Nukae nye Lennox-Gastaut Dɔléle (LGS)? Mina míaƒo nu tso eŋu!

Ðe alɔ̃madɔmadɔ dzea viwò suea dzi enuenua? Ðe tɔtrɔ gãwo va le eƒe nusɔsrɔ̃ kple nuwɔna mea? Ne nenemae la, nya si gblɔ ge magblɔ ate ŋu anɔ vevie na wò ŋutɔ. Egbea míele nu ƒom tso Lennox-Gastaut Syndrome , alo (LGS) kpuie, si nye asrãdɔ sesẽ aɖe si dada sesẽ ŋu. Esia ate ŋu adze egɔme tso eƒe ɖevime. Gake mègatsi dzi o, atike yeyewo kple atike yeyewo va li fifia.

Nuka tututue nye Lennox-Gastaut ƒe dɔléle (LGS)? Amekae xɔae?

Kpuie ko la, LGS nye asrãdɔ sesẽ aɖe si dzea egɔme tso ɖevime, zi geɖe hafi woxɔa ƒe 10, eye vevietɔ le ƒe 3 va ɖo 5. Ebɔ vie le ŋutsuviwo me. Ke hã, menye nɔnɔme si bɔ ŋutɔe wònye o. Edzea ame abe ɖeka va ɖo eve ene le miliɔn ɖeka me. LGS le asrãdɔlélawo katã dometɔ siwo ade 1% va ɖo 2% ŋu.

Aleke esia kpɔa ŋusẽ ɖe míaƒe ŋutilã dzii?

Aɖuɖɔtoedɔ nye dɔléle si me ahɔhɔ̃a ƒe elektrikŋusẽ ƒe dzesiwo, alo nyatakakawo, yia lãmenugbagbeviwo dome. (LGS) nye asrãdɔ si nu sẽ wu . Nu geɖewo gbɔe wòtsona:

• Le LGS me la, alɔ̃madɔmadɔ ƒomevi siwo wu ɖeka dzɔna. Alɔ̃madɔmadɔ siawo ƒomevi aɖewo ate ŋu ade abi ɖevia ŋu vevie.
• Alɔ̃madɔmadɔ siawo ate ŋu agblẽ nu le ahɔhɔ̃a ŋutɔ ŋu. Ðevi siwo ŋu LGS le ate ŋu agblẽ nu le woƒe ahɔhɔ̃ ŋu vevie, woƒe nusɔsrɔ̃ nasesẽ, eye woƒe tsitsi nahe ɖe megbe. Esia fia be ɖevia ate ŋu abu nu siwo wòsrɔ̃ xoxo, abe azɔlizɔzɔ kple nuƒoƒo ene, alo aŋlɔ wo be. Esia nye nɔnɔme wɔnublanui aɖe ŋutɔ.
• Zi geɖe la, (LGS) te ŋu nɔa te ɖe atikewɔwɔ nu ŋutɔ. Esia fia be esesẽna be woatsɔ atikewo aɖu edzi. Atikewoe nye atike gbãtɔ, gake zi geɖe la, wonaa atike ƒomevi vovovowo le ɣeyiɣi ɖeka me. Ne wona wo gɔ̃ hã la, ƒã hafi atike ɖeɖe dzaa te ŋu tɔa alɔ̃madɔmadɔa keŋkeŋ.

Nukae nye (LGS) ƒe dzesiwo?

Ðevi si ŋu LGS le ate ŋu aɖe dzesi vovovowo afia. Wo dometɔ aɖewo dzena le gbesiagbegbenɔnɔ kple dɔwɔnawo me, gake bubuwo ya dzena le alɔ̃madɔmadɔ me ko.

Nusɔsrɔ̃ kple nuwɔna ƒe kuxiwo

Ebɔ be ɖevi siwo ŋu LGS le la ƒe nusɔsrɔ̃ sesẽna eye nuwɔna me kuxiwo hã nɔa wo ŋu . Esiawo ate ŋu adze le alɔ̃dɔdɔ ƒe gɔmedzedze megbe kpuie, eye woate ŋu agblẽ ɖe edzi ne alɔ̃madɔmadɔawo yi edzi. Zi geɖe la, nusɔsrɔ̃ kple susu ƒe kuxi siawo nɔa anyi ɖaa, si fia be woate ŋu anɔ anyi vaseɖe tsitsime.

