi si mebɔ o kpe ɖe ʋu ƒe sisi ŋu.
- Vertigo: Seselelãme si nye be èle tsatsam alo le tsatsam le ŋuwò.
- Ʋusɔgbɔdɔ alo ʋu ƒe sisi si dzi womeɖu o.
- Taɖuame si nye taɖuame.
- Kɔ ƒe vevesese.
- Gbeɖiɖi si nye ‘swooshing’ alo ɖiɖi le to me sese.
Bu eŋu kpɔ, Nilanthi ƒe ta ʋuʋuna ɣesiaɣi, eye ɣeaɖewoɣi la, esea toɣliɖeɖe wɔnuku aɖe tso eƒe to me. Esusu be esia sɔ. Gake esi ɖɔkta la doe kpɔ la, ese ``Bruit`` ƒe gbeɖiɖi aɖe tso eƒe kɔ me. Esi wogawɔ dodokpɔ bubuwo vɔ megbe hafi wòva kpɔe be FMD le eŋu.
Lãmesẽkuxi sesẽ kawoe FMD ate ŋu ahe vɛ?
Ne womekpɔ FMD dzi nyuie o la, ate ŋu ahe lãmesẽkuxi sesẽ aɖewo vɛ , eyata ele vevie be nànya esia.
- Aneurysm: Ʋuka si le dodom abe ʋuʋudedi ene ƒe gbɔdzɔgbɔdzɔ. Esia ateŋu adzɔ le ʋuka aɖe me le ahɔhɔ̃a me (a `ahɔhɔ̃ me ʋuka`) alo ʋuka aɖe si le ƒodo me (`abdominal artery aneurysm`). Ne esia gbã la, ate ŋu ade ame ƒe agbe afɔku me.
- Arterial dissection: Aɖatsi si le ʋuka aɖe ƒe gli ememetɔ me. Le kpɔɖeŋu me, esia ate ŋu adzɔ le dzitodzito me ʋuka (carotid dissection) alo dzitodzito me ʋuka si me ʋu sina tona (carotid artery dissection le eɖokui si).
- Gbagbãdᴐ.
- Transient ischemic attack (TIA), si woyɔna hã be mini-stroke.
Esiawoe nye kuxi vevitɔ siwo ate ŋu ado mo ɖa le FMD ta. Eyata ele vevie ŋutɔ be nàdi atikewɔlawo ƒe aɖaŋuɖoɖo enumake ne dzesiwo le ŋuwò.
Aleke wowɔa dea dzesi FMD?
Ɣeaɖewoɣi la, wokpɔa FMD le vome ne ɖɔkta le dodokpɔ wɔm edziedzi (le kpɔɖeŋu me, ‘bruit’ ƒe gbeɖiɖi sese). Alo woate ŋu ake ɖe eŋu le dodokpɔ siwo wowɔna be dɔléle bubu aɖe le ame ŋu me.
Ne ɖɔkta aɖe susui be FMD le ŋuwò la, ate ŋu abia be woawɔ dodokpɔwo abe esiawo ene:
- CT-dɔdamɔnu.
- MRI ƒe fotoɖeɖe (`MRI`).
- Ultrasound scan (`Gbeɖiɖi sesẽ`).
- Angiography: Esia zãa nu tɔxɛ aɖe kple X-ray tsɔ léa ŋku ɖe wò ʋukawo ŋu.
Dodokpɔ siawo ate ŋu ade dzesi tɔtrɔ siwo va le ʋukawo me, woƒe xexe, kple woƒe vuvu me kɔte.
Ðe woate ŋu ada FMD keŋkeŋa?
Nublanuitɔe la, fifia la, womekpɔ atike aɖeke na FMD o . Eyae nye be, atike aɖeke meli na esia o. Gake atikewɔwɔ ate ŋu akpe ɖe ame ŋu wòaɖu dzesiawo dzi eye wòaxe mɔ ɖe kuxiwo nu.
Nukawoe nye atike siwo wozãna na FMD?
FMD ƒe atikewɔwɔwo toa vovo le ʋuka siwo ŋu wògblẽ nu le, dɔlélea ƒe sesẽme, kple wò dzesiwo nu. Dɔdamɔnu veviawo dometɔ aɖewoe nye:
- Ʋu ƒe ʋuʋu (Antiplatelet atikewo alo Anticoagulant atikewo): Esiawo xea mɔ na ʋu ƒe ƒoƒo eye woɖea nɔnɔmewo abe ʋusɔgbɔdɔ ene ƒe afɔkua dzi kpɔtɔna.
- Atike siwo wozãna na ʋusɔgbɔdɔ: Le kpɔɖeŋu me, atikewo abe `ACE inhibitors` kple `Angiotensin receptor blockers`.
- Taɖuame kple vevesese dada:Ɣeaɖewoɣi la, wozãa nuwo abe aspirin alo botulinum aɖi dodo (Botox®) ene.
- Angioplasty: Le dɔ sia wɔwɔ me la, wotsɔa ʋuƒo sue aɖe ŋutɔ toa ka aɖe me yia ʋukaa me, eye emegbe wodoa ya ɖe ʋukaa me be wòaʋu teƒe si xe la.
- Amekoko: Ðewohĩ ahiã be woawɔ dɔ na ame be woatsɔ adzra nuwo abe ʋuka siwo me ʋu sina tona ene ɖo alo awɔ mɔ yeyewo be ʋu nate ŋu atso.
Wò ɖɔkta akpɔ atikewɔwɔmɔnu si sɔ na wò wu.
Ðe mɔ aɖewo li siwo dzi woato axe mɔ ɖe FMD nua?
Esi womenya nusiwo tututu gbɔ FMD tsona haɖe o ta la, mɔ aɖeke meli si dzi woato axe mɔ ɖe enu o . Gake ele vevie be woazɔ ɖe agbe nyui nɔnɔ dzi, vevietɔ atamanono , elabena atamanono ate ŋu ana FMD nagblẽ ɖe edzi.
Aleke agbenɔƒe le le FMD gome?
Ame akpa gãtɔ siwo ŋu FMD le ate ŋu anɔ agbe si sɔ . Gake le go siwo mebɔ o me la, ne ʋuka mawo siwo ŋu míeƒo nu tsoe va yi dometɔ ɖeka gbã la, ate ŋu ana ʋu nado le ame ŋu eye wòaxɔ ʋusɔgbɔdɔ, lãmekawo nagblẽ tegbee, eye ɣeaɖewoɣi la, ate ŋu aku gɔ̃ hã. Esia tae wòle vevie ŋutɔ be nàwɔ atike nyuitɔ eye nàwɔ ɖe wò ɖɔkta ƒe mɔfiamewo dzi ɖo.
Ne FMD le ŋuwò la, aleke nèkpɔa ɖokuiwò dzii?
Ne wokpɔ FMD le ŋuwò la, ele vevie be nàtsɔ wò ŋutɔ wò lãmesẽnyawo ƒe agbanɔamedzi. Àte ŋu awɔ nusiawo:
- Kpɔ wò ʋu ƒe sisi ɖa edziedzi.
- Ne ènoa atama la, dzudzɔ enumake. Dzudzɔ atamanuwo zazã hã. Esiawo ate ŋu ana FMD nagblẽ ɖe edzi.
- Kpɔ egbɔ be yede atikewɔlawo ƒe dodokpɔwo kple ɣeyiɣi siwo woɖo ɖi na amewo edziedzi. Ðewohĩ ahiã be woado ʋu ƒe sisi le ʋukawo me kpɔ zi ɖeka ya teti le ƒea me.
- No atike siwo katã ɖɔkta ŋlɔ na wò pɛpɛpɛ eye nàno ɖe game dzi.
Ame aɖewo siwo ŋu FMD le kpɔe be eɖea vi be yewoage ɖe kpekpeɖeŋunahawo me afisi ame bubu siwo ŋu dɔlélea le ate ŋu agblɔ nuteƒekpɔkpɔwo le, eye woana amewo nanya nu tso FMD ŋuti numekuku ŋu.