Esesẽna na ɖevi siwo ŋu LGS le be woasrɔ̃ nu, adze xɔlɔ̃wo, eye woaɖo dze kple ame bubuwo. Ate ŋu asesẽ na wo hã be woaɖɔ woƒe seselelãmewo ɖo. Ðevi aɖewo hã ate ŋu aɖe dzesi siwo sɔ kple ɖevi siwo ŋu Autism Spectrum Disorder le .

Alɔ̃madɔmadɔ ƒe afɔɖeɖe

Zi geɖe la, alɔ̃madɔmadɔ ate ŋu adzɔ le akpa etɔ̃ me:

1. Prodrome alo aura: Esia nye nusi ame aɖewo kpɔna hafi xɔa alɔ̃, togbɔ be menye ɣesiaɣie o hã. Esia ate ŋu anye seselelãme si medzea ame ŋu le tufafa me o. Nukpɔkpɔ ƒe tɔtrɔ, sidzenu bubuwo ƒe tɔtrɔ, alo seselelãme alo nuwɔna ƒe tɔtrɔ ate ŋu adzɔ le ɣeyiɣi sia me.

2. Alɔ̃madɔmadɔ: Esiae nye ɣeyiɣi si me alɔ̃madɔmadɔ aɖe dzɔ. Esia ate ŋu ato vovo le alɔ̃dɔdɔ ƒe ƒomevi nu (míaƒo nu tso alɔ̃madɔmadɔ ƒomevi vovovoawo ŋu le ete).

3. Haya le alɔ̃dɔdɔ megbe: Esia nye ɣeyiɣi si kplɔa alɔ̃dɔdɔa ƒe nuwuwu ɖo. Esiae nye ne ame ƒe susu gaɖo eŋu bliboe.

Alɔ̃madɔmadɔ ƒomevi siwo wokpɔna le LGS me

Alɔ̃madɔmadɔ ƒomevi vevi geɖewo li siwo wokpɔna le LGS me. Alɔ̃madɔmadɔ ƒomevi siwo bɔ wu kple woƒe ŋusẽkpɔɖeamedziwoe nye esiawo:

• Atonic ƒe alɔ̃madɔmadɔ:
• Lãmetsiwo ƒe dziɖuɖu ƒe bu/alɔ̃madɔmadɔ: Wogayɔa esia be "drop attack" elabena elɔa ŋusẽ ƒe bu kpata eye wòdze anyigba, abe fefewɔvi si ƒe kawo gbã ene. Esia nye afɔku gã aɖe elabena ɖevia mete ŋu ɖua eɖokui dzi ne wodze anyi o eye ate ŋu axɔ abi vevie, si ate ŋu ade eƒe agbe afɔku me gɔ̃ hã, le ta, kɔ, akɔta, kple akɔta.
• Ame ƒe susu ƒe akpa aɖe bu: Ðewohĩ alɔ̃madɔmadɔ sia mana ame ƒe susu nabu keŋkeŋ o.
• Ɣeyiɣi kpui aɖe: Alɔ̃madɔmadɔ siawo nɔa anyi kpuie ŋutɔ, abe sɛkɛnd ʋɛ aɖewo ene.

• Tonic convulsions ƒe ʋuʋu:
• Ŋutilã bliboa ƒe sesẽ/tsikpe: Esiae nye esime lãmeka siwo katã le ŋutilãa me la ƒoa ƒu zi ɖeka, si wɔnɛ be ŋutilãa sesẽna keŋkeŋ abe ɖe wòtrɔ zu kpe ene.
• Nɔnɔme tɔxɛ aɖe: Ne wole anyigba, woƒe afɔwo kple abɔta le anyigba la, woƒe akɔta te ŋu nɔa akɔta. Woate ŋu akeke abɔwo ɖe woƒe ta dzi, alo woate ŋu abla abɔwo eye woafia asi abɔta ɖe axawo dzi, eye asibidɛawo ate ŋu ate ɖe akɔta ŋu.
• Zi geɖe la, edzɔna le alɔ̃ me: Esiawo dzɔna zi geɖe ne wole alɔ̃ dɔm. Gake woate ŋu adzɔ le ŋkeke me hã. Ne esia dzɔ esime ɖevia le ŋudzɔ la, afɔku li be wòaxɔ abi elabena ɖevia ate ŋu adze anyi.
• Ɣeyiɣi kpui aɖe: Esia hã xɔa tso sɛkɛnd ʋɛ aɖewo va ɖo abe aɖabaƒoƒo ɖeka ene.

• Alɔ̃madɔmadɔ siwo mebɔ o:
• Ŋkuwo ʋuna eye wole ŋku lém ɖe ame ŋu ƒuƒlu: Le alɔ̃madɔmadɔ sia me la, ame ƒe susu meganɔa nu ŋu o, gake ŋkuawo ya nɔa ʋuʋu ɖi. Eyata zi geɖe la, woate ŋu abu esia vodadatɔe be enye ŋkeke me drɔ̃ekuku, susumanɔamesi, kple seselelãme be yemele teƒe aɖeke o.
• Ʋuʋu enuenu: Le alɔ̃madɔmadɔ sia me la, àte ŋu akpɔ ŋku kple nu ƒe ʋuʋu. Asiwo hã ate ŋu anɔ ʋuʋum.
• Ɣeyiɣi kpui aɖe: Esia hã mexɔa wu sɛkɛnd ʋɛ aɖewo o.

Vevietɔ: Ðevi siwo ŋu LGS le ate ŋu axɔ alɔ̃dɔdɔ le "ƒuƒoƒo me," si fia be alɔ̃madɔmadɔ geɖe dzɔna le ɣeyiɣi kpui aɖe me. Ðevi siwo wu eve le etɔ̃ meNɔnɔme aɖe si woyɔna be "Status Epilepticus" dzɔna. Esia nye nɔnɔme si hiã be woawɔ atike na ame kpata!

Nukae nye Status Epilepticus?

Esia fia nu eve dometɔ ɖeka:

• Alɔ̃madɔmadɔ zi ɖeka si nɔa anyi didi si xɔa miniti 5 va ɖo 30.
• Alɔ̃madɔmadɔ si wu zi ɖeka dzɔna le aɖabaƒoƒo 30 me, eye amea megaɖoa eɖokui ŋu bliboe le alɔ̃madɔmadɔ mawo me o.

Status epilepticus nye atikewɔwɔ kpata. Afɔku le eme vevietɔ elabena ate ŋu agblẽ nu le ahɔhɔ̃a ŋu tegbee eye wòaku gɔ̃ hã.

Dzesi bubuwo kple alɔ̃madɔmadɔ ƒomevi siwo do ƒome kplii

• Tonic-clonic seizures: Tonic-clonic seizures (si woyɔna tsã be "grand mal") dzea egɔme le mɔ ma ke nu abe tonic seizures ene, gake akpa bubu aɖe le wo ŋu. Klonik ƒe akpaa nye ne ŋutilã ƒe ʋuʋu, si nye nusi bɔ wu le alɔ̃madɔmadɔa me. Zi geɖe la, tonic kple tonic-clonic ƒe alɔ̃madɔmadɔ xɔa abe miniti eve ene.
• Ʋuʋu kabakaba, kpuie, si le ʋuʋum: Myoclonic seizures nye ʋuʋu kpata, si le ʋuʋum. Sɛkɛnd ʋɛ aɖewo koe wonɔa anyi, gake ɣeaɖewoɣi la, wote ŋu nɔa anyi didi wu. Ame siwo mexɔa alɔ̃madɔmadɔ o hã ate ŋu axɔ "myoclonic jerks" siawo ƒomevi. Le kpɔɖeŋu me, woate ŋu ana ame natsi dzodzodzoe alo anyɔ tso alɔ̃ me kasia.
• Sidzenu, susu, alo dzesi bubuwo: Alɔ̃madɔmadɔ ƒe akpa aɖe alo teƒe aɖe koe wòdzena le ŋutilã ƒe akpa aɖe ko.

Nukawoe hea LGS vɛ?