Ɣekaɣie wòle be amesi ŋu FMD le nadi atikewɔlawo ƒe aɖaŋuɖoɖo?
Wò ɖɔkta ana nànya dzesi siwo wòle be nàdi atikewɔla ne FMD le ŋuwò. Esia ate ŋu ato vovo le ʋuka si ŋu dɔlélea le nu.
Vevietɔ ele be amesiwo ŋu FMD le nanya nu tso ʋusɔgbɔdɔ ƒe dzesiwo ŋu . Esiawo ate ŋu adzɔ kpata:
- Tɔtɔ.
- Taɖuame, dadasɔ, alo azɔlizɔzɔ sesẽ.
- Taɖuame sesẽ.
- Nuƒoƒo alo nya si gblɔm wole gɔmesese sesẽ.
- Nukpɔkpɔ ƒe kuxiwo.
- Gbɔdzɔgbɔdzɔ alo lãmetutudɔ le mo, alɔ, alo afɔ (vevietɔ le ŋutilã ƒe akpa ɖeka).
Ne ède dzesi dzesi siawo dometɔ aɖe la, yi kɔdzi enumake.Ẽ, elabena ʋusɔgbɔdɔ nye nudzɔdzɔ kpata si hiã be woawɔ atike nɛ enumake.
Nu vevitɔ kekeake siwo dzi wòle be míaɖo ŋkui tso nusiwo ŋu míeƒo nu tsoe me enye:
Enyo, eyata míeƒo nu geɖe tso fibromuscular dysplasia (FMD) ŋu egbea. Togbɔ be enye nyati si me kɔ vie hã la, mele mɔ kpɔm be àte ŋu ase egɔme bɔbɔe.
FMD nye nɔnɔme si me lãmenugbagbevi siwo le ʋukawo ƒe gliwo me tsina le mɔ si mesɔ o nu, si wɔnɛ be ʋukawo me tsina, wodoa go, alo dzena abe ka si wotsɔ lãgbalẽ wɔe ene.
Togbɔ be womenya nusi tututu gbɔ esia tso o hã la, ame aɖewo le afɔku me wu, vevietɔ nyɔnuwo. Menye amesiamee dzena le wo ŋu o, gake amesiwo dzena la ate ŋu ase taɖuame, ʋusɔgbɔdɔ, kple toɣliɖeɖe wɔnuku aɖe le woƒe kɔ me. Nusi me afɔku le wue nye be ate ŋu ahe nɔnɔme sesẽwo abe ʋuka me ʋu ƒe sisi kple ʋusɔgbɔdɔ ene vɛ.
Dzɔgbenyuietɔe la, woate ŋu akpɔ nɔnɔme sia gbɔ nyuie ne wodae nyuie eye wotrɔ agbenɔnɔ. Ne dzesi siwo do ƒome kple FMD le ŋuwò la, kpɔ egbɔ be yeyi ɖɔkta gbɔ. Emegbe woate ŋu awɔ dodokpɔ siwo hiã eye woaŋlɔ atike siwo woatsɔ aɖe dzesiawo dzi akpɔtɔ eye woaxe mɔ ɖe kuxiwo nu. Asitsatsa atamanono, ʋu ƒe sisi dzi ɖuɖu, kple atikewɔlawo ƒe aɖaŋuɖoɖowo dzi wɔwɔ katã le vevie na agbe nyui nɔnɔ kple FMD.
Ne nya bubu aɖewo gale asiwò la, mègahe ɖe megbe le wò ɖɔkta alo dɔnɔdzikpɔla biam o. Nɔ lãmesẽ me!
` Fibromuscular dysplasia, FMD, ʋukawo me dɔléle, ʋukawo, ʋusɔgbɔdɔ, ʋukawo ƒe ʋuʋu, ʋusɔgbɔdɔ











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Womeɖo nya aɖeke ɖe amewo haɖe o. Tsɔ wò nyaŋuɖoɖo kpe ɖe afisia zi gbãtɔ.
Tsɔ wò nyaŋuɖoɖo kpee