Nu geɖe li siwo ate ŋu ahe Lennox-Gastaut ƒe dɔlélea vɛ. Nusiwo gbɔ wòtsona dometɔ aɖewo nɔa anyi hafi wodzia vi. Bubuwo hã tsoa nudzɔdzɔ siwo dzɔna le ɖevime gbɔ. Le ``(LGS)`` ƒe nɔnɔme siwo ade enelia me la, womate ŋu ade dzesi nusi gbɔ wòtso si me kɔ o.

Susu siwo wode dzesii dometɔ aɖewoe nye esi:

• Kuxi siwo dona tso ahɔhɔ̃ ƒe tsitsi me hafi wodzia vi.
• Ta ƒe abi sesẽwo (ahɔhɔ̃ ƒe abixɔxɔ alo ʋuʋudedi).
• Dɔlékui siwo gblẽa nu le ahɔhɔ̃a ŋu, abe taɖuame alo tagbɔdɔ ene.
• Lãmetsiŋusẽ ƒe dɔléle siwo ƒe dome wonyi, le kpɔɖeŋu me `(Mitochondrial diseases)`.
• Ahɔhɔ̃ ƒe gbegblẽ si oxygen ƒe anyimanɔmanɔ do ŋgɔ na vidzidzi alo le edziɣi (cerebral hypoxia).
• Tuberous sclerosis ƒe dɔléle.
• Ahɔhɔ̃ me dɔdzẽwo.
• West syndrome (esia nye asrãdɔ ƒomevi bubu, si ate ŋu ava zu LGS emegbe).

Numekulawo kpɔe be "de novo mutations" bɔ ɖe amesiwo ŋu LGS le dome.De novo gɔmee nye "tso gɔmedzedzea me ke." Esiawo nye ame ƒe `(DNA)` ƒe gbɔdzɔgbɔdzɔ siwo dzɔna kpata, le vome. Eyae nye be, tsinyenye alo azi si dzi amea ƒe `(DNA)` ƒe gbegblẽ gbɔe tɔtrɔa tso, gake menye dzila eveawo dometɔ aɖeke ƒe `(DNA)` ƒe gbɔdzɔgbɔdzɔe o.

Gake domenyiŋusẽfianu ate ŋu akpɔ ŋusẽ ɖe nɔnɔmea dzi. Ame siwo ŋu LGS le la dometɔ siwo ade 30% ƒe ƒome ŋutinya me dɔléle nye asrãdɔ. Gake ehiã be woagawɔ numekuku geɖe wu be woatsɔ anya domenyiŋusẽfianu ƒe akpa si tututu esia nye.

Ðe esia xɔa ame mea?

Ao, Lennox-Gastaut ƒe dɔlélea mexɔa ame o. Mekaka tso ame ɖeka me yia ame bubu gbɔ o. Ke hã, dɔléle aɖewo siwo xɔa ame ate ŋu agblẽ nu le ahɔhɔ̃ ŋu eye woahe ``LGS'' vɛ. Ke hã, menye amesiame si ŋu dɔlékui mawo le lae axɔ ``LGS'' o.

Aleke wowɔna dea dzesi Lennox-Gastaut ƒe dɔléle (LGS)?

Zi geɖe la, wowɔa dodokpɔ geɖe tsɔ dea dzesi LGS, eye ɖɔkta awɔ ahɔhɔ̃mekawo ƒe dodokpɔ. Ðeviwo ƒe dɔdala ate ŋu anɔ te ɖe nya si dzilawo gblɔ tso wo vi ƒe dzesiwo ŋu ta ake ɖi nɔnɔmea, vevietɔ ne ɖevia ƒe nusɔsrɔ̃ ƒe kuxiwo alo nuwɔna me kuxiwo le eŋu.

Dodokpɔ kawoe wowɔna tsɔ dea dzesi esia?

Dodokpɔ siwo wozãna wue nye:

• Electroencephalogram (EEG): Esia bia be woatsɔ elektrikŋusẽnamɔ̃ geɖe aɖo ta ŋu kple gel si kplɔa elektrikŋusẽ be woatsɔ adzidze ahɔhɔ̃a ƒe elektrikŋusẽ ƒe dɔwɔwɔ. EEG le vevie le LGS didi me elabena eɖea elektrikŋusẽ ƒe nɔnɔme tɔxɛ aɖe fiana le ahɔhɔ̃a ƒe ƒutsotsoewo me.
• Magnetic Resonance Imaging (MRI): Esia zãa magnet sesẽ aɖe kple kɔmpiuta tsɔ ɖea ŋutilãa ƒe akpa si le eme, vevietɔ ahɔhɔ̃a ƒe foto siwo ƒe nɔnɔme deŋgɔ. Esia kpena ɖe ame ŋu ŋutɔ le ahɔhɔ̃a ƒe tsitsi ƒe kuxiwo didi me.
• Dodokpɔ le dodokpɔxɔ me: Dodokpɔ siawo léa ŋku ɖe ʋu kple aɖuɖɔ ŋu be woakpɔe ɖa be nu bubu aɖewo hã li siwo ate ŋu ahe alɔ̃dɔdɔa vɛ hã. Woléa ŋku ɖe nuwo abe ʋu ƒe dɔwɔwɔ, aklã me dɔlékuiwutikewo, kple ayiku ƒe dɔwɔwɔ ene ŋu. Togbɔ be dodokpɔ siawo mate ŋu ade dzesi LGS keŋkeŋ o hã la, woate ŋu akpe ɖe ame ŋu woaɖe nɔnɔme bubu siwo ate ŋu asrɔ̃ LGS la ɖa.
• Domenyiŋusẽfianu dodokpɔ: Esia ate ŋu akpe ɖe ame ŋu wòanya ne nɔnɔme aɖewo li siwo ƒe dome wonyi siwo ate ŋu ahe LGS vɛ, alo nenye be tɔtrɔ siwo dzɔna le wo ɖokui si.

Tsɔ kpe ɖe eŋu la, woate ŋu awɔ dodokpɔ bubuwo atsɔ aɖe nɔnɔme mawo tɔgbe ɖa. Wò ɖɔkta agblɔ nya geɖe tso esia ŋu na wò.

Aleke woate ŋu akpɔ esia gbɔe? Ðe woate ŋu adaea?

Atikewɔwɔmɔnu vovovowo li na LGS. Gake exɔ ŋkɔ be dɔlélea dada sesẽ. Zi geɖe la, woate ŋu azã atike siawo dometɔ ɖeka alo wo dometɔ ɖeka:

• Atikewo
• Nuɖuɖu ŋuti atikewɔwɔwo
• Amekoko alo mɔ̃ siwo wotsɔ dea ahɔhɔ̃a me

Atikewo

Zi geɖe la, Lennox-Gastaut ƒe dɔlélea te ŋu nɔa te ɖe atikewo nu ŋutɔ. Esia tae edzikpɔkpɔ sesẽ ŋutɔ ɖo. Le go geɖe me la, ehiãna be woazã atike geɖe. Nu bubu si hã sesẽe nye be atike aɖewo siwo tsia alɔ̃madɔmadɔ nu, siwo kpɔa alɔ̃madɔmadɔ ƒomevi aɖewo dzi, ate ŋu ana alɔ̃madɔmadɔ ƒomevi bubuwo nadzi ɖe edzi.

Ne dɔlélea te ŋu nɔa te ɖe atikewɔwɔ nu la, ɖɔktawo ate ŋu adze agbagba be yewoaxe mɔ ɖe alɔ̃madɔmadɔ ƒomevi aɖewo nu alo aɖe wo dzi akpɔtɔ. Le kpɔɖeŋu me, ele vevie ŋutɔ be woaxe mɔ ɖe atonic seizures nu, elabena edo ƒome kple abixɔxɔ le ame ƒe anyidzedze me ƒe afɔku gã aɖe.

Nuɖuɖu ŋuti atikewɔwɔwo

Le ame geɖe siwo ŋu asrã sesẽ le gome la, tɔtrɔ le woƒe nuɖuɖu ŋu ate ŋu akpe ɖe ame ŋu be woaɖe alɔ̃madɔmadɔ dzi akpɔtɔ alo atɔ te wo kura. Ketogenic nuɖuɖu na asrãdɔ – nuɖuɖu si me protein kple ami sɔ gbɔ ɖo eye carbohydrates mesɔ gbɔ o – nye nusi ɖɔktawo kafua zi geɖe. Ate ŋu anye tiatia nyui aɖe ne atikewo mewɔ dɔ o.

Togbɔ be ketogenic nuɖuɖu nye atike si ame geɖe lɔ̃a zazã na asrã sesẽ hã la, kuxi ʋɛ aɖewo le eŋu. Ne èwɔ ɖe edzi pɛpɛpɛ ko hafi nuɖuɖu sia wɔa dɔ. Esia le alea elabena carbohydrates, abe sukli kple nuɖuɖu siwo me starch le ene ɖuɖu fũ ate ŋu ana ame naxɔ alɔ̃. Gake nuɖuɖu bubu siwo ŋu wotrɔ asi le hã ate ŋu akpe ɖe ame ŋu. Ne ètsɔ ɖe le eme la, wò ɖɔkta ate ŋu akpe ɖe ŋuwò nàte nuɖuɖu siawo dometɔ ɖeka kpɔ.

Ahɔhɔ̃mekoko kple mɔ̃ siwo wotsɔ dea ahɔhɔ̃a me

Le go aɖewo me, vevietɔ ne atikewɔwɔ bubuwo mewɔ dɔ o la, amekokoe nye tiatia nyuitɔ. Amekoko ƒomevi aɖewoe nye esi:

• Vagus Nerve Stimulation (VNS): Esia bia be woatsɔ mɔ̃ aɖe ade ŋutilã me si tsɔa elektrikŋusẽ fafɛ aɖe yia tagbɔ ƒe lãmeka 10 lia, si nye vagus nerve – si do ƒome kple ahɔhɔ̃a tẽ. Fifia sia ate ŋu aɖe alɔ̃madɔmadɔ ƒe dzidziɖedzi kple eƒe sesẽ dzi akpɔtɔ. Le ɣeyiɣi aɖe megbe la, eƒe ŋusẽkpɔɖeamedziwo dzina ɖe edzi. Esia fia be alɔ̃madɔmadɔ mesɔ gbɔ o eye alɔ̃madɔmadɔ hã masẽ o. Mɔ̃ sia dede ame me nye dɔ si woate ŋu atrɔ, si me afɔkuwo mesɔ gbɔ o eye wòxɔa ɣeyiɣi kpui aɖe ƒe hayahaya, eyata wobua eŋu zi geɖe hafi woawɔ dɔ gã aɖe nɛ.
• Corpus callosotomy: Corpus callosum nye ahɔhɔ̃a ƒe akpa aɖe si wɔa dɔ abe tɔdzisasrã ene le miame kple ɖusime ƒe afã dome. Ne wotso corpus callosum la, dzesi siwo mesɔ o siwo hea alɔ̃dɔdɔ vɛ la dzudzɔa yiyi kple megbe. Esia ate ŋu aɖe alɔ̃madɔmadɔ ƒe dzidziɖedzi dzi akpɔtɔ, alo atɔ te alɔ̃madɔmadɔ sesẽ siwo wɔa nuwɔametɔwo kura gɔ̃ hã.
• Hemispherectomy `(Akpa ƒe akpa aɖe ɖeɖeɖa)`:Esia bia be woaɖe ahɔhɔ̃a ƒe akpa ɖeka ɖa to amekoko me. Togbɔ be esia adze nusi gbɔ eme hã la, eŋutinunyalawo ate ŋu azãe atsɔ atɔ te alɔ̃madɔmadɔ siwo dzi womate ŋu aɖu o. Emegbe la, kamedede ate ŋu akpe ɖe ahɔhɔ̃a ŋu zi geɖe be wòatrɔ ɖe tɔtrɔa ŋu. Ahɔhɔ̃a gbugbɔa anyigbatata wɔa eɖokui, eye akpa susɔea xɔa akpa si woɖe ɖa la ƒe dɔwɔwɔwo.
• Resection: Ahɔhɔ̃a ƒe wɔwɔme ƒe tɔtrɔ ate ŋu ahe LGS vɛ ɣeaɖewoɣi. Ne ɖɔktawo te ŋu ke ɖe nu ma tɔgbe si mesɔ o ŋu la, woate ŋu aɖe ahɔhɔ̃meka siwo gblẽ alo esiwo le dɔ lém la ɖa eye woadzudzɔ aɖuɖɔtoeawo. Gake esi wònye be le LGS me la, alɔ̃madɔmadɔ ƒe dɔwɔna nɔa ahɔhɔ̃a ƒe akpa siwo wu ɖeka ta la, zi geɖe la, esia menyea tiatia si kpɔa dzidzedze boo aɖeke na LGS o.

Kuxiwo/dɔdamɔnu ƒe nugbegblẽ le ame ŋu

Kuxi siwo dona tso atikewɔwɔ me la ku ɖe atikewɔwɔ ɖesiaɖe koŋ ŋu. Eyata anyo wu be nàƒo nu kple wò ɖɔkta tso kuxi siwo le atike si wɔm wò alo viwòa le la ŋu. Emegbe ɖɔktaa ate ŋu ana nyatakaka siwo sɔ ɖe wò nɔnɔmea, wò nɔnɔmewo, kple atikewɔwɔ ƒe nɔnɔme bubuwo nu wò.

Aleke gbegbee nye lãme asẽ le atikewɔwɔ vɔ megbe kpuie? Ɣeyiɣi didi kae wòaxɔ hafi ahaya?

Ɣeyiɣi si nàhaya le atikewɔwɔ vɔ megbe la toa vovo ŋutɔ le atikewɔwɔmɔnu siwo nèzã kple wò nɔnɔme bliboa nu. Wò ɖɔktae nye ame nyuitɔ kekeake si agblɔ nusi tututu nàkpɔ mɔ na kple ɣeyiɣi didi si wòaxɔ hafi nàhaya.

Ðe woate ŋu axe mɔ ɖe Lennox-Gastaut ƒe dɔlélea (LGS) nua?

Zi geɖe la, LGS menye nɔnɔme si woate ŋu axe mɔ na o. Eye womate ŋu aɖe afɔku si le eŋu xɔxɔ me hã dzi akpɔtɔ o. Nusi to vovo koe nye be woaxe mɔ ɖe ta kple ahɔhɔ̃ ƒe abi siwo ate ŋu ado tso LGS me nu. Mɔ ɖeka kolia si dzi nàto axe mɔ ɖe nɔnɔme sia nu enye be nàna viwòwo nado gakuku siwo dzi woda asi ɖo, siwo ŋu woɖo kpee.

Nukae wòle be makpɔ mɔ na ne nɔnɔme sia le mía alo vinyea ŋu?

Lennox-Gastaut ƒe dɔlélea nye dɔléle si me tsonuwo sesẽ zi geɖe. Ðevi geɖe siwo ŋu dɔléle sia le la va zua nusɔsrɔ̃ ƒe kuxiwo eye woƒe ahɔhɔ̃ gblẽna tegbee si wɔnɛ be woƒe susu ƒe ŋutetewo xea mɔ na wo. Azɔ hã, esi wònye be atonic seizures (drop attacks) bɔ, eye zi geɖe la, ehea ame dzea anyi ta la, ɖevi siwo ŋu nɔnɔme sia le la le afɔku me be woaxɔ abi geɖe wu.

Dɔléle sia hã dada sesẽ. Ðevi geɖe siwo ŋu wòle la hiã beléle na wo le woƒe agbemeŋkekewo katã me elabena womete ŋu kpɔa wo ɖokui dzi o. Gake ame aɖewo siwo ŋu dɔléle sia le la ƒe ahɔhɔ̃ me gblẽ vie, si fia be woate ŋu anɔ agbe le wo ɖokui si.

Ɣeyiɣi didi kae (LGS) nɔa anyi?

Negbe ɖe wowɔ atike be woatɔ te alɔ̃madɔmadɔa keŋkeŋ (si mebɔ kura o) ko hafi LGS nye dɔléle si nɔa ame ƒe agbemeŋkekewo katã me.

Nukae nye nɔnɔme sia ƒe mɔkpɔkpɔ?

Afɔku gãtɔ siwo le Lennox-Gastaut ƒe dɔlélea ŋue nye ahɔhɔ̃ ƒe gbegblẽ le alɔ̃madɔmadɔ si dzi womeɖu o ta, alo tso anyidzedze si alɔ̃madɔmadɔ hena vɛ gbɔ. Le afɔku mawo ta la, amesiwo ŋu ``LGS'' le ƒe ku ƒe agbɔsɔsɔme le ƒe 10 me tso esime wokpɔ dɔlélea le 3% va ɖo 7% dome.

Le go aɖewo me la, atikewɔwɔ ate ŋu atɔ te alɔ̃madɔmadɔ si LGS hena vɛ. Esia nana nɔnɔmea tɔa te, gake mate ŋu aɖɔ nusiwo gblẽ le ahɔhɔ̃a ŋu le alɔ̃madɔmadɔ siwo wòxɔ va yi ta o.

Aleke malé be na ɖokuinye? / Aleke mawɔ akpɔ vinye dzi?

Ne LGS le ŋuwò alo wò lɔlɔ̃tɔ aɖe ŋu la, ele vevie ŋutɔ be nàwɔ ɖe wò ɖɔkta ƒe mɔfiamewo dzi pɛpɛpɛ. Esia lɔ:

• Atikewo nono abe alesi woŋlɔe ene.
• Ðɔkta gbɔ yiyi abe alesi wokafui ene.
• Lé ŋku ɖe alɔ̃madɔmadɔ ŋu eye woaƒo asa na nusiwo hea dɔlélea vɛ alo nɔnɔme siwo ate ŋu ahe alɔ̃dɔdɔ vɛ.

Ɣekaɣie wòle be makpɔ ɖɔkta?

Wò alo viwò ƒe ɖɔkta agblɔ na wò be nàge ɖe eme hena sasrãkpɔ siwo akplɔ wò ɖo ne ehiã. Ele be nàkpɔ wò ɖɔkta hã ne wò alɔ̃madɔmadɔ ƒe dzesiwo trɔ ŋutɔ alo ne wokpɔ ŋusẽ ɖe wò gbesiagbegbenɔnɔ kple dɔwɔna siwo nèwɔna ɖaa dzi.

Ɣekaɣie wòle be mayi Atikewɔwɔ Kpata ƒe Dɔwɔƒe (ETU) ?

Ne alɔ̃madɔmadɔ alo alɔ̃madɔmadɔ zi geɖe si ɖo atikewɔwɔ ƒe nɔnɔme kpata si woyɔna be status epilepticus ƒe dzidzenuwo gbɔ la, ele be nàyi xɔ si me wowɔa dɔ kpata le le kɔdzi si te ɖe ŋuwò. Esia fia be le nɔnɔme siwo gbɔna me la:

• Ne alɔ̃madɔmadɔ zi ɖeka xɔ aɖabaƒoƒo 5 va ɖo 30.
• Ne alɔ̃madɔmadɔ eve alo esi wu nenema va le aɖabaƒoƒo 30 me eye amea ƒe susu megava nɔ ŋudzɔ bliboe le alɔ̃madɔmadɔa wɔɣi o.

Gbedasi si Wotsɔ Yi Aƒeme

Lennox-Gastaut ƒe dɔléle (LGS) nye asrãdɔ sesẽ aɖe si dzea egɔme kaba. Zi geɖe la, ate ŋu akpɔ ŋusẽ gã aɖe ɖe ɖevi ƒe agbe dzi, ɣeaɖewoɣi le eƒe agbemeŋkekewo katã me. Togbɔ be edada sesẽ hã la, atike yeyewo, amekoko, kple atikewɔwɔ ate ŋu akpe ɖe ame ŋu be wòaɖe dɔlélea ƒe sesẽ dzi akpɔtɔ eye wòaɖe dɔlélea ƒe kaka dzi akpɔtɔ. Ƒã hafi atikewɔwɔ ate ŋu ada dɔlélea keŋkeŋ. Gake numekuku geɖe hiã be woatsɔ anya nenye be woate ŋu ada dɔléle sia alo adae alo womate ŋu adae o. Ne dzesi siawo dometɔ aɖe le viwòa ŋu la, anyo wu be nàyi ɖɔkta gbɔ kaba ale si nàte ŋui.

` Lennox-Gastaut ƒe dɔléle, LGS, asrã, alɔ̃madɔmadɔ, ɖeviwo ƒe dɔlélewo, ahɔhɔ̃medɔlélewo, ahɔhɔ̃medɔlélewo